Doctor pawhin Sapropterin pills a pe che em? Hemi chungchang hi chipchiar takin sawi ila!

Chibai! Vawiin hian ruihhlo pakhat, tlem a danglam deuh, mahse mi thenkhat tan chuan an nun atan a pawimawh em em mai kan sawi dawn a ni. Chu chu Sapropterin a ni. Nangmah emaw, i hriat emaw, i fa ngei pawhin natna hlauhawm tak `Phenylketonuria` tih, a tawi zawnga `(PKU)` tia hriat bawk i neih chuan he damdawi hi i hre tawh ngei ang. Chuvangin, he damdawi hi eng nge a nih tak tak te, kan taksa a tanpui dan te, a hman hunah eng thil nge a bik takin kan fimkhur tur tih te i lo en ang u.

A hmasain, Phenylketonuria (PKU) hi eng nge ni?

A awlsam zawngin sawi ila, `Phenylketonuria` hi genetic condition, rochun atanga lo chhuak a ni. Hetiang natna vei hian amino acid `Phenylalanine` an tih chu uluk takin a ti chhe thei lo va, a process thei lo bawk. I ngaihtuah mai thei, `Phenylalanine` chu eng nge ni? Kan ei thin protein tam takah a awm a, entirnan, bawnghnute, sa, sangha, artui, leh nut.

Chuvangin, `PKU` vei miah chuan he `phenylalanine` (Phenylalanine) hi taksaah a pungkhawm tan thin. Bawlhhlawh tlem a lo awm khawm ang mai a ni. He accumulation hi a tha lo hle a, a bik takin thluak tan chuan a tha lo hle. Hei hi naupan lai atanga control a nih loh chuan thluak thanlenna a tikhawlo thei a, rilru lama hmasawnna lama harsatna, nungchang inthlak danglamna, leh epilepsy thlengin a awm thei bawk. Chuvangin `PKU` vei te hian `phenylalanine` (Phenylalanine) tlem zawk ei leh in bik an zawm a ngai a ni.

Chuti a nih chuan engtin nge Sapropterin hian he thil hi a puih?

Hetah hian damdawi `Sapropterin` (Sapropterin)` a lo lut a, `PKU` damdawi a ni lo a, mahse `PKU` vei thenkhat (a zawng zawng ni lo) taksaa `Phenylalanine` (Phenylalanine) level tihhniam nan a pui a ni. Chu chu, he damdawi hian taksain `Phenylalanine` (Phenylalanine)` (Phenylalanine) chu tlemin a ti chhe thei zawk tihna a ni. Mahse chu special diet nen chuan hman dun tur a ni. He damdawi hi i tan emaw, i fa emaw tan a tha em tih te, engzat nge pek tur tih te chu doctor in a rel ang.

He damdawi hi brand hming ``JAVYGTOR`` emaw ``KUVAN`` emaw hmangin a awm thei.

He damdawi hi ka ei tan hmaa doctor hnena ka hrilh tur te chu engte nge ni?

Nangmah emaw, he damdawi eitu emaw hian a hnuaia thil awmte hi i neih chuan damdawi i ei tan hmain i doctor hnenah i hrilh hmasa phawt tur a ni. Hengte hi thup loh a tha ber, a chhan chu mahni hriselna a nghawng thei a ni.

• Ei leh in lama harsatna danglam tak i nei em? Entirnan, anorexia emaw bulimia emaw.
• Khawsik i nei em? A nih loh leh natna chi khat i nei em?
• Kal natna i nei em?
• Liver natna i nei em?
• Seizures, epilepsy ang chi i nei tawh em?
• Sapropterin, damdawi dang, ei tur, dye, a nih loh leh preservatives te hi i allergy em?
• Naupai i ni em? A nih loh leh naupai i beisei em?
• Nu hnute pe thin i ni em?

Heng zawng zawng hi doctor nen zalen taka sawiho a pawimawh hle.

Okay, chuti a nih chuan engtin nge he damdawi hi ka hman ang?

Hei pawh hi i hriat chian a ngai a ni. Doctor-in a sawi ang chiah kha i zawm a ngai a ni.

