ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯅꯧꯅꯥ ꯄꯣꯀꯄꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯍꯥꯔꯇꯀꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯥ ꯂꯩꯔꯦ ꯍꯥꯌꯅꯥ ꯍꯥꯌꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯐꯥꯎꯔꯤꯕꯥ ꯐꯤꯚꯝ ꯑꯗꯨ ꯐꯣꯡꯗꯣꯀꯄꯥ ꯉꯃꯗꯦ꯫ ꯑꯀꯤꯕꯥ, ꯁꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯑꯗꯨꯒꯥ ꯂꯣꯌꯅꯅꯥ "ꯑꯩꯈꯣꯌꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯀꯔꯤ ꯑꯣꯏꯒꯅꯤ?" ꯅꯍꯥꯛꯀꯤ ꯋꯥꯈꯂꯗꯥ ꯏꯀꯣꯛ ꯅꯣꯟꯖꯔꯤ꯫ ꯌꯥꯝꯅꯥ ꯂꯨꯕꯥ ꯃꯇꯝ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯑꯁꯤꯒꯨꯝꯕꯥ ꯃꯇꯝ ꯑꯁꯤꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯈꯉꯕꯥ ꯑꯁꯤꯅꯤ꯫ ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯍꯥꯏꯄꯣꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯂꯦꯐꯠ ꯍꯥꯔꯠ ꯁꯤꯟꯗꯣꯝ (HLHS)ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯒꯅꯤ, ꯃꯁꯤ ꯄꯣꯀꯄꯗꯥ ꯉꯥꯏꯔꯤꯕꯥ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯃꯁꯨꯡ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯊꯣꯀꯄꯥ ꯍꯥꯔꯇꯀꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯋꯥꯔꯣꯜ ꯑꯁꯤꯗꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ, ꯑꯗꯣꯝꯅꯥ ꯈꯉꯕꯤꯕꯥ ꯌꯥꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯒꯅꯤ꯫
ꯍꯥꯏꯄꯣꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯂꯦꯐꯠ ꯍꯥꯔꯠ ꯁꯤꯟꯗ꯭ꯔꯣꯝ (HLHS) ꯍꯥꯌꯕꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯀꯔꯤꯅꯣ?
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯍꯥꯏꯄꯣꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯂꯦꯐꯠ ꯍꯥꯔꯠ ꯁꯤꯟꯗ꯭ꯔꯣꯝ (HLHS) ꯍꯥꯌꯕꯁꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯍꯥꯔꯇꯀꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯁꯦꯃꯒꯠꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯀꯣꯟꯖꯤꯅꯤꯑꯦꯜ ꯍꯥꯔꯇꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ "ꯍꯥꯏꯄꯣꯞꯂꯥꯁ꯭ꯇꯤꯛ" ꯍꯥꯌꯕꯥ ꯋꯥꯍꯩ ꯑꯁꯤꯒꯤ ꯑꯔꯊꯗꯤ "ꯑꯟꯗꯔꯗꯤꯚꯦꯂꯄꯃꯦꯟꯇ" ꯍꯥꯌꯕꯅꯤ꯫
ꯑꯩꯈꯣꯌꯒꯤ ꯊꯝꯃꯣꯌ ꯑꯁꯤ ꯔꯨꯝ ꯃꯔꯤ ꯂꯩꯕꯥ ꯑꯄꯤꯀꯄꯥ ꯌꯨꯝ ꯑꯃꯒꯨꯝꯕꯅꯤ꯫ ꯃꯊꯛꯇꯥ ꯔꯨꯝ ꯑꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯈꯥꯗꯥ ꯔꯨꯝ ꯑꯅꯤ꯫ HLHSꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯒꯤ ꯊꯝꯃꯣꯌꯒꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯀꯁꯤꯡ, ꯃꯔꯨꯑꯣꯏꯅꯥ:
- ꯂꯦꯐꯠ ꯚꯦꯟꯇꯤꯂꯦꯇꯔ (left ventricle): ꯃꯁꯤ ꯍꯥꯔꯇꯀꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯄꯝꯄ ꯆꯦꯝꯕꯔꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯍꯀꯆꯥꯡ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯁꯦꯡꯂꯕꯥ, ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯎꯕꯥ ꯏ ꯄꯝꯄ ꯇꯧꯏ꯫ HLHSꯗꯥ, ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯄꯤꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯆꯥꯎꯈꯠꯄꯥ ꯂꯩꯇꯦ꯫
- ꯑꯦꯑꯣꯔꯇꯥ (Aorta): ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯚꯦꯟꯇꯤꯂꯦꯇꯔꯗꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯥ ꯏ ꯄꯨꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯜ꯫ ꯃꯁꯤꯁꯨ ꯑꯌꯥꯝꯕꯅꯥ ꯑꯄꯤꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯑꯄꯤꯀꯄꯥ ꯑꯣꯏ꯫
- ꯃꯥꯏꯠꯔꯜ ꯑꯃꯁꯨꯡ ꯑꯦꯑꯣꯔꯇꯤꯛ ꯚꯜꯌꯨꯁꯤꯡ: ꯃꯈꯣꯌ ꯑꯁꯤ ꯊꯣꯡꯅꯥꯎꯒꯨꯝꯅꯥ ꯑꯣꯏ꯫ ꯃꯈꯣꯌꯅꯥ ꯃꯥꯌꯀꯩ ꯑꯃꯈꯛꯇꯗꯥ ꯏ ꯆꯦꯅꯕꯥ ꯌꯥꯍꯜꯂꯤ꯫ HLHSꯗꯥ, ꯚꯜꯌꯨꯁꯤꯡ ꯑꯁꯤ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯁꯦꯃꯒꯠꯄꯥ ꯉꯃꯗꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯊꯤꯡꯖꯤꯅꯕꯥ ꯌꯥꯏ꯫
ꯑꯆꯧꯕꯥ ꯁꯔꯨꯀꯁꯤꯡ ꯑꯁꯤ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯆꯥꯎꯈꯠꯄꯥ ꯉꯃꯗꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯍꯥꯔꯇꯀꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨꯅꯥ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯎꯕꯥ ꯏ ꯃꯇꯤꯛ ꯆꯥꯅꯥ ꯄꯝꯄ ꯇꯧꯕꯥ ꯉꯃꯗꯦ꯫ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯍꯥꯔꯇꯀꯤ ꯃꯊꯛꯀꯤ ꯆꯦꯝꯕꯔ ꯑꯅꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯋꯥꯜ ꯑꯗꯨꯗꯥ ꯑꯄꯤꯀꯄꯥ ꯍꯨꯔꯥꯅꯕꯥ ꯑꯃꯥ ꯂꯩꯕꯥ ꯌꯥꯏ, ꯃꯗꯨꯕꯨ ꯑꯦꯠꯔꯤꯌꯥꯜ ꯁꯦꯞꯇꯜ ꯗꯤꯐꯦꯛꯇ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫
ꯃꯁꯤꯒꯥ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯕꯥ ꯊꯝꯃꯣꯌ ꯑꯃꯒꯥ ꯀꯔꯤ ꯈꯦꯠꯅꯕꯥ ꯂꯩꯕꯒꯦ?
