He mea rerekē kei roto i ō uaua toto? Me ako tātou mō ēnei (Ngā Mate Pukupuku Toto)?

He wāhi kei roto i tō kiri kua huri te tae, he rite ki ngā puku iti, ā, he mamae i ētahi wā? He wāhi kē rānei kei tō tinana i whānau mai ai tō pēpi, engari te āhua nei kei te nui haere? He mea ngāwari noa iho ēnei. Heoi, i ētahi wā he tohu ēnei o tētahi āhuatanga rerekē e kiia nei ko ngā Vascular Malformations , arā, he rerekētanga i roto i ngā oko toto, arā, ngā oko toto. Nō reira, kaua e manukanuka. Me kōrero tātou mō tēnei mea i roto i ngā taipitopito me te ngāwari i tēnei rā.

He aha ngā āhua o ngā uaua toto? He māmā noa iho...

Ko ngā hapa o te toto he āhuatanga rerekē, he huringa rānei o ngā oko toto o te tinana. He maha ngā wā he whānau mai ēnei. Heoi, i ētahi wā ka kitea i te wā tamarikitanga, taiohitanga, tae noa ki te pakeketanga.

Whakaarohia te pūnaha toto e rere ana puta noa i ō tātou tinana he whatunga rori. I ētahi wā, ina hangaia ēnei rori, ka puta pea ngā hapa iti me ngā hononga hē. Koinei anō te mea e tupu ana i konei.

Ka puta ēnei āhua koretake o te toto ki ngā wāhi katoa o tō tinana, mai i tō mahunga ki ō waewae. I ētahi wā ka puta mai he puranga kiko ngohengohe , he mamae , he pupuhi , he rerekētanga kiri rānei. Ka puta ētahi ki te mata, ki te kaki, ki te taha o te roro, ki te taurakira rānei. Ko ētahi he rite ki ngā tohu whānau, ki ngā ira whero rānei.

He tino onge, ka hoki anō mai i muri i tētahi whara, i tētahi atu huihuinga rānei, i te pakeketanga rānei. Mēnā ka mamae, ka whakararuraru i te tirohanga, ka whakararuraru i ngā mahi o ia rā, ka toto, ka puta rānei ētahi atu raruraru, me rongoā ēnei mate toto.

Kei hea o te tinana ēnei e tino kitea ana?

Ko te tikanga o te kupu "vascular" he "e pā ana ki ngā oko toto." Nō reira, ka pā tēnei āhuatanga ki ngā oko toto katoa i roto i tō tātou pūnaha tohanga toto. Ka pā hoki ki ngā oko toto lymphatic i roto i tō tātou pūnaha lymphatic.

Ko ngā momo oko toto ka pāngia pea ko:

• Ngā uaua me ngā uaua iti - Koinei ngā uaua e kawe ana i te toto whai hāora mai i te ngākau ki ētahi atu okana.
• Ngā Kapireira - He whatunga o ngā uaua toto tino angiangi.
• Ngā uaua me ngā venule - Koinei ngā mea e whakahoki ana i te toto kua whakamahia mai i ngā whekau ki te ngākau.
• Ngā awa lymphatic- Ka kawe ēnei i te wai lymph i roto i te tinana.

He aha ngā momo matua o ngā hapa o te pūnaha toto?

Ka puta pea ēnei āhuatanga hei tohu whānau i runga i te kiri o te pēpi. E ai ki te kōrero i mua ake nei, ka taea te whanake ki ngā wāhi katoa o te tinana, tae atu ki te roro me te taurakira. Ka whakatauhia e ngā tākuta te momo i runga i te momo uaua toto e pāngia ana.

