Kāore tō tinana e aro tika ana ki te Hormone Parathyroid? Me kōrero tātou mō tēnei āhuatanga rerekē (Pseudohypoparathyroidism)!

Kei te whakaaro koe i ētahi wā kei te hē te mahi a tētahi mea i roto i tō tinana? Tērā ētahi mate tauhou, ā, he whakamataku pea ō rātou ingoa. Ko tētahi mate kāore i te tino rangona, engari he mea nui kia mōhiotia, ko te Pseudohypoparathyroidism (PHP). Ahakoa te ahua roa o te ingoa, kia māmā noa iho.

He aha te pseudohypoparathyroidism?

He kupu ngāwari noa iho tēnei, he mate ira onge tēnei. He iti ngā repe kei roto i ō tātou tinana e kiia nei ko ngā repe parathyroid. Ka whakaputahia e ēnei he homoni e kiia nei ko te Parathyroid Hormone (PTH). He mea tino nui tēnei homoni PTH mō ō tātou tinana. Nā te mea, ka āwhina tēnei homoni ki te pupuri i ngā taumata tika o te Konupūmā, te Phosphorus, me te Huaora D i roto i ō tātou toto.

Nā, e mōhio ana koe ki te aha ka pā ki te tangata e pāngia ana e te pseudohypoparathyroidism (PHP)? Ahakoa e whakaputa noa ana ā rātou repe parathyroid i te homoni PTH, kāore ngā pūtau o roto i ō rātou tinana e aro tika ana ki taua homoni, arā, kāore e taea e rātou te "mōhio" ki taua homoni. He rite ki te tangata e kōrero ana ki a koe engari kāore e taea e koe te whakarongo ki a rātou. Ka kiia tēnei he Ātete ki te Homoni Parathyroid .

He aha te hua? Ka heke te taumata o te konupūmā i roto i te toto, ka piki ake te taumata o te whākōkī. Ka taea e tēnei taurite kore te whakakorikori i ngā uaua, te ngoikore o te tinana, te haurangi, me ngā raruraru niho.

He mea nui, he rerekē tēnei āhuatanga e kiia nei ko te PHP i tētahi āhuatanga e kiia nei ko te Hypoparathyroidism. Kāore i te nui te homoni PTH e whakaputaina ana e te hunga whai hypoparathyroidism i te tīmatanga. Heoi, i roto i te PHP, ka whakaputaina te homoni, engari kāore e whakamahia e te tinana.

He aha ngā momo matua o te PHP?

He maha ngā momo matua o te tūnga PHP. Kia tirohia tātou he aha ēnei.

Momo PHP-1

Koinei te momo PHP tino noa . Haunga te ātete homoni PTH kua whakahuatia ake nei, ka kitea ētahi huringa o te pūnaha angaiwi. Hei tauira:

• Te porowhita o te mata
• Te roa iti iho (te poto o te tinana)
• Mamae kaki
• Ngā whati o ngā ringa me ngā waewae

Ka tapaina tēnei huinga o ngā tohu e ngā tākuta ko te Albright Hereditary Osteodystrophy (AHO) . Ko te hunga whai PHP-1 kei a rātou tēnei mate nā te mea he momo ira e kiia nei ko te 'GNAS' i riro mai i tētahi o ō rātou mātua.

PPHP (Pseudoppseudohypoparathyroidism)

He momo iti noa iho tēnei o te PHP-1. Tērā pea kei te hunga whai PPHP (Pseudopseudohypoparathyroidism) ngā āhuatanga tinana e kitea ana i roto i te AHO (pērā i te kanohi porowhita me te roa poto), engari kāore he ātete ki te homoni PTH . Ko te tikanga he noa ō rātou taumata konupūmā me te whākōkī.

Momo PHP-2

He ātete ki te homoni PTH te hunga whai PHP-2, arā, he iti te konupūmā, he nui hoki te whākōkī. Engari kāore i a rātou ngā āhuatanga ā-tinana (pērā i te kanohi porotaka me te roa poto) e kitea ana i roto i te AHO. Kāore anō kia kitea e ngā kairangahau he aha te hapa ira e puta ai tēnei momo PHP-2.

He aha ngā tohu o te PHP?

