Kei te whakaaro koe i ētahi wā kāore e kitea ngā kupu tika hei kōrero? He uaua rānei ki a koe te mārama ki ngā kōrero a tētahi? Tērā pea kei te mōhio koe ki tētahi o tō whānau, he whaea, he pāpā rānei, he pēnei te uauatanga? Ahakoa te āhua noa o ēnei mea ka puta i a koe e pakeke haere ana, i ētahi wā he tohu pea nō tētahi mea hohonu ake. I tēnei rā kei te kōrero tātou mō tētahi o aua āhuatanga, ko te Aphasia Whakamua Ahunga Whakamua (PPA).
He aha rawa te PPA?
He whakarāpopototanga noa iho, ko te Aphasia Tuatahi Whakamua (PPA) he mate roro. He mate neurodegenerative e ngoikore haere ana te pūnaha io, ā, ka kino haere i roto i te wā. Ina koa, ka kino ngā wāhanga o te roro e whai wāhi ana ki tō tātou kaha ki te kōrero, ki te pānui, ki te tuhituhi, me te mārama ki te reo.
Whakaarohia he rite tō tātou roro ki tētahi whare pukapuka nui. Kei roto i tētahi wāhanga motuhake o taua whare pukapuka ngā pukapuka katoa, ngā kupu, me ngā tikanga e pā ana ki te reo. Ko te PPA tonu te mea ka tupu ina pirau haere ngā pukapuka o tēnei wāhanga, takitahi, ā, ka kore e taea te whakamahi.
Ko te PPA he momo o te Mate wareware o te roro o mua o te wā (FTD) me te Mate wareware o Alzheimer . Mā ēnei mate ka ngoikore haere ngā roro o mua me te roro o te wā. Ko ēnei wāhanga te nuinga o te wā e whakahaere ana i ō tātou pūkenga reo.
He tino uaua, he tino whakarihariha hoki te noho me tēnei mate mō te tūroro me ō rātou whānau. Heoi, mā te tohutohu hauora me te tautoko tika, ka taea te whakahaere i ēnei tohu.
He aha ngā momo matua o ngā PPA?
E toru ngā momo matua o te PPA. He rerekē ngā āhuatanga o ia momo. Kia mārama tātou i tēnei ripanga.
| Momo PPA | Āhuatanga matua | He maha ngā wā e hono ana ki |
|---|---|---|
| PPA momo logopenic | He uaua ki te kimi i ngā kupu tika, te kore e taea te whakaingoa i ngā mea, me te tū i waenganui i ngā kupu i te wā e kōrero ana. Heoi, he tika te wetereo i te nuinga o te wā. | He maha ngā wā e hono ana ki te mate a Alzheimer. |
| PPA rerekē kore-matau (agrammatic) | Te ngaro o te rere o te reo me ngā hapa wetereo. Te uaua ki te hanga kupu i te wā e kōrero ana. | He momo Mate wareware o te roro o mua o te wā (FTD). |
| PPA rerekētanga tikanga | Ahakoa e rere ana te kōrero, kāore e taea te mārama ki te tikanga o ngā kupu. He uaua ki te whakaingoa i ngā taonga, ki te mārama rānei ki te tikanga o ngā kupu. | He momo Mate wareware o te roro o mua o te wā (FTD). |
He aha pea ngā tohu o tēnei mate?
He rerekē ngā tohu i runga i te momo i kōrerotia i mua ake nei. I te nuinga o te wā, ka tīmata te puta o ēnei tohu i waenga i te 50 me te 70 tau te pakeke. Ka kino haere haere i te roanga o te wā.
Ngā āhuatanga o te momo logopenic PPA
- He uaua ki te kimi i te kupu tika hei kōrero.
- Te uaua ki te mārama ki ngā rerenga roa, uaua rānei.
- He uaua ake te kī i ngā rerenga roa i ngā rerenga poto.
- Ngā wā okioki pinepine i te wā e kōrero ana.
- Te hē o te whakapuaki kupu.
