Kodi MRKH syndrome (Mayer-Rokitansky-Küster-Hauser Syndrome) ndi chiyani? Kodi tikambirane za izi?

Kodi mwana wanu wamkazi, kapena mwana wamng'ono amene mumamudziwa, sanayambe kusamba pa msinkhu woyenera? Kapena, kodi nthawi zina amamva kupweteka kapena kusasangalala akamayesa kugonana? Lero tikambirana za matenda apadera omwe angayambitse zinthuzi, koma si ofala kwambiri ndipo anthu ambiri sanamvepo za matendawa. Izi zimatchedwa Meyer-Rokitansky-Küster-Hauser syndrome , kapena ``MRKH syndrome'' mwachidule. Ngakhale dzinali lingawoneke lalitali pang'ono, ili ndi matenda osowa kwambiri omwe amakhudza akazi. Tiyeni tikambirane mwachidule, m'njira yomwe mungamvetse.

Kodi matenda a MRKH ndi chiyani kwenikweni?

Mwachidule, matenda a MRKH ndi matenda omwe mkazi amakumana nawo pamene nyini ndi chiberekero sizikukula bwino kapena sizimapangidwa mokwanira akangobadwa. Taganizirani ngati nyumba yomwe ikumangidwa ndi zipinda zina zomwe sizinapangidwe bwino. Komabe, nthawi zambiri, mazira ndi machubu a fallopian a anthu omwe ali ndi vutoli amagwira ntchito bwino . Komanso, ziwalo zoberekera zakunja, zomwe ndi gawo la pansi pa nyini, khomo la nyini, labia, clitoris, ndi kukula kwa tsitsi mozungulira, ndi zachilendo. Mtsempha wa mkodzo sukhudzidwa, kotero palibe vuto kukodza.

Komabe, mu mitundu ina ya matenda a MRKH, pakhoza kukhala mavuto ena okhudzana ndi kukula kwa ziwalo zina, monga impso ndi msana.

Kawirikawiri, vutoli limapezeka ali aang'ono, kutanthauza kuti, akafika zaka 15-16, pamene msambo suyamba. Izi zili choncho chifukwa chiberekero sichinakule bwino, kotero msambo suchitika. Nthawi zina, poyesa kugonana, nyini imatha kumva kupweteka kapena kuvutika chifukwa ndi yayifupi komanso yopapatiza.

Popeza chiberekero sichinakule mokwanira kapena sichinakule mokwanira, sizingatheke kutenga pakati ndi kubereka mwana popanda thandizo lachipatala panthawiyi. Komabe, ngati mazira akugwira ntchito ndipo mazira akupangidwa , njira monga ``IVF - in vitro fertilization`` ndi `` surrogacy`` zitha kuganiziridwa. Ngati mukuyembekeza kukhala ndi ana, ndikofunikira kwambiri kulankhula ndi dokotala wanu za izi. Kenako angakulangizeni njira zomwe zili zoyenera kwa inu.

Mayina ena angapo amagwiritsidwa ntchito pa `(MRKH syndrome)`:

• Kusakhalapo kwa chiberekero ndi nyini (CAUV)
• Kubereka kwa nyini
• Kubadwa kwa Müllerian
• Müllerian aplasia (MA)
• Matenda a khutu la genital renal (GRES)

Kodi pali mitundu ya matenda a MRKH?

Inde, pali mitundu iwiri ikuluikulu ya `(MRKH syndrome)`:

• Mtundu 1:Mu mtundu uwu, mazira ndi machubu a fallopian amagwira ntchito bwino, koma gawo lapamwamba la nyini, khomo lachiberekero, ndi chiberekero zimakhala zotsekeka kapena sizili pamalo ake. Komabe, izi sizikhudza ziwalo zina zilizonse m'thupi.

• Mtundu wachiwiri: Mu mtundu uwu, kuwonjezera pa kutsekeka kapena kusakhalapo kwa gawo la pamwamba la nyini, khomo lachiberekero, ndi chiberekero, pakhoza kukhalanso mavuto ena ndi machubu a fallopian, mazira, msana, impso, kapena ziwalo zina.

Kodi vutoli ndi lofala bwanji?

Matenda a MRKH ndi matenda osowa kwambiri . Amakhudza pafupifupi mtsikana m'modzi mwa atsikana 4,500 aliwonse. Choncho sizodabwitsa kuti sitinamve zambiri za matendawa.

Kodi zizindikiro za MRKH ndi ziti?

Zizindikiro za matenda a MRKH zimatha kusiyana malinga ndi mtundu wa matenda omwe muli nawo.

Nthawi zambiri, chizindikiro chachikulu ndi kusasamba (amenorrhea) akafika zaka 16. Ichi ndi chizindikiro chakuti chiberekero kapena nyini sizinakule bwino. Komabe, chifukwa mazira akugwira ntchito bwino, zizindikiro zina zokhudzana ndi kusamba, monga kutupa ndi kusintha kwa maganizo, zimatha kuchitika ngakhale popanda kutuluka magazi.

