Kua rahi ake ō maikuku, kua rerekē rānei ō maikuku? Me ako tātou mō tēnei Hypertrophic Osteoarthropathy!

Kua kite koe i te rahi rawa o ō matimati, o ō maihao rānei, ā, kua piko iho ō whao, kua rerekē rānei te āhua? I ētahi wā, kāore tātou e aro nui ki ēnei. Heoi, ki te kite koe i ēnei tohu, he tohu pea tēnei nō tētahi mate e kiia nei ko te 'Hypertrophic Osteoarthropathy' . E kiia ana hoki tēnei ko te HOA. Ehara i te mea tino morearea te mate, engari me rongoā pea ētahi atu mate e puta ai tēnei mate. Nō reira, me kōrero taipitopito tātou mō tēnei HOA, kia nui ake ai te ako.

He aha te osteoarthropathy hypertrophic (HOA)?

Ki te whakarapopoto, ko te hypertrophic osteoarthropathy (HOA) he āhuatanga e pupuhi ai , e porotaka ai ngā pito o ō maihao, o ō matimati rānei (e pupuhi ana te kiri, e porotaka ana te waewae) me ngā panonitanga ki ō maikuku. Tērā pea ka:

• Ka nui haere, ka pupuhi hoki ngā pito o ngā maihao me ngā matimati .
• Ka piko ngā whao ki raro, ka puta he āhua piko, me te mea kua hutia ake.

Ka tīmata pea te HOA i ētahi wā i te tamarikitanga, i te taiohitanga rānei. Mō ētahi tāngata, ka taea hoki te whanake i muri mai i te ao. Ahakoa kāore te HOA i te kino, ki te mea he mate kei raro i te pūtake, he mea nui kia rongoātia.

He aha ngā momo matua o tēnei?

E rua ngā momo matua o ngā HOA:

1. Te Osteoarthropathy Hypertrophic Primary (PHO): He momo ira tēnei, arā, ka taea te tuku iho mai i ngā mātua ki ngā tamariki.

2. Te Osteoarthropathy Hypertrophic Tuarua (SHO): Ka puta tēnei momo mai i ngā mate mau tonu pērā i te mate manawa me te mate pūkahukahu. He maha ngā wā ka iti te taumata hāora i roto i ō toto i ēnei mate.

Ko wai te mea ka nui ake te tūponotanga ka pāngia e tēnei mate?

Ina hoki, ka taea e te tangata katoa, ahakoa te ira tangata, te iwi rānei, te whakawhanake i tēnei āhuatanga e kiia nei ko te hypertrophic osteoarthropathy.

Heoi, ko te HOA tuatahi (PHO) ka puta i roto i te tau tuatahi o te oranga, i te wā taiohi rānei. Āhuatanga PHO:

• He mea noa ake i waenga i te hunga mangu.
• He nui ake te kitea o tēnei i roto i ngā tāne.

Ko te HOA Tuarua (SHO) he mate e kitea nuitia ana i roto i te hunga i waenga i te 55 me te 75 tau te pakeke.

E hia te auau o tēnei āhuatanga?

Kāore e taea e ngā kairangahau te kī tika i te tokomaha o ngā tāngata he HOA. Engari e mōhiotia ana kei waenganui i te 95% me te 97% o ngā tāngata he HOA kei a rātou te momo tuarua (SHO) . Ko te tikanga o tēnei, ko te nuinga o ngā tāngata he rerekētanga maihao nā tētahi atu āhuatanga.

He aha i whakatūria ai tēnei HOA? He aha ngā take?

Kia tirohia tātou he aha te take o tēnei.

Ngā Take mō te HOA Matua (PHO)

Nā ngā whakarerekētanga ira e kitea ana i te whānautanga mai tēnei. Tērā pea ka riro i te tamaiti tēnei whakarerekētanga ira mai i te whaea, i te pāpā, i ngā mea e rua rānei.

Ngā take mō te HOA tuarua (SHO)

Ko te tino take o te HOA tuarua (SHO) ko te mate pūkahukahu . Mēnā ka puta mai tēnei āhuatanga i te mate pūkahukahu, ka kiia ko te Hypertrophic Pulmonary Osteoarthropathy (HPOA) .

