Doctor-in i fate hian thinlung natna "Shone's Complex" tih a nei tih a hrilh che chuan i mangang a, i hlau a, i buai thei bawk . A tam hle mai. He hming hi i la hre ngai lo mai thei. "He natna hi eng nge ni? Ka naute hi engtin nge a awm ang?" I rilruah zawhna tam tak i nei mai thei. Lungngai suh. Hemi chungchang hi awlsam tak leh chiang takin sawi ila. Shone-a Complex hi eng nge ni? Naute chungah eng nge a tih tih chiang takin i hrethiam ang u.
A awlsam zawngin, he Shone’s Complex hi eng nge ni?
Shone's Complex hi pianpui thinlung natna a ni a . Hemi a thil thleng chu kan naute thinlung veilam sir thisen kalna kawngah hmun khat aia tam ah inkharkhip a awm a ni. Ngaihtuah teh, kan thinlung veilam hi chu lung atanga oxygen tamna, thianghlim thisen la chhuakin taksa pum puiah a pump chhuak thin. Tui motor ang maiin. Tunah chuan he thisen kalna kawngah hian blockage emaw lesion emaw a awm chuan eng nge thleng ang? Thinlung tan thisen lak a harsa a, taksaa thisen pump chhuah a harsa thin. Chu chu Shone-a Complex-ah pawh a thleng thin.
Hetiang dinhmun hi Shone’s Complex an ti a, a sawi hmasak ber doctor hming chawiin. Chumi nena inzawm thinlung lama harsatna pali hmuchhuak mah se, tunah chuan doctor-te chuan chhiatna eng emaw zat dang a awm tih an hmuchhuak ta a ni.
Shone’s Complex nen hian eng thinlung chhiatna nge inzawm theih?
Shone’s Complex vei nia hriat theih nan naute hian a hnuaia kan sawi tur thinlung lama harsatna pariat zinga pahnih tal a neih a ngai a ni. Eng nge an nih i en ang u. Thumal thenkhat chu a buaithlak deuhin a lang thei a, mahse awlsam takin ka sawifiah ang.
| Lung lam chhiatna | A awlsam zawngin, hei hi eng nge thleng? |
|---|---|
| Cor triatriatum a ni | Heart (left atrium) chunglam veilam chamber chhungah hian extra membrane a lo awm a. Hei hian chamber chu hmun hnih ah a then a, chu chuan lower chamber (left ventricle) ah thisen a luang lut thei lo. |
| Supravalvular mitral ring a ni | Thinlung chhunga mitral valve chungah chiah hian fibrous tissue ring a lo piang chhuak a. Hei hian valve inhawnna kawngkhar chu a ti tawi a, thisen kal dan a tikhawtlai a ni. |
| Parachute mitral valve hmanga siam a ni | A tlangpuiin mitral valve hawn leh khar tura puitu ruh pahnih (papillary muscles) a awm a. He tlin lohnaah hian pakhat chauh a awm. Parachute hrui zawng zawng hmun khata dah khawm vek ang mai a ni. Hei hian valve a ti tawi thei a, thisen chu hnunglam hawiin a leak thei bawk. |
| Hypoplastic veilam ventricle a awm a | "Hypoplastic" tih hian hmasawnna mumal lo tihna a ni. Hetah hian thinlung pumping chamber lian ber left ventricle chu a lo thang tha lo hle. A te a ni. Chuvangin thisen a pump tha thei lo. |
| Subaortic stenosis a awm thin | Extra tissue chu aortic valve hnuaiah a lo awm a, chu chuan thisen chu aorta chhungah a pump lut a, chu chuan a hmun chu a ti tawi hle. Hetianga a zim hian thinlung hian thisen pump a ti harsa zawk a ni. |
| Bicuspid aortic valve chu a awm a | A tlangpuiin aortic valve hian flap pathum a nei thin. Mahse he chhiatna nei naute hian pahnih chauh an nei. Hei hian valve a ti tawi thei a, thisen a leak thei bawk. |
| Aortic valve annulus te tak te a awm | Aortic valve bul vel a ring (annulus) chak tak chu a tlangpui aia te a lo ni ta a, chuvang chuan valve kaltlangin aorta chhunga thisen kal thei zat chu a tlahniam ta a ni. |
| Aorta (aorta) a inzawm khawm (coarctation). | Taksa lama thisen phurtu thisen kalna kawng lian ber aorta-a a zim chuan thinlung chu a tawi zawnga thisen pump chhuah tumin nasa zawkin a thawk a ni. |
A pawimawh ber chu heng defect pariat zinga pahnih emaw a aia tam emaw a awm chuan doctor-te’n Shone’s Complex an tih chu a ni. A tam zawkah chuan luhna kawngah daltu pakhat a awm a, chhuahna kawngah pawh daltu pakhat a awm bawk.
