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So worenya nkate horow a ɛyɛ nwonwa wɔ wo nipadua mu? Ebia ɛho hia sɛ wuhu Multiple System Atrophy (MSA) ho asɛm!

So worenya nkate horow a ɛyɛ nwonwa wɔ wo nipadua mu? Ebia ɛho hia sɛ wuhu Multiple System Atrophy (MSA) ho asɛm!

So wote nka da sɛ nneɛma a ɛwɔ wo nipadua mu resakra wɔ akwan horow so a wuntumi nni so? Ɛtɔ da bi a, ɛte sɛ nea worenkari pɛ bere a wonam no, anaasɛ wo ho yɛ wo yaw bere a wosɔre mpofirim no. Eyinom yɛ nneɛma a ɛtɔ mmere bi a yɛmfa yɛn adwene nsi so kɛse, nanso ebetumi ayɛ ntini mu nyarewa bi a wɔntaa nhu ho sɛnkyerɛnne nso. Ɛnnɛ yɛbɛka tebea a ɛte saa biako a ɛyɛ den kakra ho asɛm, nanso ɛho hia yiye sɛ yɛma yɛn ani da hɔ. Ɛno ne Multiple System Atrophy (MSA) .

Dɛn ankasa ne Multiple System Atrophy (MSA)?

Sɛ yɛbɛka no tiawa a, Multiple System Atrophy (MSA)ntini mu yare a ɛntaa nsi a yɛn amemene no afã horow yɛ mmerɛw nkakrankakra, kyerɛ sɛ, ɛsɛe. Bere kɔ so no, yɛn nipadua no dwumadi ne tumi a amemene no afã horow yi di so no fi ase sɛe. Eyi yɛ tebea a emu yɛ den mmom ankasa, efisɛ ɛyɛ den sɛ wobenya ahoɔden afi mu koraa.

Bere bi a atwam no, na wɔde din ahorow pii frɛ MSA. Ebia woate edin ahorow te sɛ `Shy-Drager syndrome`, `Sporadic olivopontocerebellar atrophy`, `Striatonigral degeneration` ho asɛm. Akyiri yi ara na nnuruyɛfo hui sɛ tebea horow yi nyinaa wɔ nneɛma bi a ɛtaa ba. Ɛno nti na wɔkaa wɔn nyinaa boom na wɔmaa wɔn din foforɔ, `Multiple System Atrophy` (MSA). Nsɛnkyerɛnne no gu ahorow gyina amemene no fã a asɛe so. Ɛno nti na ɛsono sɛnea obiara nya sɛnkyerɛnne ahorow a wɔaka abom no.

MSA ahorow abien na ɛwɔ hɔ, ɛnte saa? Dɛn ne wɔn?

Yiw, sɛnea ɛbɛyɛ na wɔahu MSA tebea no pefee no, nnuruyɛfo akyekyɛ mu ayɛ no ahorow atitiriw abien, a egyina sɛnkyerɛnne ahorow a ɛda adi so:

1. MSA-C : 'C' a ɛwɔ ha no gyina hɔ ma `cerebellar'. Saa ɔkwan yi ka sɛnea wutumi yɛ wo kankyee no ho nhyehyɛe titiriw. Ɛne sɛ, wohwere wo kari pɛ , a nnuruyɛfo nso frɛ no `ataxia'. Eyi ne sɛnkyerɛnne titiriw a ɛwɔ saa ɔkwan yi so. Bere koro no ara mu no, wubetumi ahu ɔhaw ahorow nso wɔ nipadua no automatic control systems (`autonomic dysfunction`) ne ahwease a ɛtaa ba no ho.

2. MSA-P : 'P' a ɛwɔ ha no gyina hɔ ma `parkinsonism'. Wɔ saa ɔkwan yi so no, wohu sɛnkyerɛnne ahorow a ɛte sɛ Parkinson yare no. Ɛwom sɛ saa Parkinson sɛnkyerɛnne ahorow yi da adi kɛse wɔ mfiase de, nanso bere kɔ so no, ɔhaw ahorow a ɛwɔ autonomic nervous system ne `ataxia' ho sɛnkyerɛnne nso betumi ada adi.

Henanom na MSA tebea yi ka no kɛse? Ɛtaa ba dɛn?

MSA taa ka mpanyimfo a wɔadi boro mfe 30. Ɛda adi kɛse sɛ yare no ho sɛnkyerɛnne bɛda adi wɔ mfe 50 kosi 59. Ebetumi aka obiara, ɛmfa ho sɛ ɔyɛ ɔbarima anaa ɔbea.

Nanso MSA yɛ tebea a ɛntaa nsi koraa . Abenfo ka sɛ nnipa 100,000 biara mu nnipa foforo 0.6 anaa 0.7 pɛ na wonya afe biara. Wobu akontaa sɛ nnipa dodow a wɔanya yare no nyinaa bɛyɛ 3.4 kosi 4.9 wɔ nnipa 100,000 biara mu. Enti wubetumi ahu sɛnea eyi ho yɛ na.

Dɛn na ɛto nipadua a ɛwɔ MSA no? Amemene no afã horow bɛn na ɛka?

MSA yɛ yare a ɛkɔ so yɛ den a ɛka amemene no afã horow. Nsɛnkyerɛnne no gyina amemene no fã a ɛka no so. Amemene no mmeae atitiriw a MSA ka no ne:

  • Basal ganglia : Eyinom wɔ amemene no mfinimfini pɛɛ. Wɔka amemene no afã horow bom na ɛboa ma wɔbom yɛ adwuma. Ɛte sɛ amemene no dan titiriw a wɔde di dwuma .
  • Brainstem : Eyi ne nea ɛhwɛ nneɛma pii a ɛkɔ so ara kwa wɔ yɛn nipadua mu no so. Ɛne sɛ, nneɛma a ɛba ara kwa a yensusuw ho, sɛ nhwɛso no, ɔhome, koma bɔ, ne mogya mmoroso. Eyinom ho hia na ama obi anya nkwa.
  • Cerebellum : Eyi wɔ ti no akyi, wɔ ase. Ɛyɛ n’asɛyɛde titiriw sɛ ɛhwɛ kankyee so na ɛkari pɛ. Ɛne amemene no afã afoforo nso yɛ adwuma. Nhwehwɛmufo da so ara resua ne dwumadi nyinaa ho ade, nanso adanse bi kyerɛ sɛ ɛka yɛn nkate ne gyinaesi nso ho.

Enti, sɛ amemene no afã horow yi sɛe a, dwumadi ahorow a saa afã horow no di so no ntumi nyɛ yiye. Sɛ nhwɛso no, sɛ `Brainstem` no sɛe a, ɔhaw ahorow a ɛfa nneɛma a ɛyɛ adwuma ankasa te sɛ mogya mmoroso ho betumi aba.

Dɛn ne MSA ho sɛnkyerɛnne ahorow? Yɛyɛ dɛn hu wɔn?

MSA ho sɛnkyerɛnne ahorow bi abu so wɔ ahorow abien no nyinaa mu, na ebi nso yɛ nea ɛfa ɔkwan biara ho pɔtee. Nanso ade biako a ɛtaa ba wɔ ahorow abien no nyinaa mu ne autonomic dysfunction. Sɛ yɛbɛka no tiawa a, wo nipadua no mfiri a ɛma wotumi di nneɛma so no kɔ so yɛ basabasa.

