Ese birakugora kumira ibiryo? Cyangwa wumva unaniwe igihe cyose, wumva ufite ubunebwe? Hari igihe ibi bintu bisa n'ibisanzwe, ariko hashobora kuba hari indi mpamvu ibyihishe inyuma. Uyu munsi tugiye kuvuga ku ndwara idakunze kugaragara ariko ikomeye. Iyo ni indwara ya Plummer-Vinson.
Indwara ya Plummer-Vinson ni iki?
Mu magambo make, Plummer-Vinson syndrome (PVS) ni indwara aho ibimenyetso bitatu bifitanye isano bibaho. Hari igihe abaganga bayita "triad," bivuze "uruvange rwa bitatu." Reka turebere hamwe izi ndwara eshatu:
1. Kubura icyuma gihagije: Ibi bibaho iyo umubiri wawe udafite icyuma gihagije cyo gukora poroteyine yitwa hemoglobine mu turemangingo dutukura tw'amaraso yawe. Urabizi, hemoglobine ni yo itwara ogisijeni kuri buri turemangingo two mu mubiri wawe. Rero, iyo udafite icyuma gihagije, hemoglobine ntikorwa neza, kandi umubiri wawe ntubone ogisijeni ukeneye. Ibi nibyo bitera ibimenyetso nko kunanirwa no kubura umwuka.
2. Urusobe rw'inkari: Ibi bibaho iyo ingingo ntoya kandi zitari zisanzwe zivutse mu muhogo wawe, cyangwa mu muyoboro w'ibiribwa. Tekereza nk'urusobe rw'inkari rugaragara mu muhogo wawe. Ibi bituma umuhogo ufungana kandi ugafunga. Ibi bituma ibiryo bigorana kunyuramo.
3. Kugorwa no kumira (Dysphagia): Iri ni ryo zina abaganga bita kugorwa no kumira ibiryo n'ibinyobwa bitewe n'imitsi yo mu gifu yavuzwe haruguru. Hari abantu bashobora kugorwa no kumira ibiryo bikomeye ndetse n'ibintu by'amazi.
Ibi byitwa andi mazina. Rimwe ni sideropenic dysphagia. Kandi mu Bwongereza, ni ukuvuga mu Bwongereza, byitwa Paterson-Brown Kelly syndrome.
Noneho, dore ikintu udakwiye gutinya. Abantu barwaye Plummer-Vinson syndrome (PVS) bivugwa ko bafite ibyago byinshi byo kurwara kanseri yo mu muhogo cyangwa kanseri yo mu gice cy'umuyoboro w'amazi nyuma y'ubuzima bwabo. Ariko, ibi ni ibyago gusa . Muganga wawe azagusuzuma buri gihe kandi azakugenzura uko bikenewe kugira ngo amenye indwara nk'izo hakiri kare.
Ni ibihe bimenyetso by'ibi?
Noneho reka turebe ibimenyetso umuntu urwaye indwara ya Plummer-Vinson syndrome (PVS) agaragaza. Ibi bimenyetso ntibibaho kuri bose mu buryo bumwe, kandi hari abantu bashobora kuba bafite bimwe mu bimenyetso gusa.
- Kumva unaniwe kandi unaniwe igihe cyose: Iki ni ikimenyetso gikomeye cy'ibura ry'ubutare. Uba unaniwe nubwo wamaze gukora uturimo duto kandi ukumva usinziriye umunsi wose.
- Guhumeka bigoranye (dyspnea): Ushobora kumva unaniwe guhumeka, atari gusa iyo ugenda gato, uzamuka ingazi, ahubwo rimwe na rimwe ndetse no iyo uhagaze gusa.
- Kugorwa no kumira ibiryo:Iki ni cyo kimenyetso kiranga iyi ndwara. Cyane cyane iyo umuntu ariye ibiryo bikomeye, nk'umuceri, umugati, inyama n'amafi, yumva afite uburibwe mu muhogo no mu gituza. Hari abantu bagomba kunywa amazi make kugira ngo bamire ibiryo. Nubwo ibiryo bikomeye bitoroshye mu ntangiriro, nyuma bishobora kugorana kumira ibinyobwa.
- Ururimi rurabyimba, rukabyimba, rukamera nk'umutuku (glossitis): Ururimi ruragenda rworoha, rugatukura, rimwe na rimwe rushobora kumva risa n'aho rurimo gushya.
- Umunwa wumye (xerostomia): Imbere mu kanwa wumva wumye igihe cyose, kandi hari ukumva udafite amacandwe.
