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Zvinhu zvaunofanira kuziva nezveThalassemia: Ngatitaurei nezvazvo zviri nyore

Zvinhu zvaunofanira kuziva nezveThalassemia: Ngatitaurei nezvazvo zviri nyore

Unogara uchinzwa kuneta uye kuneta here? Pamwe ganda rako rakachenuruka zvishoma? Izvi hazvisi zvinhu zvisina kurongeka, pamwe kupererwa neropa uku, kureva kushomeka kweropa, kunogona kunge kuri nekuda kweizvi. Nhasi tiri kutaura nezve 'Thalassemia', chirwere chekuzvarwa nacho chine chekuita neropa, chinowanzoonekwa nevanhu vazhinji munyika medu. Usatya kana ukanzwa zita iri. Ngatinzwisise zvese nezveizvi zviri nyore.

Chii chinonzi Thalassemia chaizvo?

Zvichitaurwa zviri nyore, thalassemia chirwere cheropa chinogarwa nhaka chinogarwa nhaka kubva pakuzvarwa . Hachisi chirwere chinotapukira. Chirwere ichi chinodzivirira miviri yedu kugadzira hemoglobin yakakwana ine hutano.

Zvino ungave uchishamisika kuti hemoglobin chii. Hemoglobin ipuroteni yakakosha inowanikwa mukati memasero edu matsvuku eropa. Inoshanda se 'sevhisi yekuendesa' inotakura okisijeni mumiviri yedu yese. Iyi package inonzi hemoglobin inoendeswa kumasero ese mumuviri nemotokari dzinonzi masero matsvuku eropa.

Munhu ane thalassemia ane hemoglobin shoma mumuviri wake. Nokudaro, huwandu hwemasero matsvuku eropa ane hutano mumuviri hunodererawo. Iyi mamiriro emasero matsvuku eropa akaderera ndiyo yatinodaidza kuti anemia , kana kuti 'kushomeka kweropa'. Kana masero emuviri asingagamuchire okisijeni yaanoda, zviratidzo zvakasiyana-siyana zvinotanga kuoneka.

Izvi zvinoreva kuti unganzwa zvinhu zvakaita seizvi:

  • Kunzwa kuneta zvakanyanya uye kuneta nguva dzose.
  • Kutadza kufema zvakanaka.
  • Kunzwa kutonhora.
  • Kunzwa dzungu.
  • Ganda rakachenuruka.

Chii chinokonzera thalassemia? Ndiani ari panjodzi huru?

Thalassemia inokonzerwa nekusakwana kwemajini edu. Funga nezvemajini aya se 'programu code' ine mirairo yekuti zvese zviri mumuviri wedu zvinofanira kuumbwa sei. Puroteni yehemoglobin inoumbwa zvichienderana nemirairo inobva kumajini aya. Kana paine chisina kunaka nemirairo iyi, kana chikamu chayo chisipo, muviri haugone kugadzira hemoglobin ine hutano. Tinogara nhaka majini aya asina kunaka kubva kuvabereki vedu. Ndosaka ichinzi chirwere chinogarwa nhaka.

Molekyumu yehemoglobin inoumbwa nemacheni mana eprotein: macheni maviri ealpha globin uye macheni maviri ebeta globin.

  • Majini mana anodiwa kuti pave ne alpha globin chains (maviri kubva kumubereki mumwe nemumwe).
  • Majini maviri anodiwa kuti pave ne beta globin chains (rimwe kubva kumubereki mumwe nemumwe).

Kana paine chikanganiso mumajini anogadzira aya ma alpha kana beta chains, thalassemia inoitika. Kuoma kwechirwere kunotsanangurwa nehuwandu hwemajini asina chikanganiso.

Zvinotendwa kuti kuchinja kwemajini uku kwakabva senzira yekudzivirira malaria, kunyanya munzvimbo dzakadai seAfrica, Southern Europe, neAsia (kusanganisira nyika yedu), uko malaria yaive yakawanda munhoroondo. Nokudaro, thalassemia inowanzoonekwa pakati pevanhu vari munzvimbo idzi.

