Nangmah emaw, i hmangaih tak emaw hian Amyotrophic Lateral Sclerosis (ALS) i vei a nih chuan a harsatzia kan hria. He natna, zawi zawiin kan taksa peng hrang hrangte thununtu nerve cells ti chak lotu nen hian nun hi thil awlsam a ni lo. Chuvangin vawiin hian heng symptoms te hi a na zual zel dan tur control leh ti slow thei damdawi kan sawi dawn a ni. He damdawi hi Sodium Phenylbutyrate an ti a; Taurursodiol hmanga siam a ni.
He damdawi hi eng nge thleng tak tak?
A hmasain hei hi i hrethiam ang u. He damdawi hi ALS damdawi tling tak a ni lo. Mahse thil pawimawh tak a ti a ni. He damdawi hian a tih chu natnain a tihchhiat nerve cell te a venghim a ni. Chutiang chuan a natna lan chhuah dan a tikhawtlai thei a ni. A awlsam zawngin sawi ila, he damdawi hian damlo tan hahdamna engemaw chen a pe a, natna kal zel dan pawh eng emaw chen a thunun thei a ni.
Doctor-te chuan damdawi lam thil dang atan pawh hetiang hi an rawt thei a, chuvangin he thil chungchanga zawhna i neih chuan i doctor nen inbia a, chu chu chinfel a tha ber.
Damdawi ei hmaa doctor hnena i hrilh tur thilte
He damdawi hi i tan hma hian i hriselna dinhmun kimchang takin doctor hnenah i sawi hmasak phawt a pawimawh hle. A hnuaia condition te hi i neih chuan hrilh ngei ang che.
| Natna emaw, dinhmun dang emaw | Engvangin nge doctor hnenah ka hriattir ang ? |
|---|---|
| Liver natna | A chhan chu taksa atanga damdawi lakchhuahna atan thin (liver) hi a pawimawh em em a ni. |
| Kal natna | A chhan chu kal (kidney) hian damdawi chu a filter a ni. |
| Lung natna (Heart failure) . | He damdawi hian sodium a pai a, chu chuan thinlung a tichhe thei a ni. |
| Thisen sang a sang | A chhan chu sodium hian thisen sang a tisang thei a ni. |
| Gallbladder natna a ni | A chhan chu he damdawi atana thil tel thenkhat hian gallbladder a nghawng thei a ni. |
| Pancreatic natna a ni | A chhan chu pancreatic function a nghawng thei a ni. |
| Intestinal lama harsatna a awm | A chhan chu side effects, diarrhea ang chi a awm thei a ni. |
| Damdawi dang, ei leh in emaw thil dang emaw allergy nei | Allergic reaction thlen loh nan. |
| Naupai emaw, naupai tum emaw | Nausen chunga nghawng a neih theih dan tur ngaihtuah turin. |
| Nau hnute pek | Damdawi chu nu hnute hmanga naute hnena a kal theih dan tur hre reng ang che. |
Engtin nge damdawi hi ka hman ang?
He damdawi hi hman dan dik hriat a pawimawh hle.
- Ei dan: Hei hi damdawi ei tur a ni. Nitin hun khata ei tum la, i doctor-in a tih ang chiah khan ei tum ang che.
- Inbuatsaihna: Damdawi packet atanga powder chu room temperature tui glass khatah (240 ml vel) dah la. Tichuan, a hmin theih nan uluk takin stir rawh.
- Engtikah nge in tur: Hei hi chaw ei tan tirh lamah emaw, chawhmeh ei rualin emaw in thin ang che . Pum ruak ah ei loh tur.
- Titawp: I doctor-in a tih chhung chu damdawi ei chhunzawm zel ang che. A chanve vel chu tawp suh.
Fimkhur tur: He damdawi hi i ei tam lutuk, chu chu overdose a ni tih i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah phone nghal la , emaw, damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal nghal rawh. Hei hi emergency angin en rawh.
