Ðe viwò ƒe ŋutigbalẽ le ƒoƒom hele sesẽm? Mina míaƒo nu tso Juvenile Systemic Scleroderma ŋu!

Ède dzesii be viwò sue ƒe ŋutigbalẽ trɔ vie kasia? Ðewohĩ ŋutigbalẽa va le ƒuƒlu vie, wòsẽ, eye wòsena le eɖokui me be yeto vovo ne woka asi eŋua? Ne ède dzesi nane si le abe ema ene la, ele be nàtsi dzi vie. Elabena, esia ate ŋu anye nɔnɔme aɖe si woyɔna be Juvenile Systemic Scleroderma , si ŋu míele nu ƒom tsoe egbea ƒe dzesi ɣeaɖewoɣi. Mègatsi dzi o, míaƒo nu tso esia ŋu tsitotsito.

Nukae Nye Ðeviwo ƒe Dɔwɔnawo ƒe Dɔmawɔmawɔ nyuie?

Kpuie ko la, Juvenile Systemic Scleroderma (si wogayɔna be Systemic Sclerosis ) nye nɔnɔme si me viwò ƒe ŋutigbalẽ va nɔa kpekpem eye wòsẽna wu alesi wòle dzɔdzɔmee. Bu eŋu be enye rababa gbadzɛ aɖe si va nɔa ƒoƒom vivivi eye wòzua abe aŋe sesẽ ene. Menye ŋutigbalẽa ɖeɖeko ŋue wòku ɖo o. Ɣeaɖewoɣi la, ate ŋu agblẽ nu le ŋutinu bubu siwo le ɖevia ƒe ŋutilã me hã ŋu. Nya ‘ɖoɖowɔɖi’ fia be ate ŋu akpɔ ŋusẽ ɖe ɖevia ƒe ŋutilã bliboa dzi.

Le nyateƒe me la, esia nye dɔléle si dɔlélenutsiŋutete ŋutɔ hena vɛ . Eyae nye be míaƒe ŋutilã ƒe ametakpɔnu, si nye dɔlélenutsiŋutete, dzea eya ŋutɔ ƒe lãmenugbagbevi siwo le lãmesẽ me dzi dzedze gɔme vodadatɔe. Le Scleroderma ƒe nɔnɔme sia me la, ne dɔlélenutsiŋutete dze ŋutigbalẽ ƒe lãmenugbagbeviwo dzi alea la, ŋutigbalẽa ƒe dɔdzẽ alo vuvu dzɔna. Le vuvu sia ta la, protein si woyɔna be collagen, si naa míaƒe ŋutigbalẽ te ŋu nɔa te sesĩe eye wòsẽa ŋu la, dzea wɔwɔ gɔme wògbɔa eme. Abe alesi abi dzɔna ne abi aɖe xɔ ame ene la, collagen ƒe wɔwɔ fũ sia nana ŋutigbalẽa me fibrosis alo wòsesẽna abe abi ene.

Ðe Systemic Scleroderma ƒomevi vevi aɖewo lia?

Ẽ, ƒomevi vevi etɔ̃e li. Na míakpɔ nusiwo wonye ɖa.

1. Diffuse cutaneous systemic sclerosis: Le ƒomevi sia me la, woate ŋu akpɔ ɖevia ƒe ŋutigbalẽ ƒe ʋuʋu le ŋutilã bliboa me. Azɔ hã, kuxiwo ate ŋu anɔ ŋutilãa ƒe ŋutinuwo ƒe dɔwɔwɔ ŋu. Bu eŋu kpɔ, menye abɔwo, afɔwo, kple mo ɖeɖeko o, ke teƒewo abe akɔta kple dɔgbo ene hã dzea ƒoƒo gɔme.

2. Limited cutaneous systemic sclerosis (CREST syndrome): Esia nye etɔxɛ vie. Wogayɔnae be CREST ƒe dɔléle . CREST nye kpukpui si wowɔ to nɔnɔme sia ƒe akpa vevi atɔ̃awo ƒe ŋɔŋlɔdzesi gbãtɔwo ƒoƒo ƒu me.