Nsɛnkyerɛnne a efi ɔhaw ahorow a ɛwɔ autonomic nervous system no mu ba:

  • Orthostatic hypotension : Eyi ne bere a wo mogya mmoroso so tew mpofirim, na ɛma w’adwene tu fra , bere a wosakra wo gyinabea, sɛ nhwɛso no, bere a wugyina hɔ mpofirim fi tra ase no.
  • Nsu a wontumi nni so (`urinary incontinence`) ne sɛnea wontumi nni nsu a wɔde gu nsu mu so (`fecal incontinence`).
  • Ɔbarima ne ɔbea nna mu ɔhaw, titiriw wɔ mmarima mu, yɛ den sɛ wobenya ɔbarima ne ɔbea nna mu ahoɔden (rectile dysfunction).
  • Rapid eye movement (REM) sleep behavior disorder : Te sɛ Parkinson yare no, sɛ woda dae a, woyɛ nneɛma a woyɛɛ wɔ w’adaeso mu no ho agoru ankasa. Ebia wobɛteɛteɛm anaasɛ wobɛbɔ wo nsa.
  • Fifiri a ɛso tew (anhidrosis).
  • Anisoadehu mu haw ahorow.
  • Ano a ɛyɛ nwunu.
  • Dae mu ahomegye a ɛyɛ den.
  • Nnuan a wɔyam brɛoo ne akisikuru.

Susuw ho sɛ saa autonomic sɛnkyerɛnne ahorow yi pii betumi ada adi asram pii, mfe pii mpo ansa na ntini mu sɛnkyerɛnne ahorow ada adi. Eyi ba wɔ MSA ayarefo 20% kosi 75% mu.

Adwene ne nkate mu su ahorow

Nnipa a wɔwɔ MSA no mu bɛyɛ nkyem abiɛsa mu biako nya ɔhaw ahorow wɔ sɛnea wotumi susuw nneɛma ho na wɔde wɔn adwene si biribi so no ho. Ɛyɛ den ma wɔn nso sɛ wobedi wɔn nkate so. Eyi betumi de adwenemyare te sɛ:

  • Brɛ.
  • Hahaahayɔ.
  • Nkate mu a entumi nnyina pintinn: Ɛne sɛ, osu ne serew a ɛmfata.
  • Ehu a ɛba obi so.
  • Adwene a ɛne sɛ wobɛpira wo ho anaasɛ wubekum wo ho.

Nneɛma a ɛfa kankyee ho

MSA-C (amemene mu ntini su):

Saa ɔkwan yi fa `ataxia` (kari pɛ a wɔhwere) ho titiriw. `Cerebellum` yɛ amemene no fã bi a edi dwuma titiriw wɔ ntini ahorow a ɛkɔ so no mu. Enti, sɛ saa nkitahodi no yera a, nneɛma te sɛ eyi betumi asi:

  • Akwaa a ɛwɔ nipadua no mu a wontumi nni so, a ɛyɛ basabasa .
  • Action tremor : Eyi kyerɛ sɛ, sɛ wobɔ mmɔden sɛ wobɛyɛ biribi a, wo nsa ne wo nan ase wosow no yɛ kɛse.
  • Nantew a wɔde nan a ɛtrɛw soronko nantew .
  • Aniwa a ɛtwetwe a wontumi nni so (nystagmus).

MSA-P (Parkinsonism type) no su ahorow:

Saa sɛnkyerɛnne yi taa fi ase wɔ nipadua no fã biako na afei ɛtrɛw kɔ afã abien no nyinaa. Saa sɛnkyerɛnne ahorow yi taa te sɛ eyi:

  • Nneɛma a wɔde keka ne ho brɛoo (bradykinesia), a wɔte nka te sɛ nea nkwa nni nipadua no mu .
  • Te a wɔte nka sɛ nipadua no ayɛ den na ayɛ den, na ɛde gyinabea a ɛte sɛ nea ɔde ne ho kɔ n’anim ba.
  • To hintidua a wɔtaa to bere a wɔnantew no.
  • Akasakasa bere a wɔrekasa, kasa a emu nna hɔ .

Dɛn nti na saa MSA yi ba? Dɛn nti na ɛte saa?

Wonnya nhuu nea ɛde MSA ba ankasa , nanso abenfo susuw sɛ ɛne protein bi a wɔfrɛ no `alpha-synuclein`, a ebetumi aboaboa ano wɔ yɛn amemene no afã horow no wɔ abusuabɔ. Wosusuw sɛ protein koro yi ara nso na ɛde Parkinson yare no ba titiriw.

Protein yɛ nnuru a ɛho hia na ama yɛn nipadua ayɛ adwuma. Wɔboa wɔ nneɛma pii mu, te sɛ nkitahodi a ɛda nhyehyɛe ahorow a ɛwɔ nipadua no mu ntam ne nnuru a wɔde di akɔneaba. Nanso, sɛ protein ahorow yi boaboa ano wɔ mmeae a ɛnteɛ a, ebetumi asɛe ade. Abenfo gye di sɛ saa ɔsɛe yi na ɛma amemene no mu ntini wuwu nkakrankakra wɔ MSA mu.

Nyansahufo da so ara reyɛ nhwehwɛmu wɔ nea enti a saa `alpha-synuclein` protein yi boaboa ano wɔ amemene no afã horow bi. Wɔsan nso susuw sɛ awosu mu nsakrae bi betumi asesa ɔkwan a nkwammoaa binom fa so de saa `alpha-synuclein` yi di dwuma. Adanse nso wɔ hɔ a ɛkyerɛ sɛ MSA-C type no tu mmirika wɔ mmusua mu. Nanso, wonnya nhuu awosu mu abusuabɔ a ɛte saa biara wɔ MSA-P su no ho.

Nea ɛho hia sen biara ne sɛ MSA nyɛ yare a ɛde ɔyare ba . Worentumi nnye mfi obi foforo hɔ, na saa ara nso na wuntumi ntrɛw nkɔ obi foforo so.

Wobɛyɛ dɛn ahu no yiye sɛ wowɔ MSA? Sɔhwɛ ahorow bɛn na wɔyɛ?

Sɛ MSA wɔ hɔƆkwan baako pɛ a wobɛfa so anya awerɛhyem 100% ne sɛ wobɛhwehwɛ amemene mu ntini mu bere a obi awu akyi, efisɛ ɔkwan biara nni hɔ a wobɛfa so ahu pɛpɛɛpɛ sɛ ebia `alpha-synuclein` aboaboa ano wɔ amemene no mmeae bi bere a obi te ase anaa.

Bere a obi te ase no, nnuruyɛfo gyina sɛnkyerɛnne ahorow, aduruyɛ ho abakɔsɛm, abusua abakɔsɛm, ne sɛ ebia wɔyɛ wɔn ade wɔ ayaresa ahorow bi ho anaasɛ wɔnyɛ ho biribi so susuw sɛ MSA. Mpɛn pii no, nea edi kan a wohu ne Parkinson yare anaa kankyee mu ɔhaw foforo a ɛte saa, na wɔsesa nea wohu no ma ɛyɛ MSA akyiri yi bere a sɛnkyerɛnne foforo aba anaasɛ nnuru bi gyae adwumayɛ no.

