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Kei te ngenge tonu koe? Kei te mangu haere tō kiri? Me ako tātou mō te Mate a Addison!

Kei te ngenge tonu koe? Kei te mangu haere tō kiri? Me ako tātou mō te Mate a Addison!

Kei te ngenge tonu koe, kei te ahua kore ora, ā, kei te huri haere te tae o tō kiri? Tērā pea he hiahia nui tōu ki te tote. He maha ngā wā ka warewarehia e tātou ēnei tohu, he mea noa iho. Heoi, he tohu pea ēnei mō tētahi mate i roto i tō tātou tinana kāore i te tino kitea, engari he mea tino nui kia tautuhia tika. I tēnei rā kei te kōrero tātou mō tētahi mate onge, engari ki te whakahaeretia tika, ka taea e koe te noho noa. Ko te Mate a Addison tēnā .

He aha te mate a Addison?

Āe, me whakamārama noa iho tēnei. E rua ā tātou repe iti, he tapatoru te āhua, he rite ki te pōtae, kei runga ake i ō tātou whatukuhu. Ka kiia ēnei e tātou ko ngā repe adrenal . He wāhanga tino nui ēnei o tō tātou pūnaha endocrine.

Ko te mate a Addison he āhuatanga e kore ai e nui te whakaputa a ngā repe adrenal i ngā homoni matua e rua, arā, te cortisol me te aldosterone .

He aha ngā take e hiahiatia ai ēnei homoni e rua?

  • Cortisol: He homoni tēnei e tino hiahiatia ana mō te ora. Ka āwhina i ō tātou tinana ki te aro atu ki te ahotea, pērā i te wā e mate ana tātou, e pāngia ana e te aituā, e pokanga rānei. Ka āwhina hoki ki te whakahaere i te toto toto, te tere o te manawa, te mahi a te pūnaha ārai mate, me ngā taumata huka toto.
  • Aldosterone: Ka āwhina tēnei homoni ki te whakataurite i ngā kohuke konutai (tote) me te pāhare pākawa i roto i ō tātou tinana. Ka whakahaere hoki i te nui o te wai ka tukuna e ō tātou whatukuhu hei mimi. Ka pā tika hoki tēnei ki tō tātou toto toto.

E mōhiotia ana hoki te mate a Addison ko te koretake o te adrenal tuatahi . Tērā tētahi atu āhuatanga e pā ana, e kiia ana ko te koretake o te adrenal tuarua . I roto i tēnei āhuatanga, kāore te repe pituitary i roto i te roro e tuku i te nui o te homoni ACTH , e whakaoho ana i ngā repe adrenal ki te whakaputa cortisol. Engari i tēnei rā ka kōrerohia te raruraru e puta ana i roto i ngā repe adrenal tonu.

Te rerekētanga i waenga i te mate a Addison me te mate a Cushing

Tērā pea ka pōhēhē koe i ēnei ingoa e rua. He rerekē rawa ngā āhuatanga o ēnei e rua.

Āhuatanga Te Mate a Addison Te Mate o Cushing
Raru matua Kāore i te rawaka te cortisol (me te aldosterone) i roto i te tinana. Te pikinga o te cortisol i roto i te tinana (Hypercortisolism).
Ngā āhuatanga noa Te whakahekenga taumaha, te pouri o te kiri, te toto toto iti. Te taumaha haere, te mata porotaka, te toto toto tiketike.

Ko wai te hunga tino tūpono ka pāngia e tēnei mate? He pēhea te noa o tōna pānga?

Ahakoa ka pāngia te tangata o ngā tau katoa e te mate a Addison, he mea noa iho tēnei i waenga i te 30 me te 50 tau te pakeke .

He tino onge tēnei mate . Hei tauira, i Amerika, tata ki te kotahi i roto i te kotahi rau mano tāngata ka pāngia e tēnei mate. Engari he tokomaha anō hoki e pāngia ana e tēnei mate i tō tātou whenua.

He nui ake te tūponotanga o te hunga ki te pāngia e tēnei mate. Ko rātou ēnei he hunga kei a rātou ētahi atu mate pūnaha ārai mate . Arā, ko ngā mate e whakaekea ai e te pūnaha ārai mate o tō tātou tinana ō tātou ake pūtau. Mena kei a tātou ēnei mate, ka nui ake te tūponotanga ki te pāngia e te mate a Addison.

  • Mate huka momo I
  • Te mate toto kino
  • Te mate o Graves
  • Te mate tairoiti mau tonu
  • Vitiligo - he mā ngā ira i runga i te kiri
  • Te mate pāwera

He aha ngā tohu o te mate a Addison?

I roto i te mate a Addison, he maha ngā wā ka tino puhoi te pakaru o ngā repe adrenal, i roto i te wā. Nō reira, ka āta puta ngā tohu. Ka rerekē pea ēnei tohu i ia tangata, i ia tangata.

