I thisen kalna kawngah hian thil mak tak a awm em? Heng (Vascular Malformations) te hi i zir dawn em ni?

I vun hmun hrang hrang, a rawng danglam, a hring hring ang maia lang, leh a chang chuan a na em em? A nih loh leh i taksaah hian i naute pianpui, mahse a lian chho zel niin a lang, hmun mak tak a awm em? Chûngte chu thil awlsam tak a ni thei. Mahse, a châng chuan hengte hi Vascular Malformations , tih hming pu dinhmun danglam tak chhinchhiahna a ni thei a, chu chu thisen kalna kawng, a nih loh leh thisen kalna kawng dik lo a ni. Chuvangin, lungngai suh. Hemi chungchang hi vawiin hian chipchiar tak leh awlsam takin i sawi dawn nia.

Vascular malformations hi eng nge ni? A awlsam zawngin...

Vascular malformations hi kan taksa chhunga thisen kalna kawng dik lo emaw, inthlak danglamna emaw a ni. Chungte chu pianpui a ni fo thin. Mahse, a châng chuan naupan lai te, tleirawl lai te, a nih loh leh puitling lai pawhin a lang chhuak ṭhin.

Kan taksa pum puia kal thisen kalna kawng (blood vessel system) hi kawngpui (network) angin han ngaihtuah teh. A châng chuan heng kawngte hi siam a nih hian famkim lohna tenau leh inzawmna dik lo a awm thei a ni. Hetah pawh hi chutiang chu a ni.

Heng vascular malformations te hi i taksa khawi hmunah pawh a awm thei a, i lu atanga i ke ruh thlengin a awm thei. A châng chuan soft tissue mass , natna , hring , vun rawng danglam angin an lang ṭhin . Ṭhenkhat chu hmaiah, kawr bulah, thluak bulah emaw, ruhroah emaw a lang a. A dangte chu pianpui chhinchhiahna emaw, hmun sen emaw ang maiin an lang.

A tlem hle a, trauma emaw thil dang emaw hnuah emaw, puitlin hunah pawh an lo lang leh thei. Natna an thlen a, mit an tibuai a, nitin hnathawh an tibuai a, thisen an chhuah a, harsatna dang an siam a nih chuan heng vascular malformations te hi enkawl a ngai a ni.

Taksa chungah khawiah nge hengte hi a awm tam ber?

"Vescular" tih thumal hi "thisen kalna kawng nena inzawm" tihna a ni. Chuvangin he dinhmun hian kan circulatory system-a thisen kalna kawng eng pawh a nghawng thei a ni. Kan lymphatic system-a lymphatic vessels te pawh a nghawng thei bawk.

Thisen kalna kawng chi hrang hrang a nghawng thei te chu:

• Arteries leh arterioles - Heng thisen kalna kawngte hi thinlung atanga taksa peng dangte hnena oxygenated thisen phurtu an ni.
• Capillaries - Thisen kalna kawng tha tak tak awmna network.
• Veins leh venules - Hengte hian taksa peng hrang hrang atanga thisen hman tawh chu thinlungah a rawn hruai kir leh thin.
• Lymphatic channel hrang hrang a awm- Hengte hian taksaa lymph fluid an phur chhuak thin.

Vascular malformations chi hrang hrang lian ber berte chu engte nge ni?

Heng dinhmunte hi a chang chuan naute vunah birthmark angin a lang thei bawk. A nih loh leh, a hmaa kan sawi tawh ang khan taksa khawi hmunah pawh an lo thang lian thei a, thluak leh ruhroah pawh an lo thang lian thei bawk. Doctor-te chuan thisen kalna kawng chi hrang hrang a nghawng dan a zirin a chi hi an ruat thin.

Hengte hi hmuh tam ber chi thenkhat chu an ni:

• Venous malformation: Hei hi a tam ber a ni. A hming ang bawkin vein pakhatah a lo thang lian thin. Vein hi kan taksa chhunga thisen kalna kawngte a ni a, oxygen tlachham thisen chu thinlungah a phur kir leh thin. Chungte chu blue-colored lump ang maiin a lang thei a, a chang chuan khawih pawh a hrehawm thei bawk.
• Arteriovenous malformation (AVM): Hei hi thisen kalna kawng leh thisen zam inzawmkhawm dan pangngai lo a ni. A tlangpuiin arteries te chu capillary ah a tawp a, chutah chuan veins te chu a intan leh thin. Mahse AVM-ah chuan arteries atanga thisen chu vein-ah direct-in a luang lut a, chu chu nidus an tih channel bundle pangngai lo tak hmangin a luang lut a ni. He AVM dinhmun hian thluak emaw, ruhro emaw a nghawng thei a ni.
• Capillary telangiectasia: Hei hi thluaka capillary lian tham tak awmna hmun te tak te a ni. A tam zawkah chuan hengte hi harsatna a awm lo. Mahse, a tlem hle a, thisen chhuahna , thisen chhuahna a ni.
• Cavernous malformations: Hetiang dinhmunah hian thluaka capillary te chu nghet takin an inzawm khawm a, "cavern" sei tak tak an siam thin. Heng lungpui chhungah hian thisen a luang zawi hle.
• Lymphatic malformations: Hei hian lymphatic ducts te chu a lian a, fluid-filled cysts a siam thin. Hengte hi hmai, kawr leh axillary region ang chi soft tissue-ah te hmuh tur a tam ber.

