Ake sifunde ngokuhlolwa kokujuluka ukuze sibone ukuthi une-cystic fibrosis.

Ingabe ingane yakho encane ngezinye izikhathi iba nobunzima bokuphefumula, noma inkinga yokungakhuluphali? Noma ingabe uyayibona into efana nokukhwehlela okuqhubekayo noma umsindo wokuphefumula esifubeni? Ngezinye izikhathi, ngemuva kwalezi zinto, kungase kube nesifo esingakazwa kakhulu ngaso, kodwa kubaluleke kakhulu ukuqaphela. Yilokho esizokhuluma ngakho namuhla. Lokhu kubizwa ngokuthi i-Cystic Fibrosis , ngezinye izikhathi okufingqiwe ngokuthi (CF) . Ake sibone ukuthi kuyini, kutholakala kanjani, futhi ikakhulukazi imininingwane ethile mayelana 'nokuhlolwa kokujuluka' okwenziwa kulokhu.

Iyini ngempela i-Cystic Fibrosis?

Kalula nje, i-cystic fibrosis yisifo esizuzwe njengefa . Okusho ukuthi, kuyinto engadluliselwa kusuka kubazali iye ezinganeni. Okwenzekayo kulokhu ukuthi ezinye zeziphuzo ezingaphakathi emizimbeni yethu, ikakhulukazi i-mucus, ziba zijiyile futhi zinamathele. Cabanga ngakho, ingabe i-mucus emaphashini nasema-sinuses omuntu ophilile ayisheleli njengamanzi? Yilokho okugcina izindlela zethu zokuphefumula zihlanzekile futhi kususe amagciwane.

Kodwa kubantu abane-cystic fibrosis, le mucus ijiyile kakhulu, njengeglue. Ngakho-ke le mucus ijiyile ifakwa ezithweni ezibalulekile njengamaphaphu kanye ne-pancreas , okuphazamisa ukusebenza kwazo okuvamile. Ikakhulukazi uma le mucus inqwabelana emaphashini, imigudu yomoya iqala ukuvaleka. Bese kuba nzima kakhulu ukuphefumula, futhi izifo zingavela njalo. Uma i-pancreas ithintekile, izinkinga zokugaya ukudla kanye nokungondleki kahle kungenzeka. Hhayi lokhu kuphela, kungathinta nezindawo ezifana nesibindi, amathumbu, kanye nezitho zangasese.

I-cystic fibrosis yisifo esingamahlalakhona . Lokhu kusho ukuthi sihlala isikhathi eside futhi asinakwelapheka ngokuphelele. Siphinde sibhekwe njengesifo esiqhubekayo . Lokhu kusho ukuthi izimpawu zingase ziqhubeke kancane kancane ngokuhamba kwesikhathi futhi kungase kube nezinkinga. Yingakho kubaluleke kakhulu ukuyibona kusenesikhathi futhi uyiphathe kahle.

Ziyini izimpawu zalokhu ezinganeni?

Uma ingane encane, ikakhulukazi usana, ine-cystic fibrosis, ingase ibhekane nesinye noma ngaphezulu salezi zimpawu. Akuzona zonke izingane ezizoba nazo zonke lezi zimpawu ngesikhathi esisodwa, futhi ubukhulu bezimpawu bungahluka kuye ngengane. Kubalulekile ukukhumbula lokho.

Nazi ezinye zalezo zici:

• Ukwehluleka ukukhula: Ngisho noma umntwana encelisa kahle futhi edla kahle kamuva, angase angakhuluphali futhi angase abonakale enesisindo esingaphansi uma eqhathaniswa nezinye izingane ezineminyaka efanayo.
• Indle ekhululekile noma enamafutha: Ngezinye izikhathi indle yengane yakho ingaba nkulu kakhulu, ibe namanzi, noma ibe namafutha. Ngezinye izikhathi indle ingaba nephunga elibi.
• Ubunzima bokuphefumula:Ngihlala ngizizwa sengathi kunzima ukuphefumula, sengathi uyacinana.
• Ukuphefumula okuqhubekayo: Umsindo wokuphefumula okuqhubekayo ovela esifubeni. Lokhu kungenzeka nasezimweni ezifana ne-asthma, kodwa kuyimpawu evame kakhulu ku-CF.
• Ukutheleleka kwamaphaphu okuvamile: Isibonelo, i-pneumonia kanye ne-bronchitis kuvamile. Uma uthola ukutheleleka kwamaphaphu kanye noma kabili ngenyanga, kuyinto okufanele uyikhathazeke.
• Ukutheleleka kwama-sinus okuphindaphindiwe: Ukutheleleka okuvamile ezindaweni ezizungeze ikhala (ama-sinus). Izimpawu zifaka phakathi ikhala elicijile, ikhala eligobhozayo, kanye nekhala elicijile.
• Ukukhwehlela okuqhubekayo, okungenzeka kube yi-phlegmy: Ukukhwehlela okuqhubekayo okungabe kusaba ngcono. Kungaba ngisho nokukhwehlela okukhiqiza uketshezi olujiyile.
• Ukukhula kancane: Ukuphakama nesisindo sengane kubonakala sengathi kukhula kancane uma kuqhathaniswa nezinye izingane ezingontanga efanayo.
• Ngezinye izikhathi isikhumba somntwana sinambitheka njengosawoti: Abanye abazali babika nokuthi uma behlikihla isikhumba somntwana wabo esijulukayo, sizwakala sinosawoti.

Uma usola ukuthi ingane yakho encane inesinye salezi zimpawu noma ngaphezulu, into engcono kakhulu ongayenza ukubona udokotela wezingane ukuze akunike iseluleko.

Kuyini ukuhlolwa kokujuluka futhi kwenziwani?

Odokotela baxilonga i-cystic fibrosis ngokuhlola isiguli ngokucophelela, balalele izimpawu zaso, futhi benze izivivinyo ezahlukahlukene. Lokhu kufaka phakathi izivivinyo zofuzo - okuyizivivinyo zegazi ezibheka izinguquko kuma-gene - i-X-ray yesifuba ne-sinus, kanye nokuhlolwa kokusebenza kwamaphaphu.

Kodwa-ke, isivivinyo esibaluleke kakhulu nesicacile sokuqinisekisa ukuthi une-cystic fibrosis noma cha isivivinyo sokujuluka. Lesi isivivinyo esilula kakhulu, esingenabuhlungu. Silinganisa inani le- chloride ekujulukeni kwakho. Ubuwazi ukuthi usawoti esiwudlayo wakhiwe ngamakhemikhali amabili abizwa ngokuthi i-chloride ne-sodium. Ngakho-ke, inani le-chloride ekujulukeni kwabantu abane-cystic fibrosis liphakeme kakhulu kunelomuntu ojwayelekile.

Isizathu salokhu ukuthi, ngenxa yesici sofuzo esibangela i-cystic fibrosis, umsebenzi weprotheni esiza i-chloride ukuthi ihambe emaselini ethu uyaphazamiseka. Ngenxa yalokho, i-chloride ayikwazi ukungena noma ukuphuma emaselini ngendlela efanele. Yilapho i-chloride iqoqana ngendlela engavamile ekujulukeni. Nakuba kungase kubonakale kulula kakhulu, lesi yisisekelo sesayensi esiyisisekelo sokuxilonga lesi sifo.

Ngokuvamile, odokotela batusa lokhu kuhlolwa kokujuluka uma ingane isengozini yokuthola i-cystic fibrosis (isibonelo, uma othile emndenini enalesi sifo), noma uma ekhombisa izimpawu esixoxe ngazo ekuqaleni. Ngezinye izikhathi, abafowabo nodadewabo bomntwana nabo bayacelwa ukuba benze lokhu kuhlolwa. Lokhu kwenzelwa ukubona ukuthi nabo bazuze lesi sakhi sofuzo nokuthi izingane zabo zisengozini yokuthola lesi sakhi sofuzo esikhathini esizayo.

