Ba walima fa bɛ siran ni jɔrɔnanko min sɔrɔ n’u ye fɛn kabakoma dɔ ye u denmisɛnnin fari la, n b’o faamu. Kɛrɛnkɛrɛnnenya la ni den bangenen kura barika banna ka nɔ bulu-bulumanw sɔrɔ u fari la, o bɛ se ka mɔgɔ jɔrɔ kosɛbɛ. Nin bana in ye an bɛ min wele furakɛli siratigɛ la ko "Blueberry Muffin Rash". Nin tɔgɔ in bɛ se ka kɛ kabako ye, nka a nafa ka bon k’a dɔn bawo sababu jugu damadɔ bɛ se ka kɛ a kɔfɛ.
Nin ‘blueberry muffin rash’ in ye mun ye?
N’an y’a fɔ cogo nɔgɔman na, nin ye farilabana ye min bɛ se ka den kuraw ni den fitiniw minɛ. A bɛ fɔ a ma ko ‘blueberry muffin rash’ barisa a nɔw bɛ i n’a fɔ bulu-bulu nɛrɛmuguma minnu bɛ blueberry muffin kan. U bɛ se ka ye i n’a fɔ kurukuruw walima i n’a fɔ kuru kɔrɔtalenw fari la.
Min nafa ka bon, o ye ko nin nɔ ninnu tɛ fari la, nka a bɛ i n’a fɔ u bɔra fari kɔnɔ kosɛbɛ . Nin tɛ kurukuruni ye min bɛ kɛ cogo la.
Kunba saba bɛ yen minnu b’a to nin nɔ ninnu bɛ se ka bɔ:
1. Joli bɔli kɔfɛ: A ka ca a la, an joli bɛ bɔ kolotugudaw la . Nka, furakɛli cogoya dɔw kosɔn, joli-sira-funu bɛ daminɛ ka dalajɛ ka kɛ kuluw ye kolotugudaw kɔkan, i n’a fɔ fari la. O selilu kuluw de bɛ Ye i n’a fɔ nɔgɔw.
2. Joli bɛ don fari la (Purpura): Nin nɔ jɛman suguya in bɛ se ka sɔrɔ ni joli bɛ don fari la ka a sababu kɛ joli siraw tiɲɛni ye walima ni fanga dɔgɔyali ye joli kurucogo la.
3. Kansɛribanakisɛw jɛnsɛnni (Metastasis): Kansɛri suguya dɔw la, kansɛribanakisɛw bɛ se ka jɛnsɛn fari la ka bɔ farikolo yɔrɔ wɛrɛw la ka kurukuruw lase mɔgɔ ma i n’a fɔ nin.
Furakɛcogo basigilen minnu bɛ nin saba bɛɛ lase mɔgɔ ma, olu fanba man ca. Ani fana, a ka ca a la, taamasiɲɛ wɛrɛw bɛna kɛ den na ka fara nin nɔ ninnu kan. O nɔgɔ ninnu tɛna kɛnɛya u yɛrɛ ma. O la, ‘blueberry muffin rash’ ye taamasiɲɛ barikama ye min b’a jira ko den mago bɛ dɔgɔtɔrɔso la joona.
Fɛnba jumɛnw de bɛ se ka kɛ sababu ye ka o kɛ?
Aw kana aw hakili ɲagami, an bɛna kuma ka jɛya kun suguya kunbabaw kan minnu bɛ nɔ bila nin ko in na, kelen kelen.
TORCH Banakisɛw
TORCH ye banakisɛ kulu caman daɲɛ surun ye minnu bɛ den walima den kura sɔrɔ kɔnɔbara la. Nin bana ninnu bɛ se ka bɔ ba la ka taa den na kɔnɔmaya waati, jiginni waati, walima jiginni kɔfɛ.
TORCH kɔrɔ ye ko:
- T - Toxoplasmosis (banakisɛfagalan).
- O - Banakisɛ wɛrɛw - misali la sifili, kɔnɔboli, parvovirus B19
- R. Bamako, Mali- Rubella ye
- C - Sitomegalovirusi (CMV) .
- H - Ɲɛgɛnɛsiraw banakisɛ (HSV) .