ꯍꯀꯆꯥꯡ ꯐꯕꯥ ꯊꯝꯃꯣꯌ ꯑꯃꯗꯥ, ꯑꯔꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯔꯣꯏꯕꯥ ꯑꯅꯤꯃꯛꯅꯥ ꯄꯨꯟꯅꯥ ꯊꯕꯛ ꯇꯧꯃꯤꯟꯅꯩ꯫ ꯑꯔꯣꯏꯕꯥ ꯃꯐꯝ ꯑꯗꯨꯅꯥ ꯍꯀꯆꯥꯡꯗꯒꯤ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯑꯣꯗꯕꯥ ꯏ ꯑꯗꯨ ꯂꯧꯊꯣꯛꯇꯨꯅꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯐꯪꯅꯕꯥ ꯂꯪꯁꯇꯥ ꯊꯥꯏ ꯍꯥꯌꯅꯥ ꯈꯅꯕꯤꯌꯨ꯫ ꯂꯪꯁꯇꯒꯤ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯝꯅꯥ ꯌꯥꯎꯕꯥ ꯏ ꯑꯗꯨ ꯍꯥꯔꯇꯀꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨꯗꯥ ꯍꯟꯖꯤꯜꯂꯀꯏ꯫ ꯑꯗꯨꯗꯒꯤ ꯂꯦꯡ-ꯑꯣꯠꯄꯗꯥ ꯂꯩꯕꯥ ꯁꯛꯇꯤ ꯂꯩꯕꯥ ꯄꯝꯄ (left ventricle) ꯑꯗꯨꯅꯥ ꯏ ꯑꯗꯨ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯥ ꯄꯝꯄ ꯇꯧꯏ꯫
ꯑꯗꯨꯕꯨ HLHSꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯗꯥ, ꯊꯝꯃꯣꯌꯒꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯊꯣꯀꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯃꯁꯤꯅꯥ ꯊꯕꯛ ꯑꯗꯨ ꯇꯧꯕꯥ ꯉꯃꯗꯦ꯫ ꯑꯗꯨꯅꯥ ꯀꯔꯤ ꯑꯣꯏꯒꯅꯤ? ꯊꯝꯃꯣꯌꯒꯤ ꯑꯔꯣꯏꯕꯥ ꯃꯐꯝ ꯑꯗꯨꯅꯥ ꯊꯕꯛ ꯑꯅꯤꯃꯛ ꯃꯁꯥꯅꯥ ꯇꯧꯖꯒꯗꯕꯅꯤ . ꯃꯁꯤꯅꯥ ꯇꯥꯀꯄꯗꯤ ꯔꯥꯏꯠ ꯚꯦꯟꯇꯤꯂꯦꯇꯔꯅꯥ ꯂꯪꯁꯇꯥ ꯏ ꯄꯝꯄ ꯇꯧꯒꯗꯕꯅꯤ, ꯑꯗꯨꯒꯥ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯁꯨ ꯏ ꯄꯝꯄ ꯇꯧꯒꯗꯕꯅꯤ꯫
ꯃꯁꯤ ꯀꯔꯝꯅꯥ ꯑꯣꯏꯔꯤꯕꯅꯣ? ꯑꯉꯥꯡ ꯑꯃꯅꯥ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ, ꯍꯥꯔꯇꯀꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯏꯒꯤ ꯈꯣꯡꯖꯦꯜ ꯑꯅꯤꯒꯤ ꯃꯔꯛꯇꯥ ꯃꯇꯝ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯥ ꯃꯔꯤ ꯂꯩꯅꯩ꯫ ꯃꯁꯤꯕꯨ ꯗꯛꯇꯁ ꯑꯥꯔꯇꯦꯔꯤꯑꯣꯁꯁ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ꯃꯁꯤ ‘ꯁꯣꯔꯇꯀꯠ’ ꯑꯃꯒꯨꯝꯕꯅꯤ꯫ ꯃꯁꯤꯒꯤ ‘ꯁꯣꯔꯇꯀꯠ’ ꯑꯁꯤ HLHSꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯅꯥ ꯄꯣꯀꯄꯥ ꯃꯇꯨꯡꯗꯥ ꯍꯤꯡꯅꯕꯒꯤꯗꯃꯛ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯃꯔꯃꯗꯤ ꯏ ꯑꯁꯤ ꯇꯤꯎꯕ ꯑꯁꯤꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯍꯀꯆꯥꯡꯗꯥ ꯆꯦꯜꯂꯤ꯫ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯅꯥ, ꯇꯤꯎꯕ ꯑꯁꯤ ꯑꯉꯥꯡ ꯄꯣꯀꯄꯥ ꯃꯇꯨꯡ ꯅꯨꯃꯤꯠ ꯈꯔꯅꯤꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯊꯤꯡꯖꯤꯜꯂꯤ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯇꯤꯎꯕ ꯑꯁꯤ HLHS ꯂꯩꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯗꯥ ꯊꯤꯡꯖꯤꯜꯂꯕꯗꯤ, ꯍꯀꯆꯥꯡꯗꯥ ꯏ ꯆꯦꯅꯕꯥ ꯌꯥꯕꯒꯤ ꯃꯑꯣꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯥꯏꯌꯦꯡꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯗꯤ, ꯑꯉꯥꯡ ꯑꯃꯅꯥ ꯍꯤꯡꯅꯕꯒꯤꯗꯃꯛ ꯅꯨꯃꯤꯠ ꯈꯔꯅꯤ ꯈꯛꯇꯃꯛ ꯂꯩꯒꯅꯤ꯫
ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯅꯍꯥꯛꯅꯥ ꯀꯔꯝꯅꯥ ꯈꯪꯒꯅꯤ? ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯧꯅꯥ ꯄꯣꯀꯄꯥ ꯑꯉꯥꯡ ꯑꯃꯗꯥ HLHS ꯂꯩꯔꯕꯗꯤ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯑꯍꯥꯅꯕꯗꯥ ꯎꯕꯥ ꯐꯪꯗꯦ꯫ ꯑꯗꯨꯕꯨ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯄꯨꯡ ꯈꯔꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯅꯠꯠꯔꯒꯥ ꯅꯨꯃꯤꯠ ꯈꯔꯅꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯃꯥ-ꯃꯄꯥꯁꯤꯡꯅꯥ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯈꯪꯖꯤꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫
| ꯂꯥꯏꯑꯣꯡ꯫ | ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯁꯟꯗꯣꯛꯅꯥ ꯇꯥꯀꯏ꯫ |
|---|---|
| ꯁꯥꯏꯅꯣꯁꯤꯁ (ꯁꯥꯏꯅꯣꯁꯤꯁ)꯫ | ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯈꯣꯡ, ꯃꯈꯣꯡ ꯑꯃꯁꯨꯡ ꯃꯈꯨꯠꯁꯤꯡ ꯑꯗꯨ ꯅꯤꯜ ꯅꯠꯠꯔꯒꯥ ꯑꯁꯪꯕꯥ ꯃꯆꯨ ꯑꯣꯏꯔꯀꯏ꯫ ꯃꯁꯤ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯋꯥꯠꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯣꯏꯔꯤ꯫ |
| ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫ | ꯑꯉꯥꯡ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯉꯝꯂꯤ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯋꯥꯕꯥ ꯎꯏ꯫ |
| ꯁꯉ꯭ꯒꯣꯝ ꯊꯀꯄꯗꯥ ꯑꯋꯥꯕꯥ꯫ | ꯑꯩꯅꯥ ꯁꯉ꯭ꯒꯣꯝ ꯊꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯠꯂꯤ, ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯍꯧꯔꯀꯏ, ꯑꯃꯁꯨꯡ ꯈꯔꯥ ꯊꯀꯄꯥ ꯃꯇꯨꯡꯗꯥ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯍꯧꯔꯀꯏ꯫ |
| ꯂꯦꯊꯥꯔꯖꯤ (ꯂꯦꯊꯔꯖꯤ)꯫ | ꯑꯉꯥꯡ ꯑꯗꯨ ꯄꯨꯟꯁꯤ ꯂꯩꯇꯕꯥ ꯎꯏ, ꯃꯇꯝ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯇꯨꯝꯕꯥ ꯉꯃꯗꯕꯥ ꯑꯃꯁꯨꯡ ꯋꯥꯈꯜ ꯇꯥꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯑꯣꯏ꯫ |
| ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯍꯥꯔꯇꯀꯤ ꯈꯣꯡꯖꯦꯜ ꯌꯥꯡꯕꯥ꯫ | ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠ ꯑꯗꯨ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯀꯣꯀꯊꯣꯡꯕꯗꯥ ꯊꯝꯂꯕꯥ ꯃꯇꯃꯗꯥ, ꯊꯝꯃꯣꯌ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯌꯥꯡꯅꯥ ꯆꯦꯜꯂꯀꯄꯒꯨꯝ ꯐꯥꯑꯣꯏ꯫ |
| ꯀꯣꯜꯗ, ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯈꯣꯡꯎꯞ꯫ | ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯈꯨꯠ ꯑꯃꯁꯨꯡ ꯃꯈꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯨꯄꯁꯤꯜꯂꯤ꯫ ꯈꯣꯡꯗꯥ ꯀ꯭ꯂꯦꯝ ꯑꯃꯁꯨꯡ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ ꯐꯥꯎꯏ꯫ |
| ꯋꯥꯏꯛ ꯄꯂꯁ꯫ | ꯅꯍꯥꯛꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯄꯂꯁ ꯑꯗꯨ ꯐꯥꯎꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯃꯗꯨ ꯌꯥꯝꯅꯥ ꯇꯞꯅꯥ ꯇꯞꯅꯥ ꯁꯣꯟꯊꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯣꯟꯊꯕꯥ ꯐꯥꯎꯏ꯫ |
ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯗꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯅꯤ ꯎꯔꯕꯗꯤ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯃꯗꯒꯤ ꯍꯦꯅꯕꯥ ꯂꯩꯔꯕꯗꯤ ꯈꯨꯗꯛꯇꯥ ꯗꯣꯛꯇꯔꯒꯥ ꯇꯥꯟꯅꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ .
ꯀꯔꯤꯒꯤꯗꯃꯛꯇꯥ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯃꯁꯤ ꯊꯣꯛꯂꯤꯕꯅꯣ? ꯃꯔꯝ ꯀꯔꯤꯅꯣ?
ꯋꯥꯍꯪ ꯑꯁꯤ ꯃꯃꯥ-ꯃꯄꯥ ꯈꯨꯗꯤꯡꯃꯛꯀꯤ ꯋꯥꯈꯂꯗꯥ ꯂꯩꯔꯤ꯫ "ꯑꯩꯈꯣꯌꯒꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯗꯥ ꯀꯔꯤꯒꯤ ꯃꯁꯤ ꯊꯣꯀꯈꯤꯕꯅꯣ? ꯑꯩꯈꯣꯌꯅꯥ ꯑꯔꯥꯅꯕꯥ ꯑꯃꯥ ꯇꯧꯈꯤꯕ꯭ꯔꯥ?"