Koinei ētahi o ngā momo e kitea whānuitia ana:

• Te ngoikore o te uaua: Koinei te momo tino noa. E ai ki te ingoa, ka puta i roto i te uaua. Ko ngā uaua ngā oko toto o roto i tō tātou tinana e kawe ana i te toto kore-hāora ki te ngākau. Tērā pea he rite ēnei ki te puku kikorangi, ā, i ētahi wā ka mamae te pā atu.
• Te ngoikore o te Arteriovenous (AVM): He hononga rerekē tēnei o ngā uaua me ngā uaua. I te nuinga o te wā, ka mutu ngā uaua ki ngā capillaries, kātahi ka tīmata ngā uaua. Engari i roto i te AVM, ka rere tika te toto mai i ngā uaua ki roto i ngā uaua, mā roto i tētahi paihere awa rerekē e kiia nei ko te nidus . Ka pā pea tēnei āhuatanga AVM ki te roro, ki te taurakira rānei.
• Te telangiectasia o ngā uaua toto: He wāhi iti tēnei e whakanuia ana ngā uaua toto i roto i te roro. I te nuinga o te wā, ehara ēnei i te raruraru. Heoi, he tino onge, ka puta he toto , arā, he toto.
• Ngā āhua kino o te ana: I tēnei āhua, ka piri pūmau ngā uaua toto o te roro, ka hanga he "ana" roa. Ka tino pōturi te rere o te toto i roto i ēnei ana.
• Ngā ngoikoretanga lymphatic: I roto i tēnei, ka whakanuia ngā awa lymphatic ka hanga he cyst kī tonu i te wai. Ko te nuinga o te wā ka kitea ēnei i roto i ngā kiko ngohengohe pēnei i te mata, te kaki, me ngā rohe axillary.

He aha te rerekētanga i waenga i ngā hemangioma me ngā mate pukupuku toto?

Nā ngā āhuatanga rerekē o te toto e rua i puta ai. Ka puta pea ēnei hei ira, he rite ki ngā tohu whānau. Engari he mārama ngā rerekētanga i waenganui i ngā mea e rua.

• Hemangioma: He pukupuku toto kore-matepukupuku (pai) ēnei. Ka puta mai i te wā e piri tahi ai ngā oko toto i raro i te kiri. Ko te momo e kiia nei ko "hemangioma rōpere" ka puta i muri i te whānautanga o te pēpi. Ka tere te tipu i roto i ngā marama tuatahi e ono o te pēpi. Heoi, he onge te puta o ngā raruraru i roto i ēnei pukupuku, ā, he maha ngā wā ka ngaro noa atu me te kore maimoatanga. Mena he nui te hemangioma, ka whakararuraru i ētahi mahi, ka mamae, ka puta rānei ētahi atu raruraru, ka taea te whakahaere mā te rongoā hei whakaiti tere i tōna matotoru. He onge te hiahia ki te pokanga.

• Ngā ngoikoretanga o te toto:He mea ēnei e kitea ana i te whānautanga, engari kāore pea e kitea tae noa ki te tamarikitanga, ki te pakeketanga rānei. Ka puhoi te tipu. Waihoki, ka horapa hohonu ki roto i ngā kiko me ngā hanganga e karapoti ana, ā, ka puta he raruraru. He maha ngā wā e hiahiatia ana he rongoā mō ngā hapa o te uaua.

He kupu ngāwari: He pukupuku pai te Hemangioma e memeha haere ana. Heoi, ko ngā hapa o te toto he āhuatanga pumau ka tipu, ka raru pea. Nō reira, he mea nui kia wehewehea ngā mea e rua.

He aha ngā hapa o te rere puhoi me te rere tere o ngā oko toto?

He maha ngā hapa o te toto e taka ana ki te wāhanga "rere puhoi" . Ko te tikanga he tino puhoi te neke o te toto i roto i ngā toto e pāngia ana. Ko ngā tauira o tēnei ko ngā hapa o te uaua, te lymphatic, ngā hapa e rua rānei (venolymphatic).

Heoi, ko te AVM (Arteriovenous malformation) he "tere-rere" o ngā oko toto. I roto i tēnei, ka rere te toto mai i ngā uaua ki ngā uaua i te tere nui, i te nuinga o te wā mā roto i tētahi oko toto rerekē e kiia nei ko te nidus . Ina tere te rere o te toto i roto i tētahi AVM nui, me kaha ake te mahi a te ngākau. Ka piki ake te mōrearea o te ngoikore o te ngākau .

E hia te noa o ēnei?