Ko te mate pūkahukahu matua ka puta ai te HPOA ko te mate pukupuku pūkahukahu , inā koa ko te mate pukupuku pūkahukahu kore-pūtau iti . Hei tāpiri, ko ētahi atu mate pūkahukahu ka puta ai te HPOA ko:

• Ngā pukupuku muka pai o te pleura
• Ngā mate pūkahukahu mau tonu
• Te Pūnaha Matū (he mate ira e pā ana ki te pūnaha manawa)
• Mesothelioma (matepukupuku o te arai o ngā pukahukahu)
• Te mate pukupuku kua horapa mai i ētahi atu wāhi, ā, kua pā ki ngā pukahukahu (Te mate pukahukahu metastatic)
• Te āhua rerekē o ngā oko toto i roto i ngā pukahukahu (te āhua rerekē o te hanganga o ngā oko toto i roto i ngā pukahukahu)
• Te mate kohi pūkahukahu
• Sarcoidosis (he putunga pūtau i roto i ngā wāhanga rerekē o te tinana)

Tērā atu anō ngā āhuatanga ka pā ki te HOA tuarua (SHO):

• Ngā mate o te ate, te au, me te pūkahukahu (ngā mate hepatobiliary):
• Te Ārai i te Paipa Au (Te Ārai i te Paipa Au i roto i ngā Tamariki)
• Matepukupuku
• Te mate ate
• Te Cholangitis Biliary Tuatahi
• Te mate a Wilson (te kohikohinga o te parahi i roto i te tinana)
• Ngā mate o te ngākau:
• Ko te myxoma atrial (he pukupuku kore-matepukupuku e puta ana i roto i te ngākau)
• Te Mate Ngākau Kirinotika (te mate ngākau e heke ai te hāora i roto i te toto)
• Te mate o te arai o roto o te ngākau (Infective Endocarditis)
• Ngā āhuatanga o te puku:
• Te whakamahi kino i ngā rongoā whakamāmā
• Achalasia (he raruraru ki te mahi a te sphincter esophageal)
• Matepukupuku
• Te Polyposis Adenomatous Familial (ngā tipu iti i roto i te whekau nui)
• Mate Puku Mumura

Haunga tēnei, he maha atu anō ngā āhuatanga ka puta ai te SHO:

• Mate Celiac (mate pāwera ki te kuruteni)
• Ngā mate puku pērā i te mate korere
• Te mate o Graves (hyperthyroidism)
• Te mate taiaki toto nui
• Myelofibrosis (he mate o te hinu wheua)
• Te mate POEMS
• Thymoma (he pukupuku o te repe thymus)

Whakaarohia, kua roa te maremare o tētahi e mōhiotia ana e koe, ā, kua rerekē haere ōna maihao pēnei, ā, i muri i tana kitenga i tētahi tākuta ka kitea he raruraru pūkahukahu. Nō reira, he mea nui kia aro atu ki ēnei tohu.

He aha ngā tohu o te HOA?

Ko te tohu matua o te HOA ko te pupuhi, te pākia rānei o ngā pito o ngā maihao, o ngā matimati rānei. He rite tonu te pānga o tēnei ki ngā taha e rua o te tinana. Tērā pea ka kite koe i ēnei mea:

• He pupuhi, he porotaka hoki ngā pito o ngā maihao me ngā matimati.
• Kei te ngaro haere ngā kita o ngā hononga e tata ana ki ngā pito o ngā matimati.
• He piko ngā whao ki raro , ā, te āhua nei e mānu ana.
• Ka kanapa, ka angiangi te kiri i te pūtake o te maikuku.
• Ka ngawari ngā whao.
• He whero ngā pito o ngā maihao me ngā matimati, ā, he mahana te āhua .

Ko ētahi atu āhuatanga HOA ka kitea e koe ko:

• Te whakanui ake i te repe. Ka puta pea ngā āhuatanga pēnei i te hakihaki, te werawera nui (hyperhidrosis), te kamo o runga e takoto ana (ptosis o te kamo o runga), me te dermatitis seborrheic.
• Ko te periostitis he mumura o ngā kiriuhi e hipoki ana i ngā wheua. Ka mamae pea ngā pona waewae, ngā ringaringa, ngā turi rānei i tēnei.
• Te pupuhi o ngā kiko ngohengohe o ngā waewae (te pupuhi kāore e puta mai ana i te rua).
• Te matotoru o te wheua i roto i ngā pona me ngā ringaringa.
• Te matotoru o te kiri (Pachydermia). Tērā pea ka taratara te kiri o te mata me te tumuaki, ā, ka hōhonu ngā koki.

He aha ngā āhuatanga motuhake o te HOA tuarua (SHO)?

Haunga ngā tohu noa o te HOA i whakahuatia i mua ake nei, ka pāngia pea te hunga whai HOA tuarua (SHO) e ngā rerenga wai hononga . Koinei te wā ka nui ake te wai i roto i ngā kiko i roto me te taha o ngā hononga. Ka pāngia pea te hononga e ngā rerenga wai:

• Mamae
• Whero
• Te pakari
• Pupuhi

Ko te pupuhi o ngā hononga e pā ana ki te SHO ka kitea nuitia i ngā turi me ngā ringaringa .

Me pēhea te kimi i tēnei? He aha ngā whakamātautau e mahia ana e ngā tākuta?

