Kua rongo, kua kite rānei koe i tētahi āhuatanga i heke ohorere ai te nui o te toto i roto i tētahi tangata—ina koa he tamaiti nohinohi—ka waiho ia kia ngenge, ā, i ētahi wā, ka tūtaki ki tētahi āhuatanga ohorere e morearea ana ki te ora? Koinei tonu te mea e kōrerohia ana e mātou i konei: te Aplastic Crisis . Ahakoa te ahua whakamataku o te ingoa, ko te mārama ki tēnei āhuatanga ko tāu taahiraa tuatahi ki te whakahaere tika i a ia me te whakarite kia tiakina wawe. I Nirogi Lanka, kei konei mātou hei ārahi i a koe i roto i ngā mea e hiahia ana koe kia mōhio ai koe kia noho rite ai.
He aha tonu te Aplastic Crisis?
I roto i ngā kupu māmā noa iho, ka puta te Aplastic Crisis ina mutu ohorere te hanga toto whero hou i roto i tō hinu wheua . Tērā pea ka whakaaro koe, "He aha te take o tēnei?" Āe, ko ngā toto whero ngā kaikawe nui o te hāora puta noa i tō tinana. Ina mutu tā rātou hanga, ka heke te maha o ngā toto whero, ka hua ake he anemia kino . He mate kino tēnei ka taea te whakararu i te ora.
Ko te tikanga, ko te mate aplastic ka pā ki ngā tāngata whai mate toto, pērā i te Sickle Cell Anemia . Ko te nuinga o te wā ka puta mai i te Parvovirus B19 , he mate huaketo noa. Ahakoa he maha ngā tāngata ka pangia e tēnei huaketo me te kore he raruraru nui, he mōrearea nui ki te hunga whai mate toto kua pāngia e ia. He maha ngā wā ka kitea i roto i ngā tamariki, inā koa ngā pēpi. Heoi, he rongo pai: kei Nirogi Lanka me ētahi atu pokapū hauora ngā maimoatanga whai hua, tae atu ki ngā whakawhiti toto me te rongoā Intravenous Immunoglobulin (IVIG) .
He āhuatanga noa tēnei mō te katoa?
Kāore rawa. E ai ki te kōrero, he tino noa te Parvovirus B19 , engari kāore e puta he raruraru aplastic i roto i te nuinga o te tangata. Ko te hunga kua ora kē me te mate toto mau tonu ka pāngia e te nuinga.
Ko ngā pēpi me ngā tamariki e pāngia ana e te mate toto toto Sickle te hunga tino mōrearea. Hei tāpiri, ki te mea kei a koe ētahi atu āhuatanga e puta ai te mate toto toto hemolytic (te wā e whakangaromia ai ngā toto toto whero i te wā e tika ana), ka nui ake tō mōrearea mēnā ka pāngia koe e te Parvovirus B19. Kei roto i ēnei ko:
- Te Spherocytosis Tuku Iho
- Te mate Hemoglobin C
- Te mate tākihi
- Te mate ngoikore o te G6PD
- Te korenga o te Pyruvate Kinase
- Te mate toto toto ā-tinana
- Hemoglobinuria Pō Pākiki
- Te Elliptocytosis Tuku Iho
Mena kei a koe, kei tāu tamaiti rānei tētahi o ēnei mate toto, he mea nui kia noho mataara tonu koe ki ēnei tohu.
He aha ngā tohu o te Aplastic Crisis?
Mō ngā pakeke me ngā tamariki, ka puta te raruraru aplastic mā roto i ngā tohu e pā ana ki te anemia nui. Tērā pea ka puta he āhua pōrearea, he āhua pukuriri rānei ngā pēpi me ngā tamariki nohinohi. Ki te kite koe i tāu tamaiti e tangi ana, e kore e taea te whakamarie, e āhua ohorere ana rānei, he tohu whakatūpato pea tēnei.
Ko ngā tohu matua ko:
- Ngenge: Te ngenge me te kore kaha ki te mahi i ngā mahi o ia rā.
- Kirika: Ka piki te pāmahana tinana ki te 38°C (101°F) neke atu rānei.
