Ngaba ugqirha wakho ukunike wena okanye umntu kusapho lwakho iyeza elibizwa ngokuba yiGlycerol Phenylbutyrate? Liyeza elinegama elingaqhelekanga, ngoko usenokuba nemibuzo emininzi ngalo. Ungakhathazeki, namhlanje siza kuthetha nje ngeli yeza, into eliyenzayo, indlela yokulisebenzisa, kunye nezinto ekufuneka uzilumkele.
Kalula nje, yintoni le yeza?
IGlycerol Phenylbutyrate (ekwaziwa ngegama lophawu iRAVICTI) liyeza elisetyenziselwa ukulawula ubungakanani be -ammonia egazini labantu abaneengxaki zomjikelezo we-urea .
Cinga nje, xa imizimba yethu isebenzisa iproteni, ivelisa i-ammonia njengenkunkuma. Kumntu ophilileyo, umjikelo we-urea uguqula le ammonia ibe yi-urea engenabungozi kwaye uyikhuphe emchameni. Kodwa kumntu onengxaki yomjikelo we-urea, umzimba awukwazi ukwenza lo msebenzi ngokufanelekileyo. Emva koko, i-ammonia inokuqokelelana emzimbeni ize yonakalise ingqondo kunye nenkqubo yemithambo-luvo.
Eli yeza linceda ekususeni i-ammonia egqithisileyo emzimbeni. Kodwa kukho into enye ekufuneka ikhunjulwe. Eli asiloyeza eliphilisa ngokupheleleyo isifo. Eli liyeza elinceda kuphela ekulawuleni isifo.
Ngokwesiqhelo, xa unikwa eli yeza, kuya kufuneka ulandele ukutya okukhethekileyo okuneproteni ephantsi okumiselwe ngugqirha wakho, kwaye mhlawumbi uthathe izongezo zokutya ezongezelelweyo.
Izinto ekufuneka uzixelele ugqirha wakho ngaphambi kokuba uthathe amayeza
Ngaphambi kokuba uqale eli yeza, kubalulekile ukuxelela ugqirha wakho olu lwazi lulandelayo. Musa ukuzifihla ezi zinto, kuba zibaluleke kakhulu kukhuseleko lwakho.
| Imeko ekufuneka uyixele | Kutheni oko kubalulekile? |
|---|---|
| Iingxaki zamathumbu | Umzimba unokuchaphazeleka kukufunxwa kwamayeza. |
| Isifo sezintso, isibindi okanye i-pancreatic | Ekubeni iyeza likhutshwa emzimbeni ngeli lungu, idosi ingadinga ukulungiswa ukuba kukho iimeko zempilo. |
| Ii-aleji | Qiniseka ukuba uxelela ugqirha wakho ukuba unayo nayiphi na i-allergies kweli yeza, amanye amayeza, ukutya, izithinteli, okanye imibala. |
| Ukuba ukhulelwe okanye uzama ukukhulelwa | Ufanele uthethe nogqirha wakho malunga nokuba amayeza aza kuyichaphazela na imveku esibelekweni. |
| Ukuba umntwana uncanciswa | Buza ugqirha wakho malunga nokuba iyeza lidluliselwa na kumntwana ngobisi lwebele. |
Ndingayisebenzisa njani kanye kanye le yeza?
Eli yeza liza ngendlela yesisombululo esithathwa ngomlomo, ngoko ke ziqaphele ezi zinto.
- Yisele ngomlomo: Eli liyeza eliselwa ngomlomo.
- Linganisa ngokuchanekileyo: Sebenzisa icephe, ikomityi, okanye isirinji ekhethekileyo eza neyeza ukuyilinganisa . Musa ukusebenzisa iitisipuni eziqhelekileyo ekhaya, kuba azichanekanga kakhulu.
- Yithathe nokutya: Kungcono ukuyithatha le yeza kunye nokutya okanye, kwiintsana, kunye nefomyula .
- Yithathe ngexesha: Thatha amayeza ngexesha elimiselweyo, ngamaxesha athile amiselweyo, njengoko ugqirha wakho ekuyalele. Musa ukuthatha ngaphezu komlinganiselo omiselweyo.