• Heng pills te hi chaw ei rualin ei tur a ni .
• I doctor-in damdawi a pek che kha, a damdawi ziah label-a a ziah ang chiah khan, a zat tur angin, a hun ruat angin ei rawh.
• Tablet hi tui nen a pumin ei theih a ni a, a nih loh leh tui ounces 4 atanga 8 (milliliter 120 atanga 240 vel) emaw apple tui emaw-ah a hmin thei bawk.
• A pawimawh ber: A hmin atanga minute 15 chhungin i in tur a ni. Chu aia rei chu dah bo suh.
• Tablet te hi a hmin vat duh chuan i chil chhak thei a, a hmin laiin spoon hmangin i hrual tha thei bawk.
• A châng chuan, pill-te chu a hmin vek lovin tuiah chuan a tê tête a lo inhnim pil tih i hmu thei bawk. Hei hi thil pangngai a ni. Damdawi ei zawh hnua glass chhunga thil te te a la awm chuan tui emaw apple tui emaw tlem tal dah belh la, hrual la, chu pawh chu in rawh. Chutiang chuan damdawi dose kimchang chu i hmu ang.
• Thil dang chu tablet te chu hrual a, ei tur tlemte, applesauce emaw pudding emaw nen chawhpawlh a ni.
• Nitin hun khata, nitin hun khata i damdawi ei hi a pawimawh hle. I doctor-in a tih aia tam ei suh , a nih loh leh i damdawi chu zawt lovin ei kha bansan rawh.

Naupang tê tête hnêna pêk a nih chuan a bîk hle:

He damdawi hi i fa te hnenah i pe dawn a nih chuan i pediatrician hnenah i sawipui ngei tur a ni. He damdawi hi nausen thla khat mi lek te chu thil bik thenkhatah pek theih ni mahse, fimkhur tur thil engemaw zat a awm. Chuvangin Doctor-in a sawi ang chiah chu zawm rawh.

Damdawi i ei tam lutuk chuan engtin nge i tih ang?

Chutiang a nih chuan, chu chu i ngaihtuah aia tam damdawi i ei tawh nia i hriat chuan, i hnai ber poison control center emaw, damdawi in emergency room emaw chu call nghal rawh. Hun khawhral suh.

Hriat tur pawimawh: He damdawi hi nangmah tan chauh a ni. I damdawi chu midang hnenah pe suh, nangmah ang bawka natna lanchhuahna nei pawh nise.

Damdawi dose khat ka ei loh chuan engtin nge ni ang?

Chutiang a nih chuan i hriatreng veleh missed dose kha ei nghal rawh. Mahse, i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Vawi khatah vawi hnih ei ngai suh.

He damdawi nena inzawm thei damdawi dang a awm em?

Ni e, a awm mai thei. Sapropterin nena inzawm thei damdawi engemaw zat a awm. Entir nan:

• Avanafil `(avanafil)` tih a ni
• Levodopa `(levodopa)` tih a ni
• Methotrexate hmanga siam a ni
• Pemetrexed a ni
• Pyrimethamine a ni
• Sildenafil `(sildenafil)` tih a ni
• Tadalafil `(tadalafil)` tih a ni
• Vardenafil `(vardenafil)` tih a ni

He list hi a kim lo. Chuvangin, i damdawi ei zawng zawng (prescribed emaw over-the-counter emaw), herbs, vitamins, leh dietary supplement i hman zawng zawngte chu i doctor hnenah hrilh rawh. Tin, zu i in emaw, zu i in emaw, ruihhlo i hman emaw chuan i doctor hnenah hrilh bawk ang che. Thil thenkhat chu he damdawi nen hian a inzawm thei a ni.

He damdawi hi ka ei dawnin eng nge ka fimkhur bik ang?

Hei pawh hi a pawimawh hle.

• I doctor chuan i dinhmun a enfiah reng ang. Chuvangin, ni ruat saah clinic-a kal a, i thisen test tihsak chu hloh suh . A bik takin phenylalanine level i enfiah fo tur a ni.
• He damdawi hian taksaah nghawng a neih theih nan kar 4 vel a la ngai thei. Chuvangin lungngai suh.
• I natna lan chhuah dan a tha lo a nih chuan, emaw, a na zual ang tih a hriat chuan doctor hnenah hrilh rawh.
• Pawimawh tak: He damdawi i ei lai hian ei leh in bik i zawm a ngai dawn a ni. Hei hian phenylalanine tlemna ei tur ei tihna a ni. I doctor emaw nutritionist emaw chuan chipchiar takin a hrilhfiah ang che. Doctor thurawn tel lo chuan i ei leh in hi thlak ngai suh.