- Indwara ya Angular Cheilitis: Impande z'umunwa ziracikamo uduce, zigatukura, kandi zigasa n'izibabara.
- Inzara ziracika intege kandi zigakomera nk'ibiyiko: Inzara ziracika intege cyane kandi zigacika byoroshye. Hari igihe inzara zigwa hagati, nk'ikiyiko (koilonychia).
- Kubyimba kw'uduheri twa tiroyide n'ibibyimba (utubyimba twa tiroyide): Agaheri ka tiroyide, kari imbere mu ijosi, gashobora kwaguka kakumva nk'ikibyimba.
- Splenomegali: Agace k'umugongo ni urugingo ruherereye hejuru ibumoso bw'inda yacu. Rushobora kandi kubyimba muri iyi ndwara, ariko ubusanzwe nta bimenyetso bikomeye bitera.
Impamvu ni iyihe?
Mu by’ukuri, abashakashatsi ntibaramenya neza icyatera indwara ya Plummer-Vinson syndrome (PVS). Ariko hari ibintu bike batekereza kandi bakeka:
- Ikibazo gikomeye ni ukubura icyuma: Abantu benshi batekereza ko kubura icyuma igihe kirekire bituma imitsi yo mu muhogo icika intege kandi igakora urushundura. Icyuma kirakenewe kuri enzymes nyinshi mu mubiri wacu.
- Kubura intungamubiri: Hari icyizere cy'uko atari icyuma gusa, ahubwo n'izindi vitamine n'imyunyu ngugu nabyo bishobora kugira ingaruka kuri ibi.
- Indwara z’ubudahangarwa bw’umubiri: Ushobora kuba warumvise indwara nka rubagimpande na celiac. Izi ni indwara ziterwa n’ubudahangarwa bw’umubiri zibaho iyo ubudahangarwa bw’umubiri bwacu bwibasiye uturemangingo twacu. Kubera ko hari abantu bamwe na bamwe bafite PVS nabo bafite izi ndwara, abaganga batekereza ko zishobora kuba zifitanye isano n’ubudahangarwa bw’umubiri.
- Ingaruka z'uturemangingo: Abandi bizera ko iyi ari indwara iterwa n'uturemangingo, bivuze ko iyo umuntu wo mu muryango ayirwaye, abandi bashobora kuyirwara cyane.
Ariko ibi biracyari ibitekerezo gusa. Hakenewe ubushakashatsi bwimbitse kugira ngo hamenyekane impamvu nyayo.
Ni nde uri mu kaga gakomeye ko kugira ibi?
Indwara ya Plummer-Vinson (PVS) ni indwara idakunze kugaragara . Ntiyibasira buri wese. Ariko, nk'uko imibare ibigaragaza, ikunze kugaragara ku bagore b'abazungu. Akenshi yibasira abagore bari mu kigero cyo hagati, bari hagati y'imyaka 40 na 70.Iyi ni yo mpamvu ikunze kugaragara cyane. Ariko, ni gake cyane, ni ukuvuga gake cyane, byagaragaye ko igaragara mu rubyiruko ndetse no mu bana bato.
Mu bihe byashize, ni ukuvuga mu ntangiriro za 1900, iyi ndwara yari isanzwe mu bihugu bya Skandinaviya (urugero: Suwede, Noruveje). Ariko, mu mpera za 1900, ni ukuvuga mu myaka mike ishize, yari yaragabanutse cyane muri ibyo bihugu. Impamvu nyamukuru ibi byatewe ni iterambere ry’imirire y’abaturage bo muri ibyo bihugu icyo gihe, cyane cyane ko ibiryo bikungahaye kuri feri byoroshye kuboneka.
Ni izihe ngorane zishobora guterwa na PVS?
Nkuko twabivuze mbere gato, abantu barwaye indwara ya Plummer-Vinson syndrome (PVS) basanze bafite ibyago byinshi byo kurwara kanseri yo mu muhogo na kanseri yo mu gice cyo hasi cy'umuhogo, yitwa hypopharynx, kurusha abantu badafite PVS.
Ariko ibi ntibigutere ubwoba. Si abantu bose bafite PVS bazarwara kanseri. Ibi ni ibintu bishobora gutera ibyago gusa.
Kubera ko iyi ndwara idakunze kugaragara cyane, nta makuru ahagije y’ubushakashatsi ahagije agaragaza neza umubare w’abantu barwaye PVS barwara kanseri.