Vascular malformations leh hemangiomas te hi eng nge an danglamna?

An pahnih hian vascular anomalies vang a ni. An pahnih hian spot angin an lang thei a, birthmark nen a inang. Mahse an pahnih inkarah hian danglamna chiang tak a awm.

• Hemangiomas: Hei hi cancer ni lo (benign) vascular tumor a ni. Vun hnuaia thisen kalna kawng (blood vessels) a inzawm khawm hian an lo awm thin. "Strawberry hemangiomas" an tih chi hi naute pian hnuah a lo lang tlangpui. Naute thla ruk hmasa berah an thang chak hle. Mahse, heng tumor te hian harsatna an thlen tam lo va, enkawl lohvin anmahni chauhin an bo fo thin. Hemangioma hi a lian a, hnathawh thenkhat a tibuai a, natna a thlen emaw, harsatna dang a thlen emaw chuan a tihtlem thuai thei damdawi hmanga control theih a ni. Surgery neih a ngai tlem hle.

• Vascular Malformation awm thei te: 1.1.Hengte hi pian tirh laia awm, mahse naupan lai emaw, puitling emaw thlenga hmuh theih loh a ni thei. An thang zawi zawi a. Tin, a chhehvel tissue leh structure thuk takah an darh thei a, harsatna an siam thei bawk. Vascular malformations hi enkawl a ngai fo thin.

A awlsam zawngin: Hemangioma hi benign tumor a ni a, a mah chauhin a bo fo thin. Mahse, vascular malformations hi persistent condition a ni a, a lo thang lian thei a, harsatna a thlen thei bawk. Chuvangin an pahnih hi thliar hran a pawimawh.

Slow-flow leh fast-flow vascular malformations te hi eng nge ni?

Vascular malformation tam tak hi "slow-flow" category-ah an tel a. Chumi awmzia chu thisen chu a nghawng thisen kalna kawngah hian a kal zawi hle tihna a ni. Hei hi entirnan venous, lymphatic, emaw a pahnih (venolymphatic) malformations te hi a ni.

Mahse, AVM (Arteriovenous malformation) chu "fast-flow" vascular malformation a ni. Hei hian thisen chu thisen kalna kawng a\angin thisen kalna kawng hrang hrangah chak takin a luang a, a tlangpuiin thisen kalna kawng dik lo, nidus -ah a kal \hin. AVM lian takah hetiang hian thisen a kal chak chuan thinlung hian a thawkrim zawk a ngai a ni. Hei hian heart failure a tipung a ni .

Hengte hi engtiang chiahin nge a hluar?

Vascular malformations hi a awm lo hle. Nau piang zawng zawng zinga 1% vel ah an awm thin. Chung zingah chuan venous malformations, a chi khat ber chu mi 5,000 atanga 10,000 zinga pakhat vel a ni.

Eng thilin nge vascular malformations a thlen?

A tam zawkah chuan hengte hi nausen chu nu pum chhunga (in utero) a lo seilian laiin thisen kalna kawng leh/ emaw lymphatic channels lo thanglian dan dik lo vang a ni. Hei hian a tlangpuiin congenital an ni tihna a ni .

A tlem zawkah chuan hliam laia thisen kalna kawng chhiatna chu hriat lohvin a awm thei a, hun kal zelah thisen kalna kawng malformation-ah a chang thei bawk. Venous malformations hi accident hnuah emaw , puitlin lai emaw naupai laiin hormone inthlak danglam vang emaw a vawi khat nan a lo lang thei bawk .

A tlem berah chuan mi thenkhat chuan genetic mutations an rochun a, chu chuan vascular malformations neih theihna a tipung a ni. Zirchiangtute chuan heng genetic cause hrang hrangte hi an la zir belh zel a ni.

Tute nge hengte hi vei theihna hlauhawm zawk?