Ndeapi marudzi makuru e thalassemia?

Thalassemia inogona kukamurwa kuita mazinga akasiyana-siyana zvichienderana nekuoma kwechirwere. Kureva kuti, inogona kubva pakuva isina zviratidzo zvechirwere (hunhu), kusvika kudiki, pakati, uye huru. Chimiro chakanyanya kuoma, Thalassemia Major, chinowanzoda kurapwa nguva dzose.

Thalassemia yakakamurwa kuita mhando mbiri huru, zvichienderana nekuti chikanganiso chemajini chiri mumaketani ealpha kana beta.

1. Alpha Thalassemia

2. Beta Thalassemia

Ngatinzwisisei mhando mbiri idzi zvakadzama kubva patafura iri pazasi.

Rudzi rweThalassemia Kupesvedzera kwemajini Hunhu uye zviratidzo zvechirwere
Alpha Thalassemia
Kukanganisa mune rimwe jini Kukanganisa kuri mu 1 yemajini mana e alpha globin. Hapana zviratidzo. Kazhinji vanhu ava vanongotakura chirwere ichi.
Zvikanganiso zviviri zvemajini Kukanganisa kuri mumajini maviri e alpha globin mana. Ungave usina zviratidzo zvechirwere ichi, kana kuti ungaratidza zviratidzo zvishoma zvekushaya ropa (sekuneta kudiki).
Zvikanganiso zvitatu zvemajini (chirwere cheHemoglobin H) Kukanganisa mumajini matatu kubva mana ealpha globin.Zviratidzo zvinosiyana kubva pakati nepakati kusvika pakanyanya. Kushaya ropa kunoramba kuripo kweupenyu hwese.
Kukanganisa kwemajini ese mana Majini ese mana ealpha globin haana kunaka. Dambudziko guru. Kazhinji mwana anofira mudumbu kana nguva pfupi mushure mekuzvarwa.
Beta Thalassemia
Kukanganisa mune rimwe jini (Beta thalassemia minor) Kukanganisa kuri mu 1 yemajini maviri e beta globin. Zviratidzo zvekushaya ropa zvishoma zvinoonekwa. Vanhu vazhinji vanorarama hupenyu hune hutano sevatakuri vechirwere ichi.
Kusakwana kwemajini ese ari maviri (Beta thalassemia major / Cooley's Anemia) Majini ese ari maviri e beta globin haana kunaka. Zviratidzo zvinosiyana kubva pakati kusvika pakukura. Dambudziko rakanyanya kuoma rinonzi Cooley's anemia uye rinoda kurapwa nguva dzose.

Ndezvipi zviratidzo zvinogona kuitika zve thalassemia?

Zviratidzo zvaunoona zvinoenderana nerudzi rwe thalassemia yaunayo uye kuoma kwayo.

Nyaya dzisina zviratidzo

Kana uine kanganiso ke alpha gene kamwe chete kana chirwere chisina kunyanya kuipa se beta thalassemia minor, ungasava nezviratidzo zvachose . Kana kuti unganzwa kuneta kushoma.

Zviratidzo zvinyoro uye zvine mwero

Muzviitiko zvisina kunyanya kuoma, zvakaita se beta thalassemia intermedia, pamusoro pezviratidzo zvisina kunyanya kuoma kweropa, zvinotevera zvinogona kuitika:

  • Kukura zvishoma nezvishoma kwevana.
  • Kunonoka kuyaruka.
  • Kusashanda zvakanaka kwemapfupa (semuenzaniso, osteoporosis).
  • Kukura kwetsvina (iyi inhengo inorwisa hutachiona).

Zviratidzo zvakakomba

Mumamiriro ezvinhu akaomarara, akadai sekukanganisa kwemajini matatu ealpha (chirwere cheHemoglobin H) kana beta thalassemia major (Cooley's anemia), zviratidzo zvinoonekwa mwana asati asvitsa makore maviri. Kuwedzera kune zviratidzo zvataurwa pamusoro apa, zvinotevera zvinogona kuonekwa:

  • Kurasikirwa nechido chekudya.
  • Ganda rakachenuruka kana kuti rakatsvuka (senge jaundice).
  • Weti yakasviba, yakaita setii .
  • Kukura kusina kujairika kwemapfupa echiso.