Ariko niba ufite iyi ndwara, muganga wawe azagerageza kubona ikintu nk'icya kanseri hakiri kare , kuko icyo gihe hari amahirwe menshi yo kuvurwa no gukira. Niyo mpamvu ari ngombwa kujya kwisuzumisha buri gihe, nk'uko muganga wawe abivuga.
Ni gute indwara ya Plummer-Vinson syndrome (PVS) ipimwa?
Niba ufite ibimenyetso byavuzwe haruguru, iyo ugiye kwa muganga, azakubaza ibibazo kandi agusuzume. Hanyuma, bazagutegeka gupima amaraso no gukoresha uburyo bwihariye bwo gupima kugira ngo bemeze niba ufite PVS.
- Ibipimo by'amaraso: Ibi ahanini bipima ikibazo cyo kubura amaraso mu mubiri bitewe n'ibura ry'ubutare.
- Umubare wuzuye w'amaraso (CBC): Ibi bishobora kugenzura ibintu byinshi nko mu maraso yawe, mu maraso yera, no mu maraso yawe.
- Gupima amaraso mu maraso (PBS): Ibi bikubiyemo kureba icyitegererezo cy'amaraso hakoreshejwe mikorosikopi kugira ngo harebwe imiterere n'ingano y'uturemangingo dutukura tw'amaraso. Mu gihe habuze icyuma, uturemangingo dutukura tw'amaraso dushobora kuba duto kandi tworoheje (microcytic, hypochromic).
- Ibizamini by'ingano y'icyuma: Ibizamini nka serum ferritin, serum fer, na TIBC (Total Iron Binding Capacity) bishobora gutanga igitekerezo cy'ingano y'icyuma mu mubiri.
- Ibizamini byo gupima: Ibi bireba imiyoboro y'igifu n'icyateye dysphagia.
- Indwara yo mu gice cyo hejuru cya endoscopy (OGD - Oesophago-Gastro-Duodenoscopy):Muri ibi, umuyoboro ufite kamera ntoya ushyirwamo unyuze mu kanwa hanyuma umwobo, igifu, n'igice cya mbere cy'amara mato kikagenzurwa. Ibi bigufasha kureba neza niba insinga zihari. Iyo bibaye ngombwa, agace gato k'urugingo (biopsy) gashobora gufatwa kugira ngo gasuzumwe.
- Barium swallow / Esophagram: Muri iki kizamini, unywa ikintu cyitwa barium hanyuma ugafatwa amashusho ya X-ray. Barium ituma umwobo ugaragara kuri X-ray, bigatuma ubona ahantu habyimbye cyangwa hafunganye.
- Videwo yo gupima fluoroscopy: Iki nacyo ni ikizamini cya X-ray. Gifata videwo urimo kumira ubwoko butandukanye bw'ibiryo. Ibi bishobora kugufasha kubona neza uko urimo kumira n'aho ikibazo kiri.
Hari igihe muganga ashobora gukenera gukora ibizamini byinshi kugira ngo amenye impamvu nyayo itera kubura icyuma. Urugero, bashobora gushaka ibisebe byo mu gifu cyangwa kuva amaraso mu mara.
Ibi bivurwa bite?
Hari intego ebyiri z'ingenzi mu kuvura indwara ya Plummer-Vinson syndrome (PVS). Imwe ni ugukosora ikibazo cyo kubura icyuma , indi ni ugukemura ikibazo cyo kumira ibiryo .
- Uburyo bwo kuvura ikibazo cyo kubura icyuma:
- Igikuru ni uguha umubiri wawe icyuma gikenewe. Ushobora gufata inyunganiramirire ya feri . Ugomba kuyifata nk'uko muganga wawe abikubwira, mu gihe cyose uyikeneye.
- Ku bantu bamwe, iyo ibinini bya fer binyowe bidakoreshejwe neza, cyangwa niba fer ikennye cyane, fer ishobora gutangwa mu mitsi (IV - Iron Intravenous).
- Niba ufite indi ndwara itera kubura icyuma gikozwe mu bwonko (urugero: kuva amaraso menshi mu gihe cy'imihango, hemorrhoids, ibisebe byo mu gifu), ugomba kuvura na byo.
- Uburyo bwo kuvura ingorane zo kumira (Dysphagia):
- Kenshi na kenshi, iyo iki kibazo cyo kubura icyuma gikozwe mu mubiri kivuwe, umubiri ukabona icyuma gikozwe mu muhogo, imiyoboro y'amazi irashira hafi mu buryo bwikora, kandi ingorane zo kumira ibiryo ziragabanuka cyane.
