ꯑꯌꯥꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯅꯍꯥꯛꯅꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯋꯥꯈꯜ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ ꯅꯠꯠꯔꯒꯥ ꯅꯍꯥꯛꯀꯤ ꯅꯥꯀꯣꯡꯗꯥ ꯈꯣꯟꯖꯦꯜ ꯑꯃꯥ ꯇꯥꯕꯥ ꯐꯥꯎꯕ꯭ꯔꯥ? ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯅꯣꯔꯃꯦꯜ ꯑꯣꯏꯕꯥ ꯋꯥꯐꯃꯁꯤꯡ ꯑꯣꯏꯅꯥ ꯎꯔꯕꯁꯨ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯑꯇꯣꯞꯄꯥ ꯃꯔꯝ ꯑꯃꯁꯨ ꯂꯩꯕꯥ ꯌꯥꯏ꯫ ꯑꯗꯨꯅꯥ, ꯉꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯒꯗꯧꯔꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) , ꯃꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯌꯥꯝꯅꯥ ꯄꯨꯊꯣꯀꯄꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯈꯔꯥ ꯁꯥꯡꯕꯥ ꯃꯤꯡ ꯑꯣꯏꯔꯕꯁꯨ, ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯂꯧꯁꯤ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯍꯥꯌꯕꯁꯤ ꯀꯔꯤꯅꯣ? ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ...
ꯌꯥꯝꯅꯥ ꯂꯥꯏꯅꯥ ꯍꯥꯌꯔꯕꯗꯥ, ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯍꯥꯌꯕꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡ, ꯃꯔꯨꯑꯣꯏꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯕꯣꯟ ꯃꯦꯔꯣ (ꯑꯩꯈꯣꯌꯅꯥ ``ꯕꯣꯟ ꯃꯦꯔꯣ'' ꯍꯥꯌꯅꯥ ꯀꯧꯕꯥ)ꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯄꯨꯊꯣꯀꯄꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯇ꯭ꯔꯥꯐꯤꯛ ꯖ꯭ꯌꯥꯃꯒꯨꯝꯅꯥ ꯂꯝꯕꯤꯗꯥ ꯒꯥꯔꯤ ꯌꯥꯝꯅꯥ ꯂꯩꯕꯥ ꯃꯇꯃꯗꯥ ꯏꯒꯤ ꯈꯣꯡꯖꯦꯂꯗꯥ ꯑꯀꯥꯌꯕꯥ ꯄꯤ꯫ ꯃꯁꯤꯅꯥ ꯏ ꯑꯗꯨ ꯇꯔꯨ-ꯇꯅꯥꯟꯅꯥ ꯂꯩꯍꯟꯗꯨꯅꯥ ꯆꯠꯊꯣꯛ-ꯆꯠꯁꯤꯟ ꯇꯧꯍꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫ ꯃꯁꯤꯅꯥ ꯍꯥꯔꯠ ꯑꯦꯇꯦꯛ ꯑꯃꯁꯨꯡ ꯁ꯭ꯠꯔꯣꯀꯒꯨꯝꯕꯥ ꯑꯀꯅꯕꯥ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ .
ꯃꯁꯤ ꯈꯛꯇꯥ ꯅꯠꯇꯅꯥ, ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯈꯣꯡ ꯍꯥꯝꯕꯥ, ꯅꯥꯀꯣꯡꯗꯥ ꯁꯣꯀꯄꯥ (`(Tinnitus)`), ꯈꯣꯡ ꯍꯥꯝꯕꯥ, ꯅꯥꯀꯣꯡꯗꯥ ꯏ ꯊꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯃꯤꯠ ꯎꯗꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯁꯨ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯐꯍꯅꯕꯥ ꯉꯃꯗꯕꯥ ꯀ꯭ꯔꯣꯅꯤꯛ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯋꯥꯈꯜ ꯋꯥꯕꯥ ꯂꯩꯔꯣꯏꯗꯕꯅꯤ꯫ ꯑꯐꯕꯥ ꯃꯦꯗꯤꯀꯦꯂꯒꯤ ꯂꯥꯏꯌꯦꯡꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯕꯥ ꯉꯝꯃꯤ ꯑꯃꯁꯨꯡ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇꯀꯤ ꯔꯤꯁ꯭ꯛ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯃꯤ꯫ ꯃꯤꯑꯣꯏ ꯈꯔꯅꯥ ꯃꯁꯤꯕꯨ `ꯄ꯭ꯔꯥꯏꯃꯥꯔꯤ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ`, `ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯔꯨꯕ꯭ꯔꯥ ꯚꯦꯔꯥ`, `ꯑꯦꯔꯤꯊꯦꯃꯥ` ꯑꯃꯁꯨꯡ `ꯑꯣꯁꯂꯔ-ꯚꯦꯀꯦꯖ ꯗꯤꯖꯤꯖ` ꯍꯥꯌꯅꯥꯁꯨ ꯀꯧꯏ꯫
ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ ꯍꯥꯌꯕꯁꯤꯅꯤ?
ꯍꯣꯌ, ꯃꯁꯤ ꯇꯁꯦꯡꯅꯥ ꯀꯦꯟꯁꯔ ꯃꯈꯜ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯕꯨ ꯃꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯀꯦꯟꯁꯔ ꯍꯥꯌꯕꯥ ꯋꯥꯍꯩ ꯑꯁꯤ ꯇꯥꯕꯗꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯈꯜꯂꯤꯕꯥ ꯑꯗꯨꯒꯨꯝꯅꯥ ꯌꯥꯝꯅꯥ ꯂꯨꯕꯥ ꯅꯠꯔꯒꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯅꯠꯇꯦ꯫ ꯃꯁꯤ `ꯃꯥꯏꯂꯣꯞꯔꯣꯂꯤꯐꯦꯔꯦꯇꯤꯚ ꯅꯤꯑꯣꯞꯂꯥꯖꯝ (MPN) ꯀꯧꯕꯥ ꯀꯥꯡꯂꯨꯞ ꯑꯃꯒꯤ ꯃꯅꯨꯡ ꯆꯅꯕꯥ ꯕ꯭ꯂꯗ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ꯫ `MPN` ꯍꯥꯌꯕꯁꯤ ꯇꯣꯉꯥꯟ-ꯇꯣꯉꯥꯅꯕꯥ ꯃꯈꯂꯒꯤ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯍꯦꯟꯅꯥ ꯄꯨꯊꯣꯀꯄꯥ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯂꯥꯌꯅꯥ ꯀꯥꯡꯂꯨꯞ ꯑꯃꯕꯨ ꯈꯪꯅꯩ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯃꯗꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯂꯩꯕꯥ ꯖꯤꯟ ꯑꯃꯗꯥ ꯑꯍꯣꯡꯕꯥ (mutation) ꯑꯁꯤꯅꯤ꯫ ꯃꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯄꯣꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯄꯣꯀꯄꯥ ꯋꯥꯐꯝ ꯅꯠꯇꯦ, ꯑꯗꯨꯕꯨ ꯃꯁꯛ ꯈꯉꯗꯕꯥ ꯃꯔꯝ ꯈꯔꯗꯒꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯄꯨꯟꯁꯤꯗꯥ ꯊꯣꯀꯄꯥ ꯊꯧꯗꯣꯛ ꯑꯃꯅꯤ꯫ ꯃꯁꯤꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯞꯅꯥ ꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯑꯌꯥꯝꯕꯗꯤ ꯆꯍꯤ 60 ꯁꯨꯔꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯈꯪꯗꯣꯀꯏ, ꯃꯁꯤꯒꯤ ꯀꯦꯟꯁꯔ ꯑꯁꯤꯅꯥ ꯍꯀꯊꯦꯡꯅꯅꯥ ꯁꯤꯍꯅꯕꯥ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯊꯦꯡꯅꯩ꯫ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯔꯤꯁ꯭ꯛ ꯑꯁꯤ ꯏ ꯊꯣꯀꯄꯥ (blot clots)ꯅꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯗꯒꯤ ꯂꯥꯀꯏ꯫ ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, ꯌꯥꯝꯅꯥ ꯅꯦꯝꯕꯥ ꯆꯥꯗꯥ ꯑꯃꯗꯥ, ꯃꯁꯤꯅꯥ ꯑꯇꯣꯞꯄꯥ ꯑꯀꯅꯕꯥ ꯃꯈꯂꯒꯤ ꯕ꯭ꯂꯗ ꯀꯦꯟꯁꯔꯗꯥ ꯑꯣꯟꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫
ꯐꯤꯚꯝ ꯑꯁꯤꯅꯥ ꯀꯅꯥꯕꯨ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁꯣꯀꯍꯜꯂꯤꯕꯅꯣ?
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯇꯣꯏꯅꯥ ꯊꯣꯀꯄꯥ ꯂꯥꯌꯅꯥ ꯑꯃꯅꯤ꯫ ꯑꯃꯦꯔꯤꯀꯥꯒꯨꯝꯕꯥ ꯂꯩꯕꯥꯛ ꯑꯃꯗꯥ ꯃꯁꯤ ꯃꯤꯑꯣꯏ ꯂꯥꯈ ꯑꯃꯗꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯵꯰ꯗꯥ ꯊꯣꯀꯏ꯫ ꯃꯁꯤ ꯆꯍꯤ 60ꯒꯤ ꯃꯊꯛꯇꯥ ꯂꯩꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏ꯫
ꯂꯥꯌꯅꯥ ꯑꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯗꯥ ꯀꯔꯝꯅꯥ ꯁꯣꯀꯍꯅꯕꯒꯦ?
ꯑꯩꯈꯣꯌꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯍꯥꯌꯈꯤꯕꯒꯨꯝꯅꯥ, ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯅꯥ ꯍꯀꯆꯥꯡꯗꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯜ ꯌꯥꯝꯅꯥ ꯄꯨꯊꯣꯀꯄꯥ ꯉꯃꯍꯜꯂꯤ꯫ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯑꯍꯦꯅꯕꯥ ꯑꯁꯤꯅꯥ ꯏ ꯊꯣꯀꯄꯥ, ꯁꯣꯛ-ꯄꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫ ꯏ ꯑꯁꯤ ꯇꯔꯨ-ꯇꯅꯥꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯦꯟꯅꯥ ꯇꯞꯅꯥ ꯆꯠꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯇꯤꯁꯨꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯑꯣꯔꯒꯥꯅꯁꯤꯡꯅꯥ ꯃꯊꯧ ꯇꯥꯕꯥ ꯑꯣꯛꯁꯤꯖꯦꯟ ꯐꯪꯗꯦ꯫
ꯃꯁꯤꯅꯥ ꯑꯩꯈꯣꯌꯒꯤ ꯍꯀꯆꯥꯡꯒꯤ ꯈꯣꯡꯗꯥ ꯊꯕꯛ ꯀꯌꯥ ꯑꯃꯁꯨ ꯄꯤꯔꯤ꯫ ꯁ꯭ꯞꯂꯤꯅꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯊꯕꯛ ꯑꯃꯗꯤ ꯏ ꯐꯤꯜꯇꯔ ꯇꯧꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯔꯤꯕꯥ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯂꯧꯊꯣꯀꯄꯅꯤ꯫ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯁ꯭ꯞꯂꯤꯟ ꯑꯗꯨꯁꯨ ꯍꯦꯟꯅꯥ ꯊꯕꯛ ꯇꯧꯔꯀꯏ, ꯃꯗꯨꯅꯥ ꯁꯣꯛ-ꯄꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯕꯨ `(ꯁ꯭ꯞꯂꯦꯅꯣꯃꯦꯒꯥꯂꯤ)` ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯅꯥ ꯇꯣꯉꯥꯟ-ꯇꯣꯉꯥꯅꯕꯥ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯗꯁꯨ ꯅꯠꯇꯅꯥ, PVꯅꯥ ꯑꯇꯩ ꯁꯦꯀꯦꯟꯗꯔꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯒꯤ ꯔꯤꯁ꯭ꯛ ꯑꯃꯁꯨꯡ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?
PV ꯑꯁꯤ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁꯤꯚ ꯗꯤꯖꯤꯖ ꯑꯣꯏꯔꯕꯁꯨ, ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯍꯦꯟꯅꯥ ꯄꯨꯊꯣꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯈꯪꯍꯧꯗꯅꯥ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ ꯂꯩ꯫ ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, PVꯅꯥ ꯑꯇꯩ ꯁꯦꯀꯦꯟꯗꯔꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡꯁꯨ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ, ꯃꯁꯤꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯦꯟꯁꯔ ꯑꯃꯥ ꯑꯣꯏꯔꯀꯄꯥ ꯌꯥꯏ꯫
ꯏ ꯊꯣꯀꯄꯥ꯫
ꯃꯁꯤ PVꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯈꯨꯗꯛꯀꯤ ꯑꯣꯏꯕꯥ ꯔꯤꯁ꯭ꯀꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯕ꯭ꯂꯗ ꯀ꯭ꯂꯣꯠ ꯑꯃꯥ ꯁꯦꯃꯗꯨꯅꯥ ꯍꯥꯔꯠ ꯅꯠꯠꯔꯒꯥ ꯕ꯭ꯔꯦꯅꯗꯥ ꯆꯠꯂꯕꯗꯤ, ꯃꯁꯤꯅꯥ ꯍꯥꯔꯠ ꯑꯦꯇꯦꯛ ꯅꯠꯠꯔꯒꯥ ꯁ꯭ꯠꯔꯣꯛ ꯑꯃꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ . ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯁꯤꯅꯥ ꯂꯪꯁꯇꯥ ꯆꯠꯂꯕꯗꯤ (Pulmonary Embolism - PE), ꯃꯁꯤꯅꯥ ꯂꯪꯁꯇꯥ ꯍꯥꯏ ꯕ꯭ꯂꯗ ꯄ꯭ꯔꯦꯁꯔ (pulmonary hypertension) ꯑꯃꯁꯨꯡ ꯍꯥꯔꯠ ꯐꯦꯜ ꯑꯣꯏꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏ ꯊꯣꯀꯄꯥ ꯑꯃꯥ ꯚꯦꯅꯝ ꯑꯃꯗꯥ (Venous Thromboembolism - VTE) ꯊꯤꯡꯖꯤꯜꯂꯕꯗꯤ, ꯃꯁꯤꯅꯥ ꯇꯤꯁꯨꯁꯤꯡ ꯁꯤꯍꯅꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯀ꯭ꯔꯣꯅꯤꯛ ꯚꯦꯅꯝ ꯏꯅꯁꯨꯐꯤꯁꯤꯑꯦꯟꯁꯤ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯏ ꯊꯣꯀꯄꯥ ꯑꯃꯥ ꯂꯤꯚꯔꯗꯥ ꯆꯠꯂꯤꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯜ (hepatic vein thrombosis)ꯗꯥ ꯆꯦꯟꯊꯈꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯃꯁꯤꯅꯥ ꯂꯤꯚꯔꯗꯥ ꯏ ꯊꯣꯀꯄꯥ (Budd-Chiari syndrome), ꯖꯟꯗꯥꯁꯤꯁ ꯑꯃꯁꯨꯡ ꯂꯤꯚꯔ ꯐꯦꯜ ꯑꯣꯏꯍꯅꯕꯥ ꯌꯥꯏ꯫
ꯁꯦꯀꯦꯟꯗꯔꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ꯫
ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯑꯍꯦꯅꯕꯥ ꯑꯣꯏꯅꯥ ꯄꯨꯊꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯁꯣꯀꯍꯜꯂꯕꯥ ꯃꯇꯃꯗꯥ ꯍꯀꯆꯥꯡꯗꯥ `ꯌꯨꯔꯤꯛ ꯑꯦꯁꯤꯗ`ꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯂꯀꯏ꯫ ꯃꯁꯤꯅꯥ ꯈꯨꯗꯣꯡꯆꯥꯗꯕꯥ ꯀꯌꯥ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ:
- ꯀꯤꯗꯅꯤꯗꯥ ꯁ꯭ꯇꯣꯟ (kidney stones): ꯀꯤꯗꯅꯤꯗꯥ ꯌꯨꯔꯤꯛ ꯑꯦꯁꯤꯗ ꯊꯥꯗꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ꯫
- ꯒꯥꯎꯠ: ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡꯗꯥ ꯌꯨꯔꯤꯛ ꯑꯦꯁꯤꯗ ꯌꯥꯎꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯑꯅꯥꯕꯥ ꯑꯔꯊ꯭ꯔꯥꯏꯇꯤꯁꯀꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫
- ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯂꯁꯔ: ꯑꯍꯦꯅꯕꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯦꯁꯤꯗꯀꯤ ꯆꯥꯡꯁꯨ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫ ꯑꯍꯦꯅꯕꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯍꯀꯆꯥꯡꯗꯥ ꯍꯤꯁ꯭ꯇꯥꯃꯤꯟ ꯀꯧꯕꯥ ꯀꯦꯃꯤꯀꯦꯜ ꯑꯃꯥ ꯊꯥꯗꯣꯀꯏ, ꯃꯗꯨꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯏꯅꯐꯦꯛꯁꯟ ꯑꯗꯨ ꯂꯥꯀꯁꯤꯟꯅꯕꯥ ꯁ꯭ꯇꯣꯃꯥꯛꯇꯥ ꯑꯦꯁꯤꯗ ꯍꯦꯟꯅꯥ ꯄꯨꯊꯣꯀꯏ꯫ PVꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯗꯥ ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯂꯁꯔ (peptic ulcer disease) ꯂꯥꯀꯄꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯁꯔꯨꯛ ꯃꯔꯤ ꯍꯦꯜꯂꯤ꯫
