Èse dɔléle si nye `(Sweet Syndrome)` ŋu nya kpɔa? Ðewohĩ ne èse ŋkɔ sia la, àsusu be suklidɔe wònye, gake menye nenemae o. Esia mebɔ kura o, si fia be menye dɔléle si ame geɖe xɔna o. Gake enye vevesese si dzena le ŋutilã, abɔ, afɔ, kple kɔ dzi zi ɖeka, eye asrã kpena ɖe eŋu. Ðe míaƒo nu tso esia ŋu tsitotsitoa? Elabena, togbɔ be mebɔ o hã la, enyo be nànyae.
Nuka tututue nye `(Sweet Syndrome)`?
Kpuie ko la, Sweet Syndrome nye ŋutigbalẽa ƒe dɔdzẽ ƒe dɔléle. Edzea egɔme kpata. Dzesi vevitɔwoe nye asrã sesẽ, ŋutigbalẽ ƒe abi siwo biã, siwo le veve sem, kple ɣeaɖewoɣi la, ʋuʋudedi suesuesuewo. Wokpɔa abi siawo le abɔwo, afɔwo, ame ƒe tame, eye ɣeaɖewoɣi le mo kple kɔ dzi wu. Ðɔktawo yɔe hã be Acute Febrile Neutrophilic Dermatosis. Ðe menye ŋkɔ didi aɖee nye ema oa? Efia "ŋutilãdɔ si tsoa dzoxɔxɔ gbɔ kpata si me lãmenugbagbevi ƒomevi aɖe si woyɔna be neutrophil le." Neutrophils nye ʋumenugbagbevi ɣi ƒomevi aɖe si le míaƒe dɔlélenutsiŋutete me.
Ɣeaɖewoɣi la, `(Sweet Syndrome)` sia ateŋu adzɔ kple dɔléle bubuwo. Le kpɔɖeŋu me, woate ŋu akpɔe le kansa `(Cancer)` nɔnɔmewo, dɔgbo me dɔlékuiwo `(Gastrointestinal Infections)`, alo le fufɔɣi. Wokpɔe hã be atike aɖewo siwo míenona gbɔe nɔnɔme sia ate ŋu atso. Le kpɔɖeŋu me, `(Dɔlékuiwutikewo)` ƒomevi aɖewo, si nye atike siwo wua dɔlékuiwo, (e.g. `(Co-trimoxazole (BactrimTM))`) kple `(NSAIDs)` (Nonsteroidal Anti-inflammatory Drugs) vevesesenutsitikewo (e.g. `(Advil®)`) hã ateŋu ahe esia vɛ.
Nu nyuitɔ kekeakee nye be atike aɖe li na esia. Zi geɖe la, woŋlɔa atike ƒomevi si nye `(Corticosteroid)` (e.g. `(Prednisone)`) na amewo. Atike siawo ɖea dɔdzẽ dzi kpɔtɔna eye wokpɔa dzesiawo dzi. Ne dɔléle aɖe si le ete gbɔe esia tso la, ekema `(Sweet Syndrome)` hã anyo ɖe edzi ne wonya da dɔléle ma ko.
Aleke gbegbee nɔnɔme sia bɔe?
Le nyateƒe me la, Sweet Syndrome nye dɔléle si mebɔ kura o . Ame ʋɛ aɖewo koe wokpɔ dɔlélea le le xexeame katã. Eya ta, mebɔ be woase nu tso eŋu o.
Amekae ate ŋu atu esia ɖo wu?
``Sweet Syndrome`` sia ateŋu adzɔ ɖe amesiame dzi. Gake le nyatakakawo nu la , nɔnɔme sia bɔ ɖe nyɔnu siwo xɔ tso ƒe 30 va ɖo ƒe 50. Gake ema mefia be ŋutsuwo alo ame siwo xɔ ƒe bubuwo mate ŋu axɔe o.
Kuxi bubu kawoe ateŋu ado mo ɖa le `(Sweet Syndrome)` ta?
Le go aɖewo me la, Sweet Syndrome ate ŋu agblẽ nu geɖe wu ŋutigbalẽa ɖeɖeko o, ke ate ŋu agblẽ nu le ŋutinu bubuwo hã ŋu le ŋutilãa me. Le kpɔɖeŋu me, ate ŋu agblẽ nu le lãmekawo kple dɔgbo ƒe dɔwɔwɔ ŋu.
