Lero tikambirana za mtundu wa khansa wovuta komanso wosowa kwambiri. Umatchedwa Desmoplastic Small Round Cell Tumor, kapena DSRCT monga momwe madokotala amatchulira. Mwina simunamvepo dzinali kale, chifukwa ndi matenda omwe amakhudza anthu ochepa kwambiri. Koma kudziwa za matenda otere kungakhale kofunikira kwambiri kwa ife ndi okondedwa athu.
Ndiye kodi DSRCT iyi ndi chiyani?
Mwachidule, DSRCT ndi matenda omwe amayambitsa zotupa za khansa zomwe zimakula mofulumira kwambiri . Izi zili m'gulu la soft tissue sarcoma . Izi zikutanthauza kuti zotupazi zimatha kuchitika m'malo ofewa a thupi lathu omwe alibe mafupa, monga minofu, mafuta, ndi mitsempha. Komabe, mu DSRCT, zotupazi zimakula makamaka mu nembanemba yomwe imaphimba m'mimba mwathu (peritoneum) . Taganizirani izi, iyi ndi nembanemba yopyapyala yomwe imateteza ziwalo monga chiwindi ndi matumbo mkati mwa mimba yathu. Chifukwa chake apa ndi pomwe maselo a khansa amagawikana mwachangu ndikuyamba kupanga zotupa.
Ngakhale kuti matendawa amatha kufalikira mwa aliyense, nthawi zambiri amapezeka mwa anyamata azaka zapakati pa 20 ndi 30. Kodi sizodabwitsa? Pali mankhwala ochizira izi, ndipo nthawi zina zizindikiro zimatha ndipo matendawa amapezeka m'mayeso, kutanthauza kuti, akachira . Komabe, chomvetsa chisoni n'chakuti matenda omwe achepetsedwa motere amatha kubwereranso, kutanthauza kuti, kubwereranso .
Kodi matenda amenewa otchedwa DSRCT ndi osowa bwanji?
Ndi zachilendo kwambiri moti simungathe kuziganizira. Kuyambira pamene ofufuza adapeza matendawa koyamba mu 1989, anthu pafupifupi 1 biliyoni padziko lonse lapansi apezeka ndi matendawa. Izi zikutanthauza kuti, poyerekeza ndi anthu aku Sri Lanka, n'zovuta kupeza munthu ngakhale kamodzi pa zaka zingapo. Ndi zachilendo choncho.
Kodi zizindikiro za DSRCT ndi ziti?
Nthawi zambiri, zotupa zomwe zimamera m'mimba sizimayambitsa zizindikiro zazikulu mpaka zitakula kwambiri, kutenga malo m'mimba, ndikukhudza dongosolo la m'mimba. Komabe, pali zizindikiro zingapo zodziwika bwino zomwe zingawonekere:
- Kupweteka m'mimba: Kupweteka kwa m'mimba kosalekeza, nthawi zina kumakulirakulira.
- Kudzimbidwa: Kuvutika kuchita matumbo pafupipafupi.
- Kutsegula m'mimba: Kusanza.
- Mimba yotupa: Mimba imaoneka yotupa komanso yotupa.
- Kusanza ndi kusanza: Kusowa chilakolako chofuna kudya komwe kumayenderana ndi nseru ndi kusanza.
- Kuchepetsa thupi mosadziwika: Kuchepetsa thupi mwadzidzidzi popanda malamulo enaake okhudza zakudya.
Tsopano taonani, zinthu monga kudzimbidwa, kutsegula m'mimba, ndi nseru zimathanso kuwoneka m'matenda ang'onoang'ono omwe nthawi zambiri timakumana nawo, sichoncho? Chifukwa chake si bwino kuopa matenda aakulu chifukwa chakuti muli ndi zizindikirozi.Komabe, ngati zizindikirozi zikupitirira kwa masiku angapo kapena zikuipiraipira, ndi bwino kukaonana ndi dokotala.
Nchifukwa chiyani DSRCT iyi imachitika? Chifukwa chake n'chiyani?
Ofufuza apeza kuti DSRCT imayamba chifukwa cha kusintha kwa ma chromosome m'maselo athu. Kusintha kumeneku kumapanga jini yosadziwika bwino yotchedwa EWS-WT1 . Jini iyi imayambitsa kukula kwa maselo a khansa. Komabe, sizikudziwikabe chifukwa chake ma chromosome awa amasintha motere. Imeneyi ndi mbali yovuta kwambiri ya matenda awa.
Kodi madokotala amazindikira bwanji vuto la DSRCT?
Kuti adziwe izi, madokotala amaphatikiza mayeso angapo kuti atsimikizire izi:
- Kuwunika thupi: Choyamba, dokotala adzakhudza mimba yanu kuti aone ngati mungamve chilichonse, monga ziphuphu.
- Mayeso ojambulira: Izi zikuphatikizapo ma CT scan , ma MRI scan , ndi ma ultrasound test . Izi zingathandize kudziwa ngati pali zotupa mu peritoneum, kukula kwake, komanso ngati zafalikira kumadera ena.
