Kei te ngenge tonu koe, kei te ahua kore ora, ā, kei te huri haere te tae o tō kiri? Tērā pea he hiahia nui tōu ki te tote. He maha ngā wā ka warewarehia e tātou ēnei tohu, he mea noa iho. Heoi, he tohu pea ēnei mō tētahi mate i roto i tō tātou tinana kāore i te tino kitea, engari he mea tino nui kia tautuhia tika. I tēnei rā kei te kōrero tātou mō tētahi mate onge, engari ki te whakahaeretia tika, ka taea e koe te noho noa. Ko te Mate a Addison tēnā .
He aha te mate a Addison?
Āe, me whakamārama noa iho tēnei. E rua ā tātou repe iti, he tapatoru te āhua, he rite ki te pōtae, kei runga ake i ō tātou whatukuhu. Ka kiia ēnei e tātou ko ngā repe adrenal . He wāhanga tino nui ēnei o tō tātou pūnaha endocrine.
Ko te mate a Addison he āhuatanga e kore ai e nui te whakaputa a ngā repe adrenal i ngā homoni matua e rua, arā, te cortisol me te aldosterone .
He aha ngā take e hiahiatia ai ēnei homoni e rua?
- Cortisol: He homoni tēnei e tino hiahiatia ana mō te ora. Ka āwhina i ō tātou tinana ki te aro atu ki te ahotea, pērā i te wā e mate ana tātou, e pāngia ana e te aituā, e pokanga rānei. Ka āwhina hoki ki te whakahaere i te toto toto, te tere o te manawa, te mahi a te pūnaha ārai mate, me ngā taumata huka toto.
- Aldosterone: Ka āwhina tēnei homoni ki te whakataurite i ngā kohuke konutai (tote) me te pāhare pākawa i roto i ō tātou tinana. Ka whakahaere hoki i te nui o te wai ka tukuna e ō tātou whatukuhu hei mimi. Ka pā tika hoki tēnei ki tō tātou toto toto.
E mōhiotia ana hoki te mate a Addison ko te koretake o te adrenal tuatahi . Tērā tētahi atu āhuatanga e pā ana, e kiia ana ko te koretake o te adrenal tuarua . I roto i tēnei āhuatanga, kāore te repe pituitary i roto i te roro e tuku i te nui o te homoni ACTH , e whakaoho ana i ngā repe adrenal ki te whakaputa cortisol. Engari i tēnei rā ka kōrerohia te raruraru e puta ana i roto i ngā repe adrenal tonu.
Te rerekētanga i waenga i te mate a Addison me te mate a Cushing
Tērā pea ka pōhēhē koe i ēnei ingoa e rua. He rerekē rawa ngā āhuatanga o ēnei e rua.
| Āhuatanga | Te Mate a Addison | Te Mate o Cushing |
|---|---|---|
| Raru matua | Kāore i te rawaka te cortisol (me te aldosterone) i roto i te tinana. | Te pikinga o te cortisol i roto i te tinana (Hypercortisolism). |
| Ngā āhuatanga noa | Te whakahekenga taumaha, te pouri o te kiri, te toto toto iti. | Te taumaha haere, te mata porotaka, te toto toto tiketike. |
Ko wai te hunga tino tūpono ka pāngia e tēnei mate? He pēhea te noa o tōna pānga?
Ahakoa ka pāngia te tangata o ngā tau katoa e te mate a Addison, he mea noa iho tēnei i waenga i te 30 me te 50 tau te pakeke .
He tino onge tēnei mate . Hei tauira, i Amerika, tata ki te kotahi i roto i te kotahi rau mano tāngata ka pāngia e tēnei mate. Engari he tokomaha anō hoki e pāngia ana e tēnei mate i tō tātou whenua.
He nui ake te tūponotanga o te hunga ki te pāngia e tēnei mate. Ko rātou ēnei he hunga kei a rātou ētahi atu mate pūnaha ārai mate . Arā, ko ngā mate e whakaekea ai e te pūnaha ārai mate o tō tātou tinana ō tātou ake pūtau. Mena kei a tātou ēnei mate, ka nui ake te tūponotanga ki te pāngia e te mate a Addison.
- Mate huka momo I
- Te mate toto kino
- Te mate o Graves
- Te mate tairoiti mau tonu
- Vitiligo - he mā ngā ira i runga i te kiri
- Te mate pāwera
He aha ngā tohu o te mate a Addison?
