Vanhu vazhinji pavanonzwa izwi rekuti 'anemia ' , vanobva vangofunga nezvekushaikwa kwesimbi . Ndosaka vachinzwa kuneta nguva dzese, vaneta, vachinzwa dzungu, uye dzimwe nguva vasingakwanise kurara. Asi waizviziva here kuti mune dzimwe nguva anemia, zvinopesana zvinoitika? Panzvimbo pekushaikwa kwesimbi, simbi iri mumasero eropa 'inowedzera'. Izvi hazvinzwike sezvisinganzwisisike here? Nhasi tiri kutaura nezvechimwe chirwere cheanemia chakakosha, asi chisingawanzoitiki, chinonzi sideroblastic anemia.
Zvichitaurwa zviri nyore, chii chinonzi Sideroblastic Anemia?
Kuti tinzwisise izvi, ngatitangei tatarisa ropa redu. Mukati memasero matsvuku eropa muropa redu mune puroteni inonzi hemoglobin . Basa rayo guru nderekubata okisijeni inopinda mumapapu patinofema uye kuitakura mumuviri wese. Saka okisijeni iyi inokosha kuti sero rega rega mumuviri wedu rirarame.
Zvino, kuti tigadzire hemoglobin iyi, muviri wedu unoda mineral inonzi 'iron'. Kazhinji, anemia inoitika kana muviri usina iron. Saka, haugone kugadzira hemoglobin.
Zvisinei, muSideroblastic Anemia, chimwe chinhu chakasiyana chinoitika. Pano, hapana kushomeka kwesimbi mumuviri. Kutaura zvazviri, kune iron yakawandisa! Dambudziko nderekuti nekuda kwekusakwana kuri mumasero matsvuku eropa anogadzirwa mumongo wedu wemapfupa, haakwanise kushandisa iron iyi kugadzira hemoglobin.
Fungidzira kicheni ine mupunga, mvura, nemunyu wekubikira mupunga, asi chitofu chemupunga chakatyoka. Saka haugone kubika mupunga. Ndizvo zvazviri. Muchirwere ichi, pane iron yakawanda, chinhu chinodiwa kugadzira hemoglobin. Asi fekitari inoshandisa iron iyoyo kugadzira hemoglobin, masero edu matsvuku eropa, haishande nemazvo. Saka iron isingashandiswi inotanga kuungana mukati memasero matsvuku eropa aya asina kunaka. Tinodaidza masero aya asina kujairika akaunganidza iron nenzira iyi `(Sideroblasts)`.
Ndezvipi zviratidzo zvechirwere ichi?
Zviratidzo zvechirwere ichi zvakafanana zvikuru nezvimwe zvirwere zvekushaya ropa, saka dzimwe nguva zvinogona kuvhiringidzika zviri nyore. Uye nekuda kwekuti chirwere ichi chinokura zvishoma nezvishoma, ungasatomboziva kuti unacho. Izvi ndizvo zviratidzo zvikuru zvaunogona kuona.
| Chiratidzo | Tsananguro |
|---|---|
| Kushaya simba kwemuviri uye kuneta | Kunzwa kunonoka, kuneta nekukurumidza kunyangwe nemabasa madiki. |
| Ganda rakachenuruka | Kutaridzika kusina kuchena kunoonekwa kana ropa riri shoma mumuviri. |
| Kuoma kufema | Asima inokonzerwa nekusawana oxygen yakakwana mumuviri. |
| Kurova kwemoyo nekukurumidza (Tachycardia) | Kurova kwemoyo kwakanyanya kana kurova kwemoyo zvakanyanya. |
| Musoro nekutsamwa | Kugara uchirwadziwa nemusoro uye kushatirwa. |
| Kurwadziwa kwechipfuva | Mune zvimwe zviitiko, kurwadziwa kwechipfuva kunogona kuitika. |
Ndeapi marudzi makuru eSideroblastic Anemia?
Chirwere ichi chinogona kupatsanurwa muzvikamu zviviri.
1. Kushaya ropa kweSideroblastic Anemia Kwenhaka
Ichi chirwere chisingawanzoitiki, chemajini. Kureva kuti, chinopfuudzwa kumwana kuburikidza nemajini anobva kune mumwe wevabereki. Rudzi rwakajairika rweizvi iX-linked Sideroblastic Anemia . Izvi zvinokonzerwa nekuchinja kwemajini kunokanganisa kugadzirwa kwehemoglobin. Nekuda kweizvozvo, muviri unoedza kunwisa iron yakawanda kubva muchikafu kuti utsive kushomeka kwehemoglobin. Muzviitiko zvakakomba, zvinogona kukuvadza nhengo dzakadai sechiropa . Rudzi urwu rwekuzvarwa narwo runowanzoonekwa vasati vasvitsa makore makumi matatu.
2. Rudzi rwekutanga kwechirwere (Acquired Sideroblastic Anemia)
Rudzi urwu ndirwo rwakajairika. Chinhu chakanakisa ndechekuti runogona kurapwa kazhinji . Kunyangwe vanachiremba dzimwe nguva vasingazive chikonzero chaicho, pane zvinhu zvakawanda zvinokonzera chirwere ichi:
- Mimwe mishonga: Kunyanya mimwe mishonga inopihwa yechirwere cherurindi.