Nin bana ninnu faralen ɲɔgɔn kan, den bɛ se ka taamasiɲɛ wɛrɛw fana jira i n’a fɔ farigan, balodɛsɛ, jaŋɔyi, bange kɔnɔ girinya dɔgɔyali, mɛnni gɛlɛya, ani sugunɛbilenni.
O b’a jira ko a nafa ka bon kosɛbɛ ka taa dɔgɔtɔrɔso la a waati la ani ka sɛgɛsɛgɛli wajibiyalenw kɛ kɔnɔmaya waati. O sababu fɛ, aw bɛ se ka kɔn k’a dɔn ni nin bana suguya ninnu bɛ aw la walima ni farikolo tangacogo bɛ aw la.
Tumu dɔw ni kansɛriw
Denmisɛnninw ka kansɛri suguya dɔw fana bɛ se ka nin ‘bulu mufin’ in bila mɔgɔ la. Ninnu ye banaw ye minnu man ca kosɛbɛ.
- Histiocytose (banakisɛfagalan).
- Jolidɛsɛ (joli kansɛri) .
- Mastocytose (Mastocytose) bɛ sɔrɔ
- Neuroblastoma (banakisɛfagalanw).
- Rabdomyosarcoma (rabdomyosarcoma) (Rabdomyosarcoma) ye bana ye
- Miyɛloprolifératif disorder transitoire - O ka ca kɛrɛnkɛrɛnnenya la denmisɛnniw na minnu bɛ ni Down syndrome ye.
Nin bana ninnu bɛ se ka kɛ ni taamasiɲɛw ye i n’a fɔ sɛgɛnba, farigan, farikolojidɛsɛ, ɲɛgɛnɛsiralabanaw (jodɛsɛ fɛ), ɲɛgɛnɛsira funu, ani ninakili gɛlɛya.
Gɛlɛya wɛrɛ minnu bɛ sɔrɔ joli bɔli la (Hématopoïèse extramédullaire) .
I n’a fɔ an y’a fɔ cogo min na ka tɛmɛ, o nɔ ninnu fana bɛ sɔrɔ joli-sira-funu kɔfɛ. Fɛn wɛrɛ minnu bɛ kɛ sababu ye ka o kɛ, olu ye:
- Den kuraw ka joli-sira-funubana : Den ka joli kuru bilenmanw tiɲɛni teliya la ka a sababu kɛ fɛn dɔw ye i n’a fɔ ABO joli suguya bɛnbaliya ba ni den cɛ.
- Spherocytosis héritage : Bana min bɛ sɔrɔ cɛya la, min bɛ kɛ sababu ye ka joli kuru bilenmanw cogoya Changer.
- Filaninw ni filaninw ka jolidoncogo : Joli tɛ kelen ye filaninw ni ɲɔgɔn cɛ minnu ka denso ye kelen ye.
Dɔgɔtɔrɔw bɛ a sababu yɛrɛyɛrɛ sɔrɔ cogo di?
Den ka dɔgɔtɔrɔ bɛna fɔlɔ ka den sɛgɛsɛgɛ ka ɲɛ ani ka a lajɛ ni bana taamasiɲɛ wɛrɛw tɛ a la. O kɔ, u bɛna sɛgɛsɛgɛli caman kɛ walasa ka a sababu tigitigi dɔn.
| Kɔrɔbɔli | A bɛ mun Sɛgɛsɛgɛ? |
|---|---|
| Joli sɛgɛsɛgɛliw | Joli jate dafalen (CBC), banakisɛw ni jolidɛsɛ wɛrɛw sɛgɛsɛgɛli. |
| Sugunɛ sɛgɛsɛgɛli | Banakisɛ dɔw taamasiɲɛw ani furakɛli cogoyaw. |
| Kɔnɔbara basigilen/Kɔnɔbara sɔgɔli | Aw bɛ kunsɛmɛnasumaya (CSF) sɛgɛsɛgɛ walasa ka bana taamasiɲɛw lajɛ. |
| Fari biyɔpisi (biopsie) kɛ | Walasa ka jolidɛsɛ walima kansɛribana wɛrɛw lajɛ. |
| Kolotugudaw biyopisi | Aw bɛ jolidɛsɛ ɲini, jolidɛsɛ wɛrɛw, banakisɛw, ani kansɛri. |
| Kɔnɔbara lajɛ | Ka a lajɛ ni sugunɛ ni sugunɛ bonyalen don ani kurukuruw i n’a fɔ neuroblastoma. |
Ni siga bɛ a la ko TORCH banakisɛ bɛ a la, dɔgɔtɔrɔ bɛ se ka sɛgɛsɛgɛli bɛnnenw fana fɔ ba ye.
