Whakaarohia, ka pāngia koe e te uaua ki te hikoi, ka ngaro tō taurite, ka pōuri, ka hinga ina tū ake koe i te tūnga noho. He mea noa te mataku nui ina tīmata te puta ohorere mai o ēnei mea. Ahakoa kāore tātou e aro nui ki ēnei i ētahi wā, koinei pea ngā tohu tuatahi o ētahi mate onge. I tēnei rā ka kōrero tātou mō tētahi mate io onge, engari he tino kino. Ko te Multiple System Atrophy tēnā, he mate e kīia nei e tātou e ngā tākuta me ngā tūroro ko te (MSA) . Ahakoa he kaupapa uaua tēnei, ka kōrerohia e tātou mō tēnei mea me te tino māmā, i roto i te huarahi e mārama ai koe.
He aha te tikanga o tēnei MSA?
He mate pūnaha io onge te MSA, e ngoikore haere ana, e mate haere ana hoki ētahi wāhanga o te roro. I roto i te wā, ka ngaro haere ngā āheinga me ngā mahi a te tinana e whakahaeretia ana e ēnei wāhanga kua pakaru o te roro. He pono, he āhuatanga tino pouri tēnei, nā te mea ko te mutunga iho o tēnei mate ko te mate.
I ngā wā o mua, e toru ngā ingoa i tapaina e ngā tākuta mō tēnei kohinga tohu. Koia ēnei:
- Te mate whakama-Drager
- Te ngoikore o te olivopontocerebellar tūpono
- Te pirau o te striatonigral
Engari i muri mai, ka kitea e ngā kairangahau he maha ngā āhuatanga ōrite o ēnei mate e toru. Nō reira, ka whakakotahihia katoatia e rātou, ka tapaina ko "Multiple System Atrophy" (MSA). Ko te tikanga o "Multiple System" he "maha ngā pūnaha". Ko te tikanga tēnei ka pā tēnei mate ki ētahi pūnaha o tō tātou tinana. Ka whakawhirinaki ngā tohu ki ngā wāhanga o te roro kua pakaru. Koia te take ka pāngia ia tangata e tētahi huinga tohu rerekē.
Nō muri mai, ka whakarōpūtia anō te mate, i runga i ngā tohu e puta mai ana. Nō reira, e rua ngā momo MSA.
| Momo MSA | Whakaahuatanga me ngā āhuatanga matua |
|---|---|
| MSA-C | Ko te 'C' i konei e tohu ana i te 'Cerebellar'. Ko te cerebellum te wāhanga o te roro e whakarite ana i ā tātou nekehanga. Ko ngā tohu matua o tēnei momo ko te ngaronga o te taurite (ataxia) . Ko te tikanga tēnei kāore e taea e tātou te whakahaere tika i ō tātou waewae, pērā i te hikoi. Hei tāpiri, kei reira ngā raruraru ki ngā mahi aunoa a te tinana (te koretake o te mahi a te tinana) me te hinga pinepine. |
| MSA-P | Ko te 'P' i konei e tohu ana i te 'Parkinsonism'. He rite tonu ngā tohu o tēnei momo MSA-C ki te mate a Parkinson. Hei tauira, te wiri, te puhoi o ngā nekehanga, me te pakari. Ahakoa ko ēnei tohu o Parkinson ngā mea matua i ngā wāhanga tōmua, i roto i te wā, ka puta pea ngā tohu e rite ana ki ērā o ētahi atu MSA-C (te ngaronga o te taurite, ngā raruraru ki ngā mahi aunoa). |
Ko wai te hunga tino mōrearea ki te whakawhanake i te MSA?
Ko te MSA te tikanga ka pā ki ngā pakeke, inā koa i muri i te 30 tau. Ko te nuinga o ngā tohu ka puta i waenga i te 50 me te 59 tau. Ka pāngia te tangata katoa e tēnei mate, ahakoa te ira tangata.
He mate tino onge tēnei. E ai ki ngā tatauranga, e 0.6 ki te 0.7 noa iho ngā kēhi hou mō ia 100,000 tāngata ia tau. Ko te tikanga ehara tēnei i te mate noa i roto i tō tātou hapori.