Nzira yekuziva chirwere ichi nemazvo sei?

Thalassemia iri pakati nepakati uye yakanyanya inowanzoonekwa muhudiki. Izvi zvinodaro nekuti zviratidzo zvinotanga kuoneka mukati memakore maviri ekutanga ehupenyu hwemwana. Chiremba wako anogona kuraira kuongororwa kweropa kwakasiyana-siyana kuti aone chirwere chacho.

  • Kuverengwa Kweropa Kwakakwana (CBC): Izvi zvinoyera huwandu hwemasero matsvuku eropa, saizi yawo, uye mazinga ehemoglobin. Vanhu vane thalassemia vane masero matsvuku mashoma ane hutano, uye vanogona kunge vari madiki pakukura.
  • Kuongororwa kwehuwandu hwesimbi: Kuongororwa uku kwakakosha kusiyanisa pakati pekushaikwa kwesimbi nethalassemia.
  • Hemoglobin Electrophoresis: Bvunzo iyi inoshandiswa zvakananga kuongorora beta thalassemia.
  • Kuongororwa kwemajini: Miedzo iyi inoshandiswa kusimbisa alpha thalassemia uye kuona vatakuri vechirwere ichi.

Ndeipi mishonga yekurapa thalassemia?

Nzira dzekurapa dzinoenderana nekuoma kwechirwere. Kazhinji kacho, zvirwere zvishoma hazvidi kurapwa. Zvisinei, kune nzira dzakawanda dzekurapa zvirwere zvakakomba.

  • Kuisirwa Ropa: Zvichitaurwa zviri nyore, 'kupa ropa' . Ropa rinobva kumunhu ane hutano rinopihwa murwere kuburikidza netsinga kuti masero matsvuku eropa uye hemoglobin idzorerwe. Varwere vane beta thalassemia major vanoda kuwedzerwa ropa nguva dzose, kazhinji mavhiki maviri kusvika mana ega ega.
  • Kurapa neIron Chelation: Kuwedzerwa ropa kakawanda kunogona kukonzera kuwedzera kwesimbi mumuviri. Izvi zvinonzi 'iron overload'. Iyi iron yakawandisa inogona kukuvadza nhengo dzakadai semwoyo nechiropa. Saka, mishonga inobvisa iyi iron yakawandisa mumuviri inonzi 'iron chelation'. Iyi inogona kutorwa muchimiro chemapiritsi.
  • Zvikafu zveFolic Acid: Folic acid inopihwa kubatsira muviri kugadzira masero eropa ane hutano.
  • Kudyara Bone Morrow: Uku ndiko chete kurapwa kunogona kurapa thalassemia zvizere . Zvisinei, kuvhiyiwa kune njodzi uye kwakaoma. Izvi zvinoda mupi ane hutano anonyatsoenderana nemurwere, kazhinji munin'ina kana hanzvadzi.

Dzidza nezvematambudziko, kurapwa, uye hupenyu hwese.

Kana zvikasarapwa zvakanaka, dambudziko guru kukuvara kwemoyo, chiropa, uye mahormone anogadzira mahormone, kunyanya nekuda kwekuwandisa kwesimbi mumuviri. Saka, sezvakarairwa.Kurapa ne iron chelation kwakakosha zvikuru.

Kunyangwe chirwere ichi chichigona kurapwa nekuisirwa bota remapfupa, havasi vese vanogona kurapwa nekuda kwekuoma kwekuwana mupi akakodzera uye njodzi dzekuvhiyiwa kwacho.

Panyaya yehupenyu hunotarisirwa, kana uine thalassemia minor, unogona kutarisira hupenyu hunotarisirwa zvakajairika. Kunyangwe uine chirwere chiri pakati nepakati kana chakakomba, kana ukatevera marapirwo akanyorwa (kuwedzerwa ropa uye kubviswa kwesimbi) chaizvo, une mukana wakanaka wekurarama hupenyu hurefu uye hune hutano . Chirwere chemwoyo ndicho chinhu chikuru chinokonzera njodzi yerufu. Saka, zvakakosha kuti ubvise simbi pasina kusvetuka.

