So woanya yafunu mu yaw a emu yɛ den, akisikuru, ne nsu a ɛyɛ tumm a wuntumi nkyerɛkyerɛ mu pɛn? Ɛtɔ mmere bi a, nea ɛde eyi ba no betumi ayɛ tebea bi a ɛntaa nsi a yɛn mu biara nte ho asɛm. Esiane sɛ ɛntaa nsi nti, nnipa pii nnim ho hwee. Ɛnnɛ yɛreka yare a ɛte saa biako ho asɛm, Acute Hepatic Porphyria (AHP). Mma ɛnhaw wo, yɛbɛka eyi ho asɛm tiawa, wɔ ɔkwan a obiara betumi ate ase so.
Sɛ yɛbɛka no tiawa a, dɛn ne Acute Hepatic Porphyria (AHP)?
Acute Hepatic Porphyria, anaa AHP tiawa mu no, yɛ tebea a porphyrins, nnuru bi a wɔyɛ wɔ yɛn nipadua mu, a ɛboaboa ano dodo wɔ mmerɛbo ne nipadua no afã afoforo mu ba. Eyi nyɛ yare biako ankasa, na mmom ɛyɛ nyarewa kuw bi. Sɛ porphyrins boaboa ano wɔ saa kwan yi so a, ebetumi aka ntini ahorow no na ɛde sɛnkyerɛnne afoforo pii a ɛnyɛ dɛ aba.
Ɛwom sɛ wonnya nnyaa saa yare yi ano aduru de, nanso ayaresa a ɛfata betumi aboa ma woadi sɛnkyerɛnne ahorow no so na aboa wo ma woatra ase yiye.
Dɛn nti na saa yare yi ba? Momma yɛnhwehwɛ mu yiye.
Sɛ yɛbɛte eyi ase yiye a, ɛsɛ sɛ yedi kan hu biribi a ɛho hia paa wɔ yɛn nipadua mu. Wɔfrɛ ɛno ' Heme ' .
Heme yɛ protein hemoglobin a ɛwɔ yɛn mogya mu nkwammoaa kɔkɔɔ mu no fã titiriw. Sɛnea wunim no, hemoglobin ne nea ɛgye mframa pa fi ahurututu mu na ɛkyekyɛ kɔ nipadua no nyinaa mu. Enti saa heme yi ho hia ma mmeae te sɛ mmerɛbo, ntini, ne nnompe mu ntini a ɛyɛ adwuma.
Afei hwɛ, sɛ yɛn nipadua yɛ saa ‘heme’ yi a, enzyme ahorow 8 boa ma saa adeyɛ no kɔ so yiye. Ɛte sɛ nea nnuhuam ahorow 8 na ehia na wɔde ayɛ aduan. Sɛ biribi nti enzyme 8 yi mu biara ho nhia anaasɛ ɛyɛ mmerɛw a, ɔkwan a wɔfa so yɛ ‘heme’ no gyae fã. Nea ɛba saa bere no ne sɛ ‘porphyrins’ a yɛadi kan aka ho asɛm a ɛyɛ nneɛma a wɔde yɛ ‘heme’ no fi ase boaboa ano wɔ nipadua no mu .
Wɔ AHP mu no, saa nnuru a wɔfrɛ no ‘ porphyrin ’ yi boaboa ano wɔ mmerɛbo no mu titiriw . Nea efi saa nneɛma a wɔaboaboa ano yi mu ba ne nea ɛda adi sɛ sɛnkyerɛnne ahorow.
| Nsɛnkyerɛnne a wɔtaa hu | Eyi ho nsɛm kakra |
|---|---|
| Yafunu mu yaw a emu yɛ den | Eyi ne sɛnkyerɛnne titiriw ne nea emu yɛ den sen biara. Ebia wubenya yafunu mu yaw a emu yɛ den a wontumi nkyerɛkyerɛ mu a ntease biara nnim. |
| Akisikuru ne ɔfe | Saa tebea yi betumi aba bere a yafunu mu yɛ no yaw kɛse. |
| Nsu a ɛyɛ sum | Nsu betumi ayɛ bruu tuntum anaa kɔkɔɔ. |
| Honam ani a ɛyɛ mmerɛw | Wɔ porphyria ahorow bi mu no, honam ani yɛ mmerɛw kɛse wɔ owia hann ho. |
| Ntini mu ntini mu haw ahorow | Tebea horow a emu yɛ den te sɛ akisikuru, ɛyaw, ntini a ɛyɛ mmerɛw, ne akisikuru betumi aba. |
AHP "ntua" taa fi ase denam yafunu mu yaw a emu yɛ den so. Eyi betumi atra hɔ nna pii. Wɔ tebea horow a ɛtete saa mu no , ɛyɛ ahyɛde sɛ wɔde obi bɛkɔ ayaresabea . Eyi kyerɛ sɛ wobɛkɔ Emergency Department (ETU).
