So wowɔ Sickle Cell Yare? Enti sɛ wo koko yɛ wo yaw a, nnni agoru! Eyi fa Acute Chest Syndrome ho!

So ɛtɔ mmere bi a wo koko yɛ wo yaw mpofirim na ɛyɛ den sɛ wobɛhome? Sɛ saa nsɛnnennen yi de nneɛma te sɛ ɔfe ne atiridii ba, titiriw sɛ woyɛ obi a wowɔ tebea bi a wɔfrɛ no Sickle Cell Disease (SCD) , mfa eyi nyɛ hwee. Efisɛ saa sɛnkyerɛnne ahorow yi betumi ayɛ tebea bi a emu yɛ den kɛse a wɔfrɛ no `Acute Chest Syndrome` ho sɛnkyerɛnne. Mma ɛnhaw wo, yɛbɛka eyi ho asɛm pefee na ɛnyɛ den nnɛ.

Dɛn ne Acute Chest Syndrome? Sɛ yɛbɛka no tiawa a...

Okay, afei hwɛ. Saa `Acute Chest Syndrome` yi yɛ ɔhaw a ebetumi ayɛ aniberesɛm a efi sickle cell yare (`SCD`) mu ba . Sɛ yɛbɛka no tiawa a, ɛyɛ bere a wowɔ koko mu yaw, ɔfe, atiridiinini, oxygen dodow a ɛba fam wɔ wo mogya mu, na nneɛma a ɛnyɛ ne kwan so, titiriw nsu, fi ase boaboa ano wɔ ahurututu mu ntini no mu (`lung infiltrates`).

Saa tebea yi betumi ayɛ nea emu yɛ den ntɛmntɛm paa . Nokwarem no, saa `Acute Chest Syndrome` yi yɛ ade titiriw a ɛma nnipa a wɔwɔ sickle cell yare no kɔ ayaresabea na ɛtɔ mmere bi a wowuwu . Enti, ɛho hia paa sɛ yehu eyi.

Seesei ebia woresusuw nea Sickle Cell Disease (SCD) yɛ ho. Momma yɛnkae wo ho asɛm kakra. Ɛyɛ awosu mu yare . Ɛno kyerɛ sɛ ɛyɛ agyapade. Ɛka protein a ɛwɔ yɛn mogya mu nkwammoaa kɔkɔɔ a wɔfrɛ no hemoglobin mu no . Bere a obi a ɔwɔ apɔwmuden mogya mu nkwammoaa kɔkɔɔ yɛ kurukuruwa no, obi a ɔwɔ SCD mogya mu nkwammoaa kɔkɔɔ no te sɛ nkankyee (te sɛ ɔsram a ɛyɛ ɔsram). Enti saa nkwammoaa a ɛte sɛ nkankyee yi ntumi mfa yɛn mogya ntini a ɛyɛ tratraa no mu ntɛm. Afei, hemoglobin no ntumi mfa mframa pa nkɔ nipadua no nyinaa mu yiye. Eyi ne ɔhaw titiriw a ɛwɔ SCD ho.

Acute Chest Syndrome abu so dɛn?

Nokwarem no, `Acute Chest Syndrome` yɛ tebea a abu so yiye wɔ nnipa a wɔwɔ sickle cell yare (`SCD`) mu. Sɛnea akontaabu kyerɛ no, nnipa a wɔwɔ `SCD` no mu bɛyɛ fã behyia saa tebea yi anyɛ yiye koraa no pɛnkoro wɔ wɔn asetra mu . Ɛwom sɛ ɛte sɛ nea abu so kɛse wɔ mmofra nkumaa a wɔadi fi mfe 2 kosi 4 mu de , nanso ebetumi ayɛ kɛse wɔ mpanyimfo mu sen mmofra . Wɔahu nso sɛ nnipa a wɔwɔ `SCD` ne ayamtu no wɔ asiane kɛse mu sɛ wobenya `Acute Chest Syndrome` sen afoforo.

Dɛn nti na Acute Chest Syndrome ba? Dɛn na ɛde ba?