ꯑꯗꯨꯕꯨ ꯑꯆꯨꯝꯕꯥ ꯑꯗꯨꯗꯤ, ꯑꯌꯥꯝꯕꯥ ꯀꯦꯁꯁꯤꯡꯗꯥ, HLHS ꯒꯤ ꯑꯀꯛꯅꯕꯥ ꯃꯔꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫ ꯍꯥꯌꯕꯗꯤ ꯃꯃꯥ ꯅꯠꯔꯒꯥ ꯃꯄꯥꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯋꯥꯐꯝ ꯅꯠꯇꯦ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯖꯦꯅꯦꯇꯤꯛ ꯐꯦꯛꯇꯔꯁꯤꯡꯅꯥ ꯊꯧꯗꯥꯡ ꯂꯧꯕꯥ ꯌꯥꯏ꯫ ꯍꯥꯌꯕꯗꯤ, ꯏꯃꯨꯡꯗꯥ ꯑꯀꯛꯅꯕꯥ ꯖꯤꯅꯦꯇꯤꯛ ꯑꯣꯏꯕꯥ ꯑꯍꯣꯡꯕꯁꯤꯡꯅꯥ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯇꯔꯅꯔ ꯁꯤꯟꯗꯣꯝ ꯅꯠꯠꯔꯒꯥ ꯇ꯭ꯔꯥꯏꯁꯣꯃꯤ 18ꯒꯨꯝꯕꯥ ꯑꯇꯩ ꯖꯦꯅꯦꯇꯤꯛ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯂꯩꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯗꯁꯨ HLHSꯒꯤ ꯔꯤꯁ꯭ꯛ ꯂꯩ꯫
ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯃꯇꯧ ꯀꯔꯝꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯑꯆꯨꯝꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯈꯉꯗꯣꯀꯄꯥ ꯉꯃꯒꯅꯤ?
ꯅꯨꯡꯉꯥꯏꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯉꯁꯤꯒꯤ ꯑꯍꯣꯡꯕꯥ ꯇꯦꯛꯅꯣꯂꯣꯖꯤ ꯑꯁꯤꯅꯥ ꯑꯉꯥꯡ ꯄꯣꯀꯄꯥ ꯃꯃꯥꯡꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯃꯤꯔꯣꯜꯂꯤꯉꯩ ꯃꯇꯃꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯈꯉꯗꯣꯀꯄꯥ ꯉꯝꯂꯦ . ꯀꯔꯤꯒꯨꯝꯕꯥ ꯔꯨꯇꯤꯟ ꯄ꯭ꯔꯤꯅꯦꯇꯦꯜ ꯑꯂꯠꯔꯥꯁꯥꯎꯟꯗ ꯁ꯭ꯀꯦꯟ ꯑꯃꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯍꯥꯔꯇꯇꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯂꯤꯇꯤ ꯑꯃꯥ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯀꯄꯨ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯑꯃꯗꯥ ꯔꯤꯐꯔ ꯇꯧꯒꯅꯤ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯀꯄꯨ ꯐꯤꯇꯁ ꯏꯀꯣꯀꯥꯔꯗꯤꯑꯣꯒ꯭ꯔꯥꯐ ꯑꯃꯥ ꯇꯧꯅꯕꯥ ꯍꯥꯌꯒꯅꯤ꯫ ꯃꯁꯤꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯊꯝꯃꯣꯌꯒꯤ ꯁ꯭ꯠꯔꯀꯆꯔ ꯑꯃꯁꯨꯡ ꯐꯉ꯭ꯀꯁꯟ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯎꯕꯥ ꯉꯃꯍꯜꯂꯤ꯫
ꯑꯉꯥꯡ ꯑꯗꯨ ꯄꯣꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯈꯪꯗꯣꯛꯅꯕꯥ ꯗꯣꯛꯇꯔꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯌꯦꯡꯒꯅꯤ ꯑꯃꯁꯨꯡ ꯁ꯭ꯇꯦꯊꯣꯁ꯭ꯀꯣꯞ ꯑꯃꯅꯥ ꯆꯦꯛꯁꯤꯟꯅꯥ ꯌꯦꯡꯗꯨꯅꯥ ꯍꯥꯔꯇꯀꯤ ꯈꯣꯟꯖꯦꯜ (hart murmur) ꯑꯃꯥ ꯂꯩꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯒꯅꯤ꯫ ꯃꯗꯨꯒꯤ ꯃꯇꯨꯡꯗꯥ, ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯅꯕꯥ ꯇꯦꯁ꯭ꯠ ꯀꯌꯥ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯅꯤ, ꯃꯈꯣꯌꯁꯤꯡ ꯑꯗꯨꯗꯤ:
- ꯆꯦꯁ꯭ꯠ ꯑꯦꯛꯁ-ꯔꯦ: ꯆꯦꯁ꯭ꯠ ꯑꯦꯛꯁ-ꯔꯦ ꯑꯃꯅꯥ ꯍꯥꯔꯠ ꯑꯃꯁꯨꯡ ꯂꯪꯁꯀꯤ ꯁꯥꯏꯖ ꯑꯃꯁꯨꯡ ꯃꯑꯣꯡ-ꯃꯇꯧ ꯑꯗꯨ ꯆꯦꯛ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫
- ꯏꯀꯣꯀꯥꯔꯗꯤꯑꯣꯒ꯭ꯔꯥꯐ: ꯃꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯇꯦꯁ꯭ꯇꯅꯤ꯫ ꯃꯁꯤ ꯊꯝꯃꯣꯌꯒꯤ ꯚꯤꯗꯤꯑꯣ ꯁ꯭ꯀꯦꯟ ꯑꯃꯒꯨꯝꯕꯅꯤ꯫ ꯍꯥꯔꯇꯀꯤ ꯆꯦꯝꯕꯔꯁꯤꯡ, ꯚꯜꯌꯨꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯂꯁꯤꯡ ꯄꯨꯝꯅꯃꯛ ꯃꯌꯦꯛ ꯁꯦꯡꯅꯥ ꯎꯕꯥ ꯐꯪꯏ꯫ ꯃꯁꯤꯅꯥ HLHS ꯂꯩꯕꯥ ꯑꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯔꯤ꯫
- ꯏꯂꯦꯛꯠꯔꯣꯀꯥꯔꯗꯤꯑꯣꯒ꯭ꯔꯥꯝ (EKG): ꯍꯥꯔꯇꯀꯤ ꯏꯂꯦꯛꯠꯔꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯜꯂꯤꯕꯥ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯤ꯫
- ꯄꯂꯁ ꯑꯣꯛꯁꯤꯃꯦꯇꯔꯤ ꯁ꯭ꯛꯔꯤꯅꯤꯡ: ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯃꯈꯨꯠ ꯅꯠꯠꯔꯒꯥ ꯅꯥꯀꯣꯡꯗꯥ ꯑꯄꯤꯀꯄꯥ ꯀ꯭ꯂꯤꯄꯒꯨꯝꯕꯥ ꯈꯨꯠꯂꯥꯏ ꯑꯃꯥ ꯊꯃꯗꯨꯅꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯜꯂꯤ꯫ ꯃꯁꯤꯒꯤ ꯚꯦꯜꯌꯨ ꯑꯁꯤ HLHS ꯂꯩꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯗꯥ ꯅꯦꯝꯃꯤ꯫
ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯒꯤ ꯂꯥꯏꯌꯦꯡ ꯂꯩꯕ꯭ꯔꯥ? ꯑꯉꯥꯡ ꯑꯗꯨ ꯀꯅꯕꯤꯕꯥ ꯉꯃꯒꯗ꯭ꯔꯥ?
