Skip to main content

Ingabe kukhona indawo engavamile esikhumbeni sakho? Kungaba yi-DFSP (Dermatofibrosarcoma Protuberans)!

Ingabe kukhona indawo engavamile esikhumbeni sakho? Kungaba yi-DFSP (Dermatofibrosarcoma Protuberans)!

Wake waphawula iqhubu elincane noma ukushintsha kombala esikhumbeni sakho? Ngezinye izikhathi asikunaki kakhulu, akunjalo? Kodwa ngezinye izikhathi ngisho nento encane njengale ingaba yinto okufanele uyikhathalele. Namuhla, sizokhuluma ngohlobo lomdlavuza wesikhumba olungavamile kodwa olubalulekile. Lubizwa ngokuthi i-Dermatofibrosarcoma Protuberans , noma i-DFSP ngamafuphi.

Kuyini i-DFSP (i-Dermatofibrosarcoma Protuberans)?

Kalula nje, i-DFSP uhlobo lomdlavuza wesikhumba olukhula kancane, kodwa olungavamile. Luqala engxenyeni ephakathi yesikhumba sethu, i-dermis . Ungase uzwe udokotela eyibiza ngokuthi i-DFSP.

Ngenxa yokuthi lo mdlavuza ukhula kancane kancane, awuvamile ukusabalala kwezinye izingxenye zomzimba. Kodwa-ke, akuwona umqondo omuhle ukuwushaya indiva. Kubaluleke kakhulu ukuthola ukwelashwa okufanele nokususa lesi simila. Kungaleso sikhathi kuphela lapho umdlavuza ungayeka ukubuya (ukuphindelela) noma ukusabalala kwezinye izingxenye zomzimba (umdlavuza osakazeka kakhulu) ungavinjelwa. Ngokwelashwa okufanele, umuntu one-DFSP unethuba elihle kakhulu lokululama.

Ingabe le DFSP iyisimila nje? Noma umdlavuza?

Cha, i-DFSP akuyona nje isimila esingenabungozi. Yisimo esibi . Uma sikhuluma iqiniso, uhlobo lomdlavuza wezicubu ezithambile, uhlobo lwe -sarcoma yezicubu ezithambile . Ama-Sarcomas umdlavuza owakheka ezindaweni ezifana nemisipha, amafutha, kanye nesikhumba. Ngezinye izikhathi, angathinta namathambo.

Ingabe i-DFSP ingasabalala (i-metastasize) kwezinye izingxenye zomzimba?

I-DFSP ngokuvamile akuyona uhlobo lomdlavuza olusakazeka ngokushesha kakhulu emzimbeni wonke. Kodwa-ke, akuvamile kakhulu, cishe umuntu oyedwa kwabangu-20 abane -DFSP angaba nomdlavuza osakazeka ngale kwalapho waqala khona. Lokhu kubizwa ngokuthi umdlavuza osakazeka kalula .

Lokhu kungenzeka kakhulu ukuthi kusakazeke uma kungelashwa, noma uma umdlavuza ususakazeke wajula esikhumbeni, wangena ezicutshini ezinamafutha kanye nemisipha.

Enye into ukuthi, nakuba imbangela eqondile ingaziwa, uma i-DFSP ikhula ngesikhathi sokukhulelwa, ingaba nzima kakhulu.

Futhi, inani elincane labantu abane-DFSP lingahlakulela uhlobo olunamandla kakhulu nolusakazeka ngokushesha olubizwa ngokuthi i-fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS) . Ngisho noma lawa mathumba e-DFSP-FS esuswa ngokuhlinzwa, kungenzeka kakhulu ukuthi abuye futhi angasakazeka kwezinye izindawo.

Sivame kangakanani lesi simo esibizwa ngokuthi i-DFSP?

I-DFSP uhlobo lomdlavuza olungavamile kakhulu. Emhlabeni wonke, ithinta abantu abangaba bane kuphela kubantu abayisigidi ngonyaka. I-DFSP iphakathi kuka-1% no-6% wazo zonke izicubu ezithambile ze-sarcoma.

Lo mdlavuza uvame kakhulu kubantu abadala abaneminyaka ephakathi kuka-20 no-50. Kodwa-ke, izingane ezincane nazo zingaba nalo mdlavuza wesikhumba. Ezinye izingane zingaba ne-DFSP lapho zizalwa. Ucwaningo lukhombisile ukuthi abantu abamnyama banamathuba amancane okuba nawo kunabantu bezinye izinhlanga.

Yiziphi izinhlobo eziyinhloko zama-DFSP?