- Whatiwhati: Te māhunga pōuri, te pōturi rānei mō ngā wā maha.
- Te poto o te manawa (dyspnea): Te korenga o te manawa i te wā e mahi ana i ngā mahi māmā, e piki arawhata rānei.
- Te tere o te ngakau, te koretake rānei o te manawa: Tērā pea ka rite tō ngakau ki te tere, ki te pekepeke rānei o ngā pao.
- Te kiri mā: He āhua mā rawa te āhua o tō kiri, ngutu, kapia, ngā moenga maikuku rānei.
Mena ka kitea e koe, e tāu tamaiti rānei tētahi o ēnei tohu—ina koa mēnā he mate toto tōu— me rapu tonu i te awhina hauora i te tari whawhati tata.
He aha i puta ai te Aplastic Crisis?
Ko te kupu "aplastic" e tohu ana i te mutunga o te tipu, te whakaputa rānei. I te wā o te raruraru aplastic, ka kore e taea e tō hinu wheua te whakaputa i ngā toto whero hauora. Ko te take, ko te Parvovirus B19 , ka whai i ngā toto whero kāore anō kia pakari, ka kino hoki. Nā te mea ko tō hinu wheua te kawenga mō te whakaputa tonu i ngā toto whero, ka mutu te "wheketere toto" o tō tinana, ka puta he anemia kino .
He aha ngā raruraru pea ka pā mai i tēnei mate?
Ka taea e te raruraru aplastic te whakararu i ngā raruraru nui, inā koa mō te hunga e pāngia ana e te mate toto pūtau hāripiri . He kino ēnei raruraru, ā, me rapu wawe i te awhina hauora.
- Te raruraru Vaso-occlusive roa (VOC): Ko te VOC he wā mamae ohorere, nui hoki e pāngia ana e te hunga e pāngia ana e te anemia pūtau mariao. Ka taea e te raruraru aplastic te whakaroa i tēnei mamae.
- Myocarditis: E pā ana tēnei ki te mumura o te uaua o te ngākau, ka pupuhi pea, ka ngoikore hoki te mahi a te ngākau.
- Te aukati i te whēkau: Ka puta tēnei ina mau ngā pūtau toto whero rerekē ki roto i te whēkau, ka tere ai te whakanui.
- Glomerulonephritis: He mate tēnei e pā ana ki ngā whatukuhu. Ki te kore e rongoatia, ka arahi pea ki te mate whatukuhu mau tonu, ki te ngoikore rānei o te whatukuhu.
Koia mātou e whakanui ana i te mea he mea nui te noho mataara me te aroturuki i tō hauora.
Me pēhea te tautuhi a ngā tākuta i tēnei mate?
Ina puta mai ngā tohu āwangawanga ki a koe, ki tāu tamaiti rānei, ka tangohia e tō tākuta he hītori hauora taipitopito, ā, ka whakahaerehia he whakamātautau tinana. Hei whakaū i te mate, ka tonoa pea e rātou ētahi whakamātautau:
- Tatau Toto Katoa (CBC): Ka ine tēnei i ō taumata o ngā toto whero, ngā toto mā, me ngā pereti toto. I roto i te mate pukupuku toto, he tino iti te maha o ngā toto whero.
- Te maha o ngā retikulosit: Ko ngā retikulosit he toto whero kāore anō kia pakari. Mā tēnei whakamātautau ka kitea te kaha o te whakaputa a tō hinu wheua i ngā toto whero hou. I te wā o te mate aplastic, he tino iti hoki tēnei maha.
- Whakamātautau Parvovirus B19: Mā tēnei whakamātautau toto ka whakaū mēnā kei a koe te mate Parvovirus B19 o nāianei, o nā tata nei rānei.
Mā ēnei hua, ka taea e tō tākuta te whakatau tika mēnā kei te pāngia koe e te Aplastic Crisis, e tētahi atu raruraru hauora rānei.
He aha ngā kōwhiringa maimoatanga?
