Wake wezwa ngomuntu osemusha, ophilile, odlala imidlalo efa ngokuzumayo ngenxa yokuhlaselwa yinhliziyo? Kuyadabukisa ngempela. Esikhathini esiningi, sicabanga ngesifo senhliziyo njengento eyenzeka ngokuguga. Kodwa ngezinye izikhathi, imbangela yalezi zenzakalo ezingacabangeki yisimo esingavamile kakhulu esingasazi. Namuhla, sizokhuluma ngesinye isimo senhliziyo esinjalo esingathinta abantu abasha ikakhulukazi. Lesi yi-ARVC.
Iyini ngempela i-ARVC?
Kalula nje, i-ARVC isifo senhliziyo esingavamile esizuzwa ngofuzo , okusho ukuthi singadluliselwa ezizukulwaneni ngezizukulwane. Okwenzekayo ukuthi imisipha enhliziyweni yethu yonakale.
Cabanga ngenhliziyo yethu njengephampu enamandla eyakhiwe ngamakamelo amane. Yilokhu okupompa igazi emzimbeni wonke. Kula makamelo amane, elisehlangothini olungezansi kwesokudla libizwa ngokuthi i-Right Ventricle. Ku-ARVC, amangqamuzana emisipha yenhliziyo aphilile kule ventricle yesokudla ayafa futhi athathelwa indawo yizicubu zamafutha nezicubu ezine-fibrous (izicubu zesibazi) .
Kufana nesitini esiwela odongeni oluhle bese izikhala zigcwala udaka. Kwenzekani? Udonga lwalelo gumbi lenhliziyo luba luncane, lube buthaka, futhi lunwebeke. Ngemuva kwalokho alukwazi ukufinyela kahle futhi lupompe igazi. Lokhu kungabangela izinto ezifana nokuphelelwa umoya kanye nokuquleka.
Okuyingozi nakakhulu ukuthi izicubu zamafutha nezibazi ezisanda kwakheka ziphazamisa izimpawu zikagesi enhliziyweni. Lokhu kubangela ukuthi inhliziyo ishaye ngokungajwayelekile. Lokhu sikubiza ngokuthi i-arrhythmia . Lesi yisimo esiyingozi kakhulu kulesi sifo. Ngoba singabangela ukumiswa kwenhliziyo ngokuzumayo ngisho nokufa.
Lesi sifo sibizwa nangokuthi i-ARVC, i-Arrhythmogenic Right Ventricular Dysplasia (ARVD). Ngezinye izikhathi sibizwa nangokuthi i-Arrhythmogenic Cardiomyopathy (ACM) ngoba sithinta ne-ventricle yesobunxele.
Ziyini izimpawu zalesi simo?
Inkinga eyodwa ngalesi sifo ukuthi singaba nezimpawu ezingabonakali ezigabeni zokuqala. Izimpawu zivame ukuqala ukuvela ngaphambi kweminyaka engama-40, ngezinye izikhathi ngisho nasebusheni.
Into eyesabekayo kakhulu ukuthi kwabanye abantu, uphawu lokuqala noluwukuphela kwalo olubazisa ukuthi banalesi sifo ukufa kwenhliziyo ngokuzumayo.
Ngakho-ke, kubaluleke kakhulu ukuqaphela izimpawu ezilandelayo.
| Isibonakaliso | Incazelo elula |
|---|---|
| Ukuphazamiseka kwenhliziyo (i-Arrhythmias) | Izinguquko ezingavamile ekushayeni kwenhliziyo. Kungazwakala sengathi ukushaya noma ukucindezela esifubeni. Ikakhulukazi ezimweni ezifana ne -Atrial Fibrillation . |
| Isiyezi noma ukuquleka | Kufana nokulahlekelwa ingqondo ngoba ubuchopho abutholi igazi elanele. |
| Ukukhathala | Ukuzizwa ukhathele kakhulu njalo ngoba umzimba awuphampi igazi kahle. |
| Ubuhlungu besifuba | Ubuhlungu besifuba obubangelwa ukucindezeleka enhliziyweni. |
| Ubunzima bokuphefumula | Ukuphelelwa umoya okubangelwa ukungatholakali kwegazi elanele emaphashini. |
| Ukuvuvukala komzimba | Ukuvuvukala emilenzeni, emaqakaleni, ezinyaweni, noma esiswini. |
| Ukwehluleka Kwenhliziyo | Ngokuhamba kwesikhathi, ikhono lokushaya kwenhliziyo liba buthaka cishe ngokuphelele. |
Izimbangela kanye nofuzo lwe-ARVC
Ngokuvamile, i-ARVC ibangelwa uhlobo oluthile lwezakhi zofuzo . Lokhu kuyiphutha elincane ku-planning, noma izakhi zofuzo, ezakha amangqamuzana omzimba wethu. Lesi simo senzeka lapho kukhona amaphutha ezakhi zofuzo ezithinta amaprotheni asiza ukugcina amangqamuzana emisipha yenhliziyo exhumene.