- Te whakamahi i ētahi atu kupu hei utu mō ētahi kupu (hei tauira, te kī "ngeru" hei utu mō te "kurī").
Ngā āhuatanga PPA rerekē kāore i te matatau (agrammatic)
- Te uaua ki te whakamahi i ngā ngutu me te arero ki te whakaputa tika i ngā oro (apraxia).
- Te uaua ki te horomi.
- Ngā raruraru ki te hikoi me te nekehanga (ngā nekehanga puhoi me te pakari, te ngaro o te taurite, te hinganga pinepine).
- Te tango i ngā kupu mai i ngā rerenga kōrero, me te kōrero noa iho (hei tauira, "Kei te haere a Māmā ki te kai tina" kaua ki te "Kei te haere māua ko Māmā ki te kai tina").
- Te uaua ki te mārama ki ngā rerenga roa, uaua rānei.
- Tērā pea ka uaua ki ētahi tāngata te kōrero, ā, ka wahangu pea rātou.
Ngā āhuatanga PPA rerekētanga tikanga
- Te wareware i ngā taonga e mōhiotia ana, me te aha hoki e tika ana kia mahia ki aua mea.
- Te kore e maumahara ki te tikanga o ngā kupu.
- He uaua ki te kimi i te kupu tika hei kōrero.
- Ngā uauatanga o te pānui me te tuhituhi.
He aha ngā take o te PPA? He āhuatanga mōrearea kei reira?
Ka puta tēnei āhuatanga nā te mea ka mate haere ngā pūtau i roto i ngā wāhanga o tō tātou roro e whakahaere ana i te reo. Ka meinga tēnei kia mimiti te kiko o te roro. I roto i te rongoā, ka kiia tēnei he atrophy .E kīia ana ko tēnei mimiti te take e ngaro ai ngā pūkenga e pā ana ki te reo.
Ahakoa ka pā tēnei āhuatanga ki te katoa, he nui ake te mōrearea o ētahi tāngata.
- Mena kua pāngia tetahi o te whānau e te PPA.
- Kei a rātou ētahi momo ira , pērā i te `(C9orf72, MAPT, GRN rānei)`.
- Mena he raruraru ako tōu i tō tamarikitanga.
- Kei te pāngia koe e te mate a Alzheimer.
Engari i ētahi wā ka puta tēnei āhuatanga me te kore he take mārama.
Me pēhea te kitenga a te tākuta i tēnei?
Mena he raruraru reo tōu, me toro atu koe ki te tākuta. Ka pātai atu te tākuta ki a koe mō ō tohu me te hītori hauora o tō whānau. Kātahi ka whakahaerehia pea ētahi whakamātautau hei whakaū i te mate.
- Whakamātautau io: Ka tirohia tō taurite, ō urupare, me te mahi a te pūnaha io.
- Ngā whakamātautau hinengaro: Ngā whakamātautau e ine ana i te mahara, te kaha whakaaro, me ngā kaha reo.
- Ngā matawai roro: Tērā pea ka mahia he matawai MRI (Magnetic Resonance Imaging) CT (Computed Tomography) rānei hei tirotiro mēnā he mimiti, he rerekētanga rānei kei roto i te roro.
Ngā wāhanga o te mate PPA
Nā te mea ka kino haere te mate nei i roto i te wā, he maha ngā wāhanga kua tautuhia.
1. Wāhanga 1 (tino ngāwari): Ka kitea ngā uauatanga reo iti noa iho. Tērā pea ka whakaarohia nā te koroheketanga, nā te ahotea rānei. He onge te whiwhi tātaritanga i tēnei wā.
2. Wāhanga 2 (ngāwari): Ka puta pinepine ngā raruraru reo. Ka tīmata hoki ngā mema o tō whānau ki te kite i tēnei rerekētanga. Ka tīmata tēnei ki te pā ki ngā mahi o ia rā.
3. Wāhanga 3 (Waenga): Ka tino uaua te mahi i ngā mahi o ia rā ko koe anake. Ka tino hoha te kōrero ki ētahi atu me te noho pāpori.