He pēhea te pānga o te mate MSA ki tō tātou tinana?
Ka mate ngā pūtau i ngā wāhanga rerekē o te roro nā te MSA. Ka whakawhirinaki ngā tohu ki ngā wāhanga o te roro kua pakaru. Ko ngā wāhanga matua o te roro e pāngia ana ko:
- Ngā Pūnaha Tuturu: Kei waenganui tonu o te roro ēnei. He rite ki te pokapū e hono ana i ngā wāhanga rerekē o te roro tetahi ki tetahi. Mā tēnei wāhanga ka huihui ngā wāhanga rerekē o te roro, ka mahi tahi.
- Roro: Koinei te wāhi e whakahaeretia ai ngā tukanga aunoa i roto i tō tātou tinana e tika ana mō te oranga. Hei tauira, ko ngā mea pēnei i te manawa, te tere o te ngakau, me te toto toto. Ka puta aunoa ēnei mea me te kore e whakaarohia e tātou, tika? Koinei te pokapū whakahaere.
- Te Roro o te Tinana: Kei muri o te upoko tēnei, e tata ana ki te pūtake. Koinei te wāhanga matua o tō tātou roro e whakarite ana i ngā nekehanga o ō tātou tinana, e pupuri ana hoki i tō tātou taurite. Hei tāpiri, kua kitea e ngā rangahau kei roto hoki tēnei wāhanga i roto i ō tātou kare ā-roto me te whakatau kaupapa.
Nō reira, ina pakaru ēnei wāhanga o te roro, ka tīmata te hē o ngā tukanga katoa e whakahaerehia ana e aua wāhanga. Hei tauira, ina pakaru te `(te kakau roro)`, ka puta he raruraru nui ki ngā tukanga aunoa pērā i te toto toto tiketike.
He aha ngā tohu matua o te MSA?
I roto i te MSA, he rite tonu ētahi tohu ki ngā momo e rua. Hei tāpiri, he āhuatanga motuhake ki ia momo. Ko te āhuatanga matua e rite ana ki ngā momo e rua ko te ngoikore o te pūnaha io . Ki te kī ngāwari, kāore ngā tukanga e puta aunoa ana i roto i tō tātou tinana e mahi tika.
Ngā Tohu o te ngoikore o te mana motuhake
- Te whakaheke toto toto tiketike: Koinei te tohu tuatahi ka pā ki te tini o te tangata. Ina tū ohorere koe i te tūnga noho, i te takoto rānei , ka heke ohorere tō toto . Ka taea e tēnei te whanoke, te pōuriuri te tirohanga, tae atu ki te hemo.
- Te kore e taea te whakahaere i te mimi me te paru: Ka puta pea te kore e taea te pupuri i te mimi me te kore e taea te pupuri i te paru i te wā kāore koe e whakaaro.
- Te ngoikore o te moepuku: Ka puta ngā raruraru pēnei i te ngoikore o te ure, inā koa i roto i ngā tāne, i te wā o te moepuku.
- Ngā raruraru moe: Ina koa, ka kitea te āhua e kiia nei ko te "(REM) sleep behavior disorder". I roto i tēnei, ina moemoeā koe, ka nekehia tō tinana, ka hamama, ka whiua ō waewae hei whakautu ki ō moemoeā.
- Te hekenga o te werawera (Anhidrosis): Ka tino heke te kaha o te tinana ki te werawera.
- He mea noa anō hoki ngā tohu pēnei i te raruraru tirohanga, te waha maroke, te apnea moe, me te mate kōroke .
He mea nui, ka puta pea ēnei ngoikoretanga ā-aunoa i roto i ngā marama, i ngā tau rānei, i mua i te tīmatanga o ngā tohu nekehanga (pēnei i te raruraru haere me te wiri). Ka puta tēnei i waenga i te 20% me te 75% o ngā tūroro MSA.
Ngā āhuatanga hinengaro me ngā āhuatanga kare ā-roto
Tata ki te hautoru o ngā tūroro MSA e pāngia ana e ngā raruraru ki te whakaaro me te arotahi. He uaua hoki ki a rātou te whakahaere i ō rātou kare ā-roto, ka arahi pea tēnei ki ngā momo raruraru hauora hinengaro.