I roto i te mate a Addison, he maha ngā wā ka tino puhoi te pakaru o ngā repe adrenal, i roto i te wā. Nō reira, ka āta puta ngā tohu. Ka rerekē pea ēnei tohu i ia tangata, i ia tangata.
| Ngā tohu noa e puta haere ana | |
|---|---|
| Ko te āhuatanga tino noa | Ka piki haere te ngenge me te ngenge mau tonu , kāore e taea te whakamārama. |
| Ngā huringa kiri | Te tae parauri/mangu o te kiri, inā koa ki ngā wāhi he koha, he whāriki kiri (pērā i ngā kēkē, i te hope), me ngā kapia (Hyperpigmentation). |
| Pūnaha nakunaku | Mamae puku, whakapairuaki, ruaki, korere, kore hiahia kai, me te ngaronga taumaha. |
| Ētahi atu āhuatanga | Mamae uaua me ngā hononga, matewai, whanoke ina tū (nā te toto toto iti), riri, pouri, hiahia nui ki te tote, me te huka toto iti (hypoglycemia). |
Tērā pea ka pāngia ngā wāhine e ngā tohu pēnei i te paheketanga koretake, te ngaronga o te huruhuru o te tinana, me te hekenga o te hiahia moepuku.
Āhuatanga ohorere e hiahia ana kia arohia: Te raruraru o Addisonian
I ētahi wā, inā koa i muri i te mate kino, i te aituā, i te ahotea nui rānei, ka taea e ēnei tohu te huri ohorere hei tino kino. Ka kiia tēnei he Addisonian Crisis , he acute adrenal failure rānei. He āhuatanga ohorere hauora tēnei e hiahia ana kia rongoatia tonutia, ā, ka taea hoki te whakararu i te ora!
Ngā tohu o te raruraru Addisonian:
- He ngoikore whakaharahara, kāore e taea te whakamanawanui.
- Te mamae ohorere, te mamae nui i te tuara o raro, i te puku, i ngā waewae rānei.
- Ngā huringa hinengaro pērā i te manukanuka, te pōhēhē, me te mataku.
- Te ruaki nui me te korere (ka tere pea te matewai).
- Te hekenga o te toto toto ki raro rawa.
- Te ngaronga o te māramatanga.
Ki te pāngia koe, tētahi atu rānei e mōhiotia ana e koe, me kawe tonu atu ki te Tari Ohotata (ETU) o te hōhipera tata.
He aha ngā take o te mate a Addison?
Ko te tino take o te mate a Addison ko te urupare ārai mate.. He whakarāpopototanga noa iho, ka whakaekea e tō tātou ake pūnaha ārai mate (pūnaha ārai mate) te wāhanga o waho o ō tātou ake repe adrenal (te cortex adrenal) me te whakangaro i aua repe. Kāore anō kia mōhiotia te take tuturu o tēnei. Ka tīmata ngā tohumate te puta i muri i te whakangaromanga o te 90% o ēnei repe. Ka roa pea tēnei i ngā marama, i ngā tau rānei.
Koinei te take o te 75% o ngā tūroro a Addison.
Ētahi atu take onge:
- Te mate kohi: He tino take tēnei i ngā wā o mua. He tino take tonu i ngā whenua whakawhanake.
- Ngā mate urutā: Ngā mate e pā ana ki te HIV/AIDS me ngā mate harore.
- Matepukupuku: Te horapa o ngā pūtau matepukupuku mai i ētahi atu wāhi ki ngā repe adrenal.
- Te toto ki roto i ngā repe adrenal.
- Te tango pokanga i ngā repe adrenal.
- Amyloidosis: He mate e kohia ai tētahi momo pūmua i roto i ngā whekau, ā, ka pakaru ai.
Me pēhea te tautuhi i tēnei mate? (Tautuhinga)
Nā te mea he puhoi rawa te puta mai o ngā tohu, ā, he mea noa ki te maha atu o ngā mate, he uaua ki te tautuhi i te mate a Addison i ngā wāhanga tōmua. He maha ngā wā, ka kitea "tūpono noa" te mate. Ka whakapae pea ngā tākuta i tēnei mena ka kitea e rātou he iti te konutai me te nui o te pāhare pāporo i roto i te toto i te wā o te whakamātautau toto mō tētahi atu mate. Waihoki, ko te whero o te kiri he tohu nui e arahi ana ki te whakapae kei te pāngia koe e tēnei mate.
Mena kei te whakapae tō tākuta kei te pāngia koe e tēnei mate nā ō tohumate, ka tonoa e ia ētahi atu whakamātautau hei whakaū i te mate.
Ngā whakamātautau tātaritanga:
- Ngā whakamātautau toto: Ka inehia e ngā whakamātautau toto ngā taumata o te konutai, te pāhare pāporo, te cortisol, me ngā homoni ACTH. I roto i te mate a Addison, he iti te cortisol, he teitei ngā taumata ACTH.