• C - Calcinosis: Esia fia be calcium ƒoa ƒu ɖe ŋutigbalẽa te eye wòwɔa ƒunukpeƒe suesuesuewo.
• R - Raynaud ƒe nudzɔdzɔ: Esia nye esime asibidɛwo (asi kple afɔwo) trɔna zua ɣie, blɔ, eye emegbe wozua dzĩ ne vuvɔ le wo ŋu alo ne wole nuteɖeamedzi me. Eva sesẽna be woaɖɔ ŋutilã ƒe dzoxɔxɔ ɖo.
• E - Nuɖuɖutome ƒe ʋuʋu ƒe dɔmawɔmawɔ nyuie: Esia fia be mɔ̃ si tsɔa nuɖuɖu tso ŋɔti me yia dɔgbo me (nutome) mele dɔ wɔm nyuie ne míemi o. Esia ate ŋu ana dzi nagbã.Nu mawo tɔgbe ate ŋu adzɔ.
• S - Sclerodactyly: Asibidɛwo ƒe ŋutigbalẽ ƒe ƒoƒo kple sesẽ. Asibidɛawo ate ŋu avuvu eye woasẽ abe soseti ene.
• T - Telangiectasia: Ʋuka sue siwo le ŋutigbalẽa me la lolona, ​​wodzena abe akpɔkplɔ ƒe lãgbalẽ alo teƒe dzĩwo ene.

3. Systemic sclerosis sine scleroderma: Esia nyea ɣeyiɣi si me ŋutilãa ƒe ŋutinu ememetɔwo gblẽa nu le ŋutigbalẽa ƒe ƒoƒo alo sesẽ aɖeke manɔmee. ‘Sine scleroderma’ gɔmee nye ‘scleroderma (ŋutilã ƒe sesẽ) manɔmee’. Esia fia be togbɔ be tɔtrɔ ɖedzesi aɖeke manɔ ŋutigbalẽa ŋu o hã la, ate ŋu agblẽ nu le ŋutinu siwo le ememe ŋu.

Amekae ate ŋu axɔ Juvenile Systemic Scleroderma wu? Aleke gbegbe wòbɔe?

Nɔnɔme sia si woyɔna be Juvenile Systemic Scleroderma ate ŋu adze amesiame si xɔ ƒe ɖesiaɖe dzi ŋutɔŋutɔ, eɖanye ŋutsu alo nyɔnue wònye o. Gake ƒã ŋutɔ be ɖevi suewo, si fia ɖevi siwo mexɔ ƒe 10 haɖe o, naxɔe. Nya ‘ɖevi’ ŋutɔ fia be esia nye nɔnɔme si gblẽa nu le ɖeviwo ŋu. Ne èlé ŋku ɖe akɔntabubu siwo le dukɔ abe United States ene me ŋu la, wogblɔna be ɖevi siwo ŋu Scleroderma le la ade 5,000 va ɖo 7,000. Ame siwo katã ŋu Scleroderma le ƒe 2% lɔƒoe dɔléle sia dzea wo dzi hafi xɔa ƒe 10. 7% bubuwo dzea ŋgɔ nɔnɔme sia le ƒe 10 va ɖo 19. Eyata wobua esia be enye dɔléle si mebɔ kura o .

Nukae nye Juvenile Systemic Scleroderma ƒe dzesiwo?

Le nɔnɔme sia me la, dzesiwo ate ŋu agblẽ nu le ɖevia ƒe ŋutigbalẽ kple eƒe ŋutinuwo ŋu. Tsɔ kpe ɖe eŋu la, ɖevi geɖe siwo ŋu Systemic Scleroderma le hã toa nɔnɔme aɖe si woyɔna be Raynaud ƒe nudzɔdzɔ .