- Kunwa doro zvakanyanya: Kunwa doro zvakanyanya kwenguva yakareba chinhu chikuru chinokonzera njodzi.
- Makemikoro ane chepfu : Kugara kwenguva refu uchisangana nemamwe makemikari ane chepfu, akadai semutobvu.
- Zvimwe zvirwere: Chirwere ichi chinogonawo kukonzerwa nezvimwe zvirwere zvakaita sezvirwere zvemuviri, bundu, kana zvirwere zve metabolic.
Pane chimwe chinhu chatinofanira kunyatsotarisa pano. Vanhu vanosvika gumi muzana vane chirwere ichi (Acquired) vanogona kukura nekenza yeropa inonzi Leukemia. Saka, zvakakosha kuongorora chirwere ichi nemazvo, kuwana chikonzero, uye kurapwa.
Pamusoro pezvo, mhando dzese dziri mbiri dzinogona kukura chimwe chirwere chinonzi hemochromatosis , chinoita kuti iron yakawandisa iungane mumuviri.
Nzira yekuziva sei chirwere ichi chaizvo?
Nekuti zviratidzo zvakafanana nezvimwe zvirwere zvekushaya ropa, zvinogona kuoma kuona. Saka zvakakosha kuteerera muviri wako. Kana uine chimwe kana kupfuura chezviratidzo zvakanyorwa pamusoro apa, ndapota ona chiremba wako.
Chiremba achakubvunzai nokungwarira nezvezviratidzo zvenyu, okuongororai, uye obva araira kuti muone kana muine chirwere ichi.
- Kuongororwa kweropa: Kuongororwa kweropa rose uye kuongororwa kwesimbi ndizvo zvakakosha.
- Kusveta Ropa Panze: Pano, sampuro yeropa inoongororwa nemaikorosikopu kuti ione kana paine masero asina kujairika anounganidza iron (Sideroblasts) atakataura nezvawo kare.
- Kuongororwa kweBone Morrow Biopsy: Mune zvimwe zviitiko, sampuli diki yebone morrow ingangoda kutorwa uye kuongororwa kuti chirwere chacho chionekwe.
- Mimwe miedzo: Kana zvichidikanwa, chiremba anogonawo kukurudzira kuti munhu aedze MRI scan kana kuti aedze majini.
Inorapwa sei?
Nzira dzekurapa dzinoenderana nekuti une rudzi rwekuzvarwa narwo here kana kuti rwawakawana.
- Kurapa Chikonzero: Kana uine rudzi rwawakawana, danho rekutanga kubvisa chikonzero chacho. Semuenzaniso, kana mushonga uri kukonzera chirwere ichi, chiremba wako achamisa mushonga iwoyo okupa mumwe. Kana uri munhu anonwa doro zvakanyanya, uchafanira kurega kunwa doro zvachose.
- Vhitamini B6: Ongororo dzakaratidza kuti vhitamini B6, kana kuti pyridoxine, inogona kubatsira pakurapa marudzi ese echirwere ichi. Chiremba wako anogona kukupa vhitamini iyi sekuwedzera.
- Kubvisa iron yakawandisa: Kune mishonga inogona kupihwa kubvisa iron yakawandisa mumuviri. Deferoxamine inopihwa sejekiseni pasi peganda, uye Deferasirox inopihwa sepiritsi. Zvisinei, mishonga iyi inogona kukanganisa itsvo, saka inofanira kushandiswa pasi pekutarisirwa kwachiremba.
- Kuwedzerwa Ropa: Kana muviri wako ukasagamuchira kurapwa nevhitamini B6, chiremba wako anogona kukurudzira kuwedzerwa ropa. Zvisinei, izvi zvine dambudziko. Kana ukaramba uchiwedzerwa ropa, huwandu hwesimbi mumuviri wako hunowedzera, zvichiwedzera njodzi yekukuvara kwechiropa.
- Kudyara Bone Morrow: Uku ndiko kurapwa kwekupedzisira. Kunoonekwa kana pasina kumwe kurapwa kwakakura kwakapa mushonga.
Mharidzo Yekuenda Nayo Kumba
- Kushaya ropa mumuviri (Sideroblastic anemia) hakuna kufanana nekushaya ropa kwakajairika. Chinoitika pano ndechekuti huwandu hwesimbi mumasero eropa hunowedzera, kwete kudzikira.
- Kunyangwe uine zviratidzo zvakaita sekuneta nguva nenguva uye kucheneruka, usazvisarudzire wega kuti kungova kushomeka kwesimbi mumuviri.
- Chirwere ichi chinogona kuzvarwa nacho kana kukura gare gare nekuda kwezvinhu zvakaita sedoro kana mimwe mishonga.
- Kana uine zviratidzo, tsvaga rubatsiro rwechiremba. Kuzviongorora wega uye kuzvirapa pachako kunogona kuva nengozi huru.
- Kune mishonga inoshanda, yakaita sevhitamini B6 nemishonga inobvisa iron. Chiremba wako ndiye achasarudza mushonga wakakunakira.











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