So wo duruyɛfo aka akyerɛ wo sɛ yɛ G6PD nhwehwɛmu? Anaasɛ worehwɛ sɔhwɛ yi mu esiane sɛ wo ba ketewa no anya jaundice na ɛrenkɔ nti? Ebia woate asɛmfua G6PD no nkyɛe. Ɛyɛ ade a ɛyɛ daa sɛ wobɛbɔ hu kakra efisɛ edin no yɛ nwonwa kakra. Nanso nsuro biribiara. Ɛnnɛ, yɛbɛka saa G6PD sɔhwɛ yi ne G6PD a enni hɔ a ɛde ba no ho asɛm wɔ ɔkwan a ɛyɛ mmerɛw yiye a wubetumi ate ase so.
Momma yenni kan nhwɛ, dɛn ne G6PD?
Okay, momma yɛmfa nhwɛso a ɛyɛ mmerɛw yiye mfi ase. Fa no sɛ mogya mu nkwammoaa kɔkɔɔ a ɛwɔ wo nipadua mu no te sɛ afie nketewa. Wɔ afie yi mu no, adwuma a ɛho hia a ɛne sɛ wɔde mframa pa bɛkɔ no kɔ so. Afei, ɛsɛ sɛ ‘ɔwɛmfo’ bi wɔ hɔ a ɔbɛbɔ afie yi ho ban, na wakɔ so ayɛ den. Enti, odwumayɛni titiriw bi wɔ hɔ a wɔfrɛ no G6PD a ɔbɔ yɛn afie ho ban a wɔfrɛ no mogya mu nkwammoaa kɔkɔɔ na ɔboa ma wɔtra apɔwmuden.
Wɔ aduruyɛ mu no, G6PD ne din tiawa a wɔde frɛ enzyme glucose-6-phosphate dehydrogenase . Enzyme yɛ protein a ɛboa yɛn nipadua ma ɛyɛ nnuru ahorow ahorow yiye. G6PD enzyme yi dwumadi titiriw ne sɛ ɛbɛbɔ yɛn mogya mu nkwammoaa kɔkɔɔ ho ban afi nnuru bi (a wɔfrɛ no reactive oxygen species) a ebetumi asɛe wɔn ho.
Enti, sɛ obi nipadua nni saa ɔwɛmfo, anaa enzyme a wɔfrɛ no G6PD yi a ɛdɔɔso a, yɛfrɛ no G6PD a enni hɔ . Eyi yɛ awosu mu nneɛma, a ɛkyerɛ sɛ wonya fi awo mu. Obi a saa sintɔ yi wɔ mogya mu nkwammoaa kɔkɔɔ dodow a ɛyɛ mmerɛw kakra. Ɛte sɛ ofie a ɔwɛmfo nni mu. Afei, sɛ wɔde wɔn ho hyɛ nneɛma bi mu a, mogya mu nkwammoaa kɔkɔɔ yi fi ase sɛe na ɛsɛe ntɛmntɛm. Sɛ nipadua no ntumi nyɛ mogya mu nkwammoaa kɔkɔɔ foforo na dedaw no sɛe ntɛmntɛm a, tebea bi a wɔfrɛ no mogya a ɛtɔ kɔ nipadua mu ba. Sɛ mogya mu nkwammoaa kɔkɔɔ no sɛe wɔ saa kwan yi so a, yɛfrɛ no mogya a ɛtɔ kɔ mogya mu .
Enti, bere bɛn na ɛsɛ sɛ woyɛ G6PD sɔhwɛ?
Mpɛn pii no, nnipa a wonni G6PD no nkyerɛ yare no ho sɛnkyerɛnne biara. Wɔbɔ wɔn bra sɛnea ɛsɛ. Nanso, ɛyɛ bere a wɔde wɔn ho ahyɛ ‘nneɛma bi a ɛkanyan’ mu nkutoo na mogya a ɛtɔ kɔ mogya mu tebea a yɛadi kan aka ho asɛm no ba na sɛnkyerɛnne ahorow no da adi.
