Sugunɛ ye farikolo yɔrɔ nafama dɔ ye. A bɛ iko izini belebeleba dɔ. A bɛ baara nafama caman kɛ, i n’a fɔ ka baga bɔ an ka dumuni duntaw la, ka fanga mara, ani ka bile dilan, o min b’an dɛmɛ ka dumuni sɔgɔ. O la, ka nin izini in to baara la ka ɲɛ, o nafa ka bon kosɛbɛ an farikolo bɛɛ ka kɛnɛyako la. Nka tuma dɔw la bana dɔw bɛ yen minnu bɛ sugunɛ minɛ u makun na, bana minnu tɛ mɛn kosɛbɛ. Bi an bɛna kuma o bana sugu dɔ kan. O ye Primary Biliary Cholangitis ye, walima PBC i n’a fɔ an b’a wele cogo min na ni kuma surun ye.
N’an y’a fɔ cogo nɔgɔman na, PBC ye mun ye?
Okey, an ka nin ko in kɛ cogo nɔgɔman na. I n’a fɔ n y’a fɔ cogo min na ka tɛmɛ, sugunɛ bɛ ji dɔ bɔ min bɛ wele ko bile . O de b’an dɛmɛ ka tulumafɛnw sɛnɛ an bɛ dumuni minnu dun, ka witamini dɔw minɛ, ka kolosinsinnanw ni bagaw bɔ farikolo la minnu man ɲi.
Sisan, aw ye miiri, sugunɛ kɔnɔ, joli siraw bɛ yen, minnu bɛ i n’a fɔ tubabufura fitini dɔ. Sugunɛ bɛ bile min dilan, o bɛ taama o tubabufura misɛnnin ninnu fɛ, ka mara yen, o bɛ dɛmɛ ka dumuni sɔgɔ ni a mago bɛ a la. Fɛn min bɛ kɛ PBC la , o ye ko o bile siraw bɛ tiɲɛ.
Ni o siraw tiɲɛna, bile tɛ se ka woyo ka ɲɛ, wa a bɛ daminɛ ka dalajɛ sugunɛ kɔnɔ. A bɛ iko jibolisira karilen min bɛ so fa ji la. Bili min bɛ dalajɛ o cogo la, o bɛ daminɛ ka sugunɛbilenni tiɲɛ. Ni o tiɲɛni in kɛra waati tɛmɛnen kɔfɛ, sɔgɔsɔgɔninjɛ bɛ daminɛ ka kɛ sugunɛbilenni kɛnɛmanw nɔ na. an bɛ nin bana in wele ko cirose . Ni sugunɛ kɛra joginni ye o cogo la, a ka baarakɛcogo ɲuman bɛ ɲini ka tiɲɛ pewu.
PBC bana taabolo naani
PBC tɛ juguya siɲɛ kelen. A bɛ yiriwa dɔɔni dɔɔni, ka tɛmɛ taabolo damadɔ fɛ. A ka c’a la, dakunba naani bɛ yen.
| Dakun | Min bɛ Kɛ |
|---|---|
| Etape 1 (Etape Portal) . | Nin ye taabolo fɔlɔ ye. Min bɛ kɛ yan, o ye funu ye, o ye funu ye, biɲɛdimi lamini na. O fɛn caman Changement bɛ daminɛ sugunɛ da la, joli siraw ni joli siraw bɛ fara ɲɔgɔn kan yɔrɔ min na. |
| Etape 2 (Etape Periportal) . | Sisan, funu jɛnsɛnna dɔɔni ka taa a fɛ, wa a bɛ daminɛ ka bɔ joli siraw lamini na. O waati de la, sɔgɔsɔgɔninjɛ (fibrose) hakɛ misɛnniw bɛ daminɛ ka bɔ. |
| Etape 3 (Septal Etape) . | Sisan, o sɔgɔsɔgɔninjɛ jɛnsɛnna ka taa a fɛ, ka jɛɲɔgɔnya don sugunɛ yɔrɔ dɔw ni ɲɔgɔn cɛ. A bɛ i n’a fɔ sɔgɔsɔgɔninjɛ minnu bɛ i n’a fɔ wuluwulu, olu bɛ jɛnsɛn sugunɛ fan bɛɛ la. |
| Taabolo 4nan (Cirrhose biliaire) . | Nin ye bana jugumanba ni a laban ye. O waati la, ŋɛɲɛw jɛnsɛnna sugunɛ fan bɛɛ la, ka sugunɛ girinya ani ka kurukuruw kɛ. O bana in bɛ wele ko cirose. Nin waati in na, sugunɛ ka baara bɛ tiɲɛ kosɛbɛ. |
Mun de bɛ PBC bila mɔgɔ la tiɲɛ na?
