Ngaba wakha weva ngomntu oselula, osempilweni, nowezemidlalo ofa ngequbuliso ngenxa yokuhlaselwa yintliziyo? Kubuhlungu ngokwenene. Uninzi lwexesha, sicinga ngesifo sentliziyo njengento eyenzekayo ngokuhamba kweminyaka. Kodwa ngamanye amaxesha, unobangela wezi ziganeko zingaqhelekanga kakhulu esingazaziyo. Namhlanje, siza kuthetha ngesifo sentliziyo esinjalo esinokuchaphazela abantu abaselula ngokukodwa. Le yi-ARVC.
Yintoni kanye kanye i-ARVC?
Ngamafutshane, i-ARVC sisifo sentliziyo esingaqhelekanga esizuzwe njengelifa ngokwemfuza , oko kuthetha ukuba sinokudluliselwa kwizizukulwana ngezizukulwana. Okwenzekayo kukuba izihlunu ezintliziyweni zethu zonakale.
Cinga ngentliziyo yethu njengepompo enamandla eyenziwe ngamagumbi amane. Yile nto ipompa igazi emzimbeni wonke. Kula magumbi mane, elikwicala lasekunene elisezantsi libizwa ngokuba yiRight Ventricle. Kwi-ARVC, iiseli zemisipha yentliziyo ezisempilweni kule ventricle yasekunene ziyafa kwaye zithatyathelw’ indawo ngamafutha kunye nezicubu ezine-fibrous (izicubu zesilonda) .
Kufana nesitena esiwa eludongeni oluhle kwaye izithuba zigcwala ludaka. Kwenzeka ntoni? Udonga lwelo gumbi lentliziyo luba buthathaka, lube buthathaka, kwaye lunwebeke. Emva koko alukwazi ukufinyela kakuhle kwaye lupompe igazi. Oku kunokubangela izinto ezifana nokuphefumla okufutshane kunye nokuquleka.
Okuyingozi nangakumbi kukuba amafutha asandul’ ukwakheka kunye nezicubu ezibomvu ziphazamisana nemiqondiso yombane entliziyweni. Oku kubangela ukuba intliziyo ibethe ngendlela engaqhelekanga. Oku sikubiza ngokuba yi-arrhythmia . Le yeyona meko iyingozi kakhulu kwesi sifo. Kuba inokubangela ukuminya kwentliziyo ngequbuliso kwanokufa.
Esi sifo sikwabizwa ngokuba yi-ARVC, i-Arrhythmogenic Right Ventricular Dysplasia (ARVD). Ngamanye amaxesha sikwabizwa ngokuba yi-Arrhythmogenic Cardiomyopathy (ACM) kuba sichaphazela ne-ventricle yasekhohlo.
Zithini iimpawu zale meko?
Ingxaki enye ngesi sifo kukuba sinokuba singabonakali kwasekuqaleni. Iimpawu zihlala ziqala ukubonakala ngaphambi kokuba zifikelele kwiminyaka engama-40, ngamanye amaxesha kwanakwiminyaka yokukhula.
Eyona nto yoyikisayo kukuba kwabanye abantu, uphawu lokuqala nolokuphela kwalo olubabonisa ukuba banale sifo kukufa ngesiquphe kwentliziyo.
Ngoko ke, kubaluleke kakhulu ukuqaphela ezi mpawu zilandelayo.
| Uphawu | Ingcaciso elula |
|---|---|
| Ukungahambi kakuhle kwentliziyo (iiArrhythmias) | Utshintsho olungaqhelekanga kwisantya sentliziyo. Ingavakala ngathi kukushukuma okanye ukucinezelwa esifubeni. Ingakumbi kwiimeko ezifana ne -Atrial Fibrillation . |
| Ukudinwa okanye ukuquleka | Kufana nokulahlekelwa zingqondo kuba ingqondo ayifumani gazi laneleyo. |
| Ukudinwa | Ndihlala ndiziva ndidiniwe kakhulu kuba umzimba awumpompi igazi kakuhle. |
| Iintlungu zesifuba | Intlungu yesifuba ngenxa yoxinzelelo entliziyweni. |
| Ubunzima bokuphefumla | Ukuphefumla nzima okubangelwa kukungabikho kwegazi elaneleyo emiphungeni. |
| Ukudumba komzimba | Ukudumba emilenzeni, emaqatheni, ezinyaweni, okanye esiswini. |
| Ukumelwa yintliziyo | Ekuhambeni kwexesha, amandla okupompa kwentliziyo aphantse abe buthathaka ngokupheleleyo. |
Izizathu kunye nelifa le-ARVC
Amaxesha amaninzi, i-ARVC ibangelwa lutshintsho lwemfuza . Le yimpazamo encinci kwi-blueprint, okanye ii-genes, ezenza iiseli zomzimba wethu. Le meko yenzeka xa kukho iimpazamo kwii-genes ezichaphazela iiproteni ezinceda ukugcina iiseli zemisipha yentliziyo zidibene.
