Kodi muli ndi maselo ofiira ngati minga m'magazi mwanu? Tiyeni tiphunzire za (Acanthocytosis)!

Kodi mudamvapo za maselo ofiira a magazi m'magazi mwanu? Kawirikawiri, amakhala ozungulira, ngati timipira tating'onoting'ono. Koma nthawi zina, maselo ofiira awa amatha kusintha mawonekedwe ndikukhala mawonekedwe achilendo, okhala ndi minga, komanso ngati minga. Ndicho chimene mawu azachipatala a vutoli amatchedwa `(Acanthocytosis)`. Tangoganizani, mawu achigiriki akuti "acan" amatanthauza munga, chinthu chonga munga. "Cyte" amatanthauza selo. Chifukwa chake, "maselo ofanana ndi minga" ndiye tanthauzo losavuta la izi.

Ndipotu, tonsefe tili ndi maselo ochepa a minga (Acanthocytes) m'magazi mwathu. Nthawi zambiri si vuto lalikulu. Koma, ngati muli ndi maselo ambiri a minga m'magazi mwanu, ndi pomwe mavuto ang'onoang'ono amayamba. Kodi mukudziwa zomwe zimachitika? Tili ndi chiwalo chotchedwa ndulu . Chimagwira ntchito ngati fyuluta yomwe imayeretsa magazi athu. Chomwe ndulu imachita ndi kuzindikira maselo akale, owonongeka m'magazi ndikuwawononga. Chifukwa chake, maselo ofiira aminga akadutsa mu ndulu, ndulu imaganiza kuti, "O, awa amawoneka osokonezeka pang'ono, samawoneka ngati maselo abwinobwino." Kenako ndulu imayamba kuwononga maselo aminga awa mwachangu. Izi zikachitika, kuchuluka kwa maselo ofiira athanzi m'thupi lanu kumatha kuchepa. Izi zimatchedwa kuchepa kwa magazi kapena "hemolytic anemia". Izi zikutanthauza kusowa kwa magazi komwe kumachitika chifukwa cha kuwonongeka kwa maselo ofiira amagazi. Sikuti zokhazo, vutoli lotchedwa "Acanthocytosis" lingakhalenso chizindikiro cha matenda ena angapo komanso zovuta zina. Choncho, maselo okhala ndi minga amenewa akapezeka m'magazi, zingathandizenso madokotala kuzindikira matenda ena omwe amayambitsa matendawa.

Ndiye, kodi ndi zizindikiro zotani zomwe tingazipeze chifukwa cha `(Acanthocytosis)` iyi?

Pamene ndulu yanu iwononga maselo ofiira a magazi mwachangu chifukwa cha matenda a sickle cell, vuto lotchedwa ``hemolytic anemia'' limayamba. Mutha kukhala ndi zizindikiro monga:

• Kuoneka kwachikasu pakhungu ndi maso: Timatchanso kuti "jaundice", monga momwe zimachitikira anthu ena akadwala malungo achikasu.
• Kumva kutopa kwambiri: Sikuti kungotopa kokha, komanso kumva kutopa mosasamala kanthu kuti mumagona tulo totani.
• Kuvuta kupuma: Kumva kupuma movutikira ngakhale mutachita khama pang'ono (dyspnea).
• Kugunda kwa mtima mwachangu: Kumva chifuwa chanu chikugunda mofulumira kwambiri ngakhale mutangoyima chilili (tachycardia).
• Magazi mu mkodzo: Nthawi zina mkodzo ukhoza kukhala wofiira kapena wakuda (hematuria).
• Kupweteka m'mimba: Izi nthawi zambiri zimachitika chifukwa cha kutupa kwa ndulu.

