Ðe taɖuame atraɖii, ŋkuʋuʋu sesẽ na wò, alo wò dadasɔ zi ɖeka esime nèle zɔzɔm kpɔa? Ðewohĩ ède dzesi dzesi siawo le viwòa ŋu kpɔ. Togbɔ be míeŋea aɖaba ƒua nya mawo dzi zi geɖe hã la, woate ŋu anye lãmesẽkuxi sesẽ aɖe ƒe dzesiwo ɣeaɖewoɣi. Egbea, le Nirogi Lanka , míele nu ƒom tso ahɔhɔ̃meka aɖe si mebɔ kura o gake wòle vevie be woase egɔme si woyɔna be Pineoblastoma ŋu .
Nuka tututue nye Pineoblastoma? Kpuie ko la...
Ne míagblɔe bɔbɔe la, Pineoblastoma nye dɔdzẽ vɔ̃ɖi (kansa) si dzɔna tso wò ahɔhɔ̃ ƒe pineal gland me. Dɔdzẽ sia ƒomevi wɔa adã ŋutɔ ; etsina kabakaba eye ate ŋu akaka ɖe ahɔhɔ̃meka siwo ƒo xlã wò kple tsi si le tsatsam le wò ahɔhɔ̃a ŋu me, si ana wòanye nusi ŋu nàtsi dzi ɖo vevie le atikewɔwɔ me.
Lala, nukae nye Pineal Gland?
Mina míadze egɔme tso gɔmedzenuawo dzi. Pineal gland nye ŋutinu sue aɖe si le abe kɔnu ene, si lolo abe pine-ku ene, si le wò ahɔhɔ̃ ƒe titina goglo. Lãmenugbagbevi siae naa lãmetsi aɖe si woyɔna be melatonin dona . Ðewohĩ èse melatonin ŋkɔ kpɔ—ele vevie ŋutɔ be nàɖɔ wò ɣeyiɣi ƒe didime ƒe zɔzɔme ɖo . Bu eŋu be enye wò ŋutilã ƒe dzɔdzɔme gaƒoɖokui ememetɔ si kpena ɖe ŋuwò nènɔa ŋudzɔ le ŋkeke me eye wòʋãa wò be nàdɔ alɔ̃ le zã me.
Dɔdzẽ ka ƒomevie nye Pineoblastoma?
Pineoblastoma nye ahɔhɔ̃ me dɔdzẽ si le dzidzim ɖe edzi kabakaba . Zi geɖe la ɖɔktawo bua eŋu be enye ahɔhɔ̃ me dɔdzẽ si le tagbɔ me ƒe Dzeside 4 . Esi wònye dɔdzẽ vɔ̃ɖi aɖe ta la, egblẽa nu le ŋutilã ŋu eye ate ŋu akaka.
Aleke gbegbee Pineoblastoma bɔe?
Pineoblastoma mebɔ kura o . Nyatakaka siwo woxɔ le United States ɖee fia be ahɔhɔ̃mekawo ƒe dɔdzẽwo katã ƒe 0.2% mede 0.2% o be wonye pineal gland tumors. Togbɔ be ɖevi suewo alo sɔhɛ tsitsi siwo mexɔ ƒe 20 haɖe o ŋue wokpɔa kansa sia ƒomevi wu hã la , ele vevie be míaɖo ŋku edzi be ate ŋu adzɔ le ƒe ɖesiaɖe me.
Nukae nye Pineoblastoma ƒe dzesiwo?
Mina míalé ŋku ɖe dzesi siwo ate ŋu adze le nɔnɔme sia me ŋu:
- Taɖuame sesẽ : Esiawo menye wò taɖuame si bɔ o; zi geɖe la, woƒe nu sẽna eye wonɔa anyi ɖaa.
- Ðeɖiteameŋu ɣesiaɣi : Ðeɖiteameŋu ƒe seselelãme si nu sẽ ale gbegbe be gbesiagbedɔwo va sesẽna ( Ðeɖiteameŋu ).