Chifukwa chakuti muli ndi ma chromosome ndi mahomoni achikazi, mumakumana ndi kukula kwabwinobwino kwa kugonana, monga kukula kwa mawere ndi kukula kwa tsitsi m'khwapa ndi m'malo oberekera. Komabe, mutha kumva kupweteka kapena kusasangalala mukayamba kugonana ndi abambo. Izi zili choncho chifukwa abambo anu ndi opyapyala, opapatiza, komanso afupiafupi kuposa masiku onse.

Ngati muli ndi matenda a mtundu wa 2 MRKH, mungakumanenso ndi zizindikiro zina monga:

• Mavuto a impso, kapena kulephera kwa impso imodzi kapena zonse ziwiri.
• Mavuto ndi mafupa a msana kapena zilema zina za dongosolo la mafupa.
• Kulephera kumva.
• Mavuto ena a mtima.

Kodi chimayambitsa MRKH ndi chiyani?

Ofufuza sakudziwabe chomwe chimayambitsa matenda a MRKH. Komabe, akudziwa kuti amakhudza mavuto ena ndi majini ndi ma chromosome. Komabe, sanathe kufotokoza kuti ndi jini imodzi yeniyeni. Chofunika ndichakuti si chinthu chomwe mayiyo anachita kapena sanachite panthawi ya mimba . Choncho musadandaule nazo.

Thupi la mkazi lobereka limayamba kukula m'masabata oyamba a mimba. Machubu a fallopian, chiberekero, khomo lachiberekero, ndi gawo lapamwamba la nyini zimapangidwa kuchokera ku chinthu chotchedwa Müllerian ducts . Kwa anthu omwe ali ndi matenda a MRKH, machubu a Müllerian awa sakula mokwanira. Sizikudziwikabe chifukwa chake izi zimachitika mwa anthu ena. Komabe, chifukwa mazira amakula mosiyana ndi ziwalo zina zonse zoberekera, mazira nthawi zambiri sakhudzidwa.

Kodi mungadziwe bwanji ngati muli ndi MRKH?

Madokotala nthawi zambiri amazindikira matenda a MRKH ngati mtsikana wachinyamata walephera kusamba koyamba.

Gawo loyamba pozindikira vutoli ndi kuyezetsa thupi . Dokotala wanu adzaika chala chovala magolovesi mu nyini yanu ndikuyeza kuzama ndi m'lifupi mwake. Kuyezetsa kumeneku kumatha kuzindikira MRKH chifukwa nyini ndi yafupika. Kenako, mungapemphedwe kuti muchite mayeso ojambulira zithunzi, monga ultrasound scan kapena MRI (magnetic resonance imaging scan), kuti muwone ngati chiberekero chanu, machubu a fallopian, impso, kapena ziwalo zina zakhudzidwa. Nthawi zina, mayeso a magazi angachitike kuti muwone kuchuluka kwa mahomoni anu.

Kodi mankhwala a MRKH ndi ati?

Chithandizo cha matenda a MRKH chimasiyana malinga ndi zolinga zanu ndi zizindikiro zanu. Pali njira zochizira opaleshoni komanso zosachizira opaleshoni. Zina mwa njirazi ndi monga vaginoplasty, kukula kwa nyini, ndi kuika chiberekero.

Kutambasuka kwa nyini

Njira imodzi yomwe madokotala amagwiritsa ntchito kutambasula nyini ndi kugwiritsa ntchito zipangizo zotchedwa vaginal dilators . Izi zimapangidwa ndi pulasitiki kapena silicone ndipo zimakhala ndi kutalika ndi m'lifupi mosiyanasiyana. Zipangizozi zofanana ndi chubu zimathandiza kukulitsa ndi kutambasula nyini kuchokera mkati. Dokotala wanu adzakufotokozerani njira yabwino kwambiri yogwiritsira ntchito vaginal dilator pa vuto lanu.

Vaginoplasty (kukonzanso nyini ndi opaleshoni)

Vaginoplasty ndi opaleshoni yopangira nyini . Madokotala ochita opaleshoni ali ndi njira zingapo zochitira izi. Nthawi zambiri, amabowola dzenje ndikuliphimba ndi minofu yotengedwa kuchokera ku gawo lina la thupi lanu. Izi zimakupatsani mwayi wogonana mwachizolowezi.

Kusamutsa chiberekero

Kuika chiberekero kungapatse mayi yemwe ali ndi matenda a MRKH mwayi wobereka mwana. Iyi ndi opaleshoni yaikulu. Ikuphatikizapo kuyika chiberekero kuchokera kwa wopereka kwa mayi yemwe alibe. Izi zimapatsa anthu omwe ali ndi MRKH mwayi wobereka mwana wawo. Kuika chiberekero sikunachitike kwambiri padziko lonse lapansi, koma kungakhale chithandizo chopambana kwambiri mtsogolo.

Kodi vutoli lingapewedwe?

