He damdawi Miglustat an tih hi i hre tam lo mai thei. A chhan chu damdawi lam thil awm lo deuh tan damdawi bik pek a nih vang a ni. Chuvangin vawiinah hian he damdawi Miglustat tih hi kan sawi dawn a, a enkawl natna Gaucher tih hi kan sawi dawn a ni. Nangmah emaw i hriat mi emaw hnenah he damdawi hi i lo pe tawh a nih chuan he thu hi i tan a pawimawh hle ang.
Miglustat hi eng damdawi nge ni? Eng nge a tih?
A awlsam zawngin sawi ila, Miglustat hi kan taksaa thau chi khat ti chhe thei enzyme level pangngai vawng reng tura puitu damdawi a ni. Type 1 Gaucher natna enkawlna atan bik hman a ni .
Tunah chuan Gaucher natna hi eng nge ni tih i ngaihtuah mai thei. Chu chu tlem han hrethiam ila. Gaucher natna hi thlahtute atanga lo chhuak a ni. Hemi kawngah hian thil thleng chu kan taksaa thau chi hrang hrang (a bik takin glucocerebroside) dik taka tihchhiat theihna tura enzyme mamawh glucocerebrosidase hnathawh a tlahniam emaw, a awm lo vek emaw pawh a ni. Tichuan heng thau chi hrang hrangte hi taksa peng hrang hrangah, entirnan, ril, thin, leh ruhroah te a awm a. Hei hian hriselna lama harsatna hrang hrang a thlen thei a ni. Chuvangin, damdawi Miglustat hian a tih chu taksaa chutiang thau tam lutuk lo awm chu a tihziaawm a ni.
He damdawi hi Zavesca brand name hmanga hralh a ni tlangpui . Mahse, a chang chuan doctor-te chuan he damdawi hi natna dang atan pawh an hmang thei tih hre reng ang che. Chuvangin zawhna i neih chuan i doctor emaw pharmacist emaw zawt la a tha ber.
He damdawi hi ka hman hmaa ka doctor hnena ka hrilh tur te chu engte nge ni?
Miglustat i ei tan hmain doctor hnenah i hrilh ngei tur thil tlemte a awm. Chûng thilte sawi loh chuan a ṭûl lova harsatna a thlen thei che a ni. Chuvangin heng thilte hi i doctor hnenah rinawm takin sawi rawh.
- If you have nerve problems , chu chu i taksa peng hrang hranga kang, rilru hah, tingling sensations tihna a ni.
- Kidney natna i neih chuan .
- Miglustat, damdawi dang, ei tur, food dye, emaw preservatives emaw allergy i neih chuan min hrilh la, minor pawh nise.
- Naupai emaw, nau pai tum emaw i nih chuan hei hi a pawimawh hle.
- Nu hnute pe lai i nih chuan.
Doctor chuan heng thilte hi a hriat chian hnuah chuan he damdawi hi i tan a tha em tih te, uluk taka hman dan tur te pawh a rel thei ang.
Engtin chiah nge he damdawi hi ka hman ang?
He damdawi hman dan dik tak hriat a pawimawh hle. Doctor thupek leh damdawi dawrin a pek prescription label zawm rawh.
- He damdawi hi tui glass khat nen ei tur a ni.
- I damdawi chu a hun takah ei la , i doctor-in a tih angin. Entirnan, ni khatah vawi thum a nih chuan chutiang hunah chiah chuan ei rawh.
- I doctor-in a tih aia tam damdawi ei ngai suh.
- Tin, doctor thurawn tel lo chuan damdawi ei kha titawp thut suh. Chutianga tih chuan i dinhmun a tichhe thei a ni.
He damdawi hi naupang te te hnenah ka pe tur em ni?
He damdawi hi naupang tê tête i pe a nih chuan naupang enkawltu doctor hnenah sawipuiin an thurawn zawm tur a ni. Fimkhur bik a ngai mai thei.
Damdawi i ei tam lutuk chuan engtin nge ni ang? (A tam lutuk) .
He damdawi hi accident-a i ei tam lutuk nia i hriat chuan i hnai ber poison control center emaw hospital emergency room emaw call nghal rawh. Hun khawhral suh.
Hriat tur pawimawh: He damdawi hi i tan chauh pek a ni. Eng vang pawhin midang hnenah pe suh , i neih ang symptoms nei pawh nise.
Damdawi dose i ei loh chuan engtin nge i tih ang?
A châng chuan damdawi dose khat pawh i hloh thei bawk. Chutiang a nih chuan lungngai suh.
- I hriatreng veleh missed dose kha ei nghal rawh.
- Mahse, i hriatreng hunah i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, a hun ruatah dose dang ei mai rawh.
- Dose hloh tawh chu tihpun nan double emaw extra emaw ei ngai suh. Chutianga tih chuan side effect a nei thei.
He damdawi nen hian eng inzawmna dang nge awm thei?
Miglustat nena ei hian harsatna thlen thei damdawi thenkhat a awm. Chu chu Miglustat hman tangkai dan an tihziaawm thei a, a side effect pawh an tipung thei tihna a ni.
- Hemi nena inzawm thei damdawi pakhat chu imiglucerase an tih hi a ni .
