Kua rongo koe i te 'Repe Thymus'? Kāore pea. He repe iti tēnei i roto i tō tātou uma, i mua tonu i te ngākau. He mea tino nui mō tō tātou pūnaha ārai mate i a tātou e tamariki ana. Engari i ētahi wā ka pā mai he raruraru hauora nui ki tēnei repe iti. Koinei te wā e taunaki ana ngā tākuta i tētahi pokanga e kiia nei ko te 'Thymectomy'. Nō reira, i tēnei rā ka kōrero tātou mō tēnei, arā, te pokanga hei tango i te repe thymus, i roto i ngā kupu māmā noa iho.
He aha te tikanga o te thymectomy?
He pokanga te tango i te repe thymus me ngā pukupuku katoa kua puta i te taha. Ehara i te mea tino noa. I kitea i roto i tētahi rangahau i te United States e 7,000 o ēnei pokanga i mahia i roto i te wā 13 tau. Tata ki te 1,000 ngā pokanga ia tau. Nō reira, ka taea e koe te whakaaro he pokanga motuhake tēnei.
He aha ngā āhuatanga e mahia ai te thymectomy?
Ko te nuinga o tēnei pokanga he rongoā mō ētahi raruraru e pā ana ki te repe thymus. Me titiro tātou ki ēnei.
| Āhuatanga hauora | He whakamārama māmā |
|---|---|
| Te Maistenia Gravis | He mate pūnaha ārai mate tēnei. He māmā noa iho, ka whakaekea e te pūnaha ārai mate o te tinana ngā hononga i waenga i ngā io me ngā uaua o te tinana. Ka puta mai ngā tohu pēnei i te ngoikore o te uaua, te kamo e takoto kau ana, me te uaua ki te kōrero me te horomi. Mā te tango i te repe thymus ka taea te whakahaere i tēnei āhuatanga. |
| Timoma | He momo pukupuku matepukupuku tēnei e tupu ana i roto i te repe thymus. Koinei te momo matepukupuku e tupu ana i roto i te thymus. Ko te maimoatanga matua ko te tango i te repe me te pukupuku mā te pokanga. |
| Ngā pukupuku neuroendocrine | Ko tētahi atu momo pukupuku tēnei ka puta i roto i te repe thymus. |
| Ngā pukupuku pai | I ētahi wā, ka puta mai ngā pukupuku kore-matepukupuku, ngā pukupuku pai rānei, i roto i te repe thymus. Ka tangohia hoki ēnei i roto i tēnei pokanga. |
Me pēhea te whakarite i mua i te pokanga?
I mua i te tango i te manawa, ka tangohia e tō tākuta tō hītori hauora katoa, ā, ka tirotirohia koe e ia. Hei tāpiri, ka mahia pea e rātou ēnei whakamātautau e whai ake nei:
- Whakamātautau mahi pūkahukahu: Mā tēnei ka tirohia te pai o te mahi a ō pūkahukahu.
- Electrocardiogram (EKG): Mā tēnei ka whakamātautau i te ngohe hiko o tō ngākau.
- Whakamātautau ahotea ngākau: He whakamātautau e ine ana i te mahi a te ngākau i te wā e whakakorikori ana.
- Matawai CT (Tomography Rorohiko - Matawai CT): Ka taea e tēnei te whakaputa i ngā whakaahua 3D taipitopito o roto o te tinana. Ka taea e tēnei te āwhina ki te whakatau tika i te rahi me te taunga o te repe thymus.
- Matawai MRI (Whakaahua Āhua Aukume - MRI): Ko tētahi atu tikanga tēnei e tango whakaahua taipitopito ana i ngā kiko o roto i te tinana.
- Matawai PET (Positron Emission Tomography - matawai PET): He mea nui tēnei whakamātautau hei tirotiro i te mahi a ngā pūtau i roto i te tinana, inā koa mēnā he pūtau matepukupuku kei roto.
Ko te mea nui: Me kōrero koe ki tō tākuta mō ngā rongoā katoa, ngā huaora, me ngā tāpiringa e tangohia ana e koe i mua i te pokanga. Kaua e mutu te tango i tētahi rongoā me te kore he tohutohu a tō tākuta. He maha ngā wā ka tonoa koe kia mutu te kai me te inu mai i waenganui pō o te pō i mua i te pokanga.
Hei ārai i ngā uauatanga manawa i muri i te pokanga, inā koa mēnā he myasthenia gravis tōu, ka hoatu pea he immunoglobulin intravenous ki a koe, he rongoā whakawhiti plasma rānei i mua i te pokanga.
Kia ako tātou me pēhea te whakahaere i te pokanga.