Ayi, palibe njira yopewera MRKH syndrome . Itha kuchitika mwa anthu omwe sanakhalepo nayo kale, kapena ikhoza kukhala majini. Monga tanenera kale, siimayamba ndi jini imodzi yeniyeni.

Kodi anthu omwe ali ndi MRKH angakhale ndi mwana?

Inde, anthu omwe ali ndi `(MRKH syndrome)` akhoza kukhala ndi mwana!Ngati mazira anu akugwira ntchito, mazira anu amatha kusakanikirana ndi umuna ndikuuphatikiza ndi feteleza pogwiritsa ntchito njira ya in vitro fertilization (IVF). Kenako dzira limasamutsidwira kwa mayi woyembekezera/woberekera . Izi zikutanthauza kuti mudzakhala ndi mwana wokhala ndi majini anu, omwe amakula m'mimba mwa mayi wina wathanzi.

Ndi mavuto ena ati azaumoyo omwe angayambitsidwe ndi MRKH?

Takambirana kale kuti anthu omwe ali ndi ``Mtundu wachiwiri`` MRKH amathanso kukhala ndi mavuto ndi ziwalo zina, monga impso, msana, kapena mtima. Kuphatikiza apo, mavuto ena azaumoyo omwe amapezeka mwa anthu omwe ali ndi ``Mtundu wachiwiri`` MRKH ndi awa:

• Mavuto okhudzana ndi mafupa a msana.
• Scoliosis.
• Kusokonekera kwa impso, monga kulumikizidwa kwa impso kapena kusowa kwa impso imodzi kapena zonse ziwiri (renal agenesis).
• Kuwonjezeka kwa chiopsezo cha miyala ya impso, matenda a mkodzo, komanso kutsekeka kwa mkodzo.
• Kulephera kumva.
• Matenda a mtima.

Mavuto a ziwalo zoberekera amapezeka kawirikawiri kwa anthu omwe ali ndi MRKH. Kuwonjezera pa kulephera kutenga pakati kapena kukhala ndi mwana wawowawo, anthu omwe ali ndi chiberekero chosakula bwino amathanso kudwala matenda monga endometriosis.

Ndi zonsezi, ndi zachilendo kumva kupsinjika maganizo . Dokotala wanu angakulangizeni kuti mulowe nawo gulu lothandizira kapena kufunafuna chithandizo cha uphungu wa maganizo, monga chithandizo chamaganizo ndi khalidwe (CBT), kuti chikuthandizeni kuthana ndi vutoli. Zinthu izi zingakhale zothandiza kwambiri.

Nzosadabwitsa kuti kupeza kuti muli ndi matenda a Mayer-Rokitansky-Küster-Hauser (MRKH) kungakhale kodabwitsa kwambiri. Ngati mwabadwa ndi chiberekero kapena nyini yosakula bwino, simungadziwe mpaka muli aang'ono ndipo mwangoyamba kumene kusamba. Ngakhale kuti si vuto lomwe lingawononge moyo, lingayambitse nkhawa yaikulu, kusokoneza luso la mkazi lotenga pakati komanso kugonana. Nthawi zina, lingakhudze ziwalo zina ndikuwonjezera chiopsezo cha matenda ena.

Zinthu zofunika kwambiri kuzikumbukira (Uthenga Wopita Nawo Kunyumba)

Chabwino, tsopano mwamvetsa bwino zomwe takhala tikulankhula, "MRKH syndrome." Chofunika kwambiri kukumbukira ndichakuti simuli nokha . Pali anthu ena padziko lapansi omwe akukhala ndi matendawa.

• Ngati muli ndi zizindikiro ngati izi, ndikofunikira kwambiri kuonana ndi dokotala wabwino ndikudziwitsidwa bwino za matendawa .
• Pali mankhwala ochiritsira omwe alipo. Lankhulani ndi dokotala wanu ndipo sankhani mankhwala omwe ali abwino kwa inu.
• Musataye mtima ndi ana. Ndi ukadaulo monga `(IVF)` ndi `(kuberekera ana)`, pali mwayi wokwaniritsa maloto amenewo.
• Samalaninso thanzi lanu la maganizo.Ngati kuli kofunikira, funani uphungu ndipo lowani m'magulu othandizira anthu omwe adakumanapo ndi zomwezo. Izi zikupatsani mphamvu zambiri.
• Si vuto lanu. Ichi ndi vuto lachilengedwe lomwe lingachitikire aliyense.

Dokotala wanu, komanso mwina gulu la akatswiri, adzakupatsani chithandizo ndi chitsogozo chomwe mukufunikira kuti mupite patsogolo ndi `(MRKH syndrome)` iyi. Muwakhulupirire. Ngati muli ndi mafunso ena okhudza izi, musaope kuwafunsa. Khalani ndi thanzi labwino!

Matenda a MRKH , Matenda a Mayer-Rokitansky-Küster-Hauser, matenda a vaginal agenesis, matenda a uterine agenesis, thanzi la akazi, thanzi lobereka, amenorrhea