Ina haere koe ki te tākuta, ko te mea tuatahi ka mahia e rātou ko te tirotiro mēnā he patu kei ō matimati, kei ō waewae rānei. Hei tāpiri, ka tirohia hoki e rātou ēnei i te wā o te whakamātautau tinana:

• Kua pūkeri kē ngā āhua o te kanohi?
• Kua pupuhi ō waewae?
• He mamae kei te pēhi koe i ngā pona waewae, ngā turi, ngā ringaringa rānei?
• Kei te matotoru haere ngā wheua o ngā pona me ngā ringaringa?

Mena kei te whakapae te tākuta he mate e kiia nei ko te HOA, ka whakahaerehia pea e ia ētahi whakamātautau, pēnei i:

• Te tohu kōtaha a Lovibond:Ina titiro koe ki tō maihao mai i te taha, ka kite koe i tētahi koki whānui "V" te āhua, te wāhi e tūtaki ai te pereti whao ki te kopa kiri i te pūtake o te whao (kopa whao proximal). Mena he HOA tōu, ka piko tō whao ki raro, ka piki ake tēnei koki. I roto i tētahi whao noa, he 160 nekehanga, he iti iho rānei tēnei koki. I roto i tētahi whao karapu, he 180 nekehanga, he nui ake rānei.
• Ōwehenga hohonu o te whao: E toru ō wheua (whao) i ia maihao. Ko te wheua e pupuri ana i te whao (whao tawhiti) he poto ake i te wheua e tata ana (whao waenga). Mena he HOA tōu, he poto ake tō whao waenga i tō whao tawhiti.
• Te tohu a Schamroth: Whakanohoia ngā maikuku o ō maihao tohu ki ngā taha e rua. Rapua he āputa (matapihi) āhua taimana i waenganui i te turanga o te maikuku me ngā kiriuhi. Ki te kore he āputa, tera pea he HOA tōu.

Ngā whakamātautau tāpiri hei kite i te HOA tuarua (SHO)

Mena kei te whakapae te tākuta kei tētahi atu mate hauora kei te pūtake o te HOA, ka tūtohu pea ia i ētahi atu whakamātautau:

• Angiography (whakamātautau i ngā oko toto)
• Whakamātautau hau toto uaua
• Ngā whakamātautau toto
• Matawai wheua
• X-ray o te uma
• Matawai CT (matawai Tomography Rorohiko) matawai ultrasound rānei (Ultrasound)
• Te Echocardiogram, te Electrocardiogram rānei (EKG)
• Matawai MRI (MRI - Whakaahua Aukume)
• Te whakamātautau mahi a te pūkahukahu

Mā ēnei whakamātautau ka āwhina i tō tākuta ki te kimi i te pūtake o tō HOA. Mena ka kitea he tipu rerekē i roto i te matawai (pēnei i te pukupuku), ka tūtohu pea tō tākuta kia tangohia he tauira pūtau me te whakamātautau i aua pūtau). Ka āwhina tēnei ki te whakatau i te pūtake tuturu o te tipu.

Me pēhea te rongoā mō tēnei?

He rerekē ngā tikanga maimoatanga i runga i te momo HOA.

Te maimoatanga o te HOA tuatahi (PHO)

Mena kāore koe e mamae ana, kāore rānei ō tohumate i te tino kino, kāore pea koe e hiahia ki tētahi maimoatanga motuhake mō te HOA tuatahi (PHO). Heoi, ki te mea he tohumate ōu, ka taea pea e koe te whakamahi i ngā rongoā pēnei i:

• Ngā rongoā anti-inflammatory kore-steroidal (NSAID)
• Ngā aukati COX-2
• Ngā Bisphosphonates
• Octreotide

Te maimoatanga o te HOA tuarua (SHO)

I te rongoā i te HOA tuarua (SHO), ko te mea nui ko te rongoā i te pūtake . Tērā pea ko te rongoā:

• Te rongoā paturopi mō te rongoā i te mate kohi
• Te rongoā matū hei rongoā i te mate pukupuku pūkahukahu
• Ngā tākai ate, ngā whakawhitinga ate rānei mō te mate ate
• Te pokanga whakawhitinga pūkahukahu mō te cystic fibrosis
• Te tango i te auau irirangi mō ngā pukupuku pūkahukahu (te whakamahi i te wera hei whakangaro i ngā pukupuku)
• Te pokanga mō te mate manawa, te mate pukupuku pūkahukahu rānei

Mena kāore e taea te rongoā i te mate taketake e puta ai te SHO, ka tūtohu pea te tākuta i ngā rongoā hei whakahaere i ngā tohu.

Kia pēhea te roa o te wā e ora ai i muri i te maimoatanga?

Kei te momo HOA kei a koe, te kaha o te mate, me te maimoatanga e whiwhi ana koe. Kia rongoatia te mate taketake, ka tere te memeha o te karapu.