Ka rerekē ngā tohu o te PHP i ia tangata, i ia tangata . Ko te tikanga, ehara i te mea ka pāngia te katoa e ngā tohu ōrite. Ko ētahi o ngā tohu noa ko:

• Ngā mamae o te uaua
• Te mamae pinepine o ngā uaua : He āhua e tōia ana te waewae.
• Te ngenge, te ngau rānei i ngā peka
• Ngā mate hopuhopu
• Te whakaroa o te puta o ngā niho
• Te ngoikore o te enamel niho
• Te toto toto iti
• He makawe me he whao pakarukaru
• Manukanuka
• Te pouri

Tērā pea ka pāngia te hunga whai PHP-1 e ētahi atu tohu e haere tahi ana me te mate Albright hereditary osteodystrophy (AHO) kua whakahuatia i mua. Tērā pea ka pāngia ētahi tāngata whai PHP e ēnei tohu:

• Te porowhita o te mata
• Te poto o te tinana (te poto o te tinana)
• Mamae kaki
• Ngā wheua o ngā ringa me ngā waewae : Tērā pea ka puta te āhua o ngā hononga o te ringaringa, inā koa ko ngā mea o ngā maihao tuawhā me tuarima, me te mea kei te anga whakaroto.
• Momonatanga : Ko tōna tikanga he taumaha rawa.
• Ngā ngoikoretanga o te tirohanga : ngā mea pēnei i te katarata, te tirohanga pōuri, me te aro ki te mārama.
• Ngā pupuhi wheua i raro i tō kiri
• Ngā whakaroa whanaketanga : Tērā pea ka pāngia ētahi tamariki e ētahi whakaroa whanaketanga.

He aha ngā take o te PHP?

Ko te tino take o tēnei mate ko ngā rerekētanga o roto i ō tātou ira, inā koa ko te ira e kiia nei ko te 'GNAS' . Ka riro mai i ētahi tāngata i ō rātou mātua . Ko te tikanga he mea tuku iho. Engari i ētahi wā ka puta tēnei āhuatanga me te kore he hītori whānau, ā, kāore e kitea he take.

Ko te tikanga ka kitea te PHP i te wā pēpi, i te wā kōhungahunga rānei , engari ka puta pea i te wā pakeke.

He aha ngā raruraru pea o te PHP?

Mena kei a koe te PHP, he nui ake te tūponotanga ka pāngia koe e ētahi atu mate pūnaha endocrine . Ka taea e ēnei raruraru e pā ana ki ngā homoni te whakaputa i ngā tohu pēnei i te iti o te kaha me te iti o te hiahia moepuku.

Ko ētahi tāngata whai PHP he nui ake te mōrearea ki te whakawhanake i ngā āhuatanga pēnei i:

• Te mate pākisoniE whakaatu ana i ngā tohu e rite ana ki te mate a Parkinson.
• Te uaua ki ngā pūkenga nekeneke o te tinana : Ko te tikanga he uaua ki ngā mahi ngāwari pēnei i te pātene, te tuhituhi rānei.
• Te Mate Pūnaha Carpal Tunnel : Ina koa mō te hunga whai PHP-1. He āhuatanga tēnei e pēhia ai te io i roto i te ringaringa, ka pā te ngoikore me te mamae o te ringa.
• Te whakatōtōtanga o te tuaiwi
• Te mate moe pōrearea : Ina koa i roto i ngā tamariki.

Me pēhea te tātaritanga a ngā tākuta i te PHP?

Ki te whakapae koe kei a koe te PHP, ka tirotirohia e tō tākuta te tinana i te tuatahi. Ka pātai atu hoki rātou mō tō hītori whānau . Kātahi ka mahia pea e rātou ētahi atu whakamātautau hei whakaū i te mate. Kei roto i ēnei ko:

• Ngā whakamātautau toto : Ine i ngā taumata o ngā homoni, inā koa ko te konupūmā, te whākōkī, me ngā taumata PTH.
• Ngā whakamātautau mimi : Tirohia ngā taumata o te konupūmā me te whākōkī i roto i te mimi.
• Whakamātautau ira : Tirohia mēnā he panoni kei roto i te ira 'GNAS'.
• Electrocardiogram (EKG) : Ka tirohia mēnā he rerekē te tere o te pā o te manawa.
• Ngā hihi-X o te ringa : Tirohia mēnā he whati ngā wheua me ētahi atu huringa.
• Matawai CT (CT - Matawai Tomography Rorohiko) : Hei tirotiro mēnā he huringa kei roto i te roro.

I runga i ngā mōhiotanga i riro mai i ēnei whakamātautau ka taea e te tākuta te whakaū tika i te tūnga o te PHP.

Me pēhea te whakahaere i te PHP?

Kāore anō kia kitea he rongoā mō tēnei mate . Kaua e manukanuka. Mā te maimoatanga me te whakahaere tika, ka taea e koe te whakahaere i ō tohumate me te noho i te oranga noa.

Ko te whāinga matua o te maimoatanga he pupuri i ngā taumata tika o te konupūmā me te whākōkī i roto i tō toto . Mā te pupuri i ēnei taumata ka tino whakaiti i ngā tohu. He maimoatanga mō te wā katoa tēnei.