- Ŋku ʋuʋu sesẽ : Ðewohĩ asesẽ na wò be nàlé ŋku ɖe wò ŋkuwo ŋu alo akpɔ mɔ aɖewo.
- Kuxi siwo le dadasɔ kple nuwɔwɔ aduadu me : Sese le ɖokuiwò me be yemeli ke o ne èle zɔzɔm alo nuwo léle sesẽ.
- Nuwɔna ƒe tɔtrɔ : Nɔnɔme ƒe tɔtrɔ siwo dzena, abe dzikudodo, dzitsitsi, alo asiɖeɖe le eŋu kpata ene.
- Aɖuɖɔtoe kple ʋuʋudedi .
Zi geɖe la, nɔnɔme aɖe si woyɔna be hydrocephalus , afisi ahɔhɔ̃mekawo me tsi ƒoa ƒu ɖo eye wònaa nyaƒoɖeamenu dzina ɖe edzi le ahɔhɔ̃a me gbɔe dzesi siawo tsona. Togbɔ be dɔdzẽa ate ŋu ato tsi sia me ayi Central Nervous System (CNS) ƒe akpa bubuwo hã la, ƒã hafi wòkakana ɖe CNS godo.
Kpɔe ɖa le susu me be ɖevi aɖe toa nyatoƒoe le taɖuame enuenu ŋu, megadina be yeafe fefe o, eye wòdzena abe ɖe wòdoa dziku le mɔ si mebɔ o nu ene. Dzilawo ate ŋu agbe esia be enye nuwɔna si sɔ. Gake ne dzesiawo gakpɔtɔ li la, ele vevie ŋutɔ be nàkpɔ ɖɔkta enumake.
Nukae hea Pineoblastoma vɛ?
Nusi koŋ gbɔ wòtsoe nye lãmenugbagbevi tɔxɛ siwo le pineal gland si woyɔna be pinealocytes me ƒe tsitsi kabakaba si dzi womeɖu o . Numekukuwo ɖee fia be domenyiŋusẽfianu ƒe tɔtrɔ nana lãmenugbagbevi siawo mewɔa dɔ nyuie o eye wotsina le mɔ si mesɔ o nu.
Domenyiŋusẽfianu ƒe tɔtrɔ siawo ate ŋu adzɔ le mɔ eve nu:
1. Domenyinu (dɔlékui ƒe tɔtrɔ) : Etso dzilawo gbɔ na ɖevia le fufɔɣi.
2. Dzɔdzɔmenugbagbevi siwo dzɔna ɣeaɖewoɣi : Tɔtrɔ siwo dzɔna le vome le fufɔfɔ megbe, afisi nɔnɔmea ƒe ƒome ŋutinya aɖeke menɔ do ŋgɔ o.
Amekawoe le afɔku gã me be woaxɔ Pineoblastoma?
Ame aɖewo dzea ŋgɔ afɔku gã aɖe be woaxɔ Pineoblastoma :
- Ne Retinoblastoma , si nye ŋku ƒe ŋkume ƒe kansa le ŋuwò la, ke èle afɔku me wu.
- Ame ɖekaɖeka siwo ƒe domenyiŋusẽfianu ƒe tɔtrɔ le RB1 alo DICER1 me hã le afɔku gã aɖe me be woaxɔ kansa sia . Dzɔdzɔmeŋusẽ ƒe tɔtrɔ siawo ate ŋu anye domenyinyi alo esiwo dzɔna ɣeaɖewoɣi.
Ne èle ɖoɖo wɔm be yeaɖo ƒome anyi eye nètsi dzi ɖe afɔku siawo ŋu la, anyo be nàƒo nu kple lãmesẽdɔwɔla aɖe tso domenyiŋusẽfianu dodokpɔ ŋu .
Aleke wowɔna dea dzesi Pineoblastoma?