Dzesi siwo gblẽa nu le ŋutigbalẽ kple lãkusiwo ŋu

Gbã la, mina míalé ŋku ɖe alesi esia kpɔa ŋusẽ ɖe ŋutigbalẽa kple lãmenugbagbevi siwo do ƒome kplii dzii ŋu:

• Ŋutilãa megate ŋu nɔa te ɖe enu o. Eva zua nusi me kɔ, si me kɔ, eye wòdzea ame ŋu.
• Asiwo ƒe dɔwɔwɔ dzi ɖena kpɔtɔna. Ŋutilãa va sẽna, vevietɔ le asibidɛwo kple asibidɛwo me, si wɔnɛ be esesẽna be woabɔbɔ asiwo ahalé nuwo.
• Ʋuka dzĩwo dzena le ŋutigbalẽa ŋu, vevietɔ le asiwo, mo, kple ɖa siwo ƒo xlã ɖa (telangiectasias). Esiawo ate ŋu adze abe akpɔkplɔ suewo ene.
• Calcinosis nye calcium ƒe ƒuƒoƒo suesuesue siwo le ŋutigbalẽa te alo teƒe bubuwo ƒe wɔwɔ. Esiawo ate ŋu asesẽ ɣeaɖewoɣi.

Gbã la, asiwo kple afɔwo ƒe ŋutigbalẽ ate ŋu adze abe ɖe vuvu eye wòlolo ene. Le ɣeyiɣi aɖe megbe la, ɖevia ƒe ŋutigbalẽ ate ŋu asẽ, aƒo, eye ate ŋu aƒo ƒu, teƒe siwo nyrɔ, alo do suesuesuewo. Le kpɔɖeŋu me, ɖevi aɖewo ƒe asibidɛwo ate ŋu avuvu abe soseti ene, emegbe woasesẽ ahanɔ keklẽm.

Dzesi siwo gblẽa nu le ŋutinu siwo le ememe ŋu

Systemic Scleroderma ate ŋu agblẽ nu le ɖevi ƒe ŋutinu ememetɔwo hã ŋu. Dzesiawo ate ŋu anye:

• Ƒunukpeƒewo ƒe vuvu, sesẽ, kple vevesese. Abe ƒunukpeƒetetedɔ ene.
• Abi siwo le asibidɛwo ƒe nugbɔ. Abi siawo xɔa ɣeyiɣi didi hafi wohayana.
• Nuɖuɖumeŋusẽ ƒe kuxiwo. Le kpɔɖeŋu me, dzimeve, nu mimi sesẽ, aɖuɖɔ si me mekɔ o (aɖuɖɔtoe), kple dɔgbo ƒe ʋuʋu.
• Yagbɔgbɔ ƒe kuxiwo. Àte ŋu akpɔ kɔdzi atraɖii alo gbɔgbɔ sesẽ na wò.
• Ayiku me kuxiwo. Esia ate ŋu ahe ʋusɔgbɔdɔ (ʋusɔgbɔdɔ) hã vɛ .
• Ðeɖiteameŋu ƒe seselelãme ɣesiaɣi. Ðeɖiteameŋu kabakaba le nu sue aɖe wɔwɔ vɔ megbe gɔ̃ hã.
• Lãmetsiwo ƒe gbɔdzɔgbɔdzɔ.

Zi geɖe la, nɔnɔme sia mevea ame o. Eyata ɖewohĩ ɖevi aɖewo menya gɔ̃ hã be Scleroderma le yewo ŋu o. Esia tae wòle be ɖevi si ŋu wokpɔ be Systemic Sclerosis le la nayi ɖɔkta gbɔ edziedzi be wòalé ŋku ɖe ʋusɔgbɔdɔ, lãkusi, ayiku, dɔgbo, kple dzitodzito me kuxiwo ŋu.

Raynaud ƒe nudzɔdzɔa

Esia nye dzesi si le etɔxɛ vie. Raynaud ƒe nudzɔdzɔe nye ne ɖevi ƒe asibidɛwo kple afɔbidɛwo ƒe amadede trɔ ne vuvɔ le eŋu alo ne nu te ɖe edzi. Gbã la , wozua ɣie , emegbe wozua blɔ , eye mlɔeba wozua dzĩ . Esia nye dzesi si woate ŋu akpɔ le dɔlélea ƒe gɔmedzedze. Ɣeaɖewoɣi la, esia ate ŋu anye nu gbãtɔ si afia be Systemic Sclerosis le ame ŋu.