Uma lokhu kuxhumana kuba buthaka, amangqamuzana emisipha yenhliziyo aqala ukuhlukana bese efa. Lokhu kungenzeka ikakhulukazi ngezikhathi zokucindezeleka enhliziyweni, njengasesikhathini sokuzivocavoca.
Cishe ingxenye yeziguli ze-ARVC zinomlando womndeni walesi simo. Lokhu kusho ukuthi kunomlando wezakhi zofuzo .
Ngakho-ke, uma othile emndenini wakho etholakale ene-ARVC, kubaluleke kakhulu ukuthi izihlobo eziseduze zalowo muntu (abazali, abafowabo nodadewabo, izingane, abazukulu, omalume, o-anti, abashana, abashana) bahlolwe ngokwezokwelapha. Ngisho noma kungekho zimpawu, ngisho nalabo abasebasha kufanele babone udokotela futhi bakhulume ngalokhu.
Kunezindlela ezimbili eziyinhloko zokuthi i-ARVC ingadluliselwa kanjani ngezizukulwane:
- I-Autosomal Dominant: Lolu uhlobo oluvame kakhulu. Lokhu kusho ukuthi omunye wabazali une-gene mutation. Khona-ke ingane yabo inethuba elingu-50% lokuthola lesi sifo njengefa. Kodwa-ke, izimpawu kanye nobudala bokuqala kwalesi sifo kungahluka phakathi kwamalungu omndeni.
- I-Autosomal Recessive: Lokhu kuyinto engavamile. Lapha, bobabili abazali banokuguqulwa kwezakhi zofuzo, kodwa abanazo izimpawu. Ingane yabo inethuba elingu-25% lokuthola lesi sifo. Esinye isimo esiqondile esihlobene nalokhu yisifo i-Naxos , esingabangela ukuqina kwesikhumba ezintendeni nasematheni ezinyawo kanye nokukhula kwezinwele ezijiyile, ezinjengoboya.
Ungasithola kanjani lesi sifo?
Udokotela angakwazi ukuxilonga i-ARVC ngokusekelwe ezimpawini zakho, umlando womndeni, kanye nokuhlolwa okumbalwa kwezokwelapha. Kunezindlela eziningana zokuxilonga ze-ARVC. Odokotela babheka ukuthi zingaki kulezi zindlela ozihlangabezana nazo.
Amaphuzu ayinhloko odokotela abawanakayo:
- Ukuhlola ukusebenza kwe-ventricle yesokudla okungavamile (kusetshenziswa izivivinyo ze-Echocardiogram noma ze-MRI kulokhu).
- Ukubona ukuthi kukhona yini amafutha noma isilonda esicutshini senhliziyo (i- MRI ibaluleke kakhulu kulokhu).
- Ukuhlola ukukhubazeka ekuhlolweni kwe-ECG ( i-Electrocardiogram - ECG/EKG ).
- Ukuphazamiseka kwesigqi senhliziyo, ikakhulukazi ngesikhathi sokuzivocavoca.
- Ingabe kukhona yini emndenini one-ARVC.
Ngokusekelwe kulezi zici, udokotela uzonquma ukuthi "ngokuqinisekile" unesifo, "mhlawumbe" unaso, noma "mhlawumbe" unaso. Bangase futhi bakuthumelele ukuhlolwa kwezakhi zofuzo uma kudingeka.
Ezinye izivivinyo ezisetshenzisiwe:
- Ukuskena kwenhliziyo nge-Cardiac Computed Tomography (CT )
- Ukuhlolwa kwe-ECG ngesikhathi sokuzivocavoca ( Ukuhlolwa Kokucindezeleka )
- Ukutadisha umsebenzi kagesi wenhliziyo ( Ukuhlolwa kwe-Electrophysiology )
- Ukuthatha ingxenye encane yomsipha wenhliziyo ukuze uyihlole ( i-Biopsy )
Yiziphi izindlela zokwelapha i-ARVC?
