Kan thluak hi a makzia leh a buaithlak zia hi i ngaihtuah ngai em? He taksa peng te tak te hian kan ngaihtuahna zawng zawng, kan chetna zawng zawng, leh kan hriatrengna zawng zawng a thunun vek a ni. Chuvangin, thluak hian oxygen leh nutrient pe thei thisen kal chhunzawm zel, tihtawp loh a mamawh a ni. Mahse, thluaka thisen phurtu thisen kalna kawng lian ber berte chu a inkharkhip a nih chuan eng nge thleng ang tih han ngaihtuah teh? Vawiin hian chutiang natna hmuh tur awm lo, mahse hriat tur pawimawh tak pakhat chu kan sawi dawn a ni. Chu chu Moyamoya Disease a ni.
A awlsam zawngin, Moyamoya chu eng nge ni?
Stroke hi kan thluaka thisen kalna kawngte a khawih a, kan thluaka thisen kalna kawngte a khawih thin. Damdawi lam hawi chuan thluaka thisen zam natna a ni. Kan kawr chhungah hian thisen kalna kawng lian pahnih, thluaka thisen phurtu, carotid arteries an tih chu a awm a. Stroke-ah chuan heng main artery pakhat emaw, a chang chuan a pahnih emaw hi a zim zauh zauh a, a block ta a ni. Tin, thluaka artery pawimawh dang, cerebral arteries te pawh a nghawng thei bawk. Hengte hi kan thluak hmalam peng hrang hranga thisen pe chhuaktu thisen kalna kawng lian ber berte an ni.
I in chhunga tui rawn thlentu main water pipe chu a inkhar niin han ngaihtuah teh. Chuti a nih chuan eng nge thleng? Tui a awm lo. Chuvangin, in chhunga pipe te tak te atang hian tui lak tumin a bei thin. Kan thluak hi a inang reng a ni. Thisen kalna bulpui chu a inkharkhip chuan thluak chuan a tlakchhamna phuhruk nan thisen kalna kawng te tak te, te tak te thar tam tak a siam thin. Hengte hi side road ang mai a ni. Mahse buaina chu, heng thisen kalna kawng tharte hi an chak lo hle a, an thim hle bawk. Chuvangin thisen pawh main vein ang bawkin an supply thei lo. Heng vein chak lo tak takte hi a chang chuan a puak thei bawk. Chutiang hunah chuan Moyamoya Disease hian thluak chhungah thisen a chhuak thei bawk (Brain hemorrhage). Tin, thluak hian thisen a hmuh tlem avangin stroke ang chi natna khirh tak tak a awm thei bawk.
Engvangin nge hei hi "Moyamoya" an tih?
"Moyamoya" tih hi Japanese tawng a ni. "Meikhu chhuak ang mai" tihna a ni. He natna hmuchhuak hmasa ber Japanese doctor-te chuan thluaka thisen kalna kawngte angiogram an tih chuan thisen kalna kawng te tak te lo piang tharte network chu meikhu chhuak ang maiin a inzawm khawm tih an hmu a. Chuvangin he natna hi "Moyamoya" tiin an vuah ta a ni.
Moyamoya natna lan chhuah dan chu engte nge ni?
He natna lan chhuah dan ber chu thluaka thisen kal tlem vang a ni. A châng chuan stroke emaw, transient ischemic attack (TIA) engemaw zat emaw hnuah natna hi hriat hmasak ber a ni. Heng stroke te te hi "mini-stroke" an ti fo thin. Chumi awmzia chu stroke symptoms te hi rei lo te chhung atan a lo thleng a, a bo vek tihna a ni.
He natna lan chhuah dan tlangpui thenkhat hi han thlir ila.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Stroke emaw mini-stroke emaw (TIAs) emaw a awm thei. | Taksa sir khata rilru hahna, tawng harsa, leh hmai sir khata tla te ang chi natna lan chhuah dan. Heng symptoms te hi TIA-ah hian hun rei vak lo hnuah a reh tlangpui. |
| Thluak thisen chhuak | Thluaka thisen chhuah hi thisen kalna kawng chak lo leh te tak te a puak hian a thleng thin. Hei hian lu na tak a thlen thei a ni. |
| Lu na | Lu na fo, a chang chuan na tak tak. |
| Seizures a awm thin | Fit-like condition lo awm dan. |
| Thunun theih loh chetna | Taksa peng hrang hrang, ke leh ke chi hrang hrangte chu thunun theih lohvin an che a. |
| Hmasawnna lama tlai lutuk | He natna hian naupang tête, a bik takin a nghawng a nih chuan an thanlenna leh zirnaah tihkhawtlai an tawk thei a ni. |
| Sensory lama harsatna a awm | Mit hmuhna, hriatna, rim, khawih, ei leh in lama harsatna. |
Moyamoya natna hi eng nge thlen?