He damdawi hian eng side effect nge a neih theih?

Damdawi zawng zawng ang bawkin he damdawi hian side effect tenau te a nei thei bawk. Ṭhenkhat chu an serious a, ṭhenkhat erawh chu chutiang chuan an serious lo.

Heng thilte hi a lo thleng a nih chuan Doctor hnenah i hrilh nghal a ngai!

• Allergic reaction a nih chuan: Vun natna, vun hring, hives, hmai, hmui leh lei hring tihna a ni.
• I ek chu a dum emaw, thisen emaw a nih chuan, emaw, thisen i chhuah chuan.
• Thâwk harsa.
• I luak chhuak, i lu a hah, i tlu dawn ang maia i hriat chuan.
• Symptoms te chu fidgeting, restlessness, thusawi tam lutuk, leh tlan kual vel (hyperactivity) te hi a ni. (Hei hi naupang tê tê tan chuan a dik hle)
• Pum natna nasa tak i neih chuan.

Hengte hi a hlauhawm lo tlangpui a, mahse a awm reng chuan doctor hnenah hrilh rawh :

• Khuh
• Thluak hring (diarrhea) .
• Lu na
• Nausea, luak chhuak
• Hrawk thip
• Hnar luang, hnar khar

He list-ah hian side effect zawng zawng a tel lo. Thil danglam bik i hriat chuan doctor zawt rawh. Side effects te chu FDA (Food and Drug Administration) hnenah 1-800-FDA-1088 ah i report thei bawk.

Engtin nge i damdawi i dahkhawm ang?

• Naupangte hmuh theih lohna hmunah dah rawh . Hei hi a pawimawh hle.
• Room temperature (20 leh 25 degree Celsius / 68 leh 77 degree Fahrenheit inkar) ah dah tur a ni.
• Damdawi chu a luhna original container-ah dah la, bottle chu khar nghet takin khar rawh.
• Damdawi expired hman loh tur. Anni chu paih bo rawh.

A tawp berah chuan hriat nawn tirna tlem

Hei hi damdawi `Sapropterin` chungchanga kan sawi tawhte khaikhawmna mai a ni. He damdawi chungchanga zawhna dang i neih chuan i doctor, pharmacist, emaw healthcare provider dang emaw zawt la. Engmah hlau suh la, i rilruah dah reng bawk ang che.

Thil pawimawh hriat reng tur (Take-Home Message) .

Okay, chuti a nih chuan, kan sawi tawh atang khan i ngaihtuah reng tur point te kha kan hriat nawn tir leh ang che em?

• Sapropterin hi damdawi a ni a, phenylketonuria (PKU) vei thenkhatah phenylalanine level control nan a pui a ni.
• Hei hi damdawi a ni lo va , special diet nen chauh hman tur a ni .
• Damdawi ei hmain doctor hnenah i hriselna dinhmun zawng zawng leh damdawi i ei zawng zawngte hrilh hmasa phawt ang che.
• Damdawi i dilute a nih chuan minute 15 chhungin in tur a ni.
• Test dik tak a hun takah tih a pawimawh hle.
• Side effect danglam tak i neih chuan doctor hnenah hrilh nghal rawh.
• Doctor thurawn lo chuan i ei leh in thlak danglam suh.

Nangmah emaw, i fa emaw hian he damdawi hi i lo pe tawh a nih chuan doctor-in a hrilh ang chiah chein zawm rawh. Chumi hnuah chauh chuan he damdawi hi i hlawkpui thei ang a, i `PKU` dinhmun chu i control tha thei ang a, nun hrisel tak i hmang thei ang. Ka duhsakna ka hlan a che u!

` Sapropterin, Phenylketonuria, Phenylketonuria, PKU, Phenylalanine, Phenylalanine, Damdawi, Damdawi, Side Effects te