Mwina inuyo kapena munthu wina m'banja mwanu mwauzidwa ndi dokotala wanu za mankhwala atsopano komanso osazolowereka. Angatchedwe Olipudase Alfa (Xenpozyme). Iyi si mankhwala wamba, omwe amagwiritsidwa ntchito kwambiri omwe timamva nthawi zambiri. Iyi ndi mankhwala omwe amaperekedwa pa matenda enaake. Ndicho chifukwa chake ndi zachilendo kuti mukhale ndi mafunso ambiri okhudza izi. Mungakhalenso ndi mafunso monga "Kodi izi zidzachitika ndi chiyani?", "Kodi izi ndi zotetezeka?", "Kodi zinthu zomwe muyenera kusamala nazo ndi ziti?" Musadandaule, tidzakambirana momveka bwino komanso mwachidule za mankhwalawa, zomwe amachita, komanso zinthu zomwe muyenera kusamala nazo.
Kodi kwenikweni chimachitika ndi mankhwala awa ndi chiyani?
Mankhwalawa amagwiritsidwa ntchito pochiza matenda osowa kwambiri a majini. Mwachipatala, amatchedwa Acid Sphingomyelinase Deficiency , kapena (ASMD) mwachidule.
Mwachidule, anthu omwe ali ndi ASMD sapanga enzyme yomwe imapangidwa mwachibadwa m'matupi awo. Enzyme ndi mtundu wa mapuloteni omwe amathandiza pa ntchito zosiyanasiyana za mankhwala m'matupi athu. Pamene enzyme iyi ikusowa, mtundu wapadera wa mafuta wotchedwa sphingomyelin umayamba kusonkhana m'ziwalo zofunika monga chiwindi, ndulu, ndi mapapo. Taganizirani ngati chitoliro cha madzi chomwe chimatsekedwa ndi dothi kenako n’kutsekeka kwathunthu.
Apa ndi pomwe mankhwala otchedwa Olipudase Alfa amathandiza. Chomwe mankhwalawa amachita ndikupereka enzyme yomwe ikusowa m'thupi kuchokera kunja. Izi zimatchedwa enzyme replacement therapy . Kenako kuchuluka kwa mafuta omwe amasonkhana mosafunikira kumachepa pang'onopang'ono, kuwonongeka kwa ziwalo kumawongoleredwa, ndipo zizindikiro zimachepa.
Zinthu zomwe muyenera kuuza dokotala wanu musanagwiritse ntchito mankhwalawa
Musanayambe kumwa mankhwalawa, ndikofunikira kudziwitsa dokotala wanu za zinthu zotsatirazi. Musabise zinthuzi, chifukwa ndizofunikira kwambiri pa chitetezo chanu.
- Ngati muli ndi vuto la ziwengo ndi mankhwala awa, Olipudase alfa, mankhwala ena aliwonse, chakudya, utoto kapena zosungira zomwe zawonjezeredwa ku chakudya.
- Ngati muli ndi pakati, kapena mukuyembekezera mwana posachedwa , izi ndizofunikira kwambiri. Tiyeni tikambirane zambiri za izi.
- Ngati ndinu mayi woyamwitsa .
Momwe mungaperekere mankhwala ndi zomwe muyenera kudziwa
Mankhwalawa amaperekedwa ngati jakisoni mu mtsempha. Kunena zoona, amalowetsedwa m'thupi kudzera mu mtsempha, monga momwe amachitira ndi madzi amchere. Njira imeneyi nthawi zambiri imachitika kuchipatala kapena kuchipatala, moyang'aniridwa ndi dokotala kapena anamwino ophunzitsidwa bwino.
Komabe, nthawi zina, mungakwanitse kuipeza kunyumba. Ngati ndi choncho, mudzaphunzitsidwa bwino momwe mungakonzekere bwino komanso momwe mungapangire jakisoni. Muyenera kutsatira malangizo monga momwe dokotala wanenera.
Kutaya singano ndi ma syringe
Musataye singano ndi ma syringe omwe mumagwiritsa ntchito kunyumba m'zinyalala wamba . Pali chidebe chapadera cha sharping. Ngati mulibe, funsani dokotala wanu kapena chipatala za chimodzi.
Kodi mumapereka izi kwa ana aang'ono?
Inde, mankhwalawa akhoza kuperekedwa kwa makanda ndi ana omwe ali ndi matenda enaake. Komabe, pali zinthu zingapo zomwe muyenera kusamala nazo. Chifukwa chake, ngati mukupereka mankhwalawa kwa mwana, lankhulani ndi dokotala za mankhwalawa mokwanira ndipo fotokozani zonse.