Ka naute hian hetiang natna hi a neih chuan eng symptoms nge a neih?
Hetiang natna vei naute ṭhenkhat chu a nasat chuan an pian hnu lawkah an lan chhuah ṭan nghal mai ṭhin . Hei hi a chhan chu naute thinlung hian taksaah thisen a pump tling thei lo a ni. Mahse, a châng chuan, naupan lai emaw, tleirawl lai emaw pawhin a lan chhuah theih a ni.
I fate zingah hian heng chhinchhiahnate hi zawng rawh:
- Thau tihpun harsatna: Thau tihpun dan mumal lo.
- Bawnghnute in laia chau tih hriat: Bawnghnute tlem i in zawh chuan i thawk hah tan a, thawk harsa i ti thin.
- Zun chhuah tlem: A tlangpui aia zun chhuah tlem.
- Weak pulse: Pulse hi a chak lo hle a, a bik takin kut leh keah a chak lo hle.
- Kut leh ke inkara thisen sang inthlauhna: Ke aiin kut ah thisen sang a sang zawk.
- Thisenah lactic acid a awm khawm.
I fain heng symptoms pakhat emaw, a aia tam emaw a neih chuan a rang thei ang bera doctor nena inbiakna neih a pawimawh hle.
Engvangin nge ka naute chungah hetiang hian a lo awm? Hei hi eng nge a chhan?
Tunah chuan, "Engvangin nge ka naute chungah hetiang hi a lo thlen? Ka sualna a ni em?" Dik tak chuan doctor-te chuan hei hi a chhan chiang tak an la hmu lo . A tam zawkah chuan a awm fo thin. Genetic nge environmental factor tih chiang taka sawi tur chuan information kan la nei tlem hle.
Zirchianna thenkhat chuan thlahtute atanga lo chhuak a ni thei tih sawi mah se, chhungkaw chhunga a darh dan chu a buaithlak hle. Chuvangin hei hi a taka hriatthiam theih nan zirchianna tam zawk neih a ngai a ni.
Chuvangin khawngaihin hre reng ang che, hei hi i sualna a ni lo. Heng thilte hi kan thunun thei lo.
Hetiang dinhmun avanga harsatna awm thei te chu engte nge ni?
Shone’s Complex hian harsatna engemaw zat a thlen thei a, chuvang chuan enkawl vat leh hun rei tak enkawl a pawimawh hle.
- Pulmonary hypertension: Pulmonary hypertension: Lung lama thisen phurtu thisen kalna kawng hrang hranga thisen sang a san dan pangngai lo.
- Heart rhythm pangngai lo: Lung rhythm mumal lo.
- Heart failure: Thinlung hian taksaah thisen a pump tam thei lo tihna a ni.
Doctor-te hian engtin nge hei hi an hmuh?
Doctor-te chuan he natna hi hriat chian nan test eng emaw zat an hmang a.
- Fetal echocardiogram: Hei hi naute chu a pum chhunga a la awm laiin scan bik a ni. Naute pian hmain thinlung lama harsatna a hriat theih.
- Transthoracic echocardiogram (TTE): Naute pian hnua thinlung ultrasound scan tih a ni. He test hi Shone’s Complex hmuhchhuah nan hman a ni ber.
- Cardiac CT scan emaw MRI: Hengte hi mi zawng zawng tan tih a ni tlangpui lo a, mahse a then phei chuan heng test te hian thinlung insiam dan chungchang thuk zawka hriat theih nan a pui thei a ni.
A tam zawkah chuan natna hi pian hma emaw, pian hnu emawa hriat chhuah a ni. Mahse, a châng chuan natna hi naupan lai emaw, tleirawl lai emawa hriat hmasak ber a ni a, chutih lai chuan a lan chhuah dan chu a na lo va, chutiang chuan a na lo hle. Chutiang hunah chuan doctor chuan thinlung lam ngaihthlak laiin aw pangngai lo (thinlung murmur) a hriat avangin test dang neih belh turin a refer thei a ni.
