Yala aw denmisɛnnin bɛ farigan, da ŋɛɲɛ walima dadimi sɔrɔ don kelenw na kalo o kalo wa? Yala bana kelen bɛ ban, ka segin dɔgɔkun fila walima dɔgɔkun saba kɔfɛ wa? I bɛ se ka miiri ko: “Ne den farikolo tangacogo barika ka dɔgɔ.” Ɔwɔ, o bɛ se ka kɛ tiɲɛ ye. Nka kun min bɛ nin bana basigilen in kɔfɛ, o bɛ se ka kɛ bana ye min man ca kosɛbɛ. Bi, an bɛ kuma o cogoya sugu dɔ kan, n’o ye neutropenie cyclique ye.
N’an y’a fɔ cogo nɔgɔman na, neutropenie cyclique ye mun ye?
Walasa k’o faamu, an ka kan ka fɔlɔ ka sɔrɔdasi dɔ dɔn an joli la. O sɔrɔdasi tɔgɔ ye ko neutrophil . Nin neutrophil in ye joli kuru finman suguya dɔ ye min b’an tanga banaw ma, a kɛtɔ ka banakisɛw kɛlɛ, kɛrɛnkɛrɛnnenya la banakisɛw, minnu bɛ don an fari la. A bɛ iko kɛlɛbolo min bɛ an farikolo kɔnɔ.
Neutropenie ye ni neutrophil sɔrɔdasi hakɛ bɛ joli la ka jigin ka tɛmɛ a hakɛ kan. I n’a fɔ kɛlɛbolo bɛ barika dɔgɔya cogo min na n’a ka sɔrɔdasiw ka dɔgɔ, ni neutrophils (banakisɛfagalanw) ka dɔgɔ, an farikolo farikolo tangacogo bɛ barika dɔgɔya ani an bɛ daminɛ ka banakisɛw sɔrɔ nɔgɔya la.
Sisan an ka daɲɛ cyclique kɔrɔ lajɛ . Cyclic kɔrɔ ye "cyclique" ye. O kɔrɔ ye ko neutrophils hakɛ tɛ dɔgɔya tuma bɛɛ. A bɛ wuli ka jigin ka kɛɲɛ ni waati bolodacogo ye min bɛ kɛ tuma bɛɛ, ka kɛɲɛ ni sɛrɛkili ye. Walasa ka tiɲɛ fɔ, a ka ca a la dɔgɔkun saba o dɔgɔkun saba (tile 21 ɲɔgɔn) , neutrophils hakɛ bɛ dɔgɔya kosɛbɛ tile saba fo tile duuru. O kɔ, a bɛ segin a cogo kɔrɔ la, o kɔ a bɛ jigin tuguni dɔgɔkun saba nataw kɔnɔ. O sɛrɛkili in bɛ Kɛ cogo la min bɛ Se ka Fɔ ka ɲɛ kosɛbɛ.
N’an y’a fɔ cogo nɔgɔman na, neutropenie cyclique ye bana ye min na neutrophil cellules (banakisɛfagalanw) hakɛ bɛ dɔgɔya, minnu bɛ an farikolo tanga banaw ma, ka kɛɲɛ ni don o don sɛgɛsɛgɛli latigɛlen ye, o bɛ dɔ fara banakisɛ sɔrɔli farati kan.
O bana in man ca kosɛbɛ. Sɛgɛsɛgɛlikɛlaw ko diɲɛ kɔnɔ mɔgɔ miliyɔn kelen o miliyɔn kelen dɔrɔn de bɛ nin bana in na.
Nin bana in taamasiɲɛw ye jumɛnw ye?
Nin bana in kɛrɛnkɛrɛnnen ye ko a taamasiɲɛw bɛ bɔ ka kɛɲɛ ni farikolojidɛsɛbanakisɛ hakɛ dɔgɔyali ye. O kɔrɔ ye ko nin taamasiɲɛ ninnu bɛ bɔ tile saba fo tile naani kɔnɔ ni neutrophils (banakisɛfagalanw) dɔgɔyara, wa ni neutrophils (banakisɛfagalanw) hakɛ seginna a cogo kɔrɔ la, a taamasiɲɛw bɛ tunu.
| Taamaʃyɛn | Cogojirali |
|---|---|
| Sumaya ni sɛgɛn | Ni neutrophils (banakisɛfagalanw) ka dɔgɔn, banakisɛ taamasiɲɛ fɔlɔ bɛ se ka kɛ farigan ye. Ka fara o kan, farikolo bɛ se ka kɛ ko ɲɛnamaya tɛ a la. |
| Da kɔnɔdimi ni dawolodimi | Nin ye bana taamasiɲɛ ye min ka teli ka kɛ. A bɛ se ka dimi bila da kɔnɔ ani ɲinw na. A bɛ se ka kɛ sababu ye fana ka dawolodimi bila mɔgɔ la. |
| Denso kɔnɔ bana | A bɛ se ka joli bɔ tuma caman na ani ka funu kɛ ɲinw na. |
| Banakisɛ minnu bɛ segin-ka-bɔ | Ninakilidegunw (farigan, sɔgɔsɔgɔ), dumunikɛminɛnw (kɔnɔdimi), ani faritanabana (cellulitis) bɛ se ka kɛ tuma caman. |
Nin taamasiɲɛ ninnu cogoya bɛ se ka Changé ɲɛnamaya bɛɛ kɔnɔ. Mɔgɔ caman fɛ, a taamasiɲɛw juguya bɛ dɔgɔya ni u sera balikuya la . Dawoloci ni ɲinw gɛlɛyaw ka ca funankɛninw na, ka sɔrɔ kungolodimi ni sinjibana (sinusitis) ka ca mɔgɔkɔrɔbaw la.
