I mit thununna hloh thut a, i taksa sir lehlamah i ke emaw, ke emaw i hloh tih i ngaihtuah ngai em? Hei hi a takah chuan thil hlauhawm leh ngaihtuah phak loh a ni a, mahse kan nunah hian a chang chuan kan hmachhawn tur thil a ni. Vawiin hian mi zawng zawngin kan hriat chian tur thil awm lo tak kan sawi dawn a ni. Hei hi doctor ten Weber Syndrome an tih chu a ni .
Weber Syndrome hi eng nge ni tak tak?
A awlsam zawngin, Weber Syndrome hi i midbrain tihchhiat avanga lo awm a ni . Midbrain hi bridge pawimawh tak a ni a, i thluak atanga i spinal cord thlenga thuchah a thlen thin. I thluak chung bera awm i thluak bul a ni. I mit tihchet leh i mitmeng tihsan ang chi thil control tu cranial nerve pawimawh pahnih— oculomotor nerve leh trochlear nerve —chu midbrain atanga tan a ni.
Chuvangin, he midbrain hi engti kawng pawhin a chhiat chuan hemiplegia , i nei ang a, chu chu i taksa sir khatah i thunun thei tawh lo tihna a ni. Chutih rual chuan a lehlamah mit leh mit hmuhna lamah harsatna i tawk ang. Hei hi Weber Syndrome-ah hian hmuh tur a awm ber a ni. Hei hi thil awm lo tak anga ngaih a ni.
Midbrain chhiatna thlentu ber chu stroke a ni a, chu chu thluaka thisen kal titawp nghal mai a ni. Mahse, chhan dang vangin a thleng thei bawk.
Hei hi eng symptoms nge ni? Engtin nge kan hriat chian?
Weber Syndrome-ah hian symptom lian tak tak hmuh tur a awm nual. Anni chu:
- Mit pakhata mitmeng (ptosis) tlak . Mit chu a chanve inkhar ang maiin a lang.
- Mit natna chu hnuai lam leh pawn lam hawiin a inher thei a , chu chu mit chu a thunun tha thei lo tihna a ni.
- Thil pahnih vawi khata hmuh (diplopia) . Hei hi double vision an ti a.
- Taksa sir khatah kut leh ke chu a then emaw, a paralysis vek emaw a ni . Hei hi mit natna veilam lehlamah a thleng thin.
Pawimawh tak: Heng symptoms zinga pakhat emaw, a aia tam emaw, emaw, stroke symptoms dang tam tak zinga pakhat emaw i neih chuan, thusawi thiam lo , hriatna hloh , mit hmuhna hloh , balance issues , emaw hmai tlahniam , damdawi inah i kal nghal tur a ni. Hei hi nunna emaw thihna emaw dinhmun a ni thei.
A chang chuan Weber Syndrome vei te hian...Balance leh coordination problems (ataxia) , kal leh thil man harsa tihna pawh a awm thei bawk.
A tlangpuiin Weber Syndrome chauh a awm chuan i ngaihtuahna (memory, intelligence) a nghawng lo. Amaherawhchu, thluak peng dang tihchhiatna a lo darh tawh chuan symptom dang a lo lang thei a ni. Entirnan, Weber Syndrome hi a chang chuan thluak bul thenkhat, pons paralysis nen a inzawm thei bawk. Chutiang a nih chuan symptom dang pawh hmuh tur a awm thei bawk.
Weber Syndrome hi engte nge ni?
Weber Syndrome hi i midbrain hmun bik, ventromedial part-a lesion awm vang a ni. Hetiang chhiatna chi hrang hrang thlentu ber chu:
- Stroke: Hei hi a chhan tam ber a ni. Chu thluak hmuna thisen petu thisen kalna kawngkhar (blood vessel) a block emaw, a rupture emaw avanga lo awm thei a ni.
- Brain aneurysm (thluaka thisen kalna kawng bulging leh puak).
- Thluak thisen chhuak.
- Thluak natna (brain tumor) a awm.
- Demyelinating diseases , Multiple Sclerosis ang chi hian nerve chhehvela myelin sheath a tichhe thin.
Hetiang hi tuin nge nei tam zawk? (Risk factor hrang hrang) 1.1.
Kan sawi tawh ang khan Weber Syndrome thlentu ber chu stroke a ni a, chuvangin stroke tibuaitu risk factor ang chiah hian a nghawng bawk. Chu chu:
- Thisen sang (Thisen sang / Hypertension).
- Thisenah cholesterol a sang (High cholesterol / Hyperlipidemia).
- Zunthlum.
- Meizial zuk.
Heng risk factor pakhat emaw a aia tam emaw i neih chuan damdawi lam thurawn lak fo a, control hi a pawimawh hle. Chutianga tih chuan paralysis leh Weber Syndrome ang chi natna lo awm theihna a ti tlem thei a ni.
Engtin nge doctor-te hian hei hi an hriat chian? (Diagnosis) tih a ni.