Kuwonjezera pa zizindikiro zimenezi, zizindikiro zina zingachitike kutengera matenda omwe amayambitsa maselo a scaly m'thupi lanu. Taganizirani izi kwa anthu ena:

• Kuchepetsa thupi: Ngati ndinu mwana wamng'ono, kukula kungakhale kochedwa.
• Mavuto ogwirizanitsa ntchito ya minofu: Monga kutaya mphamvu (ataxia).
• Kusuntha kosafunikira kwa ziwalo za thupi zomwe munthu sangathe kuzilamulira: mwachitsanzo, kuphethira kapena kutembenuza khosi (kugwedezeka).
• Kuvuta kuganiza ndi kukumbukira: Kumva ngati ubongo wanu ukuchedwa kugwira ntchito (kulephera kuzindikira).
• Mavuto a m'mimba.
• Chimbudzi chotuwa: Izi zitha kuchitika mafuta akasagayidwa bwino (steatorrhea).
• Mkodzo wakuda.

Ngati muli ndi chimodzi mwa zizindikiro izi kapena zingapo, ndi bwino kupita kwa dokotala mwamsanga.

N’chifukwa chiyani mitundu iyi ya maselo okhala ndi minga imapanga m’magazi mwathu? Kodi zifukwa zake ndi ziti?

Mwachidule, chifukwa chachikulu cha `(Acanthocytosis)` ndi momwe maselo ofiira akunja amakhudzira maselo ofiira, kutanthauza `(selo membrane).` Maselo amenewa amapangidwa ndi mafuta `(lipids)` ndi mapuloteni . Chifukwa chake, ngati pali matenda kapena vuto lomwe limakhudza zigawo zofunika izi, mawonekedwe ozungulira a maselo ofiira amasintha ndipo amayamba kukhala ngati minga.

Maselo oyambira osinthidwawa, monga tafotokozera kale, samasefedwa mosavuta akamadutsa mu ndulu. Chifukwa chake, ndulu imawawononga. Nthawi zina, m'malo mowononga maselo awa, ndulu imafinya minyewa yawo ndikuibweza m'magazi. Maselo oyambira osinthidwawa nthawi zina amatchedwa `(maselo oyambitsa)`.

Nazi zina mwa zifukwa zazikulu zomwe zimayambitsa acanthocytosis:

• Matenda oopsa a chiwindi: Maselo a Spur nthawi zambiri amakhala chizindikiro cha matenda aakulu a chiwindi, nthawi zina omwe amaika moyo pachiswe. Anthu ena omwe ali ndi matenda a chiwindi amadwala matenda otchedwa spur cell anemia (SPA). Izi zikutanthauza kuti ali ndi maselo a spur m'magazi mwawo, komanso ali ndi maselo ofiira ochepa.
• Abetalipoproteinemia: Iyi ndi matenda osowa kwambiri, omwe amapezeka m'majini. Ndiko kuti, amatengera kwa makolo kupita kwa ana. Matendawa amachititsa kuti thupi lisathe kuyamwa bwino mafuta ndi mavitamini osungunuka m'mafuta (mavitamini A, D, E, K).
• Neuroacanthocytosis: Ichi ndi matenda osowa kwambiri a majini. Izi zimayambitsa kulephera kulamulira mayendedwe a thupi. Zitsanzo zake ndi chorea-acanthocytosis, McLeod syndrome, pantothenate-kinase associated neurodegeneration (PKAN), ndi matenda a Huntington omwe ali ngati 2.

Kuwonjezera pa zifukwa zazikulu izi, matenda ena angayambitsenso "Acanthocytosis":

• Anorexia nervosa ndi vuto lomwe limayamba chifukwa cha kusowa chilakolako cha chakudya.
• Kuchepa kwa ntchito ya chithokomiro (Hypothyroidism).
• Matenda a Myelodysplastic ndi matenda a mafupa.
• Matenda a impso.
• Kuchotsa ndulu kwa opaleshoni (splenectomy).
• Mankhwala ena (monga mankhwala ochepetsa cholesterol monga "statins").

Kodi madokotala amazindikira bwanji acanthocytosis?