He aha tā tātou e taea ai te mahi hei whakaiti i te puta o tēnei?

Te mōrearea HOA matua (PHO)

Nā te mea he ira te PHO, kāore he mea e taea e tātou te mahi hei whakaiti i tōna hanganga.

Te mōrearea tuarua o te HOA (SHO)

Hei whakaiti i te tūponotanga o te whakawhanake i te SHO, he mea tino nui te whai i tētahi momo noho hauora . He mea nui rawa tēnei mēnā kei te mōrearea koe ki te mate manawa, ki te mate pūkahukahu rānei. Anei ētahi mea ka taea e koe te mahi:

• Te pupuri i te taumaha hauora.
• Te kai i ngā kai hauora mō te ngākau.
• Te whakakorikori tinana i ia wā, i ia wā.
• Te whakawhāiti i te whakamahinga o te waipiro me te tarukino.
• Te whakamutu i te kai paipa. He mea tino nui tēnei, nā te mea ko te kai paipa te tino take o ngā mate pūkahukahu maha.
• Te whakaiti i te ahotea.

He aha te āhua o te heke mai mō tētahi tangata whai HOA?

Mō tētahi he HOA tuatahi (PHO) tōna

Tērā pea ka mutu te kino haere o te PHO. I ētahi wā, inā koa i muri i te taiohitanga, tērā pea ka tino pai haere.

Mō tētahi he HOA tuarua (SHO) tōna

Mena ka rongoatia te pūtake o te mate, ka taea te whakaora katoa i te mate. Heoi, ki te kore e taea te rongoa i te pūtake o te mate (hei tauira, he mate pukupuku kino), ka mau tonu pea te mate.

Ka aha mēnā ka roa te wā e noho ana te āhuatanga o te HOA?

Mena kua roa te noho o te āhuatanga HOA, tera pea ka pāngia koe e ēnei āhuatanga:

• Te ngaronga o te whānuitanga o te nekehanga i roto i ngā hononga
• Osteoarthritis (mamae hononga)
• Mamae

Heoi, kia maumahara ka taea te whakahaere i te nuinga o ēnei tohu mā te maimoatanga tika .

Mena he HOA kei reira, me pēhea koe e tiaki ai i a koe anō?

Mena kei a koe te HOA, ko te mea pai rawa atu ka taea e koe ko te haere tonu ki te tango i te maimoatanga kua hoatu ki a koe hei whakahaere i ō tohu. He mea tino nui kia whai i ngā tohutohu a tō tākuta.

Āhea koe me toro atu ki te tākuta?

Me tūpato koe ki ēnei mea:

• I muri i te maimoatangaKi te hoki mai anō ngā tohumate o te pāwera, me toro atu ki te tākuta. Tērā pea he tohu tēnei kua hoki mai anō te mate taketake.
• Mena he āwangawanga āu mō ngā pānga taha o te maimoatanga .
• Ki te kore e kitea he whakapainga ahakoa te maimoatanga mō tētahi wā.

I roto i ēnei āhuatanga, ka taea e tō tākuta te tūtohu i ētahi atu maimoatanga e tika ana māu.

Whakarāpopototanga: Ngā Mea hei Mahara (Karere hei Tango ki te Kāinga)

Āe, me whakamahara poto tātou ki tā tātou i kōrero ai.

Ko te hypertrophic osteoarthropathy (HOA) he āhuatanga e pupuhi ai ngā pito o ngā maihao, e hē ai te āhua o ngā maikuku. Ka taea te take tuatahi (ira) te take tuarua rānei (nā tētahi atu mate). Ko ngā tino take o te HOA tuarua ko ngā mate pūkahukahu me te mate ngākau.

• Ngā Tohu: Te pupuhi o ngā pito o ngā maihao, te tipu o ngā matikuku o roto, te mamae o ngā hononga, me te matotoru o te kiri.
• Tātaritanga: He whakamātautau hauora, he whakamātautau motuhake (Lovibond, Shamroth scores), me ngā matawai hei rapu i te pūtake.
• Maimoatanga: Mō te PHO, ka hoatu te rongoā i runga i ngā tohu. Mō te SHO, ko te mea nui ko te rongoā i te mate pūtake.
• Ko te mea nui: Ki te kite koe i ētahi panonitanga ki ō maihao, kaua e warewaretia, engari me rapu tohutohu hauora. Nā te mea, ahakoa ehara te HOA i te mea morearea, ka morearea pea te mate e puta ai.

Ko tāku tumanako ka whai hua ēnei kōrero ki a koe. Kia ora tonu!

` Hypertrophic Osteoarthropathy, pupuhi o ngā maihao, panoni o ngā whao, PHO, SHO, mate pūkahukahu, mate ngākau, mamae hononga, karapu