ꯂꯤꯎꯀꯦꯃꯤꯌꯥꯗꯥ ꯂꯥꯀꯄꯥ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ ꯑꯁꯤ ꯕꯣꯟ ꯃꯦꯔꯣꯒꯤ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ, ꯑꯗꯨꯕꯨ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯁꯤ ꯄꯨꯟꯁꯤ ꯃꯥꯡꯍꯅꯕꯥ ꯌꯥꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯂꯥꯌꯦꯡꯕꯅꯥ ꯆꯍꯤ ꯀꯌꯥ ꯐꯖꯅꯥ ꯃꯦꯅꯦꯖ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯤꯑꯣꯏ ꯈꯔꯒꯤ ꯑꯣꯏꯅꯗꯤ, ꯄꯤ.ꯚꯤ.ꯃꯁꯤ `ꯑꯦꯛꯌꯨꯠ ꯂꯤꯎꯀꯦꯃꯤꯌꯥ`ꯒꯨꯝꯕꯥ ꯁꯥꯊꯤꯕꯥ ꯕ꯭ꯂꯗ ꯀꯦꯟꯁꯔ ꯑꯃꯗꯥ ꯑꯣꯟꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯂꯥꯌꯅꯥꯒꯤ ꯁ꯭ꯇꯦꯖꯁꯤꯡ꯫
ꯄꯤ.ꯚꯤ.ꯒꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯃꯑꯣꯡ ꯑꯁꯤꯒꯤ ꯃꯇꯨꯡ ꯏꯟꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯏ:
- ꯑꯍꯥꯅꯕꯥ ꯁ꯭ꯇꯦꯖ (`Early PV`): ꯁ꯭ꯇꯦꯖ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ, ꯂꯥꯏꯑꯣꯡ ꯈꯔꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯦ꯫
- PV ꯍꯦꯅꯒꯠꯂꯀꯄꯥ: PV ꯑꯁꯤ ꯍꯦꯟꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯔꯀꯄꯒꯥ ꯂꯣꯌꯅꯅꯥ, ꯅꯍꯥꯛꯅꯥ ꯍꯦꯟꯅꯥ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯍꯧꯔꯀꯄꯥ ꯌꯥꯏ, ꯅꯠꯠꯔꯒꯥ ꯁꯦꯀꯦꯟꯗꯔꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫
- ꯁ꯭ꯄꯦꯟꯇ ꯐꯦꯖ: ꯃꯁꯤꯕꯨ “ꯁ꯭ꯄꯦꯟꯇ ꯐꯦꯖ” ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯃꯇꯝ ꯑꯁꯤꯗꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤ ꯊꯣꯀꯍꯜꯂꯤꯕꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯃꯁꯤꯡ ꯌꯥꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯏ ꯑꯃꯁꯨꯡ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯁꯦꯃꯒꯠꯂꯤꯕꯥ ꯕꯣꯟ ꯃꯦꯔꯣ ꯑꯁꯤ ꯃꯄꯨꯡ ꯐꯥꯅꯥ ꯕ꯭ꯂꯣꯛ ꯇꯧꯏ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯁꯤꯕꯥ ꯃꯇꯃꯗꯥ ꯃꯈꯣꯌꯒꯤ ꯃꯍꯨꯠꯇꯥ ꯁ꯭ꯀꯥꯔ ꯇꯤꯁꯨ ꯁꯦꯝꯃꯤ꯫ ꯕꯣꯟ ꯃꯦꯔꯣꯒꯤ ꯑꯌꯥꯝꯕꯥ ꯁꯔꯨꯛ ꯑꯁꯤ ꯁ꯭ꯀꯥꯔ ꯇꯤꯁꯨ ꯑꯁꯤꯅꯥ ꯊꯜꯂꯕꯥ ꯃꯇꯃꯗꯥ, ꯃꯁꯤꯅꯥ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯁꯦꯝꯕꯥ ꯉꯃꯗꯦ꯫ ꯌꯥꯝꯅꯥ ꯅꯨꯡꯉꯥꯏꯇꯕꯥ ꯋꯥꯐꯝ ꯑꯃꯅꯥ ꯃꯁꯤꯅꯥ ꯑꯦꯅꯤꯃꯤꯌꯥ ꯊꯣꯀꯍꯜꯂꯤ – ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯑꯋꯥꯠꯄꯥ꯫ ꯃꯁꯤꯅꯥ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯀꯁꯨ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫
PVꯒꯤ ꯃꯇꯨꯡꯗꯥ ꯊꯣꯀꯄꯥ ꯌꯥꯕꯥ ꯑꯇꯩ ꯏꯒꯤ ꯂꯥꯌꯅꯥꯁꯤꯡ꯫
PV ꯑꯁꯤ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯃꯁꯤꯅꯥ ꯑꯇꯩ ꯕ꯭ꯂꯗ ꯗꯤꯖꯤꯖꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
- ꯃꯥꯏꯂꯣꯐꯥꯏꯕ꯭ꯔꯣꯁꯤꯁ (MF): PVꯒꯤ ``ꯁ꯭ꯄꯦꯟꯇꯦꯗ ꯐꯦꯖ'' ꯑꯃꯁꯨꯡ ``ꯃꯥꯏꯂꯣꯐꯥꯏꯕ꯭ꯔꯣꯁꯤꯁ (MF)'' , ꯑꯇꯣꯞꯄꯥ ꯃꯈꯜ ꯑꯃꯒꯤ ꯕ꯭ꯂꯗ ꯀꯦꯟꯁꯔꯒꯤ ꯃꯔꯛꯇꯥ ꯈꯦꯠꯅꯕꯥ ꯌꯥꯝꯅꯥ ꯂꯩꯇꯦ꯫ ꯗꯣꯛꯇꯔ ꯈꯔꯅꯥ ꯃꯈꯣꯌꯕꯨ ꯆꯞ ꯃꯥꯟꯅꯅꯥ ꯂꯧꯏ꯫ ``ꯃꯥꯏꯂꯣꯐꯥꯏꯕ꯭ꯔꯣꯁꯤꯁ'' ꯍꯥꯌꯕꯁꯤ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯕꯣꯟ ꯃꯦꯔꯣꯗꯥ ꯁ꯭ꯀꯥꯔ ꯇꯤꯁꯨ ꯁꯦꯃꯗꯨꯅꯥ ꯃꯗꯨ ꯃꯄꯨꯡ ꯐꯥꯍꯅꯕꯥ ꯍꯥꯌꯕꯁꯤꯅꯤ꯫ ꯍꯥꯌꯔꯤꯕꯥ ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯕꯣꯟ ꯃꯦꯔꯣꯒꯤ ꯃꯄꯥꯟꯗꯥ ꯑꯃꯁꯨꯡ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯌꯥꯏ꯫ ``MF'' ꯑꯁꯤꯁꯨ ``ꯃꯥꯏꯂꯣꯞꯔꯣꯂꯤꯐꯦꯔꯦꯇꯤꯚ ꯗꯤꯁꯑꯣꯔꯗꯔ ꯑꯃꯅꯤ꯫'' ``MF'' ꯄꯦꯁꯦꯟꯇꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 10%ꯗꯤ ``ꯑꯦꯛꯌꯨꯠ ꯃꯥꯏꯂꯣꯏꯗ ꯂꯤꯎꯀꯦꯃꯤꯌꯥ'' ꯊꯣꯀꯏ꯫
- ꯃꯥꯏꯂꯣꯗꯤꯁ꯭ꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯁꯤꯟꯗꯣꯝ (MDS): ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ, PV ꯑꯁꯤ ꯃꯥꯏꯂꯣꯗꯤꯁ꯭ꯞꯂꯥꯁ꯭ꯇꯤꯛ ꯁꯤꯟꯗꯣꯝ (MDS) ꯀꯧꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯗꯥ ꯂꯥꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯅꯥ ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯄꯤꯀꯄꯥ ꯉꯃꯗꯕꯥ, ꯃꯍꯧꯁꯥꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯈꯠꯄꯥ ꯑꯃꯁꯨꯡ ꯊꯨꯅꯥ ꯁꯤꯕꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯃꯅꯤ꯫ ꯍꯀꯆꯥꯡꯅꯥ ꯍꯀꯆꯥꯡ ꯐꯕꯥ, ꯄꯤꯀꯄꯥ ꯁꯦꯂꯁꯤꯡ ꯁꯦꯝꯕꯥ ꯉꯃꯗꯕꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯇꯣꯉꯥꯟ-ꯇꯣꯉꯥꯅꯕꯥ ꯃꯈꯂꯒꯤ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯃꯁꯤꯡ ꯍꯟꯊꯔꯀꯏ꯫ ꯑꯦꯝ.ꯗꯤ.ꯑꯦꯁ.ꯅꯥ PV ꯅꯠꯠꯔꯒꯥ MFꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏ, ꯑꯃꯁꯨꯡ ꯑꯦꯛꯌꯨꯠ ꯃꯥꯏꯂꯣꯏꯗ ꯂꯤꯎꯀꯦꯃꯤꯌꯥ (AML) ꯂꯥꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ 30% ꯂꯩ꯫
- ꯑꯦꯛꯌꯨꯠ ꯃꯥꯏꯂꯣꯏꯗ ꯂꯤꯎꯀꯦꯃꯤꯌꯥ (AML): ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏꯁꯤꯡꯒꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ 3%ꯗꯤ ꯂꯥꯏꯑꯣꯡ ꯈꯪꯗꯣꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯆꯍꯤ 10ꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯦꯛꯌꯨꯠ ꯃꯥꯏꯂꯣꯏꯗ ꯂꯤꯎꯀꯦꯃꯤꯌꯥ (AML) ꯂꯥꯀꯏ꯫ ꯑꯦ.ꯑꯦꯝ.ꯑꯦꯜ.ꯅꯥ ꯕꯣꯟ ꯃꯦꯔꯣꯗꯒꯤ ꯍꯧꯔꯀꯄꯥ ꯁꯥꯊꯤꯕꯥ ꯕ꯭ꯂꯗ ꯀꯦꯟꯁꯔ ꯑꯃꯅꯤ ꯑꯃꯁꯨꯡ ꯃꯁꯤꯅꯥ ꯏꯗꯥ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯃꯇꯨꯡꯗꯥ ꯍꯀꯆꯥꯡꯒꯤ ꯑꯇꯩ ꯃꯐꯃꯁꯤꯡꯗꯥ ꯁꯟꯗꯣꯀꯄꯥ ꯌꯥꯏ꯫ ꯃꯁꯤ ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯥ ꯃꯊꯧ ꯇꯥꯏ, ꯑꯗꯨꯕꯨ ꯍꯤꯡꯕꯒꯤ ꯆꯥꯡꯗꯤ ꯌꯥꯝꯅꯥ ꯋꯥꯡꯏ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯀꯔꯤꯅꯣ?
ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤ ꯑꯌꯥꯝꯕꯗꯤ ꯌꯥꯝꯅꯥ ꯇꯞꯅꯥ ꯎꯕꯥ ꯐꯪꯏ, ꯑꯃꯁꯨꯡ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯃꯇꯃꯗꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯕꯥ ꯌꯥꯏ꯫ ꯑꯍꯥꯅꯕꯗꯥ ꯂꯥꯌꯅꯥ ꯀꯌꯥꯗꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯃꯌꯦꯛ ꯁꯦꯡꯗꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯏ:
- ꯀꯣꯛ ꯆꯤꯛꯄ.
- ꯃꯃꯤꯠ ꯇꯥꯡꯕꯥ꯫
- ꯋꯥꯕ.