O ye gɛlɛya ye min bɛ mɔgɔ caman kan. Tiɲɛ na, dɔgɔtɔrɔw ma PBC sababu tigitigi sɔrɔ fɔlɔ. Nka, hakilina min bɛ sɔn sisan, o ye ko a ye bana ye min bɛ sɔrɔ farikolo tangacogo fɛ, min bɛ sɔrɔ jamu ni sigida fɛnw faralen ɲɔgɔn kan .
Okey, nin autoimmune bana in ye mun ye?
N’an y’a fɔ cogo nɔgɔman na, o ye an farikolo yɛrɛ ka farikolo tangacogo baarakɛbaliya ye. A ka c’a la, an ka joli kuru finmanw (kɛrɛnkɛrɛnnenya la T-cell) bɛ banakisɛw kɛlɛ minnu bɛ bana bila mɔgɔ la. Nka PBC la, o farikolo tangalanw bɛ taa juguya la, ka daminɛ ka binkanni kɛ sugunɛbilenni kɛnɛmanw kan. A bɛ iko an yɛrɛ ka kɛlɛbolo bɛ fili ka bin an yɛrɛ ka mɔgɔw kan.
Ni an yɛrɛ ka farikolokisɛw bɛ to ka bin bilenw kan o cogo la, n ye tiɲɛni min fɔ ka tɛmɛ, o bɛ daminɛ ka kɛ.
A tɛ se k’a fɔ ko nin bana in bɛ wuli ka bɔ mɔgɔw la ka taa mɔgɔw la jɛnɛya fɛ. O kɔrɔ ye ko sariya si tɛ yen min b’a jira ko a bɛ ba la dɔrɔn, a denmuso fana bɛna a yiriwa. Nka, ni PBC bɛ denbaya kɔnɔ mɔgɔ dɔ, kɛrɛnkɛrɛnnenya la a somɔgɔ gɛrɛgɛrɛ dɔ (ba, balimamuso walima balimakɛ), o bana in sɔrɔli farati ka bon dɔɔni ka tɛmɛ mɔgɔ gansan kan. O la, a bɛ se ka miiri ko jɛɲɔgɔnya bɛ ni jamu ye.
Jɔn de farati ka bon ka PBC sɔrɔ?
Hali ni mɔgɔ o mɔgɔ bɛ se ka PBC sɔrɔ, mɔgɔ dɔw ka farati ka bon dɔɔni. An k’a lajɛ u ye mɔgɔ minnu ye.
| Farati Factor (Facteur de rôle). | Fɛn wɛrɛw |
|---|---|
| Cɛya ni musoya (Cɛya) . | O ye kabako ye. PBC ka ca musow la. Musow ka teli ka bana in sɔrɔ ka tɛmɛ cɛw kan siɲɛ 9 fo siɲɛ 10 ɲɔgɔn . |
| Si | Nin bana in bɛ mɔgɔ minnu sɔrɔ, olu fanba bɛ san 30 ni san 60 cɛ , nka a bɛ se ka kɛ fana mɔgɔ minnu ka dɔgɔn walima minnu ka ca ni o ye. |
| Denbaya ka tariku | I n’a fɔ n y’a fɔ cogo min na ka tɛmɛ, ni PBC bɛ i ka denbaya kɔnɔ mɔgɔ dɔ (kɛrɛnkɛrɛnnenya la i ba walima i balimamuso) la, bana in sɔrɔli farati ka bon i la ka tɛmɛ jamanaden bɛɛ kan. |
| Jɛnkulu ka ɲɛnamaya kɛcogo | Diɲɛ kɔnɔ, nin bana in ka teli ka sɔrɔ Erɔpu woroduguyanfan mɔgɔw la (i n’a fɔ Ɛsipeɲi ani Skandinavi jamanaw). Nka, a bɛ se ka kɛ jamana ni siya suguya bɛɛ la diɲɛ kɔnɔ. |
O tuma na fɛ, a taamasiɲɛw ye jumɛnw ye?