- Mayeso a majini: Mayesowa amathandiza kutsimikizira ngati kusintha kwa majini kwa EWS-WT1 komwe kwatchulidwa kale kulipo. Ichi ndi chomwe chingathe kudziwa molondola ngati ndi DSRCT.
Kodi mankhwala a DSRCT ndi ati?
Madokotala amagwiritsa ntchito njira zingapo pochiza DSRCT. Njira zazikulu ndi izi:
- Opaleshoni: Kuchotsa khansa yochuluka momwe zingathere chifukwa cha opaleshoni.
- HIPEC (Hyperthermic Intraperitoneal Chemotherapy): Iyi ndi njira yapadera pang'ono. Pambuyo poti chotupacho chachotsedwa opaleshoni, mankhwala otentha a chemotherapy amabayidwa m'mimba kuti awononge maselo otsala a khansa.
- Chemotherapy: Mankhwala amphamvu omwe amaperekedwa m'thupi kuti awononge maselo a khansa.
- Chithandizo cha radiation: Kugwiritsa ntchito mphamvu zambiri powononga maselo a khansa.
Mankhwalawa amatha kupangitsa kuti matendawa achepe , zomwe zikutanthauza kuti palibe zizindikiro ndipo palibe mayeso omwe angazindikire matendawa. Komabe, kuchepeka kumeneku nthawi zambiri sikutenga nthawi yayitali. Matendawa amatha kubwereranso , kotero mankhwala atsopano kapena njira zina zochiritsira zingafunike kuyambika.
Chofunika: Kaya mulandire chithandizo chotani, chithandizo chochepetsa ululu kuchokera kwa gulu lanu lachipatalaOnetsetsani kuti mwafunsa za izi. Izi zimachitika kuti muchepetse ululu wakuthupi ndi kupsinjika maganizo komwe kumachitika chifukwa cha matendawa ndikukupatsani chithandizo chamankhwala, chikhalidwe, komanso chamaganizo chomwe mukufunikira kuti mukhale ndi matendawa momwe mungathere. Ichi si chithandizo chomwe chimachiritsa khansa, koma chingathandize kwambiri moyo wanu kukhala wabwino.
Kodi pali zotsatirapo zilizonse za mankhwalawa?
Inde, opaleshoni, mankhwala a chemotherapy, ndi mankhwala a radiation zonse zingayambitse zotsatira zoyipa. Pambuyo pa opaleshoni yochotsa zotupa za DSRCT, mutha kukhala ndi zotsatira zoyipa monga momwe mumachitira ndi mankhwala oletsa ululu kapena kutuluka magazi. Zotsatira zoyipa za mankhwala a radiation ndi chemotherapy ndi izi:
- Kutsegula m'mimba
- Kutopa
- Kusanza ndi kusanza
Zotsatirapo izi sizimachitika mofanana kwa aliyense, anthu ena angakumane ndi zochepa, ena angakumane ndi zambiri. Dokotala wanu adzakuuzani za izi.
Kodi matenda a DSRCT a wodwalayo ndi otani?
Ichi ndi chinthu chovuta kwambiri kukambirana, ndipo aliyense amafuna kudziwa. Madokotala amanena kuti munthu angayembekezere pambuyo pa chithandizo. Amasankha izi potengera zinthu monga komwe khansa ili, ngati yafalikira, komanso kuchuluka kwa khansa yomwe yachotsedwa panthawi ya opaleshoni.
Popeza DSRCT ndi khansa yosowa kwambiri, palibe kafukufuku wochuluka pa nkhaniyi. Choncho n'zovuta kuti madokotala anene zomwe mungayembekezere kapena nthawi yomwe mungakhale ndi moyo. Izi n'zomvetsa chisoni kwambiri.
Deta yomwe ilipo pano ikusonyeza kuti kuchuluka kwa zaka zisanu zomwe munthu amapulumuka DSRCT akapezeka ndi matendawa kuli pakati pa 15% ndi 38% . Izi zikutanthauza kuti si aliyense amene adzachira. Komabe, kafukufuku wina wasonyeza kuti odwala ochepa omwe ali ndi DSRCT yofalikira amachiritsidwa kwathunthu ndi chithandizo. Komanso, pafupifupi 60% ya omwe amachiritsidwa khansa isanafalikire amakhala amoyo patatha zaka zisanu. Chifukwa chake, mutha kuwona kufunika kozindikira msanga ndikuyamba chithandizo mwachangu, eti?
Kodi ndimadzisamalira bwanji ndi vutoli?
DSRCT ndi khansa yowopsa komanso yosowa. Imatha kubweranso miyezi kapena zaka mutalandira chithandizo. Kukhala ndi mantha kuti khansa ibwereranso sikophweka. Komabe, pali zinthu zingapo zomwe zingakuthandizeni paulendo uwu:
- Mvetsetsani vuto lanu: Popeza DSRCT ndi yosowa, zimakhala zovuta kupeza mfundo zolondola komanso zatsopano zokhudza vutoli. Choncho, musazengereze kufunsa gulu lanu lachipatala zomwe mungayembekezere. Amakudziwani bwino inu ndi vuto lanu.