Xa olu nxibelelwano lubuthathaka, iiseli zemisipha yentliziyo ziqala ukwahlukana zize zife. Oku kunokwenzeka ingakumbi ngamaxesha oxinzelelo entliziyweni, njengakwixesha lokuzilolonga.
Malunga nesiqingatha sezigulane ze-ARVC zinembali yentsapho yale meko. Oku kuthetha ukuba kukho imbali yemfuza .
Ngoko ke, ukuba kukho umntu kusapho lwakho ofunyaniswe ene-ARVC, kubaluleke kakhulu ukuba izalamane ezisondeleyo zaloo mntu (abazali, abantakwabo, abantwana, abazukulwana, oomalume, oomalume, abatshana, abatshana) zihlolwe ngugqirha. Nokuba akukho zimpawu, kwanabo baselula kufuneka babone ugqirha baze bathethe ngale nto.
Kukho iindlela ezimbini eziphambili zokusasazwa kwe-ARVC kwizizukulwana ngezizukulwana:
- I-Autosomal Dominant: Olu lolona hlobo luqhelekileyo. Oku kuthetha ukuba omnye wabazali une-gene mutation. Emva koko umntwana wabo unethuba elingama-50% lokufumana esi sifo njengelifa. Nangona kunjalo, iimpawu kunye nobudala bokuqala kwesi sifo zinokwahluka phakathi kwamalungu osapho.
- I-Autosomal Recessive: Oku kunqabile kancinci. Apha, bobabini abazali banotshintsho lwezakhi zofuzo, kodwa abanazo iimpawu. Umntwana wabo unethuba elingama-25% lokufumana esi sifo. Esinye sezizathu ezinxulumene noku sisifo iNaxos , esinokubangela ukuqina kolusu ezintendeni nasezinyaweni kunye nokukhula kweenwele ezinde, ezinjengoboya.
Indlela yokuxilonga esi sifo?
Ugqirha unokuxilonga i-ARVC ngokusekelwe kwiimpawu zakho, imbali yosapho, kunye novavanyo lwezonyango olumbalwa. Kukho iindlela ezahlukeneyo zokuxilonga i-ARVC. Oogqirha bajonga ukuba zingaphi kwezi ndlela ozifikelelayo.
Amanqaku aphambili anikwa ingqalelo ngoogqirha:
- Ukujonga ukusebenza okungaqhelekanga kwe-ventricular yasekunene (Uvavanyo lwe -Echocardiogram okanye lwe-MRI lusetyenziselwa oku).
- Ukubona ukuba kukho na izicubu ezinamafutha okanye ezibomvu kwimisipha yentliziyo (i- MRI ibaluleke kakhulu koku).
- Ukujonga iingxaki kuvavanyo lwe-ECG ( i-Electrocardiogram - ECG/EKG ).
- Ukungahambi kakuhle kwesingqisho sentliziyo, ingakumbi ngexesha lokuzilolonga.
- Nokuba kukho nabani na kusapho one-ARVC.
Ngokusekelwe kwezi zinto, ugqirha uya kugqiba ukuba "ngokuqinisekileyo" unesifo, "mhlawumbi" unaso, okanye "mhlawumbi" unaso. Banokukuthumela kuvavanyo lwemfuza ukuba kuyimfuneko.
Ezinye iimvavanyo ezisetyenzisiweyo:
- I-Cardiac Computed Tomography (CT ) scan yentliziyo
- Uvavanyo lwe-ECG ngexesha lokuzilolonga ( Uvavanyo loxinzelelo )
- Ukufunda umsebenzi wombane wentliziyo ( Uvavanyo lwe-Electrophysiology )
- Ukuthatha iqhekeza elincinci lomsipha wentliziyo ukuze lihlolwe ( iBiopsy )
Ziziphi iindlela zonyango ze-ARVC?
