Chizindikiro chachilendo pamene mbali imodzi ya thupi ndi yofiira ndipo mbali inayo ndi yotumbululuka (Chizindikiro cha Harlequin)

Tangoganizirani kuyang'ana pagalasi ndikuona mzere wowongoka pakati pa nkhope yanu, mbali imodzi yofiira kwambiri komanso yotuluka thukuta, ndipo mbali inayo yakhala yachibadwa, mwina yotumbululuka pang'ono... Kodi sizowopsa komanso zodabwitsa? Kapena bwanji ngati mutaona mbali imodzi ya thupi la mwana wanu wakhanda ikufiira mwadzidzidzi ndipo mbali inayo yakhala yachibadwa? Ichi ndi chomwe timachitcha Harlequin Sign in medicine. Popeza dzinali ndi lachilendo pang'ono, tiyeni tidziwe zambiri za izi komanso ngati izi ndi chinthu choopadi.

Kodi chizindikiro cha Harlequin ichi n'chiyani kwenikweni?

Mwachidule, Chizindikiro cha Harlequin ndi pamene mbali imodzi ya thupi lanu kapena nkhope yanu imakumana ndi kusintha kwa mtundu wa khungu (kufiira kapena mdima), pomwe mbali inayo imakhalabe yofanana, nthawi zina ngakhale yotumbululuka. Mbali ziwirizi zimaoneka kuti zalekanitsidwa ndi mzere wowongoka, pakati pa thupi.

Pamodzi ndi kusiyana kwa mtundu wa khungu, zinthu zina zitha kuwoneka mbali zonse ziwiri.

• Kufiira: Malo awa akhoza kukhala ndi hyperhidrosis (kutuluka thukuta kwambiri). Khungu lomwe lili pamalopo likhozanso kumveka lotentha pang'ono likakhudza.
• Mbali Yotumbululuka/Yabwinobwino: Mbali iyi siituluka thukuta. Khungu limamvanso kuzizira likakhudza.

Ngakhale kuti Chizindikiro cha Harlequin ichi nthawi zina chingakhale chizindikiro cha matenda monga `Harlequin syndrome`, nthawi zambiri chimakhala chosaopsa ndipo chimatha.

Kodi zifukwa zazikulu za izi ndi ziti?

Sizotheka nthawi zonse kupeza chifukwa chenicheni cha izi. Chifukwa chachikulu cha izi ndi vuto la kulankhulana mu dongosolo la mitsempha la thupi lathu. Ganizirani izi ngati dongosolo la "auto-pilot" la thupi lathu. Dongosololi limalamulira zinthu zomwe sitikudziwa kuti tili nazo, monga kupuma kwathu, kugunda kwa mtima, ndi thukuta.

Choncho, ngati pali vuto kapena vuto mu njira ya mitsempha yomwe imatumiza mauthenga ochokera ku ubongo (hypothalamus) kudzera mu msana kupita kunkhope ndi kumtunda kwa thupi, uthengawo sungatumizidwe bwino mbali imodzi yokha ya thupi. Ichi ndichifukwa chake mitsempha yamagazi kumbali imodzi imatambasuka ndi kufiira, pomwe mbali inayo silandira uthengawo ndipo imakhalabe yachibadwa.

Kodi izi zimachitikanso kwa makanda obadwa kumene?

Inde, izi ndi zomwe zimaoneka mwa makanda obadwa kumene. Malinga ndi kafukufuku, pafupifupi 10% ya makanda athanzi amatha kukhala ndi Harlequin Sign iyi. Chifukwa chake, musadandaule ngati mwana wanu ali ndi izi.

Izi nthawi zambiri zimachitika pakati pa masiku awiri ndi asanu mwana atabadwa, koma nthawi zina zimatha kuonekera mochedwa ngati milungu itatu.

Chofunika Kwambiri: Matendawa otchedwa Harlequin Sign sayenera kusokonezedwa ndi `Harlequin ichthyosis`, matenda oopsa kwambiri, oopsa komanso osowa kwambiri m'majini. `Harlequin ichthyosis` ndi matenda omwe thupi lonse la mwana limakhala ndi mamba okhuthala ngati mbale, ndi ming'alu yakuya pakati. Ndi chinthu chosiyana kwambiri.

Matenda ena okhudzana nawo

Chizindikiro cha Harlequin nthawi zina chingawoneke ngati chizindikiro cha matenda ena.

Matenda a Harlequin

Uwu ndi vuto lomwe limakhudza dongosolo lathu la mitsempha la sympathetic. Dongosolo la mitsempha ili limalamulira momwe timayankhira "nkhondo kapena kuthawa", zomwe ndi kusintha komwe kumachitika m'thupi tikamasangalala, kuchita mantha, kapena kuchita masewera olimbitsa thupi. Nthawi iliyonse dongosololi likayamba kugwira ntchito mwa munthu yemwe ali ndi Harlequin Syndrome (mwachitsanzo, panthawi yochita masewera olimbitsa thupi), mbali imodzi ya nkhope ndi thupi idzakhala yofiira komanso yotuluka thukuta, pomwe mbali inayo sidzatero.

Matenda a Horner

Imeneyi ndi vuto la mitsempha losowa kwambiri. Limakhudza maso ndi minofu yozungulira mbali imodzi ya nkhope. Limatchedwanso `oculosympathetic palsy`. Limayambitsidwa ndi kutsekeka kwa njira ya mitsempha kuchokera ku ubongo kupita ku diso ndi nkhope. Apanso, mbali ya nkhope yomwe yakhudzidwayo ikhoza kukhala yofiira.

Kodi imachiritsidwa bwanji?

Chithandizo chimadalira chifukwa cha Harlequin Sign.

• Kwa makanda obadwa kumene: Palibe chithandizo chofunikira. Chidzatha chokha pakangopita masekondi kapena mphindi zochepa.
• Pa Harlequin Syndrome: Chithandizo sichikhala chofunikira nthawi zonse. Nthawi zina vutoli limatha kuchira lokha. Komabe, ngati dokotala wanu akuganiza kuti chithandizo ndi chofunikira, adzakupatsani chithandizo kutengera chomwe chimayambitsa vutoli. Izi zikuphatikizapo:
• Katemera wotchedwa `Stellate ganglion block` amagwiritsidwa ntchito poletsa kusintha kwa mtundu wa khungu.
• Jakisoni wa poizoni wa botulinum kuti achepetse thukuta.
• Ngati pali chotupa chomwe chili mkati mwake, chingachotsedwe mwa opaleshoni kapena kudzera mu radiation therapy.
• Uphungu wa nkhawa yamaganizo yomwe imabwera chifukwa cha mawonekedwe awa.
• Pa Horner Syndrome: Ngati palibe ululu, chithandizo sichingakhale chofunikira. Pankhaniyi, dokotala adzachiza chomwe chimayambitsa vutoli.

Kodi muyenera kupita kwa dokotala liti?

Ngati inu kapena wina m'banja mwanu awona Chizindikiro cha Harlequin, chomwe chili chofiira, chotuluka thukuta, komanso chotentha mbali imodzi ya thupi, chinthu chabwino kwambiri choti muchite ndikuwonana ndi dokotala ndikuyesedwa.

Dokotala wanu adzakuyang'anirani, adzakufunsani za zizindikiro zanu, ndipo ngati kuli kofunikira, adzakuyesani kuti apeze matenda ena. Ngakhale kuti ndi osowa kwambiri, ndikofunikira kudziwa ngati pali chotupa kapena matenda ena, chifukwa ichi chingakhale chifukwa chake.