E rua ngā huarahi matua e taea ai te mahi i te pokanga thymectomy. Ko tētahi ko te tikanga tuku iho, arā, ko te whakatuwhera i te uma, ko tētahi ko te tikanga, arā, ko te whakamahi i te kāmera me te karetao mā roto i ētahi tapahi iti noa iho. Mā tō taote pokanga e whakatau ko tēhea te tikanga pai mōu.
1. Huarahi whakawhiti-sternal
He rite tēnei ki te pokanga ngākau tuwhera.
- Hipanga 1: Ka whakatuwheratia te uma mā te tapahi i te wheua katoa, i tetahi wāhanga rānei o waenganui o te uma (sternum). Ka kiia tēnei he sternotomy i roto i ngā kupu hauora.
- Hipanga 2: Ka tangohia te repe thymus me ngā kiko katoa e pāngia ana i tōna taha mai i te pūaha.
- Hipanga 3: Whai muri i te pokanga, ka whakanohoia kia kotahi, kia rua rānei ngā ngongo uma ki roto i te uma hei tango i te wai me te toto kua kohia pea ki roto.
- Hipanga 4: Hei whakamutunga, ka honoa anō te wheua o te uma mā te whakamahi i ngā waea, ā, ka tuia te kiri.
2. Āwhina-rorohiko, VATS rānei (tikanga tapahi iti)
He tikanga iti rawa te whakaekenga o tēnei. Ko te VATS he whakarāpopototanga mō te Ataata-Āwhina Pokanga Uma.
- Hipanga 1: E toru ngā kōhao iti ka hangaia ki te taha kotahi o te uma. Ka whakaurua he kāmera mā roto i tētahi o aua kōhao.
- Hipanga 2: Mā te whakamahi i te ringa karetao, i ngā taputapu roa rānei, me te ārahi a ngā whakaahua kāmera, ka wehea marietia te repe thymus (me tetahi pukupuku, mēnā kei roto) mai i ngā kiko e karapoti ana.
- Hipanga 3: Mena e tika ana, ka tapahia he tapahi rite ki tera taha o te uma hei tango katoa i te repe.
- Hipanga 4: Ka whakanohoia ngā kiko katoa kua tangohia ki roto i tētahi putea motuhake i roto i te uma, ka tangohia mai mā roto i tētahi kōhao iti i hangaia.
- Hipanga 5: Ka whakauruhia he ngongo kotahi, e rua rānei hei tango i te wai.
- Hipanga 6: Hei whakaiti i te mamae i muri i te pokanga, ka hoatu he rongoā ki a koe hei aukati i ngā io i roto i te pakitara o te uma.
- Hipanga 7: Hei whakamutunga, ka tangohia ngā taputapu, ā, ka tuia ngā kōhao iti.
E rua ki te whā hāora te roa o tēnei pokanga, i runga i te uauatanga o te pokanga me te tikanga i whakamahia.
He aha ngā mea ka tupu i muri i te pokanga?
I muri i te pokanga, ka puritia koe ki te rūma whakaora kia tae rā anō ki te wā e hoki ake ai tō māramatanga. Ka tangohia te ngongo manawa i whakatakotoria ki te rūma pokanga. I te tīmatanga, me hiahia koe ki te hāora, ki ngā wai uaua, me ngā rongoā whakamamae. I te nuinga o te wā ka whakawhitia koe ki te wāhanga noa i te rā kotahi o te pokanga.
He aha ngā painga me ngā ōrau angitu o tēnei pokanga?
He tino pai ngā hua o tēnei pokanga, inā koa mō te hunga e pāngia ana e te myasthenia gravis me te hunga me pokanga mā roto i ngā tapahi iti.
| Kāwai Painga | Ngā Painga |
|---|---|
| Ngā Painga mō ngā Tūroro Myasthenia Gravis | |
| Ngā whakaurunga hōhipera | Te hekenga o te maha o ngā tāngata e whakaurua ana ki te hōhipera nā te mate. |
| Te whakamahinga o ngā raau taero | Te whakaiti i te hiahia ki te whakamahi i ngā rongoā pēnei i te prednisone. |
| Ngā tohu | Te ngoikore o te uaua kua heke. |
| Whakaora katoa | Tērā pea ka pāngia ētahi tāngata e te murunga hara, ka ngaro katoa atu ō rātou tohumate, ā, ka taea e rātou te ora tonu me te kore rongoā. |
| Ngā Painga o te Pokanga Whakaiti i te Urunga | |
| Te wā i noho ai i te hōhipera | Te noho poto ake i te hōhipera. |
| Te mamae me ngā raruraru | Ka whakaiti i te mōrearea o te mamae, te toto, me ētahi atu raruraru. |
| Whakaora tere | Te kaha ki te hoki wawe ki ngā mahi o ia rā. |
Ko te nuinga o te hunga e pokangahia ana mō te myasthenia gravis ka kite i ngā hua pai i roto i te tau kotahi . Tata ki te 70% ka kite i te whakahekenga o ngā tohu me te hiahia ki te rongoā. I waenga i te 30% me te 40% ka kite i te memeha katoa o ngā tohu.
