I fa hian hetiang fit mak tak hi a nei em? Rasmussen-a Encephalitis chungchang hi i zir dawn teh ang!

Natna mak tak, thluak kil khat chauh a nghawng a, hun kal zelah a zual zel tih i hre ngai em? I fa te hian fit fo a nei a, taksa sir khatah chak lohna a nei a, tawng harsa a nei pawh a ni mai thei? Chutiang thil i hriat chuan hlauthawng chu hriatthiam theih a ni. Vawiin hian dinhmun hmuh tur awm lo mahse pawimawh tak kan sawi dawn a ni. Rasmussen-a Encephalitis tih a ni.

Rasmussen-a Encephalitis hi eng nge ni?

A awlsam zawngin, Rasmussen-a Encephalitis hi kan thluak hemisphere pahnih zinga pakhat, chu chu thluak sir khatah, a lo zual zel a, hun rei tak chhunga lo awm thei a ni . A dik tak chuan thluak cell te chu a hring a, a sen vek bawk. Hei hi Rasmussen syndrome an ti bawk.

Hetianga thluak sir khat a inflamed hian fits a siam fo thin. Damdawi lam hawi chuan hei hi epilepsy kan ti bawk. Hei hi fit mai a ni lo va, thluak a tichhe deuh deuh a, chu chhiatna chu siamthat a harsa hle. Hun a kal zel a, thluak lam chhia nen khaikhin chuan taksa sir khat hnathawh a tlahniam a. Ngaihtuah teh, hei hian thluak dinglam a nghawng a, chutah chuan taksa veilam chuan chakna a hloh thei a, tawng a harsat a, hriatrengna a hloh thei bawk.

He natna hi doctor pakhat Theodore Rasmussen-a chuan kum 1958 khan a hmuchhuak a, chuvangin, a chawimawina atan Rasmussen encephalitis tiin an vuah a ni.

Hetiang dinhmun hi engtiang chiahin nge a tlem?

Hei hi a takah chuan natna hmuh tur awm lo tak a ni . Zirchiangtute sawi dan chuan mi sang sawm zinga pahnih chauhvin he natna hi an vei a rinawm. Chu chu a tlem hle tihna a ni.

He natna hian naupang kum 2 leh 10 inkar a vei tam ber a, mahse, a chang chuan tleirawl leh puitling pawhin he natna hi an nei thei bawk.

Rasmussen’s Encephalitis natna lan chhuahna chu engte nge ni?

He natna chhinchhiahna hmasa ber chu fit a ni fo. He fit hi chi hrang hrang a awm thei.

A lan chhuah hmasak ber

• A severe, generalized tonic-clonic seizure: Hei hian taksa sir lehlamah taksa ruhte chu nasa takin a inzawm khawm a, hriatna hloh a awm thei bawk.
• Focal aware seizure: Hetiang a nih chuan thil thleng chu i hre chiang hle. I kut emaw ke emaw pakhatah tingling i nei thei a, hmun khatah i rilru a buai thei bawk.
• Focal impaired awareness seizure: Hei hi thluak sir khat atanga intan a, hriatna hloh tlem emaw, hriatna hloh vek emaw pawh a ni.

A pawimawh ber chu, nangmah emaw, i fa emaw hian hetiang fit hi i nei a nih chuan, .Doctor pan vat a ngai a ni. Chu chu i tih ngei ngei tur thil a ni.

Thil dang pakhat chu naupang kut emaw ke emaw a chak lo deuh pawh hi he natna chhinchhiahna hmasa ber a ni thei bawk.

Hun kal zelah symptoms lo lang thin

A tir lama seizures te hi zawi zawiin a pung chho zel a. Rasmussen encephalitis vei zinga a chanve vel chuan `(Epilepsia Partialis Continua - EPC)` tih natna an nei a. Chumi awmzia chu second engemaw zat emaw minute engemaw zat emaw chhung chu seizures hi a chhunzawm zel tihna a ni. Heng seizures te hi damdawi pangngai (intractable) hmanga control a harsa hle.

A hnuaia symptoms te hi fit hmasa ber atanga thla engemaw zat chhung emaw, kum khat emaw kum hnih emaw chhung pawhin a lang tan thin:

• Rilru chakna a tlahniam zauh zauh : Hei hian ngaihtuahna, hriatthiamna, leh hriatrengna ang chi thilte chu a tlahniam thei tihna a ni.
• Taksa sir khata chetna hloh zauh zauh (hemiparesis): Entirnan, kut dinglam leh ke dinglam chu a bengchheng thei. Hun a kal zel a, hei hi paralysis (hemiplegia) famkim thlengin a kal thei.
• Aphasia : Hei hi natnain thluak thu sawina mawhphurtu lam (a tlangpuiin veilam lam) a nghawng hian a awm thin.
• Mit sir khata mit hmuhna hloh vek (hemianopsia): Mit sir khata mit hmuhna hloh ang mai a ni.

Mi tam zawk tan chuan Rasmussen encephalitis a lo chhuah hnu thla 8 atanga thla 12 hmasa ber hi a na ber a ni . Chumi hnuah chuan natna chu a reh emaw, a reh emaw pawh a ni thei. Mahse, thluak chhiatna chu a awm reng a, tihdanglam theih a ni lo.

Hei hi eng nge a chhan?