Nyansahufo da so ara ntumi nka nea ɛde `Acute Chest Syndrome` ba ankasa. Nanso wogye di sɛ ebia ade biako anaa nea ɛboro saa na ɛde ba. Momma yɛnhwɛ nea wɔyɛ:

• Nnompe mu ntini a ɛyɛ mmerɛw:So wunim sɛ nnompe mu ntini ne ɔfã a ɛyɛ mmerɛw na ɛyɛ spongy wɔ yɛn nnompe akɛse no mu? Sɛ saa nnompe mu ntini yi wu wɔ ɔkwan bi so (a wɔfrɛ no `necrosis`) a, ne asinasin nketenkete betumi abubu na akɔ mogya no mu na atu kwan akɔ nipadua no nyinaa mu. Sɛ saa asinasin yi tu kwan kɔ ahurututu mu a, ebetumi ama `Acute Chest Syndrome` aba.
• Srade a ɛwɔ nipadua no mu: Ade foforo a ebetumi ama nnompe mu ntini a ɛyɛ adwuma yiye a yɛaka ho asɛm wɔ atifi hɔ no aba ne srade a ɛma nipadua no yɛ adwuma . Sɛ yɛbɛka no tiawa a, eyi ne bere a srade bi (susuw ho sɛ ngo a ɛtɔ gu fam) kɔhyɛ mogya ntini bi mu na esiw mogya no kwan . Eyi nso betumi ama obi anya Acute Chest Syndrome.
• Nyarewa : Nyarewa ahorow, titiriw ahurututu mu yare a mmoawa anaa mmoawa de ba , betumi ama obi anya koko mu yare a emu yɛ den. Nyarewa na ɛde tebea yi ba mmofra nkumaa so titiriw . Nanso, wɔ mpanyimfo mu no , ɛda adi sɛ srade a ɛma mogya tu na ɛde ba.

Dɛn ne obi a ɔwɔ Acute Chest Syndrome ho sɛnkyerɛnne?

`Acute Chest Syndrome` ho sɛnkyerɛnne betumi ayɛ soronko wɔ onipa biara ho. Nsonsonoe bi wɔ hɔ, titiriw wɔ mmofra nkumaa ne mpanyimfo ntam. Mmofra nkumaa taa da ɔyare mmoawa ho sɛnkyerɛnne a ɛsen biara adi:

• Ɛwa
• Huraeɛ
• Oxygen dodow a ɛso tew wɔ mogya mu (hypoxemia) .
• Ɔhome a ɛkɔ ntɛmntɛm wɔ ɔkwan a ɛnteɛ so (tachypnea) .
• Wheezing (nnyigyei a efi koko mu ba bere a wɔrehome) .

Mpanyimfo nso betumi anya saa sɛnkyerɛnne ahorow yi. Nea ɛka ho no, ebia wobɛhyɛ no nsow nso sɛ:

• Koko mu yaw , titiriw bere a ɔrehome no betumi ayɛ kɛse.
• Ɛyaw a emu yɛ den, mpofirim wɔ nsa, anan, ne akyi a mogya a ɛsiw (a wɔsan frɛ no `vaso-occlusive crisis`) de ba.
• Nsu a ɛboaboa ano wɔ ahurututu ne koko mu (pleural effusion).
• Ɔhome a ɛyɛ den (dyspnea).

Sɛ wowɔ saa sɛnkyerɛnne ahorow yi mu biako anaa nea ɛboro saa, titiriw sɛ wowɔ SCD a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu ntɛm ara .

Ɔkwan bɛn so na wohu sɛ obi anya Acute Chest Syndrome? (Nyare a Wɔahu) .