Chirwere ichi chinogona kudzivirirwa here? Uye kutarisirwa kuri kudiwa nguva dzose

Thalassemia chirwere chinokonzerwa nemajini, saka hatigone kudzivirira kuti chisaitike. Zvisinei, kuongororwa kwemajini kunogona kukubatsira kuona kana iwe kana mumwe wako muri mutakuri wemajini ethalassemia. Kana uchironga kuva nemwana, zvakakosha kuziva ruzivo urwu. Kuti uwane rumwe ruzivo, ona mupi wezano remajini kana chiremba wako.

Kana uine thalassemia, uchafanirwa kuongororwa ropa nguva dzose (CBC) uye kuongororwa kwehuwandu hwesimbi. Chiremba wako anogonawo kukurudzira kuti uongororwe mashandiro emwoyo wako nechiropa kanenge kamwe chete pagore.

Mharidzo Yekuenda Nayo Kumba

  • Thalassemia haisi chirwere chinotapuriranwa, chirwere chemajini chinogarwa nhaka kubva kuvabereki.
  • Chirwere ichi chinogona kubva pakuva nechirwere chisina zviratidzo kusvika pakuva nechirwere chakakomba chinoda kurapwa nguva dzose.
  • Kuti varwere vane thalassemia major vararame hupenyu hurefu uye hune hutano, kuwedzerwa ropa nguva dzose uye kurapwa nekubvisa iron kwakakosha.
  • Kana mumhuri menyu muine nhoroondo ye thalassemia, zvakanaka kutaura nachiremba wako nezvazvo uye kuongororwa majini usati wava nemwana.
  • Usaregeredza zviratidzo zvakaita sekuneta uye kucheneruka. Gara uchitsvaka rubatsiro rwechiremba.

Thalassemia, Anemia, Hemoglobin, Kupa ropa, Kuwedzerwa ropa, Zvirwere zvemajini
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Zvinhu zvaunofanira kuziva nezveThalassemia: Ngatitaurei nezvazvo zviri nyore
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Zvinhu zvaunofanira kuziva nezveThalassemia: Ngatitaurei nezvazvo zviri nyore

Unogara uchinzwa kuneta uye kuneta here? Pamwe ganda rako rakachenuruka zvishoma? Izvi hazvisi zvinhu zvisina kurongeka, pamwe kupererwa neropa uku, kureva kushomeka kweropa, kunogona kunge kuri nekuda kweizvi. Nhasi tiri kutaura nezve 'Thalassemia', chirwere chekuzvarwa nacho chine chekuita neropa, chinowanzoonekwa nevanhu vazhinji munyika medu. Usatya kana ukanzwa zita iri. Ngatinzwisise zvese nezveizvi zviri nyore.

Chii chinonzi Thalassemia chaizvo?

Zvichitaurwa zviri nyore, thalassemia chirwere cheropa chinogarwa nhaka chinogarwa nhaka kubva pakuzvarwa . Hachisi chirwere chinotapukira. Chirwere ichi chinodzivirira miviri yedu kugadzira hemoglobin yakakwana ine hutano.

Zvino ungave uchishamisika kuti hemoglobin chii. Hemoglobin ipuroteni yakakosha inowanikwa mukati memasero edu matsvuku eropa. Inoshanda se 'sevhisi yekuendesa' inotakura okisijeni mumiviri yedu yese. Iyi package inonzi hemoglobin inoendeswa kumasero ese mumuviri nemotokari dzinonzi masero matsvuku eropa.

Munhu ane thalassemia ane hemoglobin shoma mumuviri wake. Nokudaro, huwandu hwemasero matsvuku eropa ane hutano mumuviri hunodererawo. Iyi mamiriro emasero matsvuku eropa akaderera ndiyo yatinodaidza kuti anemia , kana kuti 'kushomeka kweropa'. Kana masero emuviri asingagamuchire okisijeni yaanoda, zviratidzo zvakasiyana-siyana zvinotanga kuoneka.