Kwenziwa kanjani lokhu kuhlolwa kokujuluka? Ingabe kuyinto okufanele uyesabe?

Lokhu kuhlolwa kokujuluka kungenziwa kunoma ubani wanoma yimuphi ubudala. Kodwa-ke, izingane ezisanda kuzalwa zingase zingakwazi ukukhiqiza ukujuluka okwanele kwalokhu kuhlolwa ezinsukwini zokuqala ezimbalwa zokuphila kwazo. Ngakho-ke, lokhu kuhlolwa kuvame ukwenziwa ezinganeni eziphakathi kwamasonto amabili kuya kwamane ubudala , lapho zingakhiqiza khona ukujuluka okwanele.

Lolu vivinyo lulula kakhulu ukulwenza, futhi alubuhlungu nhlobo. Ngakho-ke ungesabi, kulungile? Nakhu okwenzekayo:

1. Okokuqala, isisebenzi sezempilo, kungaba umhlengikazi noma udokotela, sifaka ijeli noma uketshezi oluqukethe ikhemikhali ebizwa ngokuthi i-pilocarpine esikhumbeni sengalo yengane (ngokuvamile ingalo) noma umlenze. I-Pilocarpine umuthi ovuselela izindlala zokujuluka.

2. Bese kubekwa ama-electrode amabili endaweni bese kunikezwa ukuvuselelwa kukagesi okuncane kakhulu, okungenangozi ukuze kukhuthazwe izindlala zokujuluka futhi kukhiqizwe ukujuluka. Lokhu kwenziwa cishe imizuzu emi-5. Akukho ukuhlaba noma ubuhlungu nhlobo. Ingane encane ingase izwe ukuqaqamba okuncane noma ukufudumala esandleni noma onyaweni, kodwa yilokho kuphela. Iningi lezingane alikuzwa ngisho nalokhu.

3. Okulandelayo, ama-electrode ayasuswa, indawo yesikhumba iyahlanzwa, bese kufakwa idivayisi ekhethekile yokuqoqa umjuluko (kungaba yi-coil yepulasitiki, iphepha lokuhlunga, noma ucezu lwe-gauze) endaweni. Lokhu kushiywa endaweni cishe imizuzu engama-30 ukuze kuqoqwe umjuluko.

4. Ekugcineni, le sampula yokujuluka eqoqwe ithunyelwa elabhorethri ukuze kulinganiswe ngokunembile inani le-chloride elikhona.

Ukuhlolwa konke kuthatha cishe ihora. Kulula ukugcina ingane yakho izolile uma unethoyizi noma ibhodlela lobisi eduze.

Ithini imiphumela yalolu vivinyo?

Kulungile, manje ake sibone ukuthi imiphumela yalolu vivinyo lokujuluka ithini. Uma ingane ine-cystic fibrosis, ukuhlolwa kokujuluka kuzobonisa ukuthi kune-chloride ephezulu kunejwayelekile ekujulukeni kwayo.

Ngokuphathelene namanani alinganisiwe, lawa alandelayo (lawa manani angahluka kancane kusuka elabhorethri kuya elabhorethri, kodwa ngokuvamile afana nalawa):

• Uma izinga le-chloride yengane yakho liphakeme kune-60 mmol/L (millimol/litre) : Kungenzeka kakhulu ukuthi ine-cystic fibrosis.Ngokuvamile, uma kuvela umphumela onjengalona, ​​ukuhlolwa kwenziwa futhi ukuqinisekisa.
• Izinga le-chloride yengane lingaphansi kuka-30 mmol/L (millimol/litre) (ezinye iziqondiso zithi lingaphansi kuka-40 mmol/L): Kungashiwo ukuthi akanayo i-cystic fibrosis.
• Uma izinga le-chloride yengane yakho liphakathi kuka-30 no-59 mmol/L ( kwezinye izindawo 40-59 mmol/L): Lokhu kubhekwa njengomphumela ophakathi noma onqenqemeni . Kulesi simo, ukuhlolwa kungadingeka kuphindwe . Ukuhlolwa okwengeziwe, njengokuhlolwa kofuzo, kungadingeka futhi ukuze kunqunywe ezinye izinhlobo ze-CF ezingavamile.