Mun na o bɛ ka kɛ?
neutropenie cyclique bɛ sɔrɔ jamu jiginni fɛ . A sababuba ye ELANE jamu caman yeli ye an farikolo la.
Miiri jamu dɔ la i n’a fɔ cikanw kulu minnu b’a fɔ an farikolo yɔrɔw ye u ka baara kɛcogo la. ELANE jamu kɔnɔ, cikanw bɛ sɔrɔ anzimu dɔ dilanni na min bɛ neutrophils dɛmɛ ka baara kɛ ka ɲɛ. Ni fiɲɛ walima fɛn dɔ jiginna o jamu in na, neutrophiles tɛ se ka baara kɛ ka ɲɛ.
Nin bana in bɛ se ka sɔrɔ bangebagaw fɛ ka se denw ma, walima a bɛ se ka sɔrɔ den kɔnɔbara la.
O jamu nafama in kosɔn, .
- A bɛ se ka kɛ farikolo tɛ se ka neutrophils (banakisɛfagalan) caman dilan.
- N’o tɛ, neutrophiles bɛ se ka sa joona.
- Walima a bɛ se ka kɛ ko neutrophils tɛ baara kɛ ka ɲɛ.
Dɔgɔtɔrɔ, i bɛ nin bana in sɛgɛsɛgɛ cogo di?
A ka ca a la, nin taamasiɲɛ ninnu bɛ ye kabini u bange waati, o la a ka ca a la bana in bɛ sɔrɔ denmisɛnniw na. Dɔgɔtɔrɔ bɛ fɛn caman jateminɛ walasa ka bana in dafa.
- Bana in min bɛ denbaya kɔnɔ : Ikomi nin ye ciyɛntabana ye, a bɛ lajɛ ni nin bana in bɛ mɔgɔ wɛrɛ la denbaya kɔnɔ (bangebagaw, balimakɛw).
- Joli sɛgɛsɛgɛliw: O de nafa ka bon kosɛbɛ. aw ka dɔgɔtɔrɔ bɛna aw ka jolisegindumuni hakɛ lajɛ siɲɛ fila fo siɲɛ saba dɔgɔkun kɔnɔ dɔgɔkun wɔɔrɔ ɲɔgɔn . O bɛna kɛ walasa ka a dɔn ni aw ka neutrophils hakɛ bɛ ka dɔgɔya ka taa a fɛ.
- Taamasiɲɛw cogoya : Dɔgɔtɔrɔ bɛna bana taamasiɲɛw kɛcogo sɛgɛsɛgɛ ka ɲɛ (dɔgɔkun 3 o dɔgɔkun 3 ɲɔgɔn). O cyclique pattern in bɛ dɛmɛ ka nin danfara don ni neutropenie suguya wɛrɛw ye.
- Jamu sɛgɛsɛgɛli : Tuma dɔw la, jamu sɛgɛsɛgɛli bɛ se ka kɛ walasa ka a dɔn ni fɛn dɔ b’a la ka ELANE jamu sɛgɛsɛgɛ.
Ni dɔgɔtɔrɔ bɛ nin bana in sɛgɛsɛgɛ, a ka kan ka farikolojidɛsɛ suguya wɛrɛw bɔ kɛnɛ kan minnu taamasiɲɛw bɛ ɲɔgɔn ta, i n’a fɔ `Neutropenie congénitale jugu` (a tun bɛ wele fɔlɔ ko `Kostmann syndrome`), `Neutropenie autoimmune`, ani `Neutropenie idiopathique`.
O furakɛcogo jumɛnw bɛ yen?
Furakɛli kunba fila bɛ yen. O dɔ ye ka banakisɛw furakɛ minnu bɛ yen. Tɔɔ kelen ye ka dɔ fara farikolojidɛsɛbanakisɛ hakɛ kan ani ka bana nataw bali.
| Furakɛli kɛcogo | Baarakɛcogo |
|---|---|
| Banakisɛfagalanw | Olu bɛ di walasa ka banakisɛw kɛlɛ minnu bɛ sɔrɔ waatiw la ni neutrophils dɔgɔyara. |
| G-CSF furakɛli | O de ye furakɛli kunba ye min bɛ nɔ bɔ kosɛbɛ. G-CSF (Granulocyte colony-stimulating factor) ye fura ye min bɛ an kolotugudaw lawuli walasa ka neutrophils caman dilan (misali la filgrastim (Neupogen®)). A bɛ kɛ pikiri ye, wa a ye fura ye min tɛ mɔgɔ tɔɔrɔ, a bɛ se ka kɛ waati jan kɔnɔ. |
| Kɔnɔnatumuw cili | Nin ye fɛɛrɛ ye min bɛ kɛ dɔrɔn bana jugumanba bɛ mɔgɔ minnu na, ani minnu tɛ G-CSF furakɛli jaabi. O fɛɛrɛ in na, jirisun kɛnɛmanw bɛ don farikolo la walasa ka banakisɛ bananenw bila u nɔ na. |
Yala furakɛli kɔlɔlɔ dɔw bɛ yen wa?