Mi thenkhat chuan genetic change an rochun a, chu chuan vascular malformations a tipung thei a ni. Chung dinhmun thenkhat chu:

• Blue rubber bleb nevus syndrome: Hei hian i intestines leh digestive system-ah venous malformation a thlen thin. I vunah hian dark blue, red, black lesions a siam thei bawk.
• CLOVES syndrome (congenital lipomatous overgrowth, vascular malformations, epidermal nevi leh spine deformities): Hei hian i ruhroah AVM a siam thin. Scoliosis ( ruh hring ( curvature of the spine), thau tipung te, leh rawng sen dum (dark red rash) a thlen thei bawk.
• Hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu syndrome tia hriat bawk): Hei hian capillary te tak teah tangles, a nih loh leh AVMs, a awm lo.
• Klippel-Trenaunay syndrome (KTS): Hei hian "port-wine stains" an tih birthmark sen hring (reddish-purple) a thlen a, ruh emaw tissue emaw a lo thang lian a, vein emaw lymphatic channel emaw a inrawlh malformation a thlen bawk.
• Parkes Weber syndrome: Hei hian i kut emaw ke emaw ah AVM a siam thin.

Hetiang genetic condition i neih chuan i hriat chian a pawimawh hle.

Vascular malformations symptoms te chu engte nge ni?

Symptoms chu malformation chi hrang hrangah a innghat. I vun tichhe thei vascular malformation chu raised red, blue, purple, brown, or black birthmark ang mai a ni thei . Heng hmunte hi a hring thei a, thisen a chhuak thei a, a na thei bawk.

I thluaka AVM i neih chuan , thisen a chhuah hma loh chuan symptom i nei lo mai thei. Brain AVM thisen a chhuah chuan i taksa sir khatah lu na, seizures, emaw paralysis emaw i nei thei .

Venous malformations hian natna a thlen thei a, a hring thei a, thisen zam a tichhe thei a, taksa peng hrang hrang a tichhe thei bawk.

Engtin nge hengte hi i hriat chian? Engtin nge doctor hian hei hi a hmuh theih?

Vascular malformations hian symptoms a thlen ngai lo a, doctor-te chuan harsatna dang test an neih laiin he natna hi an hmuchhuak fo thin.

Doctor-te chuan special imaging test hmangin thisen kal dan an enfiah a, vascular malformations an hmuchhuak bawk. Heng test hrang hrangte hi:

• Ultrasound , vascular ultrasound an ti bawk .
• MRI (Magnetic Resonance Imaging) , chutah chuan MR Angiogram (MRA) tih test pawh a tel a ni.
• CT scan (Computed Tomography scan), chutah chuan CT angiogram tih test pawh a tel a ni.
• Angiogram leh/ emaw venogram .
• X-ray neih fo thin .

Heng test te hian chu hmuna thisen kalna kawng awm dan te, thisen kal dan te, leh a tlangpuiin a tawi emaw, a zau emaw a awm leh awm loh te chiang takin a hmu thei a ni.

Hei hi eng enkawl dan nge ni ang?

Vascular malformations enkawlna tum ber chu symptoms tihtlem leh harsatna awm thei tihziaawmna a ni. Harsatna thlen lo malformation te hian enkawl a ngai lo mai thei a, hun kal zelah hmuh theih mai a ni.

Enkawlna chu thisen kalna kawng a nghawng danah a innghat a ni. Vawi tam tak chu heng enkawlnaah hian thisen kalna kawng natna chu khar emaw, operation hmanga lak chhuah emaw a ni. Malformation tam tak chu minimally invasive technique hmangin enkawl theih a ni . Doctor-te chuan hetiang hi an hmang thei ang:

• Sclerotherapy: Hemiah hian damdawi bik pakhat chu a natna thisen kalnaah an inject a, chu chuan thisen kalna chu a ti tlem a, a khar a ni.
• Catheter embolization: Hetiang tih danah hian thisen kalna kawng (tube) te tak te (catheter) kaltlangin thisen kalna kawng pangngai lo chu a chhung atangin an seal thin.
• Laser hmanga enkawlna: Hei hi vun natna thenkhat tan hman a ni.
• Radiation therapy (radiosurgery): Hei hi malformation thuk tak tak, enkawl harsa tak tak thenkhat tan hman a ni.

A châng chuan, i doctor chuan biopsy , tih a rawt thei a, chu chu enfiah tûra tissue ṭhenkhat lak a ngai a ni. Hei hian diagnosis nemnghet leh/ emaw genetic testing atan tissue lakchhuahna kawngah a pui thei a ni .

Vascular malformations hi thil buaithlak leh hmuh tur awm lo tak a nih avangin, team approach hmanga enkawl a tha ber a, chu chu specialist tam tak awmna a ni

Hengte hi enkawl hnuah a lo awm leh thei ang em?

Ni e, vascular malformations hi enkawl hnuah pawh a lo lang leh thei. Chuvangin, malformation lo lang leh tur chu a hmaa hriat theih nan follow-up visit leh test neih fo a ngai mai thei.

