I vunah hian rang takin, hnim hring te te a lo lang a, chu chu a puak darh a, a na a, tuar theih loh khawpa natna leh natna a thlen tih i hmu tawh em? A chang chuan eng thil nge thleng tih pawh i ngaihtuah thei lo a ni lawm ni? Vawiin hian vun natna, chutiang harsatna thlentu, mahse a tlem deuh deuh chu kan sawi dawn a ni. Hei hi `(Pemphigus Foliaceus)` an ti a. Hlau suh, he thu hi awlsam takin sawi ila.
`Pemphigus Foliaceus` tih hi eng nge ni?
A awlsam zawngin, `(Pemphigus Foliaceus)` hi kan taksa `(immune system)` a thil dik lo avanga lo awm vun natna a ni. Ngaihtuah teh, kan taksa chhungah sipai rual kan nei a, chu chu kan taksa hriselna (immune system) a ni. An hna chu pawn lam atanga hrik leh natna lo chhuakte do a, min venhim hi a ni. Mahse he `(Pemphigus Foliaceus)` dinhmunah hian heng sipaite hian kan vun cell hrisel `(skin cells)` te hi hmelma angin an ngai sual a, an rawn bei tan ta a ni. Chu chu vunah natna, itchy blisters leh sores a lo lang thin a ni.
Heng blisters te hi lu vun, hmai, kawr leh hnungzang ah te hmuh tur a tam ber . `(Pemphigus Foliaceus)` hi vun natna chi khat a ni a, natna chi hrang hrang `(Pemphigus)` an tih zingah a tel a ni.
He thil hi tuin nge nei tam ber? Hei hi a awm fo em?
A tlangpuiin `(Pemphigus Foliaceus)` symptoms hi kum 50 leh 60 inkar ah a lang a, mahse, kum eng pawhah a awm thei a, naupang tê tak têah pawh a awm thei.
Khawvel hmun thenkhatah, a bik takin South America-ah chuan ``Fogo Selvagem`` tih natna a awm a, hei hi he natna nen hian a inang hle. Insect thenkhat emaw, environment thil dang emaw avanga lo awm nia rin a ni.
Mahse, `(Pemphigus Foliaceus)` hi vun natna hmuh tur awm lo tak a ni . Khawvel pum hi i thlir chuan mi maktaduai khat zinga mi pakhat atanga panga velin kum khatah `(Pemphigus)` natna an vei thin. Chuvangin `(Pemphigus Foliaceus)` hi a tlem zawk daih.
Hei hian engtin nge taksa a nghawng? Eng nge a lan chhuah dan?
Pemphigus Foliaceus hian i vunah hliam na tak a siam thin. Heng blisters te hi a te hle a , a chhe awlsam hle . An tliak chuan hliam an lo ni ta a ni. Heng hliam te hi a hring thei a, a hnah pawh a hring thei bawk. An itch nasa thei a , a na thei a , a kang thei bawk .
A hnuaia mite hi a lan chhuah dan ber atan hriat theih a ni:
- I vun chunglam (epidermis)-ah hian blisters emaw bumps te te, tui ang chi, sen emaw a lo lang thin. Chungte chu i taksa hmun zau takah a darh thei a ni.
- Blisters hi a nem hle a , a puak awlsam hle .
- Blisters chu a puak darh a, scaly, crusty lesions a siam thin.
- Heng blisters leh sores te hian itching, na, a inflammation a thlen thin .
Taksa chungah khawiah nge a symptoms hmuh tur awm?
Blisters leh sores chi hrang hrang awm tam ber chu:
- Lu vun a ni
- Hmai
- Nghawng
- Pawn lam
- Awm
Mahse, a pawimawh ber chu, `(Pemphigus Foliaceus)` chungchangah hianKawng leh hnar chhunga membrane nalh tak takte chu a nghawng lo.
Engvangin nge hetiang `(Pemphigus Foliaceus)` hi a lo awm? A chhante chu engte nge ni?
Hei hi a chhan dik tak chu chhui chian mek a ni. Tunah hian genetic leh environmental factor engemaw zatin hmun a chang thei niin an ngai.
Hei hi nu leh pa atanga fate hnena kai darh, thlahtu natna a ni lo. Mahse, HLA gene bik i neih chuan natna hi i vei theihna a sang zawk mai thei. HLA genes chanvo chu immune system-in kan taksaa hrik lut ang chi thilte a hriat theih nan a pui a, a tichhe vek a ni.