- Musa ukuyeka: Musa ukuyeka ukuthatha amayeza ngequbuliso ngaphandle kwengcebiso kagqirha.
- Xa inikwa abantwana: Eli yeza ngamanye amaxesha linikwa neentsana ezisandul’ ukuzalwa. Nangona kunjalo, kukho amanyathelo akhethekileyo okhuseleko ekufuneka alandelwe. Ke ngoko, thetha nogqirha wezingane malunga noku ngononophelo kwaye ufumane ingcebiso.
Kuthekani ukuba umthamo weyeza unyusiwe (umthamo ogqithisileyo)?
Ukuba ucinga ukuba uthathe amayeza amaninzi kakhulu, into yokuqala ekufuneka uyenze kukufowunela iZiko loLwazi lweePoison kwiSibhedlele sikaZwelonke saseColombo . Okanye uye kwiYunithi yoNyango oluNgxamisekileyo (ETU) yesibhedlele esikufutshane. Musa ukulibazisa oku.
Yintoni omawuyenze ukuba uphoswe yidosi yeyeza?
Ukuba ulibele ukuthatha idosi, yithathe kwangoko xa ukhumbula. Nangona kunjalo, ukuba sele kusondele ixesha lokusebenzisa idosi yakho elandelayo, yitsibe idosi oyiphosileyo uze uthathe idosi yakho elandelayo ngexesha elicwangcisiweyo. Musa ukuthatha iidosi ezimbini ngaxeshanye nangasiphi na isizathu.
Ezinye izinto ezinokusebenzisana nale mithi
Amanye amayeza owasebenzisayo asenokudibana nalo mayeza, ngoko ke xelela ugqirha wakho ngawo onke amayeza owasebenzisayo (kuquka iivithamini, amayeza esintu, kunye nezongezo).
| Iintlobo zeziyobisi ezinokubangela iingxabano (imizekelo) |
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| Qaphela: Olu luhlu aluphelelanga. Xelela ugqirha wakho ukuba uyatshaya, usela utywala, okanye usebenzisa ezinye iziyobisi. |
Iziphumo ebezingalindelekanga ezinokubakho zokuthatha iyeza
Njengalo naliphi na iyeza, eli linokubangela iziphumo ebezingalindelekanga. Ezinye zinzima, ezinye ziqhelekile.
| Iziphumo ebezingalindelekanga ekufuneka uzixele kugqirha wakho ngoko nangoko |
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| Iziphumo ebezingalindelekanga ekufuneka zixelwe kugqirha ukuba ziyaqhubeka okanye ziyakhathaza |
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Ukuba ufumana naziphi na ezinye iimpawu ezingaqhelekanga ezingakhankanywanga kolu luhlu, thetha nogqirha wakho ngazo.
Ndingaligcina njani iyeza?
- Gcina kude nabantwana.
- Gcina kubushushu begumbi, phakathi kwama-20 nama-25 degrees Celsius (68-77 Fahrenheit).
- Lahla amayeza aphelelwe lixesha.
Umyalezo Wokuya Ekhaya
- I-Glycerol Phenylbutyrate ayisiyo iyeza elinyanga iingxaki zomjikelo we-urea, liyeza elinceda ukulawula amanqanaba e-ammonia egazini.
- Soloko usela eli yeza kunye nokutya, usebenzisa indebe yokulinganisa ekhethekileyo eza nalo.
- Landela ukutya okuneproteni ephantsi okuchazwe ngugqirha wakho ngokuchanekileyo.
- Musa ukuyeka ukuthatha amayeza ngaphandle kwengcebiso kagqirha wakho.
- Ukuba usela amayeza amaninzi okanye ufumana iziphumo ebezingalindelekanga ezinzulu, funa ingcebiso kagqirha ngokukhawuleza.
- Xelela ugqirha wakho ngazo zonke ezinye iindlela ozithathileyo (kuquka iivithamini kunye namayeza esintu).
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