Kodi mungachite chiyani ngati mlingo wa mankhwala wawonjezeka?
Ngati mukuganiza kuti mwamwa mankhwala ochulukirapo, musachite mantha ndipo nthawi yomweyo imbani National Poisons Information Centre ku National Hospital , kapena pitani ku Emergency Treatment Unit (ETU) ya chipatala chapafupi.
Zinthu zapadera zoti muzisamala nazo komanso zotsatira zake zoyipa
Pamene mukumwa mankhwala awa, dokotala wanu adzakupemphani kuti mubwere kudzaonana ndi dokotala nthawi zonse kuti aone momwe mulili. Adzafunikanso kuchita zinthu monga kuyeza magazi. Zingatenge nthawi kuti mumve ubwino wonse wa mankhwala awa, choncho ndikofunikira kukhala oleza mtima ndi chithandizo chanu.
Anthu ena akhoza kukhala ndi vuto lalikulu la ziwengo kapena kulowetsedwa m'madzi akapatsidwa mankhwalawa. Kuti achepetse chiopsezochi, dokotala wanu angakupatseni mankhwala ena (monga piritan) asanakupatseni mankhwalawa. Tsatirani malangizowo molondola.
Mimba ndi njira zolerera: Iyi ndi mfundo yofunika kwambiri. Kumwa mankhwalawa panthawi ya mimba kungayambitse mavuto aakulu kwa mwana. Chifukwa chake, ndikofunikira kugwiritsa ntchito njira yoyenera yolerera pamene mukumwa mankhwalawa komanso kwa masiku 14 mutasiya kumwa mankhwalawa. Lankhulani ndi dokotala wanu za izi ndipo sankhani njira yoyenera kwa inu.
Gome ili m'munsimu likuwonetsa mitundu yayikulu ya zotsatira zoyipa zomwe zingachitike ndi mankhwalawa.
| Zotsatirapo za Katemera wa Olipudase Alfa | |
|---|---|
| Zotsatirapo zoyipa zomwe muyenera kuuza dokotala wanu nthawi yomweyo | |
| Zotsatira za chifuwa kapena Angioedema | Kutupa pakhungu, kuyabwa, kutupa kwa nkhope, maso, milomo, lilime, manja kapena mapazi, kuvutika kumeza kapena kupuma. |
| Machitidwe a kulowetsedwa | Kupweteka pachifuwa, kuvutika kupuma, kukomoka, kumva chizungulire. |
| Zizindikiro za kuvulala kwa chiwindi | Kupweteka m'mimba kumtunda kumanja, kusowa chilakolako cha chakudya, nseru, ndowe zowala, mkodzo wakuda wachikasu kapena bulauni, maso kapena khungu kukhala lachikasu, kutopa kosazolowereka. |
| Zotsatirapo zomwe nthawi zambiri sizili zoopsa, koma ziyenera kufotokozedwa kwa dokotala ngati zikupitirira | |
| Zina mwazinthu | Chifuwa, kutsegula m'mimba (kusanza), malungo, mutu, kupweteka kwa mafupa, nseru, kusanza. |
Kodi pali mavuto aliwonse ndi mankhwala ena?
Monga momwe tikudziwira, mankhwalawa sananenedwe kuti amayambitsa kuyanjana kwakukulu ndi mankhwala ena. Komabe, musaganize kuti ndi choncho. Patsani dokotala wanu mndandanda wathunthu wa mankhwala onse omwe mumamwa (kuphatikizapo mavitamini, mankhwala azitsamba, ndi zowonjezera). Komanso, onetsetsani kuti mwauza dokotala wanu ngati mumasuta kapena kumwa mowa.
Uthenga Wopita Nawo Kunyumba
- Olipudase Alfa ndi njira yapadera yochiritsira matenda osowa a majini otchedwa ASMD.
- Izi zimaperekedwa ngati jakisoni mumtsempha, nthawi zambiri kuchipatala.
- Musanayambe chithandizo, uzani dokotala wanu za ziwengo zanu zonse, mapulani anu oyembekezera, ndi mankhwala ena onse omwe mukumwa.
- Mukamamwa mankhwalawa, samalani ndi zizindikiro za ziwengo, jakisoni, kapena kuwonongeka kwa chiwindi (monga khungu lachikasu, mkodzo wakuda). Uzani dokotala wanu nthawi yomweyo ngati muwona chilichonse mwa zizindikirozi.
- Pewani kutenga mimba mukumwa mankhwalawa. Lankhulani ndi dokotala wanu za njira zoyenera zolerera.
- Tsatirani malangizo a dokotala wanu molondola ndipo pita kukaonana ndi dokotala nthawi zonse.
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