I kawr, i rilru, i hnungzang, a nih loh leh i kut ah emaw, a sen, a châng chuan zungbun ang maia awm i nei em? An scaly, scaly, leh dry an ni em? Mi tam tak chuan he dinhmun hi an ngaihtuah hle. Vun natna tlanglawn tak mai nge a pawi zawk tih ngaihtuah hi thil pangngai tak a ni. Vawiin hian Subacute Cutaneous Lupus Erythematosus, a tawi zawngin SCLE , vun chauh tichhe thei lupus chi khat chungchang kan sawi dawn a ni. Hei hi i hriat chian hnu chuan he dinhmun hi i hmachhawn a awlsam tawh hle ang.
A awlsam zawngin SCLE chu eng nge ni?
Okay, hei hi a awlsam zawngin han sawi ila. SCLE hi natna chi hrang hrang lupus an tih zinga mi a ni a, vun a nghawng ber a ni. Lupus hi kan taksa invenna lama harsatna a awm avanga lo awm thin a ni. A tlangpuiin kan immune system hian natna thlentu hrik te chu a do thin. Mahse lupus ang dinhmunah chuan he system hian tihsualin kan cell hrisel tak takte chu a rawn bei tan ta a ni.
SCLE hi lupus chi khat a ni a, vun a nghawng a ni. Doctor-te chuan Cutaneous Lupus Erythematosus (CLE) an ti a. "Subacute" tih thumal hian vun biopsy-a hmuh theih inflammation chi khat a kawk a, chu chu vun te tak te lak a, enfiah a ni.
Pawimawh tak chu SCLE vei zinga a chanve vel chuan lupus natna tlanglawn zawk, Systemic Lupus Erythematosus, emaw SLE emaw an nei bawk. SLE hi vun chauh ni lovin, chhungril lam, kal, thinlung, leh thluak te pawh a nghawng thei a ni. Chuvangin SCLE symptoms i neih chuan doctor nena inbiakna neih a pawimawh.
He natna hian mi tin a nghawng dan hi a inang lo thei a, chuvangin hriat chian a harsa deuh thei a ni. A pawimawh ber chu i thusawi ngaithlatu leh i tana enkawlna dik zawngtu doctor zawn hi a ni.
SCLE chi hrang hrangte chu engte nge ni?
SCLE hi kawng lian pahnihin kan hmu thei a. Heng pahnih hi an hmel a danglam deuh hlek. Eng nge an nih i en ang u.
| SCLE type a ni | A lan dan leh a nihna |
|---|---|
| Annular SCLE a ni | Hetiang vun natna hian vunah hian a sen, a hring, a zungpui, a nih loh leh ring ang chi (plaques) a lo lang thin. Heng patch te hi ni chhuahna hmunah a lang tam ber. Heng patch te hi a dam hnuah chuan chutiang hmuna vun chu a hring deuh thei a ni. Doctor te chuan hei hi hypopigmentation an ti a . |
| Papulosquamous SCLE tih hi a ni | Hetiang vun vun rawng hi papules te tak te leh scaly appearance inzawmkhawm a ni. A hmasa berah chuan eczema emaw psoriasis emaw ang deuh a ni thei. Hetiang chi hi ni êngin a tizual ber bawk . |
SCLE natna lanchhuahna chu engte nge ni?
SCLE chhinchhiahna ber chu vun rawng a ni. Hengte hi i taksa peng ni chhuahna hmun, kawr, i rilru, hnungzang leh kutphah teah hmuh tur a tam ber.
He chhiatna hi hetiang hi a ni thei:
- A sen, ring ang maia awm, oval spot a awm. A chang chuan heng ring te hi an inzawm khawm thei a, pattern lian tak angin an lang thei bawk.
- Vun sen, hnim hring, vawt, hnim hring. Hei hi psoriasis ang deuh a ni fo.
A tha ber chu, heng hmunte hi a tlangpuiin an hrual lo va, hliam an hnutchhiah lo bawk . Mahse, vun rawng a danglam thei a, chu chu a hliam a dam hnuah pawh a awm thei.
SCLE lo awm chhan hi engte nge ni?
SCLE awm chhan pakhat chauh hriat chian a harsa hle. Thil buaithlak tak a ni. Zirchiangtute chuan thil engemaw zat inzawmkhawmin a thlen niin an ngai.
- Genetic factors: Hei hian genetic link a awm thei tihna a ni. I chhungkuaa mi tu emaw chuan lupus a vei a nih chuan i hlauhawm thei bawk.
- Environment factors: Chung zinga pawimawh ber chu ultraviolet radiation , ni êng a ni. Hei bakah hian zuk leh hmuam hman leh pesticides te pawhin nghawng a nei thei niin an ngai bawk.
- Damdawi thenkhat: SCLE vei hmun thuma ṭhena hmun khat vel chuan damdawi ṭhenkhat an ei hnuah he natna hi an nei ṭhin. Hei hi "Drug-induced SCLE" an ti a.
| Damdawi thenkhat SCLE thlen thei |
|---|
| Anti-fungal damdawi te |
| Anti-seizure damdawi thenkhat |
| Thisen sang damdawi thenkhat, entirnan ACE inhibitor |
| Chemotherapy damdawi te |
| Gastritis enkawlna atana hman damdawi thenkhat (Proton pump inhibitors - PPIs) . |
| Natna enkawlna atana hman damdawi thenkhat, ruh natna (tumor necrosis factor inhibitors) . |
Tute nge SCLE vei theihna chance sang zawk?
- Mipa aiin hmeichhiaah a tam zawk.