Dik tak chuan he natna thlentu dik tak hi hriatchhuah a la ni lo.. Mahse zirchiangtute chuan hei hi genetic link a awm niin an ngai. Chu chu thlah kal zelah a kal zel theih tihna a ni. He natna hi Japanese mite zingah a hluar hle avangin an gene-ah hian inzawmna engemaw zat a awm tih hmuhchhuah a ni. Tunah chuan `RNF213` tih gene-a inthlak danglamna hian hei hi a thlen thei tih hmuhchhuah a ni ta.
A châng chuan, he Moyamoya phenomenon hi damdawi lam thil dang nen pawh a thleng thei bawk. Tichuan Moyamoya syndrome kan ti ta a ni. Entir nan:
- Down syndrome tih hi a ni
- Graves-a natna a ni
- Neurofibromatosis chi khat a ni
- Sickle cell natna a ni
- Atherosclerosis natna a ni
Natna nei mi pakhat chu Moyamoya tih hming pu natna vei theihna hlauhawm tak a ni.
He natna hi tuin nge vei tam ber?
Moyamoya hi natna hmuh tur awm lo tak a ni . Sri Lanka ang ramah chuan a awm tlem hle. Mahse he natna hi fimkhur a pawimawh hle.
- He natna hi kum eng pawhah a vei thei a, mahse naupang kum 5 leh 10 inkar leh puitling kum 30 leh 50 inkar ah a tam ber .
- A chhan dik tak hriat ni lo mah se, hmeichhiain he natna hi mipa aiin a let hnih velin an vei tam zawk a ni.
- He natna hi Japan leh Asia chhim lam ram danga mite zingah hmuh tur a awm fo.
He natna hi engtin nge dik taka i hriat theih?
A hmaa kan sawi tawh ang khan symptoms i neih chuan i doctor chuan a enfiah hmasa ang che a, i symptoms te chu a zawt hmasa ang che. Tichuan, moyamoya natna rinhlelhna a awm chuan, a finfiah nan special test thenkhat an rawt ang.
| Fiahna | Hei hi engtin nge i tih? |
|---|---|
| Cerebral arteriography hmanga thil tih a ni | Hei hi he natna hriat theihna atana test tha ber a ni. He test-ah hian tube te tak te (catheter) chu kut emaw ke emaw artery-ah dahin, chuta tang chuan thisen kalna kawng hrang hrangah dye bik an inject a ni. Chumi hnuah chuan X-ray image an la a, thisen kalna kawngte chu engtiang chiahin nge a te tih leh thisen a luang chhuak tha tih hriat a ni. |
| MRA Scan (Magnetic Resonance Angiography) hmanga tihchhuah a ni. | Hei hi painless test a ni a, magnetic field leh radio wave hmanga thluaka thisen kalna kawng chipchiar taka thlalak lak a ni. |
| MRI scan (Magnetic Resonance Imaging) hmanga tihchhuah a ni. | MRA ang chiah hian thluak tissue dinhmun enfiah nan hman a ni. Hei hian thisen kal tlem avanga thluaka chhiatna a awm leh awm loh hriat theih nan a pui thei a ni. |
Moyamoya natna enkawlna tur a awm em?
Ni e, he natna hi enkawl dan tur a awm. Enkawlna kawngah hian tum lian tak pahnih a awm a. Pakhat chu symptoms control hi a ni. A dang chu thluaka thisen kal dan tur tihchangtlun a, stroke ang chi natna khirh tak tak awm theihna tihtlem a ni.
1. Damdawi hmanga enkawl
Doctor chuan damlo dinhmun a zirin damdawi chi hrang hrang a pe thei a.
- Aspirin: He damdawi hian thisen zam a veng a, chu thisen kalna kawng te tak te kal tlangin a ti awlsam bawk.
- Antiseizure damdawi: Natnain epileptic seizure a thlen chuan heng damdawi te hi control nan pek thin a ni.