Ðɔktawo toa dɔdaƒewo ƒe dodokpɔwo kple dɔlélewo didi ƒe dodokpɔwo ƒokpli dzi dea dzesi Pineoblastoma :
- Lãmesẽdodokpɔ : Wò ɖɔkta ada wò dzesiwo, ƒome ŋutinya kpɔ, eye wòawɔ ahɔhɔ̃mekawo ƒe dodokpɔwo, siwo dometɔ aɖewoe nye ŋkuléle ɖe wò ŋku ƒe dɔwɔwɔ ɖekae ŋu.
- Dɔlélewo didi ƒe mɔnu deŋgɔwo :
- Ahɔhɔ̃ ƒe Magnetic Resonance Imaging ( MRI ) ƒe fotoɖeɖewo .
- Kɔmpiuta dzi Tomography (CT) ƒe fotoɖeɖewo.
- Ɣeaɖewoɣi la, wowɔa Positron Emission Tomography (PET) ƒe fotoɖemɔ̃.
- Biopsy , si me woɖea lãkusi sue aɖe le hena numekuku be woatsɔ aɖo kpe dɔdzẽ ƒe ƒomevi dzi.
- Ʋudodokpɔ kple/alo ahɔhɔ̃meka me tsi dodokpɔ hena dɔdzẽ ƒe dzesi tɔxɛ aɖewo.
Ðe woate ŋu ada Pineoblastomaa?
Esia nye nusi ŋu ame geɖe tsi dzi ɖo. Ne míagblɔe tututu la, fifia la, xexeame katã ƒe atike aɖeke meli na Pineoblastoma . Ke hã, taflatse mègabu mɔkpɔkpɔ o; atikewɔwɔmɔnu vovovowo li. Ne dɔdzẽa mekaka o la, zi geɖe la, amekokoe nyea afɔɖeɖe gbãtɔ.
Esi wònye be Pineoblastoma nye kansa ƒomevi aɖe si nu sẽ ta la, edada sesẽ. Kuxiwo ate ŋu ado mo ɖa, eye ate ŋu akpɔ ŋusẽ ɖe nyagblɔɖi si anɔ anyi ɣeyiɣi didi dzi. Gakpe ɖe eŋu la, ate ŋu adzɔ ɣesiaɣi be kansa la nagadzɔ ake le atikewɔwɔ vɔ megbe.
Nukawoe nye Pineoblastoma ƒe atikewo?
Pineoblastoma ƒe atikewɔwɔ ate ŋu anye esiawo:
- Amekoko : Zi geɖe la, wowɔa amekoko be woaɖe dɔdzẽa ƒe akpa aɖe alo wo katã ɖa. Wò amekola aɖe dɔa kple afɔku siwo do ƒome kplii me tsitotsito.
- Amekoko na Hydrocephalus : Be tsi (ahɔhɔ̃ me tsi) si ƒoa xlã ahɔhɔ̃a dzi naɖe akpɔtɔ la, woate ŋu ade shunt—si nye mɔ̃ sue aɖe—be tsi si sɔ gbɔ ɖe eme la nado eye wòaɖe nyaƒoɖeamenu dzi akpɔtɔ.
- Kekeli ƒe Dɔdamɔnu : Esia nye atikewɔwɔ si bɔ tsɔ kplɔa ame ɖo le amekoko megbe. Kekeli ƒe atikewɔwɔ ate ŋu akpe ɖe ame ŋu wòaɖe dɔdzẽ ƒe lãkusi siwo susɔ la dzi akpɔtɔ alo agblẽ kansa lãmenugbagbeviwo.
- Atikewɔmɔnu : Ne wozãe kpe ɖe amekoko kple keklẽŋusẽ ŋu, eye ate ŋu akpe ɖe ame ŋu be dɔdzẽa naɖiɖi hafi woawɔ dɔ nɛ alo aɖe kansadɔlékui susɔeawo ɖa le ewɔwɔ vɔ megbe.