Ko ngā kōwhiringa maimoatanga pea ko:

• Ngā tāpiringa konupūmā me te huaora D : i roto i te ahua pire, i te ahua wai rānei.
• Ngā kāpū Calcitriol : He rongoā tēnei e whakanui ana i te nui o te konupūmā i roto i te tinana.
• Werohanga Calcitriol
• Te rongoā whakakapinga mō te homoni tipu, te homoni tairoi rānei : mēnā e tika ana.
• He kai nui te konupūmā, iti te whākōkī : E ai ki ngā tohutohu a te tohunga kai.

Ko te mea nui ko te whai i ngā tohutohu a te taote, me te whakamātautau i te wā tika.

Āhea ahau me toro atu ki te tākuta?

Mena he PHP tōu, he mea nui kia toro atu koe ki tō tākuta i ia wā, kia tirohia ai ō taumata konupūmā me te whākōkī . Mā tēnei aroturukitanga auau ka āwhina i te pupuri i ngā mea katoa kia kaua e neke haere.

Ki te pāngia koe e ngā tohu kino pēnei i te uaua ohorere ki te manawa, te wiri o ngā uaua, te haurangi rānei , haere tonu ki te rūma ohorere o te hōhipera tata , waea atu rānei ki te 1990.

He aha ngā mea ka taea e koe te tumanako atu i a koe e noho ana i roto i te āhuatanga PHP?

Mena kei a koe te PHP, me haere tonu koe ki te mahi tahi me tō Tākuta Tiaki Tuatahi . Nā te mea ka pā te PHP ki ngā wāhanga rerekē o te tinana, me toro atu pea koe ki ētahi tohunga hei whakahaere i ō tohumate. Kei roto pea i tō tīma hauora:

• Ngā tohunga endocrine : Ngā tohunga ki ngā homoni.
• Ngā taote pokanga wheua : Mō ngā raruraru e pā ana ki te wheua.
• Ngā Tākuta Tamariki : Mena he tamaiti.
• Ngā Tohunga Niho : Mō ngā raruraru e pā ana ki te pūnaha io.
• Ngā kaiwhakaora tinana
• Ngā kaiwhakaora mahi
• Ngā tohunga kai
• Ngā Tākuta Niho
• Ngā tohunga ira
• Ngā tohunga whakahaere mamae

Ko te mea pea me tango e koe aua tāpiringa mō te toenga o tō oranga .

Ka rerekē pea ngā pūkenga whanaketanga me ngā pūkenga hinengaro i runga i te momo me te kaha o te mate. Heoi , i te nuinga o te wā, he rite tonu te roa o te oranga o te hunga whai PHP ki te hunga kāore he PHP . Ka taea e tō tākuta te kī atu ki a koe he aha ngā mea hei tumanakohia i runga i tō āhua.

Nā te mea he mate onge te PHP, he uaua ki te kimi i ētahi atu he rite tonu te mate ki a koe . Ka taea hoki te noho mokemoke i ētahi wā. Mēnā kua tāpaetia koe, tāu tamaiti rānei ki te PHP, kōrero ki tō tākuta mō ngā rōpū tautoko me ngā rauemi mātauranga . Ka taea e ēnei te āwhina i a koe ki te kimi huarahi hei whakapai ake i ō tohu me te kounga whānui o te oranga.

Karere Tangohia ki te Kāinga

Āe, me titiro tātou ki ētahi mea hei maumahara mō te pseudohypoparathyroidism (PHP) kua kōrerohia ake nei.

• He āhuatanga ira onge te PHP, ā, kāore te tinana e aro tika ki te homoni parathyroid (PTH).
• Ka heke te konupūmā i roto i te toto, ka piki hoki te whākōkī.
• He maha ngā momo matua : PHP-1, PHP-2, me PHP-3.Āe. Ka taea e te PHP-1 te whakaputa i ngā huringa ki ngā wheua e kiia nei ko te AHO.
• Ka puta pea ngā tohu maha, pērā i te wiri o te uaua, te ngoikore, te haurangi, te raruraru niho, te poto, me te mata porotaka .
• Ko te tino take he whakarerekētanga ira i roto i te ira 'GNAS' .
• Ahakoa kāore he rongoā katoa, ka taea te whakahaere i ngā tohu mā te maimoatanga mō te wā katoa (konupūmā, huaora D, he kai motuhake).
• He mea nui ngā tirotiro hauora auau me te tautoko a ngā tākuta tohunga.
• Ka taea e te nuinga o te tangata te noho i te oranga noa .
• He mea nui te āwhina a ngā rōpū tautoko kia kaha ai te hinengaro.

Kaua e wareware, ehara i te mea ko koe anake. Ahakoa he mate onge tēnei, ka taea te whakahaere pai mā te tohutohu me te tautoko hauora tika. Kia maumahara kei reira ngā tākuta, te whānau, me ngā hoa hei tautoko i a koe ina hiahia koe ki te kaha.

` Pseudohypoparathyroidism, PHP, homoni parathyroid, konupūmā, whākōkī, mate ira, AHO