Nneɛma atitiriw pii wɔ hɔ a ebetumi ama nsonsonoe ada MSA ne Parkinson yare no ntam:

  • MSA kɔ so ntɛmntɛm : Egye mfe pii ansa na obi a ɔwɔ Parkinson yare no anya ɔhaw ahorow wɔ autonomic nervous system no ho. Nanso wɔ MSA mu no, ɔhaw ahorow yi betumi afi ase wɔ afe biako mu.
  • Nsɛnkyerɛnne ahorow bi da adi wɔ ɔkwan soronko so : Autonomic nervous system sɛnkyerɛnne, titiriw, mu yɛ den kɛse wɔ MSA mu. Nanso, ebia nneɛma te sɛ wosow no mu nyɛ den pii, anaasɛ enni hɔ koraa. Ɔkwan a sɛnkyerɛnne ahorow no fa so trɛw wɔ nipadua no mu nyinaa nso betumi ayɛ soronko.
  • Ayaresa no ntumi nyɛ adwuma : Levodopa ne aduru titiriw a wɔde sa Parkinson yare. Nanso, levodopa ntumi nyɛ adwuma yiye wɔ MSA mu. Eyi ne ade titiriw nti a nnuruyɛfo susuw sɛ ebia ɛyɛ MSA na ɛnyɛ Parkinson yare.

Sɔhwɛ ahorow bɛn na wɔreyɛ ama eyi?

Nhwehwɛmu kakraa bi pɛ na ɛwɔ hɔ a ɛboa tẽẽ ma wohu MSA. Wɔyɛ nhwehwɛmu dodow no ara de yi nyarewa afoforo fi hɔ na wɔboaboa adanse pii ano de foa adwenem naayɛ a ɛne sɛ ebia ɛyɛ MSA no so. Eyinom bi ne:

  • Magnetic resonance imaging (MRI) scan : Ɛtɔ mmere bi a eyi betumi akyerɛ amemene no mmeae bi a asɛe. Eyi betumi aboa ma wɔahu yare no pɛpɛɛpɛ. Ɛho wɔ mfasoɔ nso wɔ MSA-C a wɔbɛhunu mu, ɛfiri sɛ ɛtumi kyerɛ sɛ ɛyɛ nsensaneeɛ a ɛwɔ amemene no fã bi ("hot cross bun" sɛnkyerɛnne). Nanso, wobetumi ahu saa sɛnkyerɛnne yi wɔ nyarewa afoforo nso mu, enti ɛnyɛ nea ɛdɔɔso sɛ obi ankasa betumi ahu MSA.
  • Awosu mu nhwehwɛmu : Eyi betumi ahwɛ sɛ awosu mu nsakrae bi wɔ hɔ a ɛka ɔkwan a obi nipadua fa so di alpha-synuclein ho dwuma. Ɛda adi sɛ nhwehwɛmu ahorow yi betumi ahu awosu mu nsakrae a ɛbata MSA-C ho wɔ Japanfo mu.
  • Skin biopsy : Skin biopsy ahorow bi tumi hu sɛnkyerɛnne ahorow a ɛkyerɛ sɛ alpha-synuclein aboaboa ano wɔ ntini mu ntini mu. Nanso, nhwehwɛmu pii ho hia na ama wɔahu sɛ ebia eyi so wɔ mfaso araa ma ɛbɛyɛ adeyɛ a wɔde hwehwɛ yare no fã a wɔahyɛ da ayɛ no anaa.

Wo duruyɛfo bɛka nhwehwɛmu afoforo a ɛfata ne sɛnea ebetumi aboa wo ho asɛm akyerɛ wo. Wobesusuw w’akwahosan ho abakɔsɛm, w’abusua abakɔsɛm, ne nneɛma afoforo ho de asi gyinae a eye sen biara ama wo.

So aduru bi wɔ hɔ a wɔde sa MSA? So wobetumi asa no yare?

Ɛde besi nnɛ no, wonnya nhuu MSA aduru pɔtee biara.Enti, ayaresa no atirimpɔw titiriw ne sɛ wobedi sɛnkyerɛnne ahorow no so bere tenten biara a wobetumi. MSA sɛnkyerɛnne ahorow ho ayaresa gyina nneɛma pii so, a ɔyarefo no sɛnkyerɛnne ne sɛnea emu yɛ den ka ho.

Nnuru anaa ayaresa bɛn na wɔde di dwuma?

Nnuru ahorow pii wɔ hɔ a ebetumi aboa ma wɔadi MSA ho sɛnkyerɛnne ahorow so. Aduru ko a wo nsa bɛka no begyina wo yare no ho sɛnkyerɛnne ne nneɛma afoforo so. Wo duruyɛfo ne onipa a oye sen biara a ɔbɛkamfo nnuru a eye sen biara ama wo, efisɛ wɔn na wobenya wo tebea no ho nimdeɛ kɛse. Wɔbɛkyerɛkyerɛ nea ebetumi afi ayaresa ahorow no mu aba nso mu akyerɛ wo.

Nea ɛho hia: MSA yɛ tebea a oduruyɛfo a watete no na ɔfata nkutoo na obetumi ahu. Enti, mmɔ mmɔden sɛ w’ankasa wubehu yare no ho sɛnkyerɛnne anaa wobɛsa a wo ne oduruyɛfo nkasa.

So ɔkwan bi wɔ hɔ a wɔbɛfa so asiw MSA ano?

Abenfo nnya nhuu nea ɛde MSA ba anaa nneɛma a ɛde ba. Enti, mprempren ɔkwan biara nni hɔ a wɔbɛfa so asiw ano anaasɛ wɔbɛtew asiane no so .

Daakye bɛn na obi a ɔwɔ MSA betumi ahwɛ kwan?

Mpɛn pii no, nnipa a wɔwɔ MSA no di kan nya sɛnkyerɛnne ahorow a ɛfa kankyee ho. Saa tebea yi mu yɛ den nkakrankakra bere a bere kɔ so no. Ayarefo bɛyɛ fã hia mmoa a wɔde nantew wɔ saa bere yi mu. Eyi kyerɛ sɛ wode poma anaa ade a wɔde nantew bedi dwuma. Bɛyɛ mfe anum wɔ MSA mfiase akyi no, ɛsɛ sɛ ayarefo bɛyɛ 60% de mmubuafo akongua di dwuma. Wɔ mfe asia kosi awotwe mu no, anyɛ yiye koraa no, ayarefo no mu fã da mpa so.

Bere a yare no kɔ so no, ebia ɛho behia sɛ wɔyɛ nneɛma foforo anaasɛ wɔde wɔn ho gye mu na ama nipadua no akɔ so ayɛ adwuma na wɔasiw nsɛnnennen a asiane wom ano. Eyinom bi ne:

  • Tracheostomy na ama wɔatumi akɔ so ahome.
  • Aduan a wɔde fa nsukorabea (`Tube feeding` / `aduan a wɔde ma wɔ awotwaa mu`).
  • Indwelling catheters anaa urostomy a wɔde sa nsu a wontumi nhyɛ mu.
  • Colostomy ma dwensɔtwaa mu nsɛnnennen.

