Uma sibheka isisu somntwana osanda kuzalwa, sivame ukusibona sibushelelezi futhi sigcwele, akunjalo? Kodwa cabanga, ngezinye izikhathi, ngokungalindelekile, sibona ukuthi isikhumba esiswini somntwana sishwabene kakhulu, njenge-prune. Uma ubona lokhu, njengomama noma ubaba, ungase uzizwe wesaba kakhulu futhi ushaqekile. "O, kwenzekeni enganeni yami?" Ungase ucabange. Lesi empeleni yisimo esingavamile kakhulu. Namuhla sikhuluma ngesimo esingavamile esingadala lokhu, okungukuthi i-Prune Belly Syndrome . Ungakhathazeki, sizoxoxa ngakho konke kalula nangokucacile.
Kalula nje, iyini i-Prune Belly Syndrome?
I-Prune Belly Syndrome yisifo esingavamile esizalwa naso. Igama laso livela ngoba isikhumba esiswini somntwana sibukeka njenge-prune. Sinezimpawu ezintathu eziyinhloko. Yingakho ngezinye izikhathi sibizwa ngokuthi 'i-Triad Syndrome'. Sibizwa nangokuthi 'i-Eagle-Barrett Syndrome' ukuhlonipha odokotela abasitholile.
Lezi zici ezintathu eziyinhloko yilezi:
1. Imisipha yesisu ebuthakathaka noma engekho: Isisu sethu sinemisipha eminingi esiza ukugcina isimo saso futhi sivikele izitho ezingaphakathi, njengamathumbu. Ezinganeni ezinalesi sifo, le misipha ayikhuli kahle. Ngezinye izikhathi ayakheki nhlobo. Yingakho isikhumba esiswini sibukeka sishwabene futhi sigobile.
2. Amasende angakaphumi: Kumntwana wesilisa, amasende avame ukutholakala ngaphandle komzimba esinqeni samabele. Kodwa-ke, ezinganeni ezinalesi simo, amasende atholakala ngaphakathi esiswini. Awakaphumi.
3. Izinkinga zesistimu yomchamo: Lena yingxenye ebucayi kakhulu yesimo. Izinso zengane, isinyi, kanye namapayipi axhumanisa zona (ama-ureter) akukakhuli ngokugcwele. Lokhu kungabangela izinkinga ezinkulu ngokuchama.
Ngaphezu kwalezi zimpawu ezintathu eziyinhloko, ezinye izingane zingase zibe nezinkinga ezahlukahlukene ngenhliziyo, amaphaphu, amathumbu kanye nesistimu yamathambo.
Sivame kangakanani lesi simo?
Lesi yisimo esingavamile kakhulu. Sithinta cishe ingane eyodwa kwezingu-30,000 kuya kwezingu-40,000 ezisanda kuzalwa. Okukhethekile ukuthi u-95% walezi zimo zibikwa kubafana . Lokho kungenxa yokuthi inkinga yamasende angakakhuli esikhulume ngayo ekuqaleni ithinta abafana kuphela.
Yiziphi izimpawu ezingakusiza ukuthi ubone ukuthi ingane yakho inalesi simo?
Kuthiwa i-Prune Belly Syndrome inezimpawu ezingaphezu kuka-50. Kodwa-ke, lezi zimpawu zingahluka kusuka kusana kuya kosana. Ezinye izingane zingase zithinteke kakhulu, kanti ezinye zingase zingabi zimbi kangako. Udokotela wakho uzohlola ingane yakho futhi enze izivivinyo ezidingekayo ukuqinisekisa lokhu ngokuqinisekile.
Ake sibheke ithebula elingezansi ukuze sibone ukuthi yiziphi izimpawu ezivame kakhulu.
| Isibonakaliso | Incazelo elula |
|---|---|
| Isikhumba esishwabene esiswini | Ngenxa yemisipha yesisu ebuthakathaka noma engekho, isikhumba singagoba futhi sibonakale sishwabene njenge-raisin. |
| Ukuba nesisu esikhulu | Ngenxa yokuthi azikho imisipha esiswini, izinto ezifana namathumbu angaphakathi zibonakala sengathi ziyaphuma. Ngezinye izikhathi, amathumbu asontekile angabonakala ngesikhumba esincane. |
| Amasende Angaphansi | Ezinganeni zesilisa, i-testicle eyodwa noma zombili zihlala ngaphakathi esiswini ngaphandle kokwehla ziye emathunjini. |
| Izinkinga zesistimu yomchamo | Izinkinga ezinkulu ezifana nokukhula kwesinyi kanye nezinso, ukuvaleka kwe-urethra, kanye ne-vesicoureteral reflux. |
| Izinkinga zesistimu yokugaya ukudla | Izinkinga zamathumbu nezimo ezifana nokuqunjelwa. |
| Izinguquko ohlelweni lwamathambo | Izimo ezifana ne-scoliosis noma i-clubfoot. |
| Izinkinga zenhliziyo | Isifo senhliziyo esizalwa naso noma izinguquko ezithile esakhiweni senhliziyo. |
Kungani lokhu kwenzeka ezinganeni?