Izvi zvinoreva kuti unganzwa zvinhu zvakaita seizvi:

  • Kunzwa kuneta zvakanyanya uye kuneta nguva dzose.
  • Kutadza kufema zvakanaka.
  • Kunzwa kutonhora.
  • Kunzwa dzungu.
  • Ganda rakachenuruka.

Chii chinokonzera thalassemia? Ndiani ari panjodzi huru?

Thalassemia inokonzerwa nekusakwana kwemajini edu. Funga nezvemajini aya se 'programu code' ine mirairo yekuti zvese zviri mumuviri wedu zvinofanira kuumbwa sei. Puroteni yehemoglobin inoumbwa zvichienderana nemirairo inobva kumajini aya. Kana paine chisina kunaka nemirairo iyi, kana chikamu chayo chisipo, muviri haugone kugadzira hemoglobin ine hutano. Tinogara nhaka majini aya asina kunaka kubva kuvabereki vedu. Ndosaka ichinzi chirwere chinogarwa nhaka.

Molekyumu yehemoglobin inoumbwa nemacheni mana eprotein: macheni maviri ealpha globin uye macheni maviri ebeta globin.

  • Majini mana anodiwa kuti pave ne alpha globin chains (maviri kubva kumubereki mumwe nemumwe).
  • Majini maviri anodiwa kuti pave ne beta globin chains (rimwe kubva kumubereki mumwe nemumwe).

Kana paine chikanganiso mumajini anogadzira aya ma alpha kana beta chains, thalassemia inoitika. Kuoma kwechirwere kunotsanangurwa nehuwandu hwemajini asina chikanganiso.

Zvinotendwa kuti kuchinja kwemajini uku kwakabva senzira yekudzivirira malaria, kunyanya munzvimbo dzakadai seAfrica, Southern Europe, neAsia (kusanganisira nyika yedu), uko malaria yaive yakawanda munhoroondo. Nokudaro, thalassemia inowanzoonekwa pakati pevanhu vari munzvimbo idzi.

Ndeapi marudzi makuru e thalassemia?

Thalassemia inogona kukamurwa kuita mazinga akasiyana-siyana zvichienderana nekuoma kwechirwere. Kureva kuti, inogona kubva pakuva isina zviratidzo zvechirwere (hunhu), kusvika kudiki, pakati, uye huru. Chimiro chakanyanya kuoma, Thalassemia Major, chinowanzoda kurapwa nguva dzose.

Thalassemia yakakamurwa kuita mhando mbiri huru, zvichienderana nekuti chikanganiso chemajini chiri mumaketani ealpha kana beta.

1. Alpha Thalassemia

2. Beta Thalassemia

Ngatinzwisisei mhando mbiri idzi zvakadzama kubva patafura iri pazasi.

Rudzi rweThalassemia Kupesvedzera kwemajini Hunhu uye zviratidzo zvechirwere
Alpha Thalassemia
Kukanganisa mune rimwe jini Kukanganisa kuri mu 1 yemajini mana e alpha globin. Hapana zviratidzo. Kazhinji vanhu ava vanongotakura chirwere ichi.
Zvikanganiso zviviri zvemajini Kukanganisa kuri mumajini maviri e alpha globin mana. Ungave usina zviratidzo zvechirwere ichi, kana kuti ungaratidza zviratidzo zvishoma zvekushaya ropa (sekuneta kudiki).
Zvikanganiso zvitatu zvemajini (chirwere cheHemoglobin H) Kukanganisa mumajini matatu kubva mana ealpha globin.Zviratidzo zvinosiyana kubva pakati nepakati kusvika pakanyanya. Kushaya ropa kunoramba kuripo kweupenyu hwese.
Kukanganisa kwemajini ese mana Majini ese mana ealpha globin haana kunaka. Dambudziko guru. Kazhinji mwana anofira mudumbu kana nguva pfupi mushure mekuzvarwa.
Beta Thalassemia
Kukanganisa mune rimwe jini (Beta thalassemia minor) Kukanganisa kuri mu 1 yemajini maviri e beta globin. Zviratidzo zvekushaya ropa zvishoma zvinoonekwa. Vanhu vazhinji vanorarama hupenyu hune hutano sevatakuri vechirwere ichi.
Kusakwana kwemajini ese ari maviri (Beta thalassemia major / Cooley's Anemia) Majini ese ari maviri e beta globin haana kunaka. Zviratidzo zvinosiyana kubva pakati kusvika pakukura. Dambudziko rakanyanya kuoma rinonzi Cooley's anemia uye rinoda kurapwa nguva dzose.