Dzesi bubu siwo ate ŋu ado mo ɖa le Raynaud ƒe nudzɔdzɔa ŋu dometɔ aɖewoe nye:

• Ðeɖiteameŋu ƒe seselelãme ɣesiaɣi
• Ƒunukpeƒewo ƒe vevesese
• Nuɖuɖu mimi sesẽ
• Dɔgbo ƒe vevesese
• Akɔta ƒe dɔléle
• Dɔmetɔtrɔ
• Yagbɔgbɔ sesẽ

Nukatae Juvenile Systemic Scleroderma dzɔna?

Le nyateƒe me la, womenya nusi tututu gbɔ Juvenile Systemic Scleroderma tsona haɖe o . Gake numekukuwo ɖee fia be nusiwo gblẽ le lãmenugbagbevi siwo le míaƒe ʋukawo ƒe eme ŋu nana lãmenugbagbevi siwo ƒoa ƒu ɖe ŋutigbalẽa me, siwo woyɔna be fibroblasts, wɔa dɔ akpa. Fibroblast siawoe nye lãmenugbagbevi siwo wɔa proteinwo abe collagen ene. Eyata, Systemic Scleroderma ƒe dzesiwo tso collagen ƒe dzidziɖedzi fũu akpa sia gbɔ.

Nukatae vidzĩ ƒe ŋutigbalẽ xaxa alea gbegbe ɖo?

Le Systemic Scleroderma me la, ŋutigbalẽa tsina le protein si woyɔna be collagen si sɔ gbɔ ɖe ɖevia ƒe lãkusiwo me ta. Abe alesi míedzro eme va yi ene la, dɔlélenutsiŋutete ƒe dɔe nye be wòakpɔ ŋutilã ta tso dɔlékuiwo kple dɔlélewo me. Gake le ɖevi si ŋu Scleroderma le gome la, dɔlélenutsiŋutete wɔa nu wògbɔa eme eye wòdzea agbagba be yeatsɔ ye ŋutɔ yeƒe lãmenugbagbevi siwo le lãmesẽ me akpɔ ŋutilãa ta – si fia be edzea eya ŋutɔ ƒe lãmenugbagbeviwo dzi . Esia wɔnɛ be ɖevia ƒe lãmenugbagbeviwo tea collagen wɔwɔ fũ akpa. Collagen sia si sɔ gbɔ la gena ɖe ɖevia ƒe ŋutigbalẽ kple eƒe ŋutinuwo me, si wɔnɛ be wòdzena abe ɖe wòsesẽna eye wòtsia ene, abe abi ene.

Aleke wowɔna dea dzesi Systemic Scleroderma?

Viwò ƒe ɖɔkta akpɔ Systemic Scleroderma to nu geɖe ŋu bubu me.

• Dzesiwo kple ŋutilã me dzesiwo, abe ŋutigbalẽ ƒe ƒoƒo kple asibidɛwo ƒe tɔtrɔ ene.
• Tɔtrɔ tɔxɛ siwo vaa ŋutigbalẽa me, abe teƒe siwo le ɣie, woƒe lolome, woƒe nɔnɔme, kple amadede ene.
• Atikewɔwɔ ŋutinya blibo kple ŋutilãmedodokpɔ ana nyatakaka tso ɖevia ƒe dɔléle siwo wòxɔ va yi kple nenye be nɔnɔme mawo tɔgbe nɔ ƒomea me dometɔ aɖe ŋu.

Dodokpɔ kawoe wozãna tsɔ dea dzesi Systemic Scleroderma?