He list hi a kimchang lo hle. Chuvangin, i doctor hnenah damdawi dang zawng zawng (prescription leh non-prescription), herb, dietary supplement, leh zu i in emaw, zu i in emaw, dan loa ruihhlo i hman chuan i doctor hnenah hrilh rawh. Thil thenkhat chu i damdawi nen a inzawm thei.
He damdawi ei lai hian eng thilte nge fimkhur tur?
Miglustat ei lai hian fimkhur tur tlemte a awm.
- I doctor hnenah check-up neih fo tur a ni. Hei hian i doctor-in i dinhmun leh i damdawi a thawk tha em tih a hriat theih nan a pui ang.
- He damdawi i ei lai hian lab hna engemaw zat tihsak a ngai thei bawk. Hemi chungchang hi i doctor chuan a hrilh ang che.
- Mi thenkhat chuan he damdawi hi an ei lai hian riltam an nei thei. Chutiang a nih chuan i doctor nen in sawipui ang che. Thurawn \ha tak a pe ang che.
Naupai leh mipa tan thupek bik:
Hei hi a pawimawh hle a, a bik takin hmeichhia leh mipa chhungkaw din tumte tan chuan a pawimawh hle.
- Hmeichhia: Naupai i tum a nih chuan, a nih loh leh naupai i nih i ring a nih chuan i doctor hnenah hrilh nghal rawh. Nausen piang lai hian side effect na tak a thlen theihna a awm. Chuvangin hemi chungchang hi i doctor hnenah zawt la.
- Mipa: He damdawi hi i ei lai leh damdawi i ei loh hnu thla 3 chhung fa neih tum suh. Hemi hun chhung hian naupai venna kawng tha tak tak hmang thin ang che. Hemi chungchang pawh hi doctor nen inbiakna neih a pawimawh hle.
He damdawi hian eng side effect nge a neih theih?
Damdawi zawng zawng ang bawkin Miglustat hian side effect a nei thei a, mahse mi zawng zawngin an vei vek lo. Side effect thenkhat chu a na hle a, i hriat chuan doctor hnenah i hrilh nghal tur a ni. Ṭhenkhat chu an pawi lo tlangpui a, mahse an awm reng chuan doctor hnêna hrilh a ṭha .
Side effects i doctor hnena i hrilh nghal tur:
Heng symptoms zinga pakhat tal i neih chuan doctor emaw healthcare provider emaw hnenah sawi hmasa phawt ang che.
- Kang, rilru hah, tingling feelings – a bik takin taksa peng hrang hrangah.
- Menstrual cycle inthlak danglamna .
- Mit hmuhna inthlak danglamna – mit hmuhna chu a fiah lo va, hmun hnih a hmuh ang maiin.
- Tremor – Ke ruh leh ke ruhte chu thunun theih loh khawpin a nghing.
- Thisen chhuah emaw, hliam emaw – I taksaah hliam danglam tak i neih chuan, emaw, hliam tenau tak atanga pawh thisen chhuah a tawp loh chuan.
Side effects nasat loh tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur:
Chûngte chu ni engemaw zât chhûngin a bo ṭhîn a, mahse a awm reng emaw, a tihbuai emaw chuan i doctor hnênah hrilh rawh .
- Kawthalo
- Luak chhuak thei
- Lu na
- Chaw ei chakna hloh
- Lower sperm count – Hei hi mipa tibuaitu thil a ni.
- Nausea, luak chhuak
- Pum natna , gas
- Rihna tihtlem
He list hi a kim lo tih hre reng ang che. He list-a tel lo thil danglam tak i hmuh chuan i doctor hnenah hrilh rawh. Side effects chungchangah medical advice dil turin i doctor zawhfiah rawh.
He damdawi hi engtin nge i dahkhawm?
Damdawi tha taka dahkhawm a pawimawh hle bawk.
- Naupang tê tête hmuh theih lohna hmunah dah rawh.
- Room temperature-ah dah la, 15 leh 30 degree Celsius (59 leh 86 degree Fahrenheit) inkar ah dah rawh . Khua lum leh vawt nasa takah dah suh.
- Damdawi expired hman loh tur. Anni chu uluk takin paih rawh.
A tawp berah chuan thu pawimawh tlemte (Take-Home Message) .
Okay, chuvangin he damdawi Miglustat tih hi hriatthiamna tha tak i neih kan beisei.
- He thuziak hi a tawi zawng chauh a ni tih hre reng ang che. A chipchiar zawng zawng a huam vek lo.
- He damdawi chungchanga zawhna dang i neih chuan i doctor, pharmacist emaw, healthcare provider dang emaw zawt la.
- Gaucher natna hi natna awm lo tak a nih avangin leh Miglustat hi damdawi bik a nih avangin doctor thupek zawm a pawimawh hle.
- I damdawi ei tur dik tak leh a hun takah ei thin ang che. Side effects te chu fimkhur rawh. Date ruat saah doctor hmu rawh.
Hriselna tha tak nei turin duhsakna kan hlan e!
` Miglustat, Zavesca, Gaucher natna, enzyme, damdawi side effects, prescription damdawi, Gaucher natna











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