Weber Syndrome nena inzawm symptoms i neih chuan doctor-te chuan stroke i vei em tih finfiah an tum hmasa ang. Hei hi a chhan chu enkawl vat hi a pawimawh ber a ni. Chutiang ti tur chuan:
- I nervous system ah neurological exam kimchang tak neih a ni ang .
- Brain CT scan an ti nghal a.
- A châng chuan lu leh kawr thisen kalna kawngte enfiah nân scan hran neih leh thluak MRI scan neih a ṭha bawk.
I symptoms leh heng scans te hian midbrain ah chhiatna i nei tih a nemnghet a nih chuan doctor te chuan Weber Syndrome i nei tih an sawi chhuak ang.
Hei hi eng enkawl dan nge ni ang?
Weber Syndrome enkawlnaah hian a chhan bulpui (a tam zawkah chuan stroke) enkawl hi ngaih pawimawh hmasak ber a ni. I medical team chuan rang takin i thawkna kawng an enkawl ang a, i thluaka thisen kal dan chu a siam tha leh ang. In some cases , thluak surgery (neurosurgery) pawh a ngai thei bawk.
Weber Syndrome enkawlna bik atana hman ber chu rehabilitation strategy hi a ni.
Rehabilitation chu eng nge ni? Engtiang chiahin nge a pawimawh?
Stroke vei tam tak tan chuan rehabilitation hi dam lehna atana thil pawimawh tak a ni. I thluak inthlak danglamna avanga i thiamna hloh tawhte chu i neih let leh theihna tura tanpui che emaw, inthlak danglamna nena nun dan zir tura tanpui che emaw a ni. Hemi kawngah hian stroke rehabilitation team emaw physical therapist emaw, a bik taka training nei chuan a pui thei che a ni. He rehabilitation programme hi a rang thei ang bera tan a tha ber.
Weber Syndrome leh midbrain palsy te rehabilitation-ah hian hetiang hi a tel thei:
- Ke ruh natna (paralyzed limb) tihchakna tura puitu exercise (Range-of-motion exercises) .
- Balance leh coordination tihchangtlunna tura exercise neih thin.
- I mit enfiah la, exercise dik tak ti la, double vision tih tlem nan.
- Mi thenkhat chuan an zun (urinary incontinence) an thunun thei lo mai thei. Chumi atan chuan training bik a ngai a ni (Bladder training) .
- Stroke risk factor awmsa control nan leh nakin lawka stroke lo awm tur venna atan damdawi leh intervention dangte a ngai a ni.
Hetiang dinhmun atanga dam leh tur hian eng chen nge a mamawh ang? (A dam leh theih beisei)
Weber Syndrome vei mi pakhat prognosis hi thil engemaw zatin a nghawng a, chungte chu:
- Hei hi eng nge a chhan ?
- Engtiang chiahin nge enkawlna i dawng rang .
- Weber Syndrome chauh i nei em, thluak hmun dang pawh a chhiat em ?
- Nakin lawka paralysis lo awm tur venna atan engtiang chiahin nge i tih .
Weber Syndrome chauh nei, thluak chhiatna dang nei lote hian a tlangpuiin prognosis tha tak an nei . Tin, rehabilitation tan hma hi dam lehna kawngah a pawimawh hle bawk.
Rehabilitation a awm chuan mi thenkhat chuan an taksa peng leh mit natna vei te chu hna engemaw zat an nei leh thei a ni. Mahse, mi dangte chuan permanent mobility problem leh neurological complication dang an nei thei bawk.
I medical team chuan i dinhmun a zirin eng nge i beisei tur tih chiang takin an pe thei ang che.
Weber Syndrome vang hian eng harsatna dang nge awm thei?
Weber Syndrome hian harsatna a thlen tam zawk a, a bik takin khumah i muhil a nih chuan. Chuvangin i medical team chuan a rang thei ang bera leh him taka i kal theih nan an bei ang. Harsatna lo awm thei thenkhat chu:
- Muscle rigidity leh contracture te .
- Bedsores te chu .
- Aspiration pneumonia hi ei leh in emaw thawkna kawng a luh a, lung infection a thlen hian a awm thin.
- Ke ruh thuk takah thisen a chhuak (Deep vein thrombosis - DVT) .
- Chu thisen zam chu lung (pulmonary embolism) -ah a kal a ni .
- Zun kawng natna (UTIs) .
A tawp berah chuan hriat reng tur pawimawh ber
Stroke hian i nun chu a tidanglam thei a ni. Chuvangin a natna lan chhuah dan hriat chian a pawimawh hle a, nangmah emaw, i hnaih ber emaw pawhin chutiang chhinchhiahna an neih chuan damdawi in pan nghal a pawimawh hle. Weber Syndrome hi thil awm lo tak a ni thei a, i hriat chuan hlauhna leh lungkhamna i nei thei bawk. Mahse thil pakhat hre reng ang che, i medical team te hian tanpui turin an inpeih reng a, i dam lehna kawngah pawh an awmpui reng che a ni. Chuvangin i rilru kha nghet takin vawng la, thurawn pekte chu zawm rawh.
` Weber Syndrome, paralysis, cerebral palsy, midbrain, mit natna, thluak lam natna, rehabilitation











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