Wakamboona here kuti mazino evamwe vanhu ane ruvara rusinganzwisisike, pamwe ruvara rwebhuruu-grey, kana ruvara rweyero-brown? Kana kuti une mazino asina kusimba zvekuti anotyoka kana kupera kunyangwe kana ukadya chimwe chinhu chidiki? Ungafunga kuti izvozvo zvakajairika. Zvisinei, izvi zvinogonawo kukonzerwa nechirwere chisingawanzoitiki chinoitika panguva yekukura kwezino chinonzi `(Dentinogenesis Imperfecta)`. Ngatitaurei nezvazvo zvishoma nhasi, zvakanaka here?
Chii chinonzi `(Dentinogenesis Imperfecta)`? Ngatizvinzwisise zviri nyore, handiti?
Zvichitaurwa zviri nyore, `(Dentinogenesis Imperfecta)` idambudziko rinowanzoitika kana mazino aumbwa, ndiko kuti, kana mazino achikura. Chinoitika munyaya iyi ndechekuti mazino ako anova asina simba uye anotyoka nyore nyore . Kufanana nebhisikiti, kana ukatyora zvishoma, rinotyoka. Uyewo, mazino evanhu vane chirwere ichi anopenya zvishoma. Sezvandambotaura kare, ruvara rwacho rwunopenyawo , rwebhuruu-grey kana yero-brown .
Dambudziko iri, rinonzi ``Dentinogenesis Imperfecta,'' rinogona kukanganisa mazino ako ekutanga nemazino ako echigarire . Izvi zvinoreva kuti zviratidzo zvinogona kutanga pazera diki, kana kuti zvinogona kuoneka gare gare muhupenyu.
Zvino tarisai, patinotora zino, rine zvikamu zvakati wandei. Chikamu chakasimba chinopenya pamusoro chinonzi `(Enamel)`. Pasi pacho pane chimwe chikamu, chinonzi `(Dentin)`. Chikamu ichi `(Dentin)` ndicho chinonyanya kupa zino simba neruvara. Chinoitika mu `(Dentinogenesis Imperfecta)` ndechekuti chikamu `(Dentin)` hachikure zvakanaka. Chii chinoitika ipapo? Nekuti `(Dentin)` haina simba, `(Enamel)` iri pamusoro haina kubatana zvakanaka nezino. Ndosaka `(Enamel)` ichikurumidza kupwanyika uye kupera simba.
Zvakakosha: `(Dentinogenesis Imperfecta)` yakasiyana ne`(Amelogenesis Imperfecta)`. Mu`(Amelogenesis Imperfecta)`,`(Enamel)` yezino inokanganiswa zvakananga. Mu`(Dentinogenesis Imperfecta)`, dambudziko riri mu`(Dentin)`.
Izvi zvinonzi hazviwanzoitiki . Kazhinji, chirwere ichi chinoitika mumunhu mumwe chete pavanhu 6,000 kusvika 8,000.
Pane mhando dze `(Dentinogenesis Imperfecta)` here?
Ehe, tiri kutaura nezvemhando nhatu huru dze `(Dentinogenesis Imperfecta)`. Ngationei kuti ndedzipi.
1. `(Dentinogenesis Imperfecta)` Rudzi 1 (Rudzi I): Izvi zvakakosha. Nekuti rudzi urwu runoitika nechirwere chinonzi `(Osteogenesis Imperfecta)`. `(Osteogenesis Imperfecta)` chirwere chinoita kuti mapfupa asanyanya kusimba (chirwere chemapfupa asina kusimba). Saka, pamwe nematambudziko emazino, vanhu ava vanewo matambudziko emapfupa. Chikonzero cheizvi ndechekuti pane shanduko dzakati wandei mu`(Majini)` emajini e`(COL1A1)` kana `(COL1A2)`. Majini ese aya anobatsira kugadzira puroteni `(Collagen)` mumuviri wedu.
2. `(Dentinogenesis Imperfecta)` Rudzi rwechipiri (Rudzi rwechipiri): Rudzi urwu rwakajairika kupfuura mazino anogara aripo.Zvinowanzoitika mumazino emwana. Vanhu ava vanowanzova nezvimwe zvirwere zvishoma zvekuzvarwa nazvo. Zvisinei, zvakaonekwa kuti dzimwe nguva pane mukana wekurasikirwa nekunzwa nekuda kwekukwegura .
3. `(Dentinogenesis Imperfecta)` Rudzi rwechitatu (Rudzi rwechitatu): Iyi ndiyo mhando isingawanzoitiki . Inobata mazino anogara kwenguva refu kupfuura mazino evana. Vaongorori vakataura nezverudzi urwu kunyanya pakati pevanhu vedzinza rechiJudha vanonzi `(Ashkenazi Jewish)`, uye mumhuri dzinoverengeka dzinogara kumaodzanyemba kweMaryland.