ꯍꯣꯌ, ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ, ꯑꯗꯨꯕꯨ ꯂꯥꯏꯌꯦꯡꯁꯨ ꯂꯩ꯫ ꯑꯗꯨꯕꯨ ꯃꯁꯤ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯁꯤꯖꯤꯟꯅꯗꯨꯅꯥ ꯐꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯄꯨꯟꯁꯤ ꯀꯟꯅꯕꯥ, ꯁ꯭ꯇꯦꯖ ꯀꯌꯥ ꯌꯥꯎꯕꯥ ꯀꯃꯞꯂꯦꯛꯁ ꯑꯣꯏꯕꯥ ꯁꯔꯖꯔꯤꯒꯤ ꯁꯤꯔꯤꯖ ꯑꯃꯥ ꯄꯥꯡꯊꯣꯛꯀꯗꯕꯅꯤ꯫
ꯈꯣꯡꯊꯥꯡ ꯑꯃꯥ: ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯁ꯭ꯇꯦꯕꯤꯂꯥꯏꯖ ꯇꯧꯕꯥ꯫
ꯁꯔꯖꯔꯤꯒꯤ ꯃꯃꯥꯡꯗꯥ, ꯑꯉꯥꯡ ꯑꯗꯨ ꯁ꯭ꯇꯦꯕꯤꯂꯥꯏꯖ ꯇꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯏ꯫ ꯑꯍꯥꯅꯕꯥ ꯈꯣꯡꯊꯥꯡꯗꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯈꯤꯕꯥ ‘ꯁꯣꯔꯇꯀꯠ’ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯜ , ꯗꯛꯇꯁ ꯑꯥꯔꯇꯦꯔꯤꯑꯣꯁꯁ ꯑꯁꯤ ꯍꯥꯡꯗꯣꯛꯇꯨꯅꯥ ꯊꯝꯕꯅꯤ꯫ ꯄ꯭ꯔꯣꯁ꯭ꯇꯥꯒ꯭ꯂꯥꯟꯗꯤꯟ ꯀꯧꯕꯥ ꯗ꯭ꯔꯒ ꯑꯃꯥ ꯏꯅꯠꯔꯥꯚꯦꯅꯁ ꯑꯣꯏꯅꯥ ꯄꯤ꯫ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯊꯝꯃꯣꯌꯒꯤ ꯈꯣꯡꯖꯦꯂꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯑꯇꯩ ꯗ꯭ꯔꯒꯁꯤꯡꯁꯨ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯌꯥꯏ, ꯑꯃꯁꯨꯡ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯅꯕꯥ ꯚꯦꯟꯇꯤꯂꯦꯇꯔ ꯑꯃꯥ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯌꯥꯏ꯫
ꯈꯣꯡꯊꯥꯡ ꯑꯅꯤ: ꯁ꯭ꯇꯦꯖ ꯑꯍꯨꯃꯒꯤ ꯁꯔꯖꯤꯀꯦꯜ ꯁꯤꯔꯤꯖ꯫
ꯁꯔꯖꯔꯤ꯫ ꯃꯁꯤ ꯏꯒꯤ ꯈꯣꯡꯖꯦꯜ ꯑꯁꯤ ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯇꯣꯉꯥꯅꯕꯥ ꯃꯥꯏꯀꯩ ꯑꯃꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯂꯃꯖꯤꯡꯕꯒꯥ ꯃꯥꯟꯅꯩ꯫
1. ꯅꯣꯔꯎꯗ ꯄ꯭ꯔꯣꯁꯤꯗ꯭ꯌꯨꯑꯣꯔ: ꯃꯁꯤ ꯑꯉꯥꯡ ꯄꯣꯀꯄꯥ ꯃꯇꯨꯡ ꯑꯍꯥꯅꯕꯥ ꯅꯨꯃꯤꯠ ꯑꯅꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯄꯥꯡꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯀꯝꯞꯂꯦꯛꯁ ꯑꯣꯏꯕꯥ, ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯁꯔꯖꯔꯤ ꯑꯃꯅꯤ꯫ ꯃꯐꯝ ꯑꯁꯤꯗꯥ, ꯁꯔꯖꯔꯤꯁꯤꯡ:
- ꯑꯟꯗꯔꯗꯦꯚꯦꯂꯞ ꯇꯧꯔꯕꯥ ꯑꯦꯑꯣꯔꯇꯥ ꯑꯗꯨ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯁꯦꯃꯒꯠꯂꯤ꯫
- ꯔꯥꯏꯠ ꯚꯦꯟꯇꯤꯂꯦꯇꯔꯗꯒꯤ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯂꯪꯁꯇꯥ ꯏ ꯊꯥꯅꯕꯥ ꯑꯈꯟꯅꯕꯥ ꯇꯤꯎꯕ (shant) ꯑꯃꯥ ꯊꯥꯏ꯫