Gake kuxi si bɔ wue nye ŋku ƒe kuxiwo.Esiawo ate ŋu anye ŋku ƒe dɔdzẽ (si biã, vevesese), ŋku ƒe tete ƒe dzidziɖedzi (ŋkudɔ), kple ŋkume ƒe abi. Eyata ele vevie ŋutɔ be amesi ŋu Sweet Syndrome le nalé be na eƒe ŋkuwo.
Nukae nye nusiwo hea `(Sweet Syndrome)` vɛ?
Ne míagblɔe tututu la, womenya nusi tututu gbɔ Sweet Syndrome tsona haɖe o. Gake ɖɔktawo dae ɖe hatsotso vevi etɔ̃ me le alesi wòdzɔnae nu:
1. Klasik atsyã
Nusi dzɔna le nɔnɔme sia me enye be ``Sweet Syndrome'' dzena le ɣeyiɣi ɖeka me kple atikewɔwɔ ƒe nɔnɔme bubu.
- Le kpɔɖeŋu me, ate ŋu ava kple gbɔgbɔtsixe ƒe akpa si le etame ƒe dɔlékuiwo abe ŋɔti me dɔlékuiwo kple lãkusi me dɔlékuiwo ene. Tsɔe be dzamezã sesẽ aɖe le ŋuwò, asrã le ŋuwò, eye kasia ŋutigbalẽ me ʋuʋudedi mawo va dze dziwò. Ate ŋu anye nane si le abe ema ene.
- Esia ate ŋu adzɔ le fufɔɣi hã na ame aɖewo.
- Ate ŋu ado ƒome kple dɔgbo me dɔlékuiwo hã (e.g., dɔgbo ƒe vevesese, aɖuɖɔtoe).
2. Nusiwo do ƒome kple dɔléle vɔ̃ɖi
Ɣeaɖewoɣi la, Sweet Syndrome do ƒome kple kansa ƒomevi aɖewo . Esia nye nyateƒe vevietɔ le kansa siwo do ƒome kple ʋu abe Acute Myeloid Leukemia ene gome. Ŋutilã ƒe nɔnɔme sia dzɔna le tɔtrɔ siwo kansa la hena vɛ le ŋutilã me ta.
3. `(Drug-induced)` le atike aɖewo ta
Esia hã nye nya vevi aɖe. Atike aɖewo siwo míenona hã ateŋu ahe ``Sweet Syndrome'' vɛ.
- `(Dɔlékuiwutikewo)` ƒomevi aɖewo, le kpɔɖeŋu me `(BactrimTM)` (si me `(Co-trimoxazole)` le).
- Vevesesenutsitikewo kple dɔlékuiwutike siwo woyɔna be ``NSAIDs''.
- Atike aɖe si woyɔna be `Granulocyte Colony-Stimulating Factor (G-CSF). Wotsɔa esia naa be woatsɔ aʋã ŋutilã la be wòawɔ ʋumenugbagbevi ɣi ƒomevi aɖe si woyɔna be `Neutrophil`. Lãmenugbagbevi siawoe wɔa avu kple dɔlékuiwo.
Bu eŋu kpɔ, ne èdze dɔléle aɖe ƒe atike nono gɔme vɔ la, ne asrã dze wò ŋutigbalẽ dzi kasia eye wò ŋutigbalẽ biã le ŋkeke ʋɛ aɖewo alo kwasiɖa ɖeka alo eve me la, ele be nàsusui be ate ŋu atso atike ma gbɔ.
Nukae nye `(Sweet Syndrome)` ƒe dzesiwo?
``Sweet Syndrome`` ƒe dzesiwo dzea egɔme kpata. Dzesi vevi siwo wokpɔnae nye:
- Aɖuɖɔtoe dzĩ siwo le veve sem alo ɣeaɖewoɣi la, ʋuʋudedi suesuesue siwo yɔ fũ kple ʋuʋudedi dona le mo, kɔ, abɔwo, kple afɔwo dzi. Ðewohĩ abi siawo dometɔ ɖeka alo esi wu nenema anɔ anyi, eye ɣeaɖewoɣi la, woate ŋu atsi ɖekae.
- Abi alo ƒoƒoe le ŋutigbalẽa ŋu eye ɣeaɖewoɣi le nu me.
- Ŋutilã ƒe Amadede: Teƒe siwo dɔlélea le ƒe amadede ate ŋu atrɔ le ɣeyiɣi aɖe megbe.