Ndezvipi zviratidzo zve `(Dentinogenesis Imperfecta)`? Ungazviziva sei?
Sezvandambotaura, zviratidzo zvikuru kuchinja ruvara uye mazino asina simba uye anotsemuka . Mazino anowanzo penya, aine ruvara rweyero-brown kana bhuruu-grey .
Kunze kweizvozvo, unogona kuona zvimwe zviratidzo zvakaita se:
- Kurasikirwa nemazino emwana kunonoka: Mazino emwana anodonha kunonoka kupfuura zvakajairika.
- Enamel Hypoplasia: Izvi zvinoreva kuti enamel layer iri pamusoro pemazino yakarasika zvakakwana.
- Kufamba-famba kwemajoini: Vamwe vanhu vanogona kukotama majoini avo, akadai seminwe nemagokora, vachidzokera shure zvakanyanya.
- Kubereka Kwemazino: Izvi zvinoreva kuzvarwa usina mazino.
- Enamel yemazino isina simba: Enamel yacho haina simba uye inokurumidza kupera.
Chimbofungai, kana mazino emwana mudiki aine ruvara rusinganzwisisike, aine ruvara rwebhuruu, kana kuti akatyoka nyore nyore, unofanira kunetseka nawo.
Sei `(Dentinogenesis Imperfecta)` iyi ichiitika? Chii chinokonzera?
Chikonzero chikuru cheizvi kuchinja kwemajini edu. Kunyanya, kuchinja kwemajini kunonzi `(DSPP) ` kunokonzera `(Dentinogenesis Imperfecta). Iri `(DSPP)` jini rinopa mirairo yekugadzira `(Dentin)`, chikamu chepakati chemazino edu. Saka kana paine dambudziko nejini iri, `(Dentin)` hariumbike zvakanaka.
Kuchinja kwemajini uku kunogona kutorwa kubva kuvabereki , kana kuti kunogona kuitika zvisina tsarukano .
Avo vane Dentinogenesis Imperfecta type 1, sezvandambotaura, vane shanduko mumajini eCOL1A1 kana COL1A2. Idzi ndidzo shanduko dzemajini dzinoonekwawo kune avo vane Osteogenesis Imperfecta (chirwere chinokonzera mapfupa asina kusimba).
Vanachiremba vanoongorora sei izvi?
Kana iwe kana mwana wako muine chimwe chezviratidzo izvi, munofanira kutanga maona chiremba wemazino . Iye ndiye achatanga aongorora muviri wake obvunza kana paine mumwe munhu mumhuri menyu akambosangana nechirwere ichi..
Uyezve, kana uchifungidzira kuti une Dentinogenesis Imperfecta, bvunzo dzinotevera dzinogona kuitwa kusimbisa chirwere ichi:
- Kutora X-ray yemazino.
- Pamwe unogona kuita CT scan .
Nekutarisa mifananidzo iyi, chiremba anogona kunzwisisa mamiriro emukati memazino, uye hunhu hwe "Dentin".
Dzimwe nguva, chiremba wako anogona kukurudzira kuongororwa kwemajini kuti aone kuti chii chaizvo chinokonzerwa nekuchinja kweDNA yako kunokonzera dentinogenesis imperfecta.
Ndeapi marapirwo eizvi? (Kurapwa)
Chinangwa chikuru chekurapa Dentinogenesis Imperfecta ndechekusimbisa mazino asina simba . Vanachiremba vemazino vanoshandisa nzira dzakasiyana-siyana dzekugadzirisa mazino kuti vaite izvi.
Semuyenzaniso:
- Kuzadza mazino: Zadza mipata nemakatsemuka mumazino.
- Maveneer: Aya magoko matete anoiswa pamberi pezino. Anogonawo kuvandudza chitarisiko chezino.
- Korona: Korona yakafanana nekavha inoiswa pazino. Inofukidza zino rose uye inorisimbisa.
Mishonga iyi inoshandisa zvinhu zvine ruvara rwemazino, saka unogona kuchengetedza kunyemwerera kwako kwakanaka.
Kana uine Dentinogenesis Imperfecta, une mukana wekuti mazino ako apere kana wakura. Kana ukarasikirwa nemazino, unogona kuatsiva nemazino emazino kana mazino emazino .
Itariro yerudzii yaungave nayo paunenge uchirarama nemamiriro ezvinhu aya? (Outlook)
Maonero ako anoenderana nezvinhu zvakati wandei:
- Zera rako pawakaongororwa chirwere ichi.
- Wakatanga kurapwa nguva yakareba sei.
- Une rudzii rweDentinogenesis Imperfecta?