Wowɔa dodokpɔ vovovowo tsɔ ɖea nɔnɔme bubu siwo ɖi ŋutigbalẽa ɖa, be woanya alesi gbegbe lãkusia wɔa dɔe, eye woakpɔe ɖa be ŋutinu bubu siwo kpe ɖe ŋutigbalẽa ŋu hã gblẽa nu le wo ŋu hã. Dodokpɔ siwo wowɔ be woakpɔ protein siwo dɔlékuiwutikewo le ate ŋu ana míanya alesi dɔlélea le edzi yim vie. Ƒã ŋutɔ hafi ɖɔktawo wɔa ŋutigbalẽ ƒe lãmenugbagbeviwo ƒe dɔwɔwɔ .

Dodokpɔ bubu aɖewo siwo woawɔ le Systemic Scleroderma ŋue nye esi:

• Ʋudodokpɔ: Dzidze protein ƒe agbɔsɔsɔ si tso dɔlélenutsiŋutete gbɔ kple ayiku ƒe dɔwɔwɔ.
• X-ray dodokpɔwo: Di tɔtrɔ le ɖevia ƒe ŋutigbalẽ, ƒuwo, kple ŋutinuwo (abe lãkusi kple dɔgbo ene) ŋu.
• Dodokpɔ siwo wowɔna tsɔ léa ŋku ɖe nu mimi ƒe ɖoɖo si le nuɖuɖutome ŋu: Esia fia be woalé ŋku ɖe mɔ̃ si tsɔa nuɖuɖu tso nu me yia dɔgboa me ƒe dɔwɔwɔ ŋu.
• Aklã ƒe dɔwɔwɔ dodokpɔ: Yagbɔgbɔ dodokpɔ be woakpɔe ɖa be ɖevia ƒe lãkusiwo le dɔ wɔm nyuie hã.
• Dzi ƒe ultrasound (Echocardiography): Kpɔ alesi viwòa ƒe dzi le dɔ wɔm ɖa.

Amekae dea dzesi Juvenile Systemic Scleroderma?

Viwòa ƒe atikewɔla, lãmekaŋutinunyala si bi ɖe nɔnɔme siawo me, ŋutigbalẽŋutinunyala , alo ɖɔkta siwo bi ɖe ŋutilã ƒe akpa aɖewo koŋ (nuɖuɖumeŋusẽ, dzi, lãkusi, ayiku) ye dea dzesi Systemic Scleroderma, léa ŋku ɖe eŋu, eye wòdaae.

Aleke wodaa Juvenile Systemic Scleroderma ƒe dɔléleae?

Taɖodzinu vevi siwo le ɖoɖowɔɖi ƒe scleroderma dada ŋue nye be woatɔ te dɔdzẽ, axe mɔ na nɔnɔmea be wòagagblẽ ɖe edzi o, eye woaxe mɔ ɖe nusiwo gblẽ le ŋutinuwo ƒe ememe ŋu nu.

Ŋutilã takpɔkpɔ

Wò ŋutigbalẽ takpɔkpɔ kpena ɖe ŋuwò be ʋu nayi wò ŋutigbalẽ kple abɔwo kple afɔwo me geɖe wu. Esia le vevie ŋutɔ na ɖevi siwo ŋu Raynaud ƒe nudzɔdzɔa le . Nu aɖewo siwo nàte ŋu awɔ atsɔ akpɔ viwò ƒe ŋutigbalẽ tae nye esi:

• Ƒo asa na nuvevi wɔwɔ teƒe siwo dɔlélea le, vevietɔ asibidɛwo kple afɔbidɛwo.Aɖatsi sue aɖe gɔ̃ hã ate ŋu ava zu kuxi gã aɖe.
• Ta viwòa ƒe asiwo kple afɔwo ta tso vuvɔ me. Na xɔa me naxɔ dzo. Le dzomeŋɔli (le teƒe siwo vuvɔ le abe míaƒe dukɔa ƒe togbɛwo ene) la, do awu bubu siwo woatsɔ akpe ɖe viwòa ŋu, abe kposɔ si ŋu tomeka le, asigɛ, kple sox siwo me dzo le ene. Alẽfu xɔa dzo wu kotoku alo avɔ siwo wotsɔ lãfu wɔe. Azɔ hã, anyo wu be woado awu tsɛ geɖe tsɔ wu be woado awu ʋlaya ɣi ɖeka.
• Ƒo asa na atamanono alo viwòa ƒe atamanono.
• Ƒo asa na dzamezãtike siwo me nusi nye pseudoephedrine le nana viwò.
• Ta viwòa ta tso ɣe ƒe keklẽ si gbɔ eme me. Zã ɣe ƒe keklẽŋusẽtikewo abe alesi wò ɖɔkta kafui ene.
• Mègazã adzalẽ sesẽwo, atike siwo wotsɔna klɔa viwòa (atike siwo wotsɔna klɔa ŋutilã alo mo, atike siwo wotsɔna klɔa nu sesẽwo) ɖe viwòa ƒe ŋutigbalẽ ŋu o.
• Zã atikekuiwo be viwòa ƒe ŋutigbalẽ nanɔ blɔ abe alesi ɖɔkta gblɔe ene.