Ko te rongoā matua mō te Aplastic Crisis ko te whakawhiti toto . Mā tēnei ka whakaratohia he toto whero hauora, tere tonu hei whakakapi i ngā mea kāore e taea e tō tinana te whakaputa i tēnei wā. Hei tāpiri, ka taea te tuku tika i te rongoā Intravenous Immunoglobulin (IVIG) mā roto i te uaua.
Ka ora te nuinga o ngā tūroro i roto i ngā rā 10 ki te 14 i muri i te tīmatanga o te maimoatanga. Ko tētahi āhuatanga pai ko te mea ina pangia koe e te Parvovirus B19, ka whakawhanakehia e tō tinana te ārai mate mō te wā katoa, ka whakaitihia te tūponotanga o ngā raruraru aplastic a muri ake nei e puta mai ana i tēnei huaketo.
Ka taea te ārai i te Aplastic Crisis?
He uaua ki te ārai katoa, nā te mea ka puta he raruraru aplastic ina pangia te tangata he mate toto kē tōna e te Parvovirus B19 . He huaketo tino noa tēnei, ā, kāore anō kia kitea he kano ārai mate mōna.
Heoi, ki te mea kei a koe, kei tāu tamaiti rānei te mate toto hāripiri , he mate toto rite rānei, kōrero ki tō tākuta mō ngā rautaki tiaki. Mā ngā mahi ngāwari pēnei i te karo i ngā wāhi kī tonu i te tangata i te wā o te pakarutanga me te pupuri i te akuaku pai o ngā ringa ka āwhina i te whakaiti i tō tuponotanga whānui ki te pangia.
He aha te āhua o te oranga i muri i tēnei āhuatanga?
Ko te matapae e pā ana ki te āhua o tō mate. Ko te hunga e pāngia ana e te Aplastic Crisis ka ora pai i roto i ngā rā 10 ki te 14 i muri i te tīmatanga o te wawaotanga hauora. Ahakoa he ngāwari pea ētahi tāngata ki te hoki mai anō, he mea nui te noho mataara ki ō tohumate me te whai i te mahere tiaki roa a tō tākuta i Nirogi Lanka mō tō oranga tonutanga.
Me pēhea taku tiaki i ahau anō, i taku tamaiti rānei?
Ko te Aplastic Crisis tētahi o ngā raruraru maha e pā ana ki ngā mate toto pērā i te Sickle Cell Anemia . Ahakoa kāore pea e taea e koe te ārai i te huaketo i ngā wā katoa, ka taea e koe te tautoko i tō hauora whānui:
- Me tirotiro hauora i ia wā: Mā te whakarite i ngā wā hui ki tō tīma hauora i Nirogi Lanka ka taea te kite wawe i ngā raruraru pea.
- Whakaitihia te mōrearea o te mate: Kōrerohia ngā rautaki me tō tākuta hei tiaki i a koe mai i ngā mate urutā pēnei i te rewharewha, te makariri rānei.
- Kai i tētahi kai hauora, taurite hoki: Whakaritea ngā kai totika hei kai matua, ā, kia mau tonu tō wai mā te inu i te 8–10 karāhe wai ia rā.
- Whakakorikori tinana mārie: Mā te whakakorikori tinana auau ka pai ake te wairua me te hauora whānui. Whakarongo ki tō tinana, okioki ina ngenge koe, ā, kia nui te wai.
Ka whakapakari ēnei tikanga i tō pūnaha ārai mate, ā, ka whai wāhi hoki ki tō hauora whānui.
Āhea ahau me toro atu ki te tākuta?
He āhuatanga ohorere hauora te Aplastic Crisis.
Mena kei a koe, kei tāu tamaiti rānei te mate toto toto iti , rapua tonutia te awhina hauora mena ka pāngia koe e te ngenge ohorere, te ngoikore nui, te ngoikore nui, tetahi atu tohu whakamataku rānei. Kaua e whakaroa; he mea nui te maimoatanga tere mo te whakaoranga haumaru. Mena e tika ana, haere ki te ruma urupare tata, waea atu rānei ki te 911.
He aha ngā pātai me pātai atu e au ki taku tākuta?