Afei ma yɛnhwɛ nea saa nneɛma a ɛkanyan adwene yi yɛ.
| Nneɛma a ɛkanyan obi a ɛde sɛnkyerɛnne ahorow ba | Nkyerɛkyerɛmu tiawa bi a ɛfa eyi ho |
|---|---|
| Nyarewa bi a wɔde nyarewa ba | Adwennwen a ɛwɔ nipadua no mu a ɔyare mmoawa anaa mmoawa de ba no betumi ama mogya mu nkwammoaa kɔkɔɔ no asɛe ntɛmntɛm. |
| Fava bankye a wɔde yɛ | Eyi ne ade a ɛtaa kanyan tebea yi. Nnipa binom betumi anya yare no ho sɛnkyerɛnne afi fava bankye a wodi anaasɛ wɔn pollen a wɔhome mpo mu. Wɔsan frɛ eyi sɛ ‘favism’. |
| Nnuru bi | Nanso, ɛnyɛ nnuru nyinaa na ebetumi ama tebea no asɛe kɛse, te sɛ nnuru bi a ekum ɔyare mmoawa, nnuru a ekum asramma, ne nnuru a ɛnyɛ steroid a ɛko tia ɔyare mmoawa (NSAID). Enti, sɛ wowɔ G6PD a, ɛho hia sɛ woka kyerɛ wo duruyɛfo ansa na woanom aduru biara. |
Enti, sɛ wuhyia biribi a ɛkanyan wo saa a, ebia wubenya mogya a ɛtɔ kɔ mogya mu a ɛma mogya tu ho sɛnkyerɛnne. Ɛno ne bere a ebia oduruyɛfo bi bɛkyerɛ sɛ wɔnyɛ G6PD nhwehwɛmu. Hwɛ sɛ saa sɛnkyerɛnne ahorow yi te sɛ nea wunim anaa.
| Nsɛnkyerɛnne a ɛkyerɛ | Dɛn na eyi kyerɛ? |
|---|---|
| Ɔtotɔtɔ a ɛba mpofirim (syncope) . | Sɛ amemene no nnya mframa pa a ɛdɔɔso a, ebetumi aba sɛ obi ntumi nhu hwee. |
| Ɔbrɛ kɛse a wɔte nka (Ɔbrɛ) . | Sɛ mogya mu nkwammoaa kɔkɔɔ a ɛde mframa pa kɔ nipadua no mu nyinaa so tew a, ebia wobɛte nka sɛ woabrɛ dodo sɛ wobɛyɛ nnwuma a ɛfata mpo. |
| Sɛ wote nka sɛ wo koma rebɔ ntɛmntɛm | Ɛsɛ sɛ koma no yɛ adwumaden na ama mogya no akɔ ntɛmntɛm na ama nipadua no anya mframa pa a ehia. |
| Ɔhome a ɛyɛ den (dyspnea) . | Sɛ oxygen dodow a ɛwɔ mogya no mu so tew a, ebia wobɛte nka sɛ wo home yɛ den na woate nka sɛ woatɔ piti. |
| Nsu a ɛyɛ kɔkɔɔ anaa bruu | Sɛ mogya mu nkwammoaa kɔkɔɔ pii mu paapae a, emu nneɛma kɔ nsu no mu, na ɛma nsu no kɔla sesa. |
| Wora a ɛyɛ mmerɛw | Sɛ mogya mu dodow so tew a, honam ani kɔla a ɛyɛ pink no hwere na ɛyɛ fitaa. |
| Wora ne aniwa a ɛyɛ kɔkɔɔ (jaundice) . | Sɛ mogya mu nkwammoaa kɔkɔɔ sɛe a, ade kɔkɔɔ bi a wɔfrɛ no bilirubin boaboa ano wɔ nipadua no mu. Eyi na ɛma aniwa honam ani fitaa dan kɔla. |
Dɛn nti na wɔyɛ G6PD nhwehwɛmu ma nkokoaa nkumaa?
Jaundice abu so kɛse wɔ nkokoaa a wɔawo wɔn foforo mu. Mpɛn pii no, n’ankasa befi hɔ wɔ nna kakraa bi kosi adapɛn abien ntam. Nanso, sɛ nkokoaa binom nya jaundice bɛboro adapɛn abien na wontumi nhu nea ɛde ba pefee a, wo duruyɛfo betumi akamfo akyerɛ sɛ wɔnyɛ G6PD nhwehwɛmu.