Uma ngikhuluma iqiniso, odokotela abakayitholi imbangela eqondile yalokhu, kodwa kunemibono eminingana.
Abanye odokotela bakholelwa ukuthi lesi simo sibangelwa ukungajwayelekile kwesinyeni okwenzeka ngesikhathi umntwana ekhula esibelethweni. Okusho ukuthi, lapho umgudu womchamo uvaleka, wonke umchamo uqoqana esinyeni bese uvuvukala kakhulu. Njengoba esinyeni sikhula ngale ndlela, siphazamisa ukukhula kwemisipha yesisu.
Abanye bakholelwa ukuthi le nkinga yenzeka ngoba imisipha yesisu ayikhuli kahle kwasekuqaleni. Abanye bathi kungenzeka ukuthi ibangelwa yimbangela yofuzo. Lesi simo sibikwe nakwabanye abafowabo nodadewabo. Futhi, ezinye izingane ezinezinkinga ze-chromosome ezifana ne-'Trisomy 18 (Edwards Syndrome)' kanye ne-'Trisomy 21 (Down Syndrome)' nazo ziyabhekana nale Prune Belly Syndrome.
Yiziphi izinkinga ezingaba khona ngenxa yalesi simo?
Ubunzima be-Prune Belly Syndrome buxhomeke kwezinye izinkinga ezihlobene nayo, ikakhulukazi izinga lomonakalo ohlelweni lomchamo.
Izinkinga ezivame kakhulu yilezi:
- Ukuqunjelwa: Imisipha yesisu ebuthakathaka yenza kube nzima ukusunduza ngamandla ukuze kuphume indle.
- Ukukhubazeka kwamathambo: izinto ezifana nokuhlukana kwezinqe, ukukhubazeka kwezandla, iminwe, noma izinzwane.
- Ukutheleleka njalo komgudu womchamo: Ukutheleleka kungenzeka kalula ngoba umchamo awukhishwa kahle. Lokhu kutheleleka kungalimaza izinso.
- Ukungazali: Ukwehluleka kwamasende ukwehla kungathinta ikhono lokuba nabantwana esikhathini esizayo. Kukhona futhi nengozi yomdlavuza wamasende.
- I-Pulmonary Hypoplasia: Amaphaphu angase angakhuli kahle ngenxa yokuntuleka kwesikhala esibelethweni.
- Ukwehluleka Kwezinso Okungapheli: Lena inkinga enkulu kakhulu. Izinkinga eziqhubekayo ohlelweni lomchamo zingaholela ekuhlulekeni kwezinso kancane kancane.
Lesi simo sitholakala kanjani?
Ezimweni eziningi, lesi simo singatholakala kusenesikhathi ngesikhathi sokukhulelwa kwakho nge-ultrasound scan yengane.Odokotela bazosola lokhu uma ukuhlolwa kukhombisa ukuthi isinye somntwana sikhulu kakhulu noma izinso zivuvukele. Ukuhlolwa kungabonisa nokuthi umntwana akanayo imisipha yesisu.
Ngemva kokuzalwa kwengane, udokotela angase asole lokhu ngokusekelwe ekubukekeni kwengane kwangaphandle, okungukuthi, ukubukeka kwesisu okushwabene. Ngemuva kwalokho, kwenziwa izivivinyo ezahlukahlukene ukuqinisekisa lesi sifo nokunquma izinga lomonakalo wezitho zomzimba.
Yiziphi izivivinyo ezenziwayo?
- Ukuhlolwa Kwegazi: Funda ngokusebenza kwezinso.
- I-Ultrasound Scan: Hlola isimo sezitho zomzimba ngaphakathi kwesisu, njengezinso kanye nesinye.
- I-X-ray: Ukuhlola noma yiziphi izinkinga ohlelweni lwamathambo.
- I-CT Scan noma i-MRI Scan: Thola isithombe esicacile nesiningiliziwe sezitho zomzimba.
- I-VCUG (i-Voiding Cystourethrogram): Lokhu ukuhlolwa kwe-X-ray okukhethekile. Lokhu kuhilela ukufaka uketshezi olukhethekile esinyeni bese ubuka uketshezi lugeleza ngalo njengoba umntwana echama. Lokhu kusiza ekunqumeni ukuthi umchamo ugeleza ubuyela emuva yini (i-reflux).
Yiziphi izindlela zokwelapha lokhu?
Ukwelashwa kwe-Prune Belly Syndrome kuyahlukahluka kuye ngosana. Ngoba akuzona zonke izingane ezithinteka ngendlela efanayo. Ngokuvamile, ithimba lochwepheshe, njengodokotela bezingane, odokotela bezifo zomchamo wezingane, kanye nodokotela bezifo zezinso, basebenzisana ukuthuthukisa uhlelo lokwelapha olungcono kakhulu lomntwana wakho.
Uma unquma ukwelashwa, lezi zici ziyacatshangelwa:
- Impilo yomntwana iyonke.
- Ubudala bomntwana.
- Ubunzima besifo nokuthi yiziphi izitho zomzimba ezilimele.
- Ikhono lomntwana lokubekezelela ukuhlinzwa nokwelashwa.