Mena ka pāngia koe, tāu tamaiti rānei e te Aplastic Crisis, he mea nui kia kōrero tuwhera koe ki tō rōpū hauora. Anei ētahi pātai matua ka hiahia pea koe ki te pātai:
- Āhea ahau/taku tamaiti e tumanako ai kia ora?
- He aha te tūponotanga ka puta anō tēnei?
- He aha ngā mahi whakatūpato motuhake hei mahi māku i a au e whakahaere ana i tēnei āhuatanga?
He mea nui te pātai i ēnei pātai hei whakamama i ō āwangawanga, hei pupuri hoki i tō mōhiotanga ki tō mahere tiaki.
He rite tonu te Aplastic Crisis me te Aplastic Anemia?
Ahakoa he hekenga o te maha o ngā toto toto whero i roto i ēnei āhuatanga e rua, he rerekē tonu ngā take hauora.
Ko te Aplastic Crisis e pā ana ki te aukati ohorere me te wā poto o te hanga o ngā toto toto whero.
He mate mau tonu te mate toto koretake (Aplastic Anemia) e puta ake ana i roto i te wā, e pā pinepine ana ki ngā momo toto katoa—tae atu ki ngā toto toto mā me ngā pereti toto—ehara i te mea ko ngā toto toto whero anake.
I te kīanga māmā noa, he āhuatanga ohorere poto te Aplastic Crisis, engari he āhuatanga roa te Aplastic Anemia e ahu mai ana i te hinu wheua.
Ngā Kaupapa Matua māu
Ko te tumanako ka mārama ake koe i tēnei tirohanga whānui mō te Aplastic Crisis. He raruraru nui tēnei ka pā ki ngā tāngata whai mate toto pēnei i te Sickle Cell Anemia . Ka puta tēnei ina mutu ohorere te hanga o ngā pūtau toto whero i roto i te hinu wheua, ka hua ake he anemia kino, ka morearea pea ki te ora.
Nā te tere o te puta mai o ngā tohu, ka tino pāngia pea koe e te mamae. Heoi, ka taea e ngā tohunga hauora te whakahaere i tēnei mā te whakawhiti toto me te tiaki tika.
Mena kei roto koe, tāu tamaiti rānei i te mōrearea, kōrerohia ngā tohu whakatūpato ki tō tākuta. Ahakoa kāore pea e taea e koe te ārai i te Aplastic Crisis i ngā wā katoa, he mea nui te mōhio ki te aha me mahi me te wā e rapu ai i te āwhina ohorere (911). Ko te whakarite whai whakaaro te parepare pai rawa atu māu.
👩🏽⚕️ Ngā Pātai Auau (FAQs)
💬 He aha te Āhuatanga Aplastic?
Ko tō tātou hinu wheua te kawenga mō te whakaputa i ngā toto whero. Ka puta te Aplastic Crisis ina mutu ohorere te whakaputanga o te hinu wheua mō ētahi rā, he maha ngā wā ka puta mai i te mate huaketo (pērā i te Parvovirus B19).
💬 He aha te mea ka pā ki te tūroro i tēnei hinganga ohorere?
I te mea kei te kawe ngā toto toto whero i te hāora puta noa i tō tinana, ka puta he mate toto nui mēnā ka heke ohorere. Tērā pea ka kite koe i te kiri mā, i ngā ngutu, i ngā moenga maikuku, ka piki ake te tere o te manawa, ka uaua te manawa, ka hemo rānei.
💬 Me pēhea te rongoā i tēnei, inā koa mō ngā tamariki?
He mea tino nui tēnei mō ngā tamariki e pāngia ana e te Mate Pūtau Hāri. Mena kei te hōhipera, ka tukuna e ngā tākuta he whakawhiti toto hei whakaū i te tūroro. I te nuinga o te wā, ka tīmata te hinu wheua ki te hoki anō ki te mahi noa i roto i ngā rā 10 ki te 14 i muri i te maimoatanga.
Te Mate Pāpaka o Nirogi Lanka , Ngā Pūtau Toto Whero, Te Huka Wheua, Te Korekore o te Tinana, Te Parvovirus B19, Te Korekore o te Tinana
