Wakamboona here kuti maziso emwana wako akaparadzaniswa zvishoma kupfuura zvakajairika? Kana kuti pane chiremba akakuudza nezvazvo here? Mukurapa, tinodana chirwere ichi kuti Orbital Hypertelorism . Dzimwe nguva chinonziwo Ocular Hypertelorism. Kunyange zvazvo mashoko aya achigona kutyisa, izvi hazvina kuipa sezvatinofunga. Nhasi, tichataura nezvazvo zviri nyore, nenzira yaunogona kunzwisisa.
Chii chinonzi Orbital Hypertelorism?
Zvichitaurwa zviri nyore, Orbital Hypertelorism haisi chirwere chakasiyana. Inowanzoonekwa sechiratidzo chehumwe hurema hwekuzvarwa nahwo kana chirwere chemajini.
Funga nezvazvo, kana mwana ari mudumbu, mapfupa echiso chake anochinja zvishoma nezvishoma. Panguva ino, maburi maviri emaziso anochengetedza maziso ake anenge akaparadzaniswa zvishoma pane zvakajairika. Nokudaro, mukaha uri pakati pemaziso unoonekwa zvakanyanya kupfuura mumwana akajairwa. Nzvimbo iyi yakawedzerwa inozadzwa nemapfupa ekuwedzera.
Chinhu chakakosha ndechekuti vana vazhinji vane maziso ari kure kudaro havazove nematambudziko ekuona. Kuti kuona kwacho kwakanganiswa here zvinoenderana nekuti maziso ari kure zvakadii uye zvimwe zviratidzo zvemwana.
Vanachiremba vanoongorora sei izvi chaizvo?
Kazhinji, chiremba anoona chirwere ichi mwana achangozvarwa. Dzimwe nguva, chinogona kuonekwa panguva yekuongorora mwana achiri mudumbu.
Hapana daro rakatarwa pakati pemaziso, asi vanachiremba vanoshandisa zviyero zviviri zvikuru kuti vaone izvi.
| Nzira yekuyera | Zvakatsanangurwa zviri nyore |
|---|---|
| Kureba kweInner Canthal | Kureba kubva pakona yeziso rimwe riri pedyo nemhino kusvika pakona yerimwe ziso riri pedyo nemhino. |
| Nharaunda yevana vechikoro | Kureba kubva pakati pemboni yeziso rimwe kusvika pakati pemboni yerimwe ziso. |
Zviyero izvi zvose zvakakwirira kupfuura zvakajairwa muvana vane orbital hypertelorism.
Sei izvi zviri kuitika? Ndezvipi zvikonzero zvikuru?
Vanachiremba vanotenda kuti hwaro hwechirwere ichi hunoiswa pakati pevhiki yechina neyechisere yekukura kwemwana. Funga nezvemapfupa edehenya remwana sezvidimbu zvepuzzle ine mativi matatu (3D) zvichisangana. Kana paine kukanganiswa kana shanduko mumatanho anobatanidzwa mukubatanidza zvidimbu izvi, masokisi maviri emaziso anogona kusarongeka uye kuparadzaniswa zvakanyanya.
Zvikonzero zvikuru zviviri zveizvi ndeizvi:
1. Zvirema zvekuzvarwa nazvo
2. Matambudziko emajini
1. Zvirwere zvekuzvarwa nazvo
Kuremara kwekuzvarwa nakwo kunokanganisa chitarisiko, nhengo dzemukati, kana maitiro emakemikari mumuviri wemwana pakuzvarwa. Izvi zvinogona kukonzerwa ne:
- Zvinhu zvemajini uye zvenhaka.
- Zvimwe zvirwere zvinotapuriranwa naamai panguva yekuzvitakura.
- Kusangana nemwaranzi.
- Kushandisa zvinodhaka kana doro panguva yekuzvitakura.
Dzimwe nguva zvikanganiso zvekuzvarwa zvinogona kuitika pasina chikonzero chakajeka, kunyangwe zvisina kurongeka. Craniosynostosis ndeimwe yezvikanganiso zvekuzvarwa. Chinoitika pano ndechekuti machira anobatanidza mapfupa edehenya remwana anobatanidzwa. Izvi zvinogona zvakare kukonzera Orbital Hypertelorism.
2. Matambudziko emajini
Majini madiki eDNA anopa mirairo kumasero ari mumuviri wedu. Kuchinja kwemajini aya kunogona kukonzera zvirwere zvemajini. Zvimwe zvezvirwere zvemajini zvinogona kukonzera orbital hypertelorism ndeizvi:
- Chirwere cheApert
- DiGeorge syndrome
- Chirwere cheEdwards
- Chirwere cheCrouzon
- Chirwere cheNoonan
- Neurofibromatosis rudzi 1
Kana mwana wako aine chirwere ichi, chiremba wako anogona kukutumira kuti uwane mazano ezvemajini, izvo zvinogona kukubatsira kunzwisisa zvakawanda nezvenjodzi yemhuri yako yekubatwa nezvirwere zvemajini.
Ndezvipi zvinorapwa izvi?
Vana vane chirwere ichi vanogona kudzoserwa maziso avo pamwe chete kuburikidza nekuvhiyiwa. Izvi zvinonzi kuvhiyiwa kwekuvakazve . Kuvhiyiwa uku kunowanzoitwa kana mwana ava nemakore ari pakati pe5 ne7. Kuvhiyiwa uku kunoita kuti mwana aonekwe zvakanaka uye kunoderedza daro riri pakati pemaziso.