Dokotala wanu akhoza kuzindikira acanthocytosis mwa kuchita peripheral blood smear (PBS) . Izi zimaphatikizapo kutenga chitsanzo chaching'ono cha magazi anu ndikuyang'ana pansi pa maikulosikopu. Izi ziwonetsa bwino kupezeka kwa maselo osazolowereka komanso okhala ndi minga.

Kenako, kuti mudziwe chomwe chimayambitsa matenda a sebaceous cysts, muyenera kuyezetsa magazi ena. Izi ndi izi:

• Kuchuluka kwa magazi (CBC)
• Mayeso a ntchito ya chiwindi
• Mayeso a ntchito ya impso
• Mayeso a mahomoni a chithokomiro
• Kuyesa kuchuluka kwa mafuta m'magazi `(Lipid panel)`
• Mayeso a majini: Yang'anani kusintha kwa majini komwe kumachitika chifukwa cha matenda enaake obadwa nawo.

Kuphatikiza apo, dokotala wanu angakulangizeninso mayeso monga kujambula zithunzi kuti awone ngati pali kuwonongeka kulikonse kwa minofu kapena ziwalo mkati mwa thupi lanu.

Kodi mankhwala ochizira izi ndi otani?

Chithandizo cha acanthocytosis chimadalira chomwe chimayambitsa. Nthawi zambiri, vuto lomwe limayambitsa matendawa likachiritsidwa bwino, maselo ofiira a magazi amabwerera m'malo abwinobwino.

Taganizirani izi, mankhwala a matenda a chiwindi ndi matenda monga ``Neuroacanthocytosis`` cholinga chake chachikulu ndi kuchepetsa zizindikiro. Matendawa nthawi zambiri amakhala ovuta kuwachiritsa kwathunthu. Amakula kwambiri pakapita nthawi. Komabe, pa matenda oopsa a chiwindi, pali nthawi zina pomwe kuyika chiwindi ndiye mankhwala okhawo.

Ngati muli ndi vuto la majini lotchedwa abetalipoproteinemia, mungafunike kuchepetsa kudya mafuta osapatsa thanzi ndikupeza ma calorie okwanira. Mungafunikenso kumwa mavitamini owonjezera kuti muwonetsetse kuti mumapeza mavitamini okwanira (A, D, E, K) kuti mupange maselo ofiira athanzi.

Ngati acanthocytosis imayamba chifukwa cha anorexia kapena hypothyroidism, vutoli nthawi zambiri limakhala bwino akalandira chithandizo cha vutoli. Komanso, ngati zapezeka kuti mankhwala enaake ndi omwe amayambitsa acanthocytosis, vutoli nthawi zambiri limatha mankhwalawo akangoyimitsidwa.

Ngati ndili ndi vutoli, ndiyenera kuyembekezera chiyani?

Nthawi zina, vuto lotchedwa acanthocytosis limatha kuchiritsidwa kwathunthu ndi chithandizo. Izi zikutanthauza kuti maselo ofiira a magazi amabwerera mwakale.

Komabe, nthawi zambiri, zotsatira za thanzi lanu zimadalira zomwe zinayambitsa kukula kwa ma sebaceous glands awa komanso momwe mumayambira chithandizo mwachangu.

Mwachitsanzo, matenda monga `(Neuroacanthocytosis)` ndi `(Abetalipoproteinemia)` angayambitse kuwonongeka kwa minofu ya thupi kwa nthawi yayitali. Komabe, ngati matendawa apezeka ndi kuchiritsidwa msanga,, zimatha kuchepetsa kukula kwa zizindikiro.

Kawirikawiri, ngati muli ndi `(Acanthocytosis)` yokhala ndi matenda a chiwindi, zingakhale zovuta pang'ono. Anthu ambiri omwe ali ndi `(spur cell anemia)` omwe atchulidwa pamwambapa amafa mkati mwa miyezi ingapo. Chifukwa chake, njira yabwino yodziwira za vuto lanu ndi kuchokera kwa dokotala amene amakuchizani. Iye adzayang'ana thanzi lanu lonse komanso chomwe chimayambitsa maselo amenewa, ndikukufotokozerani zomwe zikukuchitikirani.

