Wake wacabanga ukuthi inhliziyo yethu imangalisa kangakanani? Kodwa ngezinye izikhathi, ngisho nale nhliziyo ingakhula izifo ngezindlela ezingalindelekile. Namuhla sizokhuluma ngesimo somdlavuza esingavamile, kodwa esibi kakhulu. Ukuzwa lokhu kungakwenza uzizwe wesaba kancane, kodwa kubaluleke kakhulu ukuqaphela lokhu.
Kuyini lokhu okubizwa ngokuthi i-cardiac angiosarcoma?
Kalula nje, i-cardiac angiosarcoma iyisimila esibi esikhula enhliziyweni yakho. Siqala olwelwesini lwemithambo yegazi enhliziyweni yakho. Ukusuka lapho, sisakazekela emisipheni yenhliziyo.
Ngokuvamile, cishe ama-80% ezimo, lesi simila esingavamile sikhula ekamelweni eliphezulu kwesokudla senhliziyo, elibizwa ngokuthi i-atrium efanele . Ngezinye izikhathi singakhula futhi ekamelweni eliphansi kwesokudla, elibizwa ngokuthi i-ventricle efanele , noma esikhwameni esivikelayo esizungeze inhliziyo, esibizwa ngokuthi i-pericardium . Akuvamile kakhulu, singakhula ohlangothini lwesobunxele lwenhliziyo.
Lo mdlavuza unamandla kakhulu, usakazeka ngokushesha. Ungavimba noma ucindezele izindawo ezibalulekile ezizungeze inhliziyo, njengemithambo yegazi nama-valve. Ngenxa yemvelo yalo mdlavuza, ngezinye izikhathi kungaba nzima ukuwususa ngokuphelele ngokuhlinzwa.
Sivame kangakanani lesi sifo?
Eqinisweni, i-cardiac angiosarcoma iyisifo esingavamile kakhulu. Ngokusho kwemibiko yokuhlolwa kwesidumbu, kubikwa ukuthi kungaphansi kuka-0.03% wamacala ezimila zenhliziyo eziyinhloko. Ngakho-ke cabanga, lolu hlobo lwe-angiosarcoma luyivelakancane kakhulu.
Kodwa, ngokumangazayo, ezimila eziyingozi ezingakheka enhliziyweni yomuntu omdala, lolu uhlobo oluvame kakhulu .
Lesi sifo sivame ukutholakala kubantu abangaphansi kweminyaka engama-65. Sivame kakhulu kubantu abaneminyaka ephakathi kwama-20 nama-40. Kuthiwa futhi amadoda anamathuba aphindwe kabili kuya kwamathathu okuthola lo mdlavuza kunabesifazane.
Ziyini izimpawu zalokhu?
Izimpawu ze-cardiac angiosarcoma zingahluka kuye ngokuthi isimila sikuphi. Abanye abantu bangase bangabi nazo izimpawu ezinkulu ekuqaleni. Kodwa-ke, kunezimpawu ezivamile ezingabonakala:
- Ubunzima bokuphefumula (odokotela babiza lokhu ngokuthi "ukuphelelwa umoya"). Kungazwakala sengathi uphefumula kanzima ngokukhuphuka izitebhisi.
- Ubuhlungu besifuba . Kuzwakala sengathi kuyacindezelwa, sengathi kuyacindezelwa.
- Ukukhathala nokukhathala . Ukuzizwa ukhathele ngaso sonke isikhathi ngaphandle kwesizathu.
- Ukulahlekelwa yingqondo ngokuzumayo (i-syncope).
- Ukuzizwa sengathi inhliziyo yakho ishaya ngokungajwayelekile futhi ngokushesha (lokhu sikubiza ngokuthi "ukushaya kwenhliziyo").
Cabanga nje, kukhona umuntu osemusha ogama lakhe linguNalini. Sekuyisikhathi eside ezizwa ekhathele futhi ezwa ukuqina okuncane esifubeni sakhe. Wayecabanga ukuthi mhlawumbe kungenxa yokusebenza ngokweqile. Kodwa ngemva kwezinsuku ezimbalwa, waya kudokotela lapho ekuthola kunzima ukuphefumula. Mhlawumbe lezi yizimpawu zokuqala zesifo esinjengalesi.