Hei hi eng enkawlna nge ni?
Shone’s Complex enkawl dan awmchhun chu surgery a ni . Tunah hian he natna tidam thei damdawi a la awm lo. Mahse, doctor chuan naute natna lan chhuah dan thunun nan leh zai a nih hma loh chuan thinlung hnathawhna pui turin damdawi a pe thei a ni.
Hemi atan hian surgery bik a awm lo. Chu ai chuan doctor-te chuan i fain thinlung lama harsatna a neih leh a thinlung a thawh that dan a zirin eng surgery nge mamawh tih an rel ang.
I fa hian a hnuaia operation pakhat emaw, a aia tam emaw a mamawh mai thei:
- Mitral valve chhehvela extra tissue ring awm chu lakchhuah a ni.
- Mitral valve siamthat a ni.
- Mitral valve thlak (hei hi a tlem deuh).
- Aortic valve hnuaia tissue tam lutuk lakchhuah.
- Aortic valve hawnna zau zawk siam.
- Aorta hmun zau tak siamthat.
Surgery tih dan tur
A châng chuan doctor te chuan staged approach hmangin an ti thin . Chu chu vawi khatah surgery an ti vek lo tihna a ni. Hmun hnihah an ti a, hun bituk inthen a ni. Entirnan, zai hmasak ber hian thinlung atanga thisen chhuah dan a blockage chu a paih chhuak thin. Tichuan, operation vawi hnihnaah chuan thinlung chhunga thisen kal dan a blockage chu a paih chhuak leh ta a ni. I doctor chuan i fain operation engzat nge a mamawh dawn tih leh engtikah nge tih a tha ber tih chiang takin a hrilhfiah ang che.
Naupang hmalam hun tur leh a hmalam hun tur chu eng nge ni?
Naupang hmalam hun nun leh hriselna chu thil engemaw zatah a innghat a ni:
- Natna nasat dan: Lung chhiatna hi engtiang chiahin nge a nasat.
- Enkawlna hman chak dan: Enkawlna a tan thuai dan.
- Harsatna: Harsatna dang a awm leh awm loh.
- Harsatna lo awm leh zel: Tun hmaa lung lam chhiatna enkawl tawhte chu hun kal zelah a lo lang leh dawn em?
Entirnan, aorta coarctation ang chi thil hi hun kal zelah a lo lang leh thei a ni. Chuvangin, i fa a lo upat deuh deuh chuan operation tam zawk neih a ngai mai thei. I fa dinhmun a zirin hemi chungchang hi i doctor chuan a pe ang che.
Zirna tam takah chuan operation hnua dam rei zawng chu 75% aia tam a ni a, kum 20 thleng a ni . Chumi awmzia chu naute pali zinga pathum chu enkawl hnuah nun tha leh hrisel takin an khawsa tihna a ni.
I fate natna hmuhchhuah chungchang i hriat hnuah i rilruah zawhna sangkhat i nei thei a ni. Chu chu thil pangngai tak a ni. I rilrua zawhna lo lutte chu notebook-ah ziak rawh. Doctor hmu tura i kal hunah chuan zawt vek rawh. I fa medical team chuan heng zawng zawng hi an hrilhfiah ang che a, a hnua i tih tur chu an kaihruai ang che.
Take-Home Thuchah a ni
- Shone’s Complex hi pianpui lung natna hmuh tur awm lo tak a ni a, thinlung veilam a thisen kal chu a tikhawlo a ni.
- He natna hi a vei tih hriat theih nan naupang hian heart defects bik 8 zinga 2 tal a neih a ngai a ni.
- Hei hi enkawlna awm chhun chu surgery a ni. Surgery hi a hlawhtling fo thin.
- Operation hnuah naupang chu a dam chhung zawng cardiologist nen enkawl a ngai dawn a ni. Heng appointment zawng zawng hi thlahthlam suh.
- A pawimawh ber chu he dinhmun hi i sualna emaw, i kawppui sualna emaw a ni lo. Ngaihtuah buai suh.











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