Ngā tohu noa e puta haere ana
Ko te āhuatanga tino noa Ka piki haere te ngenge me te ngenge mau tonu , kāore e taea te whakamārama.
Ngā huringa kiri Te tae parauri/mangu o te kiri, inā koa ki ngā wāhi he koha, he whāriki kiri (pērā i ngā kēkē, i te hope), me ngā kapia (Hyperpigmentation).
Pūnaha nakunaku Mamae puku, whakapairuaki, ruaki, korere, kore hiahia kai, me te ngaronga taumaha.
Ētahi atu āhuatanga Mamae uaua me ngā hononga, matewai, whanoke ina tū (nā te toto toto iti), riri, pouri, hiahia nui ki te tote, me te huka toto iti (hypoglycemia).

Tērā pea ka pāngia ngā wāhine e ngā tohu pēnei i te paheketanga koretake, te ngaronga o te huruhuru o te tinana, me te hekenga o te hiahia moepuku.

Āhuatanga ohorere e hiahia ana kia arohia: Te raruraru o Addisonian

I ētahi wā, inā koa i muri i te mate kino, i te aituā, i te ahotea nui rānei, ka taea e ēnei tohu te huri ohorere hei tino kino. Ka kiia tēnei he Addisonian Crisis , he acute adrenal failure rānei. He āhuatanga ohorere hauora tēnei e hiahia ana kia rongoatia tonutia, ā, ka taea hoki te whakararu i te ora!

Ngā tohu o te raruraru Addisonian:

  • He ngoikore whakaharahara, kāore e taea te whakamanawanui.
  • Te mamae ohorere, te mamae nui i te tuara o raro, i te puku, i ngā waewae rānei.
  • Ngā huringa hinengaro pērā i te manukanuka, te pōhēhē, me te mataku.
  • Te ruaki nui me te korere (ka tere pea te matewai).
  • Te hekenga o te toto toto ki raro rawa.
  • Te ngaronga o te māramatanga.

Ki te pāngia koe, tētahi atu rānei e mōhiotia ana e koe, me kawe tonu atu ki te Tari Ohotata (ETU) o te hōhipera tata.

He aha ngā take o te mate a Addison?

Ko te tino take o te mate a Addison ko te urupare ārai mate.. He whakarāpopototanga noa iho, ka whakaekea e tō tātou ake pūnaha ārai mate (pūnaha ārai mate) te wāhanga o waho o ō tātou ake repe adrenal (te cortex adrenal) me te whakangaro i aua repe. Kāore anō kia mōhiotia te take tuturu o tēnei. Ka tīmata ngā tohumate te puta i muri i te whakangaromanga o te 90% o ēnei repe. Ka roa pea tēnei i ngā marama, i ngā tau rānei.

Koinei te take o te 75% o ngā tūroro a Addison.

Ētahi atu take onge:

  • Te mate kohi: He tino take tēnei i ngā wā o mua. He tino take tonu i ngā whenua whakawhanake.
  • Ngā mate urutā: Ngā mate e pā ana ki te HIV/AIDS me ngā mate harore.
  • Matepukupuku: Te horapa o ngā pūtau matepukupuku mai i ētahi atu wāhi ki ngā repe adrenal.
  • Te toto ki roto i ngā repe adrenal.
  • Te tango pokanga i ngā repe adrenal.
  • Amyloidosis: He mate e kohia ai tētahi momo pūmua i roto i ngā whekau, ā, ka pakaru ai.

Me pēhea te tautuhi i tēnei mate? (Tautuhinga)

Nā te mea he puhoi rawa te puta mai o ngā tohu, ā, he mea noa ki te maha atu o ngā mate, he uaua ki te tautuhi i te mate a Addison i ngā wāhanga tōmua. He maha ngā wā, ka kitea "tūpono noa" te mate. Ka whakapae pea ngā tākuta i tēnei mena ka kitea e rātou he iti te konutai me te nui o te pāhare pāporo i roto i te toto i te wā o te whakamātautau toto mō tētahi atu mate. Waihoki, ko te whero o te kiri he tohu nui e arahi ana ki te whakapae kei te pāngia koe e tēnei mate.

Mena kei te whakapae tō tākuta kei te pāngia koe e tēnei mate nā ō tohumate, ka tonoa e ia ētahi atu whakamātautau hei whakaū i te mate.

Ngā whakamātautau tātaritanga:

  • Ngā whakamātautau toto: Ka inehia e ngā whakamātautau toto ngā taumata o te konutai, te pāhare pāporo, te cortisol, me ngā homoni ACTH. I roto i te mate a Addison, he iti te cortisol, he teitei ngā taumata ACTH.
  • Whakamātautau whakaohooho ACTH: Koinei te whakamātautau matua hei whakaū i te mate. I roto i tēnei whakamātautau, ka werohia te homoni ACTH hangai, ā, ka inehia te taumata cortisol i roto i tō toto i te haora i muri mai. Mena kei te ora ō repe adrenal, me piki ake tō taumata cortisol. Heoi, ki te kore, ka whakaū kāore ō repe adrenal e mahi tika ana.
  • Whakamātautau huka toto i puta mai i te insulin: Ka mahia tēnei whakamātautau hei kimi mēnā he raruraru kei te repe pituitary te take o ō tohumate.
  • Matawai CT: Tērā pea ka mahia he matawai CT hei tirotiro mēnā kua pakaru, kua pangia, kua whakaitihia rānei te rahi o ō repe adrenal.