- Manukanuka
- Te pouri
- Te tangi, te kata rānei i te mea kāore i te tika
- Ngā whakaekenga mataku
- Ngā whakaaro mō te whara, te whakamate rānei i a koe anō
Ngā Tohu e pā ana ki te Nekehanga
Ka rerekē ēnei āhuatanga i runga i ngā momo MSA e rua i kōrerotia i mua ake nei.
| Ngā āhuatanga o te MSA-C (Cerebellar) | Ngā tohu o te MSA-P (Parkinsonism) |
|---|---|
| Ko te tohu matua ko te ataxia , arā, ko te ngaronga o te taunga o ngā mahi. | Ko ngā tohu matua ko te mate a Parkinson , arā, he rite ngā tohu ki te mate a Parkinson. |
| - Ngā nekehanga pōrearea, kore whakahaere o ngā peka. | He tino puhoi ngā nekehanga (bradykinesia) . |
| - Te wiri nui haere o ngā waewae me ngā waewae i te wā e ngana ana ki te mahi i tetahi mea (Te wiri ā-ringa). | - Te āhua o te kikī me te pakari o te tinana, me te āhua nei kua piko whakamua. |
| - Te hikoi me ngā waewae i tawhiti rawa atu, me te mea he hikoi whakakorikori. | - He maha ngā hinganga i te wā e hikoi ana. |
| - Te kimokimo me te nekehanga o ngā kanohi kāore e taea te whakahaere (nystagmus) . | - Te korekore me te korekore o ngā kupu i te wā e kōrero ana. |
He aha ngā take o te MSA?
Kāore anō kia mōhiotia te tino pūtake o te MSA . Heoi, e whakapae ana ngā kaipūtaiao nā te pūmua e kiia nei ko te alpha-synuclein te pūtake. E whakaarohia ana ka kohia tēnei pūmua i roto i ngā wāhanga rerekē o te roro, ka pakaru ai ngā pūtau roro. He mea whakamiharo, e whakapaetia ana hoki ko tēnei pūmua anō te pūtake o te mate a Parkinson.
He mea nui ngā pūmua mō te mahi a ō tātou tinana. Heoi, ina huihui ēnei pūmua ki ngā wāhi hē, i te ara hē, ka taea e rātou te kino i ngā pūtau. Koinei te mea ka tupu i roto i te MSA.
Kei te haere tonu ngā rangahau mō te take e kohia ai tēnei pūmua alpha-synuclein i roto i te roro. E whakapaetia ana ko ngā whakarerekētanga ira pea te take. Ina koa, kei reira ngā taunakitanga e taea ai te tuku i te momo MSA-C mai i tētahi whakatipuranga ki tētahi whakatipuranga ki tētahi taumata. Heoi, kāore anō kia kitea he hononga ira pēnei mō te momo MSA-P.
He mea nui: Ehara te MSA i te mate hopuhopu. Kāore e horapa mai i te tangata ki te tangata i tētahi ara.
Me pēhea te tautuhi i te MSA?
Koinei te wāhanga tino uaua o te mate. Koinei anake te huarahi hei whakaū i te MSA me te tino pono 100%.ko te tirotiro i te kiko roro i muri i te matenga o te tangata. Ko te take o tēnei, kāore anō kia kitea he hangarau hei tirotiro mēnā kei roto te pūmua alpha-synuclein i te roro o te tangata ora.
Heoi, i te mea kei te ora tonu te tūroro, ka taea e ngā tākuta te whakapae i te mate. Ka whakamahia e rātou ngā mea pēnei i ngā tohu, te hītori hauora o te tūroro, te hītori whānau, me te urupare ki ētahi maimoatanga. He maha ngā wā, ka taea e ngā tākuta te tautuhi tuatahi i te mate a Parkinson. Heoi, i te mea ka puta ake ētahi atu tohu i roto i te wā, i te wā rānei ka mutu te mahi a te rongoā a Parkinson, me huri pea te tautuhi ki te MSA.