Sɛ wohu `Acute Chest Syndrome` ntɛm a, ebetumi agye obi nkwa.Sɛ wowɔ SCD na wɔde wo akɔ ayaresabea a, ɛho behia sɛ wɔhwɛ wo daa na wɔyɛ nhwehwɛmu a ɛho hia. Nhwehwɛmu ahorow pii wɔ hɔ a ebetumi aboa nnuruyɛfo ma wɔahu ɔhaw yi:

• Mogya mu mframa a ɛwɔ ntini mu nhwehwɛmu: Eyi betumi akyerɛ sɛnea wo mogya mu acid (pH), oxygen, ne carbon dioxide dodow te.
• Mogya mu nhwehwɛmu: Sɛ wokan mogya a edi mũ a , ebetumi ama woanya wo mogya mu nkwammoaa kɔkɔɔ, wo mogya mu nkwammoaa fitaa, ne mogya nkwammoaa ho nsɛm.
• Chest X-ray: Wobetumi de eyi ahwɛ sɛ ahurututu mu nyarewa anaasɛ saa nneɛma a ɛnteɛ (infiltrates) a yɛadi kan aka ho asɛm no aboaboa ano anaa.
• Amammerɛ: Saa nhwehwɛmu ahorow yi boa ma wohu nyarewa ahorow denam wo mogya, wo nsu, anaa wo nipadua mu nsu afoforo a wɔhwehwɛ mu no so.

Wo duruyɛfo betumi agyina nhwehwɛmu yi mu aba ne wo sɛnkyerɛnne ahorow so akyerɛ sɛ Acute Chest Syndrome yɛ nea emu nyɛ den, ɛyɛ mmerɛw, anaasɛ emu yɛ den .

Dɛn ne ayaresa ahorow a wɔde sa Acute Chest Syndrome?

Wɔ tebea yi mu no , ayaresa a wobefi ase ntɛm no ne ɔkwan a eye sen biara a wɔbɛfa so asiw nsɛnnennen a emu yɛ den ano . Ayaresa a wobetumi apaw bi ne:

• Mogya a wɔde ma: Eyi hwehwɛ sɛ woyi wo mogya no bi na wɔma wo mogya anaa mogya no mu nneɛma bi fi obi a ɔde mogya ma wo hɔ.
• Nsu a wɔde fa IV mu: Eyi boa ma wosiw nsu a ɛho nhia (nsu a ɛtwetwe), a ebetumi ama sickle cell yare no ayɛ kɛse na ama ɛyaw no ayɛ kɛse no ano.
• Nnuru a wɔde kum ɛyaw: Wobetumi de nnuru te sɛ `ketorolac` anaa `opioids` ama de asiw ɛyaw ano.
• Spirometer a Ɛkanyan: Saa afiri ketewa yi boa wo ma wohome denneennen. Ɛboa ma w’ahurututu ho tew na ɛyɛ adwuma yiye.
• Oxygen ayaresa a wɔde ka ho: Sɛ oxygen dodow a ɛwɔ mogya no mu no sua a, wɔma oxygen.
• Nnuru a ekum ɔyare mmoawa: Sɛ ɔyare mmoawa bi na ɛde tebea yi ba a, wɔma no nnuru a ekum ɔyare mmoawa.
• Nnuru a ekum ɔyare mmoawa: Sɛ nea ɛde ba no yɛ ɔyare mmoawa a, wɔma no nnuru a ɛfata a ekum ɔyare mmoawa.

So wobetumi atew asiane a ɛwɔ hɔ sɛ obi benya Acute Chest Syndrome no so?

Sɛ wowɔ sickle cell disease (SCD) a, ɛho hia sɛ wo ne w’aduruyɛfo kuw no kasa fa akwan a wobɛfa so asiw Acute Chest Syndrome ano ho. Ebia wɔbɛkyerɛ nneɛma te sɛ:

• Toa a wobɛbɔ mu daa: Ɛwom sɛ ebia ɛbɛyɛ te sɛ nea ɛyɛ mmerɛw de, nanso eyi boa ma wo mframa kwan no mu da hɔ na ɛtew nsu a ɛho nhia a ɛboaboa ano wɔ w’ahurututu ho no so.
• Apɔw-mu-teɛteɛ a wobɛyɛ no daa: Eyi betumi ama w’ahurututu mu ahoɔden ayɛ kɛse.
• Mogya a wɔde ma daa: Ebia nnipa binom behia eyi.
• Nnuru te sɛ `Hydroxyurea` anaa `L-glutamine` a wɔnom: Saa nnuru yi betumi aboa ma ɛyaw so atew na ɛtew asiane a ɛwɔ ayaresabea a wɔbɛtaa akɔ no so. Nanso, ɛsɛ sɛ wɔfa eyinom wɔ nnuruyɛfo afotu ase nkutoo.