4. Wāhanga 4 (Nui rawa): He tino uaua ki te kōrero me te mārama ki te reo. Me āwhina i ngā mahi o ia rā. He mea morearea te noho ko koe anake.
5. Wāhanga 5 (tino kino): Kua ngaro te nuinga o te māramatanga ki te kōrero me te reo. Ka puta ngā huringa whanonga me te whakaaro. Me tiaki i roto i ngā haora 24.
6. Wāhanga 6 (whakamutunga): Kāore e taea te kōrero, te mārama rānei i te reo. Tērā pea ka puta ngā oro kore-waha. Tērā pea ka ngaro te kaha ki te neke.
He rongoā kei reira mō tēnei?
Engari, kāore anō kia kitea he maimoatanga hei whakaora katoa i te PPA.Ā, kāore e taea te aukati i te kino haere o te mate. Engari he maimoatanga kei reira hei āwhina i te whakahaere i ngā tohu, hei whakaroa i te haere whakamua o te mate, hei whakangawari ake hoki i te oranga.
Ka tūtohu pea tō tākuta i ngā maimoatanga pēnei i:
- Whakaora kōrero: Ka āwhina tēnei ki te pupuri i ngā pūkenga reo mō te wā roa me te ako i ngā tikanga whakawhitiwhiti kōrero hou.
- Te ako i ngā tikanga whakawhitiwhiti kōrero hou: Te taunga ki te whakamahi i ngā mea pēnei i te reo tohu, i ngā kāri pikitia rānei.
- Rongoā: Ka taea te tohu rongoā pēnei i te Selective Serotonin Reuptake Inhibitors (SSRIs) hei whakahaere i ngā huringa whanonga, te pouri, te manukanuka rānei.
- Ngā rongoā a Alzheimer: Mena ko te mate a Alzheimer te take o te PPA, ka tohua pea ngā rongoā pēnei i te donepezil , te rivastigmine rānei e whakamahia ana mō taua āhuatanga.
Ka pēhea rā te āhua o te oranga me tēnei mate?
He mate te PPA ka kino haere i te roanga o te wā. Ā tōna wā, ka ngaro katoa ngā pūkenga reo me te whakawhitiwhiti kōrero. I te horapa o te mate ki ētahi atu wāhanga o te roro, ka pāngia hoki te whakaaro me te whanonga.
He mea nui kia kōrero wawe tonu koe ki ō whanaunga mō tēnei mate. Mā tēnei ka āwhina i a rātou ki te mārama me pēhea te tiaki i a koe mēnā kāore e taea e koe te whakatau i ngā mea kei te heke mai.
Ko te tikanga, ko te roanga o te oranga i muri i te tīmatanga o ngā tohu he rima ki te whitu tau, engari he rerekē rawa tēnei i ia tangata, i ia tangata. Nō reira kaua e mataku ki ngā tatauranga. Ko tō tākuta anake ka taea te hoatu ki a koe ngā mōhiohio pai rawa atu mō tō āhua.
Karere Tangohia ki te Kāinga
- Ko te Aphasia Tuatahi Ahunga Whakamua (PPA) he āhuatanga e ngoikore haere ana ngā wāhanga o te roro e whakahaere ana i te reo.
- Ehara tēnei i te koroheketanga noa. Ki te mea he uaua ki a koe te kimi kupu, te kōrero, te mārama rānei ki ngā kōrero a ētahi atu, kaua e warewaretia. Me toro atu ki te tākuta.
- Ahakoa kāore he rongoā katoa mō tēnei, kei reira ngā maimoatanga me ngā mahi whakaora hei whakahaere i ngā tohumate me te whakamāmā ake i te oranga.
- Mena kei te pāngia koe, tētahi rānei o tō whānau e tēnei mate, he mea nui kia rapu tohutohu hauora i te wā e taea ai, kia kōrero tūmatanui ki te whānau, kia whiwhi hoki i te tautoko e tika ana.











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