Ngā rerekētanga matua i waenga i te MSA me te mate a Parkinson
| Āhuatanga | Te Atrophy Pūnaha Maha (MSA) | Te mate a Parkinson |
|---|---|---|
| Te tere o te horapa o te mate | Ka tino tere te kino haere o ngā tohu. | Ka āta haere te mate. |
| Ngā ngoikoretanga aunoa | Ko ngā raruraru nui (hei tauira, ngā raruraru toto toto) ka puta pinepine i roto i te tau tuatahi o te tīmatanga o te mate. | Ka roa pea ngā tau ka puta mai ai ēnei tohu. |
| Wiri | He iti ake ngā wiri, kāore pea i te kitea . | He tohu nui te wiri e puta ana i te wā e okioki ana . |
| Te urupare ki a Levodopa | He iti noa iho te hunga e aro nui ana ki tēnei rongoā.Kāore rawa rānei. | He tino pai te urupare ki tēnei rongoā. |
Ngā whakamātautau tātaritanga
He tino ruarua ngā whakamātautau ka taea te tautuhi tika i te MSA. I te nuinga o te wā, ka whakahaerehia he raupapa whakamātautau hei whakakore i ētahi atu mate me te kohikohi taunakitanga hei tautoko i te whakapae ko te MSA pea te take.
- Matawai MRI (Atahanga Āhuatanga Matū): Ka taea e tēnei te whakaatu i ētahi wā i te kino o ngā wāhanga o te roro. I roto i te MSA-C, ina koa, ka kitea he tauira e kiia nei ko te tohu "pāpā ripeka wera" i roto i tētahi wāhanga o te roro. He rite ki te pāpā ripeka wera. Heoi, ka kitea anō hoki tēnei tohu i roto i ētahi atu mate, nō reira ehara i te mea he tautuhi tuturu mō te MSA.
- Whakamātautau ira: Ka taea e tēnei te tirotiro mō ngā whakarerekētanga ira e pā ana ki te pūmua alpha-synuclein.
- Te koiora kiri: E kī ana ētahi rangahau hou ka taea e tēnei whakamātautau te āwhina ki te whakatau mēnā kei roto i te kiko io o te kiri te alpha-synuclein. Heoi, kei roto tonu i te wāhanga rangahau tēnei.
Mā tō tākuta koe e whakamārama he aha ngā whakamātautau e whakaarohia ana e ia he mea tika, i runga i tō āhua, me ngā mea hei tumanakohia mai i aua whakamātautau.
He rongoā kei te wātea mō te MSA?
Engari, kāore anō kia kitea he rongoā mō te MSA i tēnei wā . Nō reira, ko te whāinga matua o te maimoatanga he whakahaere i ngā tohu me te pupuri i te kounga pai o te oranga mō te wā roa rawa atu.
Ko te maimoatanga e hoatu ana ka whakawhirinaki ki ngā tohumate o te tūroro me tōna kaha. Hei tauira, ka hoatu ngā rongoā toto totoka mō te whakaheke toto toto tiketike, ngā rongoā whakangāwari uaua mō te pakari, me ētahi atu rongoā hei whakahaere i te mimi. He mea tino nui anō hoki ngā mahi pēnei i te whakaora tinana me te whakaora kōrero.
Mena kei a koe, kei tētahi atu rānei e mōhio ana koe, kaua e ngana ki te rongoā i a koe anō, kaua hoki e whakahaere i ngā tohumate. Me toro atu ki tētahi tākuta whai tohu, me te whai i āna tohutohu.
He aha te momo āmua ka taea e te tangata whai mate te tumanako?
He mate haere tonu te MSA. Tata ki te haurua o te hunga e pāngia ana ka hiahia ki tētahi āwhina hikoi (pērā i te tokotoko, i te taputapu hikoi rānei) i roto i ngā tau e 5 i muri i te tīmatanga o ngā tohu. Tata ki te 60% ka hiahia ki tētahi tūru wīra i roto i ngā tau e 5. I roto i ngā tau 6 ki te 8, ko te nuinga o ngā tūroro kua takoto noa i te moenga.