- Tuvuge ko ubuvuzi bw'icyuma bwonyine butavura burundu ingorane zawe zo kumira. Niba ari uko bimeze, hari uburyo bwo kwagura, cyangwa kongera, umwobo wawe. Byitwa kwagura umwobo . Ibi bikorwa mu gihe cyo gupima umwobo. Agakoresho gato kameze nk'agapira gashyirwa mu gice cy'umwobo gito hanyuma kakavugururwa cyangwa kakagurwa kugira ngo umwobo wawe ukwaguke. Ubu si ukubaga gukomeye, ahubwo ni uburyo bworoshye, busanzwe butababaza kandi busaba kudacamo uduce mu mwobo. Hari abantu bashobora gukenera kubikorerwa inshuro zirenze imwe.
Ni iki giteganyijwe kuri iki kibazo?
Mu by’ukuri, umuntu urwaye indwara ya Plummer-Vinson syndrome (PVS) ashobora kwitega ibisubizo byiza no gukira .
Ku bantu benshi, iyo ikibazo cyo kubura icyuma gikozwe mu mubiri gikemutse, ibimenyetso byo kubura amaraso mu mubiri (nk'umunaniro no guhumeka nabi) biragabanuka cyane. Nanone, ingorane zo kumira ibiryo ziragabanuka cyane.
Iyo ikibazo cyo kumira kidakemutse hakoreshejwe icyuma gusa, uburyo bwo kwagura umuyoboro bwavuzwe haruguru bukunze gutuma ikibazo cyo kumira kirushaho kuba cyiza. Hari abantu bashobora gukenera kuvurwa ubu buryo inshuro zirenze imwe. Ariko ni uburyo bworoshye cyane kandi bufite ingaruka nke.
Muganga wawe ashobora gushaka gukora isuzuma rya endoskopi kugira ngo arebe niba hari indwara nka kanseri mu muhogo wawe cyangwa mu gifu cyawe. Ariko ibuka ko kugira PVS ari ikintu gishobora gutera kanseri gusa . Kugira PVS ntibivuze ko uzagira kanseri nta kabuza.
Vugana na muganga wawe uburyo kugira PVS bigira ingaruka ku byago byawe bya kanseri, uburyo bwo kubyitwaramo mu gihe kiri imbere, n'inshuro ugomba kwipimisha.
Ese indwara ya Plummer-Vinson Syndrome (PVS) ishobora kwirindwa?
Abaganga ntibaramenya neza icyatera indwara ya Plummer-Vinson syndrome (PVS), bityo ntibishoboka kumenya neza niba hari uburyo bwihariye bwo kuyirinda.
Ariko, kwirinda kubura icyuma gihumanya ikirere no kugivura vuba bishoboka niba ufite ikibazo gitera kubura icyuma gihumanya ikirere bishobora kugabanya ibyago byo kurwara PVS.
Kubwibyo, ni byiza kumenya neza ko ubona feri ihagije mu byo urya n'ibyo unywa. Shyira mu ndyo yawe ibiryo bikungahaye kuri feri (urugero: inyama zitukura, amashaza, epinari, lentils, soya).
Ni ryari ngomba kujya kwa muganga?
Niba ufite ibimenyetso bya anemia (urugero, umunaniro ukabije, guhumeka nabi buri gihe, uruhu rwera), kandi niba ibyo bimenyetso bitarakira nyuma y'ibyumweru bibiri, menya neza ko wagiye kwa muganga.
Nanone, niba wumva ufite ikibazo cyo kumira ibiryo, cyane cyane niba wumva urimo kubura ibiryo bikomeye , kandi indwara ntiyongere kumera neza, ni byiza kujya kwa muganga kugira ngo akugire inama aho kubyirengagiza.
Ni iki ngomba kubaza muganga?
Iyo ugiye kwa muganga, mubaze impungenge zawe n'ubwoba bwawe. Urugero, ushobora kubaza ibibazo nk'ibi:
- Ni iyihe mpamvu ishobora kuba intera iyi ndwara yo kubura amaraso?
- Ni ibihe bipimo ngomba gukora kugira ngo menye neza niba mfite indwara ya Plummer-Vinson syndrome (PVS)?
- Ni ubuhe bwoko bw'ubuvuzi ungira inama yo kunkorera?
- Ese nkeneye kubagwa mu gukamura umwobo kugira ngo nkosore ikibazo cyanjye cyo kubura umwuka? Bizakenerwa ko bikorwa kangahe?