- High-Dose Chemotherapy and Autologous Stem Cell Transplant : Le dɔdamɔnu sia me la, woƒoa wò ŋutɔ wò lãmenugbagbeviwo nu ƒu hafi xɔa atike si ƒe agbɔsɔsɔme sɔ gbɔ. Emegbe wogatsɔa lãmenugbagbevi siawo dea wò ŋutilã me be wòakpe ɖe wò ŋutilã ŋu wòahaya le atikewɔwɔa megbe.
Ne atikewɔwɔ ŋuti numekukuwo le ŋgɔ yim la, mɔnukpɔkpɔ ate ŋu asu asiwò be nàkpɔ gome le dɔdamɔnu dodokpɔwo me. Esiawo ate ŋu abia be woado atike yeye siwo ŋu woɖo taɖodzinu ɖo alo dɔlélenutsiŋutete ƒe atikewɔwɔwo kpɔ.
Amekae le wò belélenameha me?
Ne wokpɔe be Pineoblastoma le ŋuwò la, wò belélenameha si le Nirogi Lanka ate ŋu anye:
- Ahɔhɔ̃ŋutinunyala aɖe
- Dɔdzẽŋutinunyala aɖe
- Kekeli ƒe Dɔdzẽŋutinunyala aɖe
- Ahɔhɔ̃mekaŋutinunyala aɖe
Ðe atikewɔmɔnu siawo ƒe nugbegblẽ le ame ŋua?
Ẽ, atikewɔwɔ aɖewo, vevietɔ keklẽŋusẽ, ate ŋu ahe nugbegblẽ le ame ŋu vɛ. Esiawo ate ŋu akpɔ ŋusẽ ɖe wò lãmenugbagbeviwo ƒe dɔwɔwɔ dzi, siwo dometɔ aɖewoe nye:
- Tsitsi
- Ŋusẽ ƒe agbɔsɔsɔme
- Vidzidzi ƒe ŋutete
Hafi nàdze atikewɔwɔ gɔme la, ɖo dze tsitotsito kple wò ɖɔkta tso eƒe nugbegblẽ le ame ŋu si ate ŋu ado tso eme ŋu . Woalé ŋku ɖe ŋuwò edziedzi eye woaɖe afɔ siwo hiã atsɔ akpɔ nya ɖesiaɖe si ado mo ɖa gbɔ.
Ðe nàte ŋu atsi agbe le Pineoblastoma mea?
Ẽ, dɔnɔ geɖe tsia agbe le Pineoblastoma me nyateƒe. Ƒe atɔ̃ ƒe agbetsitsi le Pineoblastoma ŋu tso 60% va ɖo 69.5% . Togbɔ be dɔléle sia si wokpɔ ate ŋu atrɔ ame ƒe agbenɔnɔ hã la, atikewɔmɔnu nyui aɖewo li siwo ŋu wotrɔ asi le be woakpe ɖe ŋuwò nànɔ agbe nyuie eye nàdidi wò agbenɔƒe ɖe edzi.
Nukae nye Pineoblastoma ƒe ŋgɔdonya?
Le wò dɔlélea didi vɔ megbe la, wò ɖɔkta adzro wò ŋgɔdonya me. Togbɔ be "atike" ɖeka aɖeke meli o hã la, atikewɔwɔmɔnu geɖe li. Nuwo abe lãmesẽ bliboa, alesi wò ŋutilã wɔa nui ɖe atikewɔwɔ ŋu, kple alesi dɔdzẽa tsinae dzie afia nusi ado tso dɔnɔ aɖe me .
Ne wokpɔ dɔlélea le ŋuwò vɔ la, àwɔ kpekpewo be woakplɔ wò ɖo enuenu ale be wò atikewɔlawo nate ŋu alé ŋku ɖe eƒe nugbegblẽ le ame ŋu ŋu eye woana kpekpeɖeŋu si hiã.
Ðe woate ŋu axe mɔ ɖe Pineoblastoma nua?
Nublanuitɔe la, mɔ aɖeke meli si wonya fifia si dzi woato axe mɔ ɖe Pineoblastoma nu o .