Odokotela bezifo, odokotela abahlola izicubu zomzimba ngaphansi kwesibonakhulu, bangakutshela ukuthi hlobo luni lwe-DFSP onalo ngokuhlola amaseli. Kunezinhlobo eziningana eziyinhloko:

  • Amathumba aseBednar (aziwa nangokuthi i-DFSP enemibala): Lezi zinhlobo zamaseli ziqukethe i-melanin eningi, umbala onikeza isikhumba umbala waso. Yingakho la mathumba angavela ngemibala ehlukahlukene, okuhlanganisa obomvu, onsundu, oluhlaza okwesibhakabhaka, nonsomi. Lolu hlobo lubangela cishe u-5% wokuxilongwa kwe-DFSP.
  • I-Giant cell fibroblastoma: Lolu hlobo lubonakala ngokuba khona kwama-giant cell. Lolu hlobo lubizwa nangokuthi i-juvenile DFSP ngoba luvame kakhulu ezinganeni nakubantu abadala abasebasha.
  • I-Fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS): Njengoba kushiwo ngaphambili, lolu uhlobo lwe-sarcoma yezicubu ezithambile olunolaka, olusakazeka ngokushesha.
  • Ama-Myxoid DFSP: Lawa akhiwe uhlobo olungavamile lwezicubu ezixhumeneyo ezibizwa ngokuthi i-myxoid stroma. Lolu hlobo lwe-DFSP aluvamile kakhulu.

Yini ebangela i-DFSP?

Ngokumangalisayo, abantu abangu-9 kwabayi-10 abathola i-DFSP banokuguquka kwezakhi zofuzo okubangela lesi simo . Lokhu kuguquka kwezakhi zofuzo kwenzeka emaseli ethu ngemva kokuzalwa kwethu. Lokhu kusho ukuthi i-DFSP ayibangelwa yisici sofuzo esizuzwe kubazali bethu.

Yiziphi izici eziyingozi zokuthuthukisa i-DFSP?

Ngaphezu kohlanga, ukuba nanoma yiluphi uhlobo lokulimala kwesikhumba noma izibazi kungandisa ingozi yokuthola i-DFSP. Kunezindlela eziningana isikhumba esingalimala ngazo:

  • Ukusha
  • Ukwelashwa ngemisebe
  • Ukusikwa kokuhlinzwa
  • Ama-tattoo

Cabanga nje, wake waba nokusha okukhulu kanye nesibazi esikhulu. Noma, wake welashwa ngemisebe yesifo esithile. Uma isikhumba sonakaliswa yizinto ezinjengalezi, kunethuba elincane lokuthi isimo esifana ne-DFSP sizovela esikhathini esizayo, nakuba kungavamile. Yingakho kufanele sihlale siqaphela izinguquko esikhumbeni.

Ziyini izimpawu ze-DFSP?

Izimpawu zokuqala ze-DFSP zicashile kangangokuthi singase singaziboni noma sizibone. Lezi zimila zivame ukuvela esifubeni, emhlane, emahlombe, esiswini, noma ezinqeni. Zingavela nasezingalweni, emilenzeni, ekhanda, nangaphakathi emlonyeni.

Ekuqaleni, ungase ubone indawo encane efana nokuklwebheka esikhumbeni.Iyisicaba futhi ayibuhlungu. Ingase izwakale ilukhuni kancane uma uyithinta, futhi umbala ungase ushintshe kancane.

Ezinsaneni nasezinganeni ezincane, i-DFSP ingabukeka njengophawu lokuzalwa . Lawa mabala ngokuvamile aphakathi kwengxenye yesentimitha kuya kwamabili ububanzi (1 kuya ku-5 cm).

Izimpawu ze-DFSP ziyabonakala njengoba umdlavuza ukhula. Njengoba isimila sikhula, singena engxenyeni ephezulu yesikhumba (i-epidermis). Lokhu kubangela ukuthi kuvele amaqhubu aqinile (amaqhubu) ebusweni besikhumba . Igama elithi "protuberance" lisho "ukuvela."

Ungase ubone lezi zimpawu kulezi ziqhubu:

  • Ingaqhekeka noma yophe kalula.
  • Inamathele ngokuqinile esikhumbeni (ayikwazi ukushukunyiswa).
  • Njengoba ukhula, isikhumba sakho siyanwebeka.
  • Kuzwakala kunzima uma kuthintwa, noma njengerabha.
  • Umbala ungaba nsundu ngokubomvu, onsomi, oluhlaza okwesibhakabhaka, noma obomvu.
  • Kungase kube mnene kancane uma kuthintwa.