He tino onge ngā mate pēhanga toto. Tata ki te 1% o ngā whānautanga katoa ka puta. O ēnei, ko ngā pēhanga toto, te momo tino noa, ka pā ki te kotahi i roto i te 5,000 ki te 10,000 tāngata.

He aha ngā take o ngā hanganga uaua koretake?

I te nuinga o te wā, ka puta mai ēnei i te rerekētanga o te whanaketanga o ngā oko toto me/ranei ngā awa lymphatic i te wā e tipu ana te tamaiti i roto i te kōpū o te whaea (i roto i te kōpū). Ko te tikanga he whānau mai ēnei.

Kāore i te tino kitea te kino o ngā uaua toto i te wā e whara ana, ā, ka huri hei hapa o ngā uaua toto i roto i te wā. Ka puta anō hoki ngā hapa uaua toto mō te wā tuatahi i muri i tētahi aituā, nā ngā huringa homoni rānei i te wā o te pakeketanga, i te wā e hapu ana rānei .

I roto i tētahi āhuatanga tino onge, ka riro i ētahi tāngata ngā whakarerekētanga ira e whakanui ana i te mōrearea o te whakawhanake i ngā hapa o te toto. Kei te ako tonu ngā kairangahau i ētahi atu kōrero mō ēnei take ira.

Ko wai kei te nui ake te mōrearea ki te whakawhanake i ēnei?

Ka riro i ētahi tāngata ngā huringa ira ka piki ake te mōrearea o ngā hanganga toto ngoikore. Ko ētahi o ēnei āhuatanga ko:

• Te mate puru rapa bleb nevus: Ka puta he hapa o ngā uaua i roto i ō whekau me te pūnaha nakunaku. Ka puta hoki he kikorangi pouri, he whero, he mangu rānei i runga i tō kiri.
• Te mate CLOVES (te tipu nui o te lipomatous whānau, ngā āhua kino o te toto, ngā nevi epidermal me ngā āhua kino o te tuaiwi): Ka puta ngā AVM i roto i tō taurakira. Ka taea hoki e ia te puta he scoliosis ( te piko o te tuaiwi), he tipu o ngā kiko ngako, me te ponana whero pouri.
• Te telangiectasia hemorrhagic tuku iho (e mōhiotia ana ko te mate Osler-Weber-Rendu): Ka puta ngā tangles rerekē, ngā AVM rānei, i roto i ngā capillaries iti.
• Te mate Klippel-Trenaunay (KTS): Ka puta ngā tohu whānau whero-papura e kiia nei ko ngā "waini-poti", ngā tupu o te wheua, o te kiko rānei, me ngā āhua kino e pā ana ki ngā uaua, ki ngā awa lymphatic rānei.
• Te mate Parkes Weber: Ka puta ngā AVM i roto i ō ringaringa, i ō waewae rānei.

Mena kei a koe ēnei āhuatanga ira, he mea nui kia mōhio koe ki aua āhuatanga.

He aha ngā tohu o ngā ngoikoretanga o te pūnaha toto?

Ko ngā tohumate e whakawhirinaki ana ki te momo āhua o te mate. Ko te āhua o te mate toto e pā ana ki tō kiri, tera pea ka rite ki te tohu whānau whero, kikorangi, papura, parauri, mangu rānei e ara ake ana . Ka pupuhi, ka toto, ka mamae rānei ēnei ira.

Mena he AVM kei roto i tō roro , kāore pea he tohu e pā mai ana kia toto rā anō. Mena ka toto te AVM o te roro, ka pāngia pea koe e te ānini, e te haurangi, e te pararutiki rānei i te taha kotahi o tō tinana .

Ka taea e ngā āhua ngoikore o te uaua te whakararu i te mamae, te pupuhi, te raruraru ki te toto totoka, me te kino o ngā okana.

Me pēhea te tautuhi i ēnei? Me pēhea te kimi a te tākuta i tēnei?

Nā te mea kāore e puta he tohu i ngā wā katoa i ngā hapa o ngā toto, ka kitea e ngā tākuta te mate i ētahi wā i a rātou e whakamātautau ana mō tētahi atu raruraru.