O furakɛcogo jumɛnw bɛ yen?
O ye gɛlɛya ye min bɛ mɔgɔ caman kan. Aw ye aw hakili to a la ko ‘blueberry muffin rash’ furakɛli ye ka bana basigilen furakɛ min ye a sababu ye. O kɔrɔ ye ko ikomi nin nɔ ninnu ye taamasiɲɛ ye, an ka kan ka bana basigilen furakɛ min ye bana in bila mɔgɔ la.
I n'a fo:
- Ni a sababu ye TORCH banakisɛ ye, banakisɛfagalanw, banakisɛfagalanw, walima banakisɛfagalanw bɛ di a ma.
- Ni a sababu ye kansɛri ye i n’a fɔ neuroblastoma, opereli, chimiothérapie, immunothérapie, walima radiation therapy bɛ se ka kɛ wajibi ye.
Aw den ka dɔgɔtɔrɔso jɛkulu bɛna furakɛli fɛɛrɛ ɲuman ɲɛfɔ aw den ye, o la aw kana siga ka kuma u fɛ ɲininkali walima haminanko minnu bɛ se ka kɛ aw la.
Tuma jumɛn na aw ka kan ka taa dɔgɔtɔrɔso la joona?
O jaabi kelenpe ye "O yɔrɔnin bɛɛ!"
Ni aw ye nɔ bulu-buluman walima kuru dɔ ye aw den fari la i n’a fɔ nin, aw kana aw ɲɛmajɔ o la. Ni den bɛ furakɛli la kaban dɔgɔtɔrɔso la, aw bɛ dɔgɔtɔrɔ walima dɔgɔtɔrɔso baarakɛla ladɔnniya joona. Ni aw bɛ so kɔnɔ, aw bɛ teliya ka taa ni den ye dɔgɔtɔrɔso la min ka surun aw la, furakɛli kɔrɔtɔlen yɔrɔ (ETU).
Hali ni nin bana in man ca, a bɛ se ka kɛ taamasiɲɛ ye min b’a jira ko fɛn jugu dɔ bɛ ka kɛ den fari la. O bɛ se ka siran kosɛbɛ, nka min nafa ka bon kosɛbɛ, o ye ka siran ani ka teliya ka wale kɛ. Dɔgɔtɔrɔso jɛkulu bɛna a sababu sɔrɔ joona ani ka furakɛli ɲuman di aw den ma.
Take-Home cikan
- Blueberry Muffin Rash tɛ farikolojidɛsɛ dɔrɔn ye, a bɛ se ka kɛ bana jugu dɔ taamasiɲɛ ye min bɛ a kɔnɔ.
- Fɛn kɛrɛnkɛrɛnnen dɔ ye ko a bɛ i n’a fɔ o nɔgɔ ninnu bɛ sɔrɔ fari kɔnɔ, u tɛ kɛ fari sanfɛ.
- Ni aw ye nin nɔ suguya ninnu kɔlɔsi den fari la, aw kana mɛn ka u jira dɔgɔtɔrɔ la joona walima ka taa dɔgɔtɔrɔso la furakɛli kɔrɔtɔlen yɔrɔ la (ETU).
- A nafa ka bon ka dɔgɔtɔrɔw ka ladilikan ɲumanw ɲini ani ka sɛgɛsɛgɛli kɛ kɔnɔmaya waati walasa ka banakisɛw bali walima k’u dɔn i n’a fɔ TORCH joona.
- Aw bɛ kuma kɛnɛ kan ni aw ka dɔgɔtɔrɔso jɛkulu ye aw ka bana sɛgɛsɛgɛli ni a furakɛcogo kan. Aw ni aw den mago bɛ dɛmɛ min na, u bɛna o di.











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