Me pēhea te rongoā?

Ko te tikanga matua mō te rongoā i te mate a Addison ko,Ko te Whakaora Whakakapinga Homoni (HRT) he tukanga whakakapi i ngā homoni ngoikore o te tinana mā te whakamahi i ngā pire hangai.

Nā te mea he mate mau tonu tēnei, me tango e koe tēnei rongoā mō te toenga o tō oranga .

  • Ka hoatu he rongoā e kīia ana ko te hydrocortisone hei whakakapi mō te homoni cortisol .
  • Ka hoatu he rongoā e kīia ana ko te fludrocortisone hei utu mō te homoni aldosterone .

He rerekē te horopeta o ēnei rongoā i ia tangata, i ia tangata. Waihoki, ka whakanuia pea e tō tākuta tō horopeta mō te wā poto hei ārai i te mate urutā Addisonian mēnā ka pāngia koe e tētahi āhuatanga taumaha, pērā i te mate pāwera, te aituā, te pokanga rānei.

Mena kei te tango koe i te fludrocortisone, ka tohutohu tō tākuta kia tāpirihia he tote anō ki tō kai, inā koa i te wā wera, werawera, me muri i te whakakori tinana kaha.

Te noho tahi me te mate me te aha me mahi

Mā te maimoatanga tika, ka taea e te tangata whai mate a Addison te ora i te oranga noa, hauora hoki . Heoi, he mea tino nui kia mau tonu te horopeta tika o te rongoā.

Mena he nui rawa te horopeta o te rongoā, ka puta pea ngā pānga taha pēnei i te momona, te mate huka momo 2, te osteoporosis, me te toto toto tiketike. Nō reira, he mea nui kia toro atu koe ki tō tākuta (he endocrinologist) i ia wā, kia whai whakamātautau hoki hei pupuri i te horopeta tika o te rongoā.

Ngā mea me mahi e koe hei tiaki i a koe anō:

  • Me mau tonu he kāri tuakiri, he poroporo/heihei whakatūpato hauora rānei. Mā tēnei ka mōhio ngā kaimahi hauora kei a koe te mate a Addison mēnā ka ngaro tō mārama i roto i tētahi āhuatanga ohorere.
  • Kōrero ki tō tākuta mō te pupuri i tētahi werohanga cortisol mēnā ka puta he āhuatanga ohorere. Me whakaako hoki tētahi mema o te whānau, tētahi whanaunga rānei ki te pēhea te hoatu i te werohanga ki a koe.
  • Pātai atu ki tō tākuta me aha koe ina pāngia koe e te mate, ina pāngia rānei koe e te ahotea nui. I roto i ēnei āhuatanga, me whakarerekē pea te horopeta o tō rongoā.
  • Me haere tonu ki te kite i tō tākuta.

He mea whakapouri te hinengaro mēnā kei a koe tētahi mate mau tonu. Engari ko te rongo pai, he tino pai te whakahaere i te mate a Addison mā te rongoā. Ko te mea nui ko te noho tonu ki te whakapā atu ki tō tākuta me te whiwhi i te maimoatanga e hiahiatia ana e koe.

Karere Tangohia ki te Kāinga

  • Ko te mate a Addison he āhuatanga e kore ai e nui te whakaputa a ngā repe adrenal i ngā homoni cortisol me te aldosterone.
  • Ko ngā tohu matua ko te ngenge mau tonu, kāore he take e kitea ana, te pōuri o te kiri me ngā kapia, me te hiahia nui ki ngā kai tote.
  • He āhuatanga ohorere e morearea ana te "raruraru Addisonian" e hiahia ana kia rongoatia tonutia.
  • Ko te maimoatanga he tango i ngā pire homoni iti te horopeta mō te oranga katoa.
  • Mā te maimoatanga tika, ka taea e koe te noho i tētahi oranga noa me te hauora, engari he mea nui kia mau tonu tō whakapā atu ki tō tākuta.
  • Mena kei a koe tēnei mate, he mea tino nui kia mau tonu he kāri whakatūpato hauora, he poroporo rānei, me te whai mahere āwhina mō tō haumaru.

Te Mate a Addison, ngā repe adrenal, cortisol, aldosterone, te mate pūnaha ārai mate, te pōuri o te kiri, te ngenge mau tonu, ngā homoni, hydrocortisone, fludrocortisone, te ngoikore o te adrenal
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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