Chinhu chakakosha ndechekuti Dentinogenesis Imperfecta hairapiki . Zvisinei, nekuchengetedza mazino zvakanaka uye tsika dzakanaka dzekuchenesa muromo, unogona kubatsira kudzivirira kukuvara kwemazino ako uye kuramba akasimba. Kana chirwere ichi chikaonekwa nekukurumidza uye chikarapwa, mhedzisiro yacho inova nani.
Dentinogenesis Imperfecta inogona kudzivirirwa here?
Zvinosuwisa kuti Dentinogenesis Imperfecta haigone kudzivirirwa nekuti inokonzerwa nekuchinja kwemajini kwatisingagoni kudzora. Zvisinei, kutanga kurapwa nekukurumidza kunogona kuderedza kukuvara kwenguva refu kwemazino.
Ndingachengetedza sei mazino angu? (Kuzvitarisira)
Kana uine `(Dentinogenesis Imperfecta)`, kuchena kwemuromo kwakakosha.Zvakakosha kuchengetedza mazino. Kuti uderedze kuora kwemazino nekukuvara, ita zvinotevera:
- Bvunza chiremba wemazino nezvemishonga yekusimbisa mazino ako ne fluoride .
- Shamba mazino ako kaviri kana katatu pazuva uchishandisa bhurashi remazino rakapfava uye mushonga wemazino une fluoride .
- Deredza kudya zvine shuga yakawanda uye zvine acid.
- Sukurudza muromo wako ne fluoride sukurudza kamwe chete pazuva.
- Shanyirai chiremba wemazino nguva nenguva kuti muongororwe uye mucheneswe .
Chii chakanaka kudya nekunwa kana uine `(Dentinogenesis Imperfecta)`?
Chinhu chakanakisa chekuita kusarudza zvekudya nezvinwiwa zvine shuga shoma uye acid shoma . Izvi zvinoreva kuderedza zvinwiwa zvakaita sesoda, michero yecitrus senge lime, uye tomato sauces zvakanyanya sezvinobvira. Zvakanakawo kuderedza kudya zvekudya zvinoda kutsengwa uye zvakaoma kana kuti zvinogocha .
Heano mamwe ezvekudya zvakanaka zvemunhu ane `(Dentinogenesis Imperfecta):`
- Hove dzakabikwa
- Mhando dzeCasseroles
- Muriwo wakabikwa
- Oatmeal
- Pasta ine muto wakagadzirwa nekirimu
- Mazai akakuyiwa
- Smoothies
Izvi zvikafu zviri nyore kudya uye hazvikuvadzi mazino zvakanyanya.
Ndinofanira kuona chiremba rini?
Kana iwe kana mwana wako mukaona chimwe chinhu chisina kujairika kana chakasiyana pamusoro pemazino ake, zvakanaka kuudza chiremba wako nekukasika . Yeukai, zviratidzo zveDGI zvinogona kuonekwa chero pazera ripi zvaro. Kana mazino ekutanga emwana wako achiratidzika sebhuruu, grey, kana brown , iva nechokwadi chekuona chiremba wemazino wevana kuti akupe mazano.
Mibvunzo ipi yaunofanira kubvunza chiremba?
Kana ukaonekwa uine Dentinogenesis Imperfecta, ungangoda kubvunza chiremba wako mibvunzo yakaita seiyi:
- Rudzii rwe `(DGI)` rwandinarwo?
- Rudzii rwekurapwa rwandinoda?
- Kurapwa kuchatora nguva yakareba sei? Kurapwa kuchatora nguva yakareba sei?
- Ndinofanira kucheneswa mazino angu kangani?
- Ndeapi matanho ekudzivirira andingatora kuderedza kupera uye kukuvara kwezino?
Pakupedzisira chimwe chinhu... (Mharidzo Yekuenda Kumba)
Kuva nemazino asina simba uye anotyoka nyore nyore kunonetsa zvikuru. Zvinonetesawo kungwarira pese paunodya. Kana uine `(Dentinogenesis Imperfecta)`, unogona kunyara nezvekuonekwa kwemazino ako. Nekuda kweizvi, ungasade kutarisana nevanhu.
Asi yeuka, hausi wega.Kune vanachiremba vanogona kukubatsira. Vanogona kukurudzira marapirwo ekusimbisa mazino ako, kunatsiridza kunyemwerera kwako, uye kuwedzera kuzvivimba kwako. Saka, usazvidya mwoyo nezvechinhu chero chipi zvacho, uye tevera zano rachiremba wako.
Nekuongorora chirwere ichi pakutanga, kugamuchira kurapwa kwakakodzera, uye kutevedzera tsika dzakanaka dzekuchenesa muromo, unogona kurarama hupenyu hune hutano, hunofadza kunyangwe uine chirwere che `(Dentinogenesis Imperfecta).'
` dentinogenesis imperfecta, zvirwere zvemazino, mazino asina simba, kuchinja kweruvara rwemazino, zvirwere zvemajini, hutano hwemazino, mazino evacheche

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