Thil dang pakhat chu, he damdawi hi i tan chauh a ni. Midang hnenah share ngai suh, chu mi chuan nangmah ang bawka symptoms nei mahse.
Damdawi dose pakhat i ei loh chuan engtin nge i tih?
Lungngai suh. Dose i miss a nih chuan i hriatreng veleh ei nghal rawh. Mahse i dose leh tur a hun tawh dawn a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Dose hloh tawh chu tihpun nan double dose ei ngai suh.
He damdawi nena inzawm thei damdawi dang
Damdawi dang i ei lai thenkhat chu he damdawi nen hian a inzawm thei a ni. Damdawi ei tur zawng zawng hi doctor hnenah hrilh vek a pawimawh. A bik takin a hnuaia damdawi te hi i ei a nih chuan:
- Anticid thenkhat
- Cholestyramine a ni
- Colesevelam chuan a rawn ti a
- Colestipol chuan a rawn ti a
- Cyclosporine a ni
- Probenecid a ni
He list hi a kimchang lo hle. I damdawi ei zawng zawng, prescription leh nonprescription damdawi, vitamin, herbal remedies, leh traditional medicines te pawh i doctor hnenah hrilh vek a pawimawh. Tin, zu i in emaw, zu i in emaw, ruihhlo dang i hman emaw a nih chuan doctor hrilh a pawimawh bawk.
Side effect awm thei te chu engte nge ni?
Damdawi dang ang bawkin he damdawi hian side effect engemaw zat a nei thei. Ṭhenkhat chu serious an ni a, ṭhenkhat chu common tak an ni.
| Side effect chi hrang hrang | Natna |
|---|---|
| Side effects te chu doctor hnenah hriattir nghal tur a ni | |
| Allergy natna a awm thei | Vun vun rawng, hnim hring, hmai, hmui, lei emaw kawr emaw a hring, thawk harsa. |
| Side effect tlangpui, a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hriattir tur a ni | |
| Kawthalo | Flatulence a awm. |
| Luhai | Luak chhuak ang maia hriatna. |
| Pum natna | Pum natna emaw, nuam lo emaw. |
He list-ah hian side effect awm thei zawng zawng a tel lo. Heng bakah hian thil danglam bik i tawn chuan doctor thurawn la rawh.
Engtin nge damdawi chu ka dahkhawm ang? Engtin nge ka paih chhuah ang?
- Storage: He damdawi hi naupang leh ran vulhte hmuh theih lohna hmunah dah tur a ni . Room temperature (20 leh 25 degree Celsius inkar)-ah dah a tha ber. Damdawi expired hman loh tur.
- Disposal: Damdawi hman hun tawp tawh emaw, mamawh tawh lo emaw paih dawnin him taka tih a pawimawh. Damdawi package-a instruction awmte chu enfiah rawh. Bawlhhlawh paih a him tih a sawi chuan damdawi chu a bawm atang chuan la chhuakin, ui bawlhhlawh, leilung, emaw coffee ground hman tawh ang chi thil nen chawhpawlh rawh. Tichuan, a hmin chu bag khauh takah dah la, bawlhhlawh bawmah paih rawh. I chiang lo a nih chuan doctor hnenah thurawn dil rawh.
Take-Home Thuchah a ni
- He damdawi (Sodium Phenylbutyrate; Taurursodiol) hian ALS a tidam lo a, mahse a natna lan chhuahna rate a ti hniam thei a ni.
- I damdawi chu chaw ei rualin ei fo la, i doctor-in a tih angin.
- Damdawi dang i ei zawng zawng leh i damdawi lam harsatna dang (a bik takin liver, kidney, emaw thinlung natna) i neihte chu i doctor hnenah hrilh rawh.
- Allergic reaction chhinchhiahna (vun rawng, hring) a awm chuan doctor lam pan nghal tur a ni.
- I overdose chuan National Poisons Information Center emaw, damdawi in hnai ber Emergency Department (ETU)-ah emaw kal nghal rawh.
- He damdawi hi i tan chauh a ni. Midang hnenah share ngai suh.











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