- ꯕ꯭ꯂꯗ ꯄ꯭ꯔꯦꯁꯔ ꯋꯥꯡꯈꯠꯄꯥ꯫
- ꯕ꯭ꯂꯔ ꯚꯤꯖꯟ ꯅꯠꯠꯔꯒꯥ ꯗꯕꯜ ꯚꯤꯖꯟ꯫
- ꯅꯥꯀꯣꯡꯗꯥ ꯔꯤꯡ ꯁꯣꯀꯄꯥ (`(Tinnitus)`)꯫
ꯃꯇꯃꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ, ꯍꯦꯟꯅꯥ ꯑꯀꯛꯅꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯥꯀꯄꯥ ꯌꯥꯏ:
- ꯃꯔꯨꯑꯣꯏꯅꯥ ꯑꯌꯨꯛ-ꯅꯨꯡꯊꯤꯂꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
- ꯃꯔꯨꯑꯣꯏꯅꯥ ꯂꯦꯡ-ꯑꯣꯠꯄꯗꯥ ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
- ꯃꯔꯨꯑꯣꯏꯅꯥ ꯑꯁꯥꯕꯥ ꯏꯁꯤꯡꯗꯥ ꯂꯨꯄꯊꯣꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯈꯣꯡ ꯍꯥꯝꯕꯥ꯫ (ꯃꯁꯤ PVꯒꯤ ꯑꯀꯛꯅꯕꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯅꯤ)
- ꯂꯦꯡ-ꯑꯣꯠꯄꯗꯥ ꯂꯥꯎꯕꯥ, ꯑꯁꯥꯕꯥ, ꯅꯥꯕꯥ, ꯅꯠꯠꯔꯒꯥ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯃꯩꯅꯥ ꯆꯥꯀꯄꯥ꯫
- ꯏ ꯌꯥꯝꯅꯥ ꯊꯣꯀꯄꯥ ꯅꯠꯠꯔꯒꯥ ꯁꯣꯀꯄꯥ꯫
- ꯅꯥꯀꯣꯡ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯒꯤ ꯏ ꯊꯣꯀꯄꯥ꯫
- ꯃꯔꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯇꯅꯥ ꯊꯤꯅꯥ ꯂꯩꯕꯥ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ PV ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ ꯑꯃꯁꯨꯡ ꯁꯦꯀꯦꯟꯗꯔꯤ ꯀꯟꯗꯤꯁꯅꯁꯤꯡꯗꯥ ꯄ꯭ꯔꯣꯒ꯭ꯔꯦꯁ ꯇꯧꯔꯕꯗꯤ, ꯃꯔꯤ ꯂꯩꯅꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯁꯨ ꯊꯣꯀꯄꯥ ꯌꯥꯏ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅ:
ꯁ꯭ꯞꯂꯦꯅꯣꯃꯦꯒꯥꯂꯤꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯀꯔꯤꯒꯨꯝꯕꯥ ꯄꯣꯠꯁꯛ ꯑꯃꯒꯨꯝꯕꯥ ꯑꯅꯥꯕꯥ ꯑꯃꯥ ꯈꯣꯡꯒꯤ ꯃꯊꯛꯀꯤ ꯂꯦꯃꯍꯧꯔꯤꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨꯗꯥ ꯆꯦꯟꯊꯈꯤ꯫
- ꯁ꯭ꯇꯣꯃꯥꯛ-ꯐꯤꯜꯂꯤꯡ ꯑꯦꯛꯁꯄꯤꯔꯤꯑꯦꯟꯁ ꯑꯃꯥ꯫
- ꯈꯔꯥ ꯆꯥꯕꯥ ꯂꯣꯏꯔꯕꯥ ꯃꯇꯨꯡꯗꯁꯨ ꯊꯋꯥꯌ ꯌꯥꯑꯣꯕꯥ ꯐꯥꯑꯣꯏ꯫
ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯂꯁꯔ (`ꯄꯦꯄꯇꯤꯛ ꯑꯂꯁꯔ ꯗꯤꯖꯤꯖ`)ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯈꯣꯡ ꯍꯥꯝꯕꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯂꯥꯀꯄꯥ ꯑꯅꯥꯕꯥ꯫
- ꯊꯝꯃꯣꯌ ꯁꯣꯀꯄꯥ꯫
- ꯑꯦꯁꯤꯗ ꯔꯤꯐ꯭ꯂꯛꯁ ꯇꯧꯕꯥ꯫
ꯒꯥꯎꯇꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ: ꯱.
- ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯍꯅꯕꯥ꯫
- ꯁꯔꯨ ꯇꯥꯡꯁꯤꯡ (joint stiffness) ꯂꯩꯕꯥ꯫
- ꯑꯆꯧꯕꯥ ꯈꯣꯡꯄꯥꯛ ꯑꯗꯨ ꯁꯣꯀꯄꯥ꯫
ꯀꯤꯗꯅꯤ ꯁ꯭ꯇꯣꯅꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯃꯈꯥ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ ꯅꯠꯠꯔꯒꯥ ꯐ꯭ꯂꯦꯉ꯭ꯀꯇꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯄꯥ꯫
- ꯌꯨꯔꯤꯟ ꯇꯧꯕꯥ ꯃꯇꯃꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯄꯥ꯫
- ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯌꯨꯔꯤꯟ ꯇꯧꯕꯥ ꯃꯊꯧ ꯇꯥꯕꯥ꯫
ꯕꯨꯗ-ꯆꯤꯌꯥꯔꯤ ꯁꯤꯟꯗꯣꯃꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯂꯤꯚꯔ ꯁꯣꯟꯊꯕꯥ, ꯈꯣꯡꯒꯤ ꯃꯊꯛ ꯊꯪꯕꯥ ꯁꯔꯨꯛꯇꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯏꯪꯊꯕꯥ꯫
- ꯃꯤꯠ ꯑꯃꯁꯨꯡ ꯈꯣꯡꯗꯥ ꯌꯦꯔꯨꯝ ꯀꯣꯀꯄꯥ (jaundice)꯫
- ꯑꯦꯁꯤꯇꯤꯁ ꯑꯃꯁꯨꯡ ꯏꯗꯤꯃꯥ꯫
ꯗꯤꯞ ꯚꯦꯟ ꯊ꯭ꯔꯣꯝꯕꯣꯁꯤꯁ (DVT)ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯃꯈꯨꯠ ꯅꯠꯠꯔꯒꯥ ꯈꯣꯡ ꯑꯃꯗꯥ ꯁꯣꯛ-ꯄꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯁꯣꯀꯄꯥ ꯃꯇꯃꯗꯥ ꯑꯁꯣꯛ-ꯑꯄꯟ ꯊꯣꯀꯄꯥ꯫
- ꯃꯐꯝ ꯑꯗꯨꯗꯥ ꯂꯥꯂꯍꯧꯕꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯁꯥꯕꯥ ꯏꯁꯤꯡ ꯂꯩ꯫
- ꯈꯣꯡꯒꯤ ꯃꯊꯛꯇꯥ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯂꯁꯤꯡ (bulging blood vessels) ꯎꯕꯥ ꯐꯪꯕꯥ꯫
ꯂꯪꯁꯇꯥ ꯏ ꯊꯣꯀꯄꯥ (Pulmonary Embolism - PE)ꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ:
- ꯈꯪꯍꯧꯗꯅꯥ ꯊꯝꯃꯣꯌ ꯁꯣꯀꯄꯥ꯫
- ꯁ꯭ꯕꯔ ꯍꯣꯅꯕꯥ ꯋꯥꯕꯥ꯫
- ꯍꯥꯔꯇꯀꯤ ꯔꯦꯠ ꯍꯦꯅꯒꯠꯂꯀꯏ꯫
ꯑꯦꯅꯤꯃꯤꯌꯥꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ (PV ꯂꯥꯌꯅꯥꯒꯤ ꯑꯔꯣꯏꯕꯥ ꯁ꯭ꯇꯦꯖꯁꯤꯡꯗꯥ):
- ꯃꯤꯠ ꯎꯗꯕꯥ (vertigo)꯫
- ꯄꯦꯂꯦ ꯁ꯭ꯀꯤꯟ꯫
- ꯋꯥꯕ.
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯀꯔꯤꯅꯥ ꯊꯣꯀꯍꯅꯕꯒꯦ?
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯑꯩꯈꯣꯌꯒꯤ ꯁꯔꯨ ꯇꯥꯡꯒꯤ ꯇꯔꯨ-ꯇꯅꯥꯅꯕꯥ, ꯁ꯭ꯄꯣꯟꯖ ꯑꯣꯏꯕꯥ ꯁꯔꯨꯛ ꯑꯗꯨꯗꯒꯤ ꯍꯧꯏ, ꯃꯗꯨ ꯕꯣꯟ ꯃꯦꯔꯣ ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫ ꯃꯁꯤꯗꯥ ꯑꯅꯧꯕꯥ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯁꯦꯃꯒꯠꯂꯤ꯫ PV ꯑꯁꯤ ꯕꯣꯟ ꯃꯦꯔꯣꯗꯥ ꯂꯩꯕꯥ ꯁ꯭ꯇꯦꯝ ꯁꯦꯜ ꯑꯃꯈꯛꯇꯗꯥ ꯖꯤꯟ ꯑꯃꯈꯛꯇꯒꯤ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯃꯗꯒꯤ ꯍꯧꯏ꯫ ꯃꯇꯃꯒꯤ ꯹꯰% ꯍꯦꯟꯅꯥ, ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤ JAK2 ꯀꯧꯕꯥ ꯖꯤꯟ ꯑꯃꯗꯥ ꯂꯩ꯫
ꯃꯁꯤꯒꯤ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯇꯧꯔꯕꯥ ꯖꯤꯟ ꯑꯁꯤꯅꯥ ꯁ꯭ꯇꯦꯝ ꯁꯦꯜ ꯑꯁꯤ ꯃꯈꯥ ꯇꯥꯅꯥ ꯄꯣꯀꯄꯥ ꯉꯝꯅꯕꯥ ꯍꯥꯌꯔꯤ꯫ ꯄꯨꯊꯣꯀꯄꯥ ꯁꯦꯜ ꯈꯨꯗꯤꯡꯃꯛ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯃꯈꯥ ꯇꯥꯅꯥ ꯔꯤꯞꯂꯤꯀꯦꯠ ꯇꯧꯏ꯫ ꯂꯣꯏꯁꯤꯜꯂꯀꯄꯗꯥ, ꯑꯦꯕꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯕꯣꯟ ꯃꯦꯔꯣ ꯑꯗꯨ ꯃꯄꯨꯡ ꯐꯥꯍꯜꯂꯤ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯅꯣꯔꯃꯦꯜ ꯁꯦꯂꯁꯤꯡꯒꯤꯗꯃꯛꯇꯥ ꯃꯐꯝ ꯑꯃꯠꯇꯥ ꯂꯩꯍꯟꯗꯦ꯫
ꯑꯌꯥꯝꯕꯥ ꯀꯦꯁꯁꯤꯡꯗꯥ, ꯃꯁꯤꯒꯤ `JAK2` ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯏꯅꯍꯦꯔꯤ ꯇꯧꯕꯥ ꯄꯣꯠꯁꯛ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯃꯗꯥ ꯊꯣꯀꯄꯥ ꯊꯧꯗꯣꯛ ꯑꯃꯅꯤ, ꯃꯔꯝ ꯈꯉꯗꯅꯥ ꯊꯣꯀꯄꯥ ꯊꯧꯗꯣꯛ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯌꯥꯝꯅꯥ ꯊꯨꯅꯥ, ꯏꯃꯨꯡꯒꯤ ꯃꯤꯑꯣꯏ ꯀꯌꯥꯗꯥ ꯄꯤ.ꯚꯤ.
ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯈꯪꯗꯣꯀꯄꯒꯦ?
ꯋꯥꯔꯜꯗ ꯍꯦꯜꯊ ꯑꯣꯔꯒꯅꯥꯏꯖꯦꯁꯟ (ꯗꯕꯜꯌꯨ.ꯑꯩꯆ.ꯑꯣ.)ꯅꯥ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (ꯄꯤ.ꯚꯤ.) ꯈꯉꯗꯣꯛꯅꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ ꯑꯍꯨꯝ ꯊꯝꯂꯦ꯫ ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ ꯑꯍꯨꯝ ꯑꯁꯤ ꯀꯅꯐꯥꯔꯝ ꯇꯧꯒꯗꯕꯅꯤ꯫
ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ 1: ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯜ ꯃꯁꯤꯡ ꯌꯥꯝꯅꯥ ꯂꯩꯕꯥ ꯕ꯭ꯂꯗ ꯇꯦꯁ꯭ꯠ ꯑꯃꯥ:
ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯌꯥꯏ:
- ꯍꯦꯃꯣꯒ꯭ꯂꯣꯕꯤꯅꯒꯤ ꯆꯥꯡ ꯋꯥꯡꯈꯠꯄꯥ (ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯗꯥ ꯌꯥꯎꯕꯥ ꯄ꯭ꯔꯣꯇꯤꯟ ꯑꯃꯥ)꯫
- ꯍꯦꯃꯥꯇꯣꯛꯔꯥꯏꯠ ꯂꯦꯚꯦꯜ ꯋꯥꯡꯈꯠꯄꯥ (ꯏꯗꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯆꯥꯗꯥ)꯫
- ꯕ꯭ꯂꯗ ꯚꯣꯜꯌꯨꯝ ꯋꯥꯡꯕꯥ (ꯔꯦꯗ ꯁꯦꯜ ꯃꯥꯁ)꯫
ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ 2: ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯕꯨ ꯎꯠꯂꯤꯕꯥ ꯕꯣꯟ ꯃꯦꯔꯣ ꯕꯥꯏꯑꯣꯞꯁꯤ:
- ꯕꯣꯟ ꯃꯦꯔꯣꯗꯥ ꯕ꯭ꯂꯗ ꯁꯦꯜ ꯌꯥꯝꯅꯥ ꯌꯥꯎꯕꯥ, ꯅꯠꯠꯔꯒꯥ...
- ꯄꯤꯀꯄꯥ ꯃꯦꯒꯥꯀꯦꯔꯤꯑꯣꯁꯥꯏꯇꯁꯤꯡ (ꯕ꯭ꯂꯗ ꯄ꯭ꯂꯦꯇꯂꯦꯇꯁꯤꯡ ꯁꯦꯝꯕꯥ ꯁꯦꯂꯁꯤꯡ) ꯌꯥꯝꯅꯥ ꯌꯥꯎꯕꯥ꯫
ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ ꯳: ꯑꯍꯨꯃꯁꯨꯕꯥ ꯀ꯭ꯔꯥꯏꯇꯦꯔꯤꯌꯥ ꯑꯁꯤ ꯑꯅꯤꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯕꯨ ꯎꯠꯇꯨꯅꯥ ꯂꯣꯏꯁꯤꯅꯕꯥ ꯌꯥꯏ:
- ꯃꯣꯂꯤꯛꯌꯨꯂꯔ ꯇꯦꯁ꯭ꯇꯤꯡꯒꯤ ꯈꯨꯠꯊꯥꯡꯗꯥ ꯖꯦ.ꯑꯦ.ꯀꯦ.꯲ ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯂꯩ ꯍꯥꯌꯕꯥ ꯀꯅꯐꯔꯝ ꯇꯧꯕꯥ, ꯅꯠꯔꯒꯥ...
- ꯏꯒꯤ ꯇꯦꯁ꯭ꯠ ꯑꯃꯅꯥ ꯏꯗꯥ `ꯏꯔꯤꯊ꯭ꯔꯣꯄꯣꯏꯇꯤꯟ' (ꯀꯤꯗꯅꯤꯅꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯄꯨꯊꯣꯀꯄꯗꯥ ꯊꯧꯒꯠꯄꯥ ꯍꯣꯔꯃꯣꯟ ꯑꯃꯥ)ꯒꯤ ꯆꯥꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯅꯦꯝꯃꯤ ꯍꯥꯌꯕꯥ ꯀꯅꯐꯤꯗ ꯇꯧꯏ꯫
"ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯅꯥ ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ ꯂꯩꯕ꯭ꯔꯥ ꯅꯠꯔꯒꯥ ꯂꯩꯇꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨ ꯑꯆꯨꯝꯕꯥ ꯃꯑꯣꯡꯗꯥ ꯈꯉꯍꯟꯅꯕꯥ ꯍꯥꯌꯔꯤꯕꯥ ꯄꯨꯝꯅꯃꯛ ꯑꯁꯤ ꯌꯦꯡꯒꯅꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡ ꯑꯃꯠꯇꯥ ꯂꯩꯔꯕꯗꯤ ꯗꯣꯛꯇꯔ ꯑꯃꯒꯥ ꯇꯥꯟꯅꯗꯨꯅꯥ ꯄꯥꯎꯇꯥꯛ ꯂꯧꯕꯥ ꯑꯁꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯐꯩ꯫"
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯀꯔꯝꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯒꯦ?
PVꯒꯤ ꯑꯍꯥꯅꯕꯥ ꯁ꯭ꯇꯦꯖꯁꯤꯡꯗꯥ, ꯂꯥꯏꯌꯦꯡ ꯑꯁꯤ ꯌꯥꯝꯅꯥ ꯂꯥꯏ꯫ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯁꯤꯡꯁꯤ ꯌꯥꯎꯏ:
ꯐ꯭ꯂꯦꯕꯣꯇꯣꯃꯤ (ꯕ꯭ꯂꯗꯂꯦꯇꯤꯡ) .
ꯃꯁꯤ PVꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯃꯁꯨꯡ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡꯅꯤ꯫ ꯃꯁꯤ ꯑꯗꯣꯝꯅꯥ ꯏ ꯄꯤꯕꯤꯔꯝꯕꯥ ꯑꯗꯨꯒꯨꯝꯅꯥ ꯇꯧꯏ꯫ ꯍꯦꯂꯊꯀꯦꯌꯔ ꯄ꯭ꯔꯣꯚꯥꯏꯗꯔ ꯑꯃꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯈꯨꯠꯁꯥꯗꯥ ꯂꯩꯕꯥ ꯚꯦꯅꯝ ꯑꯃꯗꯥ ꯅꯤꯗꯜ ꯑꯃꯥ ꯊꯥꯗꯨꯅꯥ ꯏꯒꯤ ꯆꯥꯡ ꯈꯔꯥ ꯂꯧꯊꯣꯀꯏ (ꯃꯍꯧꯁꯥꯅꯥ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯄꯤꯟꯇ ꯑꯃꯥ, ꯑꯗꯨꯕꯨ ꯆꯥꯡ ꯑꯗꯨ ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯅꯒꯤ ꯃꯇꯨꯡꯏꯟꯅꯥ ꯈꯦꯠꯅꯕꯥ ꯌꯥꯏ)꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯑꯄꯨꯅꯕꯥ ꯕ꯭ꯂꯗ ꯚꯣꯜꯌꯨꯝ ꯑꯃꯁꯨꯡ ꯑꯍꯦꯅꯕꯥ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡꯒꯤ ꯃꯁꯤꯡ ꯍꯟꯊꯍꯜꯂꯤ꯫
ꯂꯣ-ꯗꯣꯖ ꯑꯦꯁ꯭ꯄꯤꯔꯤꯟ꯫
ꯃꯁꯤ ꯑꯗꯣꯝꯅꯥ ꯐꯥꯔꯃꯥꯁꯤꯗꯥ ꯂꯧꯕꯥ ꯌꯥꯕꯥ ꯍꯤꯗꯥꯛ ꯑꯃꯅꯤ꯫ ꯃꯍꯧꯁꯥꯅꯥ ꯃꯁꯤ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ ꯍꯟꯊꯍꯟꯅꯕꯒꯤꯗꯃꯛ ꯄꯤꯖꯩ꯫ ꯅꯣꯡꯃꯗꯥ ꯑꯃꯨꯀꯈꯛꯇꯪ ꯌꯥꯝꯅꯥ ꯅꯦꯝꯕꯥ ꯗꯣꯖꯗꯥ ꯊꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯑꯦꯁ꯭ꯄꯤꯔꯤꯟ ꯑꯁꯤꯅꯥ ꯕ꯭ꯂꯗ ꯄ꯭ꯂꯦꯇꯂꯦꯇꯁꯤꯡ ꯑꯁꯤ ꯂꯦꯡꯗꯅꯥ ꯂꯩꯍꯟꯗꯦ꯫ ꯃꯁꯤꯅꯥ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯁꯣꯀꯄꯒꯨꯝꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯗꯁꯨ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯃꯁꯤꯅꯥ ꯈꯣꯡꯗꯥ ꯈꯔꯥ ꯁꯣꯀꯍꯜꯂꯤ ꯑꯃꯁꯨꯡ ꯏ ꯊꯣꯀꯄꯥ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫ ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯁ꯭ꯇꯣꯃꯥꯛ ꯑꯂꯁꯔ ꯂꯩꯔꯕꯗꯤ ꯃꯁꯤ ꯑꯐꯕꯥ ꯋꯥꯈꯜꯂꯣꯟ ꯑꯃꯅꯤ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯌꯥꯝꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯅꯠꯠꯔꯒꯥ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯃꯃꯥꯡꯗꯥ ꯏ ꯊꯣꯀꯄꯥ (thrombosis)ꯒꯤ ꯍꯤꯁ꯭ꯇꯔꯤ ꯂꯩꯔꯕꯗꯤ, ꯅꯍꯥꯀꯄꯨ ꯔꯤꯁ꯭ꯛ ꯂꯩꯕꯥ ꯀꯥꯡꯂꯨꯞ ꯑꯃꯗꯥ ꯊꯃꯖꯤꯅꯕꯥ ꯌꯥꯏ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯑꯣꯄꯁꯅꯁꯤꯡꯁꯨ ꯄꯤꯕꯥ ꯌꯥꯏ꯫ ꯃꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈꯔꯗꯤ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤ:
ꯏꯆꯝ ꯆꯝꯕꯥ ꯍꯟꯊꯍꯟꯅꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ:
ꯄꯤ.ꯚꯤ.