G-CSF furakɛli bɛ se ka kɔlɔlɔ misɛnniw lase mɔgɔ ma. Nka, a ka ca a la dɔgɔtɔrɔw bɛ nin bana in furakɛli daminɛ ni a tata hakɛ dɔgɔman ye, o la a kɔlɔlɔw ka dɔgɔn.
- Kunkolodimi
- Dimi bɛ kɛ kolotugudaw ni kolotugudaw la
- Dusukunnata ni kɔnɔboli
Nin ɲɔgɔnna kow bɛ se ka kɛ. Aw bɛ kuma aw ka dɔgɔtɔrɔ fɛ ka ɲɛ aw bɛ furakɛli min kɛ ani a kɔlɔlɔw kan.
Ne ka kan ka dɔgɔtɔrɔ wele waati jumɛn?
Ni aw walima aw den bɛ ni cyclique neutropénie ye, a nafa ka bon kosɛbɛ aw ka dɔgɔtɔrɔ ka ladilikan ɲini ni aw ye banakisɛ taamasiɲɛ dɔw ye dɔrɔn .
Aw ye aw janto kɛrɛnkɛrɛnnenya la nin fɛn ninnu na:
* Farigan
* Dimi bɛ kɛ farikolo yɔrɔ dɔ la
* Fari funu walima a bilenni
Ni aw ye nin taamasiɲɛ ninnu dɔ ye, aw bɛ taa dɔgɔtɔrɔso la joona. Aw kana siga ka taa Kɔrɔtɔko ɲɛmɔgɔso la (ETU) ni a mago bɛ a la.
An ka kan ka mun kɛ walasa ka an yɛrɛ tanga banakisɛw ma?
Ka fara aw yɛrɛ tanga banakisɛw ma, aw ka kan ka aw janto fana ni aw ka jolisegindumuni hakɛ dɔgɔyara.
- Aw bɛ aw tɛgɛw ko ka ɲɛ tuma bɛɛ, kɛrɛnkɛrɛnnenya la sani aw ka dumuni kɛ ani aw kɛlen kɔ ka baara kɛ ni ɲɛgɛn ye.
- Aw bɛ da kɔnɔ kɛnɛya ɲuman mara. aw bɛ aw ɲinw ko don o don ani ka taa ɲinw furakɛla fɛ tuma bɛɛ .
- Aw bɛ boloci ladilikanw bɛɛ kɛ a waati la.
- Aw kana maga aw ɲɛda, aw ɲɛw ani aw nugu la k’a sɔrɔ aw ma aw tɛgɛ ko.
- Aw bɛ furaw ta i n’a fɔ dɔgɔtɔrɔ y’a fɔ cogo min na tigitigi ani ka aw joli sɛgɛsɛgɛli kɛ a waati la.
Hali ni nin bana in bɛ kɛ a si bɛɛ la, furakɛli ɲɛtaa i n’a fɔ G-CSF ye sira di sisan mɔgɔ caman ma minnu bɛ ni cyclique neutropenie ye, olu ka se ka ɲɛnamaya kɛ cogo la min bɛ bɛn pewu . Nafa min b’a la, o ye ko hali ni neutropenie suguya wɛrɛw bɛ kansɛri sɔrɔli farati lase mɔgɔ ma, i n’a fɔ jolidɛsɛ, neutropenie cyclique tɛ o kɛ.
Take-Home cikan
- Neutropenie cyclique ye bana ye min man teli ka sɔrɔ jamu fɛ, neutrophil cellules minnu bɛ banakisɛ kɛlɛ, olu hakɛ bɛ dɔgɔya cycliquement.
- A ka ca a la, bana taamasiɲɛw (sumaya, da kɔnɔdimi) bɛ ye cogo la min bɛ kɛ siɲɛ kelen ɲɔgɔn dɔgɔkun 3 o dɔgɔkun 3.
- Walasa ka bana sɛgɛsɛgɛ, joli sɛgɛsɛgɛli ka kan ka kɛ ka to ka dɔgɔkun caman kɛ walasa ka a jira ko jolisegindumuni hakɛ bɛ taa ɲɔgɔn fɛ.
- Ikomi furakɛli minnu bɛ se ka kɛ kosɛbɛ i n’a fɔ G-CSF, olu bɛ yen, banabagatɔw bɛ se ka ɲɛnamaya kɛ cogo bɛnnen na.
- A nafa ka bon kosɛbɛ ka dɔgɔtɔrɔso laadilikan ɲini ni aw ye bana taamasiɲɛ o taamasiɲɛ ye dɔrɔn (sumaya, dimi, funu).











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