Zikhona yini ezinye izimo ezibangela izimpawu ezifana ne-DFSP?

Yebo, kukhona isifo sesikhumba esingeyona umdlavuza esibizwa ngokuthi i-cellular dermatofibroma . Lokhu kungafana kakhulu ne-DFSP, ikakhulukazi ezigabeni zaso zokuqala. I-Cellular dermatofibroma iyizimila ezithambile zezicubu ezingengozini. Zivame kakhulu ukuvela emilenzeni. Ngezinye izikhathi zingaluma futhi zibe buhlungu. Iningi le-dermatofibroma alidingi ukwelashwa. Kodwa-ke, kuwukuhlakanipha ukungadidanisi lokhu kokubili, ngakho kuwukuhlakanipha ukubona udokotela uma ubona noma yini entsha esikhumbeni sakho.

Itholakala kanjani i-DFSP (i-Dermatofibrosarcoma Protuberans)?

I-DFSP ihlolwa odokotela besikhumba , abangodokotela abaqeqeshwe ngokukhethekile ngomdlavuza wesikhumba nezifo zesikhumba. Udokotela wakho uzoqala athathe isampula encane yeqhubu lesikhumba noma ibala alithumele elebhu ukuze lihlolwe (i-biopsy yesikhumba) . Iqhubu lonke lingasuswa bese lithunyelwa elebhu. Odokotela bezifo bazobe sebebheka izicubu ngaphansi kwe-microscope ukuze babone ukuthi zinamaseli omdlavuza yini.

Uma ukuhlolwa kwesikhumba kuqinisekisa ukuthi une-DFSP, ungase ucelwe ukuthi wenze i-MRI scan . Lokhu kuzosiza ekunqumeni ubukhulu obuqondile besimila nokuthi sisakazeke kangakanani esikhumbeni. Lolu lwazi lubaluleke kakhulu ekuhleleni ukwelashwa.

Yiziphi izindlela zokwelapha i-DFSP (Dermatofibrosarcoma Protuberans)?

Ukwelashwa okuyinhloko nokungcono kakhulu kwe-DFSP ukususa isimila ngokuhlinzwa. Odokotela besikhumba bavame ukusebenzisa inqubo ekhethekile ebizwa ngokuthi ukuhlinzwa kwe-Mohs ukususa izimila ze-DFSP. Nakhu okwenzekayo phakathi nalokhu kuhlinzwa:

  • Okokuqala, kufakwa umuthi wokubulala izinzwa wendawo endaweni yokwelashwa, ukuze ungezwa ubuhlungu.
  • Ngemuva kwalokho, udokotela usika futhi asuse isimila esinomdlavuza. Kodwa hhayi isimila kuphela, kodwa nendawo encane yesikhumba esinempilo esizungezile. Lokhu kubizwa ngokuthi i-margin .
  • Okulandelayo, imiphetho (imingcele) yezicubu ezisusiwe ihlolwa ngaphansi kwe-microscope ukuze kubonakale ukuthi kukhona yini amangqamuzana omdlavuza asele.
  • Uma kusekhona amangqamuzana omdlavuza emaphethelweni, udokotela uzosusa ezinye izicubu endaweni lapho ukuhlinzwa kwenziwe khona futhi.
  • Ngale ndlela, ukususwa kwezicubu kuyaqhubeka kuze kube yilapho kungatholakali amangqamuzana omdlavuza emaphethelweni.
  • Ngemva kokuba umdlavuza usususwe ngokuphelele, kwenziwa ukuhlinzwa kokuvuselela uma kudingeka.

Ingabe kukhona ezinye izindlela zokwelapha i-DFSP ngaphandle kokuhlinzwa?

Ngisho noma izimila ze-DFSP zisuswa ngokuhlinzwa, ngezinye izikhathi zingabuya. Ngemva kokususwa okujwayelekile okubanzi, kunethuba elingu-20% kuya ku-30% lokuthi zizobuya zingakapheli iminyaka emithathu. Ngemva kokuhlinzwa kukaMohs, le ngozi yehliswa ibe ngu-4% kuya ku-5%. Kodwa-ke, kubalulekile ukuhlala uqaphile, njengoba izimila zingabuya ngisho nangemva kweminyaka eyi-10 noma ngaphezulu.

Ngezinye izikhathi, uma umdlavuza ususakazekele kwezinye izingxenye zomzimba (i-metastatic DFSP), noma uma isimila sikhulu kakhulu noma sisendaweni ethile ukuba singasuswa ngokuhlinzwa, odokotela basebenzisa umuthi obizwa ngokuthi i-Imatinib . Lo muthi unganciphisa nesimila, okwenza kube lula ukusisusa ngokuhlinzwa.