I te haere whakamua o te mate, e hiahiatia ana ngā tikanga hauora maha hei pupuri i ngā mahi a te tinana.
- Ko te tracheostomy he tikanga e hangaia ai he kōhao iti ki te korokoro, ā, ka whakaurua he ngongo hei āwhina i ngā uauatanga manawa.
- Ko te whāngai i roto i te ngongo ko te hoatutanga o te kai mā roto i te ngongo i te wā e kore e taea e te tūroro te horomi.
- Ngā ngongo, ngā tikanga pokanga rānei hei whakahaere i te mimi me te paru.
Ko te tikanga, ko te roanga o te oranga mō te tūroro e pāngia ana e te MSA mai i te wā i kitea ai tōna mate kei waenganui i te 6 me te 10 tau. I ētahi wā kāore i te tino kino, ka taea te ora ki te 15 tau. Heoi, ki te tino kino te mate, ka poto ake te roanga o te oranga.
Ko te nuinga o te mate ka puta mai i ngā raruraru o te mate. Hei tauira:
- Pūngāwerewere.
- Sepsis (paitini toto) nā te mate mimi.
- Te matenga ohorere i puta mai i ngā raruraru ki te whakahaere manawa o te roro i te wā e moe ana.
Me pēhea tātou e tiaki ai i ō tātou whanaunga?
I te kaha haere o ngā tohu o te tangata whai MSA i roto i te wā, ka kore pea e taea e rātou te noho motuhake. Tērā pea ka ngaro i a rātou te kaha ki te whakaaro, ki te kōrero, me te whakatau i a rātou anō.
Nō reira, he mea tino nui te kōrero mō te heke mai ki ō whanaunga i te tīmatanga o te mate, i te wā e mōhio tonu ana te tūroro. Mēnā kei roto koe i tētahi āhuatanga kāore e taea e koe te whakatau, he mea tino whai hua ki te katoa mēnā ka taea e koe te kōrero i mua i ngā whakatau me whakatau mō tō maimoatanga hauora, me te whakarite tuhinga ture.
Āhea koe me toro atu ki te tākuta?
He maha ngā tohu tōmua o te MSA he mea me kōrero koe ki te tākuta.
- Te moepuku.
- Te whanoke tonu me te ngaronga o te māramatanga ina tū ake.
- Ngā raruraru moe, inā koa ko te apnea moe.
Mena kua kōrero mai tō tākuta kei a koe tētahi mate nekehanga pērā i te mate a Parkinson, he mea nui kia kōrerohia ngā huringa o ō tohumate. Ina koa mēnā kāore te rongoā (levodopa) mō te mate a Parkinson e mahi, he tohu nui tēnā kei a koe te MSA.
He mate kino, he mate whakamate te MSA. He pono kāore he rongoā mōna. Heoi, he maha ngā tohu ka taea te rongoā. Mā taua maimoatanga, ka taea te pupuri i te kounga o te oranga o te tūroro ki tētahi taumata pai mō ngā tau maha. He wā utu nui taua wā ki te noho harikoa me ō rātou whānau me te koa ki te oranga katoa.
Karere Tangohia ki te Kāinga
- He mate onge, he mate whakamate te MSA, e whakangaro haere ana i ngā wāhanga o te roro.
- E rua ngā momo matua: MSA-C (ko te ngaronga o te taurite te mea nui) me MSA-P (ko ngā āhuatanga o te Parkinsonism te mea nui).
- Ka puta wawe mai te ngoikore o te pūnaha ā-tinana, pērā i te hekenga o te toto toto i te tū me te ngaronga o te mana whakahaere mimi.
- He tere ake te whanaketanga o te MSA i te mate a Parkinson, ā, he iti ake te aro ki ngā rongoā a Parkinson.
- Ahakoa kāore he rongoā mō te mate, kei reira ngā maimoatanga hei whakahaere i ngā tohu me te whakapai ake i te kounga o te oranga.
- He mea tino nui kia mōhio wawe ki ngā tohu, kia rapu tohutohu hauora, ā, kia whakamahere mō te heke mai.
💬 Comments (0)
No comments yet. Be the first to share your thoughts here.
Add Your Comment