Ngelishwa, akukho nyango lwe-ARVC. Nangona kunjalo, kukho unyango oluninzi olusebenzayo olunokukunceda ukulawula iimpawu zakho, uthintele iingxaki eziyingozi, kwaye uphile ubomi obuqhelekileyo. Injongo ephambili kagqirha wakho kukulawula isingqisho sentliziyo kunye neemeko zentliziyo.
| Indlela yonyango | Kwenzekani? |
|---|---|
| Amayeza | Amayeza okulwa nokubetha kwentliziyo , ii-beta-blockers , kunye ne -anticoagulants zinikwa ukuthintela ukungahambelani kwesantya sentliziyo. |
| Ukususwa kweCatheter | Ukuba uneentliziyo ezibetha ngokungalungelelananga ezingenakulawuleka ngamayeza, inkqubo etshisa iindawo zentliziyo apho kuvela khona imiqondiso yombane engaqhelekanga. |
| Isixhobo se-ICD (Implantable Cardioverter-Defibrillator) | Olu lolunye lonyango olubaluleke kakhulu. Kubantu abasengozini enkulu yokufa ngenxa yokuma kwentliziyo ngequbuliso, isixhobo esincinci sifakwa phantsi kwesikhumba sesifuba. Xa kuvela ingxaki yentliziyo eyingozi, esi sixhobo senza umbane ubuyisele intliziyo esiqhelweni. |
| Ukufakelwa kwentliziyo | Kuthathwa njengenyathelo lokugqibela ukuba zonke ezinye iindlela zonyango aziphumeleli, kodwa uninzi lwabantu abane-ARVC akufuneki bahambe umgama ongako. |
Izinto ekufuneka uziqwalasele xa uphila ne-ARVC
Wakuba ufunyenwe une-ARVC, kuya kufuneka wenze utshintsho oluthile kwindlela ophila ngayo. Ezi zinto zinokunceda ekunciphiseni uxinzelelo entliziyweni yakho.
- Nciphisa umthambo: I-ARVC inokwenziwa mandundu ngokuzilolonga. Ke ngoko, unokufuna ukuyiphepha imidlalo yokhuphiswano ngokupheleleyo. Qiniseka ukuba uthetha nogqirha wakho malunga nobungakanani kunye nohlobo lomthambo onokuwenza yonke imihla.
- Indlela yokuphila enempilo: Kubaluleke kakhulu ukunciphisa ukusetyenziswa kotywala, ukuphepha ukutshaya, ukutya ukutya okunesondlo, kunye nokunciphisa iziselo ezine-caffeine (ikofu, iti).
- Sela amayeza akho njengoko uyalelwe: Ungaze ulibale ukuthatha amayeza owalelwe ngugqirha wakho.
- Ukuhlolwa rhoqo kwezonyango: Kuya kufuneka ubone ugqirha wakho ubomi bakho bonke . Ukuba une-ICD, kuya kufuneka uyihlolwe rhoqo .
Ukufumanisa ukuba unesifo sentliziyo kunokuba yinto enzima kakhulu ukujongana nayo, ingakumbi xa usemncinci. Ukuba ungumdlali wezemidlalo, kunokuba lusizi ukuyeka loo nto. Kodwa khumbula, ubomi bakho buxabiseke kakhulu. Ngonyango olufanelekileyo nendlela yokuphila, ungaphila ubomi obuhle.
Umyalezo Wokuya Ekhaya
- I-ARVC yimeko engaqhelekanga, efunyanwa njengelifa echaphazela kakhulu icala lasekunene lentliziyo.
- Eyona nto iyingozi ngesi sifo kukoyika ukumiwa yintliziyo ngesiquphe nokufa ngaphandle kwempawu.
- Ukuba ufumana iimpawu ezinje ngokuxinana kwesifuba, isiyezi, okanye ubunzima bokuphefumla, bonana nogqirha ngokukhawuleza.
- Ukuba kukho umntu kusapho lwakho one-ARVC, ngokuqinisekileyo kufuneka uhlolwe ngugqirha.
- Nangona esi sifo singenakunyangwa ngokupheleleyo, sinokulawulwa ngempumelelo kwaye siphile kakuhle ngamayeza, izixhobo ze-ICD, kunye notshintsho kwindlela yokuphila.
- Kubaluleke kakhulu ukuba aba baguli baphephe ukwenza umthambo onzima nokhuphisanayo.
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