Kodi pali njira yopewera `(Acanthocytosis)` iyi kuti isachitike?

Ndipotu, ngati acanthocytosis imayamba chifukwa cha matenda a majini, palibe njira yopewera. Chifukwa ndi chinthu chomwe timatengera. Komabe, pali zinthu zomwe tingachite kuti tichepetse chiopsezo chotenga matendawa chifukwa cha zifukwa zina.

• Pewani kapena chepetsani kumwa mowa: Izi zingathandize kupewa matenda a chiwindi omwe amabwera chifukwa cha mowa.
• Idyani zakudya zopatsa thanzi: Thupi lanu limafunika kupeza zakudya zoyenera kuti lipange maselo ofiira a magazi. Ngati mukufuna thandizo posankha zakudya zoyenera kwa inu, funsani katswiri wa zakudya.
• Pezani chithandizo msanga: Matenda ena omwe amayambitsa matenda a sebaceous cysts amatha kukhala oopsa kwambiri ngati sanalandire chithandizo. Chifukwa chake, ndikofunikira kwambiri kuonana ndi dokotala zizindikiro zikayamba kuwonekera, kuzindikira vutoli, ndikuyamba kulandira chithandizo.

Kodi ndingasamalire bwanji thanzi langa?

Chofunika kwambiri ndikutsatira chithandizo chomwe dokotala wanu wakupatsani chifukwa cha vuto lomwe limayambitsa acanthocytosis yanu.

Ngati muli ndi vuto la majini lotchedwa acanthocytosis, ganizirani zopeza uphungu wa majini . Mlangizi wa majini angakulangizeni momwe vutoli lingakhudzireni inu ndi banja lanu, komanso mwayi woti mupatsire ana anu kusintha kwa majini komwe kumayambitsa vutoli.

Ndi mafunso ati omwe ndiyenera kufunsa dokotala wanga?

Mukapita kwa dokotala, musazengereze kufunsa mafunso ngati awa:

• Kodi ndiyenera kuda nkhawa ndi kukhala ndi maselo aminga (Acanthocytes) m'magazi mwanga?
• Ndi mayeso ena ati omwe ndiyenera kuchita kuti ndipeze chomwe chayambitsa izi?
• Kodi mukundilangiza chithandizo chamtundu wanji?
• Kodi ndi zotsatira zotani zomwe ndingayembekezere kuchokera ku mankhwala awa?
• Kodi ndiyenera kupita kwa katswiri wa majini?

Pomaliza, ndiyenera kunena... (Uthenga Wopita Nawo Kunyumba)

Madokotala akamakupezani matenda, amawonanso mawonekedwe a maselo ofiira a magazi anu. Ngati mwapezeka ndi `(Acanthocytosis)` zikutanthauza kuti muli ndi maselo ofiira osazolowereka m'magazi mwanu. Musadandaule. Nthawi zina, chithandizo chingabwezeretse maselo ofiira a magazi anu kukhala abwinobwino. Kapena, chingathandize kuwongolera matenda oyamba. Komabe, nthawi zina, kukhala ndi ma acanthocyte m'magazi mwanu kungakhale chizindikiro cha matenda aakulu, monga matenda oopsa a chiwindi. Chifukwa chake, dokotala wanu ndiye munthu wabwino kwambiri wofotokoza momwe kukhala ndi `(Acanthocytosis)` kumakhudzira thanzi lanu. Ngati mumvera zomwe akunena ndikutsatira chithandizocho molondola, vutoli nthawi zambiri limatha kulamulidwa.

Acanthocytosis , Maselo ofiira a magazi, Scutellaria, Spleen, Anemia, Matenda a chiwindi