MSA di bere tenten ahe?

MSA yɛ nkwa nna nyinaa mu tebea a ɛtra hɔ daa. Sɛ wɔkyekyem pɛpɛɛpɛ a, nkwa nna a yare no di no yɛ mfe asia kosi du . Wɔ tebea horow a emu nyɛ den pii mu no, ebetumi adi mfe 15. Nanso, wɔ tebea horow a emu yɛ den mu no, nkwa nna no betumi ayɛ tiaa koraa. Mpɛn pii no, saa nsɛm a emu yɛ den yi ka sɛnkyerɛnne ahorow a edidi so yi ho:

  • Autonomic nervous system sɛnkyerɛnne ahorow no mu yɛ den ansa na sɛnkyerɛnne ahorow a ɛfa kankyee ho afi ase.
  • Mfe a obi adi bere a wɔahu yare no.
  • Sɛ obi nya kankyee ho sɛnkyerɛnne a ɛma ɔtaa hwe ase.

Adwene bɛn na wɔwɔ wɔ tebea yi ho?

MSA ho anidaso nyɛ papa koraa. Saa tebea yi ho sɛnkyerɛnne no mu yɛ den nkakrankakra, na ɛtaa siw nipadua no dwumadi kwan na ɛde ɔhaw ahorow a edi awu ba. Nsɛnnennen a ebetumi ama obi awu no bi ne:

  • Ahurututu mu yare.
  • Nsuo mu yareɛ (UTIs) betumi ama obi anya sepsis (mogya mu awuduru).
  • Owu mpofirim (mpɛn pii no anadwo, esiane ɔkwan a amemene no fa so di ɔhome so bere a wɔada no mu basabasayɛ nti).

Mɛyɛ dɛn ahwɛ me ho/me dɔfo? Dɛn na ɛsɛ sɛ ɛhaw me?

Nnipa a wɔwɔ MSA no nya yare no ho sɛnkyerɛnne a ɛkɔ so nkakrankakra. Eyi kyerɛ sɛ, sɛ yare no ho sɛnkyerɛnne no du baabi a, wontumi mfa wɔn ho ntra ase bio. Awiei koraa no, tebea no betumi aka sɛnea w’ankasa wususuw nneɛma ho, kasa, na wusi gyinae. Esiane saa nneɛma yi nyinaa nti, ɛho hia sɛ wo ne w’adɔfo kasa fa nea wopɛ daakye ho na sɛ wuntumi nsi gyinae a, woyɛ nhyehyɛe ma w’ayaresa .

Bere bɛn na ɛsɛ sɛ wokɔ oduruyɛfo nkyɛn?

MSA ho sɛnkyerɛnne a edi kan no pii yɛ nneɛma a ɛsɛ sɛ wo ne oduruyɛfo susuw ho. Eyinom bi ne:

  • Ɔbarima ne ɔbea nna mu ɔbrasɛe.
  • Orthostatic hypotension (akisikuru a ɛkɔ so daa anaasɛ ɔtotɔ piti a ntease biara nnim).
  • Dae mu haw ne nna mu mframa a ɛmma obi ntumi nkɔ (ahomegye bere a wada).

Sɛ oduruyɛfo bi hu sɛ wowɔ kankyee mu ɔhaw bi te sɛ Parkinson yare a, ɛho hia sɛ wo ne wɔn kasa fa nsakrae biara a ɛbɛba wo sɛnkyerɛnne ahorow mu ho. Wo duruyɛfo bɛyɛ nhyehyɛe akɔhwɛ wo tebea no na wayɛ nsakrae wɔ w’aduru no mu. Wubetumi aka nsakrae biara a wubehu wɔ saa nsrahwɛ ahorow yi mu ho asɛm. Ɛtaa ba sɛ nnipa a wɔahu sɛ wɔwɔ Parkinson yare no bɛsesa wɔn yare no akyiri yi, bere a sɛnkyerɛnne foforo aba anaasɛ bere a levodopa gyae adwumayɛ yiye no.

Nnipa a wɔwɔ MSA taa nya sɛnkyerɛnne afoforo, titiriw adwenemyare. Ɛho hia sɛ wɔhwehwɛ ayaresa ma adwenemyare a ɛfa MSA ho, ne nipadua mu sɛnkyerɛnne ahorow nso. Wo duruyɛfo betumi akamfo ayaresa akyerɛ wo anaasɛ ɔde wo bɛkɔ adwenemyare ho ɔbenfo nkyɛn.

Sɛ yɛbɛbɔ no mua a (Take-Home Message) .

Multiple System Atrophy (MSA) yɛ yare a emu yɛ den, na awiei koraa no ekum obi. Nea ɛyɛ awerɛhow no, wonnya nnyaa saa tebea yi ano aduru anaa ayaresa tẽẽ biara.

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Nanso, wobetumi asa ne yare no ho sɛnkyerɛnne pii , na akwan bi wɔ hɔ a wɔbɛfa so atew nea efi mu ba ne ne sɛnkyerɛnne ahorow no so. Sɛ wɔde ayaresa ma nnipa pii a, wobetumi akura wɔn asetra pa mu mfe pii, de bere a ɛsom bo ama wɔn adɔfo, na wɔde wɔn bere adi dwuma yiye. Enti, ɛho hia sɛ wode aduruyɛ mu afotu a ɛfata di sɛnkyerɛnne ahorow no ho dwuma, a ɛremma abasamtu mma.


`Multiple System Atrophy, MSA, Ntini mu Yare, Amemene mu Yare, Parkinson Nsɛnkyerɛnne, Kankyee mu Nsɛnnennen, Autonomic Nnervous System Problems

Frequently Asked Questions (FAQ)

Sɔhwɛ ahorow bɛn na wɔreyɛ ama eyi?

Nhwehwɛmu kakraa bi pɛ na ɛwɔ hɔ a ɛboa tẽẽ ma wohu MSA. Wɔyɛ nhwehwɛmu dodow no ara de yi nyarewa afoforo fi hɔ na wɔboaboa adanse pii ano de foa adwenem naayɛ a ɛne sɛ ebia ɛyɛ MSA no so. Eyinom bi ne:

Nnuru anaa ayaresa bɛn na wɔde di dwuma?

Nnuru ahorow pii wɔ hɔ a ebetumi aboa ma wɔadi MSA ho sɛnkyerɛnne ahorow so. Aduru ko a wo nsa bɛka no begyina wo yare no ho sɛnkyerɛnne ne nneɛma afoforo so. Wo duruyɛfo ne onipa a oye sen biara a ɔbɛkamfo nnuru a eye sen biara ama wo, efisɛ wɔn na wobenya wo tebea no ho nimdeɛ kɛse. Wɔbɛkyerɛkyerɛ nea ebetumi afi ayaresa ahorow no mu aba nso mu akyerɛ wo.

Adwene bɛn na wɔwɔ wɔ tebea yi ho?