Lãmesẽfefewɔwɔ

Kamedede ƒe ɖoɖo vevi siwo wowɔna tsɔ kekea lãmekawo eye wofiaa mɔe, siwo kamededeŋutinunyalawo kple dɔdamɔnufialawo wɔna la ate ŋu akpe ɖe ɖevia ŋu wòate ŋu atrɔ ɖe nɔnɔmewo ŋu, wòate ŋu aʋuʋu le ƒunukpeƒewo, eƒe lãmekawo ƒe ŋusẽ, kple ʋu ƒe sisi yi teƒe siwo dɔlélea le. Dɔdamɔnu siawo ate ŋu akpe ɖe ame ŋu hã be woaxe mɔ ɖe ƒunukpeƒewo ƒe ʋuʋu nu, si nye ƒunukpeƒewo ƒe sesẽ. Ne ehiã la, ɖɔkta ate ŋu aɖo aɖaŋu be woatsɔ aŋe alo akɔtaɖonu ablae.

Amekoko

Ƒã ŋutɔ la, ahiã be woawɔ dɔ na ame le ƒumeŋuɖui me alo awɔ atsyɔ̃ɖoɖo na ame be woatsɔ aɖɔ ƒunukpeƒe alo ŋutigbalẽ ƒe gbagbã sesẽwo alo abi siwo le wo ŋu ɖo. Gake hafi woawɔ dɔ nɛ la, ele be nɔnɔmea naɖe le ɖiɖi me , si fia be megale dɔ wɔm o ƒe geɖee nye sia.

Viwò ƒe ɖɔkta ate ŋu abu ƒumeŋuɖui dodo na ame ɖokui be enye atikewɔmɔnu. Wole atikewɔwɔ bubuwo me kum fifia.

Atike kawoe wonana na Systemic Scleroderma?

Ðɔkta ate ŋu aŋlɔ atike vovovowo na viwòa atsɔ ada dɔlélea. Le kpɔɖeŋu me:

• Corticosteroids: Eɖea lãmekawo, ƒunukpeƒewo, kple ŋutigbalẽ ƒe abi dzi kpɔtɔna. Steroid ate ŋu akpe ɖe ame ŋu hã be woada dɔdzẽ ƒe gɔmedzedze le ŋutinuwo me. Gake zi geɖe la, steroids mewɔa dɔ boo aɖeke le fibrotic ƒe akpa siwo va emegbe le systemic sclerosis me o.
• Atike siwo me steroid mele o siwo tsia dzodzodzoetsitsi nu (NSAIDs): Le kpɔɖeŋu me , ibuprofen kple naproxenWozãa atikewo abe NSAID ene ɣeaɖewoɣi tsɔ ɖea ƒunukpeƒetetedɔ dzi kpɔtɔna le ɖevi siwo ŋu ƒunukpeƒetetedɔ le me. Gake ele be woakpɔ nyuie be woagazã NSAID-tikewo fũu akpa ne ayiku ƒe dɔwɔwɔ me gblẽ o.
• Atike bubu siwo trɔa dɔlélenutsiŋutete: Wona esiawo be woatsɔ aɖe dɔlélenutsiŋutete ƒe dɔwɔwɔ dzi akpɔtɔ eye woaxe mɔ ɖe dɔdzẽ kple abi siwo kplɔe ɖo nu.
• Atike siwo kekea ʋukawo ɖe enu eye ʋu ƒe sisi nyuie wu: Wozãa esiawo tsɔ daa Raynaud ƒe nudzɔdzɔa .

