I naute piang thar i en hian a hmui leh a kut zungtang chu a sen deuh tih i hmu em? Chaw a pek hnuah a chau hle a, a thawmhnaw a hah a, a muhil hle niin a lang em? Nu emaw pa emaw chuan heng thilte hi an hmuh hian hlauhna nasa tak an nei hi thil pangngai a ni. A châng chuan chutiang chhinchhiahna hnuaiah chuan pianpui thinlung natna hmuh tur awm lo tak, Truncus Arteriosus tih chu a awm thei bawk. He hming i hriat hian hlau suh. Hemi chungchang hi awlsam tak leh chiang takin sawi ila.
A awlsam zawngin, he Truncus Arteriosus hi eng nge ni?
Hei hi hriatthiam harsa deuh angin a lang thei a, mahse a awlsam hle. Nausen hrisel tak chuan a thinlung a\angin thisen kalna (arteries) lian pahnih a lo chhuak ang tih han ngaihtuah teh.
1. Pulmonary Artery: Hei hian thisen "bawlhhlawh" oxygen level hniam tak nei chu thinlung atanga lung thlengin a phur a. He thisen atang hian lung hian oxygen a la chhuak thin.
2. Aorta: Hei hi lung atanga oxygen pek chhuah thisen "thianghlim" chu thinlungah a phur kir leh a, chuta tang chuan taksa pum puiah a pump chhuak thin.
Tunah hian i hrethiam em? Kawngpui pahnih ang mai a ni. Pakhat chu lungah, pakhat chu taksaah.
Mahse, Truncus Arteriosus vei nauteah chuan heng thisen kalna kawng pahnih hi thisen kalna kawng lian pakhat chauhvin a thlak a ni. Hei hian oxygen nei thisen leh oxygen nei thisen chu a inzawm khawm tir a ni.
He thisen inzawm hi naute taksa pum puiah a kal a. Hei hi kerosene tlem tal gasoline nena chawhpawlh a, car-a pump luh ang a ni. Engine hi a rit hlein a hria a ni lawm ni? Chutiang chuan naute thinlung leh lung te te hian phurrit lian tak leh thawhrimna nasa tak a phur a ngai a ni.
Hemi avang hian doctor-te chuan hei hi pianpui thinlung natna lian tak niin an ngai a ni . Naute pian hnu lawkah operation hmanga siamthat a ngai a ni.
Engtin nge ka naute hian he natna hi a nei tih ka hriat theih ang?
Heng symptoms te hi naute pian hnu ni engemaw zat chhungin a lang tan tlangpui. Hemi chungchangah hian i fimkhur hle tur a ni.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Vun dum emaw, vun dum emaw (Cyanosis) . | Naute hmui, kut zungtang leh nail, a bik takin a hmui vel chu a sen vek a. Hei hi taksaa thisen luang chhuak oxygen a tlem vang a ni. |
| Thâwk harsa | Naute chu a thaw rang hle mai. Thâwk chhuah laiin rilru chu chhung lam pan ang maiin a lang thei. |
| Bawnghnute in harsat | Bawnghnute tlem ka in hnuah ka chau hle. Bawnghnute in laiin ka thawmhnaw a chhuak a, a nih loh leh ka muhil. |
| Mutthilh lutuk | Naute chu a muhil reng a. Inkhelh leh active taka awm duhna a nei lo. |
| Thau tihpun loh | Naute hian bawnghnute a in tha a nih pawhin a rihna chu a pangngaiin a pung lovang. |
| Thinlung thawk chak tak leh pulse chak lo | Naute rilruah i kut i dah chuan heart rate chu a rang zawkin a lang thei. Pulse pawh a chak lo thei bawk. |
Heng chhinchhiahnate hi i hmuh chuan i naute chu doctor hnenah hruai nghal rawh . Tikhawtlai suh.
Engvangin nge nauteah hian hetiang dinhmun hi a lo awm?
A tam zawkah chuan naute thenkhatah hetiang thil hi a thlen chhan chiang takin doctor-te pawhin an sawi thei lo. Mahse a chhan ber chu nu pum chhunga naute lo than chhoh tirh laia thinlung lo thang lianin a lo awm thin defect a awm vang a ni. Chu thisen kalna kawng pahnih kan sawi tawh kha a tir lamah chuan a inzawm tlat a ni. Nakinah chuan pahnihah an inthen ta a ni. Hetiang a nih chuan chu inthenna chu a thleng dik lo.
He thinlung chhiatna hi genetic condition thenkhat nen a inzawm thei a, chu chu DiGeorge syndrome , a ni a, naupai laiin nuin a hmachhawn tur risk factor thenkhat vang pawh a ni thei bawk.