- Whakamātautau whakaohooho ACTH: Koinei te whakamātautau matua hei whakaū i te mate. I roto i tēnei whakamātautau, ka werohia te homoni ACTH hangai, ā, ka inehia te taumata cortisol i roto i tō toto i te haora i muri mai. Mena kei te ora ō repe adrenal, me piki ake tō taumata cortisol. Heoi, ki te kore, ka whakaū kāore ō repe adrenal e mahi tika ana.
- Whakamātautau huka toto i puta mai i te insulin: Ka mahia tēnei whakamātautau hei kimi mēnā he raruraru kei te repe pituitary te take o ō tohumate.
- Matawai CT: Tērā pea ka mahia he matawai CT hei tirotiro mēnā kua pakaru, kua pangia, kua whakaitihia rānei te rahi o ō repe adrenal.
Me pēhea te rongoā?
Ko te tikanga matua mō te rongoā i te mate a Addison ko,Ko te Whakaora Whakakapinga Homoni (HRT) he tukanga whakakapi i ngā homoni ngoikore o te tinana mā te whakamahi i ngā pire hangai.
Nā te mea he mate mau tonu tēnei, me tango e koe tēnei rongoā mō te toenga o tō oranga .
- Ka hoatu he rongoā e kīia ana ko te hydrocortisone hei whakakapi mō te homoni cortisol .
- Ka hoatu he rongoā e kīia ana ko te fludrocortisone hei utu mō te homoni aldosterone .
He rerekē te horopeta o ēnei rongoā i ia tangata, i ia tangata. Waihoki, ka whakanuia pea e tō tākuta tō horopeta mō te wā poto hei ārai i te mate urutā Addisonian mēnā ka pāngia koe e tētahi āhuatanga taumaha, pērā i te mate pāwera, te aituā, te pokanga rānei.
Mena kei te tango koe i te fludrocortisone, ka tohutohu tō tākuta kia tāpirihia he tote anō ki tō kai, inā koa i te wā wera, werawera, me muri i te whakakori tinana kaha.
Te noho tahi me te mate me te aha me mahi
Mā te maimoatanga tika, ka taea e te tangata whai mate a Addison te ora i te oranga noa, hauora hoki . Heoi, he mea tino nui kia mau tonu te horopeta tika o te rongoā.
Mena he nui rawa te horopeta o te rongoā, ka puta pea ngā pānga taha pēnei i te momona, te mate huka momo 2, te osteoporosis, me te toto toto tiketike. Nō reira, he mea nui kia toro atu koe ki tō tākuta (he endocrinologist) i ia wā, kia whai whakamātautau hoki hei pupuri i te horopeta tika o te rongoā.
Ngā mea me mahi e koe hei tiaki i a koe anō:
- Me mau tonu he kāri tuakiri, he poroporo/heihei whakatūpato hauora rānei. Mā tēnei ka mōhio ngā kaimahi hauora kei a koe te mate a Addison mēnā ka ngaro tō mārama i roto i tētahi āhuatanga ohorere.
- Kōrero ki tō tākuta mō te pupuri i tētahi werohanga cortisol mēnā ka puta he āhuatanga ohorere. Me whakaako hoki tētahi mema o te whānau, tētahi whanaunga rānei ki te pēhea te hoatu i te werohanga ki a koe.
- Pātai atu ki tō tākuta me aha koe ina pāngia koe e te mate, ina pāngia rānei koe e te ahotea nui. I roto i ēnei āhuatanga, me whakarerekē pea te horopeta o tō rongoā.
- Me haere tonu ki te kite i tō tākuta.
He mea whakapouri te hinengaro mēnā kei a koe tētahi mate mau tonu. Engari ko te rongo pai, he tino pai te whakahaere i te mate a Addison mā te rongoā. Ko te mea nui ko te noho tonu ki te whakapā atu ki tō tākuta me te whiwhi i te maimoatanga e hiahiatia ana e koe.
Karere Tangohia ki te Kāinga
- Ko te mate a Addison he āhuatanga e kore ai e nui te whakaputa a ngā repe adrenal i ngā homoni cortisol me te aldosterone.
- Ko ngā tohu matua ko te ngenge mau tonu, kāore he take e kitea ana, te pōuri o te kiri me ngā kapia, me te hiahia nui ki ngā kai tote.
- He āhuatanga ohorere e morearea ana te "raruraru Addisonian" e hiahia ana kia rongoatia tonutia.
- Ko te maimoatanga he tango i ngā pire homoni iti te horopeta mō te oranga katoa.
- Mā te maimoatanga tika, ka taea e koe te noho i tētahi oranga noa me te hauora, engari he mea nui kia mau tonu tō whakapā atu ki tō tākuta.
- Mena kei a koe tēnei mate, he mea tino nui kia mau tonu he kāri whakatūpato hauora, he poroporo rānei, me te whai mahere āwhina mō tō haumaru.

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