Uma umdlavuza ususakazekele ngaphesheya kwenhliziyo kwezinye izingxenye zomzimba, kungase kuvele ezinye izimpawu, njenge- anemia , noma ukwehla kwesisindo okungachazeki .
Kungani kwenzeka into efana nale? Yiziphi izizathu?
Ayikho imbangela ecacile necacile yokuthuthukiswa kwe-cardiac angiosarcoma, kodwa odokotela bakholelwa ukuthi izici ezithile zingadlala indima.
- Kucatshangwa ukuthi abantu abanezinguquko ezakhiweni zabo zofuzo , njengezakhi zofuzo ze-POT1, banamathuba amaningi okuthola lo mdlavuza.
- Okunye okungenzeka ukuthi abantu abathola ukwelashwa ngemisebe esifubeni njengokwelashwa komunye umdlavuza besebancane bangase babe sengozini enkulu yokuthola lesi sifo kamuva ekuphileni.
Yiziphi izinto ezibangela ingozi?
Kunezinye izici eziningana eziyingozi ezingathinta ukuthuthukiswa kwalesi sifo:
- Njengoba ngithole ukwelashwa ngemisebe ngaphambilini njengokwelashwa komunye umdlavuza.
- Ukuchayeka kumakhemikhali athile angabangela umdlavuza.
- Kulabo abanesifo esibizwa ngokuthi i-lymphedema, okuwukuvuvukala kohlelo lwe-lymphatic .
Yiziphi izinkinga ezingaba khona ngenxa yalesi sifo?
Ngenxa yokuthi i-cardiac angiosarcoma iyisimo esibi kakhulu, ingaholela ezinkingeni ezahlukahlukene.
- Ukwehluleka kwenhliziyo : Ukungakwazi kwenhliziyo ukupompa igazi ngendlela efanele.
- Ukuvaleka kwe-Vena cava : Ukuvaleka komthambo oyinhloko othwala igazi lisuka emzimbeni ongaphezulu liye enhliziyweni.
- Ukuphazamiseka kwesigqi senhliziyo (i-arrhythmia) : Izinguquko ezingavamile ekushayweni kwenhliziyo.
- Ukuphuma kwegazi enhliziyweni : Uketshezi olufana nolwelwesi olugcwalisa isikhwama esizungeze inhliziyo.
- I-tamponade yenhliziyo : Lokhu kwakheka koketshezi okukhulunywe ngakho kubeka ingcindezi enhliziyweni.
- Ukubuyela kwe-valve yenhliziyo: Igazi livuza emuva ngama -valve enhliziyo ngaphandle kokuvala kahle.
- Ukushaqeka okuvimbelayo: Isimo esibi esibangelwa ukuvinjelwa kokugeleza kwegazi.
Ukuzwa konke lokhu kungase kuphazamise kancane, kodwa kubalulekile ukwazi lezi zinto.
Lesi sifo sitholakala kanjani?
Udokotela uzokwenza izivivinyo eziningana ukuqinisekisa ukuthi unalesi sifo noma cha.
- I-echocardiogram ye-Transthoracic `(i-echocardiogram ye-transthoracic)`: Lokhu kufana nokuskena kwenhliziyo nge-ultrasound. Kuwukuhlolwa okungenabuhlungu okwenziwa ebusweni besifuba.
- I-Transesophageal echocardiogram : Lokhu kuhilela ukufaka ipayipi elincane elidlula emhubheni ukuze kubonakale inhliziyo ngokucacile.
- I-CT scan (i-computed tomography - i-CT scan) : Lokhu kungaveza izithombe ezinemininingwane zenhliziyo nezindawo ezizungezile.
- I-MRI Yenhliziyo (i-magnetic resonance imaging) : Isebenzisa insimu yamagnetic namagagasi omsakazo ukukhiqiza izithombe ezinemininingwane zenhliziyo.
- Ukuskena kwe-positron emission tomography (PET) : Lokhu kusiza ekuboneni amaseli asebenzayo, njengamaseli omdlavuza.