Ka whakamahia e ngā tākuta ngā whakamātautau whakaahua motuhake hei tirotiro i te rere o te toto me te kite i ngā hapa o ngā oko toto. Kei roto i ēnei whakamātautau:

• Ko te ultrasound , e kiia ana hoki ko te ultrasound vascular .
• MRI (Ata Whakaahua Āhua Aukume) , kei roto hoki ko te whakamātautau e kiia nei ko te MR Angiogram (MRA) .
• Ko te matawai CT (matawai Tomography Rorohiko), kei roto hoki he whakamātautau e kiia nei ko te CT angiogram .
• Angiogram me/ranei venogram .
• Ngā hihi -X noa .

Ka taea e ēnei whakamātautau te kite mārama i te āhua o ngā uaua toto i te rohe, te rere o te toto, me te mea kei te whaiti, kei te whānui rānei tetahi mea rerekē.

He aha te rongoā mō tēnei?

Ko te whāinga matua o te maimoatanga mō ngā mate pūngao toto he whakaiti i ngā tohu me ngā raruraru pea. Ko ngā mate pūngao kāore e puta he raruraru, kāore pea e hiahiatia he maimoatanga, ā, ka kitea noa iho i roto i te wā.

Ko te maimoatanga e whakawhirinaki ana ki te momo oko toto e pāngia ana. He maha ngā wā, ko ēnei maimoatanga he kati, he tango pokanga rānei i te oko toto e pāngia ana. He maha ngā āhua kino ka taea te rongoā mā te whakamahi i ngā tikanga iti rawa te whakaekenga . Ka whakamahia pea e ngā tākuta ngā tikanga pēnei i:

• Te Whakaora-ā-whatu: I tēnei mahi, ka werohia he rongoā motuhake ki roto i te uaua toto e pāngia ana, ā, ka mimiti, ka kati hoki te uaua toto.
• Te whakatō catheter: I roto i tēnei tikanga, ka tukuna he ngongo iti (catheter) mā roto i tētahi oko toto, ā, ka hiritia te oko toto rerekē mai i roto.
• Ngā maimoatanga taiaho: Ka whakamahia tēnei mō ētahi āhua kiri koretake.
• Te rongoā irahiko (pokanga irahiko): Ka whakamahia tēnei mō ētahi āhua hōhonu, uaua ki te pokanga.

I ētahi wā, ka tūtohu pea tō tākuta i tētahi koiora , arā, ko te tango i tētahi wahi kiko hei tirotiro. Ka āwhina tēnei ki te whakaū i te mate me/ranei te tiki kiko hei whakamātautau ira .

Nā te mea he uaua, he onge hoki ngā mate pēnei i te mate toto, he pai ake te whakahaere i ēnei mā te mahi tahi a te rōpū e whai wāhi mai ana ngā tohunga maha .

Ka taea e ēnei te puta anō i muri i te maimoatanga?

Ae, ka taea e ngā mate toto te hoki mai anō ahakoa kua oti te maimoatanga. Nō reira, me haere tonu pea koe ki te tirotiro me te whakamātautau i ia wā kia kitea wawe ai ngā mate e hoki mai ana.

He ara hei ārai i ēnei kei puta?

He mea whānau mai ngā koha toto, arā, kāore he huarahi hei ārai i ēnei.

Heoi, ki te mea he mate ira tō tetahi o tō whānau e puta ai ngā hapa o ngā oko toto, me toro atu pea koe ki tētahi kaitohutohu ira.Ka taea e tēnei tohunga te whakamārama ki a koe ngā kōwhiringa e wātea ana hei whakaiti i te mōrearea o te tuku i tēnei mate ki āu tamariki.

He aha ngā raruraru ka puta mai i ēnei āhua koretake o te toto?

Kāore ētahi āhua hē e puta ai he raruraru, ā, ka kitea noa iho. Heoi, i roto i te nuinga o ngā wā, ka mamae, ka pupuhi hoki .

Ka taea e ētahi āhua koretake te whakararu i te uaua, te hononga, te io rānei, ka whakararuraru pea i te whakakori tinana, ngā hākinakina, te mahi, ngā mahi o ia rā rānei .