MSA ho anidaso nyɛ papa koraa. Saa tebea yi ho sɛnkyerɛnne no mu yɛ den nkakrankakra, na ɛtaa siw nipadua no dwumadi kwan na ɛde ɔhaw ahorow a edi awu ba. Nsɛnnennen a ebetumi ama obi awu no bi ne:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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So worenya nkate horow a ɛyɛ nwonwa wɔ wo nipadua mu? Ebia ɛho hia sɛ wuhu Multiple System Atrophy (MSA) ho asɛm!
Nyarewa ne Tebea Ahorow5, Kutawonsa, 2026

So worenya nkate horow a ɛyɛ nwonwa wɔ wo nipadua mu? Ebia ɛho hia sɛ wuhu Multiple System Atrophy (MSA) ho asɛm!

So wote nka da sɛ nneɛma a ɛwɔ wo nipadua mu resakra wɔ akwan horow so a wuntumi nni so? Ɛtɔ da bi a, ɛte sɛ nea worenkari pɛ bere a wonam no, anaasɛ wo ho yɛ wo yaw bere a wosɔre mpofirim no. Eyinom yɛ nneɛma a ɛtɔ mmere bi a yɛmfa yɛn adwene nsi so kɛse, nanso ebetumi ayɛ ntini mu nyarewa bi a wɔntaa nhu ho sɛnkyerɛnne nso. Ɛnnɛ yɛbɛka tebea a ɛte saa biako a ɛyɛ den kakra ho asɛm, nanso ɛho hia yiye sɛ yɛma yɛn ani da hɔ. Ɛno ne Multiple System Atrophy (MSA) .

Dɛn ankasa ne Multiple System Atrophy (MSA)?

Sɛ yɛbɛka no tiawa a, Multiple System Atrophy (MSA)ntini mu yare a ɛntaa nsi a yɛn amemene no afã horow yɛ mmerɛw nkakrankakra, kyerɛ sɛ, ɛsɛe. Bere kɔ so no, yɛn nipadua no dwumadi ne tumi a amemene no afã horow yi di so no fi ase sɛe. Eyi yɛ tebea a emu yɛ den mmom ankasa, efisɛ ɛyɛ den sɛ wobenya ahoɔden afi mu koraa.

Bere bi a atwam no, na wɔde din ahorow pii frɛ MSA. Ebia woate edin ahorow te sɛ `Shy-Drager syndrome`, `Sporadic olivopontocerebellar atrophy`, `Striatonigral degeneration` ho asɛm. Akyiri yi ara na nnuruyɛfo hui sɛ tebea horow yi nyinaa wɔ nneɛma bi a ɛtaa ba. Ɛno nti na wɔkaa wɔn nyinaa boom na wɔmaa wɔn din foforɔ, `Multiple System Atrophy` (MSA). Nsɛnkyerɛnne no gu ahorow gyina amemene no fã a asɛe so. Ɛno nti na ɛsono sɛnea obiara nya sɛnkyerɛnne ahorow a wɔaka abom no.

MSA ahorow abien na ɛwɔ hɔ, ɛnte saa? Dɛn ne wɔn?

Yiw, sɛnea ɛbɛyɛ na wɔahu MSA tebea no pefee no, nnuruyɛfo akyekyɛ mu ayɛ no ahorow atitiriw abien, a egyina sɛnkyerɛnne ahorow a ɛda adi so:

1. MSA-C : 'C' a ɛwɔ ha no gyina hɔ ma `cerebellar'. Saa ɔkwan yi ka sɛnea wutumi yɛ wo kankyee no ho nhyehyɛe titiriw. Ɛne sɛ, wohwere wo kari pɛ , a nnuruyɛfo nso frɛ no `ataxia'. Eyi ne sɛnkyerɛnne titiriw a ɛwɔ saa ɔkwan yi so. Bere koro no ara mu no, wubetumi ahu ɔhaw ahorow nso wɔ nipadua no automatic control systems (`autonomic dysfunction`) ne ahwease a ɛtaa ba no ho.

2. MSA-P : 'P' a ɛwɔ ha no gyina hɔ ma `parkinsonism'. Wɔ saa ɔkwan yi so no, wohu sɛnkyerɛnne ahorow a ɛte sɛ Parkinson yare no. Ɛwom sɛ saa Parkinson sɛnkyerɛnne ahorow yi da adi kɛse wɔ mfiase de, nanso bere kɔ so no, ɔhaw ahorow a ɛwɔ autonomic nervous system ne `ataxia' ho sɛnkyerɛnne nso betumi ada adi.

Henanom na MSA tebea yi ka no kɛse? Ɛtaa ba dɛn?

MSA taa ka mpanyimfo a wɔadi boro mfe 30. Ɛda adi kɛse sɛ yare no ho sɛnkyerɛnne bɛda adi wɔ mfe 50 kosi 59. Ebetumi aka obiara, ɛmfa ho sɛ ɔyɛ ɔbarima anaa ɔbea.

Nanso MSA yɛ tebea a ɛntaa nsi koraa . Abenfo ka sɛ nnipa 100,000 biara mu nnipa foforo 0.6 anaa 0.7 pɛ na wonya afe biara. Wobu akontaa sɛ nnipa dodow a wɔanya yare no nyinaa bɛyɛ 3.4 kosi 4.9 wɔ nnipa 100,000 biara mu. Enti wubetumi ahu sɛnea eyi ho yɛ na.

Dɛn na ɛto nipadua a ɛwɔ MSA no? Amemene no afã horow bɛn na ɛka?

MSA yɛ yare a ɛkɔ so yɛ den a ɛka amemene no afã horow. Nsɛnkyerɛnne no gyina amemene no fã a ɛka no so. Amemene no mmeae atitiriw a MSA ka no ne:

  • Basal ganglia : Eyinom wɔ amemene no mfinimfini pɛɛ. Wɔka amemene no afã horow bom na ɛboa ma wɔbom yɛ adwuma. Ɛte sɛ amemene no dan titiriw a wɔde di dwuma .
  • Brainstem : Eyi ne nea ɛhwɛ nneɛma pii a ɛkɔ so ara kwa wɔ yɛn nipadua mu no so. Ɛne sɛ, nneɛma a ɛba ara kwa a yensusuw ho, sɛ nhwɛso no, ɔhome, koma bɔ, ne mogya mmoroso. Eyinom ho hia na ama obi anya nkwa.
  • Cerebellum : Eyi wɔ ti no akyi, wɔ ase. Ɛyɛ n’asɛyɛde titiriw sɛ ɛhwɛ kankyee so na ɛkari pɛ. Ɛne amemene no afã afoforo nso yɛ adwuma. Nhwehwɛmufo da so ara resua ne dwumadi nyinaa ho ade, nanso adanse bi kyerɛ sɛ ɛka yɛn nkate ne gyinaesi nso ho.

Enti, sɛ amemene no afã horow yi sɛe a, dwumadi ahorow a saa afã horow no di so no ntumi nyɛ yiye. Sɛ nhwɛso no, sɛ `Brainstem` no sɛe a, ɔhaw ahorow a ɛfa nneɛma a ɛyɛ adwuma ankasa te sɛ mogya mmoroso ho betumi aba.

Dɛn ne MSA ho sɛnkyerɛnne ahorow? Yɛyɛ dɛn hu wɔn?

MSA ho sɛnkyerɛnne ahorow bi abu so wɔ ahorow abien no nyinaa mu, na ebi nso yɛ nea ɛfa ɔkwan biara ho pɔtee. Nanso ade biako a ɛtaa ba wɔ ahorow abien no nyinaa mu ne autonomic dysfunction. Sɛ yɛbɛka no tiawa a, wo nipadua no mfiri a ɛma wotumi di nneɛma so no kɔ so yɛ basabasa.

