An ka Budd-Chiari Syndrome dɔn, o ye bana jugumanba ye min na sugunɛbilenni joli siraw bɛ datugu.

Sugunɛ ye an farikolo yɔrɔ nafama dɔ ye. I n’a fɔ iziniba, sugunɛ bɛ ni joli siraba dɔ ye min bɛ nɔgɔw bɔ joli la. Miiri k’a filɛ, mun bɛ kɛ ni o joli sira kelen walima u caman bɛ datugu walima ni u bɛ dɔgɔya? Furakɛcogo la, nin ye bana ye min man teli ka sɔrɔ nka a ka jugu kosɛbɛ, a bɛ sɔrɔ joli siraw datuguli fɛ minnu bɛ joli ta ka bɔ sugunɛ na . A nafa ka bon kosɛbɛ ka o dɔn. An ka kuma o kan cogo nɔgɔman na.

N’an y’a fɔ cogo nɔgɔman na, Budd-Chiari Syndrome ye mun ye?

O faamuyacogo ɲuman ye ka miiri min bɛ kɛ ni jibolisira dɔ datugulen don an ka so kɔnɔ. I n’a fɔ pibiliki datugulen bɛ fa ji la cogo min na, ni sugunɛbaralabana bɛ datugu, joli bɛ daminɛ ka ɲɔgɔn lajɛ sugunɛ kɔnɔ. O bɛ se ka kɛ joli kurulen ye, jolisira kɔnɔ funu, walima degun min bɛ bɔ kɛnɛma.

Ni joli dalajɛra o cogo la, sugunɛ bɛ funu ka bonya. O dɔrɔn tɛ, nka ɲɛgɛnɛsira fana bɛ se ka bonya o degun in sababu fɛ. Ni nin bana in tora senna, a ka ca a la kɔlɔlɔ jugu damadɔ wɛrɛw bɛ se ka sɔrɔ.

• Tansiyɔn jiginni dawolo la : Tansiyɔn damatɛmɛnen jolisiraba la min bɛ joli ta ka taa sugunɛ na (`portal vein`).
• Varices : K’a sababu kɛ nin tansiyɔnba in ye, joli sira minnu bɛ yɔrɔw la i n’a fɔ dumunikɛminɛnw ni kɔnɔbara, olu bɛ bonya, wa u bɛ se ka pɛrɛn ka joli bɔ.
• Ascite (Ascite): O ye bana ye min na ji i n’a fɔ ji bɛ kɔnɔbara fa, ka a to a bɛ funu. An b'o Weele ko "ascites".
• Cirrhose : Sugunɛ tiɲɛni kuntaalajan, o bɛ kɛ sababu ye ka sugunɛbilenniw faga ani ka sugunɛbilenni bila a la. Nin ye bana jugu ye min tɛ se ka kɔsegin.

Nin bana in suguya wɛrɛw bɛ yen wa?

Ɔwɔ, a bɛ se ka tila suguya kunbaba caman na ka da a taamasiɲɛw teliya ni u juguya kan. Ani fana, suguya fila bɛ yen minnu sinsinnen bɛ sababu basigilen kan.

Ka kɛɲɛ ni a sababu ye, suguya belebele fila bɛ yen:

1. Budd-Chiari Syndrome primaire : O cogo la, gɛlɛya bɛ joli sira yɛrɛ kɔnɔ . O bɛ se ka sɔrɔ joli kurulen (thrombus) walima funu fɛ jolisira kɔnɔ.

2. Budd-Chiari Syndrome filanan : Yan, gɛlɛya bɛ bɔ joli sira kɔkan . Misali la, kansɛri walima kansɛri tɛ kuru min bɛ sugunɛ kɛrɛfɛ, o bɛ se ka kɛ sababu ye ka joli sira dɔ datugu.

O taamasiɲɛw ye mun ye?

Nin bana in taamasiɲɛw bɛ se ka ɲɔgɔn ta mɔgɔ kelen-kelen bɛɛ la. U fana bɛ ɲɔgɔn ta ka kɛɲɛ ni bana suguya ye. Nka, taamasiɲɛ damadɔw bɛ yen minnu ka teli ka ye, minnu bɛ se ka ye.

Mun na Budd-Chiari Syndrome bɛ sɔrɔ? O sababu ye mun ye?

A ka ca a la, o bɛ sɔrɔ furakɛli dɔ fɛ min bɛ dɔ fara farikolo ka joli kurulenw bɔli kan.

• Jolibanaw (Myeloproliferative neoplasms - MPNs): Ninnu ye joli kansɛri suguya dɔw ye minnu man ca. U bɛ kɛ sababu ye farikolo ka joli kuru caman bɔ, o bɛ dɔ fara joli kuruli farati kan.
• Jolilabanaw (hypercoagulable disorders): Joli bɛ wuli joona kojugu ka a sababu kɛ jamu sababuw walima bana wɛrɛw ye. Misali la, banaw i n’a fɔ `Protéine C` walima `S` dɛsɛ, `Antiphospholipid anticorps syndrome`.
• Sugunɛ walima sugunɛbilenni : Kansɛri walima tumu jugumanw bɛ se ka kɛ sababu ye ka joli siraw degun ka bɔ kɛnɛma.
• Kɔnɔmaya: A dacogo la, musow ka joli kurulen ka bon dɔɔni kɔnɔmaya waati.
• Bangekɔlɔsi furakisɛw : Bangekɔlɔsi furakisɛ suguya dɔw tali fana bɛ se ka dɔ fara joli kuruli kan.
• Bana wɛrɛw : Bana minnu bɛ i n’a fɔ `Sickle cell disease` ani `Inflammatory bowel disease (IBD)` fana bɛ se ka o lase mɔgɔ ma.