Ndezvipi zviratidzo zvinogona kuitika zve thalassemia?

Zviratidzo zvaunoona zvinoenderana nerudzi rwe thalassemia yaunayo uye kuoma kwayo.

Nyaya dzisina zviratidzo

Kana uine kanganiso ke alpha gene kamwe chete kana chirwere chisina kunyanya kuipa se beta thalassemia minor, ungasava nezviratidzo zvachose . Kana kuti unganzwa kuneta kushoma.

Zviratidzo zvinyoro uye zvine mwero

Muzviitiko zvisina kunyanya kuoma, zvakaita se beta thalassemia intermedia, pamusoro pezviratidzo zvisina kunyanya kuoma kweropa, zvinotevera zvinogona kuitika:

  • Kukura zvishoma nezvishoma kwevana.
  • Kunonoka kuyaruka.
  • Kusashanda zvakanaka kwemapfupa (semuenzaniso, osteoporosis).
  • Kukura kwetsvina (iyi inhengo inorwisa hutachiona).

Zviratidzo zvakakomba

Mumamiriro ezvinhu akaomarara, akadai sekukanganisa kwemajini matatu ealpha (chirwere cheHemoglobin H) kana beta thalassemia major (Cooley's anemia), zviratidzo zvinoonekwa mwana asati asvitsa makore maviri. Kuwedzera kune zviratidzo zvataurwa pamusoro apa, zvinotevera zvinogona kuonekwa:

  • Kurasikirwa nechido chekudya.
  • Ganda rakachenuruka kana kuti rakatsvuka (senge jaundice).
  • Weti yakasviba, yakaita setii .
  • Kukura kusina kujairika kwemapfupa echiso.

Nzira yekuziva chirwere ichi nemazvo sei?

Thalassemia iri pakati nepakati uye yakanyanya inowanzoonekwa muhudiki. Izvi zvinodaro nekuti zviratidzo zvinotanga kuoneka mukati memakore maviri ekutanga ehupenyu hwemwana. Chiremba wako anogona kuraira kuongororwa kweropa kwakasiyana-siyana kuti aone chirwere chacho.

  • Kuverengwa Kweropa Kwakakwana (CBC): Izvi zvinoyera huwandu hwemasero matsvuku eropa, saizi yawo, uye mazinga ehemoglobin. Vanhu vane thalassemia vane masero matsvuku mashoma ane hutano, uye vanogona kunge vari madiki pakukura.
  • Kuongororwa kwehuwandu hwesimbi: Kuongororwa uku kwakakosha kusiyanisa pakati pekushaikwa kwesimbi nethalassemia.
  • Hemoglobin Electrophoresis: Bvunzo iyi inoshandiswa zvakananga kuongorora beta thalassemia.
  • Kuongororwa kwemajini: Miedzo iyi inoshandiswa kusimbisa alpha thalassemia uye kuona vatakuri vechirwere ichi.

Ndeipi mishonga yekurapa thalassemia?

Nzira dzekurapa dzinoenderana nekuoma kwechirwere. Kazhinji kacho, zvirwere zvishoma hazvidi kurapwa. Zvisinei, kune nzira dzakawanda dzekurapa zvirwere zvakakomba.