Ka taea e ngā hanganga nui, rere nui te arahi ki te ngoikore o te ngakau .

Ka taea e ngā ngoikoretanga o ngā toto totoka i roto i ngā whekau totoka pērā i te ate, te whatukuhu, te kōpū rānei te whakararu i te mahi a ngā whekau me ētahi atu raruraru.

Ka taea e ētahi o ngā hanganga uaua, pērā i ngā AVM i roto i te roro, i te taurakira rānei, te whakaiti i te nui o te toto whai hāora e tae atu ana ki te roro. Ka taea e tēnei te arahi ki ngā raruraru morearea, pērā i:

• Ngā aneurysm ( te ngoikore o te pakitara o ngā oko toto me te pupuhi pērā i te poihau)
• Te toto i roto i te angaanga
• Ngā whiu

He aha te heke mai mō te hunga whai mate pēnei? He aha te pānga o tēnei ki ō rātou oranga?

Ka pāngia te āhua me te whakapono o te tangata e ngā mate toto ngoikore, e rite ana ki ngā tohu whānau. Ka arahi pea tēnei ki ngā āhuatanga hinengaro pērā i te pouri me te manukanuka . Heoi, he pai te urupare a te nuinga o ēnei mate ki te rongoā.

Ko ngā āhua kino rawa atu, pērā i ngā AVM i roto i te roro, ka mōrearea pea te ora mēnā ka tīmata te toto.

Engari, ko te mea nui, ka taea te rongoā i te nuinga o ngā koha, ā, ka pai te urupare ki te maimoatanga. Nō reira, he mea nui kia rapu tohutohu hauora tika, kaua e mataku.

He aha ngā mea me pātai atu koe ki tō tākuta?

Mena he ruarua āu mō tēnei mate, mēnā rānei kua kitea tō mate, ka taea e koe te pātai atu ki tō tākuta i ēnei pātai:

• Nā te aha ahau i pā mai ai tēnei mate toto? (He aha te take?)
• He aha te momo mate toto kei a au?
• He aha te maimoatanga pai rawa atu mōku?
• He aha ngā mōrearea, ngā pānga taha rānei ka puta mai i te maimoatanga?
• Me āwangawanga ahau mō ngā tohu o ngā raruraru? He aha aua tohu?

Pātaihia ēnei pātai, kia mārama ai koe ki tō āhuatanga.

Hei whakamutunga, ko ngā mea tino nui hei maumahara (Karere hei tango ki te kāinga)

Āe, me titiro tātou ki ngā tino kōrero hei maumahara māu mai i ngā mea kua kōrerotia e tātou.

• He rerekētanga onge ngā koha toto i te whānautanga mai, ā, he maha ngā wā ka puta mai i te whānautanga mai anō.
• Ka puta ēnei i ngā wāhi katoa o te tinana , ka whakaatu i ngā tohu rerekē, i ētahi wā kāore rānei he tohu e puta.
• He rerekē ngā Hemangioma me ngā Vascular Malformations. He mea nui kia mōhio ki te rerekētanga i waenganui i ngā mea e rua.
• He maha ngā maimoatanga mō tēnei mate. Mā tō tākuta e whakatau te maimoatanga pai rawa atu mōu.
• Ka taea e ētahi momo mate kino, inā koa ko ngā AVM i roto i te roro, te whakararuraru i a rātou, nō reira he mea nui te tirotiro tika a te rata.
• Ki te pāngia koe, tāu tamaiti rānei e tētahi o ēnei tohu, kaua e mataku, engari me toro atu ki te tākuta mō ētahi tohutohu.

Kia maumahara, ehara i te mea ko koe anake i te wā e pāngia ana e tēnei mate. Mā te mōhiotanga tika me te tautoko hauora, ka taea te whakahaere pai i tēnei mate.

Ngā hapa o ngā uaua toto, ngā rerekētanga o ngā uaua toto, ngā tohu whānau, ngā AVM, ngā hapa o ngā uaua toto, ngā raruraru o ngā uaua toto, ngā mate whānautanga