Hengte hi a lo pian loh nan kawng a awm em?

Vascular malformations hi congenital a ni fo thin , chu chu ven dan tur a awm tak tak lo tihna a ni.

Mahse, i chhungkuaa mi pakhatin genetic condition a neih chuan vascular malformations a nei a nih chuan genetic counselor i hmuh a ngai mai thei.He specialist hian i fate hnena he natna hi a thlen theihna tur tihziaawmna tur duhthlan tur awmte chu a hrilhfiah thei che a ni.

Heng vascular malformations avang hian eng complication nge awm thei?

Malformation thenkhat chuan harsatna a thlen lo va, hmuh theih chauh a ni. Mahse, thil tam takah chuan natna leh hliam an thlen thei a ni .

Malformation ṭhenkhat chuan natna a thlen thei a, a nih loh leh taksa ruh, ruh, a nih loh leh nerve inrawlhna a thlen thei a, chu chuan exercise, infiamna, hnathawh, a nih loh leh ni tin thiltih a tibuai thei a ni .

Flow sang tak nei malformation lian tak takte chuan a tâwpah chuan heart failure a thlen thei a ni .

Solid organs, liver, kidney, uterus-a vascular malformation awm hian organ dysfunction leh harsatna dang a thlen thei a ni.

Vascular malformation thenkhat, thluak emaw spinal cord-a AVM awm te hian thluaka oxygenated thisen a thlen zat a tihtlem thei a ni. Hei hian nunna atana hlauhawm harsatna a thlen thei a, chungte chu:

• Aneurysms ( thisen kalna kawng bang chak lo leh balloon ang maia bulging) .
• Lung chhunga thisen chhuak
• Stroke a awm

Hetiang natna vei te hmalam hun eng nge ni? Chu chuan engtin nge an nun a nghawng?

Vascular malformations, pian chhinchhiahna ang maia lang hian mi hmel leh mahni inrintawkna a nghawng thei a ni. Hei hian rilru lam thila harsatna leh lungkhamna a thlen thei a ni . Mahse, heng malformation tam tak hian enkawlna an dawng tha hle.

Malformation na zawk, thluaka AVM awm te hi thisen chhuak tan chuan nunna atana hlauhawm tak a ni thei.

Mahse, a pawimawh ber chu malformation tam zawk hi enkawl theih a ni a, enkawlnaah pawh a chhang tha hle. Chuvangin, hlauthawng lova damdawi lam thurawn mumal tak zawn a pawimawh.

I doctor hnenah eng nge i zawh tur?

He natna chungchangah hian rinhlelhna i neih chuan, emaw, i vei tih hmuhchhuah a nih chuan, i doctor hnenah heng zawhnate hi i zawt thei ang:

• Engtin nge he vascular malformation hi ka neih theih? (Eng nge a chhan?)
• Eng ang vascular malformation nge ka neih?
• Ka tan enge inenkawlna tha ber?
• Enkawlna avanga hlauhawmna emaw, nghawng tha lo emaw awm thei te chu engte nge ni?
• Complication symptoms hi ka ngaihtuah tur em ni? Chu chhinchhiahnate chu engte nge ni?

Heng zawhnate hi zawt la, i dinhmun hriatthiamna chiang tak nei rawh.

A tawp berah chuan hriat reng tur pawimawh ber ber (Take-Home Message) .

Okay, chuvangin kan sawi tawh atang khan i hriat reng tur thupui ber berte chu han en mai ila.

• Vascular malformations hi thisen kalna kawng dik lo awm lo tak a ni a, nau piang laiin a awm fo thin.
• Hengte hi taksa khawi hmunah pawh a thleng thei , symptom hrang hrang a lantir thei a, a chang chuan symptoms engmah a lantir lo thei bawk.
• Hemangiomas leh Vascular Malformations hi thil chi hrang hrang pahnih a ni. An pahnih inthlauhna hriat a pawimawh.
• He natna hi enkawlna hrang hrang a awm a. I doctor chuan i dinhmun enkawlna tha ber tur a ruat ang.
• Thil pawi tak tak thenkhat, a bik takin thluaka AVM te hian harsatna a thlen thei a, chuvangin damdawi lam enkawlna mumal tak neih a pawimawh hle.
• Nangmah emaw i fa emaw hian heng symptoms te hi i neih chuan hlauthawng suh la, doctor hnenah thurawn dil rawh.

Hetiang dinhmun i hmachhawn hian nangmah chauh i ni lo tih hre reng ang che. Thu hriat dik leh damdawi lam puihna a awm chuan he natna hi uluk taka enkawl theih a ni.

` Vascular malformations, thisen kalna kawng dik lo, pianpui chhinchhiahna, AVMs, venous malformations, thisen kalna kawng harsatna, pianpui natna