- Ukuhlolwa kwe-catheter yenhliziyo : Ukuhlolwa lapho ithubhu elincane lidluliselwa khona ngemithambo yegazi liye enhliziyweni ukuze kulinganiswe ukucindezeleka futhi kuthathwe amasampula.
- I-biopsy yenhliziyo : Kuthathwa ingxenye encane yezicubu enhliziyweni bese ihlolwa ngaphansi kwe-microscope ukuqinisekisa umdlavuza.
Iphathwa kanjani?
Ukwelashwa kwalesi sifo kuyinkimbinkimbi kancane. Izindlela eziyinhloko zokwelapha yilezi:
- Ukuhlinzwa : Uma kungenzeka, ukususa isimila ngokuphelele kunikeza ithuba elihle kakhulu lokusinda . Kodwa-ke, uma umdlavuza ususakazekele kwezinye izingxenye zenhliziyo, kungaba nzima ukuwususa ngokuphelele. Kubaluleke kakhulu ukukhetha udokotela ohlinzayo onolwazi ngalezi zimila ezingavamile.
- Ukwelashwa ngamakhemikhali : Lokhu kungasiza ekunciphiseni izimpawu futhi kusize abanye abantu baphile isikhathi eside.
- Ukwelashwa ngemisebe : Kwezinye izimo, lokhu kungasiza ekuthuthukiseni isimo.
Ingabe izinkinga zingavela ngenxa yokwelashwa?
Yebo, ezinye izindlela zokwelapha zingabangela izinkinga, ikakhulukazi ngemva kokuhlinzwa:
- Ukopha.
- Ukungalingani kwesigqi senhliziyo (i-arrhythmia).
- Ubuthakathaka ekusebenzeni kwenhliziyo.
Yingakho odokotela behlela ukwelashwa ngemva kokucabanga ngakho konke lokhu.
Yini ongayilindela ngalesi sifo?
Uma ngikhuluma iqiniso, lesi isimo esinzima kancane.
Ngisho nangemva kokwelashwa , isimila singabuya . Ngokuvamile, ngesikhathi kutholakala ukuthi i-cardiac angiosarcoma inesifo, isisabalale (isakazeke kakhulu) kwezinye izindawo, njengesibindi, amaphaphu, kanye nobuchopho. Ngezinye izikhathi, singasakazekela emathanjeni nasezindlala ze-adrenal. Yingakho ukwelapha lo mdlavuza nokusindisa izimpilo kuyinselele.
Iyini inhloso yalesi sifo? (Indlela yokuphila)
Kuyadabukisa ukusho lokhu, kodwa isibikezelo se-cardiac angiosarcoma asisihle neze . Lesi sifo sinamandla kakhulu futhi sisakazekela ezicutshini ezizungezile.
Isilinganiso sokuphila komuntu onalesi sifo siphakathi kwezinyanga eziyi-10 neziyi-16.Yileyo ndlela ebalwa ngayo. Ngaphandle kokuhlinzwa, ngisho nangezinye izindlela zokwelapha, abantu abaningi baphila phakathi kwezinyanga ezingu-9 nezingu-12. Ezinye izilinganiso zithi lesi sikhathi singaba sifushane njengezinyanga ezi-5 noma ngaphansi.
Abantu abangu-14% kuphela abatholakale benesifo senhliziyo abasaphila eminyakeni emihlanu ngemva kokuxilongwa. Isifo senhliziyo esisabalele (esasakazeke) kwezinye izingxenye zomzimba sivame ukuba yingozi.
Kuvamile ukuzizwa udabuke futhi wesaba uma uzwa into efana nale. Kodwa-ke, ukwazi lolu lwazi kuzokusiza ukuthi ukhulume nodokotela bakho futhi uqonde ukuthi yiziphi izinketho zakho ezingcono kakhulu.
Ingabe zikhona izindlela zokunciphisa le ngozi?
Nakuba kungekho ndlela yokugwema lokhu ngokuphelele, kunezinto ongazizama ukunciphisa ingozi.
- Kubalulekile ukunciphisa ukuchayeka kumakhemikhali angabangela umdlavuza.
- Uma unesifo sofuzo esikubeka engcupheni enkulu yalolu hlobo lomdlavuza, khuluma nodokotela wakho ngaso. Ngemuva kwalokho, ungase ukwazi ukuthola ukuhlolwa okungasithola lesi sifo kusenesikhathi.