Ne Systemic Scleroderma le vinye ŋu la, nukae wòle be makpɔ mɔ na?

Atike aɖeke koŋ meli na scleroderma o. Ke hã, àte ŋu akpe ɖe viwòa ŋu wòakpɔ nɔnɔmea gbɔ ahanɔ agbe ɖe enu.

Systemic Scleroderma nye dɔléle si nɔa anyi didi , si nɔa anyi didi, eye wòyia edzi vivivi. Ate ŋu anɔ anyi ɣleti alo ƒe geɖe. Viwòa ƒe nukpɔsusu nɔ te ɖe alesi dzesiawo kakae kple alesi gbegbe wògblẽa nu le ŋutilãa ƒe akpa aɖe (vevietɔ ŋutigbalẽ kple ŋutinu ememetɔwo) dzi.

Ðevi siwo ŋu lãkusi, dzi, alo ayiku me kuxiwo le la ate ŋu axɔ kuxiwo, abe ƒunukpeƒewo ƒe ƒoƒo kple atsyɔ̃ɖoɖo ƒe tɔtrɔ ene. Nɔnɔme sia ate ŋu akpɔ ŋusẽ ɖe ɖevia ƒe ƒu ƒe tsitsi hã dzi.

Zi geɖe la, Systemic Scleroderma medzona keŋkeŋ o, gake ate ŋu anɔ nenema ke ƒe geɖe evɔ magagblẽ ɖe edzi o.

Ɣeyiɣi didi kae nàte ŋu anɔ agbe kple Juvenile Systemic Scleroderma?

Ðevi si ŋu wokpɔ be Systemic Scleroderma le ƒe agbenɔƒe toa vovo le alesi dɔlélea nu sẽe nu, vevietɔ ne ekpɔ ŋusẽ ɖe woƒe ŋutinuwo dzi. Ele vevie be nàƒo nu tso esia ŋu kple wò ɖɔkta be nàse egɔme nyuie.

Ðe woate ŋu axe mɔ ɖe Ðeviwo ƒe Systemic Scleroderma nua?

Esi womenya nusi tututu gbɔ wòtso o ta la, mɔ aɖeke meli si dzi woato axe mɔ ɖe Systemic Scleroderma nu o.

Aleke malé be na vinye si wokpɔ be exɔ Systemic Scleroderma?

Ele be ɖevi siwo ŋu Systemic Scleroderma le nanɔ agbe si sɔ alesi woate ŋui. Ele be woayi suku, afe fefe, eye woakpɔ gome le dɔwɔnawo me. Le goawo katã me la, seɖoƒe meli na kamedede agbɔsɔsɔme si ɖeviwo ate ŋu awɔ o (zi alesi wòle dedie ko). Kamedede kpena ɖe ame ŋu be wòaxe mɔ ɖe gbɔdzɔgbɔdzɔ nu eye wònaa lãmekawo ƒe ŋusẽ, te ŋu trɔna ɖe nɔnɔmewo ŋu, kple dzidodo dzina ɖe edzi.

Ɣekaɣie wòle be makplɔ vinyea ayi ɖɔkta gbɔ?

Ele be woakplɔ viwòa ayi aɖadoe kpɔ edziedzi. Vevietɔ lé ŋku ɖe dzesi siwo gblẽa nu le ame ƒe ŋutinuwo ŋu. Ne viwòa le veve sem vevie , esesẽna nɛ be wòaʋuʋu eƒe ŋutilã ƒe akpa aɖewo, alo dzesi siwo le ŋusẽ kpɔm ɖe eƒe gbesiagbegbenɔnɔ dzi la, .Yi ɖɔkta gbɔ enumake.

Nya kawoe wòle be mabia nye ɖɔkta?