Mwana wako achada kuongororwa maziso nguva nenguva asati avhiyiwa uye mushure mekuvhiyiwa kuti aongorore shanduko dziri mumaziso nemaonero ake.
Vanachiremba vanovhiya vanoshandisa nzira mbiri dzekuvhiya pakuita izvi.
| Rudzi rwekuvhiyiwa | Chii chiri kuitika? |
|---|---|
| Osteotomy yeBhokisi | Pano, chiremba anobvisa mapfupa neganda zvakawandisa pamusoro pemhino uye anogadzirisa maburi emaziso kuti akwane munzvimbo iyoyo. Fungidzira uchicheka chikamu chakaita sesikweya pamwe chete netsiye nepamusoro pemhino, woisa maburi emaziso muchikamu ichocho. |
| Kupatsanurana kwechiso | Uku kuvhiyiwa kwakaoma zvishoma. Kunoitwa pavana vane orbital hypertelorism nedzimwe matambudziko emapfupa echiso (semuenzaniso, shaya, mapfupa ematama). Kunosanganisira kugadzira patsva maburi emaziso, mhino, uye mapfupa ematama kuti maziso aswedere pedyo, ukuwo kuchigadziriswa matambudziko eshaya nemazino. |
Matambudziko anogona kuitika mushure mekuvhiyiwa
Sekunge kune chero kuvhiyiwa kupi zvako, pane njodzi diki diki dzinobatanidzwa. Idzi dzinosanganisira:
- Kubuda ropa
- Utachiona
- Mavanga
- Maziso akarembera ( Ptosis )
- Kuona kaviri (diplopia )
- Kurasikirwa nekuona kana upofu (izvi hazviwanzoitiki)
Chiremba wako achakutsanangurira njodzi idzi zvakadzama.
Unofanira kuona chiremba rini?
Kana mukaona shanduko mumaziso emwana wenyu kana kuona kwake, kurumidzai kuona chiremba.
Uyewo, kana mwana wako akaonekwa nechimwe chezviratidzo zvinotevera, enda kuEmergency Department (ETU) yechipatara chiri pedyo nekukurumidza.
- Kurasikirwa kamwe kamwe kana kudzikira kwekuona.
- Kurwadziwa kwakanyanya mumaziso.
- Kuona zvinhu zvitsva kana kuti zvinoyangarara pamberi pemaziso.
Yeukai, kungoti mwana anozvarwa aine Orbital Hypertelorism hazvirevi kuti haazokure aine hutano hwakanaka sevamwe vana. Zvichienderana nechirwere chakakonzera izvi, mwana wako angangoda kurapwa kwenguva yakati. Taura nachiremba wako nezvazvo.
Mharidzo Yekuenda Nayo Kumba
- Orbital Hypertelorism haisi chirwere chakasiyana. Ichi chiratidzo chehumwe hurema hwekuzvarwa nahwo kana chirwere chemajini.
- Vana vazhinji vane chirwere ichi havana matambudziko ekuona.
- Kana mwana ava nemakore angangoita 5-7, anogona kuvhiyiwa kuti maziso ake adzoke panzvimbo yaagara ari.
- Kana mwana wako aine chirwere ichi, usatya kutaura pachena nachiremba wako wowana mazano anodiwa uye kurapwa.
- Zvakakosha kuona chiremba nenguva uye kuongororwa maziso.
👩🏽⚕️ Mibvunzo yekuwedzera (Mibvunzo Inowanzo bvunzwa)
💬 Orbital Hypertelorism chirwere cherudzii?
Uku hakusi kuchinja kwechitarisiko kwakajairika! 'Orbital Hypertelorism' idambudziko rekuzvarwa naro rinoitika kana dehenya remwana nemapfupa akakomberedza maziso (orbits) zvikakura mudumbu, zvichiita kuti daro riri pakati pemaziso rive rakasiyana zvakanyanya/rakaparadzana zvakanyanya. Iri harisi chirwere chemaziso, asi dambudziko remapfupa echiso!
💬 Ndezvipi zvikonzero zvikuru zvinoita kuti maziso emwana aonekwe kure zvakanyanya (Orbital Hypertelorism)?
Ichi hachisi chirwere chinowanzoitika chega, asi chiratidzo chikuru chezvirwere zvine njodzi zvikuru zve 'Genetic Syndromes'! Muzvirwere zvakakomba zvakaita se'Apert Syndrome', 'Crouzon Syndrome' uye 'DiGeorge Syndrome', mapfupa aya anosundidzirwa parutivi nekuda kwematambudziko ari mudehenya. Dzimwe nguva, bundu rinokura pachiso uri mudumbu (encephalocele) rinogonawo kukonzera kuti maziso asundidzirwe parutivi.
💬 Ndezvipi zvimwe zviratidzo zvine njodzi zvinosangana nevana vane maziso akareba uye ndeapi maoparesheni anogona kuitwa kuti izvi zvirapwe?
Kazhinji, vana ava vane matambudziko ekuona, kuremara kwepfungwa, zvikanganiso zvemwoyo, uye zvirwere zvinouraya zvakaita se cleft palate. Kuti varape izvi, kana mwana ava nemakore angangoita 5-8, vanofanira kuvhiyiwa zvakakomba uye zvakaoma (Craniofacial reconstruction / Facial Bipartition) umo dehenya rinochekwa, uropi hunochengetedzwa, gomba reziso rinochekwa uye rinoswededzwa pedyo, uye chiso chinovakwazve.











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