Ɣekaɣie wòle be nàkpɔ ɖɔkta?
Ne wò alo viwòa kpɔ Pineoblastoma ƒe dzesiwo, abe:
- Taɖuame si nɔa anyi ɖaa
- Nuwɔna ƒe tɔtrɔ
- Ŋku ƒe ʋuʋu sesẽ
Taflatse yi ɖɔkta gbɔ enumake.
Ne èle atike wɔm na wò fifia eye nèkpɔ nugbegblẽ yeyewo la, ke na wò dɔnɔdzikpɔlawo nanya. Ne ètsi dzi ɖe viwòa ƒe tsitsi alo tsitsi ŋu le atikewɔwɔ me la, dzro nu siawo me kple wò ɖeviwo ƒe dɔdala alo kansadɔdala.
Nya kawoe wòle be mabia nye ɖɔkta?
Ne èdo go kple wò ɖɔkta la, anyo be nàbia be:
- Atikewɔwɔ kae nèkafu?
- Ðe kansa la kakaa?
- Ðe wòhiã be woawɔ dɔ nam?
- Nukawoe ate ŋu agblẽ le atikewɔwɔ sia ŋu?
- Nukae nye nye nyagblɔɖi?
Nya "kansa" sese ate ŋu agbɔ eme eye wòado vɔvɔ̃ na ame. Enye nusi sɔ kura be nàse le ɖokuiwò me be yeƒe mo wɔ yaa alo atsi dzimaɖi ɖe etsɔme ŋu. Mègase le ɖokuiwò me be yetsi akogo o. Wò atikewɔlawo ƒe ƒuƒoƒo si le Nirogi Lanka le afisia be yewoakpe ɖe ŋuwò nàzɔ mɔ le dɔléle sia didi me eye nàtia atikewɔwɔ ƒe ɖoɖo si sɔ na wò wu. Ðo ŋu ɖe xɔ̃wòwo kple ƒowòmetɔwo ŋu hena kpekpeɖeŋu. Numekuku siwo yi edzi le Pineoblastoma ƒe atike yeyewo ŋu yi edzi le mɔkpɔkpɔ nam.
Gbedasi si Wotsɔ Yi Aƒeme
- Pineoblastoma nye dɔdzẽ si mebɔ o, si tsina kabakaba, si dona le ahɔhɔ̃a ƒe pineal gland me.
- Dzesiwo abe taɖuame, ŋku ƒe kuxiwo, dadasɔ ƒe anyimanɔmanɔ, kple nuwɔna ƒe tɔtrɔ ene ate ŋu ado mo ɖa, zi geɖe la, tsi si nye hydrocephalus (tsi si ƒoa ƒu ɖe ahɔhɔ̃a me) gbɔe wòtsona.
- Zi geɖe la, domenyiŋusẽfianu gbɔe nusi gbɔ wòtsona; ame ɖekaɖeka siwo ŋu Retinoblastoma alo RB1/DICER1 domenyiŋusẽfianu ƒe tɔtrɔ le la le afɔku gã aɖe me.
- Dɔlélea didi bia be woawɔ MRI, CT scan, kple biopsies.
- Togbɔ be dɔdamɔnu siwo wɔa dɔ nyuie abe amekoko, keklẽŋusẽ, kple atikewɔmɔnu ene sesẽ hã la, li.
- Ne ède dzesi dɔlélea ƒe dzesiwo la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake . Mègahe ɖe megbe le nyabiabia me o.
- Nɔ mɔkpɔkpɔ me eye nàsẽ ŋu; menye wò ɖeka koe le mɔzɔzɔ sia me o.
Míele mɔ kpɔm be nyatakaka sia akpe ɖe mía ŋu. Ne nane si ŋu nètsi dzi ɖo ku ɖe wò lãmesẽ ŋu la, taflatse wɔ ɖoɖo be yeakpɔ lãmesẽdɔwɔla aɖe.