- Kum 40 leh 60 inkar ah a awm tam ber .
- Mihring var zingah a tam zawk nachungin, he natna hi chi hrang hrangah a awm thei a ni.
Natna hriatchhuah leh enkawl dan
Heng symptoms te hi i neih chuan doctor pan hmasak tur a ni. Dermatologist emaw, rheumatologist emaw hnenah refer i ni thei bawk.
Engtin nge natna hi kan hriat theih ang?
Doctor chuan i vun a enfiah ang a, i symptoms te a zawt ang che. Chumi hnuah chuan a hnuaia test te hi an ti thei ang a, an natna hmuhchhuah chu an nemnghet thei ang:
- Skin biopsy: Hei hian i vunah mole pakhat atanga vun sample tlemte tak tak anesthesia hmanga lak a, microscope hmanga enfiah a ni. Hei hian mole hi SCLE emaw vun natna dang emaw avanga lo awm a nih leh nih loh hriat theih nan a pui thei a ni.
- Thisen test: Thisen test eng emaw zat tih theih a ni.
- Thisen chhiar kim (CBC) 1.1.
- Sed rate (ESR) leh C-reactive protein (CRP) - Hengte hian taksaa inflammation awm leh awm loh a enfiah thin.
- Antinuclear antibody (ANA) test: Hei hi lupus hriat theihna atana test pawimawh tak a ni.
- Kidney leh Liver function test neih a ni
- Urinalysis tih a ni
SCLE hi engtin nge enkawl a nih?
SCLE enkawlna atana thil pawimawh ber leh number one chu ni laka invenna a ni , ni êng hi he natna tizualtu ber a nih avangin.
Tin, i doctor chuan i natna lan chhuah dan azirin topical cream emaw, oral medication emaw a rawt thei bawk.
| Enkawlna chi hrang hrang | Entirnan (damdawi lam damdawi pek chauh) . |
|---|---|
| Topical steroid hman thin a ni | Hydrocortisone, Triamcinolone, Clobetasol te a awm bawk |
| Skin cream dang (Topical calcineurin inhibitors) te pawh a awm bawk. | Tacrolimus, Pimecrolimus tih te hi a awm a |
| Malaria dotu ei theih a ni | Hydroxychloroquine, Chloroquine tih a ni |
| Immunosuppressive damdawi ei theih a ni | Methotrexate, Azathioprine hmanga siam a ni |
| Damdawi chi dang | Dapsone, Retinoids, Monoclonal antibodies (IVIG, Rituximab) te a awm a, a chhuahna tur hmun leh a hmanna tur hmun chu a inthlau hle. |
Vaukhânna: Damdawi lam thurawn tel lo chuan heng damdawi te hi hman loh tur a ni. I doctor chauhvin i tana enkawlna tha ber a ruat thei ang.
SCLE nen hian engtin nge kan awm ang?
SCLE hi dam chhung (chronic) natna a ni. Chumi awmzia chu a chang chuan symptoms a pung thei a, a chang chuan a tlahniam thei tihna a ni. Mahse, a thunun tha thei a, nun pangngaiin i nung thei bawk.
Ni laka invenna hi number 1 a ni!
Hei hi i tih theih pawimawh ber a ni.
- Nitin ni chhuahna hmuna i chhuah dawnin SPF 50 aia sang nei broad-spectrum sunscreen hmang thin ang che . Hei hi thil tih ngei ngei tur a ni, ni chhum zingah pawh.
- Zing dar 10 leh tlai dar 4 inkarah ni chak tak chu pumpelh tur a ni.
- Ni chhuahna hmuna i chhuah dawnin ni laka invenna thawmhnaw, lukhum zau tak leh kawrfual kawr sei tak te ha la.
- Tanning bed hman hi bansan vek rawh.
Mahni in enkawl that pawh hi a damdawi a ni!
- Natna hrethiam rawh: He natna chungchang hi rintlak a\angin chhiar la, inzirtir rawh. Hei hian i taksaa thil thlengte chu a hrethiam zawk ang.
- I rintlak doctor zawng rawh: Doctor i hmuh fo a ngai mai thei a, chuvangin i thusawi ngaithlatu leh hrethiamtu doctor hnenah enkawlna zawng chhunzawm zel ang che.
- Support system siam rawh: Chutiang dinhmuna dingte nena inbiakna leh i thil tawn te sawi chhuah hian rilru chakna nasa tak a pe ang che.
- Mahni in enkawl rawh: Ei leh in hrisel ei la, exercise la, mut tha la, stress control rawh. Heng thilte hian natna enkawlna kawngah nasa takin a pui ang che.
SCLE i neih avangin ni laka invenna nasa tak i mamawh avangin vitamin D tlakchhamna i nei thei a ni . Hemi chungchang hi doctor nen inbia la, a tul chuan vitamin D supplement ei thin ang che.
Take-Home Thuchah a ni
- SCLE hi nun chhung zawnga natna a ni a, lupus natna vei hian vun a nghawng a ni.
- A lan chhuah dan ber chu ni chhuahna hmuna vunah sen, ring ang chi, a nih loh leh scaly patches lo lang hi a ni.
- He natna dona kawngah hian ni laka invenna hi a pawimawh ber leh number 1 a ni.
- Heng hmunte hian a tlangpuiin a ti na lo va, hliam a siam lo va, mahse vun rawng a thlak danglam thei a ni.
- Heng symptoms te hi i neih chuan hlauthawng suh la, a rang thei ang bera doctor pan rawh. Enkawlna leh enkawl dan dik tak nen chuan nun pangngai i hmang thei ang.











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