  • Kuisirwa Ropa: Zvichitaurwa zviri nyore, 'kupa ropa' . Ropa rinobva kumunhu ane hutano rinopihwa murwere kuburikidza netsinga kuti masero matsvuku eropa uye hemoglobin idzorerwe. Varwere vane beta thalassemia major vanoda kuwedzerwa ropa nguva dzose, kazhinji mavhiki maviri kusvika mana ega ega.
  • Kurapa neIron Chelation: Kuwedzerwa ropa kakawanda kunogona kukonzera kuwedzera kwesimbi mumuviri. Izvi zvinonzi 'iron overload'. Iyi iron yakawandisa inogona kukuvadza nhengo dzakadai semwoyo nechiropa. Saka, mishonga inobvisa iyi iron yakawandisa mumuviri inonzi 'iron chelation'. Iyi inogona kutorwa muchimiro chemapiritsi.
  • Zvikafu zveFolic Acid: Folic acid inopihwa kubatsira muviri kugadzira masero eropa ane hutano.
  • Kudyara Bone Morrow: Uku ndiko chete kurapwa kunogona kurapa thalassemia zvizere . Zvisinei, kuvhiyiwa kune njodzi uye kwakaoma. Izvi zvinoda mupi ane hutano anonyatsoenderana nemurwere, kazhinji munin'ina kana hanzvadzi.

Dzidza nezvematambudziko, kurapwa, uye hupenyu hwese.

Kana zvikasarapwa zvakanaka, dambudziko guru kukuvara kwemoyo, chiropa, uye mahormone anogadzira mahormone, kunyanya nekuda kwekuwandisa kwesimbi mumuviri. Saka, sezvakarairwa.Kurapa ne iron chelation kwakakosha zvikuru.

Kunyangwe chirwere ichi chichigona kurapwa nekuisirwa bota remapfupa, havasi vese vanogona kurapwa nekuda kwekuoma kwekuwana mupi akakodzera uye njodzi dzekuvhiyiwa kwacho.

Panyaya yehupenyu hunotarisirwa, kana uine thalassemia minor, unogona kutarisira hupenyu hunotarisirwa zvakajairika. Kunyangwe uine chirwere chiri pakati nepakati kana chakakomba, kana ukatevera marapirwo akanyorwa (kuwedzerwa ropa uye kubviswa kwesimbi) chaizvo, une mukana wakanaka wekurarama hupenyu hurefu uye hune hutano . Chirwere chemwoyo ndicho chinhu chikuru chinokonzera njodzi yerufu. Saka, zvakakosha kuti ubvise simbi pasina kusvetuka.

Chirwere ichi chinogona kudzivirirwa here? Uye kutarisirwa kuri kudiwa nguva dzose

Thalassemia chirwere chinokonzerwa nemajini, saka hatigone kudzivirira kuti chisaitike. Zvisinei, kuongororwa kwemajini kunogona kukubatsira kuona kana iwe kana mumwe wako muri mutakuri wemajini ethalassemia. Kana uchironga kuva nemwana, zvakakosha kuziva ruzivo urwu. Kuti uwane rumwe ruzivo, ona mupi wezano remajini kana chiremba wako.

Kana uine thalassemia, uchafanirwa kuongororwa ropa nguva dzose (CBC) uye kuongororwa kwehuwandu hwesimbi. Chiremba wako anogonawo kukurudzira kuti uongororwe mashandiro emwoyo wako nechiropa kanenge kamwe chete pagore.

Mharidzo Yekuenda Nayo Kumba

  • Thalassemia haisi chirwere chinotapuriranwa, chirwere chemajini chinogarwa nhaka kubva kuvabereki.
  • Chirwere ichi chinogona kubva pakuva nechirwere chisina zviratidzo kusvika pakuva nechirwere chakakomba chinoda kurapwa nguva dzose.
  • Kuti varwere vane thalassemia major vararame hupenyu hurefu uye hune hutano, kuwedzerwa ropa nguva dzose uye kurapwa nekubvisa iron kwakakosha.
  • Kana mumhuri menyu muine nhoroondo ye thalassemia, zvakanaka kutaura nachiremba wako nezvazvo uye kuongororwa majini usati wava nemwana.
  • Usaregeredza zviratidzo zvakaita sekuneta uye kucheneruka. Gara uchitsvaka rubatsiro rwechiremba.

Thalassemia, Anemia, Hemoglobin, Kupa ropa, Kuwedzerwa ropa, Zvirwere zvemajini
⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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