O de ye ko ye min nafa ka bon kosɛbɛ. Siranfɛn min bɛ PBC la, o ye ko mɔgɔ caman tɛ taamasiɲɛ foyi jira a daminɛ na. A bɛ sɔrɔ tuma dɔw la a danma ni joli sɛgɛsɛgɛli kɛra bana wɛrɛ kan.
Nka ni bana bɛ ka taa ɲɛ, a taamasiɲɛw i n’a fɔ ninnu bɛ se ka bɔ kɛnɛ kan:
- Sɛgɛn: A taamasiɲɛba dɔ ye ka sɛgɛn kojugu kun ɲɛnama tɛ, hali ni i bɛ sunɔgɔ.
- Fari bɛ nɛ bɔ: Aw bɛ se ka nɛ bɔ aw fari fan bɛɛ la min tɛ se ka muɲu, kɛrɛnkɛrɛnnenya la aw bolokɔniw ni aw senkɔniw na.
- Ɲɛ ni da jalen : Ɲɛji bɔli bɛ dɔgɔya ɲɛw la ani nɔgɔ bɔli da la, o bɛ kɛ sababu ye ka jalen ye.
- Joli ni kolotugudaw dimi.
- Dimi dɔɔni walima a tɛ dimi kɔnɔbara kiniyanfan sanfɛla la.
Ni bana bɛ ka taa ɲɛ (ka se sirozi) taamasiɲɛw fana bɛ se ka kɛ i n’a fɔ senw fununi, ji bɛ bɔ kɔnɔbara la, ani ɲɛ ni fari jɛman (jaŋaniya).
Aw ka kan ka taa dɔgɔtɔrɔso la tuma jumɛn?
Ni aw, kɛrɛnkɛrɛnnenya la ni aw ye muso ye min si bɛ san 30 ni san 60 cɛ, aw bɛ taamasiɲɛw sɔrɔ i n’a fɔ sɛgɛn basigilen ani fari bɛ nɛ bɔ kun ɲɛnama tɛ, aw kana a jate dɔrɔn ko “aw bɛ kɔrɔbaya dɔrɔn” walima “ka baara caya kojugu.” Aw bɛ taa aw yɛrɛ lajɛ dɔgɔtɔrɔso la o yɔrɔnin bɛɛ ka kuma o kan.
Dɔgɔtɔrɔ bɛna aw sɛgɛsɛgɛ ani ni a mago bɛ a la, aw bɛ yamaruya di aw ma aw ka joli sɛgɛsɛgɛli caman kɛ. Nin bana in bɛ se ka dɔn nɔgɔya la ni aw ye sugunɛbilenniw ni farikolojɔlifɛn kɛrɛnkɛrɛnnenw (AMA - Antimitochondrial Antibodies) lajɛ. O la, aw kana aw ɲɛmajɔ a taamasiɲɛw la. Ni a sɛgɛsɛgɛra joona, a ka teli ka furakɛ ani ka a kunbɛn.
Take-Home cikan
- PBC ye bana basigilen ye min bɛ sugunɛbaralabana misɛnniw tiɲɛ.
- Nin tɛ bana ye min bɛ mɔgɔw minɛ. A ka ca a la, a bɛ sɔrɔ an farikolo yɛrɛ ka farikolo tangacogo (autoimmune) fili fɛ.
- A daminɛ na, a bɛ se ka kɛ ko bana taamasiɲɛ si tɛ yen fewu. A taamasiɲɛ fɔlɔ minnu ka teli ka ye, olu ye sɛgɛn ni fari ŋɛɲɛ ye.
- Nin bana in ka ca musow la, kɛrɛnkɛrɛnnenya la minnu si bɛ san 30 ni san 60 cɛ.
- Ni siga walima taamasiɲɛ dɔ bɛ aw la nin ko in na, aw bɛ aw yɛrɛ sɛgɛsɛgɛ (A jira, o ye Tayilandikan ye. Typo in my thought process. Must be career). Aw kana aw sen don aw yɛrɛ sɛgɛsɛgɛli la, nka siga t’a la ka taa dɔgɔtɔrɔso la min bɛ se kosɛbɛ ani ka laadilikan ɲini.











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