- Anticoagulants: Hengte hian thisen zam a veng thei a, mahse doctor-te chuan thisen chhuah theihna a awm avangin thil bik tak takah chauh hengte hi an rawt a ni.
- Calcium channel blockers: Hengte hian lu natna ang chi symptoms te chu a tiziaawm thei a ni. Mahse, thisen sang a tihniam thei bawk a, chu chuan stroke hlauhawmna a tipung thei a, chuvangin fimkhur taka hman tur a ni.
A pawimawh ber chu damdawi hian thisen kalna kawng a ti thim thei lo , chuvangin natna hi zawi zawiin a zual thei a ni.
2. Surgery hmanga enkawlna (Bypass Surgery) .
Damdawi hmanga natna hi tihreh theih a nih loh chuan, zawi zawiin a zual zel a nih chuan doctor-in zai a rawt thei a ni. Hei hi bypass surgery an ti a.
A awlsam zawngin, hei hian thluaka thisen kalna tur kawng thar siam a, thisen kalna kawng khar chu kal pelin a huam a ni. Hei hian lu vuna thisen pe thin artery hrisel tak lak a, thluaka thisen kalna kawng pakhat nena inzawm tir a huam a ni. Kawngpui buai tak paltlang turin flyover thar siam ang mai a ni. He surgery hian thluak thlenga thisen a tipung thei a, stroke hlauhawmna nasa takin a ti tlem thei a ni.
I doctor chuan eng surgical procedure nge i tan a tha ber tih chipchiar takin a hrilhfiah ang che, a thatna leh that lohna te pawh a hrilhfiah ang che.
Engtikah nge emergency medical help i zawn ang? Stroke natna lan chhuah dan (FAST) .
Moyamoya natna vei tan chuan stroke symptoms hriat a pawimawh hle . Enkawlna an dawn hma poh leh thluak chhiatna a tlem phawt chuan ven theih a ni. Acronym FAST hi stroke symptoms hriat reng nan hman a ni.
| Stroke Symptoms (FAST) - Thiltih nghal rawh! | |
|---|---|
| F - Hmai | I hmai sir khat chu a hlim hmel em? I nuih hian i hmai sir khat chu a inher em? |
| A - Arms | I kut pahnih chu i chawi sang thei em? Kut pakhat a tla thla em? |
| S - Thusawi | Inbiakna chu a buaithlak em? I bengchheng em? Thumal awlsam tak sawi a har em? |
| T - Hun | Heng symptoms te hi i neih chuan tihkhawtlai suh. Damdawi in pakhat Emergency Department (ETU) ah kal nghal la, ambulance pawh ko rawh. Hun hi a pawimawh ber a ni! |
Heng bakah hian natna lan chhuah dan , rilru buai thut, taksa sir khata bengchheng, mit lama harsatna, kal harsa, emaw, lu na na tak, tuar theih loh ang chi te pawh hi stroke chhinchhiahna a ni thei bawk.
He natna nena kan khawsak hian natna hi a hmaa hriatchhuah a nih a, uluk taka enkawl a nih chuan mi tam zawk chuan nun pangngaiin an khawsa thei a ni. Enkawl loh chuan natna hi a na thei hle a, thihna pawh a thlen thei a ni. Chuvang chuan natna lan chhuah dan fimkhur a, Doctor thupek dik taka zawm a pawimawh hle.
Take-Home Thuchah a ni
- Moyamoya natna hi thil awm lo tak a ni a, thluaka thisen petu main artery chu a zim zauh zauh a, a block ta a ni.
- Hei hian thluaka thisen kalna a tlahniam thei a, chu chuan natna khirh tak tak, stroke emaw thluaka thisen chhuak emaw a thlen thei a ni.
- A lan chhuah dan ber chu stroke ang chi, lu na, leh seizure te hi a ni.
- He natna hi a hmaa hriatchhuah a, damdawi emaw, zai emaw hmanga enkawl a nih chuan hlawhtling taka enkawl theih a ni.
- Nangmah emaw, i hriat miin emaw stroke (FAST) symptoms i neih chuan damdawi in Emergency Department (ETU) ah i kal nghal tur a ni. Hun khawhral hian thluak chhiatna a tipung thei a ni.
- Hemi chungchangah hian rinhlelhna emaw zawhna emaw i neih chuan i doctor hnenah thurawn dil rawh.











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