Futhi, uma ukuhlinzwa kungenakuwususa ngokuphelele umdlavuza, noma uma ukuhlinzwa kungenzeki nhlobo, ukwelashwa ngemisebe kungasetshenziswa.

Uyini umbono womuntu one-DFSP?

Lezi izindaba eziduduzayo ngempela. Njengoba i-DFSP ingumdlavuza okhula kancane, ongasebenzi kahle, uma uphathwa ngendlela efanele, abantu abangaphezu kuka-99% bazosinda iminyaka eyi-10 noma ngaphezulu. Ngakho-ke, into ebaluleke kakhulu ukungesabi bese ulandela iseluleko sikadokotela wakho.

Yini engingayenza ukuze ngithuthukise umbono wami?

Kunezinto eziningana ongazenza ukuze uthuthukise umbono wakho:

  • Zihlole njalo isikhumba sakho. Bheka noma yiziphi izinguquko ezintsha, amabala, noma amaqhubu esikhumbeni sakho. Uma ubona noma yini, tshela udokotela wakho ngokushesha.
  • Ngemva kokwelashwa, bona udokotela wakho ukuze ahlolwe isikhumba okungenani njalo ezinyangeni ezintathu kuya kweziyisithupha eminyakeni emithathu yokuqala. Bese uya kohlolwa kanye ngonyaka, noma njengoba kuqondiswe udokotela wakho.
  • Nciphisa ukuchayeka elangeni. Imisebe ye-UV evela elangeni yandisa ingozi yeminye imidlavuza yesikhumba. Ngakho-ke, gqoka isivikelo selanga uma uphuma elangeni, gqoka izingubo zokuzivikela , futhi unciphise isikhathi sakho ngaphandle ngesikhathi sosuku olushisa kakhulu.

Kufanele ngimbone nini udokotela?

Uma ubona noma yiziphi izinguquko ezintsha esikhumbeni sakho, ikakhulukazi uma unanoma yikuphi kwalokhu okulandelayo, qiniseka ukuthi ubona udokotela:

  • Amaqhubu noma amabala amasha, aqhubekayo, noma ukukhula kwesikhumba okusha.
  • Izinguquko kuma-warts, ama-birthmarks, ama-scar amadala, noma ama-tattoo.
  • Uma amaqhubu esikhumbeni ephuma igazi kalula.

Khumbula, izinguquko zesikhumba ngokuvamile azinangozi. Kodwa-ke, ezinye izinguquko zingaba uphawu lomdlavuza wesikhumba. Ngakho-ke, uma unemibuzo, kungcono ukubona udokotela ukuze akulungise.

Yini okufanele ngiyibuze udokotela wami?

Uma kutholakale ukuthi une-DFSP, ungase ufune ukubuza udokotela wakho imibuzo efana nalokhu:

  • Kungani ngithole lo mdlavuza wesikhumba?
  • Ingabe ngisengozini yokuthola ezinye izinhlobo zomdlavuza wesikhumba?
  • Yikuphi ukwelashwa okungcono kakhulu kimi?
  • Ingabe ikhona ingozi yokuthi lo mdlavuza usabalale kwezinye izingxenye zomzimba?
  • Kufanele ngize kangaki ukuzohlolwa umdlavuza?

Ukwazi izimpendulo zale mibuzo kuzokusiza ukuthi uqonde kangcono lesi simo futhi kungakusiza ukuthi ucacise ukwelashwa kwakho kanye nezinhlelo zakho zesikhathi esizayo.

Okokugcina, izinto okufanele uzikhumbule

Nakuba i-DFSP ingumdlavuza wesikhumba ongavamile, akunakwenzeka ukuthi isakazekele kwezinye izingxenye zomzimba. Kodwa-ke, ukwelashwa ngokuhlinzwa kubalulekile ukuze kumiswe ukukhula. Ukutholwa kusenesikhathi kanye nokwelashwa okufanele kungathuthukisa kakhulu umbono wakho. Ngakho-ke, qaphela isikhumba sakho futhi ubone udokotela uma ubona noma yini engavamile. Awuwedwa, futhi kukhona odokotela abangakusiza kulolu hambo.


` I-DFSP, umdlavuza wesikhumba, umdlavuza wesikhumba, amaqhubu esikhumba, ukuhlinzwa kwe-Mohs, izimpawu zomdlavuza, izifo zesikhumba

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

No comments yet. Be the first to share your thoughts here.

Add Your Comment

Please calculate: 9 + 5 =