Dik tak chuan scientist-te chuan Rasmussen encephalitis thlentu hi eng nge ni tih chiang takin an la hre lo . Mahse theory lian tak pahnih an nei a:

1. Autoimmune disease : Hei hi kan immune system, natna laka min vengtu system-in kan cell tha tak takte a rawn beih sual hian a ni. Chuvangin, Rasmussen encephalitis hi chutiang bawka autoimmune natna, thluak sir khat chauh beitu niin an ngai.

2. Infection : Hriat chian loh virus thluaka lut a, he natna hi a thlen thei a ni. Amaherawhchu, zirchiangtute chuan he natna vei tawhte thluak an enfiah a, mahse virus bik an la hmuchhuak lo.

He natna hi engtin nge an hriat chhuah? (Diagnosis) tih a ni.

Doctor-te chuan Rasmussen encephalitis hi i fa natna lan chhuah dan leh special test engemaw zat result a zirin an hmuchhuak thin.

• MRI scan (Magnetic Resonance Imaging - MRI): Hei hian naupang thluak sir khata thluak tissue chu a atrophied emaw shrunk emaw a nih leh nih loh a entir thei. Thla engemaw zat emaw, kum engemaw zat emaw chhunga thluak sir khat chu a lo tlahniam zauh zauh a nih chuan natna chhinchhiahna lian tak a ni.
• EEG test a niElectroencephalography (EEG): Hei hian natna hriatchhuahna kawngah pawh a pui thei bawk. EEG test hian thluaka electrical activity a record a. Hei hian seizure hi engtin nge a awm tih leh thluak a thawk dik lo em tih hriat theih nan a pui thei a ni.

Chuvangin, doctor-te chuan Rasmussen encephalitis natna lan chhuahna leh scan-a thil hmuhchhuah, thluak sir khata atrophy ang chi te chu an inzawm khawm a, an nemnghet a ni.

Rasmussen’s Encephalitis hi eng enkawlna nge ni?

Vanduaithlak takin Rasmussen encephalitis hi damdawi a la awm lo a , chuvangin enkawlna tum ber chu symptoms control leh thluaka inflammation tihziaawm a ni.

Enkawlna atan a hnuaia mite hi tih theih a ni:

Antiseizure damdawi hman tur

Heng damdawi te hian Rasmussen encephalitis vanga seizures awmte chu a titawp vek lo mai thei. Mahse, seizure awm tam leh nasat lutuk tihtlem nan an pui thei a ni .

Immunotherapy hmanga enkawl a ni

Immunotherapy-ah hian immune system hnathawh tidanglam thei damdawi pek a ni a, natna hi a tir lamah chuan a attack te chu a control thei a, immune system atanga thluak chhiatna a tihziaawm thei bawk.

Thluak surgery neih a ni

Rasmussen encephalitis natna a fit control dan tha ber chu thluak surgery hi a ni . Hei hi hemispherectomy an ti a. He surgery-ah hian naupang thluak (hemisphere) natna vei chu then hran a ni a, chu chu chu thluak lam chu a sir lehlamah then hran emaw, paih vek emaw a ni.

A tam zawkah chuan naupang he surgery nei te hian an thluak natna vei lamah hian hnathawhna nasa tak an hloh tawh a ni. Chuvangin, operation hnua hnathawh hloh belh theihna a tlem hle. Doctor te chuan surgery hi a hlawknain a hlauhawmna a tluk phah chauhvin an ngaihtuah thin .

He natna hmalam hun hi eng nge ni ang? (Prognosis) tih a ni.

Rasmussen encephalitis vei tur prognosis hi mi hrang hrangah a inang lo thei . Mi thenkhat tan chuan operation hnuah natna hi a darh tawh lo thei a, seizure awm tam dan pawh a stabilise thei bawk.

Mahse, mi tam tak chu eng emaw chen chu paralysis, finna leh hriatrengna hloh, leh thusawi harsatna neiin an awm thei a ni. A tlem hle a, he natna hi thluak hmun dangah a darh thei a ni.

Rasmussen-a Encephalitis hi a veng thei ang em?

Rasmussen encephalitis hi natna hmuh tur awm lo tak a nih avangin leh a chhan dik tak hriat a la nih loh avangin a venna tur engmah kan ti thei lo

A chhan chu thil awm lo tak a nih avangin scientist tan chuan zirchian a harsa hle. Mahse thu lawmawm tak chu seizures leh symptom dangte control thei tur enkawlna a awm tih hi a ni. I fain a tel theihna tur clinical trial pawh a awm thei a, hetiang diagnosis i dawn hian i rilru a hah lutuk hi thil pangngai a ni. Mahse, i fate damdawi lam team chu kawng engkimah nang leh i fate ṭanpui tûrin an awm tih hre reng ang che .

I hre reng ang u (Take-Home Message) .

Rasmussen’s Encephalitis hi thluak natna a awm lo hle a, mahse thluak natna na tak a ni thei.

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* Hetiang a nih chuan thluak sir khatah inflammation a awm a, chu chuan fit fo thin, taksa sir khatah paralysis, tawng harsa a ti thin.

* Naupang tê tête chu a tuar nasa ber.

* Symptom i hmuh chuan Doctor pan nghal tur a ni.

* Enkawlna hian symptoms a control thei.

* Hetiang hunah hian nangmah chauh i ni lo va, doctor leh i hnaih berte hnen atangin tanpuina zawng rawh.

He thu hi in tan a tangkai ngei ka beisei. Zawhna i neih chuan Doctor biak hreh suh.

` Rasmussen encephalitis, thluak natna, epilepsy, fit, naupang enkawl, thluak natna, thluak lam natna