- Dzoxɔxɔ ŋutɔ.Xɔxɔ. Dzoxɔxɔ ate ŋu anɔ Celsius degree 38 (Fahrenheit 100.4) alo esi wu nenema.
- Lãmetsiwo Kple Ƒunukpeƒewo Vevesese, Taɖuame, Kple Ðeɖiteameŋu.
- Seselelãme si bɔ be yeƒe lãme mekɔ o.
Ne dzesi siawo dometɔ ɖeka alo esi wu nenema dze kpata, vevietɔ ne asrã kple ŋutigbalẽ ƒe abi siwo le veve sem kpe ɖe eŋu la, anyo wu be nàdi atikewɔlawo ƒe aɖaŋuɖoɖo.
Aleke nàwɔ anya ne `(Sweet Syndrome)` le ŋuwò?
Ne dzesi siawo le ŋuwò la, ɖɔkta aɖe ado wò ŋutilã kpɔ nyuie. Woabia nya geɖe wò tso wò dzesiwo ŋu, abe ɣeyiɣi si me wodze egɔme, nenye be atikewɔwɔ ƒe nɔnɔme bubuwo le ŋuwò, kple nenye be èle atike aɖewo zãm.
Ɣeaɖewoɣi la, ne ŋutilãmedodokpɔ ɖeɖe mesɔ gbɔ be woanya dɔlélea o la, wò ɖɔkta ate ŋu aɖo aɖaŋu be woaɖe ŋutigbalẽ ƒe akpa sue aɖe ɖa, si bia be woaɖe ŋutigbalẽ sue aɖe atsɔ aɖoe ɖe dodokpɔxɔ me be woadoe kpɔ . Esia ate ŋu akpe ɖe ŋuwò nànya ne Sweet Syndrome alo dɔléle bubu aɖe le ŋuwò ne èlé ŋku ɖe tɔtrɔ siwo va le wò ŋutigbalẽ me lãmenugbagbeviwo me ŋu.
Tsɔ kpe ɖe eŋu la, nu bubuwo hã li siwo kpena ɖe ame ŋu le dɔlélea didi me:
- Asrã si ƒe dzoxɔxɔ wu Celsius 38 (Fahrenheit 100.4) ƒe amesinɔnɔ.
- Dɔwɔwɔ nyuie ɖe corticosteroid-tikewo ŋu.
- Le ɣeyiɣi ma ke me la, kansa, dɔléle bubu, alo fufɔfɔ.
- Ʋumenugbagbeviɣidɔlékuiwo ƒe agbɔsɔsɔ si dzi ɖe edzi le mɔ si mesɔ o nu.
Esi ɖɔkta la bu nusiawo katã ŋu vɔ la, eƒo nya ta be enye ``Sweet Syndrome''.
Nukae nye atike siwo wozãna na `(Sweet Syndrome)`?
Nya nyuiae nye be ɣeaɖewoɣi la, Sweet Syndrome nu yina le eɖokui si atike aɖeke manɔmee. Ke hã, ame geɖe hiã atikewɔwɔ.
Atike vevitɔe nye corticosteroid-tike siwo wozãna le ɖoɖo nu (e.g., prednisone). Atike siawo wɔa dɔ to abi si le ŋutilãa me dzi ɖeɖe kpɔtɔ kple dɔlélenutsiŋutete ƒe dɔwɔwɔ dzi ɖeɖe kpɔtɔ me. Corticosteroids ɖea ʋumenugbagbevi ɣiwo kple dɔlélenutsiŋutete ƒe akpa bubuwo dzi kpɔtɔna, si wɔnɛ be lãmenugbagbeviwo megblẽa nu le ame ŋu o.
Nu vevitɔe nye be nàno atike sia abe alesi wò ɖɔkta gblɔe ene pɛpɛpɛ, le agbɔsɔsɔ si nèŋlɔ na wò nu, kple ɣeyiɣi si nèŋlɔ nɛ. Menyo be nàdzudzɔ enono kpata o.
- Ne nu bubu aɖe li si gbɔ Sweet Syndrome tsona (e.g., dɔlékuiwo, kansa) la, anɔ eme be dɔléle ma si gbɔ wòtso la dada akpɔ ŋutigbalẽ ƒe kuxi siawo gbɔ.
- Ne wokpɔe be atike aɖe gbɔe esia tso (Drug-induced Sweet Syndrome) la, dzesiawo adze ɖeɖeɖa gɔme ne wonya dzudzɔ atikeawo zazã ko .