- Imibono nezifiso zenu njengabazali.
Ezinye izingane zingadinga ukuqhubeka zithatha ama-antibiotic ukuze zivimbele ukutheleleka komgudu womchamo uma izimpawu zazo zingembi kakhulu.
Kodwa-ke, izingane eziningi kuzodingeka zenze ukuhlinzwa okuningana. Lokhu kuhlinzwa kuhloselwe ukuqinisa udonga lwesisu, ukwehlisa amasende, nokulungisa izinkinga ohlelweni lomchamo.
Kunezinhlobo eziningana eziyinhloko zokuhlinzwa ezenziwayo:
- Ukuhlinzwa kwe-Vesicostomy: Lokhu kuhilela ukwenza imbobo encane esiswini esingezansi iye esinyeni. Lokhu kuvumela umchamo ukuthi uphume ngqo. Lokhu kunganciphisa umonakalo ezinso.
- I-Orchiopexy: Lokhu kuhilela ukuhambisa amasende ngokuhlinzwa, atholakala ngaphakathi esiswini, ehlele phansi aye emasendeni bese ewalungisa.
- I-Cystoplasty: Lokhu kuyindlela yokuhlinzwa eyinkimbinkimbi kancane. Kuhilela ukwakha kabusha ngokuphelele isinyi.
Kwezinye izimo ezinzima, uma izinso zingasebenzi kahle ngokuphelele,Kungadingeka nokufakelwa izinso.
Lizoba njani ikusasa lalaba bantwana?
Ngiyazi ukuthi lokhu kunzima ukukuzwa. Kodwa kubalulekile ukwazi iqiniso. Isikhathi sokuphila salezi zingane sincike ebunzimeni besifo. Ngeshwa, phakathi kuka-10% no-25% wezingane ziyafa esibelethweni noma zife ngenxa yezinkinga phakathi namasonto ambalwa okuqala okuzalwa.
Kodwa, kukhona uhlangothi oluhle. Cishe ama-40% ezingane ezine-Prune Belly Syndrome, naphezu kokuba nezinkinga ezincane ohlelweni lwazo lomchamo, zigcina ukusebenza kwezinso okuvamile futhi ziphila impilo evamile kakhulu.
Abanye abangu-30% bangadinga ukufakelwa izinso ngesikhathi esithile empilweni yabo. Okubaluleke kakhulu, noma ubani onalesi simo udinga ukuba ngaphansi kokuqashwa kwezokwelapha impilo yakhe yonke. Ukuqapha njalo uhlelo lomchamo kubalulekile ukuze kuncishiswe noma yimuphi umonakalo ezinso.
Ungayinakekela kanjani ingane yakho nokuthi kufanele ubonane nini nodokotela?
Uma ingane yakho itholakale ine-Prune Belly Syndrome, into ebaluleke kakhulu ukuthola udokotela onolwazi onolwazi ngalesi simo. Uzochaza konke kuwe futhi akuqondise ukuthi ungayinakekela kanjani ingane yakho.
Izifo Zomgudu Womchamo (UTIs) ziyingozi kakhulu kulezi zingane. Ngakho-ke, uma ubona ngisho nophawu oluncane lokutheleleka komgudu womchamo, kufanele ushayele udokotela wakho ngokushesha.
| Izimpawu okufanele uziqaphele uma kwenzeka ukutheleleka ngomchamo | |
|---|---|
| Umkhuhlane noma ukubanda | Isidingo sokuphuza njalo |
| Kunesidingo esiphuthumayo sokuchama, kodwa kuphuma inani elincane kuphela. | Ukushisa noma ubuhlungu lapho uchama |
| Ubuhlungu besisu noma umhlane ongezansi | Umchamo omnyama noma onamafu |
| Iphunga elinamandla nelingathandeki elivela emchameni | Igazi emchameni |
Uma ubona noma yiziphi zalezi zimpawu, ungalibali. Funa iseluleko sezokwelapha ngokushesha. Futhi, kubalulekile ukuya emitholampilo ngezikhathi ezihleliwe bese uhlola ingane yakho, njengoba udokotela encoma.
Umlayezo Wokuya Nawe Ekhaya
- I-Prune Belly Syndrome yisimo esingavamile sokuzalwa esibangela imisipha yesisu ebuthakathaka, amasende angakhuli kahle, kanye nezinkinga zomchamo.
- Leli gama livela eqinisweni lokuthi isikhumba esiswini somntwana sibukeka sigobile njenge-raisin.
- Lesi simo singatholakala kusenesikhathi ngokusebenzisa ama-scan ngesikhathi sokukhulelwa.
- Izindlela zokwelapha ziyahlukahluka kuye ngesimo somntwana, futhi kuvame ukudingeka ukuhlinzwa okuningi.
- Ukutheleleka komgudu womchamo kuyingozi kakhulu kulaba bantwana. Uma ubona ngisho nophawu oluncane lokutheleleka, bona udokotela ngokushesha.
- Lezi zingane zidinga ukubhekwa nokunakekelwa impilo yonke kodokotela abangochwepheshe. Ngokuphathwa okufanele, izingane eziningi zingaphila impilo enhle.
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