- ꯑꯦꯟꯇꯤꯍꯤꯁ꯭ꯇꯥꯃꯤꯅꯁꯤꯡ: ꯃꯁꯤ ꯑꯦꯂꯥꯔꯖꯤꯒꯤꯗꯃꯛꯇꯥ ꯄꯤꯕꯥ ꯀꯃꯟ ꯑꯣꯏꯕꯥ ꯍꯤꯗꯥꯀꯁꯤꯡꯅꯤ꯫
- ꯐꯣꯇꯣꯊꯦꯔꯥꯄꯤ: ꯑꯂꯠꯔꯥꯚꯥꯏꯑꯣꯂꯦꯠ (UVA) ꯃꯉꯥꯜ ꯑꯁꯤ ꯁꯣꯔꯥꯂꯦꯟ (ꯃꯉꯥꯜ ꯊꯦꯔꯥꯄꯤꯗꯥ ꯈꯣꯡꯗꯥ ꯁꯦꯟꯁꯤꯇꯤꯚ ꯑꯣꯏꯕꯥ ꯑꯣꯔꯒꯥꯅꯤꯛ ꯀꯝꯄꯥꯎꯟꯗ ꯑꯃꯥ) ꯀꯧꯕꯥ ꯀꯦꯃꯤꯀꯦꯜ ꯑꯃꯒꯥ ꯄꯨꯟꯁꯤꯟꯅꯗꯨꯅꯥ ꯂꯥꯌꯦꯡꯕꯅꯤ꯫
- ꯑꯦꯁ.ꯑꯦꯁ.ꯑꯥꯔ.ꯑꯥꯏ.ꯁꯤꯡ (ꯁꯦꯂꯦꯛꯇꯤꯚ ꯁꯦꯔꯣꯇꯣꯅꯤꯟ ꯔꯤꯌꯨꯄꯇꯦꯛ ꯏꯅꯍꯤꯕꯤꯇꯔꯁꯤꯡ): ꯃꯁꯤ ꯃꯍꯧꯁꯥꯅꯥ ꯗꯤꯞꯔꯦꯁꯅꯒꯤꯗꯃꯛꯇꯥ ꯄꯤꯕꯥ ꯍꯤꯗꯥꯛ ꯃꯈꯜ ꯑꯃꯅꯤ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯌꯥꯝꯅꯥ ꯅꯦꯝꯕꯥ ꯗꯣꯖꯗꯥ ꯄꯤꯔꯀꯄꯥ ꯃꯇꯃꯗꯥ, ꯃꯈꯣꯌ ꯑꯁꯤ ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯨꯝꯕꯥ ꯍꯀꯆꯥꯡꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯗꯁꯨ ꯏꯐꯦꯛꯇꯤꯕ ꯑꯣꯏ ꯍꯥꯌꯕꯥ ꯈꯉꯂꯦ꯫
ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯜ ꯃꯁꯤꯡ ꯍꯟꯊꯍꯅꯕꯥ ꯉꯝꯕꯥ ꯗ꯭ꯔꯒꯁꯤꯡ:
ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤ ꯃꯁꯥ ꯃꯊꯟꯇꯥ ꯅꯠꯠꯔꯒꯥ ꯑꯃꯒꯥ ꯑꯃꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯁꯤꯖꯤꯟꯅꯕꯥ ꯌꯥꯏ꯫ ꯈꯨꯗꯃꯁꯤꯡ: ꯱.
- `ꯍꯥꯏꯗ꯭ꯔꯣꯛꯁꯤꯌꯨꯔꯤꯌꯥ`꯫
- `ꯏꯟꯇꯔꯐꯦꯔꯣꯟ ꯑꯥꯂꯐꯥ`꯫
- `ꯔꯨꯛꯁꯣꯂꯤꯇꯤꯅꯤꯕ`꯫
- `ꯕꯨꯁꯨꯂꯐꯥꯟ` ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫
ꯀ꯭ꯂꯤꯅꯤꯀꯦꯜ ꯇ꯭ꯔꯥꯏꯑꯦꯜ ꯇꯧꯕꯥ꯫
ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯃꯤꯌꯥꯃꯗꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯅꯧꯕꯥ ꯂꯥꯌꯦꯡꯁꯤꯡ ꯍꯣꯠꯅꯕꯒꯤ ꯈꯨꯗꯣꯡꯆꯥꯕꯥ ꯄꯤꯔꯤ ꯑꯃꯁꯨꯡ ꯃꯦꯗꯤꯀꯦꯜ ꯔꯤꯁꯔꯆꯇꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯂꯤ꯫ ꯍꯧꯖꯤꯛ ꯔꯤꯁꯔꯆꯀꯤ ꯇꯥꯉ꯭ꯀꯛꯇꯥ ꯂꯩꯔꯤꯕꯥ ꯗ꯭ꯔꯒ ꯈꯔꯗꯤ ꯃꯈꯥꯒꯤ ꯑꯁꯤꯅꯤ:
- `ꯄꯦꯒꯏꯟꯇꯔꯐꯦꯔꯣꯟ ꯑꯥꯂꯐꯥ-꯲ꯑꯦ`꯫
- `ꯒꯤꯚꯤꯅꯣꯁ꯭ꯇꯦꯠ`꯫
- `ꯏꯗꯥꯁꯅꯇꯂꯤꯟ` ꯍꯥꯌꯅꯥ ꯀꯧꯏ꯫
ꯕꯣꯟ ꯃꯦꯔꯣ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯕꯥ꯫
ꯀꯦꯁ ꯈꯔꯗꯗꯤ, ꯕꯣꯟ ꯃꯦꯔꯣ ꯇ꯭ꯔꯥꯟꯁꯞꯂꯥꯟꯇ ꯇꯧꯅꯕꯥ ꯔꯦꯀꯃꯦꯟꯗ ꯇꯧꯕꯥ ꯌꯥꯏ꯫ ꯗꯣꯛꯇꯔ ꯑꯃꯅꯥ ꯃꯁꯤꯒꯤ ꯋꯥꯔꯦꯞ ꯑꯁꯤ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯒꯤ ꯁꯥꯊꯤꯕꯥ ꯃꯑꯣꯡ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯆꯥꯡꯅꯥ ꯐꯒꯠꯂꯀꯄꯥ ꯉꯝꯕꯒꯤ ꯃꯑꯣꯡ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯐꯦꯛꯇꯔ ꯀꯌꯥꯗꯥ ꯌꯨꯝꯐꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯂꯧꯒꯅꯤ꯫
ꯁꯄꯣꯔꯇꯤꯕ ꯀꯦꯌꯔ꯫
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯀꯤ PV ꯑꯗꯨ ꯂꯥꯏꯌꯦꯡꯂꯕꯁꯨ ꯃꯈꯥ ꯇꯥꯅꯥ ꯐꯒꯠꯂꯛꯂꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯃꯦꯅꯦꯖ ꯇꯧꯕꯗꯥ ꯃꯤꯠꯌꯦꯡ ꯊꯃꯒꯅꯤ꯫ PVꯒꯤ ꯃꯇꯨꯡꯒꯤ ꯁ꯭ꯇꯦꯖꯁꯤꯡꯗꯥ, ꯅꯍꯥꯛꯅꯥ ꯑꯦꯅꯤꯃꯤꯌꯥ ꯑꯃꯁꯨꯡ ꯁ꯭ꯞꯂꯤꯟ ꯍꯦꯅꯒꯠꯂꯀꯄꯥ ꯌꯥꯏ꯫ ꯅꯍꯥꯀꯄꯨ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤꯕꯥ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯑꯁꯤ ꯄꯤꯕꯥ ꯌꯥꯏ:
- ꯄꯦꯏꯅꯀꯤꯂꯥꯔꯁꯤꯡ꯫
- ꯕ꯭ꯂꯗ ꯇ꯭ꯔꯥꯟꯁꯐ꯭ꯌꯨꯁꯟ ꯇꯧꯕꯥ꯫
- ꯁ꯭ꯞꯂꯤꯅꯗꯥ ꯂꯣ-ꯗꯣꯖ ꯔꯦꯗꯤꯑꯦꯁꯟ ꯊꯦꯔꯥꯄꯤ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯅꯥ ꯅꯥꯕꯥ ꯃꯤꯑꯣꯏ ꯑꯃꯒꯤ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯀꯌꯥꯅꯣ?
ꯍꯟꯗꯛꯀꯤ ꯁ꯭ꯇꯗꯤꯁꯤꯡꯅꯥ ꯇꯥꯛꯂꯤ ꯃꯗꯨꯗꯤ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯈꯪꯗꯣꯛꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯆꯥꯡꯆꯠꯇꯥ ꯄꯨꯟꯁꯤꯒꯤ ꯃꯇꯝ ꯑꯁꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ 20ꯅꯤ꯫ ꯁꯤꯕꯒꯤ ꯆꯥꯡꯆꯠ ꯑꯁꯤ ꯆꯥꯎꯔꯥꯛꯅꯥ ꯆꯍꯤ ꯷꯷ꯅꯤ꯫ ꯁꯤꯕꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯝ ꯑꯁꯤ ꯏ ꯊꯣꯀꯄꯒꯤ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ (ꯆꯥꯎꯔꯥꯛꯅꯥ 33%)ꯅꯤ꯫ ꯑꯅꯤꯁꯨꯕꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯃꯔꯝ ꯑꯁꯤ ꯀꯦꯟꯁꯔ (ꯆꯥꯎꯔꯥꯛꯅꯥ 15%)ꯅꯤ꯫
"ꯁ꯭ꯇꯦꯇꯤꯁ꯭ꯇꯤꯀꯦꯂꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯂꯥꯡꯇꯛꯅꯒꯅꯨ꯫ ꯃꯁꯤ ꯅꯣꯔꯃꯦꯜ ꯚꯦꯜꯌꯨꯁꯤꯡꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯑꯆꯨꯝꯕꯥ ꯂꯥꯌꯦꯡ ꯐꯪꯂꯕꯗꯤ ꯑꯃꯁꯨꯡ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯑꯃꯥ ꯄꯨꯔꯛꯂꯕꯗꯤ ꯅꯍꯥꯛꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯕꯥ ꯉꯃꯒꯅꯤ꯫"
ꯑꯩꯅꯥ ꯏꯁꯥꯕꯨ ꯀꯔꯝꯅꯥ ꯌꯦꯡꯁꯤꯅꯕꯤꯒꯅꯤ ꯑꯃꯁꯨꯡ ꯑꯩꯒꯤ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯗꯨ ꯀꯔꯝꯅꯥ ꯃꯦꯅꯦꯖ ꯇꯧꯒꯅꯤ?
ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯀꯟꯇꯦꯛꯇ ꯇꯧꯕꯥ ꯍꯥꯌꯕꯁꯤ ꯌꯥꯝꯅꯥ ꯃꯔꯨꯑꯣꯏ꯫ ꯃꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯀꯔꯝꯅꯥ ꯍꯦꯅꯒꯠꯂꯀꯄꯒꯦ ꯍꯥꯌꯕꯗꯨ ꯌꯦꯡꯁꯤꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯒꯅꯤ꯫ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯌꯦꯡꯕꯗꯥ ꯀꯔꯝꯅꯥ ꯔꯦꯁꯄꯣꯟꯁ ꯇꯧꯔꯤꯕꯒꯦ ꯑꯃꯁꯨꯡ ꯅꯍꯥꯛꯅꯥ ꯁꯥꯏꯗ ꯏꯐꯦꯛꯇ ꯑꯃꯠꯇꯥ ꯊꯦꯡꯅꯔꯤꯕ꯭ꯔꯥ ꯍꯥꯌꯕꯗꯨꯁꯨ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯗꯥ ꯈꯪꯍꯅꯕꯥ ꯌꯥꯏ꯫ ꯅꯍꯥꯛꯅꯥ ꯁꯥꯊꯤꯕꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯂꯩꯍꯟꯗꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯍꯤꯡꯕꯥ ꯌꯥꯏ꯫
ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯇꯦꯁ꯭ꯠ ꯇꯧꯕꯥ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯌꯦꯡꯕꯒꯤ ꯃꯊꯛꯇꯥ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯅꯥ ꯏ ꯊꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯑꯇꯩ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡ ꯊꯤꯡꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯕꯥ ꯌꯥꯕꯥ ꯏꯆꯝ ꯆꯝꯕꯥ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡꯒꯤ ꯑꯍꯣꯡꯕꯥ ꯈꯔꯁꯨ ꯄꯤꯒꯅꯤ꯫ ꯈꯨꯗꯝ ꯑꯣꯏꯅ:
- ꯁꯥꯖꯦꯜ ꯇꯧꯕ. ꯑꯦꯛꯁꯔꯁꯥꯏꯖ ꯈꯔꯥ ꯇꯧꯕꯅꯥ ꯕ꯭ꯂꯗ ꯁꯔꯛꯌꯨꯂꯦꯁꯟ ꯐꯒꯠꯍꯅꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ꯫
- ꯃꯩꯈꯨ ꯊꯥꯗꯣꯀꯄꯥ ꯊꯤꯡꯖꯤꯜꯂꯨ꯫ ꯃꯩꯈꯨ ꯁꯤꯖꯤꯟꯅꯕꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯕ꯭ꯂꯗ ꯚꯦꯁꯦꯂꯁꯤꯡ ꯑꯗꯨ ꯀꯨꯄꯁꯤꯜꯂꯤ꯫
- ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯝꯕꯥ ꯑꯀꯣꯌꯔꯣꯅꯁꯤꯡꯗꯒꯤ ꯂꯥꯞꯅꯥ ꯂꯩꯌꯨ꯫ ꯑꯋꯥꯡꯕꯥ ꯃꯐꯃꯗꯥ ꯂꯩꯕꯅꯥ ꯏꯗꯥ ꯑꯣꯛꯁꯤꯖꯦꯅꯒꯤ ꯆꯥꯡ ꯅꯦꯃꯊꯍꯅꯕꯥ ꯌꯥꯏ꯫
- ꯅꯍꯥꯛꯀꯤ ꯕ꯭ꯂꯗ ꯄ꯭ꯔꯦꯁꯔ ꯑꯗꯨ ꯀꯟꯠꯔꯣꯜ ꯇꯧ꯫ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯑꯔꯨꯝꯕꯥ ꯑꯃꯥ ꯊꯝꯕꯅꯥ ꯃꯁꯤꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯒꯅꯤ꯫
ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV) ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯃꯈꯜ ꯑꯃꯅꯤ ꯍꯥꯌꯔꯕꯁꯨ, ꯃꯤꯑꯣꯏ ꯀꯌꯥꯅꯥ ꯂꯥꯌꯅꯥ ꯑꯁꯤꯅꯥ ꯅꯥꯔꯦ ꯍꯥꯌꯅꯥ ꯈꯪꯂꯕꯥ ꯃꯇꯨꯡꯗꯥ ꯆꯍꯤ ꯇꯔꯥꯒꯤ ꯈꯨꯖꯤꯡ ꯀꯌꯥ ꯐꯅꯥ ꯍꯤꯡꯏ꯫ ꯃꯁꯤꯒꯤ ꯀꯦꯟꯁꯔ ꯑꯁꯤ ꯁꯦꯂꯁꯤꯡ ꯑꯁꯤ ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯄꯨꯊꯣꯀꯄꯅꯥ ꯃꯔꯝ ꯑꯣꯏꯗꯨꯅꯥ ꯊꯣꯀꯏ꯫ ꯑꯗꯨꯝ ꯑꯣꯏꯅꯃꯛ, ꯀꯟꯠꯔꯣꯜ ꯇꯧꯗꯅꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ ꯄꯨꯊꯣꯀꯄꯅꯥ ꯅꯍꯥꯀꯄꯨ ꯁꯣꯀꯍꯅꯕꯥ ꯍꯧꯕꯗꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯆꯪꯏ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯇꯧꯔꯕꯁꯨ, ꯅꯍꯥꯛꯀꯤ ꯑꯍꯦꯅꯕꯥ ꯏ ꯈꯔꯗꯤ ꯂꯧꯊꯣꯛꯇꯨꯅꯥ ꯃꯇꯝ ꯁꯥꯡꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯗꯨ ꯃꯦꯅꯦꯖ ꯇꯧꯕꯥ ꯌꯥꯏ꯫
ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (PV)ꯗꯒꯤ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯆꯥꯎꯕꯥ ꯆꯩꯊꯦꯡ ꯑꯁꯤ ꯀꯦꯟꯁꯔ ꯃꯁꯥꯃꯛ ꯅꯠꯇꯦ, ꯑꯗꯨꯕꯨ ꯏ ꯊꯣꯀꯄꯒꯤ ꯔꯤꯁ꯭ꯛ ꯑꯁꯤꯅꯤ꯫ ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ PVꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯍꯤꯡꯂꯤꯕꯥ ꯑꯣꯏꯔꯕꯗꯤ, ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔ ꯑꯗꯨ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯁꯣꯌꯗꯅꯥ ꯌꯦꯡꯎ꯫ ꯑꯃꯁꯨꯡ "ꯑꯄꯤꯀꯄꯥ ꯄꯣꯠꯁꯀꯁꯤꯡ" - ꯍꯥꯌꯕꯗꯤ ꯍꯀꯆꯥꯡ ꯐꯕꯥ ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡꯒꯤ ꯍꯩꯅꯕꯤꯁꯤꯡꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯏꯁꯥꯕꯨ ꯌꯦꯡꯁꯤꯅꯕꯥ ꯀꯥꯑꯣꯔꯣꯏꯗꯕꯅꯤ꯫ ꯍꯥꯌꯔꯤꯕꯁꯤꯡ ꯑꯁꯤꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯀꯥꯔꯗꯤꯑꯣꯚꯥꯁ꯭ꯀꯨꯂꯥꯔ ꯁꯤꯁ꯭ꯇꯦꯃꯒꯤ ꯖꯦꯅꯦꯔꯦꯜ ꯍꯦꯜꯊ ꯉꯥꯛꯇꯨꯅꯥ ꯊꯝꯕꯗꯥ ꯃꯇꯦꯡ ꯄꯥꯡꯏ, ꯃꯁꯤꯅꯥ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥꯒꯤ ꯃꯦꯗꯤꯀꯦꯜ ꯇ꯭ꯔꯤꯠꯃꯦꯟꯇ ꯑꯃꯠꯇꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯑꯣꯏꯕꯥ ꯌꯥꯏ꯫
ꯋꯥꯔꯤ ꯑꯁꯤꯗꯒꯤ ꯑꯩꯈꯣꯌꯅꯥ ꯌꯨꯃꯗꯥ ꯄꯨꯔꯀꯄꯥ ꯄꯥꯝꯂꯤꯕꯥ ꯄꯥꯎꯖꯦꯜ ꯑꯗꯨ ꯀꯔꯤꯅꯣ?