Nsɛnkyerɛnne a efi ɔhaw ahorow a ɛwɔ autonomic nervous system no mu ba:

  • Orthostatic hypotension : Eyi ne bere a wo mogya mmoroso so tew mpofirim, na ɛma w’adwene tu fra , bere a wosakra wo gyinabea, sɛ nhwɛso no, bere a wugyina hɔ mpofirim fi tra ase no.
  • Nsu a wontumi nni so (`urinary incontinence`) ne sɛnea wontumi nni nsu a wɔde gu nsu mu so (`fecal incontinence`).
  • Ɔbarima ne ɔbea nna mu ɔhaw, titiriw wɔ mmarima mu, yɛ den sɛ wobenya ɔbarima ne ɔbea nna mu ahoɔden (rectile dysfunction).
  • Rapid eye movement (REM) sleep behavior disorder : Te sɛ Parkinson yare no, sɛ woda dae a, woyɛ nneɛma a woyɛɛ wɔ w’adaeso mu no ho agoru ankasa. Ebia wobɛteɛteɛm anaasɛ wobɛbɔ wo nsa.
  • Fifiri a ɛso tew (anhidrosis).
  • Anisoadehu mu haw ahorow.
  • Ano a ɛyɛ nwunu.
  • Dae mu ahomegye a ɛyɛ den.
  • Nnuan a wɔyam brɛoo ne akisikuru.

Susuw ho sɛ saa autonomic sɛnkyerɛnne ahorow yi pii betumi ada adi asram pii, mfe pii mpo ansa na ntini mu sɛnkyerɛnne ahorow ada adi. Eyi ba wɔ MSA ayarefo 20% kosi 75% mu.

Adwene ne nkate mu su ahorow

Nnipa a wɔwɔ MSA no mu bɛyɛ nkyem abiɛsa mu biako nya ɔhaw ahorow wɔ sɛnea wotumi susuw nneɛma ho na wɔde wɔn adwene si biribi so no ho. Ɛyɛ den ma wɔn nso sɛ wobedi wɔn nkate so. Eyi betumi de adwenemyare te sɛ:

  • Brɛ.
  • Hahaahayɔ.
  • Nkate mu a entumi nnyina pintinn: Ɛne sɛ, osu ne serew a ɛmfata.
  • Ehu a ɛba obi so.
  • Adwene a ɛne sɛ wobɛpira wo ho anaasɛ wubekum wo ho.

Nneɛma a ɛfa kankyee ho

MSA-C (amemene mu ntini su):

Saa ɔkwan yi fa `ataxia` (kari pɛ a wɔhwere) ho titiriw. `Cerebellum` yɛ amemene no fã bi a edi dwuma titiriw wɔ ntini ahorow a ɛkɔ so no mu. Enti, sɛ saa nkitahodi no yera a, nneɛma te sɛ eyi betumi asi:

  • Akwaa a ɛwɔ nipadua no mu a wontumi nni so, a ɛyɛ basabasa .
  • Action tremor : Eyi kyerɛ sɛ, sɛ wobɔ mmɔden sɛ wobɛyɛ biribi a, wo nsa ne wo nan ase wosow no yɛ kɛse.
  • Nantew a wɔde nan a ɛtrɛw soronko nantew .
  • Aniwa a ɛtwetwe a wontumi nni so (nystagmus).

MSA-P (Parkinsonism type) no su ahorow:

Saa sɛnkyerɛnne yi taa fi ase wɔ nipadua no fã biako na afei ɛtrɛw kɔ afã abien no nyinaa. Saa sɛnkyerɛnne ahorow yi taa te sɛ eyi:

  • Nneɛma a wɔde keka ne ho brɛoo (bradykinesia), a wɔte nka te sɛ nea nkwa nni nipadua no mu .
  • Te a wɔte nka sɛ nipadua no ayɛ den na ayɛ den, na ɛde gyinabea a ɛte sɛ nea ɔde ne ho kɔ n’anim ba.
  • To hintidua a wɔtaa to bere a wɔnantew no.
  • Akasakasa bere a wɔrekasa, kasa a emu nna hɔ .

Dɛn nti na saa MSA yi ba? Dɛn nti na ɛte saa?

Wonnya nhuu nea ɛde MSA ba ankasa , nanso abenfo susuw sɛ ɛne protein bi a wɔfrɛ no `alpha-synuclein`, a ebetumi aboaboa ano wɔ yɛn amemene no afã horow no wɔ abusuabɔ. Wosusuw sɛ protein koro yi ara nso na ɛde Parkinson yare no ba titiriw.

Protein yɛ nnuru a ɛho hia na ama yɛn nipadua ayɛ adwuma. Wɔboa wɔ nneɛma pii mu, te sɛ nkitahodi a ɛda nhyehyɛe ahorow a ɛwɔ nipadua no mu ntam ne nnuru a wɔde di akɔneaba. Nanso, sɛ protein ahorow yi boaboa ano wɔ mmeae a ɛnteɛ a, ebetumi asɛe ade. Abenfo gye di sɛ saa ɔsɛe yi na ɛma amemene no mu ntini wuwu nkakrankakra wɔ MSA mu.

Nyansahufo da so ara reyɛ nhwehwɛmu wɔ nea enti a saa `alpha-synuclein` protein yi boaboa ano wɔ amemene no afã horow bi. Wɔsan nso susuw sɛ awosu mu nsakrae bi betumi asesa ɔkwan a nkwammoaa binom fa so de saa `alpha-synuclein` yi di dwuma. Adanse nso wɔ hɔ a ɛkyerɛ sɛ MSA-C type no tu mmirika wɔ mmusua mu. Nanso, wonnya nhuu awosu mu abusuabɔ a ɛte saa biara wɔ MSA-P su no ho.

Nea ɛho hia sen biara ne sɛ MSA nyɛ yare a ɛde ɔyare ba . Worentumi nnye mfi obi foforo hɔ, na saa ara nso na wuntumi ntrɛw nkɔ obi foforo so.

Wobɛyɛ dɛn ahu no yiye sɛ wowɔ MSA? Sɔhwɛ ahorow bɛn na wɔyɛ?

Sɛ MSA wɔ hɔƆkwan baako pɛ a wobɛfa so anya awerɛhyem 100% ne sɛ wobɛhwehwɛ amemene mu ntini mu bere a obi awu akyi, efisɛ ɔkwan biara nni hɔ a wobɛfa so ahu pɛpɛɛpɛ sɛ ebia `alpha-synuclein` aboaboa ano wɔ amemene no mmeae bi bere a obi te ase anaa.

Bere a obi te ase no, nnuruyɛfo gyina sɛnkyerɛnne ahorow, aduruyɛ ho abakɔsɛm, abusua abakɔsɛm, ne sɛ ebia wɔyɛ wɔn ade wɔ ayaresa ahorow bi ho anaasɛ wɔnyɛ ho biribi so susuw sɛ MSA. Mpɛn pii no, nea edi kan a wohu ne Parkinson yare anaa kankyee mu ɔhaw foforo a ɛte saa, na wɔsesa nea wohu no ma ɛyɛ MSA akyiri yi bere a sɛnkyerɛnne foforo aba anaasɛ nnuru bi gyae adwumayɛ no.