Ka sawi tawh ang khan Pemphigus Foliaceus hi autoimmune condition a ni . Hei hian nangmah ngeiin i immune system hian cell hrisel tak tak a bei tihna a ni. A bik takin Pemphigus Foliaceus-ah hian immune system (antibodies kan ti) siam protein te hian kan vun cell te inzawmkhawmtu adhesion point te chu an rawn bei sual a ni. Heng adhesion points te hi epidermis chhunga cell te inzawmkhawmtu sticky tape ang mai a ni. Chuvangin, taksain hengte hi a beih hian Pemphigus Foliaceus symptoms a lo lang thin.
Eng thilin nge hei hi a pung nghal (flare-ups)?
A hnuaia thilte hian `(Pemphigus Foliaceus)`, emaw ``flare-up`` symptoms a tipung nghal thei a ni:
- Damdawi thenkhat: Damdawi thenkhat, non-steroidal anti-inflammatory drugs (NSAIDs), penicillamine, nifedipine, captopril, leh enalapril te hian natna lan chhuahna a ti na zual thei a, a lan chhuah dan thar a thlen thei bawk. I doctor chuan i damdawi ei pakhatin natna a thlen nia a rinhlelh chuan damdawi chu a titawp thei a, a thlak danglam thei bawk. Doctor thurawn tel lo chuan damdawi ei kha bansan ngai suh.
- Insect seh: Khawvel hmun thenkhatah, a bik takin South America-ah chuan insect seh hian pemphigus chi khat ``Fogo Selvagem'' an tih chu a thlen thei a ni.
- Ni chhuahna: Ni atanga vun atanga ultraviolet (UV) rays a tlak chuan symptoms a pung thei.
He natna hi kai theih a ni em?
Ni lo, `(Pemphigus Foliaceus)` hi natna hrik kai theih a ni lo. Mi pakhat atanga mi dang hnenah khawih hmangin a darh thei lo. Chuvangin ṭul lova hlauhna thlen suh.
Engtin nge doctor hian hei hi a hriat theih?
I doctor chuan i medical history leh symptoms te a zawt ang. Tichuan, i vun chu a hring emaw, a hliam emaw a awm leh awm loh an enfiah ang. `(Pemphigus Foliaceus)` symptoms nen an inmil em tih test dang pawh an ti thei bawk.
Hemi atan hian eng test nge tih a nih?
Diagnosis finfiah nan a hnuaia test te hi tih theih a ni:
- Vun te tak te lak (Skin Biopsy):I vun sample tlemte la in microscope hmangin an enfiah thin. Hei hian test bik ``Immunofluorescence test'' tih a huam a ni.
- Thisen test: I thisen sample lak a, natna lan chhuahna thlentu antibodies a awm leh awm loh enfiah a ni.
Hei hi eng enkawlna nge ni?
`(Pemphigus Foliaceus)` enkawl dan hi mi hrang hrangah a inang lo thei . I doctor chuan i dinhmun a zirin enkawl dan tur a rel ang. A hnuaia enkawlnate hi hman a ni tlangpui:
- Damdawi natna lanchhuahna thlentu nia ngaih damdawi tihtawp emaw thlak emaw .
- Blisters tihziaawmna turin topical cream emaw, corticosteroid ang chi oral medication emaw hmang thin ang che. A nih loh leh topical calcineurin inhibitor te pawh a awm thei bawk.
- Immunosuppressive drugs, taksa hriselna tichaktu damdawi. Entirnan, damdawi `(Rituximab)`, `(Methotrexate)`, `(Mycophenolate)` emaw `(Azathioprine)` ang chi te.
Enkawlna zawng zawng hian side effect a nei thei tih hre reng ang che. Chuvangin enkawlna i tan hmain i doctor nen he thil hi sawipui hmasa phawt ang che. Damdawi thar i ei dan tur te, eng chen nge i ei tur tih te, tuna i damdawi hman mek chu a tibuai dawn em tih te zawt rawh.
Enkawl i tan hnuah i doctor chuan kar engemaw zat hnuah a enfiah leh ang che a, enkawlna a thawk tha em tih a en ang. I natna lan chhuah dan a zual emaw, kar engemaw zat hnua i dam loh chuan doctor hnenah hrilh ngei ang che.
Engtiang chiahin nge enkawl hnuah ka dam leh thuai ang?