Bio nso, sɛ wunim sɛ obi wɔ w’abusua mu a G6PD nnim a, ɛyɛ papa sɛ wobɛma wɔayɛ nhwehwɛmu yi bere a wɔawo akokoaa no akyi. Saa kwan no so no, wubetumi adi kan ahu eyi na woayɛ ahwɛyiye.
G6PD a enni nipadua no mu abu so dɛn?
Eyi yɛ awosu mu tebea a abu so kɛse wɔ wiase ankasa. Wogye di sɛ nnipa bɛboro ɔpepem 400 na wɔwɔ saa tebea yi wɔ wiase nyinaa. Nanso, sɛnea yɛadi kan aka no, saa nnipa yi mu dodow no ara renhu sɛnkyerɛnne biara wɔ wɔn nkwa nna nyinaa mu.
G6PD a enni nipadua mu a ɛkyerɛ yare no taa ba mmarima so sen mmea, na ɛtaa ba nnipa a wofi Asia, Afrika, anaa Mediterranea abusua mu.
Ɔkwan bɛn so na wɔyɛ G6PD sɔhwɛ no?
Eyi yɛ mogya mu nhwehwɛmu a ɛyɛ mmerɛw yiye, a wɔyɛ no daa. Biribiara nni hɔ a ɛsɛ sɛ yesuro ɔkwan biara so. Egye nea ennu simma anum.
- Wɔde ade ketewaa bi hyɛ ntini bi a ɛwɔ ɔyarefo bi abasa mu mu na wogye mogya.
- Afei woyi mpaapaemu no na wɔde plaster ketewaa bi gu so.
Nnipa binom suro kakra wɔ nnade ho (wɔfrɛ eyi trypanophobia). Sɛ wowɔ saa ehu yi a, ka kyerɛ ɔyarehwɛfo a ɔtwe wo mogya no. Wɔbɛboa wo. Wubetumi ahwɛ baabi foforo, ahome brɛoo, anaasɛ w’adamfo anaa w’abusua muni bi bɛka wo ho bere a wɔretwe mogya no.
Sɛnea wɔyɛ sɔhwɛ yi ma nkokoaa
Esiane sɛ ɛyɛ den sɛ wobenya mogya afi akokoaa abasa mu nti, wogye mogya fi wɔn nan ase. Wɔde ahwɛyiye kɛse yɛ ade ketewaa bi de tow baabi ketewaa bi wɔ nan ase na wɔboaboa mogya kakraa bi ano. Afei wɔde aduru ketewaa bi a wɔde kyekyere baabi no gu so. Ebia akokoaa no bɛte nka sɛ ɔte nka kakra, nanso eyi befi hɔ ntɛm. Ebia akuru kakra bɛba, nanso eyi bɛsa wɔ da koro anaa nnanu mu.
So ɛsɛ sɛ misiesie me ho ansa na sɔhwɛ no aba?
Eyi yɛ asɛm a ɛho hia paa. Yiw, nneɛma bi wɔ hɔ a ɛsɛ sɛ yɛhwɛ yiye wɔ ho.
- Ka nnuru a wonom nyinaa (a vitamin ne nnuru a wɔde ka aduan ho ka ho) kyerɛ wo duruyɛfo.
- Nnuru ne nnuan bi betumi aka nea efi sɔhwɛ yi mu ba no. Enti ebia wo duruyɛfo bɛka akyerɛ wo sɛ kwati fava bankye a wubedi anaasɛ gyae nnuru bi a sulfa wom nom nna kakraa bi.
- Mpɛn pii no, ɛho nhia sɛ wodi mmuada ansa na sɔhwɛ yi aba.
Biribi a ɛho hia yiye ni: Sɛ wowɔ mogya a ɛtɔ kɔ mogya mu a ɛma mogya tu (e.g., jaundice, ɔbrɛ) ho sɛnkyerɛnne a ɛyɛ nnam da a wobɛyɛ wo nhwehwɛmu no a, ebia wo duruyɛfo bɛtwe nhwehwɛmu no akɔ akyiri akosi da foforo. Eyi te saa efisɛ bere a wubenya yare no ho sɛnkyerɛnne no, mogya mu nkwammoaa kɔkɔɔ a G6PD nnim no taa sɛe. Ɛno ma nkwammoaa a ɛte apɔw nkutoo na ɛka wo mogya mu. Sɛ woyɛ sɔhwɛ saa bere no a, ebia wubenya atoro aba a ɛkyerɛ sɛ wo G6PD dodow no yɛ nea ɛfata.