- ꯃꯁꯤꯒꯤ ꯃꯑꯣꯡ ꯑꯁꯤꯅꯥ, ꯍꯥꯔꯇꯀꯤ "ꯇꯨꯕ꯭ꯌꯨꯂꯔ ꯁꯤꯁ꯭ꯇꯦꯝ" ꯑꯁꯤ ꯃꯣꯗꯤꯐꯥꯏ ꯇꯧꯏ, ꯃꯗꯨꯅꯥ ꯔꯥꯏꯠ ꯚꯦꯟꯇꯤꯂꯦꯇꯔꯅꯥ ꯍꯀꯆꯥꯡ ꯑꯃꯁꯨꯡ ꯂꯪꯁ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯏ ꯄꯝꯄ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫
2. ꯒ꯭ꯂꯦꯟ ꯁꯔꯖꯔꯤ (Bidirectional Glenn shant operation): ꯃꯁꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯊꯥ 4 ꯑꯃꯁꯨꯡ 6ꯒꯤ ꯃꯔꯛꯇꯥ ꯂꯩꯕꯥ ꯃꯇꯃꯗꯥ ꯄꯥꯡꯊꯣꯀꯏ . ꯃꯐꯝꯁꯤꯗ:
- ꯑꯍꯥꯅꯕꯥ ꯁꯔꯖꯔꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯏꯅꯁꯥꯔꯁ ꯇꯧꯔꯕꯥ ꯇꯤꯎꯕ (shant) ꯑꯗꯨ ꯂꯧꯊꯣꯀꯏ꯫
- ꯍꯀꯆꯥꯡꯒꯤ ꯃꯊꯛ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ (ꯁꯨꯄꯤꯔꯤꯌꯔ ꯚꯦꯅꯝ ꯀꯥꯚꯥ ꯀꯧꯕꯥ ꯚꯦꯅꯝ ꯑꯃꯗꯒꯤ) ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯑꯣꯗꯕꯥ ꯏ ꯑꯁꯤ ꯂꯪꯁꯇꯥ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯁꯝꯅꯍꯜꯂꯤ꯫
- ꯃꯁꯤꯅꯥ ꯔꯥꯏꯠ ꯚꯦꯟꯇꯤꯂꯦꯁꯅꯒꯤ ꯄꯣꯠꯂꯨꯝ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯍꯟꯊꯍꯜꯂꯤ, ꯃꯔꯃꯗꯤ ꯍꯧꯖꯤꯛꯇꯤ ꯃꯁꯤꯅꯥ ꯃꯊꯛꯀꯤ ꯍꯀꯆꯥꯡꯗꯒꯤ ꯏ ꯊꯥꯗꯣꯀꯄꯥ ꯃꯊꯧ ꯇꯥꯗ꯭ꯔꯦ, ꯃꯁꯤꯅꯥ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯂꯪꯁꯇꯥ ꯆꯠꯂꯤ꯫
꯳.ꯐꯣꯟꯇꯟ ꯄ꯭ꯔꯣꯁꯤꯖꯔ: ꯃꯁꯤ ꯑꯔꯣꯏꯕꯥ ꯇꯥꯉ꯭ꯀꯛꯅꯤ꯫ ꯃꯁꯤ ꯆꯍꯤ ꯱꯸ꯗꯒꯤ ꯆꯍꯤ ꯴ ꯐꯥꯑꯣꯕꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯄꯥꯡꯊꯣꯀꯏ . ꯃꯐꯝꯁꯤꯗ:
- ꯍꯀꯆꯥꯡꯒꯤ ꯃꯈꯥ ꯊꯪꯕꯥ ꯁꯔꯨꯛ (inferior vena cava ꯀꯧꯕꯥ ꯚꯦꯅꯝ ꯑꯃꯗꯒꯤ)ꯗꯒꯤ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯎꯗꯕꯥ ꯏ ꯑꯁꯤ ꯂꯪꯁꯇꯥ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯁꯝꯅꯍꯜꯂꯤ꯫
- ꯃꯁꯤꯒꯤ ꯁꯔꯖꯔꯤ ꯑꯁꯤꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯍꯀꯆꯥꯡꯗꯒꯤ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯑꯣꯗꯕꯥ ꯏ ꯄꯨꯝꯅꯃꯛ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯂꯪꯁꯇꯥ ꯆꯠꯂꯤ꯫ ꯍꯥꯔꯇꯀꯤ ꯑꯔꯣꯏꯕꯥ ꯚꯦꯟꯇꯤꯂꯦꯇꯔ ꯑꯗꯨꯅꯥ ꯂꯪꯁꯇꯒꯤ ꯍꯀꯆꯥꯡ ꯄꯨꯝꯅꯃꯛꯇꯥ ꯑꯁꯦꯡꯕꯥ, ꯑꯣꯛꯁꯤꯖꯦꯟ ꯌꯥꯝꯅꯥ ꯌꯥꯎꯕꯥ ꯏ ꯑꯗꯨ ꯄꯝꯄ ꯇꯧꯕꯥ ꯈꯛꯇꯃꯛ ꯃꯊꯧ ꯇꯥꯏ꯫
ꯁꯔꯖꯔꯤ ꯑꯍꯨꯝ ꯑꯁꯤ ꯂꯣꯌꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯁꯔꯛꯌꯨꯂꯦꯇꯔꯤ ꯁꯤꯁ꯭ꯇꯦꯝ ꯑꯁꯤ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯑꯅꯧꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯊꯕꯛ ꯇꯧꯕꯥ ꯍꯧꯏ꯫
ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?