- Ese nkwiye guhangayikishwa n'ibyago byanjye byo kurwara kanseri mu gihe kiri imbere? Nkwiye gukora iki kuri ibyo?
Niba utekereza ko ufite ibimenyetso bya Plummer-Vinson syndrome (PVS), jya kwa muganga ako kanya. Ntabwo ugomba kwihanganira umunaniro ukabije uterwa no kubura amaraso. Ntabwo ugomba kandi kwihanganira ububabare bwo kumira (dysphagia) butuma kurya biba ikibazo gikomeye. Hari igihe igisubizo kiba cyoroshye nko kunywa ibinini bike bya feri. Bitabaye ibyo, ushobora kubona ihumure ukoresheje kwagura umwobo wawe. Ariko, hari uburyo bwo kuvura bushobora kugufasha kumva umeze neza .
Amaherezo, ibintu by'ingenzi cyane ugomba kwibuka
Indwara ya Plummer-Vinson syndrome (PVS) ni indwara ikunze kugaragara cyane. Ariko, ibimenyetso byayo by'ingenzi ni ukubura amaraso mu mubiri, kugorwa no kumira (dysphagia), no kurwara imiyoboro y'imiyoboro y'amaraso . Niba uhora ubabara, ugorwa no kumira, cyangwa ubabara ururimi, ni ngombwa kujya kwa muganga aho kubitekereza nk'ibisanzwe.
Hari uburyo bwiza bwo kuvura PVS. Akenshi, ibimenyetso byinshi biragenda neza iyo ikibazo cyo kubura icyuma gikozwe mu mubiri gikosowe kandi umwobo ukaguka bibaye ngombwa.
Nubwo tuvuga ku byago byo kurwara kanseri, ibuka ko ari ikintu gishobora gutera ibyago gusa. Iyo uganiriye na muganga wawe, ugahabwa ibizamini bikenewe, kandi ugahabwa ubuvuzi bukwiye, ushobora gukomeza kugira ubuzima bwiza. Bityo rero ntugire ubwoba bw'ikintu icyo ari cyo cyose, kandi niba ufite ikibazo, shaka inama z'abaganga vuba. Ubuzima bwawe ni ubw'agaciro kanini kuri wewe!
👩🏽⚕️ Ibibazo by'inyongera (Ibibazo Bikunze Kubazwa)
💬 Ese indwara ya Plummer-Vinson ni indwara yo mu muhogo?
Iki si ikibazo cyo mu muhogo gusa, ni indwara iteje akaga ifata umuhogo bitewe n’ibura ry’indyo y’ibanze. Bitewe no kubura amaraso menshi mu mubiri kubera kubura icyuma, imiterere isa n’urusobe rw’amaraso (urusobe rw’amaraso) igaragara hejuru y’umuhogo, bigatuma bigoye kumira ibiryo.
💬 Nzumva meze nte nindya mfite iki kibyimba mu muhogo?
Ikimenyetso nyamukuru ni (Dysphagia) cyangwa 'kugorwa no kumira'! Nubwo ushobora kunywa amazi, iyo uriye ibiryo bikomeye nk'umuceri/inyama, wumva ufite 'ikibyimba cyafashe mu muhogo'. Nanone, bitewe no kubura icyuma, iminwa yawe irababara impande zombi (Cheilitis), ururimi rwawe rugatukura kandi rukabyimba (Glossitis), kandi inzara zawe zigahinduka nk'ikiyiko (Koilonychia).
💬 Ese uru rurerure/urushundura rurimo kuziba umuhogo rukurwaho binyuze mu kubagwa?
Nta kubagwa gukomeye gukenewe! Igitangaza gikomeye ku bantu benshi ni uko iyo muganga atanze 'inyongeramusaruro z'icyuma' akanahindura urugero rw'icyuma mu maraso, ururenda rwo mu muhogo rushonga ubwarwo kandi ibiryo bishobora kumirwa! Ariko iyo rutazimiye, hashyirwamo kamera ya endoskopi hanyuma agapira gato (Balloon dilation) koherezwa kugira ngo kaguke/kamene ururenda.
Indwara ya Plummer -Vinson, PVS, kubura icyuma, kubura amaraso, kugorwa no kumira, kuribwa mu mihogo, kubura amaraso











💬 Comments (0)
Kwipimisha kanseri y'ibere, kwisuzuma no kwirinda byakozwe byoroshye. Kanseri y'ibihaha
Ishyirireho intego ya calorie hanyuma ubare itariki yo kugabanya ibiro.