Into ebaluleke kakhulu ukuthi le miphumela kufanele ihunyushwe udokotela. Ngakho-ke, uma imiphumela ifika, into engcono kakhulu ongayenza ukukhuluma nodokotela ngayo bese ulandela imiyalelo yakhe. Ungesabi.

Uyilungiselela kanjani ingane yakho ukuhlolwa kokujuluka? Ingabe kukhona okudingeka ukwenze?

Lokhu kulula kakhulu kumama nobaba. Awudingi ukwenza lutho olukhethekile ukuze ulungiselele ingane yakho ukuhlolwa kokujuluka.

• Asikho isidingo sokushintsha noma ukuyeka noma yikuphi ukudla kwengane (indlela yokondla, ukudla okuqinile uma kunikezwa), imisebenzi, noma imithi ingane eyithathayo ngaphambi kwalokhu kuhlolwa. Gcina lokhu njengokujwayelekile.
• Okuwukuphela kwento ukuthi, ungafaki noma yimaphi amakhrimu noma ama-lotion esikhumbeni sengane yakho amahora angama-24 ngaphambi kokuhlolwa. Ikakhulukazi ungafaki lutho engalweni noma emlenzeni ohlolwayo. Lokhu kungathinta imiphumela yokuhlolwa.

Uyabona, kulula kakhulu. Gqokisa ingane yakho izingubo ezikhanyayo nezikhululekile ngosuku lokuhlolwa.

Izinto ezibaluleke kakhulu okudingeka sizikhumbule kule ndaba (Umyalezo Ohamba Nawo Ekhaya)

Kulungile, ngakho-ke ngithemba ukuthi usuyaqonda kahle lokho esikhulume ngakho namuhla, i-Cystic Fibrosis kanye ne-Sweat Test. Nakuba lokhu kungase kubonakale kuyisihloko esiyinkimbinkimbi, akunzima kangako uma usuqonda izisekelo. Kusukela kulokho esikuxoxile, nansi ezinye izinto okufanele uzikhumbule:

• I-Cystic fibrosis (CF) yisifo esibangelwa izakhi zofuzo esibangela ukuba ulwelwesi lomzimba luqine, ikakhulukazi oluthinta amaphaphu kanye nohlelo lokugaya ukudla.
• Qaphela izimpawu: Uma unesinye noma ngaphezulu kwalezi zimpawu, njengokwehla kwesisindo, ukuphelelwa umoya njalo, ukukhwehlela okuqhubekayo, noma indle enamafutha, bona udokotela bese uxoxa ngazo.
• Ukuhlolwa kokujuluka kuyivivinyo eliyinhloko nelithembekile kakhulu lokuqinisekisa i-cystic fibrosis: lilinganisa izinga le-chloride ekujulukeni.
• Ukuhlolwa akubuhlungu futhi kuphephile: ngakho ungesabi ukuthatha ingane yakho ngenxa yalokhu.
• Kubaluleke kakhulu ukuqaphela lesi sifo kusenesikhathi:Ngoba-ke, izindlela zokwelapha ezidingekayo kanye nokuphathwa kwazo zingaqalwa ngokushesha, kuncishiswe izinkinga ingane engase ibhekane nazo futhi kuyisize iphile impilo engcono nenempilo.

Uma wena noma othile omaziyo enale nkinga, into engcono kakhulu ongayenza ukungesabi noma ukukholelwa kukho konke okutholayo ku-inthanethi, kodwa ukukhuluma nodokotela ofanelekayo. Bazokuqondisa kahle futhi bakunikeze ukwesekwa okudingayo.

I- Cystic Fibrosis, ukuhlolwa kokujuluka, i-chloride, izifo zezingane, izifo zofuzo, izifo zamaphaphu