Nka, tuma dɔw la, ko dɔw bɛ yen, sababu tigitigi tɛ se ka sɔrɔ minnu na . An b'o Weele ko `idiopathique`.

Dɔgɔtɔrɔ bɛ o sɔrɔ cogo di?

Ni aw taara dɔgɔtɔrɔso la, a bɛna aw ka bana taamasiɲɛw lamɛn ka ɲɛ, ka aw sɛgɛsɛgɛ, ka tila ka yamaruya di aw ma ka sɛgɛsɛgɛli caman kɛ walasa ka bana in sɛgɛsɛgɛ.

1. Joli sɛgɛsɛgɛli : Olu bɛ dɛmɛ ka sugunɛbilenni anzimu hakɛ lajɛ ani ka a dɔn ni farati bɛ joli kuruli la.

2. Jala sɛgɛsɛgɛliw:

• Doppler Ultrasound Scan: Nin ye sɛgɛsɛgɛli fɔlɔ ye, min ka nɔgɔn, wa a nafa ka bon kosɛbɛ. A bɛ baara kɛ ni mankanw ye walasa ka joli bolicogo lajɛ sugunɛ joli siraw la. O bɛ se ka hakilina ɲuman di a ma ni balili bɛ yen.
• CT Scan walima MRI Scan: Nin scan suguya ninnu bɛ se ka sugunɛ ni a lamini yɔrɔw ja jɛlenw ta. Tuma dɔw la, ji kɛrɛnkɛrɛnnen dɔ (`contrast material`) bɛ se ka pikiri kɛ farikolo la walasa joli siraw ka ye ka ɲɛ.
• Venography (venogramme): Nin sɛgɛsɛgɛli in bɛ kɛ ni sɛgɛsɛgɛli wɛrɛw ma ɲɛ. Nin sɛgɛsɛgɛli in na, ji kɛrɛnkɛrɛnnen dɔ bɛ pikiri kɛ joli sira dɔ la ani ka X-ray ja ta walasa ka joli bolicogo lajɛ.

3. Sugunɛbilenni : Walasa ka a dɔn tigitigi tiɲɛni hakɛ min kɛra sugunɛ na ani ni kirinni kɛra, sugunɛ yɔrɔ fitininba dɔ bɛ ta ni pikirijikɛlan fitinin ye ka a lajɛ ni mikroskɔpu ye.

O furakɛcogo jumɛnw bɛ yen?

Furakɛli kunba fila bɛ yen. O dɔ ye ka joli sira min datugulen don, o da wuli kokura walima ka sira wɛrɛ dabɔ joli la. Tɔɔ kelen ye ka a sababu jugumanba furakɛ.

Furakɛli ni furaw ye

A daminɛ na, furaw i n’a fɔ joli-sira-funu-minɛnw (joli-minɛnw ) bɛ di walasa ka joli kurukuruw labɔ ani ka joli kuru kura bali. Misali la, furaw i n’a fɔ ɛpirini walima warfarin.

Furakɛli kɛrɛnkɛrɛnnen minnu tɛ opereli ye

Ni fura dɔrɔn tɛ se ka bana in kunbɛn, furakɛli fɛɛrɛ caman bɛ yen minnu bɛ kɛ dɔgɔtɔrɔ kɛrɛnkɛrɛnnenw fɛ.

• Transjugular Intrahepatic Portosystemic Shunt (TIPS): Nin ye fɛɛrɛ ye min ka gɛlɛn dɔɔni. N'an y'a Fɔ cogo nɔgɔman na, a bɛ "bypass" dɔ Dabɔ sugunɛ kɔnɔ. Tubabufura fitini dɔ (stent) bɛ don tansiyɔnba dawolo sira ni sugunɛbara cɛ, o bɛ joli bɔ sugunɛ na. O bɛ sira kura dabɔ joli ka woyo ka sɔrɔ a ma datugu.
• Percutaneous Transluminal Angioplasty : O ye ka joli sira dɔ fiyɛ min datugulen don walima min bɛ dɔgɔya ni balon ye. Tuma dɔw la, tubabufura fitinin dɔ bɛ don a kɔnɔ min bɛ i n’a fɔ nɛgɛ (`stent`) walasa minɛn kana dɔgɔya tuguni.

Sugunɛbilenni

Ni furakɛli tɔw bɛɛ ma ɲɛ, walima ni sugunɛ ma ɲɛ pewu (sugunɛ dɛsɛ) walima ni sirozi ye a sɔrɔ, fɛɛrɛ laban ye sugunɛbilenni ye min ka kɛnɛ.

Siniɲɛsigi ye mun ye ni nin bana in ye?

A ɲɛfɔli bɛ bɔ fɛn caman na. Bana in bɛ dɔn joona cogo min na, a tiɲɛni hakɛ, ani a bɛ furakɛ cogo min na, o bɛɛ nafa ka bon.

Ni a ma furakɛ, banabagatɔ min joli siraw datugulen don pewu, o bɛ se ka sa sugunɛbaralabana fɛ san saba ɲɔgɔn kɔnɔ. Nka, ni furakɛli kɛra ka ɲɛ, kɛrɛnkɛrɛnnenya la sugunɛbilenni, a ka ca a la, aw bɛ se ka ɲɛnamaya jan kɛ. O la, kunnafoni ɲuman min bɛ sɔrɔ o ko la, o bɛ bɔ aw ka dɔgɔtɔrɔ fɛ. A bɛna o ɲɛfɔ i ye tigitigi ka kɛɲɛ ni i ka ko ye.