He maha ngā wā ka taea e te pokanga mō te mate pukupuku thymoma te whakaora katoa i tēnei mate pukupuku.
He aha ngā mōrearea ka puta mai i te pokanga?
Pērā i ngā pokanga katoa, tera pea ētahi mōrearea me ngā raruraru ka pā mai i te thymectomy, engari he tino onge ēnei.
- Te kino ki te ngākau, ki te io, ki te oko toto tata rānei.
- Te toto nui.
- Pneumothorax: Te hinganga o te pukahukahu.
- Pneumonia: He mate pūkahukahu.
- Hemothorax: He kohi toto i waenganui i te pakitara o te uma me te pukahukahu.
- Chylothorax: He kohinga wai i waenganui i te pakitara o te uma me te pukahukahu.
- He tino onge, ka kino haere ngā tohu o te myasthenia gravis ( myasthenic crisis ) i te ahotea o te pokanga.
Te whakaoranga me ngā mea hei tumanakohia i te heke mai
Ko te roa o te whakaoranga e whakawhirinaki ana ki te pokanga tuwhera, ki te pokanga iti rawa rānei. Me noho te nuinga o te tangata ki te hōhipera mō te pō kotahi pea. Ko te mamae o te pokanga ka memeha haere i muri i te rua wiki pea. Me tango e koe ngā rongoā whakamamae mamae i hoatu e tō tākuta ki a koe.
I muri i te pokanga, ka haere tonu te tirotiro a tō tākuta roro i a koe. I runga i ō tohumate, māna e whakatau te roa o te wā e tangohia ai e koe tō rongoā myasthenia gravis me pēhea hoki te whakaiti i te horopeta.
Mō te mate pukupuku thymoma, ka whakawhirinaki te āhua o te mate ki te wāhanga o te mate pukupuku.
- Wāhanga I: Neke atu i te 95% te tūponotanga o te ora katoa.
- Wāhanga II: E 75% ki te 80% te tūponotanga ka ora. Tērā pea ka hiahiatia he rongoā irahiko.
- Wāhanga III: E 25% ki te 40% te tūponotanga ka ora. Tērā pea e hiahiatia ana te rongoā irahiko me te rongoā matū.
Āhea ahau me kite anō i te tākuta?
I muri i te hokinga ki te kāinga i muri i te pokanga, ki te pāngia koe e tētahi o ngā tohu e whai ake nei, me whakamōhio tonu atu koe ki tō tākuta .
- Te uaua ki te manawa.
- Te mamae nui i te taha kotahi o te uma.
- Te manawa tere.
- Te tere o te manawa o te ngakau.
- Te kirika.
- Maremare.
- Te toto e puta mai ana i te patunga pokanga.
- Te hokinga mai o ngā tohu o te myasthenia gravis.
He mea noa ki te tangata te mataku i te rongonga mō te pokanga. Engari kia maumahara, he mahi tonu ēnei a ngā taote pokanga. Ko tā rātou whāinga he hoatu i te hua pai rawa atu ki a koe. Nō reira, kaua e mangere ki te pātai atu ki tō tākuta mō āu pātai mō tō pokanga, mō te tikanga rānei. Ka whakamarie i tō hinengaro.
Karere Tangohia ki te Kāinga
- Ko te thymectomy he tango pokanga i te repe thymus i roto i te uma.
- Ko te nuinga o te wā, ka mahia tēnei pokanga hei rongoā mō ngā mate pēnei i te Myasthenia Gravis me te Thymoma .
- Ka taea te pokanga tuwhera , te pokanga iti rānei te whakaekenga . Mā te tikanga iti te whakaekenga ka tere ake te ora, ka iti ake te mamae me ngā raruraru.
- Ka rerekē pea te roa o te whakaoranga me ngā hua i ia tangata, i ia tangata, ā, i runga anō hoki i te tikanga pokanga.
- Ki te pā mai ētahi tohu rerekē i muri i te pokanga, me whakamōhio tonu atu ki tō tākuta .
- Kōrerohia ō pātai, ō āwangawanga rānei mō tō pokanga ki tō tākuta.

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