- Funsani za kutenga nawo mbali mu mayeso azachipatala:Ofufuza akuyesa njira zatsopano zochizira DSRCT. Funsani dokotala wanu ngati mungathe kutenga nawo mbali mu mayeso azachipatala .
- Ganizirani za kupulumuka khansa: Kuyambira tsiku lomwe mudapezeka ndi khansa, mwakhala mukulimbana ndi khansa komanso moyo wanu wonse. Funsani gulu lanu lachipatala za mapulogalamu apadera a anthu omwe ali ndi khansa yobwerezabwereza.
- Pezani chithandizo: Funsani gulu lanu lachipatala za magulu othandizira anthu omwe ali ndi khansa yosowa. Kukhala ndi nthawi yocheza ndi anthu omwe akukumana ndi zokumana nazo zomwezo monga inu, kapena omwe ali ndi zokumana nazo zofanana, kungathandize kuchepetsa kusungulumwa komwe kumakhala ndi DSRCT.
Ndiyenera kukaonananso ndi dokotala wanga liti?
DSRCT ndi vuto lomwe nthawi zambiri limatha kubwereranso. Chifukwa chake, dokotala wanu angakulangizeni kuti muyesedwe zithunzi (monga CT scan) miyezi itatu kapena isanu ndi umodzi iliyonse kuti muwone ngati pali zotupa zatsopano m'mimba kapena kwina kulikonse. Ndikofunikira kwambiri kuti musaphonye mayeso otsatirawa .
Ndi mafunso ati omwe ndiyenera kufunsa dokotala wanga?
Pa nthawi ngati iyi, mungakhale ndi mafunso ambiri. N'zovuta kumvetsa chilichonse nthawi imodzi. Musachite mantha, phunzirani zonsezi pang'onopang'ono. Nazi mafunso ena omwe mungafunse poyamba:
- Kodi ndingadziwe bwanji kuti zizindikiro zanga zimayambitsidwa ndi vuto lotchedwa DSRCT?
- Kodi izi zingathe kuchiritsidwa kwathunthu ndi chithandizo?
- Kodi mumalimbikitsa chithandizo chanji?
- Kodi zotsatirapo zake ndi ziti?
- Kodi ndiyenera kuganizira zolowa nawo mu mayeso azachipatala?
Ngati mwapezeka ndi matenda a DSRCT, zingakhale zinthu zomwe zingasinthe moyo wanu. Mungamve ngati muli ndi nkhawa kwambiri. Mungakhale ndi nkhawa ndi zomwe zichitike pambuyo pake, momwe chithandizocho chidzakhalire, komanso momwe tsogolo lanu lidzakhalire. Zingakhalenso zokhumudwitsa kupeza chidziwitso chokhudza matenda omwe amakhudza anthu ochepa chabe padziko lonse lapansi.
Gulu lanu lachipatala limamvetsetsa malingaliro onsewa. Adzakupatsani nthawi yokwanira kuti mumvetse zomwe zikukuchitikirani komanso zomwe zingachitike pambuyo pake. Musaope kulankhula nawo ndikufunsa mafunso aliwonse omwe muli nawo.
Uthenga Womaliza Wopita Nawo Kunyumba
Ndi zachilendo kumva kutopa kwambiri mukadziwa za vutoli lotchedwa DSRCT. Komabe, kumbukirani mfundo izi:
- DSRCT ndi khansa yosowa kwambiri komanso yoopsa. Ndikofunikira kuzindikira zimenezo kaye.
- Dziwani zizindikiro. Ngati mukumva kupweteka m'mimba kosalekeza, kudzimbidwa, kapena kuchepa thupi, funsani upangiri kwa dokotala.
- Kuzindikira msanga ndi kulandira chithandizo mwachangu n'kofunika kwambiri. Izi zitha kusintha momwe matendawa akuyendera pang'onopang'ono.
- Simuli nokha.Gulu lachipatala, mabanja, ndi magulu othandizira alipo kuti akuthandizeni.
- Ganizirani chisamaliro chochepetsa ululu. Izi zingakuthandizeni kwambiri kukhala ndi moyo wabwino.
- Musaope kufunsa mafunso. Onetsetsani kuti mwamva zonse momveka bwino kuchokera kwa dokotala wanu.
Tikukhulupirira kuti izi zakuthandizani kumvetsetsa za vutoli losowa. Kumbukirani, kuzindikira ndi mphamvu yayikulu yothanirana ndi vuto lililonse.
DSRCT , Chotupa cha Desmoplastic Small Round Cell, Khansa, Khansa ya m'mimba, Khansa yosowa, Zizindikiro za Khansa, Chithandizo cha Khansa, Khansa ya Peritoneum

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