Uzinakekela kanjani?
Izinto eziyisisekelo ozenzayo uma uphilile ziba zibaluleke kakhulu uma ulwa nomdlavuza.
- Ukudla ukudla okunomsoco kunikeza umzimba amandla owadingayo.
- Uma uzizwa ukhathele ngenxa yokwelashwa, kubaluleke kakhulu ukuthola ukuphumula okwanele .
- Zama izinto ezifana ne -yoga, ukuzindla, kanye nokuzivocavoca ngokuphefumula okujulile ukuze uphumule ingqondo yakho.
- Kungumqondo omuhle futhi ukujoyina iqembu lokusekelana (noma ngabe liku-inthanethi) lapho ungabelana khona ngemizwa yakho.
Ukunakekelwa kwe-hospice kungakusiza ukuthi uhlale ukhululekile ekupheleni kwempilo yakho.
Kufanele ngimbone nini udokotela?
Ungakhohlwa ukubona udokotela wakho kuzo zonke izikhathi zokuqokwa. Kodwa-ke, xhumana nodokotela wakho ngokushesha uma:
- Uma izimpawu zakho ziphinde zivele.
- Uma izimpawu ziba zimbi kakhulu.
- Uma udinga usizo ngemiphumela emibi evela ekwelashweni.
Kufanele uye nini egumbini lezimo eziphuthumayo?
Uma unalezi zimpawu, funa ukwelashwa okuphuthumayo ngokushesha:
- Uma unenkinga enkulu yokuphefumula .
- Uma uzwa ubuhlungu obukhulu esifubeni .
- Uma uke wenziwa i-chemotherapy, uba nomkhuhlane noma ezinye izimpawu zokutheleleka (isib., ukubanda, isilonda esibonakala sengathi siyaqhuma).
Yimiphi imibuzo okufanele uyibuze udokotela wakho?
Ngenxa yokuthi i-cardiac angiosarcoma iyisifo esingavamile, kungaba nzima ukuthola ulwazi oluningi ngaso. Ungabuza udokotela wakho imibuzo efana nale:
- "Ingabe lo mdlavuza ususakazekele kwezinye izingxenye zomzimba wami?"
- "Ngingahlinzwa?"
- "Uma ubheka ama-scan, kubonakala sengathi lonke isimila lingasuswa?"
- "Ungincoma uhlobo luni lokwelashwa?"
- "Uyini umbono ngomuntu osesimweni sami?"
Njengoba abantu abaningi bengakaze bezwe nge-cardiac angiosarcoma, kungaba nzima ukuchaza isimo sakho emndenini nakubangane bakho. Ungesabi ukubuza udokotela wakho nganoma yini ongayiqondi. Sebenzisa noma yiziphi izinsiza nezinsizakalo ezitholakalayo ukuze usize. Uma umbono wakho ungemuhle, khuluma nomuntu omethembayo ngezidingo zakho. Ukukhuluma nomeluleki nokuhlela izinsizakalo ze-hospice kungakusiza uzizwe ukhululekile kakhudlwana.
Okokugcina, izinto okufanele uzikhumbule
I-Cardiac Angiosarcoma ingumdlavuza ongavamile kakhulu futhi oyingozi. Kubalulekile ukuqaphela lokhu nokuqaphela izimpawu. Uma kusheshe kutholakale ukuthi unesifo, kulapho amathuba okuba welashwe khona.
- Lona umdlavuza ongavamile kodwa onzima.
- Uma kuvela izimpawu, funa iseluleko sezokwelapha ngokushesha.
- Khuluma nodokotela wakho ngokukhululekile mayelana nokwelashwa kanye nemiphumela yako.
- Unganqikazi ukufuna induduzo nokusekelwa ngokwengqondo.
Ngiyethemba ukuthi lolu lwazi luwusizo kuwe. Hlala uphilile!
Umdlavuza wenhliziyo , i-angiosarcoma, isifo senhliziyo, izimpawu zomdlavuza, ukwelashwa komdlavuza, impilo yenhliziyo, umdlavuza ongavamile

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