Nneɛma atitiriw pii wɔ hɔ a ebetumi ama nsonsonoe ada MSA ne Parkinson yare no ntam:

  • MSA kɔ so ntɛmntɛm : Egye mfe pii ansa na obi a ɔwɔ Parkinson yare no anya ɔhaw ahorow wɔ autonomic nervous system no ho. Nanso wɔ MSA mu no, ɔhaw ahorow yi betumi afi ase wɔ afe biako mu.
  • Nsɛnkyerɛnne ahorow bi da adi wɔ ɔkwan soronko so : Autonomic nervous system sɛnkyerɛnne, titiriw, mu yɛ den kɛse wɔ MSA mu. Nanso, ebia nneɛma te sɛ wosow no mu nyɛ den pii, anaasɛ enni hɔ koraa. Ɔkwan a sɛnkyerɛnne ahorow no fa so trɛw wɔ nipadua no mu nyinaa nso betumi ayɛ soronko.
  • Ayaresa no ntumi nyɛ adwuma : Levodopa ne aduru titiriw a wɔde sa Parkinson yare. Nanso, levodopa ntumi nyɛ adwuma yiye wɔ MSA mu. Eyi ne ade titiriw nti a nnuruyɛfo susuw sɛ ebia ɛyɛ MSA na ɛnyɛ Parkinson yare.

Sɔhwɛ ahorow bɛn na wɔreyɛ ama eyi?

Nhwehwɛmu kakraa bi pɛ na ɛwɔ hɔ a ɛboa tẽẽ ma wohu MSA. Wɔyɛ nhwehwɛmu dodow no ara de yi nyarewa afoforo fi hɔ na wɔboaboa adanse pii ano de foa adwenem naayɛ a ɛne sɛ ebia ɛyɛ MSA no so. Eyinom bi ne:

  • Magnetic resonance imaging (MRI) scan : Ɛtɔ mmere bi a eyi betumi akyerɛ amemene no mmeae bi a asɛe. Eyi betumi aboa ma wɔahu yare no pɛpɛɛpɛ. Ɛho wɔ mfasoɔ nso wɔ MSA-C a wɔbɛhunu mu, ɛfiri sɛ ɛtumi kyerɛ sɛ ɛyɛ nsensaneeɛ a ɛwɔ amemene no fã bi ("hot cross bun" sɛnkyerɛnne). Nanso, wobetumi ahu saa sɛnkyerɛnne yi wɔ nyarewa afoforo nso mu, enti ɛnyɛ nea ɛdɔɔso sɛ obi ankasa betumi ahu MSA.
  • Awosu mu nhwehwɛmu : Eyi betumi ahwɛ sɛ awosu mu nsakrae bi wɔ hɔ a ɛka ɔkwan a obi nipadua fa so di alpha-synuclein ho dwuma. Ɛda adi sɛ nhwehwɛmu ahorow yi betumi ahu awosu mu nsakrae a ɛbata MSA-C ho wɔ Japanfo mu.
  • Skin biopsy : Skin biopsy ahorow bi tumi hu sɛnkyerɛnne ahorow a ɛkyerɛ sɛ alpha-synuclein aboaboa ano wɔ ntini mu ntini mu. Nanso, nhwehwɛmu pii ho hia na ama wɔahu sɛ ebia eyi so wɔ mfaso araa ma ɛbɛyɛ adeyɛ a wɔde hwehwɛ yare no fã a wɔahyɛ da ayɛ no anaa.

Wo duruyɛfo bɛka nhwehwɛmu afoforo a ɛfata ne sɛnea ebetumi aboa wo ho asɛm akyerɛ wo. Wobesusuw w’akwahosan ho abakɔsɛm, w’abusua abakɔsɛm, ne nneɛma afoforo ho de asi gyinae a eye sen biara ama wo.

So aduru bi wɔ hɔ a wɔde sa MSA? So wobetumi asa no yare?

Ɛde besi nnɛ no, wonnya nhuu MSA aduru pɔtee biara.Enti, ayaresa no atirimpɔw titiriw ne sɛ wobedi sɛnkyerɛnne ahorow no so bere tenten biara a wobetumi. MSA sɛnkyerɛnne ahorow ho ayaresa gyina nneɛma pii so, a ɔyarefo no sɛnkyerɛnne ne sɛnea emu yɛ den ka ho.

Nnuru anaa ayaresa bɛn na wɔde di dwuma?

Nnuru ahorow pii wɔ hɔ a ebetumi aboa ma wɔadi MSA ho sɛnkyerɛnne ahorow so. Aduru ko a wo nsa bɛka no begyina wo yare no ho sɛnkyerɛnne ne nneɛma afoforo so. Wo duruyɛfo ne onipa a oye sen biara a ɔbɛkamfo nnuru a eye sen biara ama wo, efisɛ wɔn na wobenya wo tebea no ho nimdeɛ kɛse. Wɔbɛkyerɛkyerɛ nea ebetumi afi ayaresa ahorow no mu aba nso mu akyerɛ wo.

Nea ɛho hia: MSA yɛ tebea a oduruyɛfo a watete no na ɔfata nkutoo na obetumi ahu. Enti, mmɔ mmɔden sɛ w’ankasa wubehu yare no ho sɛnkyerɛnne anaa wobɛsa a wo ne oduruyɛfo nkasa.

So ɔkwan bi wɔ hɔ a wɔbɛfa so asiw MSA ano?

Abenfo nnya nhuu nea ɛde MSA ba anaa nneɛma a ɛde ba. Enti, mprempren ɔkwan biara nni hɔ a wɔbɛfa so asiw ano anaasɛ wɔbɛtew asiane no so .

Daakye bɛn na obi a ɔwɔ MSA betumi ahwɛ kwan?

Mpɛn pii no, nnipa a wɔwɔ MSA no di kan nya sɛnkyerɛnne ahorow a ɛfa kankyee ho. Saa tebea yi mu yɛ den nkakrankakra bere a bere kɔ so no. Ayarefo bɛyɛ fã hia mmoa a wɔde nantew wɔ saa bere yi mu. Eyi kyerɛ sɛ wode poma anaa ade a wɔde nantew bedi dwuma. Bɛyɛ mfe anum wɔ MSA mfiase akyi no, ɛsɛ sɛ ayarefo bɛyɛ 60% de mmubuafo akongua di dwuma. Wɔ mfe asia kosi awotwe mu no, anyɛ yiye koraa no, ayarefo no mu fã da mpa so.

Bere a yare no kɔ so no, ebia ɛho behia sɛ wɔyɛ nneɛma foforo anaasɛ wɔde wɔn ho gye mu na ama nipadua no akɔ so ayɛ adwuma na wɔasiw nsɛnnennen a asiane wom ano. Eyinom bi ne:

  • Tracheostomy na ama wɔatumi akɔ so ahome.
  • Aduan a wɔde fa nsukorabea (`Tube feeding` / `aduan a wɔde ma wɔ awotwaa mu`).
  • Indwelling catheters anaa urostomy a wɔde sa nsu a wontumi nhyɛ mu.
  • Colostomy ma dwensɔtwaa mu nsɛnnennen.