Nukae dzɔna le atikewɔwɔ vɔ megbe?
Le ame geɖe gome la, ŋutigbalẽ ƒe abi kple abi siwo Sweet Syndrome hena vɛ la hayana abi aɖeke manɔmee. Esia nye nu nyui aɖe. Gake ne dzesiawo nu yi keŋkeŋ gɔ̃ hã la, ŋutigbalẽ ƒe amadede ate ŋu anɔ anyi ɣleti geɖe.Eva le dzɔdzɔm vivivi.
Ðe woate ŋu axe mɔ ɖe Sweet Syndrome nua?
Nublanuitɔe la, esi womenya nusi tututu gbɔ Sweet Syndrome tso o ta la, mɔ aɖeke meli si dzi woato axe mɔ ɖe enu o. Míenya be afɔku aɖewo li (e.g., atike aɖewo, dɔléle aɖewo), gake menye amesiamee xɔa esia o.
Nukae nye amesi ŋu dɔléle sia le ƒe mɔkpɔkpɔ? (Nukpɔsusu) .
Le ame akpa gãtɔ gome la, Sweet Syndrome ƒe dzesiwo nu tsona le wo ɖokui si alo ne wowɔ atike na wo. Dzesiawo ate ŋu anɔ anyi kwasiɖa alo ɣleti geɖe.
Gake ne atikewɔwɔ alo atike aɖe si gbɔ wòtso gbɔe Sweet Syndrome tso la, dzesiawo ate ŋu anɔ anyi hena ɣeyiɣi aɖe. Dzesiawo ate ŋu anɔ anyi vaseɖe esime woada nusi gbɔ wòtso alo woadzudzɔ atikeawo zazã.
Ɣekaɣie wòle be nàkpɔ ɖɔkta?
Ne dzesiwo le ŋuwò abe esiwo ŋu míeƒo nu tsoe le nyati sia me ene, siwo dometɔ aɖewoe nye dzoxɔxɔ ƒe gɔmedzedze kpata kple teƒe dzĩ siwo le veve sem, ƒoƒo, alo ʋuʋudedi le wò ŋutigbalẽ ŋu la, ele be nàkpɔ ɖɔkta godoo. Azɔ hã, ne ènya xoxo be Sweet Syndrome le ye ŋu eye wòdze abe wò dzesiwo le sesẽm ɖe edzi ene, alo ne dzesi yeyewo va dze ŋuwò la, gblɔe na wò ɖɔkta enumake. Atikewɔwɔ kaba ate ŋu akpe ɖe ŋuwò nàɖe kuxi siwo ate ŋu ado mo ɖa dzi akpɔtɔ.
Gbedasi si Wotsɔ Yi Aƒeme
- Sweet Syndrome nye dɔdzẽ ƒe dɔléle si mebɔ o si nana ŋutigbalẽ ƒe abi dzĩ siwo le veve sem eye dzoxɔxɔ kpata kpena ɖe eŋu.
- Togbɔ be womenya nusi tututu gbɔ esia tso o hã la, ate ŋu atso dɔléle aɖewo, fufɔfɔ, kple atike aɖewo gbɔ.
- Dzesi vevitɔwoe nye asrã, ŋutigbalẽ biã, kple ŋutilã ƒe vevesese.
- Ŋku ƒe kuxiwo ate ŋu ado mo ɖa.
- Woate ŋu atsɔ corticosteroids adae dzidzedzetɔe. Ele vevie hã be woada nusi gbɔ wòtso.
- Zi geɖe la, edaa gbe le eŋu abi aɖeke manɔmee, gake ŋutigbalẽ ƒe amadede ate ŋu atrɔ hena ɣeyiɣi aɖe.
- Ne dzesi siawo le ŋuwò la, di atikewɔlawo ƒe aɖaŋuɖoɖo enumake.
Mele mɔ kpɔm be nyatakaka sia aɖe vi na wò. Aleke kee wò atikewɔwɔ ƒe nɔnɔme ɖale o, ele vevie ŋutɔ be woana nànya nu tso eŋu nyuie.
` Sweet Syndrome, dzoxɔxɔ, ŋutigbalẽ ƒe abi, ŋutigbalẽ ƒe dɔlélewo, dɔdzẽ, corticosteroids, dɔléle siwo mebɔ o











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