Anemia, mahse taksaah iron tam lutuk? Sideroblastic Anemia chungchang hi han sawi ila

Mi tam zawk chuan ‘anemia ’ tih thumal an hriat hian iron tlakchhamna an ngaihtuah nghal thin. Chuvangin an chau reng a, an chau a, an luak a, a chang chuan an muhil thei lo bawk. Mahse, thisen tlakchhamna ṭhenkhatah chuan a kalh zawngin a thleng tak tak tih i hria em? Iron tlakchhamna ai chuan thisen cell chhunga iron awm chu ‘a pung’ zawk a ni. Hei hi a mak deuhin a ri lo em ni? Vawiin hian chutiang special, mahse a tlangpui lo, anemia condition pakhat sideroblastic anemia tih kan sawi dawn a ni.

A awlsam zawngin, Sideroblastic Anemia chu eng nge ni?

Hei hi hrethiam tur chuan kan thisen hi han thlir hmasa ila. Kan thisen chhunga thisen sen chhungah hian protein pakhat hemoglobin tih a awm a . A hna ber chu kan thawk chhuah huna lung chhunga oxygen lo lut chu man a, taksa pum puia phurh chhuah hi a ni. Chuvangin he oxygen hi kan taksaa cell tinte nung turin a pawimawh hle.

Tunah chuan he hemoglobin siam tur hian kan taksa hian mineral ‘iron’ hi a mamawh tak zet a ni. A tlangpuiin taksain iron a tlakchham chuan thisen tlakchhamna (anemia) a awm thin. Chuvangin hemoglobin a siam thei lo.

Kitchen pakhatah chuan buhfai, tui leh chi te chu buhfai siam nan a awm a, mahse buhfai siamna chu a chhe tawh tih han mitthla teh. Tichuan buhfai i siam thei lo. Chutiang chu a ni. He natnaah hian hemoglobin siamna atana mamawh iron a tam hle. Mahse chu iron hmanga hemoglobin, kan thisen sen (red blood cells) siamna factory chuan hna a thawk tha lo. Chuvangin hman loh iron chu heng thisen sen chhia chhungah hian a pung khawm tan ta a ni. Hetianga iron khawlkhawmtu cell pangngai lo te hi `(Sideroblasts)` kan ti a.

Hetiang natna lan chhuah dan hi engte nge ni?

He natna lan chhuah dan hi thisen tlakchhamna dang nen a inang hle a, chuvangin a chang chuan awlsam takin a buai thei bawk. Tin, natna hi a lo thang zawi zawi a, i vei tih pawh i hre lo mai thei bawk. Hengte hi i hmuh theih symptom lian ber berte chu an ni.

Sideroblastic Anemia chi hrang hrangte chu engte nge ni?

He natna hi chi hnih ah then theih a ni ber.

1. Sideroblastic Anemia rochun atanga lo chhuak

Hei hi thil awm lo tak, genetic condition a ni. Chu chu nu leh pa zinga pakhat atanga genes hmanga naupang hnena pek chhuah a ni tihna a ni. Hei hi a tlangpuiin X-linked Sideroblastic Anemia a ni. Hei hi hemoglobin siam chhuahna tichhe thei gene pakhata mutation vang a ni. Chuvang chuan taksain hemoglobin tlakchhamna phuhruk nan ei tur atanga iron tam zawk lakluh a tum thin. A nasat chuan liver ang chi taksa peng hrang hrang a tichhia thei a ni . He congenital type hi kum 30 an tlin hmain hmuhchhuah a ni tlangpui.

2. A hnu lama lo awm chi (Acquired Sideroblastic Anemia) .

Hei hi a tam ber chi a ni. A tha ber chu tihdam theih a ni fo thin . Doctor-te chuan a chhan dik tak chu a châng chuan hre lo mah se, he natna thlentu lian tak tak engemaw zat a awm a:

• Damdawi thenkhat: A bik takin TB damdawi thenkhat pek thin.
• Zu in tam lutuk: Hun rei tak chhunga zu in tam lutuk hi a hlauhawmna lian tak a ni.
• Chemical tha lo : Hun rei tak chhunga chemical tha lo thenkhat, lead ang chi te nena inzawmna nei.
• Natna dang: Hetiang dinhmun hi natna dang, immune disorder, tumor, emaw metabolic diseases vang pawh a ni thei.

Chu bâkah, chi hnih hian natna dang, hemochromatosis , tih chu an nei thei a, chu chuan taksaah iron tam lutuk a tipung a ni.

He natna hi engtin nge dik taka kan hriat theih ang?

A natna lan chhuah dan hi thisen tlakchhamna dang nen a inang avangin hriatchhuah a harsa deuh thei. Chuvangin i taksa ngaihthlak a pawimawh. A chunga tarlan symptoms pakhat emaw a aia tam emaw i neih chuan doctor pan rawh.

Doctor chuan uluk takin i natna lan chhuah dan a zawt ang che a, a enfiah ang che a, chutah chuan he natna hi i nei em tih finfiah turin test eng emaw zat a ti ang.

• Thisen Test: Thisen chhiar kim leh iron zirchianna hi a pawimawh ber a ni.
• Peripheral Blood Smear: Hetah hian thisen sample pakhat chu microscope hmangin an enfiah a, a hmaa kan sawi tawh ang khan iron-accumulating cells (Sideroblasts) pangngai lo tak tak a awm em tih an enfiah thin.
• Bone Marrow Biopsy: A then phei chuan bone marrow sample te tak te lak a ngai mai thei a, natna hriat chian nan test a ngai mai thei.
• Test dang: A tul chuan doctor chuan MRI scan emaw, genetic test emaw pawh a rawt thei bawk.

Engtin nge enkawl a nih?

Enkawl dan tur chu congenital emaw acquired type emaw i neih danah a innghat.

• A chhan enkawl dan: Acquired type i neih chuan a chhan hmasa ber chu paih chhuah a ni. Entirnan, damdawi pakhatin natna a thlen a nih chuan i doctor chuan chu damdawi chu a titawp ang a, a dang a pe ang. Zu in nasa tak i nih chuan zu in hi i bansan vek a ngai dawn a ni.
• Vitamin B6: Zirna hrang hrangah chuan vitamin B6, a nih loh leh pyridoxine hian natna chi hnih enkawlnaah a pui thei tih hmuhchhuah a ni. I doctor chuan he vitamin hi supplement atan a pe thei ang.
• Iron tam lutuk paih dan: Taksa atanga Iron tam lutuk paih chhuah nan damdawi pek theih a awm. Deferoxamine hi vun hnuaiah injection angin pek a ni a, Deferasirox hi pill angin pek a ni bawk. Amaherawhchu, heng damdawi te hian kal (kidney) a nghawng thei a, chuvangin doctor enkawlna hnuaiah hman tur a ni.
• Thisen pek: I taksain vitamin B6 enkawlna a dawn loh chuan i doctor chuan thisen pek a rawt thei ang. Mahse, hei hian a chhe lam a nei a ni. Thisen pek chhunzawm zel chuan i taksaah iron level a sang ang a, chu chuan liver tihchhiatna a tipung ang.
• Bone Marrow Transplant: Hei hi enkawlna hnuhnung ber a ni. Damdawi dangin damdawi a chhuah loh chuan natna khirh tak takah ngaihtuah a ni.