Hena na wonya saa yare yi? Henanom na wɔwɔ asiane mu?
Mpɛn pii no, yare yi fi awosu mu . Ɛne sɛ, wunya awosu mu nkwaadɔm a ɛde yare yi ba no fi w’awofo hɔ.
Nanso ade a ɛho hia wɔ ha ne sɛ ɛnyɛ obiara a ɔwɔ awosu mu abɔde a ɛde yare no ba no na obenya yare no ho sɛnkyerɛnne . Nnipa dodow no ara a wɔwɔ AHP awosu mu abɔde no betumi akɔ so anya apɔwmuden wɔ wɔn nkwa nna nyinaa mu a wonni sɛnkyerɛnne biara.
Eyi te sɛ gyata a wada. Sɛ mpo awosu mu abɔde no wɔ hɔ a, sɛ biribiara nni hɔ a ɛkanyan no, anaasɛ "ɛkanyan" no a, ebetumi atra hɔ a ɔhaw biara nni ho.
Enti dɛn ne nneɛma a ɛkanyan yare yi?
Eyi yɛ ɔfã a ɛho hia paa. Sɛ wo anaa obi a wunim no wɔ AHP a, ɛho hia sɛ wuhu saa nneɛma yi.
| Nkanyan | Nsɛntitiriw a ɛho hia |
|---|---|
| Nnuru bi | Nnuru bi a wɔde kum ɛyaw, nnuru a ɛma obi dwo, barbiturates, nnuru a ɛma obi dwo, ne nnuru a wɔde siw awo ano betumi ayɛ nneɛma atitiriw a ɛkanyan obi. Sɛ wususuw sɛ wowɔ AHP anaasɛ woahu sɛ wowɔ AHP a, nnom nnuru biara a wonkɔ oduruyɛfo nkyɛn. |
| Nsã a wɔnom ne sigaretnom | Ɛnyɛ den sɛ eyinom betumi akanyan yare no efisɛ ɛde nhyɛso kɛse ba mmerɛbo no so. |
| Aduane a wɔde di dwuma katee anaa mmuadadi | Aduan a wodi ano hye anaasɛ wubehuruw adidi de abɔ mmɔden sɛ wɔbɛtew wɔn mu duru so mpofirim no pira ayarefo yi kɛse. Calories a nipadua no hia a wonnya no yɛ ade a ɛkanyan no denneennen. |
| Adwene ne nipadua mu nhyɛso | Nneɛma te sɛ adwennwen a emu yɛ den, oprehyɛn, ne ɔyare mmoawa nso betumi akanyan yare no. |
Dɛn na ɛsɛ sɛ meyɛ?
Sɛ worehu sɛnkyerɛnne ahorow a wɔaka ho asɛm wɔ asɛm yi mu no bi , titiriw yafunu mu yaw a emu yɛ den a wontumi nkyerɛkyerɛ mu daa a , yɛsrɛ sɛ nsusuw sɛ ɛyɛ nea ɛfata. Kɔ oduruyɛfo a ɔfata ntɛm ara.
Oduruyɛfo no bɛhwɛ wo na sɛ ɛho hia a, ɔhyɛ sɛ wɔnyɛ wo nsu, mogya, ne awosu mu nhwehwɛmu na ama woahu sɛ wowɔ yare no anaa.
Aduan a ɛkari pɛ ho hia yiye ma obi a ɔwɔ AHP. Sɛ ɛho hia a, wo duruyɛfo betumi de wo akɔma aduannuru ho ɔbenfo.
Nkrasɛm a Wɔde Kɔ Fie
- Acute Hepatic Porphyria (AHP) yɛ yare a ɛntaa nsi, a wonya fi awo mu a nnuru bi a wɔfrɛ no porphyrin a ɛboaboa ano wɔ mmerɛbo mu na ɛde ba.
- Nea ɛde eyi ba titiriw ne enzyme bi a ɛho hia wɔ ‘heme’ a wɔyɛ mu no a enni hɔ.
- Nsɛnkyerɛnne titiriw ne yafunu mu yaw a wontumi nnyina ano. Ebetumi nso de ntini mu haw ahorow aba.
- Sɛ wowɔ awosu mu abɔde a ɛde yare no ba mpo a, sɛ wokwati nneɛma a ɛkanyan yare no a, ebia worenhu sɛnkyerɛnne biara.
- Nnuru bi, nsa, sigaretnom, aduan a wodi katee, ne adwennwen yɛ nneɛma atitiriw a ɛkanyan no.
- Sɛ wowɔ saa sɛnkyerɛnne ahorow yi bi anaasɛ wususuw sɛ wowɔ AHP a, akyinnye biara nni ho sɛ wo ne oduruyɛfo nkasa. Mma w’ankasa mfi adi nkɔhwehwɛ nnuru da.
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