Nyabiase siawo tɔgbe biabia akpe ɖe ŋuwò:

• Aleke gbegbee vinye ƒe nɔnɔmea nu sẽe?
• Aleke mate ŋu akpe asi ɖe vinye ƒe ŋutigbalẽ takpɔkpɔ ŋu le aƒeme?
• Zi nenie wòle be vinye nayi kamedede gbɔ?
• Dzesi kawoe wòle be malé ŋku ɖo ne dɔlélea gagblẽ ɖe edzi?
• Ðe wòhiã be woawɔ dɔ na vinyea?

Ðe scleroderma ƒomevi bubuwo lia?

Tsɔ kpe ɖe Systemic Scleroderma ƒomeviwo ŋu la, Scleroderma ƒomevi vevi eve hã li. Woawoe nye:

• Localized scleroderma: Ŋutilã si le ŋutilã ƒe akpa aɖewo koe ƒomevi sia gblẽa nu le eŋu. Ate ŋu akaka ɖe lãmeka alo ƒu siwo le ete hã me, alo manɔ anyi o. Ƒã hafi wògblẽa nu le ŋutinu siwo le ememe ŋu.
• Systemic scleroderma (si woyɔna hã be systemic sclerosis): Esiae nye nusi ŋu míeƒo nu tsoe le nyati sia katã me. Le nɔnɔme sia me la, ŋutigbalẽa ate ŋu aƒo ɖe ŋutilãa ƒe akpa sia akpa. Tsɔ kpe ɖe ŋutigbalẽ ƒe tɔtrɔ ŋu la, abi ƒe lãkusi ate ŋu ado ɖe ŋutinu ememetɔwo abe ayiku, dzi, lãkusi, kple dɔgbo ƒe dɔwɔwɔ ene me. Ðevi siwo ŋu systemic sclerosis le ate ŋu anye be ƒunukpeƒewo ƒe ʋuʋu seɖoƒe li na le ŋutigbalẽ ƒe tɔtrɔ siwo bɔ ta.

Nu vevitɔ kekeake siwo dzi wòle be nàɖo ŋkui le nyati sia me

Juvenile Systemic Scleroderma nye dɔléle si mebɔ o le ɖeviwo me si nana ŋutigbalẽa ƒoa ke eye wòsesẽna, eye ɣeaɖewoɣi la, egblẽa nu le ŋutinu ememetɔwo ŋu. Enye dɔléle si dɔlélenutsiŋutete ŋutɔ hena vɛ.

• Dzesiwo: Ŋutilã ƒe tete, asibidɛwo ƒe vuvu, Raynaud ƒe nudzɔdzɔ (asibidɛwo ƒe amadede trɔna le vuvɔŋɔli), ƒunukpeƒewo ƒe vevesese, nuɖuɖumeŋusẽ ƒe kuxiwo, kple gbɔgbɔ sesẽ ate ŋu ado mo ɖa.
• Nusi gbɔ wòtso: Togbɔ be womenya tututu o hã la, wosusu be dɔlélenutsiŋutete ƒe dɔmawɔmawɔ nyuie kple collagen ƒe wɔwɔ fũ gbɔe wòtso.
• Atikewɔwɔ: Aɖu dɔlélea dzi, akpɔ ŋutigbalẽa ta, zã kamedede kple ne ehiã la, zã atikewo. Togbɔ be womate ŋu adae bliboe o hã la, woate ŋu akpɔ dzesiawo gbɔ.
• Vevietɔ wu: Ne dzesiwo le viwòa ŋu la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake. Ele vevie ŋutɔ be nàɖo viwòa ɖe atikewɔƒe edziedzi eye nàkpe ɖe eŋu wòanɔ agbe si sɔ. Mègatsi dzi o, àte ŋu anɔ te ɖe nɔnɔme sia nu to ɖɔktawo ƒe kpekpeɖeŋu me.

` Scleroderma, ɖeviwo ƒe ŋutigbalẽdɔlélewo, ŋutigbalẽ ƒe tete, collagen, autoimmune dɔlélewo, Raynaud ƒe nudzɔdzɔ, CREST syndrome