MSA di bere tenten ahe?

MSA yɛ nkwa nna nyinaa mu tebea a ɛtra hɔ daa. Sɛ wɔkyekyem pɛpɛɛpɛ a, nkwa nna a yare no di no yɛ mfe asia kosi du . Wɔ tebea horow a emu nyɛ den pii mu no, ebetumi adi mfe 15. Nanso, wɔ tebea horow a emu yɛ den mu no, nkwa nna no betumi ayɛ tiaa koraa. Mpɛn pii no, saa nsɛm a emu yɛ den yi ka sɛnkyerɛnne ahorow a edidi so yi ho:

  • Autonomic nervous system sɛnkyerɛnne ahorow no mu yɛ den ansa na sɛnkyerɛnne ahorow a ɛfa kankyee ho afi ase.
  • Mfe a obi adi bere a wɔahu yare no.
  • Sɛ obi nya kankyee ho sɛnkyerɛnne a ɛma ɔtaa hwe ase.

Adwene bɛn na wɔwɔ wɔ tebea yi ho?

MSA ho anidaso nyɛ papa koraa. Saa tebea yi ho sɛnkyerɛnne no mu yɛ den nkakrankakra, na ɛtaa siw nipadua no dwumadi kwan na ɛde ɔhaw ahorow a edi awu ba. Nsɛnnennen a ebetumi ama obi awu no bi ne:

  • Ahurututu mu yare.
  • Nsuo mu yareɛ (UTIs) betumi ama obi anya sepsis (mogya mu awuduru).
  • Owu mpofirim (mpɛn pii no anadwo, esiane ɔkwan a amemene no fa so di ɔhome so bere a wɔada no mu basabasayɛ nti).

Mɛyɛ dɛn ahwɛ me ho/me dɔfo? Dɛn na ɛsɛ sɛ ɛhaw me?

Nnipa a wɔwɔ MSA no nya yare no ho sɛnkyerɛnne a ɛkɔ so nkakrankakra. Eyi kyerɛ sɛ, sɛ yare no ho sɛnkyerɛnne no du baabi a, wontumi mfa wɔn ho ntra ase bio. Awiei koraa no, tebea no betumi aka sɛnea w’ankasa wususuw nneɛma ho, kasa, na wusi gyinae. Esiane saa nneɛma yi nyinaa nti, ɛho hia sɛ wo ne w’adɔfo kasa fa nea wopɛ daakye ho na sɛ wuntumi nsi gyinae a, woyɛ nhyehyɛe ma w’ayaresa .

Bere bɛn na ɛsɛ sɛ wokɔ oduruyɛfo nkyɛn?

MSA ho sɛnkyerɛnne a edi kan no pii yɛ nneɛma a ɛsɛ sɛ wo ne oduruyɛfo susuw ho. Eyinom bi ne:

  • Ɔbarima ne ɔbea nna mu ɔbrasɛe.
  • Orthostatic hypotension (akisikuru a ɛkɔ so daa anaasɛ ɔtotɔ piti a ntease biara nnim).
  • Dae mu haw ne nna mu mframa a ɛmma obi ntumi nkɔ (ahomegye bere a wada).

Sɛ oduruyɛfo bi hu sɛ wowɔ kankyee mu ɔhaw bi te sɛ Parkinson yare a, ɛho hia sɛ wo ne wɔn kasa fa nsakrae biara a ɛbɛba wo sɛnkyerɛnne ahorow mu ho. Wo duruyɛfo bɛyɛ nhyehyɛe akɔhwɛ wo tebea no na wayɛ nsakrae wɔ w’aduru no mu. Wubetumi aka nsakrae biara a wubehu wɔ saa nsrahwɛ ahorow yi mu ho asɛm. Ɛtaa ba sɛ nnipa a wɔahu sɛ wɔwɔ Parkinson yare no bɛsesa wɔn yare no akyiri yi, bere a sɛnkyerɛnne foforo aba anaasɛ bere a levodopa gyae adwumayɛ yiye no.

Nnipa a wɔwɔ MSA taa nya sɛnkyerɛnne afoforo, titiriw adwenemyare. Ɛho hia sɛ wɔhwehwɛ ayaresa ma adwenemyare a ɛfa MSA ho, ne nipadua mu sɛnkyerɛnne ahorow nso. Wo duruyɛfo betumi akamfo ayaresa akyerɛ wo anaasɛ ɔde wo bɛkɔ adwenemyare ho ɔbenfo nkyɛn.

Sɛ yɛbɛbɔ no mua a (Take-Home Message) .

Multiple System Atrophy (MSA) yɛ yare a emu yɛ den, na awiei koraa no ekum obi. Nea ɛyɛ awerɛhow no, wonnya nnyaa saa tebea yi ano aduru anaa ayaresa tẽẽ biara.

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Nanso, wobetumi asa ne yare no ho sɛnkyerɛnne pii , na akwan bi wɔ hɔ a wɔbɛfa so atew nea efi mu ba ne ne sɛnkyerɛnne ahorow no so. Sɛ wɔde ayaresa ma nnipa pii a, wobetumi akura wɔn asetra pa mu mfe pii, de bere a ɛsom bo ama wɔn adɔfo, na wɔde wɔn bere adi dwuma yiye. Enti, ɛho hia sɛ wode aduruyɛ mu afotu a ɛfata di sɛnkyerɛnne ahorow no ho dwuma, a ɛremma abasamtu mma.


`Multiple System Atrophy, MSA, Ntini mu Yare, Amemene mu Yare, Parkinson Nsɛnkyerɛnne, Kankyee mu Nsɛnnennen, Autonomic Nnervous System Problems

Frequently Asked Questions (FAQ)

Sɔhwɛ ahorow bɛn na wɔreyɛ ama eyi?

Nhwehwɛmu kakraa bi pɛ na ɛwɔ hɔ a ɛboa tẽẽ ma wohu MSA. Wɔyɛ nhwehwɛmu dodow no ara de yi nyarewa afoforo fi hɔ na wɔboaboa adanse pii ano de foa adwenem naayɛ a ɛne sɛ ebia ɛyɛ MSA no so. Eyinom bi ne:

Nnuru anaa ayaresa bɛn na wɔde di dwuma?

Nnuru ahorow pii wɔ hɔ a ebetumi aboa ma wɔadi MSA ho sɛnkyerɛnne ahorow so. Aduru ko a wo nsa bɛka no begyina wo yare no ho sɛnkyerɛnne ne nneɛma afoforo so. Wo duruyɛfo ne onipa a oye sen biara a ɔbɛkamfo nnuru a eye sen biara ama wo, efisɛ wɔn na wobenya wo tebea no ho nimdeɛ kɛse. Wɔbɛkyerɛkyerɛ nea ebetumi afi ayaresa ahorow no mu aba nso mu akyerɛ wo.

Adwene bɛn na wɔwɔ wɔ tebea yi ho?

MSA ho anidaso nyɛ papa koraa. Saa tebea yi ho sɛnkyerɛnne no mu yɛ den nkakrankakra, na ɛtaa siw nipadua no dwumadi kwan na ɛde ɔhaw ahorow a edi awu ba. Nsɛnnennen a ebetumi ama obi awu no bi ne:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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