Naupai laiin risk factors te
- Nu zunthlum vei
- Viral infection thenkhat, rubella ang chi lo awm
- Zu emaw ruihhlo emaw hman
- Lead ang chi naute tan a hlauhawmChemical tha lo tak tak nena inzawmna
Doctor-te hian engtin nge hei hi an hmuh?
A châng chuan, naute pian hnua damdawi inah routine test an tih laiin hei hi rinhlelh theih a ni. Naute oxygen level tehna pulse oximetry test-ah oxygen level hniam a awm a nih chuan doctor-te chuan test dang an nei leh ang.
He natna hi finfiahna atana test ber chu echocardiogram a ni . Hei hi thinlung scan a ni. Chu chuan thinlung pianzia te, thisen kalna hmun awmna te, leh thisen kal dan te chiang takin a hmu thei a ni.
A châng chuan, doctor chuan nau neih hmaa ultrasound a neih laiin thinlungah thil dik lo a hmuh chuan, naute thinlung chu a bik takin a enfiah ṭhin fetal echocardiogram , tih a rawt thei a ni.
Hei hi eng enkawlna nge ni? Surgery neih a ngai em?
Awle. He natna hi damdawi hmang chauhin tihdam theih a ni lo. Naute chu a pian tirh kar tlemte chhungin heart operation neih a pawimawh hle. Hei hi naute nunna chhanhim tura tih a ni.
Chumi atana surgery ber chu Rastelli repair an ti a . Hemiah hian surgeon-te chuan:
- Heart wall-a khur (`VSD`) chu patch hmanga khar a ni.
- Thisen kalna kawng lian (`truncus`) awm tawh awmchhun hmangin aorta thar siam a ni.
- Artificial conduit leh valve hmangin lungah thisen phur turin pulmonary artery thar siam a ni.
A awlsam zawngin, doctor-te chuan thinlung chhunga thisen kalna kawng pahnih bo chu an siam thar leh a ni. Hei hi surgery buaithlak tak ni mahse, Sri Lanka rama heart surgeon thiam tak takte chuan heng surgery te hi hlawhtling takin an ti thin.
A pawimawh ber chu naute a lo seilian chhoh zel chuan artificial conduit (`conduit`) chu a lian lo hle a ni. Chuvang chuan nakin lawkah nausen a lo puitlin chhoh zel chuan a thlakna tur surgery vawi khat emaw a aia tam emaw i neih a ngai dawn a ni. Hemi chungchang hi i doctor chuan a hrilh belh ang che.
Naute hi he natna nen hian a dam thei ang em?
He zawhna hi i rilrua hlauhna lian ber a ni ngei ang. A chhanna chu, a ni, a theih ngei ang. Mahse, operation i neih phawt chuan. Enkawl loh a nih chuan kum khatna chhungin naute nunna atan hlauhawmna nasa tak a awm a ni.
Mahse, tunah chuan operation hnua damchhuah zat chu a sang tawh hle. Data thar ber atanga a lan dan chuan he surgery hlawhtlinna hi 80% atanga 97% vel a ni . Naute operation atanga kum khat chhunga dam tawh chuan kum 20 thlenga dam theihna chance 92% aia tam a nei a ni.
Heng statistics te hi hlau suh. Naute tin hi a danglam vek. I naute hmalam hun chu heng number te hian a hril lo. A pawimawh ber chu i naute mamawh damdawi lam enkawlna leh i hmangaihna leh enkawlna pek hi a ni.
Nun pangngai an hmang thei a, mahse a chang chuan naupang dang ang bawka tlan kual leh inkhelh hian hah deuhin an inhria thei. Mahse sikul an kal thei a, lehkha an zir thei a, an hna an thawk thei bawk. A pawimawh ber chu an dam chhung zawnga cardiologist enkawlna hnuaia awm hi a ni .
Take-Home Thuchah a ni
- Truncus Arteriosus hi pianpui thinlung natna na tak, mahse enkawl theih a ni.
- I naute vun rawng sen, thawk harsa, hnute pek harsa tih ang chi symptom i hmuh chuan doctor pan nghal rawh.
- Nausen nunna chhanhim nan nausen pian hnu kar hmasa lama lung zai (heart surgery) tih hi a pawimawh hle.
- Operation hnuah pawh i fa hian a dam chhung zawng cardiologist hnenah enkawl a ngai dawn a ni.
- He zinkawng hi harsa i ti mai thei, mahse nangmah chauh i ni lo. I doctor, damdawi ina thawktute, leh chutiang thil tawn tawh nu leh pa dangte hnen aṭangin ṭanpuina la rawh.











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