ꯑꯣꯀꯦ, ꯃꯔꯝ ꯑꯗꯨꯅꯥ ꯑꯩꯈꯣꯌꯅꯥ ꯄꯣꯂꯤꯁꯥꯏꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ (ꯄꯤ.ꯚꯤ.)ꯒꯤ ꯃꯇꯥꯡꯗꯥ ꯌꯥꯝꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯈ꯭ꯔꯦ꯫ ꯅꯤꯡꯁꯤꯡꯒꯗꯕꯥ ꯈ꯭ꯕꯥꯏꯗꯒꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯋꯥꯐꯝ ꯈꯔꯥ ꯃꯈꯥꯗꯥ ꯄꯤꯔꯤ:
- PV ꯍꯥꯌꯕꯁꯤ ꯍꯀꯆꯥꯡꯅꯥ ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯜ ꯌꯥꯝꯅꯥ ꯄꯨꯊꯣꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯃꯍꯧꯁꯥꯗꯒꯤ ꯍꯦꯟꯅꯥ ꯆꯥꯎꯈꯠꯄꯥ ꯕ꯭ꯂꯗ ꯗꯤꯖꯤꯖ ꯑꯃꯅꯤ꯫ ꯃꯁꯤ `ꯃꯥꯏꯂꯣꯞꯔꯣꯂꯤꯐꯦꯔꯦꯇꯤꯚ ꯅꯤꯑꯣꯞꯂꯥꯖꯝ (MPN)` ꯀꯧꯕꯥ ꯀꯦꯟꯁꯔ ꯀꯥꯡꯂꯨꯞ ꯑꯃꯒꯤ ꯃꯅꯨꯡ ꯆꯜꯂꯤ꯫
- ꯃꯔꯨꯑꯣꯏꯕꯥ ꯔꯤꯁ꯭ꯛ ꯑꯁꯤ ꯏ ꯊꯨꯃꯖꯤꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯏ ꯊꯨꯃꯖꯤꯅꯕꯗꯒꯤ ꯂꯥꯀꯏ, ꯃꯗꯨꯅꯥ ꯍꯥꯔꯠ ꯑꯦꯇꯦꯛ ꯑꯃꯁꯨꯡ ꯁ꯭ꯠꯔꯣꯀꯒꯨꯝꯕꯥ ꯁꯥꯊꯤꯕꯥ ꯀꯟꯗꯤꯁꯅꯁꯤꯡ ꯊꯣꯀꯍꯅꯕꯥ ꯌꯥꯏ꯫
- ꯂꯥꯏꯑꯣꯡꯁꯤꯡꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯈꯣꯡ ꯍꯥꯝꯕꯥ (ꯃꯔꯨꯑꯣꯏꯅꯥ ꯂꯨ-ꯅꯥꯅꯕꯥ ꯃꯇꯨꯡꯗꯥ), ꯂꯦꯡ-ꯑꯣꯠꯄꯒꯤ ꯃꯑꯣꯡ-ꯃꯇꯧ, ꯃꯀꯣꯛ ꯁꯣꯀꯄꯥ, ꯑꯃꯁꯨꯡ ꯃꯤꯠ ꯎꯗꯕꯥ ꯑꯁꯤꯅꯆꯤꯡꯕꯥ ꯌꯥꯎꯕꯥ ꯌꯥꯏ꯫
- ꯃꯁꯤ ꯃꯄꯨꯡꯐꯥꯅꯥ ꯐꯍꯅꯕꯥ ꯉꯃꯗ꯭ꯔꯕꯁꯨ, ꯃꯑꯣꯡ ꯆꯨꯝꯅꯥ ꯂꯥꯌꯦꯡꯕꯅꯥ, ꯄꯨꯟꯁꯤ ꯃꯍꯤꯡꯗꯥ ꯑꯍꯣꯡꯕꯥ ꯄꯨꯔꯀꯄꯥ ꯑꯃꯁꯨꯡ ꯍꯤꯗꯥꯛ-ꯂꯥꯡꯊꯛ ꯄꯤꯕꯅꯥ ꯐꯖꯅꯥ ꯃꯦꯅꯦꯖ ꯇꯧꯕꯥ ꯉꯝꯃꯤ꯫ ꯐ꯭ꯂꯦꯕꯣꯇꯣꯃꯤ (ꯕ꯭ꯂꯗꯂꯤꯡ) ꯑꯃꯁꯨꯡ ꯂꯣ-ꯗꯣꯖ ꯑꯦꯁ꯭ꯄꯤꯔꯤꯟ ꯑꯁꯤ ꯃꯔꯨꯑꯣꯏꯕꯥ ꯂꯥꯏꯌꯦꯡꯅꯤ꯫
- `JAK2` ꯖꯤꯟ ꯃ꯭ꯌꯨꯇꯦꯁꯟ ꯑꯁꯤꯅꯥ ꯑꯌꯥꯝꯕꯅꯥ ꯃꯁꯤꯒꯤ ꯃꯔꯝ ꯑꯣꯏ꯫
- ꯀꯔꯤꯒꯨꯝꯕꯥ ꯅꯍꯥꯛꯅꯥ ꯂꯥꯏꯑꯣꯡꯁꯤꯡ ꯑꯁꯤꯒꯤ ꯃꯅꯨꯡꯗꯥ ꯑꯃꯍꯦꯛꯇꯥ ꯂꯩꯔꯕꯗꯤ, ꯄꯥꯎꯇꯥꯛ ꯂꯧꯅꯕꯒꯤꯗꯃꯛ ꯗꯣꯛꯇꯔ ꯑꯃꯗꯥ ꯁꯣꯌꯗꯅꯥ ꯇꯥꯀꯄꯤꯌꯨ꯫ ꯉꯟꯅꯥ ꯈꯪꯗꯣꯀꯄꯅꯥ ꯅꯍꯥꯛꯀꯤ ꯀꯃꯞꯂꯤꯀꯦꯁꯅꯁꯤꯡꯗꯒꯤ ꯂꯥꯞꯅꯥ ꯂꯩꯅꯕꯥ ꯑꯃꯁꯨꯡ ꯍꯀꯁꯦꯜ ꯐꯕꯥ ꯄꯨꯟꯁꯤ ꯑꯃꯥ ꯍꯤꯡꯅꯕꯒꯤ ꯆꯥꯡ ꯍꯦꯅꯒꯠꯍꯜꯂꯤ꯫
ꯂꯥꯡꯇꯛꯅꯒꯅꯨ, ꯑꯗꯨꯕꯨ ꯃꯁꯤꯕꯨꯁꯨ ꯂꯥꯏꯅꯥ ꯂꯧꯔꯣꯏꯗꯕꯅꯤ꯫ ꯅꯍꯥꯛꯀꯤ ꯍꯀꯁꯦꯜ ꯑꯗꯨ ꯌꯦꯡꯁꯤꯅꯕꯤꯌꯨ꯫ ꯅꯍꯥꯛꯀꯤ ꯗꯣꯛꯇꯔꯒꯥ ꯆꯥꯡ ꯅꯥꯏꯅꯥ ꯋꯥꯔꯤ ꯁꯥꯅꯕꯤꯌꯨ, ꯃꯊꯧ ꯇꯥꯕꯥ ꯇꯦꯁ꯭ꯇꯁꯤꯡ ꯑꯃꯁꯨꯡ ꯂꯥꯏꯌꯦꯡꯁꯤꯡ ꯃꯇꯝ ꯆꯥꯅꯥ ꯂꯧꯕꯤꯌꯨ꯫ ꯑꯗꯨꯗꯒꯤ ꯅꯍꯥꯛꯅꯥ ꯀꯟꯗꯤꯁꯟ ꯑꯁꯤꯒꯥ ꯂꯣꯌꯅꯅꯥ ꯐꯥꯑꯣꯕꯥ ꯍꯀꯆꯥꯡ ꯐꯅꯥ ꯂꯩꯕꯥ ꯌꯥꯏ!
` ꯄꯣꯂꯤꯁꯤꯊꯦꯃꯤꯌꯥ ꯚꯦꯔꯥ, ꯔꯦꯗ ꯕ꯭ꯂꯗ ꯁꯦꯂꯁꯤꯡ, ꯕ꯭ꯂꯗ ꯀ꯭ꯂꯣꯠꯁꯤꯡ, ꯑꯦꯝ.ꯄꯤ.ꯑꯦꯟ., ꯖꯦ.ꯑꯦ.ꯀꯦ.꯲, ꯐ꯭ꯂꯦꯕꯣꯇꯣꯃꯤ, ꯀꯦꯟꯁꯔ꯫











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