So asiane ahorow bi wɔ sɔhwɛ yi mu?
Eyi yɛ sɔhwɛ a asiane nnim koraa. Te sɛ mogya mu nhwehwɛmu foforo biara no, .
- Kuru ketewaa bi a wɔde ade no hyɛɛ mu.
- Akuru ketewaa bi
- Ɛntaa mma koraa, mogya anaa ɔyare mmoawa
Nneɛma a ɛte saa betumi asi, nanso mpɛn pii no eyinom sa koraa wɔ da koro anaa nnanu mu.
Dɛn na sɔhwɛ ho amanneɛbɔ no ka?
Sɛ w’amanneɛbɔ kyerɛ sɛ wo G6PD dodoɔ no sua a, ɛkyerɛ sɛ wowɔ G6PD a enni mu. Nanso ɛnkyerɛ sɛ akyinnye biara nni ho sɛ wowɔ mogya a ɛtɔ kɔ mogya mu. Nnipa pii tra ase a wonni yare no ho sɛnkyerɛnne biara. Ade a ɛho hia sen biara ne sɛ wobɛtwe wo ho afi nneɛma a ɛkanyan yare no ho sɛnkyerɛnne ahorow no ho.
Ebia mmea binom G6PD dodow a ɛba fam kakra sen sɛnea ɛte daa. Wei kyerɛ sɛ wɔyɛ ‘asoafoɔ’ ma G6PD a enni hɔ. Sɛ yɛbɛka no tiawa a, wɔwɔ awosu mu abɔde a ɛma G6PD a enni nipadua mu ne awosu mu abɔde a ɛwɔ apɔwmuden no nyinaa wɔ wɔn awosu mu. Mpɛn pii no, saa nkurɔfo yi nnya yare no ho sɛnkyerɛnne biara. Nanso wobetumi de awosu mu abɔde no akɔma wɔn mma.
Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?
Nnipa pii a wonni G6PD no tra ase yiye a nneɛma a ɛkanyan wɔn nni mu. Nanso sɛ wunya mogya a ɛtɔ kɔ mogya mu ho sɛnkyerɛnne ahorow, na saa sɛnkyerɛnne ahorow no bi ne:
- Sɛ emu yɛ den dodo sɛ wobɛyɛ wo da biara da dwumadi ahorow a
- Sɛ ɛkyɛ boro nnɔnhwerew 24-48 a
Kɔ wo duruyɛfo nkyɛn ntɛm ara. Wɔ tebea horow a emu yɛ den mu no, ebia ebehia sɛ wɔde wo kɔ ayaresabea ma wɔsa wo yare. Wɔ tebea a egye ntɛmpɛ a ɛte saa mu no, ɛsɛ sɛ wokɔ Emergency Department (ETU) a ɛwɔ ayaresabea a ɛbɛn wo no.
Nkrasɛm a Wɔde Kɔ Fie
- G6PD yɛ enzyme a ɛho hia a ɛbɔ yɛn mogya mu nkwammoaa kɔkɔɔ ho ban.
- Enzyme yi a enni hɔ (G6PD a enni hɔ) yɛ awosu mu tebea.
- Nnipa pii wɔ saa tebea yi nanso wɔnna yare no ho sɛnkyerɛnne biara adi.
- Sɛ obi nya nneɛma a ɛkanyan obi te sɛ fava bankye, nnuru bi, ne ɔyare mmoawa a, ebetumi ama mogya mu nkwammoaa kɔkɔɔ no asɛe, na ɛde mogya a ɛtɔ kɔ mogya mu a ɛma mogya tu aba.
- G6PD nhwehwɛmu no yɛ mogya mu nhwehwɛmu a ɛnyɛ den a wɔyɛ de hu tebea yi.
- Sɛ wowɔ G6PD a enni hɔ a, ade a ɛho hia sen biara ne sɛ wubehu nea ɛkanyan wo na kwati.
- Nea ɛho hia sen biara: Sɛ wowɔ G6PD a, hwɛ hu sɛ wobɛbɔ wo duruyɛfo amanneɛ ansa na woakyerɛw nnuru foforo biara ama wo.

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