ꯁꯔꯖꯔꯤꯁꯤꯡ ꯑꯁꯤ ꯄꯨꯟꯁꯤ ꯀꯅꯕꯥ ꯉꯝꯂꯕꯁꯨ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯀꯝꯞꯂꯦꯛꯁ ꯑꯣꯏ ꯑꯃꯁꯨꯡ ꯔꯤꯁ꯭ꯛ ꯑꯃꯁꯨꯡ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯄꯨꯔꯀꯄꯥ ꯌꯥꯏ꯫ ꯁꯔꯖꯔꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯁꯨꯡ ꯃꯇꯨꯡꯗꯥ ꯄ꯭ꯔꯣꯕ꯭ꯂꯦꯃꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫
- ꯔꯥꯏꯠ ꯚꯦꯟꯇꯤꯂꯦꯇꯔ ꯑꯗꯨꯅꯥ ꯂꯧꯒꯗꯕꯥ ꯑꯀꯅꯕꯥ ꯂꯣꯗ ꯑꯗꯨꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯁꯣꯟꯊꯔꯀꯏ꯫
- ꯍꯥꯔꯠ ꯚꯜꯌꯨꯁꯤꯡꯗꯒꯤ ꯏ ꯊꯣꯀꯄꯥ꯫
- ꯂꯤꯚꯔꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ꯫
- ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯍꯥꯔꯇꯀꯤ ꯔꯤꯗꯃꯁꯤꯡ꯫
- ꯏ ꯊꯣꯀꯄꯥ꯫
- ꯏꯅꯐꯦꯛꯁꯅꯁꯤꯡ ꯂꯩꯕꯥ꯫
- ꯆꯥꯕꯗꯥ ꯑꯋꯥꯕꯥ ꯊꯣꯀꯄꯥ꯫
- ꯁꯤꯖ꯭ꯌꯨꯔꯁꯤꯡ (seizures) ꯂꯩꯕꯥ꯫
- ꯀꯤꯗꯅꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯏꯐꯦꯛꯇꯁꯤꯡ꯫
ꯗꯣꯛꯇꯔꯅꯥ ꯔꯤꯁ꯭ꯛ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯥ ꯂꯣꯌꯅꯅꯥ ꯑꯀꯨꯞꯄꯥ ꯃꯔꯣꯂꯗꯥ ꯈꯟꯅꯒꯅꯤ꯫ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯀꯥꯡꯕꯨꯅꯥ ꯃꯈꯣꯌꯒꯤ ꯈꯣꯉꯆꯠ ꯑꯁꯤ ꯆꯠꯊꯔꯤꯉꯩꯗꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯌꯥꯝꯅꯥ ꯀꯨꯞꯅꯥ ꯌꯦꯡꯁꯤꯅꯒꯅꯤ꯫
ꯍꯥꯔꯠ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯑꯁꯤ ꯑꯐꯕꯥ ꯑꯣꯄꯁꯟ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯁꯤꯅꯤ?
ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯍꯥꯔꯇꯀꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯀꯝꯞꯂꯦꯛꯁ ꯑꯣꯏꯔꯕꯗꯤ ꯅꯠꯠꯔꯒꯥ ꯗꯣꯛꯇꯔꯁꯤꯡꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨ ꯁꯔꯖꯔꯤ ꯑꯗꯨꯗꯒꯤ ꯍꯤꯡꯍꯧꯔꯣꯏ ꯍꯥꯌꯅꯥ ꯈꯜꯂꯕꯗꯤ, ꯃꯈꯣꯌꯅꯥ ꯍꯥꯔꯠ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯅꯕꯥ ꯄꯥꯎꯇꯥꯛ ꯄꯤꯕꯥ ꯌꯥꯏ . ꯑꯗꯨꯕꯨ ꯃꯈꯣꯌꯅꯥ ꯀꯝꯄꯦꯇꯤꯇꯤꯕ ꯍꯥꯔꯠ ꯑꯃꯥ ꯐꯪꯗ꯭ꯔꯤꯐꯥꯑꯣꯕꯥ ꯉꯥꯏꯗꯨꯅꯥ ꯂꯩꯒꯗꯕꯅꯤ꯫ ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, ꯍꯥꯔꯠ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ, ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯏꯝꯝꯌꯨꯅꯣꯁꯞꯔꯦꯁꯤꯚ ꯗ꯭ꯔꯒꯁꯤꯡ ꯂꯧꯒꯗꯕꯅꯤ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯑꯉꯥꯡ ꯑꯃꯗꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯂꯩꯔꯕꯗꯤ, ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥ-ꯃꯄꯥ ꯑꯣꯏꯅꯥ ꯀꯔꯤ ꯈꯪꯒꯗꯒꯦ?
ꯈꯣꯉꯆꯠ ꯑꯁꯤ ꯁꯤꯡꯅꯕꯥ ꯑꯃꯅꯤ, ꯑꯗꯨꯕꯨ ꯃꯇꯤꯛ ꯆꯥꯕꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯁꯨꯄꯔꯚꯤꯖꯟ ꯑꯃꯁꯨꯡ ꯀꯦꯌꯔꯒꯥ ꯂꯣꯌꯅꯅꯥ HLHSꯅꯥ ꯅꯥꯕꯥ ꯑꯉꯥꯡꯁꯤꯡꯅꯥ ꯑꯐꯕꯥ ꯄꯨꯟꯁꯤ ꯍꯤꯡꯕꯥ ꯉꯃꯒꯅꯤ꯫
- ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯃꯦꯗꯤꯀꯦꯜ ꯁꯨꯄꯔꯚꯤꯖꯟ: ꯁꯔꯖꯔꯤꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯀꯥꯔꯗꯤꯑꯣꯂꯣꯖꯤꯁ꯭ꯠ ꯑꯃꯗꯥ ꯆꯠꯄꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫ ꯃꯈꯣꯌꯅꯥ ꯆꯍꯤ ꯑꯃꯗꯥ ꯌꯥꯃꯗ꯭ꯔꯕꯗꯥ ꯑꯃꯨꯛ ꯍꯟꯅꯥ ꯆꯦꯛ-ꯑꯞ ꯇꯧꯒꯗꯕꯅꯤ꯫
- ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯀꯁꯤꯡ: ꯑꯉꯥꯡ ꯀꯌꯥꯅꯥ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯍꯥꯔꯇꯀꯤ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯀꯁꯤꯡ ꯂꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫
- ꯑꯇꯣꯞꯄꯥ ꯁꯔꯖꯔꯤꯁꯤꯡꯒꯤ ꯃꯃꯥꯡꯗꯥ ꯑꯦꯟꯇꯤꯕꯥꯏꯑꯣꯇꯤꯀꯁꯤꯡ: ꯑꯇꯣꯞꯄꯥ ꯁꯔꯖꯔꯤ ꯑꯃꯍꯦꯛꯇꯒꯤ ꯃꯃꯥꯡꯗꯥ, ꯍꯥꯌꯕꯗꯤ ꯍꯥꯠꯄꯥ, ꯍꯥꯔꯠ ꯏꯅꯐꯦꯛꯁꯟ (endocarditis) ꯊꯤꯡꯅꯕꯥ ꯑꯦꯟꯇꯤꯕꯥꯏꯑꯣꯇꯤꯀꯁꯤꯡ ꯂꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯏ꯫
- ꯐꯤꯖꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤ: ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯐꯤꯖꯤꯀꯦꯜ ꯑꯦꯛꯇꯤꯚꯤꯇꯤ ꯑꯗꯨ ꯂꯤꯃꯤꯠ ꯂꯩꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯌꯥꯏ꯫ ꯀꯝꯄꯤꯇꯤꯇꯤꯕ ꯁ꯭ꯄꯣꯔꯇꯁꯒꯨꯝꯕꯥ ꯑꯀꯅꯕꯥ ꯊꯕꯛ ꯊꯧꯔꯃꯁꯤꯡ ꯑꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯔꯦꯀꯃꯦꯟꯗ ꯇꯧꯗꯦ꯫ ꯃꯁꯤꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯗꯥ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯕꯤꯌꯨ꯫
- ꯅꯍꯥꯛꯀꯤ ꯋꯥꯈꯂꯒꯤ ꯍꯀꯁꯦꯜ: ꯈꯣꯉꯆꯠ ꯑꯁꯤ ꯃꯃꯥ-ꯃꯄꯥꯁꯤꯡꯒꯤꯗꯃꯛꯇꯥ ꯌꯥꯝꯅꯥ ꯋꯥꯅꯥ ꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯁ꯭ꯠꯔꯦꯁ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ, ꯅꯍꯥꯛꯀꯤ ꯃꯄꯨꯔꯣꯏꯕꯥ/ꯅꯨꯄꯤ ꯑꯃꯁꯨꯡ ꯏꯃꯨꯡ-ꯃꯅꯨꯡꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯐꯤꯚꯃꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯋꯥꯔꯤ ꯁꯥꯕꯤꯌꯨ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯊꯧ ꯇꯥꯔꯕꯗꯤ ꯀꯥꯎꯟꯁꯦꯂꯤꯡ ꯂꯧꯕꯤꯌꯨ꯫ ꯅꯍꯥꯛꯅꯥ ꯃꯄꯥꯉ꯭ꯒꯜ ꯀꯅꯕꯥ ꯃꯇꯃꯗꯥ ꯈꯛꯇꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯉꯥꯡ ꯑꯗꯨꯕꯨ ꯑꯐꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯉꯃꯒꯅꯤ꯫
ꯇꯦꯛ-ꯍꯣꯝ ꯃꯦꯁꯦꯖ ꯇꯧꯕꯥ꯫
- ꯍꯥꯏꯄꯣꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯂꯦꯐꯠ ꯍꯥꯔꯠ ꯁꯤꯟꯗ꯭ꯔꯣꯝ (HLHS) ꯍꯥꯌꯕꯁꯤ ꯍꯥꯔꯇꯀꯤ ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ ꯑꯗꯨ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯁꯦꯃꯒꯠꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯣꯟꯖꯤꯅꯤꯑꯦꯜ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫
- ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯂꯥꯏꯌꯦꯡꯗ꯭ꯔꯕꯗꯤ ꯁꯤꯍꯅꯕꯥ ꯌꯥꯏ, ꯑꯗꯨꯕꯨ ꯉꯁꯤꯗꯤ ꯁ꯭ꯇꯦꯖ ꯑꯍꯨꯃꯒꯤ ꯁꯔꯖꯤꯀꯦꯜ ꯄ꯭ꯔꯣꯁꯤꯗ꯭ꯌꯨꯑꯣꯔ ꯑꯃꯅꯥ ꯑꯉꯥꯡ ꯑꯗꯨꯒꯤ ꯄꯨꯟꯁꯤ ꯀꯅꯕꯥ ꯉꯝꯂꯦ꯫
- ꯃꯁꯤꯒꯤ ꯈꯣꯡꯆꯠ ꯑꯁꯤ ꯁꯤꯡꯅꯕꯥ ꯑꯃꯥ ꯑꯣꯏꯔꯤ꯫ ꯑꯉꯥꯡ ꯑꯗꯨꯅꯥ ꯃꯍꯥꯛꯀꯤ ꯄꯨꯟꯁꯤ ꯆꯨꯞꯄꯥ ꯁ꯭ꯄꯦꯁꯤꯑꯦꯂꯤꯁ꯭ꯠ ꯃꯦꯗꯤꯀꯦꯜ ꯁꯨꯄꯔꯚꯤꯖꯟ, ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯑꯃꯁꯨꯡ ꯑꯈꯟꯅꯕꯥ ꯀꯦꯌꯔ ꯃꯊꯧ ꯇꯥꯒꯅꯤ꯫
- ꯃꯁꯤ ꯃꯃꯥ-ꯃꯄꯥꯒꯤ ꯑꯁꯣꯌꯕꯥ ꯅꯠꯇꯦ꯫ ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ, ꯑꯀꯛꯅꯕꯥ ꯑꯟꯗꯔꯂꯥꯏꯟ ꯃꯔꯝ ꯑꯃꯠꯇꯥ ꯈꯪꯗꯣꯀꯄꯥ ꯉꯃꯗ꯭ꯔꯤ꯫
- ꯃꯃꯥ-ꯃꯄꯥ ꯑꯣꯏꯕꯁꯤꯡ ꯑꯣꯏꯅꯥ, ꯈꯣꯉꯆꯠ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯅꯍꯥꯛꯀꯤ ꯋꯥꯈꯂꯒꯤ ꯍꯀꯁꯦꯜ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯅꯍꯥꯛꯀꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇꯤꯃꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯌꯥꯝꯅꯥ ꯅꯛꯅꯥ ꯊꯕꯛ ꯇꯧꯃꯤꯟꯅꯧ ꯑꯃꯁꯨꯡ ꯁꯤꯡꯅꯕꯥ ꯑꯁꯤ ꯊꯦꯡꯅꯅꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯁꯄꯣꯔꯠ ꯑꯗꯨ ꯐꯪꯕꯤꯌꯨ꯫











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