Ngeshwa, ayikho ikhambi le-ARVC. Kodwa-ke, kunezindlela eziningi zokwelapha ezisebenzayo ezingakusiza ukulawula izimpawu zakho, uvimbele izinkinga eziyingozi, futhi uphile impilo evamile. Umgomo oyinhloko kadokotela wakho ukuphatha isigqi senhliziyo kanye nezimo zenhliziyo.
| Indlela yokwelapha | Kwenzakalani? |
|---|---|
| Imithi | Imithi efana nemithi yokulwa nokuvuvukala, ama-beta-blockers , kanye nama-anticoagulants iyanikezwa. |
| Ukususwa kwe-Catheter | Uma unenhliziyo engavamile engakwazi ukulawulwa ngemithi, inqubo eshisa izindawo zenhliziyo lapho kuvela khona izimpawu zikagesi ezingavamile. |
| Idivayisi ye-ICD (I-Implantable Cardioverter-Defibrillator) | Lokhu kungenye yezindlela zokwelapha ezibaluleke kakhulu. Kubantu abasengozini enkulu yokufa ngenxa yokuma kwenhliziyo ngokuzumayo, idivayisi encane ifakwa ngaphansi kwesikhumba sesifuba. Uma kwenzeka ukuphazamiseka kwenhliziyo okuyingozi, le divayisi ibangela ukushaqeka kukagesi ukubuyisela inhliziyo esimweni sayo esijwayelekile. |
| Ukufakelwa Inhliziyo | Kubhekwa njengendlela yokugcina uma zonke ezinye izindlela zokwelapha zingaphumeleli, kodwa abantu abaningi abane-ARVC akudingeki bahambe ibanga elide kangaka. |
Izinto okufanele uzicabangele uma uhlala ne-ARVC
Uma usutholakale une-ARVC, kuzodingeka wenze izinguquko ezithile endleleni yakho yokuphila. Lezi zinto zingasiza ekunciphiseni ukucindezeleka enhliziyweni yakho.
- Nciphisa ukuzivocavoca: I-ARVC ingenziwa ibe yimbi kakhulu ngokuzivocavoca. Ngakho-ke, kungadingeka ugweme ngokuphelele imidlalo yokuncintisana. Qiniseka ukuthi ukhuluma nodokotela wakho mayelana nenani kanye nohlobo lokuzivocavoca ongalwenza nsuku zonke.
- Indlela yokuphila enempilo: Kubaluleke kakhulu ukunciphisa ukusetshenziswa kotshwala, ukugwema ukubhema, ukudla ukudla okunempilo, kanye nokunciphisa iziphuzo ezine-caffeine (ikhofi, itiye).
- Thatha imithi yakho njengoba uyalelwe: Ungalokothi weqe ukuthatha imithi oyiyalelwe udokotela wakho.
- Ukuhlolwa njalo kwezokwelapha: Kuzodingeka ubone udokotela wakho impilo yakho yonke . Uma une-ICD, kuzodingeka ukuthi uyihlolwe njalo .
Ukuthola ukuthi unesifo senhliziyo kungaba yinto enzima kakhulu ukubhekana nayo, ikakhulukazi usemncane. Uma ungumdlali wezemidlalo, kungaba buhlungu ukuyeka lobo buwena. Kodwa khumbula, impilo yakho ibaluleke kakhulu. Ngokwelashwa okufanele nendlela yokuphila, ungaphila impilo enhle.
Umlayezo Wokuya Nawe Ekhaya
- I-ARVC yisimo esingavamile, esizuzwa njengefa esithinta kakhulu uhlangothi lwesokudla lwenhliziyo.
- Into eyingozi kakhulu ngalesi sifo ingozi yokuma kwenhliziyo ngokuzumayo nokufa ngaphandle kwezimpawu.
- Uma uzwa izimpawu ezifana nokuqina kwesifuba, isiyezi, noma ubunzima bokuphefumula, bonana nodokotela ngokushesha.
- Uma othile emndenini wakho ene-ARVC, kufanele nakanjani uhlolwe udokotela.
- Nakuba lesi sifo singelapheki ngokuphelele, singalawulwa ngempumelelo futhi siphile kahle ngemithi, amadivayisi e-ICD, kanye nezinguquko zendlela yokuphila.
- Kubaluleke kakhulu ukuthi laba ziguli bagweme ukuvivinya umzimba okunzima nokuncintisanayo.
💬 Comments (0)
Awekho amazwana athunyelwe okwamanje. Faka amazwana akho lapha okokuqala ngqa.
Engeza amazwana akho