Mi tin taksa hi a dam dan a inang lo. A tlangpuiin, kar hnih vel hnuah chuan blister thar a lo lang tawh lo va, vun natna chu a dam tan ta tih i hmu ang . Mahse, vun natna zawng zawng a dam vek theih nan kar engemaw zat a ngai thei. Pemphigus hi natna khirh tak a nih avangin nakin lawkah a natna lanchhuahna hi a lo lang leh thei a, a na zual thei bawk.
Pemphigus Foliaceus hi ven theih a ni em?
Pemphigus Foliaceus thlentu zawng zawng hi ven theih ni lo mah se, flare-up tihtlem nan a hnuaia mi hi i ti thei ang:
- Ni chhuahna hmun hi pumpelh rawh . Pawn lama i chhuah chuan invenna puan ha la, sunscreen hmang bawk ang che.
- Tuna i damdawi ei mekte chu i doctor nen sawiho la , heng symptoms te hi a thlen em tih en rawh. I doctor-in a tih hma loh chuan damdawi engmah ei kha bansan suh.
- Insect-in natna a darh na hmuna i awm chuan, invenna thawmhnaw ha la, insect repellent hmang la , window-ah screen dah rawh.
- I vun tana tha tur sahbawn rimtui lo leh lotion hmang thin ang che.
Hetiang dinhmun nen hian eng nge i beisei tur?
Pemphigus Foliaceus hi damdawi kimchang a la awm lo .Mahse, lungngai suh, hei hian i dam chhung a nghawng dawn lo. Enkawlna hian a natna, itchy blisters leh sores te chu a control thei a ni.
A tam zawkah chuan heng blisters te hian scarring a thlen tam lo hle . Amaherawhchu, hliam tuar emaw, hrual fo emaw a nih chuan hliam a lo awm thei a ni.
`(Pemphigus Foliaceus)` leh `(Pemphigus Vulgaris)` te hi eng nge an danglamna?
`(Pemphigus Foliaceus)` leh `(Pemphigus Vulgaris)` te hi dinhmun inzawm pahnih an ni. An pahnih hian an symptom hi a inang deuh a, pakhat leh pakhat anga ngaih sual theih a ni.
A danglamna ber chu Pemphigus Vulgaris hian i vun chauh ni lovin i hmui, i rilru leh i taksa peng hrang hranga mucous membrane te pawh a nghawng a ni . Chuvangin, Pemphigus Vulgaris vei te hian hmui natna avangin chaw nêm, rimtui lo tak tak an ei a ngai mai thei.
Mahse, `(Pemphigus Foliaceus)`-ah chuan heng membrane nalh tak takte hi a nghawng lo . Tin, a natna lan chhuah dan hi `(Pemphigus Vulgaris)` aiin a na lo zawk tlangpui bawk. Chuvangin `(Pemphigus Foliaceus)` vei te hian ei leh in lama khuahkhirh bik an mamawh lo.
Engtikah nge Doctor ka hmuh ang?
Heng symptoms te hi i neih chuan doctor pan ngei ang:
- Blisters emaw hliam emaw a dam loh chuan .
- Taksa hmun zau takah blisters a awm chuan.
- Hliam a lian (a hring) a nih chuan, tui sen emaw, var emaw a chhuah chuan, emaw, hliam chhehvelah yellow crust a lo awm a nih chuan (hengte hi natna kai chhinchhiahna a ni thei).
- Khawsik, khawsik, leh taksa ruh na ang chi symptoms i neih chuan .
Doctor zawh tur zawhna pawimawh
Doctor hmu tura i kal hunah heng zawhnate hi zawh theihnghilh suh:
- Eng enkawlna nge ka tan a tha ber?
- Enkawlna hian eng side effect nge a neih?
- Eng thil nge ka natna lan chhuah chhan?
- Hliam ah hian engzat nge hriak hnawih tur?
A tawp berah chuan take-home message:
`(Pemphigus Foliaceus)` hi vun natna a ni deuh ber a, mahse damdawi lam enkawlna leh thurawn dik tak nen chuan a control tha thei hle . Natna hrik kai theih a nih loh avangin ṭul lova lungngai suh. Heng symptoms te hi i neih chuan doctor pan nghal la, enkawl tan rawh. I vun enkawl la, doctor thupek ang chiah zawm rawh. Hliam chu hrual emaw, hrual emaw loh tur. A chhan chu i tih chuan i kai thei a, hliam i hnutchhiah thei bawk. Dam leh thuai turin duhsakna ka hlan e!
` Pemphigus Foliaceus, Pemphigus Foliaceus, Vun natna, Tui hring, Immune System, Autoimmune Disease, Vun Natna











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