Dɛn ne obi a ɔwɔ saa tebea yi ho anidaso (wɔn ho bɛtɔ no)?

Ɛho hia sɛ wohwehwɛ ayaresa ntɛm ara bere a `Acute Chest Syndrome` aba no. Sɛ wɔanyɛ saa a, ebetumi de nsɛnnennen a emu yɛ den te sɛ:

• Acute Respiratory Distress Syndrome (ARDS): Eyi yɛ ahurututu mu yare a emu yɛ den a ebetumi de nkwa ato asiane mu.
• Adwene mu tebea a ɛsakra.
• Asaabo mu opira.
• Mmɛn a ɛnyɛ adwuma yiye.
• Akwaa ahorow pii a entumi nyɛ adwuma yiye.
• Ɔhome a entumi nyɛ adwuma yiye koraa.
• Ɛyaw a emu yɛ den yiye.
• Nea ɛyɛ awerɛhow no, owu mpo betumi aba.

Sɛnea akontaabu kyerɛ no, nnipa dodow a wowuwu wɔ `Acute Chest Syndrome` mu wɔ mpanyimfo mu no bɛyɛ 4% . Wɔ mmofra mu no, saa dodow yi bɛyɛ 1% . Eyi kyerɛ sɛ wobetumi agye nnipa pii nkwa denam ayaresa a wɔyɛ no ntɛm so.

Afei nso, kae sɛ sɛ wɔsa `Acute Chest Syndrome` yiye na wɔsa no yiye mpo a, obi a ɔwɔ `SCD` no betumi anya saa tebea yi bio daakye .

Mewɔ sickle cell yare. Sɛ minya Acute Chest Syndrome ho sɛnkyerɛnne ahorow a, dɛn na ɛsɛ sɛ meyɛ?

Eyi ne ade a ɛho hia sen biara. Sɛ wowɔ SCD na wufi ase nya Acute Chest Syndrome ho sɛnkyerɛnne biara (koko mu yaw, ahome a ɛyɛ tiaa, ɔfe, atiridii) a, nkyɛ simma biako na hwehwɛ aduruyɛfo afotu ntɛm ara .

• Ka kyerɛ nnuruyɛfo no sɛ wowɔ sickle cell yare bere a wokɔ baabi a wɔhwɛ wɔn a wɔwɔ ayaresa a egye ntɛmpɛ anaa ayaresabea foforo no.
• Bisa sɛ wɔnyɛ wo koko X-ray ntɛm ara . Eyi betumi asi so dua ntɛm ara sɛ ebia wowɔ Acute Chest Syndrome na woafi ase sa yare ntɛm.

Kae sɛ, sɛ woyɛ ade ntɛm wɔ bere a ɛte sɛɛ mu a, ebetumi aboa kɛse ma woagye wo nkwa.

Nkrasɛm a Wɔde Kɔ Fie

Seesei wunim sɛ `Acute Chest Syndrome`, a yɛaka ho asɛm no yɛ ɔhaw a ebetumi ayɛ kɛse wɔ sickle cell yare mu. Nsɛnkyerɛnne titiriw ne koko mu yaw, ahome a ɛyɛ tiaa, ɔfe, ne atiridii . Sɛ wowɔ sickle cell yare a, sɛ wuhu saa sɛnkyerɛnne ahorow yi bi a, hwehwɛ aduruyɛfo afotu ntɛm ara .. Mma wo werɛ mmfi sɛ wobɛma wo nnuruyɛfo ahu sɛ wowɔ sickle cell yare. Sɛ wuhu yare no ntɛm na wosa wo yare ntɛm ara a, ɛno ne akwan a eye sen biara a wobɛfa so abɔ wo ho ban afi tebea yi ho. Kɔ so nya apɔwmuden! Koko mu Yare a Ɛyɛ Hu, Sickle Cell Yare, Koko mu Ɛyaw, Ɔhome a Ɛyɛ Den, Koko mu Yare a Ɛyɛ Hu, Sickle Cell Yare, Ahurututu mu Nyarewa